Ke lohe kākou i ka huaʻōlelo kanesa, makaʻu iki kākou a pau, ʻeā? Akā, aia kekahi mau ʻano kanesa a kākou i lohe ʻole ai, a he mea kakaikahi loa ia. ʻO Yolk Sac Tumor kekahi o lākou. He mea hou paha kēia inoa iā ʻoe. I kēia lā, e kamaʻilio kākou e pili ana i kēia kanesa, hiki ke ulu nui i nā keiki ʻōpio a me nā mākua ʻōpio, ma ke ʻano maʻalahi loa e hiki ai iā ʻoe ke hoʻomaopopo. He mea nui loa ka ʻike i kēia.
He aha maoli ka Yolk Sac Tumor?
I ka ʻōlelo maʻalahi, he ʻano maʻi kanesa ka Yolk Sac Tumor. Ua kapa ʻia hoʻi ʻo ia ʻo Endodermal Sinus Tumor. Kū mai ia mai kahi ʻano cell kūikawā i loko o ko mākou kino. ʻO ia hoʻi, mai nā cell e lilo i sperm i loko o ke kāne, a mai nā cell e lilo i hua manu i loko o ka wahine. I ka lāʻau lapaʻau, kapa mākou i kēia mau cell he germ cells. No laila, no ka māhele kēia o Germ Cell Tumor.
Hoʻomohala pinepine kēia mau puʻupuʻu i loko o nā ovaries i nā wahine a i ʻole nā testicles i nā kāne. Eia naʻe, he mea kakaikahi loa, hiki iā lākou ke ulu ma waho o kēia mau ʻōpū hānau, no ka laʻana ma ka umauma, ka ʻōpū, a i ʻole ka lolo.
He mea kākaʻikahi loa kēia ʻano maʻi kanesa ma ke ʻano holoʻokoʻa. Eia nō naʻe, ʻo ke ʻano maʻi kanesa germ cell i hōʻike pinepine ʻia i nā keiki ʻōpio ʻo ia kēia ʻano i kapa ʻia ʻo Yolk Sac Tumor.
ʻO ka mea koʻikoʻi e pili ana i kēia, ʻo ia ka ulu wikiwiki ʻana o kēia maʻi kanesa a hiki ke laha koke . No laila, inā ʻaʻole mālama ʻia, hiki ke hoʻoweliweli i ke ola. Akā ʻo ka nūhou maikaʻi, inā ʻike mua ʻia ka maʻi, hiki ke ho'ōla loa ʻia me ka lāʻau lapaʻau . No laila, he mea nui loa ka ʻike ʻana i nā hōʻailona i ka wā mua.
He aha nā ʻano nui o kēia maʻi kanesa?
E like me kā mākou i kūkākūkā ai ma mua, hiki ke hoʻokaʻawale ʻia kēia maʻi ʻaʻai i kekahi mau ʻano nui ma muli o kahi e ulu ai.
- Nā puʻupuʻu ʻeke yolk testicular: He ʻano maʻi ʻaʻai testicular kēia. ʻO ka mea maʻamau ia i nā keikikāne ma lalo o 3 mau makahiki a me nā kāne ʻōpio i ko lākou mau makahiki 20 a me 30. I ka hapanui o nā hihia, hiki ke ʻike mua ʻia kēia mau mea, ma mua o ko lākou laha ʻana i nā ʻāpana ʻē aʻe o ke kino. ʻOi aku ka maʻalahi o ka ho'ōla ʻia ʻana.
- ʻO nā puʻupuʻu ʻeke yolk ovarian: He ʻano maʻi ʻaʻai ovarian kēia. He ʻano ʻoi aku ka ikaika ʻole, ʻo ia hoʻi hiki ke laha koke. ʻO ka mea maʻamau ia i nā kaikamahine ʻōpio he 20 makahiki a ʻoi aʻe paha . Ua hōʻike ʻia, hoʻokahi hapakolu o ka poʻe i ʻike ʻia me kēia maʻi he mau kaikamahine ʻōpio i hoʻomaka ʻole i ka menstruation.
- Nā maʻi kanesa e ulu ana ma waho o nā ʻōpū hānau (Extragonadal germ cell tumors):I kekahi manawa, ulu kēia mau maʻi ʻaʻai germ cell ma nā wahi ʻē aʻe o ke kino, ma waho o nā ovaries a i ʻole nā testicles. No ka laʻana, hiki iā lākou ke ulu ma ka lolo, ka waena o ka umauma, ke kua o ka ʻōpū, a i ʻole ka iwi huelo .
He aha nā hōʻailona o kēia?
ʻO nā hōʻailona o kahi Yolk Sac Tumor e pili ana i kahi o ke kino i loaʻa ai ka puʻupuʻu. No ka laʻana, hiki i kahi makuahine ke loaʻa kahi puʻupuʻu liʻiliʻi i loko o ka testicle o kahi pēpē i ka wā e ʻauʻau ana. A i ʻole hiki i kahi kaikamahine ʻōpio ke loaʻa i nā wā maʻamau ʻole me ka ʻeha o ka ʻōpū. He mea nui e makaʻala i kēia mau hōʻailona.
E nānā i ka papa ma lalo no nā hōʻailona maʻamau ma muli o ka wahi o ke kanesa.
| Kahi o ke kanesa | Nā hōʻailona e ʻike ʻia |
|---|---|
| Nā ʻōpū | He paʻakikī ʻeha ʻole a i ʻole he puʻu i loko o ka testicle. |
| I loko o nā ovaries | ʻO ka pehu ʻana o ka ʻōpū a i ʻole ka manaʻo o kahi puʻupuʻu i loko o ka ʻōpū, ʻeha o ka ʻōpū a i ʻole ke kua, nā loli i nā ʻano hana ʻōpū (e like me ka paʻa ʻana o ka ʻōpū), ke kahe koko ʻana o ka menstrual i kūpono ʻole a kaumaha paha. |
| lolo | ʻEha poʻo a pilikia paha ka ʻike. |
| Umauma | ʻŪhū a me ka pilikia o ka hanu ʻana. |
| ʻO ka hopena haʻahaʻa o ka iwi kuamoʻo (Tailbone) | Hiki ke pehu ka ʻāpana, ʻike ʻia he palapū, a i ʻole e like me kahi puʻu i loaʻa i ka maʻi. |
No ke aha e ulu ai kēia ʻano maʻi kanesa?
He pilikia kēia i loaʻa i nā kānaka he nui. Akā, ʻo ka ʻoiaʻiʻo, ʻaʻole i loaʻa i nā kānaka noiʻi lapaʻau ke kumu pololei o ka Yolk Sac Tumor. E like me nā maʻi kanesa ʻē aʻe, ua hana ʻia kēia e nā loli (mutation) i loko o nā genes, a i ʻole DNA, i loko o nā cell. ʻO kēia mau loli ke kumu o ka māhele wikiwiki ʻana o nā cell a me ke kāohi ʻole ʻia. I ka hala ʻana o ka manawa, hiki i kēia mau cell ke ulu pū e hana i kahi puʻupuʻu. Inā ʻaʻole mālama ʻia, hiki i kēia mau cell cancer ke laha i nā ʻāpana ʻē aʻe o ke kino.
Eia nō naʻe, ke hoʻomau nei ka noiʻi ʻana i ke kumu e hoʻomaka ai kēia mau hoʻololi genetic ma kahi mua.
Pehea e ʻike ai i kēia maʻi?
Inā loaʻa iā ʻoe a i ʻole kāu keiki kekahi o nā hōʻailona i helu ʻia ma luna, pono ʻoe e ʻike koke i ke kauka . E hana mua ke kauka i kahi hoʻokolokolo kino a nānā i nā puʻupuʻu a i ʻole nā pehu ʻē aʻe i loko o ka ʻōpū a i ʻole nā testicles. A laila, e nīnau lākou iā ʻoe e pili ana i kāu mau hōʻailona.
Hiki ke hana ʻia kekahi mau hoʻokolohua e hōʻoia i ka maʻi:
- Nā hoʻāʻo koko: Lawe ʻia kahi hāpana o kou koko a nānā ʻia kahi protein kūikawā. Ua kapa ʻia ʻo Alpha-fetoprotein (AFP) . He kiʻekiʻe loa kēia pae AFP i loko o ke koko i nā mea āpau me ka Yolk Sac Tumor. He hōʻailona koʻikoʻi loa kēia no ka ʻike ʻana i kēia maʻi kanesa.
- Nā hoʻāʻo kiʻi: ʻO nā scan CT (Computed Tomography scans) a me nā scan MRI (Magnetic Resonance Imaging) nā hoʻāʻo i hoʻohana pinepine ʻia. Hiki i kēia ke ʻike maopopo i nā ʻōpū i loko o ke kino.
- ʻO ke ʻoki ʻana i ke ʻoki kino: ʻO kēia wale nō ke ala e maopopo ai he 100% e pili ana i ka maʻi. E hana ke kauka i ke ʻoki kino e wehe i ka puʻupuʻu holoʻokoʻa (i kekahi manawa ʻo ke kino holoʻokoʻa kahi i loaʻa ai ka puʻupuʻu). A laila e hoʻouna ʻia ka puʻupuʻu i kahi keʻena hoʻokolohua e hoʻāʻo ʻia no nā hunaola kanesa.
Pehea e hoʻoholo ʻia ai nā pae o ka maʻi kanesa?
Ke ʻike ʻia ka maʻi, hoʻoholo nā kauka i ka mamao o ka laha ʻana o ke kanesa, a i ʻole ke kahua o ke kanesa. Hoʻoholo ʻia kēia kahua e nā mea e like me ka nui o ka puʻupuʻu a me ka mamao o ka laha ʻana o ke kanesa. Inā haʻahaʻa ke kahua (e.g. Stage 1), ʻo ia hoʻi ke kanesa i kona mau kahua mua. Inā kiʻekiʻe ke kahua (e.g. Stage 3, 4), ʻo ia hoʻi ua laha iki ke kanesa. He mea nui ka ʻike ʻana i kēia kahua no ke koho ʻana i ka lāʻau lapaʻau maikaʻi loa.
No nā ʻōpū Testicular
- Pae 1: Aia ke kanesa ma ka testicle wale nō.
- Pae 2: Ua pālahalaha ke kanesa mai ka testicle a i nā lymph nodes.
- Pae 3: Ua pālahalaha nā hunaola kanesa i nā ʻōpū ʻē aʻe.
No nā ʻōpū ovarian
- Pae 1: Ua kaupalena ʻia ke kanesa i hoʻokahi a i ʻole nā ovaries ʻelua.
- Pae 2: Ua pālahalaha nā hunaola kanesa i nā wahi ʻē aʻe o ka pelvis, akā ʻaʻole i hiki i nā ʻōpū fallopian.
- Pae 3: Ua pālahalaha ke kanesa i nā lymph nodes a me ka membrane e uhi ana i loko o ka ʻōpū (peritoneum).
- Pae 4: Ua pālahalaha ke kanesa ma waho o ka uhi o ka ʻōpū i nā ʻiʻo a me nā ʻōpū ʻē aʻe.
He aha nā lāʻau lapaʻau no kēia?
ʻO ka pahuhopu nui o ka mālama ʻana, ʻo ia ka wehe loa ʻana i ka puʻupuʻu kanesa. Hoʻohana ʻia ʻelua mau ʻano mālama nui no kēia.
1. ʻO ke ʻoki kino: Pili kēia i ka wehe ʻana i ka testicle holoʻokoʻa (i kapa ʻia he orchiectomy ) a i ʻole ka ovary (i kapa ʻia he oophorectomy ) i hoʻopilikia ʻia e ke kanesa. Inā ua pālahalaha ke kanesa i nā vesicles seminal, pono paha e wehe ʻia.
2. Chemotherapy: Ma hope o ke ʻoki ʻana, hāʻawi ʻia kēia lāʻau lapaʻau e pepehi i nā hunaola kanesa e waiho ʻia ana i loko o ke kino i ʻike ʻole ʻia e ka maka ʻōlohelohe. I kekahi manawa, inā nui loa ka puʻupuʻu, hiki ke hāʻawi ʻia ka chemotherapy e hoʻēmi i ka puʻupuʻu ma mua o ke ʻoki ʻana.
Ke ʻano hana lapaʻau BEP
ʻO ka lāʻau lapaʻau chemotherapy nui no ka Yolk Sac Tumor i kapa ʻia ʻo BEP . Ma muli o ke kahua o ke kanesa a me ke ʻano o ka pane ʻana o kou kino i ka lāʻau lapaʻau, pono paha ʻoe e lawe i kekahi mau pōʻai o BEP. ʻO BEP ka hui pū ʻana o ʻekolu mau lāʻau lapaʻau:
- B leomycin
- ʻO ka toposide E
- ʻO Cisplatin ( P latinol®)
Ke hui pū ʻia kēia mau lāʻau ʻekolu, hana maikaʻi loa lākou e hoʻopau i nā hunaola Yolk Sac Tumor.
Pehea ke kūlana ma hope o ka mālama ʻana? (Prognosis)
He mea kēia e pono ai ka poʻe he nui e ʻike. He ʻoiaʻiʻo inā ʻaʻole mālama ʻia, he mea hoʻoweliweli ke Yolk Sac Tumor i ke ola. ʻO ia ke kumu i ʻōlelo ai mākou mai kinohi mai he mea nui loa ka ʻike ʻana i ka maʻi a hoʻomaka i ka mālama ʻana i ka wā mua . E like me nā maʻi kanesa āpau, ʻo ka wikiwiki o ka hoʻomaka ʻana o ka mālama ʻana, ʻoi aku ka kiʻekiʻe o ka manawa e hoʻōla ai.
Aia kou wānana ma luna o kekahi mau kumu. Pono ʻoe e kūkākūkā me kāu kauka i nā mea e like me ke kahua o ke kanesa, pehea e pane ai kou kino i ka lāʻau lapaʻau, a me kāu pae AFP ma mua o ka hoʻomaka ʻana i ka chemotherapy (ʻo ka haʻahaʻa o kēia, ʻoi aku ka maikaʻi o ka hopena).
Akā, mai hopohopo. Ua hoʻomaikaʻi nui nā lāʻau lapaʻau e like me ke ʻoki kino a me ka BEP i ka nui o ke ola no ka poʻe me ka Yolk Sac Tumor. No ka laʻana, hiki ke ho'ōla loa ʻia ke kanesa testicular Stage 1 me kēia mau lāʻau lapaʻau. Ua hōʻike ʻia kahi noiʻi hou nei he 91.5% o ka poʻe i mālama ʻia no ka maʻi ʻaʻai ovarian mua e ola ana ma hope o ʻelima mau makahiki.
Leka Lawe-Home
- He ʻano maʻi kanesa kakaikahi ka Yolk Sac Tumor i ʻike nui ʻia i nā keiki a me nā ʻōpio.
- E makaʻala i nā hōʻailona e like me kahi puʻupuʻu ʻeha ʻole i loko o ka testicle a i ʻole ka pehu/ʻoluʻolu ʻole i loko o ka ʻōpū. Inā ʻike ʻoe i kekahi mea e like me kēia, mai hilahila a makaʻu paha, akā e ʻike koke i ke kauka.
- ʻOiai e laha koke ana kēia maʻi ʻaʻai, hiki ke ho'ōla loa ʻia inā ʻike mua ʻia.
- He kūpono loa nā lāʻau lapaʻau ʻoki kino a me ka chemotherapy (ʻoi aku hoʻi ka BEP).
- ʻOiai ma hope o ka pau ʻana o ka lāʻau lapaʻau, he mea nui e hana i nā hoʻokolohua hahai i ka manawa i hoʻonohonoho ʻia e like me ke kauoha a ke kauka.











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