Ðe viwò suea mele to ɖom nyuie ne èle nu ƒom oa? Alo ɖe nèsena le ɖokuiwò me be nya si gblɔm nèle la le tɔtɔm? Ɣeaɖewoɣi la, vovototo aɖewo ate ŋu anɔ ale si ɖevi suewo sea gbeɖiɖiwoe me. Le nɔnɔme mawo me la, nɔnɔme aɖe si woyɔna be Auditory Neuropathy Spectrum Disorder, alo (ANSD) kpuie, ate ŋu anye nusi gbɔ wòtso. Mègatsi dzi o, mina míaƒo nu tso esia ŋu bɔbɔe.
Nukae nye esia (Auditory Neuropathy Spectrum Disorder - ANSD)?
Kpuie ko la, míaƒe towoe nana míesea gbeɖiɖi siwo ƒo xlã mí. Emegbe, wotrɔa gbeɖiɖi mawo wozua gbedasi siwo gɔme ahɔhɔ̃a ate ŋu ase eye woɖoa wo ɖe ahɔhɔ̃a. Ke hã, ɣeaɖewoɣi la, gbedasi siawo tsakana ne woɖo ahɔhɔ̃a gbɔ, alo womeɖoa afima kura o. Emae nye nusi míeyɔna be Auditory Neuropathy Spectrum Disorder, alo (ANSD).
Nusiwo ate ŋu adzɔ ɖe ɖevi siwo ŋu dɔléle sia le (ANSD) dzi dometɔ aɖewoe nye esi:
- Ate ŋu asesẽ be woade vovototo gbeɖiɖi ɖeka kple bubu dome.
- Ðewohĩ màte ŋu ase nya si gblɔm ame aɖe le la gɔme nyuie o .
- Ate ŋu ase le ɖokuiwò me abe ɖe nèse gbeɖiɖi aɖe eye kasia wòbu ene .
- Adze abe nusi nèse gbeɖeka menye nusi nèse le ŋufɔke o ene, si fia be nusi nèsena trɔna .
Gake nya nyui aɖe li. Ðevi siwo ŋu dɔléle sia le (ANSD) gɔ̃ hã ate ŋu ana woƒe gbegbɔgblɔ ƒe ŋutetewo nanyo ɖe edzi eye woaɖo dze kple ame bubuwo nyuie to atikewɔnuwo zazã, atikewɔwɔ, kple kadodomɔnu siwo wokpɔna (i.e., kadodomɔnu siwo wozãna tsɔ zãa nukpɔkpɔ ƒe dzesiwo) me.
Nukatae esia (ANSD) dzɔna? Nukawoe gbɔ wòtsona?
Nu vevitɔ si gbɔ nɔnɔme sia (ANSD) tsonae nye nusiwo gblẽ le to ƒe akpa aɖe , si nye míaƒe to ememetɔ ƒe akpa si woyɔna be tomeka (si ƒoa gbeɖiɖi nu ƒu hewɔa gbedasiwo) kple ahɔhɔ̃a.
Ðevi siwo le abe esiawo ene ate ŋu axɔ (ANSD):
- Le vidzĩ siwo wodzi do ŋgɔ na woƒe dzidziɣi (vidzĩ siwo wodzi do ŋgɔ na ɣeyiɣi si woɖo ɖi).
- Ne ƒomea me tɔ aɖe xɔ nɔnɔme sia (ANSD) kpɔ.
- Ne jaundice sesẽ aɖe do mo ɖa le vidzidzi me.
- Ne oxygen mesɔ gbɔ do ŋgɔ na vidzidzi alo le vidzidzi megbe o ((oxygen sue)) .
- Atike aɖewo li siwo ate ŋu agblẽ nu le to ƒe akpa siwo sea nu gɔme alo tomeka la ŋu. Ne ɖevia xɔ atike mawo tɔgbe kpɔ .
- Ne domenyiŋusẽfianu alo ahɔhɔ̃mekawo ƒe dɔléle aɖewo le ŋuwò , abe Charcot Marie Tooth dɔléle ene.
- Ne abi gã aɖe le ta na wò la .
Aleke nàwɔ anya ne (ANSD) le ŋuwò? Nukawoe nye dzesiawo?
Dzesi siawo ate ŋu adze egɔme le ƒe ɖesiaɖe me. Gake wodzia vidzĩ akpa gãtɔ kple dɔléle sia (ANSD). Tosese ƒe kuxiwoAte ŋu atso esi nu mesẽ o dzi va ɖo esi nu sẽ dzi. Nukutɔe la, ɖevi aɖewo te ŋu sea gbeɖiɖiwo le mɔ si sɔ nu gake esesẽna na wo be woase nya si gblɔm wole la gɔme nyuie.
Vidzĩ siawo ate ŋu ato vidzĩ yeyewo ƒe tosese dodokpɔa me, gake le ɣeyiɣi aɖe megbe hafi wova kpɔnɛ dzea sii vivivi be tosese me kuxiwo le yewo ŋu.
Lé be na nu siawo le viwòa ƒe ƒe gbãtɔ me.
Kpɔe ɖa be viwòa wɔa nu nyuie ɖe nusese ƒe nu vevi siawo ŋu le eƒe agbe ƒe gbãtɔ me hã. Ne menye nenema o la, anyo be nàƒo nu kple ɖɔkta.
- Vidzĩ si wodzi yeyee : Ðe wòti kpo alo "tsɔa nu ƒua gbe" ne ese toɣliɖeɖe sesẽ aɖe kasia?
- Kaka wòaxɔ abe ɣleti 3 ene : Ðe viwòa dea dzesi wo dada alo wo fofo ƒe gbea? Ðe wotrɔa woƒe ta ɖe mɔ ma nua?
- Kaka wòaxɔ abe ɣleti 6 ene : Ðe viwòa trɔa woƒe ŋku alo ta ɖe mɔ ma nu ne ese gbeɖiɖi yeye aɖea? Ðe wogbugbɔa gbeɖiɖiwo abe "uh" kple "ah" enea?
- Kaka wòaxɔ abe ɣleti 12 ene (ƒe ɖeka) : Ðe viwòa wɔa gbeɖiɖi suesuesue siwo gɔmesese aɖeke mele o (gbeɖiɖi siwo le ɖiɖim)? Ðe viwòa ɖoa eŋu ne èyɔ eƒe ŋkɔa? Ðe viwòa dzea agbagba be yeasrɔ̃ nyawoa? Ðe viwòa gblɔa nya ʋɛ aɖewo, abe "mama" kple "bye-bye" enea?
Ne viwòa tsi vie la, kpɔe ɖa be dzesi siawo dometɔ aɖe le wo ŋu hã.
Ne viwòa le tsitsim la, ate ŋu aɖe dzesi siawo tɔgbe afia ne tosese ƒe kuxi aɖe le eŋu:
- Nuƒoƒo mebɔ o, me mekɔ o, alo womeƒoa nu kura o .
- Ðe nèsena le ɖokuiwò me be womele to ɖom ye o alo be yemele mɔfiamewo dzi wɔm oa ?
- Ðe mèɖoa nya ŋu ne woƒo nu na wò le mɔ si sɔ nu oa, alo ɖe nèɖoa ŋuɖoɖo siwo mehiã o ?
- Ðe wò susu nɔa nu ŋu bɔbɔe ne toɣliɖeɖe geɖe ƒo xlã wòa?
- Èdi be yeadzi TV la ƒe gbeɖiɖi ɖe edzia ?
- Ðe nusɔsrɔ̃ ƒe kuxiwo le ŋuwòa ?
Ne ɖikeke aɖe le mewò le viwò ŋu le nane si le abe esia ene ŋu la, ele be nàƒo nu kple ɖɔkta godoo. Emae nye nu nyuitɔ kekeake si nàwɔ.
Aleke nàwɔ anya ne (ANSD) ƒe nɔnɔme le ŋuwò?
Toŋutinunyala koe ate ŋu anya ANSD nyuie. Eyae nye amesi wɔa dodokpɔ tɔxɛwo eye wòkpena ɖe amesiwo ƒe to me gblẽ ŋu. Dodokpɔ vevi geɖe li siwo ate ŋu akpe ɖe ame ŋu wòanya ANSD:
Nukawoe nye dodokpɔ siawo?
- Otoacoustic emission (OAE) test : Esia doa alesi to ememetɔ ƒe akpa si woyɔna be cochlea le dɔ wɔm nyuie la kpɔna. Wowɔa esia ne vidzĩa le alɔ̃ dɔm alo bɔbɔ nɔ anyi kpoo. Wotsɔa tomeka suewo dea to me eye gbeɖiɖi fafɛ aɖe, abe gbeɖiɖi si le ʋuʋum ene, dona. Emegbe wotsɔa nu suesuesue siwo woyɔna be electrodes dzidzea alesi to ememetɔ wɔa nui.
- Tome ahɔhɔ̃ ƒe dɔwɔwɔ (ABR) dodokpɔ: Esia doa alesi gbeɖiɖi si tso to me la zɔa to tosese ƒe lãmekaa me yia ahɔhɔ̃meka si le ahɔhɔ̃a ƒe gɔme la nyuie eye wòdzena nyuie la kpɔna. Ne nyatakakaawo mele yiyim ɖe ahɔhɔ̃a me nyuie o la, dodokpɔ sia aɖee afia. Zi geɖe la, ne (OAE) dodokpɔa sɔ, eye (ABR) dodokpɔa mewɔa nu boo aɖeke o alo womewɔa dɔ aɖeke kura o la, ekema wosusuna be mɔnukpɔkpɔ gã aɖe li be (ANSD) naxɔe.
- Middle ear muscle reflex (MEMR) test : Lãmetsi sue aɖe le míaƒe to me si sesẽna le eɖokui si ne míese gbeɖiɖi sesẽ aɖe. Esia tae woyɔnɛ be (MEMR). Le dodokpɔ sia me la, wotsɔa rababa ƒe nugbɔ sue aɖe dea to me eye woɖoa gbeɖiɖi sesẽ aɖe ɖa. Wozãa mɔ̃ aɖe tsɔ kpɔa alesi lãmeka sia wɔa nu ɖe gbeɖiɖia ŋui. Le ɖevi si ŋu (ANSD) le gome la, nuwɔna sia medzɔna ɖe gbeɖiɖi sesẽwo ta o, alo ebia gbeɖiɖi sesẽ aɖe sã wu ame dzɔdzɔe hafi wòaxɔ nuwɔna sia.
Vidzĩ yeyewo ƒe tosese dodokpɔ ƒe ɖoɖowo ate ŋu azã dodokpɔ siawo (OAE) kple (ABR) ƒe mɔnu bɔbɔewo. Gake hafi woate ŋu akpɔ dɔlélea (ANSD) nyuie la, ele be woawɔ dodokpɔ siawo bliboe.
Dodokpɔ bubu kawoe ate ŋu ahiã?
Ne wokpɔe be (ANSD) le ɖevia ŋu vɔ la, ahiã be woawɔ dodokpɔ bubu geɖe:
- (MRI) dodokpɔ : Be woakpɔe ɖa be kuxi aɖe le toa me hã eye nenye be tomeŋusẽ le to eveawo me hã.
- Domenyiŋusẽfianu dodokpɔ : Be woakpɔe ɖa be nɔnɔme sia (ANSD) nye domenyiŋusẽfianu ƒe dɔléle aɖe ƒe akpa aɖe hã.
- Ahɔhɔ̃ŋutinunya dodokpɔ : Kpɔe ɖa be ahɔhɔ̃mekawo ƒe kuxi bubuwo hã le ŋuwò hã.
- Nukpɔkpɔ dodokpɔ : Zi geɖe la, tosese kple nukpɔkpɔ ƒe kuxiwo ate ŋu azɔ ɖekae. Eyata ele vevie ŋutɔ be woayi ŋkudɔdala gbɔ ne wokpɔ ɖevi si ŋu ANSD le.
Aleke wokpɔa dɔlélea (ANSD) gbɔe?
Eŋutinunyala bibiwo ƒe ƒuƒoƒo aɖee daa dɔ na ɖevi siwo ŋu ANSD le . Esia fia be toŋutinunyala (toŋutinunyala), to, ŋɔti kple ŋɔti ŋuti nunyala (ENT ɖɔkta), nuƒoƒo kple gbegbɔgblɔ ŋuti dɔdala (nuƒoƒo kple gbegbɔgblɔ ŋuti dɔdala), kple hehenana ŋuti nunyala wɔa dɔ ɖekae wɔa atikewɔwɔ ƒe ɖoɖo nyuitɔ kekeake.
Atikewɔwɔ nɔ te ɖe nu geɖe dzi, siwo dometɔ aɖewoe nye ƒe si ɖevia xɔ, tomeka ƒe akpa si mele dɔ wɔm nyuie o, kple alesi tosese ƒe kuxia nu sẽe.
Zi geɖe la, ɖevi siawo kpɔa viɖe geɖe tso toɖoɖomɔ̃ siwo kpena ɖe ame ŋu zazã me. Tsɔ kpe ɖe mɔ̃ siawo ŋu la, nuƒoƒo kple gbegbɔgblɔ ƒe atikewɔwɔ dzi yiyi be ɖevia ƒe nuƒoƒo kple toɖoɖo ƒe ŋutete nanyo ɖe edzi ye nye mɔ nyuitɔ si dzi woato akpɔ emetsonuwo .
Nukawoe nye mɔ̃ siawo siwo kpena ɖe ame ŋu?
- Frequency modulation (FM) ƒe ɖoɖowo: (FM) ɖoɖo sia ɖea toɣliɖeɖe si mèdi o si ƒo xlã wò dzi kpɔtɔna eye wònana nuƒola (le kpɔɖeŋu me, nufiala ƒe) gbe sena nyuie eye wòsena sesĩe. Nuƒomɔ̃a doa nuƒomɔ̃ sue aɖe kple (nuƒomɔ̃). Esia (nyaɖoɖomɔ̃) ɖoa elektrɔnik dzesi aɖe ɖe (nuxɔla) si ɖevia dona ɖe woƒe to me alo wotsɔe bla ɖe (tomemɔ̃) ŋu tẽ. Esia ɖea vi ŋutɔ le sukuxɔwo kple teƒe bubu siwo toɣliɖeɖe le elabena woate ŋu atsɔe atsae.
- Tomemɔ̃ : Wozãa esia tsɔ doa gbeɖiɖi si ɖoa to gbɔ la ɖe ŋgɔ. Ðevi aɖewo siwo ŋu ANSD le ate ŋu akpɔ viɖe tso tomemɔ̃wo me, vevietɔ ne wozã wo kpe ɖe FM-mɔ̃ si ŋu míeƒo nu tsoe va yi ŋu. Gake tomemɔ̃ ɖeɖe dzaa mekpena ɖe ɖevi siwo ŋu ANSD le ŋu boo o , elabena gbeɖiɖi si wotu xoxo la koe wodoa ŋusẽe.
- Tomemɔ̃ : Le ɖevi aɖewo siwo ŋu ANSD le gome, vevietɔ amesiwo mekpɔa kpekpeɖeŋu si sɔ tso tomemɔ̃wo gbɔ o la, tomekadodo nye tiatia nyui aɖe. Esia nye mɔ̃ si wotsɔa amekoko dea to me . Etoa to ƒe akpa siwo mele dɔ wɔm nyuie o ŋu eye wòʋãa tomeka la tẽ. Ne hehe nyui na ɖevi siwo wotsɔ tomeka de to me eye woyi edzi le atike wɔm na wo la, woate ŋu asrɔ̃ alesi woase nu nyuie ahaƒo nu nyuie.
Nu bubu kae nèdi be yeanya?
Tsɔ kpe ɖe tomemɔ̃wo zazã ŋu la, ɖevi siwo ŋu ANSD le ate ŋu asrɔ̃ nukpɔkpɔ ƒe kadodomɔnu hã, siwo nye mɔ siwo dzi woato aɖo dze to nusiwo wokpɔna kple woƒe ŋkuwo zazã me.
Nukawoe nye kadodomɔnu siawo siwo wokpɔna?
- Tokunɔgbe : Esia nye gbegbɔgblɔ si to vovo. Gbeŋutise, nyagbewo, kple nyagbewo ƒe ɖoɖo le esi. Wotrɔ asi le eŋu be woazãe ɖe gbe si wodona teƒe.
- Cued Speech : Esia bia be nuƒola la nawɔ asiwɔwɔ ɖe nu dzi. Asi ƒe dzesi siawo kpena ɖe nyasela ŋu wòdea vovototo ŋɔŋlɔdzesi siwo ɖi wo nɔewo dome (le kpɔɖeŋu me, ‘ব’ kple ‘প’, alo ‘ম’ kple ‘ব’). Woateŋu azã Cued Speech le gbegbɔgblɔ ɖesiaɖe me, eye wòɖea vi ŋutɔ na gbe eve dolawo ƒe ƒomewo.
- Signing Exact English (SEE) : Esia nye tokunɔgbe ƒe ɖoɖo si zãa Eŋlisigbe ma ke tututu si wodona le mɔ ɖeka nu, nya ɖe nya nu. Tokunɔgbe ƒe akpa aɖewo hã le eme, gake wodo nyagbewo ƒe ɖoɖo kple gbeŋutise tso Eŋlisigbe me.
Cued Speech kple SEE siaa ɖea nusi wogblɔ la gɔme tẽ. Wotrɔ asi le wo ame evea siaa ŋu be woazã wo kpe ɖe gbe si wodona ŋu be wòakpe ɖe ŋuwò nàse nusiwo nuyi xexlẽ ɖeɖe mate ŋu ase o gɔme nyuie.
Dzilawo wɔa akpa vevi aɖe ŋutɔ le wo vi siwo ŋu ANSD le la fiafia me be woaɖo dze kple ame bubuwo ahaɖo dze kple wo. Woate ŋu akpɔ nu nyuitɔ kekeake ne wowɔ dɔ kplikplikpli kple atikewɔlawo ƒe ƒuƒoƒoa.
Àte ŋu akpɔ nyatakaka bubuwo kple kpekpeɖeŋu le nyatakakadzraɖoƒewo abe esiawo ene:
- CDC: Tosese ƒe Dɔléle Kple Viwò (United States ƒe Dɔlélenutsitsi Dɔwɔƒe ƒe nyatakakadzraɖoƒe)
- Asiwo Kple Gbewo (dzilawo kple dɔnyala bibiwo ƒe kadodo) .
Nu vevitɔ kekeake siwo dzi wòle be nàɖo ŋkui (Take-Home Message) .
Enyo, eyata mina míaɖo ŋku nu siwo ŋu míeƒo nu tsoe siwo dzi wòle be nàɖo ŋkui la dometɔ aɖewo dzi na wò.
- Auditory Neuropathy Spectrum Disorder (ANSD) nye nɔnɔme si me gbeɖiɖi ƒe gbedasi siwo tso to me yi ahɔhɔ̃a me gblẽna alo mezɔa mɔ nyuie o.
- Ele vevie be nàde dzesi esia kaba . Ne èsusu be tɔtrɔ aɖewo le viwòa ƒe tosese ŋu alo tsi megbe la, yi ɖɔkta gbɔ enumake.
- Dodokpɔ tɔxɛwo abe (OAE) kple (ABR) koe woate ŋu akpɔ dɔléle sia nyuie .
- Mègatsi dzi o, mɔ̃wo abe (FM)-mɔ̃wo, (tomemɔ̃wo), (tomemɔ̃ siwo wotsɔ dea tome), nuƒoƒo ƒe atikewɔwɔ, kple nukpɔkpɔ ƒe kadodomɔnu ate ŋu ana viwòa ƒe nuƒoƒo ŋutete nanyo ɖe edzi .
- Abe dzilawo ene la, miaƒe ɖetsɔleme, ɖokuitsɔtsɔna, kple dɔwɔwɔ ɖekae kple atikewɔlawo ƒe ƒuƒoƒoae nye ŋusẽ gãtɔ kekeake na viwòa .
Ðo ŋku edzi be ɖevi ɖesiaɖe to vovo, eyata ele vevie be nàdi atikewɔwɔ kple kpekpeɖeŋu si sɔ na viwòa.
Tome ƒe Ahɔhɔ̃mekawo ƒe Dɔlélewo, ANSD, Tosese ƒe Kuxiwo, Ðeviwo ƒe Lãmesẽ, Tosese Dodokpɔwo, Tomeŋusẽ ƒe Dɔlélewo, Nuƒoƒo ƒe Dɔdamɔnu










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