Ke manaʻo nei ʻoe i kekahi manawa ua pōwehiwehi iki kou ʻike a ua palaualelo paha? Manaʻo paha ʻoe he mea maʻamau kēia, he mea wale nō ia o ka hoʻoluhi ʻana i kou mau maka. Eia naʻe, i kekahi manawa he hōʻailona kēia o kahi mea ʻoi aku ka koʻikoʻi. I kēia lā e kamaʻilio mākou e pili ana i kahi kūlana i kapa ʻia ʻo optic atrophy , ka mea e hoʻopilikia ai i kā mākou ʻike. Mai hopohopo, e kamaʻilio mākou e pili ana i kēia ma ke ʻano maʻalahi e hiki ai iā ʻoe ke hoʻomaopopo.
He aha maoli ka Optic Atrophy?
I ka ʻōlelo maʻalahi, ʻo Optic Atrophy ka wā e hōʻino ʻia ai nā cell i loko o kou nerve optic a luku mālie ʻia. ʻO ka huaʻōlelo "atrophy" ʻo ia hoʻi kahi mea e palaho ana, nāwaliwali, a mae paha. No laila, ʻo ka mea e hana ʻia ma kēia hihia, ʻo ia ka nāwaliwali o ke nerve optic, kahi e hana ai e like me ke kaula kelepona e lawe ana i nā leka ma waena o ko mākou mau maka a me ka lolo. He kūlana koʻikoʻi loa kēia.
E noʻonoʻo i kēia ʻano: ua like ko kākou mau maka me ke kāmela. Lawe ke aʻalolo optic i ke kiʻi (ʻike maka) mai ke kāmela a haʻi aku i ka lolo, "ʻO kēia kāu e ʻike nei." No laila, inā ua hōʻino ʻia kēia aʻalolo, me he mea lā ua ʻoki ʻia ke kaula e lawe ana i ka leka. A laila, ʻoiai ke ʻike nei ka maka, ʻaʻole hele ka ʻike i ka lolo, no laila loaʻa iā mākou nā pilikia ʻike . I kekahi manawa hiki i kēia ke alakaʻi i ka nalowale loa o ka ʻike, hiki ke alakaʻi i ka makapō . Eia kekahi, ʻo ka pilikia nui ma ʻaneʻi, ʻo ia ka hiki ʻole ke hoʻihoʻi ʻia kēia pōʻino, ʻo ia hoʻi, ʻaʻole hiki ke hoʻihoʻi ʻia .
He aha nā hōʻailona e ʻike ai mākou inā loaʻa iā mākou kēia?
ʻO ka Optic Atrophy ka hōʻailona nui o nā pilikia ʻike. E nānā e ʻike inā loaʻa iā ʻoe kēia mau hōʻailona:
- Lilo ka ʻike i mea pōwehiwehi a lilo nā mea i mea pōwehiwehi: ʻO nā leka a me nā kiʻi i ʻike maopopo ʻia ma mua, i kēia manawa ke ʻano pōwehiwehi iki a maopopo ʻole. Me he mea lā ua nalowale ke kiko o ke kāmela.
- Ka nalowale o ka ʻike peripheral: ʻOiai hiki iā ʻoe ke ʻike pololei i mua, hiki iā ʻoe ke nalowale i kou hiki ke ʻike i nā mea ma nā ʻaoʻao o kou mau maka. Hiki ke manaʻo e like me ʻoe e nalowale ana i kāu ʻike peripheral, e like me ka lio.
- Makapō kala: Hiki ke paʻakikī ke hoʻokaʻawale i kekahi mau kala, ʻoi aku ka ʻulaʻula a me ka ʻōmaʻomaʻo. Hiki ke ʻike ʻia nā kala ua mae iki a i ʻole he kala ʻokoʻa.
Inā loaʻa iā ʻoe kekahi a ʻoi aku paha o kēia mau hōʻailona, mai hoʻowahāwahā iā lākou . He mea nui e ʻike koke i ke kauka maka.
No ke aha mākou e ulu ai i ka Optic Atrophy? He aha nā kumu?
Aia kekahi mau kumu e hiki ai ke hōʻino ʻia kēia aʻalolo optic. ʻO ia hoʻi, ke hoʻopilikia nei kekahi mea i ka leka e hele ana ma o ke aʻalolo optic i ka lolo. E nānā kākou i nā kumu nui:
- ʻO ka nele o ke kahe koko i ke aʻalolo optic (Vascular/Ischemia): ʻO kēia ke kumu maʻamau . E like me nā ʻāpana āpau o ko mākou kino, pono pū ke aʻalolo optic i ke koko e hana. Loaʻa iā ia ka oxygen a me nā meaʻai mai ke koko. No laila, inā e hoʻopilikia ʻia kēia kahe koko , e hoʻomaka ana nā hunaola aʻalolo e make.
- Nā kūlana hānau a i ʻole nā kūlana hoʻoilina: Ua hānau ʻia kekahi poʻe me kēia mau kūlana. No ka laʻana, ʻo kahi kūlana i kapa ʻia ʻo Leber hereditary optic neuropathy hiki ke hoʻopilikia i ka ʻike ma kekahi maka ma mua, a laila hoʻopilikia i kekahi maka.
- ʻO ke kaomi ʻana o waho/loko: E noʻonoʻo i kahi puʻupuʻu lolo e kaomi ana i ke aʻalolo optic. Hiki i kēlā ke hōʻino i ke aʻalolo. Pēlā nō, i ke kūlana i kapa ʻia ʻo glaucoma , hiki i ke kaomi i loko o ka maka ke hoʻonui a hōʻino i ke aʻalolo optic.
- ʻO ka mumū i hoʻokumu ʻia e nā maʻi ʻē aʻe a i ʻole ke aʻalolo ponoʻī: ʻO ka optic neuritis kekahi kumu. Hiki ke hana ʻia e nā kūlana e like me ka hydrocephalus , ʻo ia ka hōʻiliʻili ʻana o ka wai i loko o ka lolo.
- Nā maʻi: Hiki i kekahi mau maʻi ke hōʻino i ke aʻalolo optic. No ka laʻana, nā maʻi e like me ka syphilis a me ka measles .
- ʻEha/ʻEha maka: E noʻonoʻo inā ua pā ʻia kou maka e kahi pōpō i kou wā e pāʻani ana i ka cricket, a inā ua ʻeha ʻoe i kahi ulia kaʻa, hiki i kekahi mea e like me kēia ke hōʻino i ke aʻalolo optic a hoʻoulu i kēia ʻano. Hoʻokomo pū kēia i nā ulia ma ka hana, i ka wā hakakā.
- Nā maʻi o ka retina: ʻO nā kūlana e like me ka retinopathy pili i ka maʻi diabetes a me ka retinal vein occlusion hiki ke hoʻopilikia i ke aʻalolo optic.
- Nā mea ʻawahia, nā hemahema meaʻai, a i ʻole nā lāʻau lapaʻau: Hiki ke hana ʻia kēia ʻano ma muli o ka ʻai ʻana i kekahi mau mea ʻawahia, ka nele o nā meaʻai koʻikoʻi e like me nā huaora, a i ʻole he hopena ʻaoʻao o kekahi mau lāʻau lapaʻau. Hoʻopilikia pinepine kēia mau kumu i nā maka ʻelua.
He maʻi lele anei kēia?
ʻAʻole, ʻaʻole hiki ke laha ka Optic Atrophy mai kekahi kanaka a i kekahi kanaka . Eia nō naʻe, e like me kā mākou i kūkākūkā ai ma mua, hiki ke hana ʻia kēia ʻano e kekahi mau maʻi . ʻO ia hoʻi, inā he maʻi lele ka maʻi, hiki ke loaʻa ka optic atrophy ma muli o ia mea. Eia kekahi mau maʻi e hiki ke hana i kēia:
- ʻO ka maʻi syphilis
- Ka maʻi ahulau
- ʻO ka maʻi puʻupuʻu
- Nā ʻūpā
- Maʻi puʻupuʻu
- Maʻi Lyme
- ʻO Aspergillosis (ʻoi aku hoʻi i nā poʻe immunocompromised)
- ʻO Cryptococcosis (ʻoi aku hoʻi i nā poʻe immunocompromised)
He aha ka pōʻino o kēia maʻi? A i ʻole he aha nā pilikia?
E like me kā mākou i ʻōlelo ai ma mua, ʻo ka hōʻino ʻana i ke aʻalolo optic ma muli o ka optic atrophy he mea paʻakikī loa ia e hoʻihoʻi, ʻo ia hoʻi, e ho'ōla . ʻO ia ka pilikia nui loa ma ʻaneʻi. ʻO ka mea nui e hiki ke hana ʻia , ʻo ia ka emi mālie ʻana o ka ʻike, a ma ka hopena, ka nalowale loa o ka ʻike, ʻo ia hoʻi ka makapō.
E hoʻomanaʻo: Inā nalowale kou ʻike ma muli o kēia ʻano, he mea paʻakikī loa ke loaʻa hou. No laila he mea nui e ʻimi i ke kōkua lapaʻau i ka wā e ʻike ʻia ai nā hōʻailona.
Pehea e ʻike pololei ai ke kauka i kēia?
Inā loaʻa iā ʻoe kekahi mau loli a ʻoluʻolu ʻole paha i kou ʻike, pono ʻoe e ʻike i kahi kauka maka . E nīnau mua ke kauka iā ʻoe e pili ana i kāu mau hōʻailona, inā paha ua loaʻa i kekahi o kou ʻohana nā kūlana like, a me kou olakino holoʻokoʻa. Hiki iā ia ke nīnau e pili ana i nā meaʻai, nā lāʻau lapaʻau, a me nā huaora āu e lawe ai. A laila, e nānā pono ʻo ia i kou mau maka.
He aha nā hoʻokolohua e hana ʻia nei no kēia?
I ka wā o ka hoʻokolokolo maka, e nānā kāu kauka i loko o kou maka me ka hoʻohana ʻana i kahi mea hana i kapa ʻia he ophthalmoscope . Ke nānā ʻoe i loko o ka maka o kekahi kanaka me ka optic atrophy, ʻike ʻia paha ka optic disc he keʻokeʻo a ʻeleʻele paha . ʻO kēia no ka mea ua hōʻino ʻia nā hunaola nerve a ua emi ke kahe koko iā lākou.
Hiki i ke kauka ke hana i nā hoʻokolohua ʻē aʻe e ʻike ai i ke kumu o ke kūlana (no ka laʻana, kahi puʻupuʻu lolo a i ʻole kahi maʻi o ka ʻōnaehana nerve, e like me ka "Multiple Sclerosis"). ʻO kekahi o kēia mau mea:
- ʻO ka Optical Coherence Tomography (OCT): Hiki i kēia ke ʻike i ka mānoanoa o nā papa o ke aʻalolo optic a me ka retina.
- Nā hoʻāʻo kahua ʻike: He hoʻāʻo e ana i ka mamao o kou ʻike ʻana a puni ʻoe.
- ʻO ke kiʻi ʻana o ka Magnetic Resonance Imaging (MRI): Hiki ke kiʻi i nā kiʻi maopopo o ka lolo a me ke aʻalolo optic.
- ʻO ka angiography Fluorescein: He hoʻāʻo e nānā i ke kūlana o nā kīʻaha koko i loko o ka maka.
- Nā hoʻokolohua ultrasound.
- Nā hoʻāʻo koko: No ka ʻike ʻana i nā mea e like me nā maʻi a me nā hemahema meaʻai.
He aha nā lāʻau lapaʻau no kēia? Hiki ke ho'ōla loa ʻia?
ʻO ka mea pōʻino, ʻaʻohe lāʻau lapaʻau no ka optic atrophy i kēia manawa . ʻO ia hoʻi, he paʻakikī ke hoʻihoʻi i nā hunaola optic nerve i hōʻino ʻia. ʻO ia ke kumu e ʻōlelo mau ai mākou e mālama i kou mau maka, e hana i nā hoʻokolohua maka maʻamau, a e ʻike i ke kauka inā ʻike ʻoe i kekahi mau loli i kou ʻike.
Eia nō naʻe, hoʻāʻo nā kauka e ʻimi i ke kumu o ke kūlana a mālama iā ia . I ka hana ʻana pēlā, hoʻāʻo lākou e hoʻōki a hōʻemi paha i ka hōʻino hou ʻana i ke aʻalolo optic. Eia kekahi laʻana:
- Inā he puʻupuʻu lolo kēia, hiki ke hana ʻia ke ʻoki ʻana e wehe i ka puʻupuʻu.
- Inā he hōʻiliʻili wai ma ka lolo (hydrocephalus), aia nā ala e wehe ai i kēlā wai.
- I ke ʻano o ka glaucoma, hiki ke hāʻawi ʻia ka lāʻau lapaʻau e hōʻemi i ke kaomi o nā maka.
- Inā he maʻi ka hopena, hiki ke hāʻawi ʻia nā antibiotics.
Hiki iā kākou ke pale aku i kēia mai ka hana ʻana?
I ka hapanui o nā hihia, he mea paʻakikī iā mākou ke pale loa i ka Optic Atrophy. No ka mea, ʻo ka nui o nā kumu e hoʻoulu ai ma waho o kā mākou mana. Eia nō naʻe, i kekahi mau hihia, aia nā mea hiki iā mākou ke hana e hōʻemi i ko mākou pilikia. Eia kekahi laʻana:
- Ke kau nei i nā aniani palekana e pale aku i nā ʻeha maka: E akahele loa i ka hana ʻana i nā mea e like me ka hana metala, ka hana lāʻau, a me ka pāʻani haʻuki.
- ʻO ka loaʻa ʻana o nā lāʻau pale e pono ai i ka manawa kūpono: Kōkua kēia i ka pale ʻana i nā maʻi e like me ka maʻi ʻōpala.
- E hoʻomaʻamaʻa i ka moekolohe palekana: E pale i nā maʻi i laha ma ke moekolohe e like me ka syphilis.
- Inā loaʻa iā ʻoe nā maʻi e like me ka maʻi diabetes a me ke koko kiʻekiʻe, e kaohi pono iā lākou.
Inā loaʻa iaʻu kēia maʻi, he aha ka mea e hiki mai ana i ka wā e hiki mai ana?
ʻO ka wā e hiki mai ana o kekahi me kēia maʻi, ʻo ia hoʻi, pehea kā lākou hihiʻo , e hilinaʻi ʻia ana i ke kumu .
- Inā kumu ʻia kēia e ka mumū o ke aʻalolo optic (optic neuritis), i ka hapa nui o ka manawa, e hoʻi hou ka ʻike i kekahi kekelē ke pau ka mumū.
- Inā ua hōʻino ʻia ke aʻalolo optic no kekahi kumu ʻē aʻe (optic neuropathy), ʻaʻole paha e hoʻomaikaʻi ka ʻike.
- Inā ʻike ʻia a mālama koke ʻia ka glaucoma,, hiki ke kāohi ʻia ka hōʻino hou ʻana o ka ʻike.
- Inā he mea e like me ka puʻupuʻu lolo, inā ʻike ʻia a mālama koke ʻia , hiki ke hoʻemi ʻia ke kaomi ma ke aʻalolo optic a hiki ke pale ʻia nā pōʻino hou aʻe.
Inā maikaʻi ʻole kou ʻike maka, mai hoʻōki i ka manaʻolana . E kamaʻilio me kāu kauka a nīnau e pili ana i nā mea kōkua ʻike maka haʻahaʻa . Aia nā mea e like me nā aniani kūikawā, nā aniani hoʻonui, a me nā polokalamu heluhelu kikokikona.
Āhea wau e ʻike ai i ke kauka e pili ana i kēia?
He mea nui e nānā pinepine ʻia kou mau maka , ʻoiai inā he mau maʻi maka ʻē aʻe kou. Eia kekahi, e ʻike pono i ke kauka inā loaʻa iā ʻoe kekahi o kēia mau mea:
- ʻO kēlā me kēia loli i ka ʻike (e like me ke akahele ʻole, ka nalowale o ka mālamalama)
- Inā pilikia ʻoe i ka ʻike ʻana i nā kala
- Inā manaʻo ʻoe e nalowale ana kou ʻike
ʻO ka mea nui loa: Inā nalowale koke kou ʻike a ʻeha paha kou maka, e ʻimi koke i ke kōkua lapaʻau . He mau hōʻailona paha kēia o nā maʻi maka koʻikoʻi.
He aha nā mea nui loa e pono iaʻu e nīnau aku i ke kauka e pili ana i kēia?
He nui paha kāu mau nīnau e nīnau aku ai i kāu kauka e pili ana i kēia. Inā hiki, e lawe mai i kahi hoaaloha a ʻohana paha me ʻoe. E hana i kahi papa inoa o nā nīnau āu e makemake ai e nīnau a lawe mai i kahi puke liʻiliʻi e kākau i kāu mau pane. Eia kekahi mau nīnau hiki iā ʻoe ke nīnau:
- He aha ke kumu o koʻu atrophy optic?
- He aha kaʻu mau koho no ka mālama ʻana i kēlā kumu?
- He aha nā hopena ʻaoʻao o kēlā mau lāʻau lapaʻau?
- He maʻi hoʻoilina anei kēia?
- He kūpono anei i koʻu ʻohana ke hana i nā hoʻāʻo genetic?
- Aia kekahi mau hoʻokolohua lapaʻau e hiki iaʻu ke komo?
- Hiki iā ʻoe ke hāʻawi i ka ʻike e pili ana i nā hui kākoʻo e kōkua ana i nā poʻe me kēia maʻi?
- He aha nā mea kōkua no ka ʻike haʻahaʻa āu e ʻōlelo mai nei iaʻu e hoʻohana?
Inā ʻoe i pilikia no ka hōʻino ʻia ʻana o ke aʻalolo optic, he mea nui e ʻike pinepine i kāu kauka maka. Hiki i ka hōʻino ʻia ʻana o ke aʻalolo optic ke alakaʻi i ka nalowale ʻana o ka ʻike, a hiki iā ia ke loaʻa ka hopena nui i kou nohona. E hoʻomanaʻo, ʻo kāu mau kauka kou mau hoa hana maikaʻi loa i ke kōkua ʻana iā ʻoe e noho olakino. ʻOiai he maʻi koʻikoʻi kēia, aia nā ala e loaʻa ai ke kōkua āu e pono ai.
No laila, eia kekahi mau mea e hoʻomanaʻo ai mai kā mākou i kamaʻilio ai (Leka Lawe-Home):
- He ʻano koʻikoʻi ka optic atrophy e hōʻino ana i ke aʻalolo optic, ka mea e lawe ana i nā leka ma waena o ka maka a me ka lolo, a hoʻopilikia i ka ʻike.
- Inā ʻike ʻoe i nā hōʻailona e like me ka ʻike maka pōwehiwehi, ka emi ʻana o ka ʻike peripheral, a i ʻole ka paʻakikī o ka ʻike ʻana i nā kala , mai hoʻowahāwahā iā lākou.
- Nui nā kumu no kēia; ʻo ka emi ʻana o ke kahe koko, ke kaomi, ka mumū, ka maʻi, a me nā ulia pōpilikia he mau mea wale nō ia.
- ʻAʻole laha kēia maʻi, akā hiki ke hana ʻia e kekahi mau maʻi lele.
- ʻAʻohe lāʻau lapaʻau piha no kēia i kēia manawa. Kuhi ʻia ka lāʻau lapaʻau i ke kumu nui, e pale aku i ka piʻi ʻana o ka ʻino.
- He mea nui loa ka ʻike mua ʻana i ka maʻi a hoʻomaka i ka lāʻau lapaʻau. No laila, e nānā mau i kou mau maka.
- Aia nā mea hana a me nā lawelawe e hiki ke kōkua i ka poʻe me nā pilikia maka. Mai hoʻopau i ka manaʻolana.
ʻO kou kuleana ka mālama ʻana i kou mau maka, no ka mea, ʻo ia kekahi o nā waiwai waiwai nui loa i loaʻa iā kākou no ka ʻike ʻana i ke ao nei.











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