Ɣeaɖewoɣi ne míenɔ anyi kpoo ko la, lãmeka aɖe si le míaƒe ŋutilã me ʋuʋuna zi ɖeka, alo? Ðewohĩ míele alɔ̃ dɔm eye míanyɔ kple ʋuʋudedi. Zi geɖe la, nu siawo tɔgbe dzɔna ɖe amesiame dzi. Gake ne lãmeka ƒe ʋuʋu sia yi edzi, ne edo kplamatse gbesiagbedɔwo la, ate ŋu anye atikewɔwɔ ƒe nɔnɔme aɖe ƒe dzesi. Eyata egbea, mina míaƒo nu tso nusi ‘Myoclonus’ sia nye, nusi henɛ vɛ, kple ɣeyiɣi si wòle be míatsi dzi ɖe eŋu ŋu.
Nukae nye Myoclonus?
Kpuie ko la, Myoclonus nye lãmeka ɖeka alo esi wu nenema ƒe ʋuʋu alo ʋuʋu kpata, le lɔlɔ̃nu faa me, eye wònɔa ʋuʋum ɣeyiɣi kpui aɖe. Ate ŋu anɔ abe elektrikŋusẽ ƒe ƒoƒo ene eye wòanɔ anyi sɛkɛnd ɖeka ƒe akpa sue aɖe ko. Ate ŋu agblẽ nu le lãmeka ɖeka ko ŋu le abɔ, afɔ, abɔta, akɔta, akɔta, alo mo, alo ate ŋu agblẽ nu le lãmeka geɖe ŋu zi ɖeka.
Ame si le lãmesẽ me gɔ̃ hã ate ŋu ato esia me le eƒe agbemeɣeyiɣi aɖe me. Gake ɣeaɖewoɣi la, ate ŋu anye atikewɔwɔ me nɔnɔme sesẽ geɖe ƒe dzesi hã.
Myoclonus ate ŋu adzɔ le mɔ vevi eve nu:
- Positive myoclonus: Esiae nye esime lãmekaawo ƒoa ƒu zi ɖeka.
- Negative myoclonus: Esia nye lãmekawo ƒe ɖiɖi kpata. Le atikewɔwɔ me la, wogayɔnɛ be ``Asterixis''. Eƒe dzesi enye asiʋuʋu si wotsɔa asi ƒoa ƒui.
Nukawo koŋue hea Myoclonus vɛ?
Nu geɖe li siwo gbɔ myoclonus tsona. Wo dometɔ aɖewo bɔ ŋutɔ eye wokpɔa mɔ na wo. Gake bubuwo ate ŋu atso atikewɔwɔ me nɔnɔme siwo gblẽa nu le míaƒe ŋutilã ƒe ɖoɖo vovovowo ŋu gbɔ. Eŋutinunyalawo ma nu siawo siwo gbɔ wòtsona ɖe hatsotso vevi ene me.
Nusiwo gbɔ wòtsona le dzɔdzɔme nu, le ŋutilã me (Physiological Myoclonus) .
Esiawo nye myoclonus ƒomevi siwo megblẽa nu le ame ŋu o siwo tsoa nusiwo yia edzi le míaƒe ŋutilã me gbɔ. Susu aɖeke meli si ta wòle be míavɔ̃ esia o.
- Hiccups: Esia hã nye Myoclonus ƒomevi aɖe. Gake ne enɔ anyi wu ŋkeke eve la, anyo wu be nàyi ɖɔkta gbɔ.
- Sleep myoclonus/Hypnic jerks: Ŋutilã ƒe ʋuʋu kpata , ne èle alɔ̃ dɔm alo ne èle nyɔnyrɔ ge. Esia bɔ ɖe ame geɖe gome.
- Startle reflexes: Ne vɔvɔ̃ ɖo mí alo wɔ nuku na mí zi ɖeka la, míaƒe ŋutilã ʋuʋuna le mɔ si dzi míate ŋu aɖu o nu.
Myoclonus si tsoa asrãdɔ gbɔ
Lãmetsiwo ƒe ʋuʋu siawo ate ŋu adzɔ kple asrãdɔ aɖewo. Nɔnɔme sia bɔ vevietɔ le `(myoclonic seizures)` me. Ateŋu ado ƒome kple nɔnɔmewo abe `(Lennox-Gastaut ƒe dɔléle)` kple `(ɖeviwo ƒe myoclonic epilepsy)` hã.
Abe atikewɔwɔ ƒe nɔnɔme bubu aɖe ƒe dzesi ene (Secondary Myoclonus) .
Ne myoclonus dzɔ abe dɔléle bubu ƒe dzesi ene la, woyɔnɛ be ‘Secondary Myoclonus’. Nu geɖewo ate ŋu ahe esia vɛ. Mina míasrɔ̃ nu geɖe tso eŋu le kplɔ̃ si le ete la dzi.
| Nusi gbɔ wòtso | Numeɖeɖe kple kpɔɖeŋuwo |
|---|---|
| Dɔlélenutsiŋutete ƒe dɔlélewo | Dɔléle siwo me ŋutilã ƒe dɔlélenutsiŋutete dzea eya ŋutɔ ƒe lãmenugbagbeviwo dzi le. Le kpɔɖeŋu me: (Celiac dɔléle) . |
| Atikewo ƒe masɔmasɔ le ŋutilãa me | Ayiku alo aklãdɔ, lãkusi ƒe kuxiwo, vitamin alo mineral ƒe anyimanɔmanɔ, kple elektrikŋusẽ ƒe masɔmasɔ . |
| Ahɔhɔ̃ me abiwo | Nusiwo gblẽ le ahɔhɔ̃mekawo ŋu le oxygen ƒe anyimanɔmanɔ (cerebral hypoxia) alo ʋusɔgbɔdɔ ta. |
| Ahɔhɔ̃medɔléle siwo gblẽa nu le ame ŋu | Le kpɔɖeŋu me: tagbɔdɔ si do ƒome kple (Alzheimer ƒe dɔléle) , (Lewy ƒe ŋutilã ƒe tagbɔdɔ) , kple (Parkinson ƒe dɔléle) . |
| Domenyiŋusẽfianu ƒe dɔlélewo | Dɔléle siwo DNA ƒe tɔtrɔ siwo woate ŋu anyi tso dzilawo gbɔ hena vɛ. Le kpɔɖeŋu me: (Krabbe ƒe dɔléle) , (Wilson ƒe dɔléle) . |
| Dɔlékuiwo | Dɔlékui alo dɔlékuiwo ƒe dɔléle siwo gblẽa nu le ahɔhɔ̃ alo lãmekawo ŋu. Le kpɔɖeŋu me: (Herpes simplex dɔlékui) , (Lyme dɔléle) .. |
| Lãmetsi alo aklã ƒe abixɔxɔ | Afɔku gblẽa kadodo me le ahɔhɔ̃a kple ŋutilã ƒe akpa aɖewo dome, si wɔnɛ be akpa mawo wɔa dɔ le wo ɖokui si. |
| Atikewo kple atikewo | Esia ate ŋu atso atike siwo wozãna ɖɔkta ƒe atikewɔmɔnu manɔmee (abe aha sesẽ, cocaine, heroin ene) gbɔ. Ate ŋu atso atike siwo ɖɔkta ŋlɔ nɛ hã gbɔ, abe atike siwo wua asrã, blanuilélenutsitikewo , ʋusɔgbɔdɔtikewo, kple dɔlékuiwutikewo ene . |
| Aɖi kple aɖinuwo | Ga kpekpewo abe lead, manganese, mercury ene ɖuɖu. Aɖiwo abe nudzodzoeviwutikewo (e.g. methyl bromide ). |
Myoclonus Vevietɔ
Esia nye domenyiŋusẽfianu ƒe nɔnɔme si tso dzidzime yi dzidzime. Zi geɖe la, megblẽa nu le ame ŋu o eye megagblẽna ɖe edzi le ɣeyiɣi aɖe megbe o. Gake ahanono ate ŋu ana lãmekawo ƒe ʋuʋu siawo nadze ƒã vie.
Ðe woate ŋu axe mɔ ɖe nɔnɔme sia nua?
Myoclonus nye nusi dzɔna kpata, nuxlɔ̃ame aɖeke manɔmee. Eyata womate ŋu axe mɔ ɖe myoclonus ƒomevi siwo ŋu míeƒo nu tsoe va yi, siwo woyɔna be physiological and essential myoclonus, nu o.
Gake míate ŋu aɖu myoclonus ƒe nɔnɔme siwo dɔléle bubuwo (secondary) kple epilepsy (epileptic) hena vɛ dzi vaseɖe afi aɖe.
- Ƒo asa na atike muamewo zazã: Ƒo asa na atike siwo ɖɔkta meŋlɔ na wò o la zazã. Azɔ hã, ne èkpɔ dzesi siawo le atike si ɖɔkta ŋlɔ na wò nono vɔ megbe la, na wò ɖɔkta nanya enumake. Wole afima be yewoakpe ɖe ŋuwò, ke menye be yewoadrɔ̃ ʋɔnu wò o. Eyata ele vevie na wò dedienɔnɔ kple atikewɔwɔ nyuie be nàgblɔ nusianu si nèzã la na wo.
- Takpɔ wò lãmekawo ta: Dedienɔnɔ ƒe dɔwɔnuwo abe gakuku kple zikpuimeka ene zazã ate ŋu axe mɔ ɖe abixɔxɔ nu le wò ahɔhɔ̃ kple aklã ŋu.
- Kpɔ nɔnɔme siwo nɔa anyi didi gbɔ: Ne dɔléle siwo nɔa anyi didi abe asrã alo lãkusidɔ ene le ŋuwò la, wò ɖɔkta ƒe mɔfiamewo dzi wɔwɔ pɛpɛpɛ ate ŋu akpe ɖe ŋuwò nàxe mɔ ɖe myoclonus ƒe dzɔdzɔ nu alo aɖe edzi akpɔtɔ.
Ɣekaɣie wòle be míayi ɖɔkta gbɔ?
Spasticity si bɔ mehiã be woawɔ atike nɛ o. Gake ne lãmeka siawo ƒe ʋuʋu yi edzi, vevietɔ ne wodo kplamatse wò gbesiagbedɔwo alo alɔ̃dɔdɔ la, ele be nàkpɔ ɖɔkta godoo.
Ðo ŋku edzi be mehiã be nàtsi dzodzodzoe le nane abe ʋuʋudedi si sɔ ene ŋu o. Gake ne ʋuʋudedi siawo gakpɔtɔ li la, ate ŋu anye nu sesẽ aɖe ƒe dzesi, eyata nunya le eme be nàdi atikewɔlawo ƒe aɖaŋuɖoɖo.
Ne èsusu be yeɖu aɖi aɖe la, yi kɔdzi ƒe Atikewɔwɔ Kpata ƒe Dɔwɔƒe (ETU) enumake. Àte ŋu aƒo ka na Dukɔa ƒe Aɖi Ŋuti Nyatakaka Dɔwɔƒe si le Colombo Dukɔa ƒe Kɔdzi hã axɔ aɖaŋuɖoɖo.
Myoclonus ƒomevi tɔxɛ bubuwo
Myoclonus ƒomevi tɔxɛ bubu geɖewo li, siwo ƒe hatsotso aɖewo me koe wòdzɔna le alo le mɔ aɖewo koŋ nu.
Vidzĩ ƒe alɔ̃dɔdɔ ƒe myoclonus si me dɔlékui aɖeke mele o
Esia nye nɔnɔme si dzea vidzĩ yeyewo dzi. Vidzĩ siawo ƒe abɔwo alo ŋutilãwo ʋuʋuna zi ɖeka ne wole alɔ̃ dɔm. Togbɔ be esia adze abe asrãdɔ ene ne wokpɔe gbã hã la, electroencephalogram (EEG) meɖea asrãdɔ aɖeke fiana o. Esia megblẽa nu le vidzĩa ŋu o eye zi geɖe la, ebuna keŋkeŋ ne exɔ ɣleti 6.
Titina to ƒe myoclonus
Esiae nye ne lãmeka aɖe si woyɔna be tensor tympani si le wò to me la ƒo ɖe to me le mɔ si dzi womate ŋu aɖu o nu. Zi geɖe la, lãmeka sia tsia ne míele nu ƒom, le nu ɖum, alo le nu kom be wòakpɔ to ememetɔ ta. Gake le go sia me la, lãmeka sia ƒoa ke ɖe to le ɣeyiɣi si mesɔ o me, si wɔnɛ be gbeɖiɖi si le to me nɔa ƒoƒom alo nɔa dodom ɣesiaɣi. Esia doa dziku, gake menye afɔku o. Woate ŋu atsɔ amekoko alo mɔnu bubuwo adae.
Opsoclonus-myoclonus ƒe dɔléle (OMS) .
Opsoclonus nye lãmeka siwo kpɔa ŋkuawo ƒe mɔfiame dzi ƒe ʋuʋu le wo ɖokui si. OMS nye nɔnɔme si mebɔ o si me ŋku ƒe ʋuʋu kple ŋutilã ƒe lãmekawo ƒe ʋuʋu siaa dzɔna ɖekae. Ɣeaɖewoɣi la, edzɔna ne míaƒe dɔlélenutsiŋutete dze mía ŋutɔwo ƒe lãmekawo dzi vodadatɔe. Le ɖeviwo gome la, ahɔhɔ̃mekansa ƒomevi aɖe si woyɔna be neuroblastoma ate ŋu atso dɔlélenutsiŋutete ƒe ŋuɖoɖo sia gbɔ. Le ame tsitsiwo gome la, nɔnɔmea ate ŋu ado ƒome kple aɖuɖɔtoe, no, alo azigolo me dɔdzẽ.
Aɖuɖɔtoe me myoclonus
Esia nye myoclonus ƒomevi aɖe si gblẽa nu le aɖu falɛfalɛ ƒe lãmeka siwo le míaƒe nu me ŋu. Esia ate ŋu ana gbeɖiɖi si mebɔ o nado le to me si nye ‘clicking’. Esia ate ŋu anye domenyiŋusẽfianu alo ahɔhɔ̃a ƒe gbegblẽ ƒomevi aɖe ƒe dzesi. Zi geɖe la, woate ŋu atsɔ atikewo aɖu nɔnɔme sia dzi.
Gbedasi si Wotsɔ Yi Aƒeme
- Myoclonus nye lãmekawo ƒe ʋuʋu kpata. Nuwo abe ʋuʋudedi kple alɔ̃dɔdɔ ene sɔ eye womegblẽa nu le ame ŋu o.
- Gake ne lãmeka ƒe ʋuʋu sia yi edzi, edzɔna enuenu, esẽna, alo doa kplamatse wò gbesiagbegbenɔnɔ la, ate ŋu anye atikewɔwɔ me nɔnɔme bubu aɖe ƒe dzesi.
- Le nɔnɔme sia tɔgbe me la, mègaŋe aɖaba ƒu edzi o, eye nàkpɔ wò ɖɔkta godoo.
- Atikewɔwɔ nɔ te ɖe nusi gbɔ wòtso dzi, si wò ɖɔkta koe ate ŋu anya.
- Nuƒoƒo na wò ɖɔkta anukwaretɔe tso atikewo alo nu bubu siwo zãm nèle ŋu le vevie ŋutɔ be nàte ŋu akpɔ dɔlélea nyuie ahadae dedie.
👩🏽 ⚕️ Nyabiase bubuwo (FAQs)
💬 Dɔléle kae woŋlɔ na Metoprolol Tartrate / Lopressor tablets na?
Esiae nye ‘dzimetike’ si kpɔ dzidzedze wu eye ŋusẽ le eŋu wu, si wɔa dɔ kabakaba wu le xexeame (Cardioselective Beta-blocker)! Enye ‘Tartrate’, eyata exɔna kabakaba ɖe ŋutilã me ne wozãe. Ðɔktawo zãnɛ tsɔ léa ‘Ʋu ƒe Ʋuʋudedi’ sesẽ, angina, eye vevietɔ abe atike gbãtɔ si woatsɔ aɖe dɔnɔa ƒe agbe le ɣeyiɣi kpui siwo le ‘Dzidɔ’ megbe ene.
💬 Aleke dzitodzito ƒe atikekui sia si wozãna enumake (Metoprolol Tartrate) ɖea ʋu ƒe sisi kple dzi ƒe ɖeɖiteameŋu dzi kpɔtɔnae?
Ne dzidɔ dze ame dzi la, dzia ƒoa kabakaba le gbedasi si nye ‘adrenaline (Epinephrine)’ si woɖona ɖa tso ahɔhɔ̃a me ta. Ne atikekui sia nya ge ɖe ŋutilã me ko la, eyia dzi si le kuku ge oxygen manɔmee la gbɔ tẽ, eye agbo siwo me adrenaline tona (Beta-1 Receptors) la ƒe 100% xea/tu, eye wotua wo sesẽe. Esi mɔ aɖeke meli si dzi gbedasia ato o ta la, ɖeko dzia ɖea blewu eye wòdzea ƒoƒo gɔme ne egbɔ ɖe eme. Emegbe agba si le dzia dzi dzi ɖena kpɔtɔna eye woɖea dɔnɔa tso ku me.
💬 Nukatae wogblɔ be mele be woadzudzɔ atike sia (Lopressor) nono kpata o? Afɔku kawoe le eme (Aɖaka Yibɔ ƒe Nuxlɔ̃ame)?
Ne èno atikekui sia ɣleti geɖe eye emegbe ‘wòdzudzɔ zi ɖeka’ la, adrenaline-xɔla mawo katã siwo xe mɔ na wo la aʋu zi ɖeka màte ŋu aɖu wo dzi o! Emegbe le aɖabaƒoƒo ʋɛ aɖewo ko me la, dzidɔ sesẽ aɖe adze dziwò eye wò dzi atɔ (Angina Exacerbation / Myocardial Infarction / Severe Tachycardia) si wua ame ale gbegbe be àte ŋu aku! Azɔ hã, atikekui sia ate ŋu ana wò dzi nagbɔdzɔ akpa eye wòana nàtɔtɔ/alɔ̃dɔdɔ fũu akpa/alɔ̃madɔmadɔ/ɖeɖiteameŋu.











💬 Comments (0)
Womeɖo nya aɖeke ɖe amewo haɖe o. Tsɔ wò nyaŋuɖoɖo kpe ɖe afisia zi gbãtɔ.
Tsɔ wò nyaŋuɖoɖo kpee