Èsusui kpɔ be kasia yeate ŋu agate ŋu aɖu yeƒe ŋkuwo dzi o eye le ɣeyiɣi ma ke me la, yeƒe abɔ alo afɔ aɖe nabu le yeƒe ŋutilã ƒe akpa kemɛa? Le nyateƒe me la, esia nye nusi dzi ŋɔ eye wòsesẽ be míasusui, gake enye nɔnɔme si wòle be míado goe ɣeaɖewoɣi le míaƒe agbe me. Egbea míele nu ƒom tso nɔnɔme aɖe si mebɔ o si ŋu wòle vevie ŋutɔ be amesiame nanya ŋu. Esiae nye nusi ɖɔktawo yɔna be Weber Syndrome .
Nuka tututue nye Weber Dɔlélea?
Kpuie ko la, Weber Syndrome nye dɔléle si tsoa nusiwo gblẽ le wò ahɔhɔ̃ titina ŋu . Ahɔhɔ̃ titina nye tɔdzisasrã vevi aɖe si tsɔa gbedasiwo tso wò ahɔhɔ̃ me yia wò aklã me. Enye wò ahɔhɔ̃meka ƒe akpa si le wò ahɔhɔ̃a tame. Tagbɔ ƒe lãmeka vevi eve siwo kpɔa nuwo abe wò ŋkuwo ʋuʋu kple wò ŋkume ƒe ʋuʋu dzi— ŋku ƒe lãmeka si nye oculomotor nerve kple trochlear nerve —dzea egɔme tso ahɔhɔ̃a ƒe titina.
Eyata ne ahɔhɔ̃meka sia gblẽ le mɔ aɖe nu la, àkpɔ hemiplegia , si fia be màgate ŋu akpɔ ŋusẽ ɖe wò ŋutilã ƒe akpa ɖeka dzi o. Le ɣeyiɣi ma ke me la, àdo go kuxiwo le ŋku kple nukpɔkpɔ le akpa kemɛ ŋu. Esiae nye nusi wokpɔna koŋ le Weber Dɔlélea me. Wobua esia be enye nɔnɔme si mebɔ kura o .
Nusi gbɔ ahɔhɔ̃a ƒe titina ƒe nugbegblẽ tsona wue nye ʋusɔgbɔdɔ , si nye ʋu ƒe sisi yi ahɔhɔ̃a me ƒe nutsotso kpata. Ke hã, ate ŋu adzɔ le susu bubuwo hã ta.
Nukae nye esia ƒe dzesiwo? Aleke míewɔna dea dzesii?
Dzesi vevi geɖewo li siwo woate ŋu akpɔ le Weber Dɔlélea me. Woawoe nye:
- Ŋku ƒe akpa si le gegem ɖe ŋku ɖeka me (ptosis) . Edze abe ŋkua tu afã ene.
- Ŋku si ŋu dɔlélea le ate ŋu atrɔ ayi anyime kple gota , si fia be womate ŋu aɖu ŋkua dzi nyuie o.
- Nu eve kpɔkpɔ zi ɖeka (diplopia) . Woyɔa esia be nukpɔkpɔ eve.
- Abɔ kple afɔ ƒe akpa aɖe alo lãmetutudɔ keŋkeŋ le ŋutilã ƒe akpa ɖeka . Esia dzɔna le ŋku si ŋu dɔlélea le ƒe akpa si tsi tre ɖe eŋu.
Vevietɔ ŋutɔ: Ne èkpɔ dzesi siawo dometɔ ɖeka alo esi wu nenema, alo ʋusɔgbɔdɔ ƒe dzesi bubu geɖeawo dometɔ aɖe , abe nuƒoƒo ƒe gbegblẽ , seselelãme ƒe bu , nukpɔkpɔ ƒe bu , dadasɔ ƒe nyawo , alo mo ƒe ʋuʋu ene la , ele be nàyi kɔdzi enumake. Esia ate ŋu anye agbe alo ku ƒe nɔnɔme.
Ɣeaɖewoɣi la, ame siwo ŋu Weber Syndrome le la xɔa...Dadasɔ kple nuwɔwɔ aduadu ƒe kuxiwo (ataxia) , si fia be azɔlizɔzɔ kple nuwo léle sesẽ hã ate ŋu ado mo ɖa.
Zi geɖe la, ne Weber Syndrome ɖeɖeko le eme la, wò tamebubu (ŋkuɖoɖonudzi, nunya) mekpɔa ŋusẽ ɖe edzi o. Gake ne nusiwo gblẽ le ahɔhɔ̃a ƒe akpa bubuwo ŋu kaka la, dzesi bubuwo ate ŋu adze. Le kpɔɖeŋu me, ɣeaɖewoɣi la, pons, si nye ahɔhɔ̃meka ƒe akpa aɖe, ƒe lãmetutudɔ ate ŋu akplɔ Weber ƒe Dɔlélea ɖo. Le nɔnɔme ma me la, woate ŋu akpɔ dzesi bubuwo hã.
Nukawoe hea Weber ƒe Dɔlélea vɛ?
Weber Syndrome tsoa abi aɖe si le wò titina ahɔhɔ̃ ƒe akpa aɖe koŋ si le ventromedial me gbɔ. Nu vevi siwo gbɔ nusiwo gblẽa nu sia ƒomevi tsonae nye:
- Ʋusɔgbɔdɔ: Esiae nye nusi gbɔ wòtsona wu. Ate ŋu atso ʋuka aɖe si naa ʋu yia ahɔhɔ̃a ƒe akpa ma ƒe xexe alo eƒe gbagbã gbɔ.
- Brain aneurysm (ʋuka aɖe ƒe ʋuʋu kple eƒe gbagbã le ahɔhɔ̃a me).
- Ʋu si dona le ahɔhɔ̃ me.
- Ahɔhɔ̃ me dɔdzẽ.
- Dɔléle siwo ɖea lãmekawo ɖa , abe Multiple Sclerosis ene, gblẽa nu le myelin ƒe akɔta si ƒo xlã lãmekawo ŋu.
Amekae ate ŋu axɔ nusia wu? (Afɔku siwo ate ŋu ahe ame) .
Abe alesi míedzro eme va yi ene la, nusi koŋ gbɔ Weber ƒe Dɔlélea tsonae nye ʋusɔgbɔdɔ, eyata afɔku mawo ke siwo gblẽa nu le ʋusɔgbɔdɔ ŋu hã kpɔa ŋusẽ ɖe edzi. Ema nye:
- Ʋusɔgbɔdɔ (Ʋu ƒe sisi / Ʋusɔgbɔdɔ).
- Lãmetsi si sɔ gbɔ ɖe ʋu me (High cholesterol / Hyperlipidemia).
- Suklidɔ.
- Sigaretnono.
Ne afɔku siawo dometɔ ɖeka alo esi wu nenema le ŋuwò la, ele vevie ŋutɔ be nàxɔ atikewɔlawo ƒe aɖaŋuɖoɖo edziedzi ahaɖu wo dzi. Esia wɔwɔ ate ŋu aɖe afɔku si le nɔnɔmewo abe lãmetutudɔ kple Weber ƒe Dɔléle ene xɔxɔ me dzi akpɔtɔ.
Aleke ɖɔktawo dea dzesi esiae? (Dɔléle ƒe dzesi) .
Ne dzesi siwo do ƒome kple Weber Syndrome le ŋuwò la, ɖɔktawo adze agbagba gbã be yewoaɖo kpe edzi nenye be ʋusɔgbɔdɔ le ŋuwò. Esia le alea elabena atikewɔwɔ kabae nye nu vevitɔ kekeake. Be nàwɔ esia la:
- Woado ahɔhɔ̃mekawo ƒe dɔwɔwɔ kpɔ bliboe le wò lãmekawo ŋu .
- Wowɔa ahɔhɔ̃a ƒe CT-dɔdamɔnu enumake.
- Ɣeaɖewoɣi la, woate ŋu akafui hã be woado ʋuka siwo le ta kple kɔ me kpɔ eye woawɔ ahɔhɔ̃a ƒe MRI-dɔdamɔnu hã.
Ne wò dzesiwo kple fotoɖeɖe siawo ɖo kpe edzi be nu gblẽ le ahɔhɔ̃a ƒe titina ŋu la, ɖɔktawo aƒo nya ta be Weber Syndrome le ŋuwò.
Nukae nye esia ƒe atikewɔwɔ?
Ne wole Weber ƒe Dɔlélea dam la, nu gbãtɔ si ŋu wotsia dzi ɖoe nye nusi gbɔ wòtso (zi geɖe la, ʋusɔgbɔdɔ) dada . Wò atikewɔlawo ƒe ƒuƒoƒoa akpɔ wò yaƒoƒomɔ̃a dzi kaba eye wòana ʋu nagaɖo wò ahɔhɔ̃ me. Le go aɖewo me la , ahɔhɔ̃mekawo ƒe dɔwɔwɔ (ahɔhɔ̃mekawo ƒe dɔwɔwɔ) hã ate ŋu ahiã.
Gbugbɔgaɖɔɖomɔnue nye atike vevitɔ si wozãna koŋ na Weber Dɔlélea.
Nukae nye gbugbɔgaɖɔɖo? Aleke gbegbee wòle vevie?
Gbugbɔgaɖɔɖo nye hayahaya ƒe ɖoɖoa ƒe akpa vevi aɖe na ame geɖe siwo ŋu ʋusɔgbɔdɔ le. Ebia be woakpe ɖe ŋuwò nàgakpɔ aɖaŋu siwo nèbu le tɔtrɔ siwo va le wò ahɔhɔ̃ me ta, alo akpe ɖe ŋuwò nàsrɔ̃ alesi nànɔ agbe ɖe tɔtrɔawo nu. Ʋusɔgbɔdɔ gbugbɔgaɖɔɖoha alo kamededeŋutinunyala si wona hehee etɔxɛe ate ŋu akpe ɖe ŋuwò le esia me. Anyo wu be nàdze ɖɔɖɔɖoɖoɖo sia gɔme kaba ale si nàte ŋui.
Weber Syndrome kple ahɔhɔ̃mekawo ƒe ʋuʋu ƒe ɖɔɖɔɖo ate ŋu anye:
- Kamedede siwo kpena ɖe ame ŋu wòʋuʋua abɔ kple afɔ si tu (Range-of-motion exercises) .
- Kamedede siwo ana woada asɔ ahawɔ ɖeka nyuie wu.
- Na woado wò ŋkuwo kpɔ eye nàwɔ kamedede nyuitɔwo be nàɖe ŋku eve dzi akpɔtɔ.
- Ðewohĩ ame aɖewo mate ŋu aɖu woƒe aɖuɖɔ (urinary incontinence) dzi o. Hehe tɔxɛ hiã na ema (Tsinyegoe ƒe hehexɔxɔ) .
- Atikewo kple nu bubu siwo woawɔ atsɔ akpɔ ʋusɔgbɔdɔ ƒe afɔku siwo li fifia dzi eye woaxe mɔ ɖe ʋusɔgbɔdɔ si ava dzɔ le etsɔme nu.
Ɣeyiɣi didi kae wòaxɔ hafi wòahaya tso nɔnɔme sia me? (Mɔkpɔkpɔ be woahaya)
Nu geɖe kpɔa ŋusẽ ɖe amesi ŋu Weber ƒe Dɔlélea le ƒe nyagblɔɖi dzi, siwo dometɔ aɖewoe nye:
- Nuka tae wòle alea ɖo?
- Aleke gbegbee nèxɔ atike kabae nye si .
- Weber Syndrome koe le ŋuwòa, alo ɖe ahɔhɔ̃a ƒe akpa bubuwo hã gblẽa ?
- Aleke gbegbe nèle edzi dzem nyuie be nàxe mɔ ɖe lãmetutudɔ nu le etsɔme .
Zi geɖe la, amesiwo ŋu Weber Syndrome ɖeɖeko le, siwo ƒe ahɔhɔ̃ megblẽ nu bubu aɖeke o, ƒe ŋgɔdonya nyui nɔa wo si . Azɔ hã, gbugbɔgaɖɔɖo gɔmedzedze kaba le vevie ŋutɔ na hayahaya ƒe ɖoɖoa.
Ne wogbugbɔ ame aɖewo ɖɔ ɖo la, ate ŋu agate ŋu awɔ dɔ vie le woƒe abɔ kple afɔ siwo ŋu dɔlélea le la me. Gake ame bubuwo ate ŋu ato ʋuʋu sesẽ tegbee kple ahɔhɔ̃mekawo ƒe kuxi bubuwo.
Wò atikewɔlawo ate ŋu ana nàkpɔ nusi nàkpɔ mɔ na nyuie le wò nɔnɔmea nu.
Kuxi bubu kawoe ate ŋu ado mo ɖa le Weber ƒe Dɔlélea ta?
Weber Syndrome ate ŋu ahe kuxiwo vɛ wu, vevietɔ ne èle aba dzi. Esia tae wò atikewɔlawo ƒe ƒuƒoƒoa adze agbagba be yewoana nàʋu kabakaba eye nànɔ dedie alesi nàte ŋui ɖo. Kuxi siwo ate ŋu ado mo ɖa dometɔ aɖewoe nye:
- Lãmetsiwo ƒe sesẽ kple woƒe ʋuʋu .
- Abatidzivɔwo .
- Aspiration pneumonia dzɔna ne nuɖuɖu alo nunono ge ɖe yaƒoƒomɔ̃a me eye wòhe lãkusi me dɔlékuiwo vɛ.
- Ʋu ƒe sisi le afɔwo ƒe ʋuka goglowo me (Deep vein thrombosis - DVT) .
- Ʋu ma zɔna yia lãkusiwo me (aklã me ʋu ƒe sisi) .
- Aɖuɖɔtoe me dɔlélewo (UTIs) .
Mlɔeba la, nu vevitɔ kekeake si dzi wòle be míaɖo ŋkui
Ʋusɔgbɔdɔ ate ŋu atrɔ wò agbenɔnɔ le ɣeyiɣi kpui aɖe ko me. Eyata ele vevie ŋutɔ be nànya eƒe dzesiwo nyuie eye nàyi kɔdzi enumake ne wò alo ame aɖe si te ɖe ŋuwò la dze dzesi mawo gɔme. Weber ƒe Dɔléle ate ŋu anye dɔléle si mebɔ o, eye àte ŋu avɔ̃ eye nàtsi dzimaɖi ne èse eŋu nya. Gake ɖo ŋku nu ɖeka dzi be, wò atikewɔlawo ƒe ƒuƒoƒoa le klalo ɣesiaɣi be yewoakpe ɖe ŋuwò ahanɔ gbɔwò le wò hayahaya ƒe mɔzɔzɔa me. Eyata na wò susu nasẽ eye nàwɔ ɖe aɖaŋuɖoɖo siwo wona dzi.
` Weber Syndrome, lãmetutudɔ, ahɔhɔ̃mekawo ƒe ʋuʋu, ahɔhɔ̃ titina, ŋku ƒe dzesiwo, ahɔhɔ̃medɔlélewo, gbugbɔgaɖɔɖo










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