Skip to main content

E aʻo kākou e pili ana i ka Anaplastic Large Cell Lymphoma (ALCL) ma nā ʻōlelo maʻalahi.

E aʻo kākou e pili ana i ka Anaplastic Large Cell Lymphoma (ALCL) ma nā ʻōlelo maʻalahi.

Ua lohe paha ʻoe i ka Anaplastic Large Cell Lymphoma (ALCL)? Malia paha he ʻano paʻakikī iki kēia inoa. Akā, mai hopohopo, he ʻano maʻi kanesa laha ʻole kēia. I kēia lā, e kamaʻilio mākou e pili ana i ke ʻano o ka ALCL, pehea e ulu ai, he aha nā hōʻailona, ​​he aha nā lāʻau lapaʻau, a me nā mea ʻē aʻe he nui ma ke ʻano maʻalahi loa e hiki ai iā ʻoe ke hoʻomaopopo. E like me ke kamaʻilio ʻana me kahi hoaaloha.

He aha ka ALCL (Anaplastic Large Cell Lymphoma)?

I ka ʻōlelo maʻalahi, he ʻano maʻi kanesa kakaʻikahi a ʻano ʻē ʻole ʻo ALCL no kahi hui nui o nā maʻi kanesa i kapa ʻia ʻo Non-Hodgkin Lymphoma . Ua ʻike anei ʻoe e like me nā Non-Hodgkin Lymphoma āpau, he ʻano maʻi kanesa nō hoʻi ʻo ALCL? Hana ia i ka wā e ulu ai kahi ʻano koko keʻokeʻo i kapa ʻia ʻo lymphocytes i loko o ko mākou kino ma waho o ke kaohi a ma ka wikiwiki ma mua o ka mea e pono ai.

E noʻonoʻo i kēia mau lymphocytes e like me nā koa liʻiliʻi i loko o ko mākou kino. He ʻāpana lākou o kā mākou ʻōnaehana pale, e pale ana iā mākou mai nā germs a me nā maʻi. ʻElua ʻano nui o nā lymphocytes: nā cell B a me nā cell T. I loko o ALCL, ulu kūpono ʻole kāu mau lymphocytes T, a i ʻole nā ​​​​cell T.

I kēia manawa, e nānā kākou i ke ʻano o kēia inoa "anaplastic large cell lymphoma".

  • Anaplastic : ʻO ke ʻano o kēia huaʻōlelo, i ka nānā ʻana ma lalo o kahi microscope, ʻano ʻē loa kēia mau hunaola kanesa a ʻokoʻa hoʻi i ka hoʻohālikelike ʻia me nā hunaola T lymphocyte olakino. Me he mea lā ua hoʻopilikia ʻia ko lākou ʻano a me ke ʻano.
  • Kelepona Nui : ʻO ke ʻano kēia, ʻoi aku ka nui o nā lymphocytes T hana maʻamau ma mua o nā kelepona T maʻamau. ʻIke maopopo ʻia kēia ʻokoʻa ma lalo o kahi microscope.
  • Lymphoma : ʻO ka Lymphoma kahi maʻi ʻaʻai e kū mai ana ma muli o ka ulu ʻole ʻana o nā hunaola koko keʻokeʻo i kapa ʻia ʻo lymphocytes. Hoʻomohala kūikawā ʻia ʻo ALCL mai nā lymphocytes T.

Ua maopopo iaʻu? I ka ʻōlelo maʻalahi, he maʻi ʻaʻai ʻo ALCL kahi e lilo ai nā pūnaewele T i mea nui loa, loli, a ulu me ke kāohi ʻole.

Aia kekahi mau ʻano like ʻole o ALCL?

ʻAe, aia nā ʻano ALCL like ʻole. Ua hoʻokaʻawale ʻia kēia mau mea ma muli o kahi o ke kanesa i loko o kou kino a me nā ʻano o nā hunaola kanesa.

ALCL ʻōnaehana

ʻO kēia ke ʻano nui. ʻO ke ʻano "Systemic" hiki ke hoʻopilikia i ke kino holoʻokoʻa. Hiki iā ia ke hoʻopilikia i kāu mau lymph nodes , a i ʻole "glands" e like me kā mākou e kapa nei iā lākou, a me nā ʻōpū kūloko e like me kou ake a me nā māmā, a i kekahi manawa kou ʻili.

Ua māhele ʻia ka ALCL ʻōnaehana i ʻelua ʻano. Hoʻokumu ʻia kekahi ma muli o ka loaʻa ʻana o kahi mutation i loko o kahi gene i kapa ʻia ʻo ka gene "Anaplastic Lymphoma Kinase (ALK)" . Ua like nā genes me nā puke kuhikuhi liʻiliʻi no kā mākou mau cell, a haʻi kēia mau genes i kahi T lymphocyte pehea e hana ai.

  • ALK-positive ALCL: He ʻano maʻi kanesa kēia nona ka mutation i loko o ka gene ALK. He maʻi kanesa ikaika pinepine kēia. Eia nō naʻe, ʻoi aku ka maʻamau i nā keiki a me nā ʻōpio . ʻO ka mea pōmaikaʻi, pane maikaʻi kēia ʻano i ka chemotherapy .
  • ʻALK-maikaʻi ʻole ALCL : ʻAʻohe o kēia ʻano i ka hoʻololi ʻana o ka gene ALK. He maʻi kanesa ulu wikiwiki (hoʻouka kaua) nō hoʻi kēia. Eia nō naʻe, pili nui ia i ka poʻe ʻelemakule , ʻo ka poʻe ma luna o 60 mau makahiki. Hiki i kēia ʻano ke hoʻomaha ma hope o ka chemotherapy a laila hoʻi hou. No laila, ʻoi aku ka paʻakikī o ka mālama ʻana iā ALK-maikaʻi ʻole ALCL, a ʻoi aku ka maikaʻi ʻole o ka wānana ma mua o ALK-positive ALCL.

Nā ʻano ʻē aʻe o ALCL

Aia kekahi mau ʻano ALCL e ulu lohi ana ma mua o nā ʻano ʻōnaehana.

  • ʻO ka ALCL ʻili mua : He ʻano kēia e hoʻopilikia nui i ka ʻili. Hiki ke loaʻa nā hōʻailona e like me nā pehu, nā puʻupuʻu, a me ka eczema. I ka hapa nui o nā hihia (ma kahi o 90%) ʻaʻole ia e pālahalaha ma waho o ka ʻili.
  • ʻO ka ALCL e pili ana i ka implant umauma (BIA-ALCL) : He ʻano ALCL kēia e ulu a puni nā implant umauma. Hoʻomaopopo pinepine ʻia ma kahi o 10 mau makahiki ma hope o ke kaʻina hana hoʻonui umauma a i ʻole ke kaʻina hana kūkulu hou ʻana i ka umauma.

ʻO wai ka mea e loaʻa ana iā ALCL?

ʻOiai hiki ke ulu aʻe ʻo ALCL i nā kānaka o kēlā me kēia makahiki, ʻoi aku ka hoʻopilikia o kekahi mau ʻano i kekahi mau hui.

  • ʻO ALK-positive ALCL : Hoʻopilikia pinepine kēia i nā keiki ma hope o ke kula kamaliʻi, nā ʻōpio, a me nā mākua ʻōpio i ko lākou mau makahiki 20 a me 30. ʻOi aku ka maʻamau i nā kāne .
  • ALK-maikaʻi ʻole ALCL : Hoʻopilikia nui kēia i ka poʻe ma luna o 60 mau makahiki. ʻOi aku ka maʻamau o ia i nā kāne.
  • ʻO ka ALCL ʻili mua : ʻIke pinepine ʻia kēia i nā pākeke ma luna o 40 mau makahiki. ʻOi aku ka maʻamau i nā kāne a me ka poʻe keʻokeʻo.
  • BIA-ALCL : ʻIke pinepine ʻia kēia i nā poʻe i ko lākou mau makahiki 50. Hiki iā ia ke ulu i loko o ka poʻe i loaʻa nā implants umauma silicone a me saline. Ua ʻike ʻia he pili pono ia me nā implants umauma textured .

Pehea ka maʻamau o ALCL?

He maʻi kanesa laha ʻole ʻo ALCL. Ma kahi o 2% wale nō o nā lymphomas non-Hodgkin i nā pākeke i ʻike ʻia he ALCL. He pakeneka liʻiliʻi loa kēlā.

He aha nā hōʻailona o ALCL?

ʻOkoʻa nā hōʻailona o ALCL ma muli o ke ʻano.

Nā hōʻailona o ka ALCL ʻōnaehana

I loko o nā ALCL ALK-positive a me ALK-negative, he mea maʻamau nā lymph nodes pehu ma kahi e ulu ana ke kanesa. Hiki iā lākou ke manaʻo e like me nā puʻupuʻu ma nā wahi e like me kou ʻāʻī, nā armpits, a i ʻole ka groin . ʻO nā hōʻailona ʻē aʻe:

  • Ka wela pinepine.
  • Manaʻo luhi loa (`Fatigue`).
  • Ka hou ʻana i ka pō ('Night sweats').
  • Ka pohō kaumaha i wehewehe ʻole ʻia.

Ke ʻike ʻia ka hapa nui o nā kānaka, ua pālahalaha iki paha ke kanesa, ʻo ia hoʻi, aia ia i kahi 'paepae holomua' . I kēlā hihia, ua pālahalaha paha ke kanesa i nā ʻōpū e like me kou māmā, ke akepaʻa, a i ʻole nā ​​iwi. A laila, hiki ke ʻike ʻia nā hōʻailona ma muli o ke ʻano i hoʻopilikia ʻia. No ka laʻana, inā he ʻūlū kou umauma a i ʻole ka ʻū pinepine, ua hoʻopilikia paha ka ALCL i ka umauma.

Nā ʻano o ka ALCL ʻili mua

Hiki ke ʻike ʻia nā loli o ka ʻili ma kēia ʻano.

  • ʻIke ʻia nā puʻupuʻu ʻulaʻula a ʻulaʻula paha ma kekahi a ʻoi aku paha mau wahi o ka ʻili, a hiki ke ulu nui aʻe i ka hala ʻana o ka manawa.
  • Nā puʻupuʻu i hāpai ʻia , ʻoi aku ka nui ma mua o ke kālā. Hiki i kēia ke maneʻo i kekahi manawa.
  • Hiki i nā puʻupuʻu ke lilo i ʻeha a laila lilo i ʻōpala .

Nā ʻano o BIA-ALCL (Breast Implant-Associated ALCL)

Ma kēia, hiki ke ʻike ʻia nā loli maopopo i nā umauma.

  • ʻEha umauma.
  • Pehu ʻana o ka umauma.
  • ʻO ka ʻili a i ʻole ka eczema.
  • Ka pehu ʻana a i ʻole ka hōʻiliʻili ʻana o ka wai kokoke i kou implant umauma.
  • He puʻu paʻa kokoke i ke kāpili umauma.

ʻIke pinepine ʻia kēia mau loli ma ka umauma hoʻokahi, akā i kekahi manawa hiki ke ʻike ʻia nā loli ma nā umauma ʻelua.

He aha ke kumu o ALCL?

Hana ʻia ka ALCL i ka wā e hoʻonui nui ʻole ʻia ai nā pūnaewele lymphocyte a mākou i kamaʻilio ai ma mua a hoʻomaka e ulu ma mua o nā ʻiʻo olakino a puni lākou. ʻAʻole maopopo i nā kānaka noiʻi ke kumu e lilo ai kēia mau pūnaewele lymphocyte i maʻi kanesa (nā pūnaewele malignant).

Eia nō naʻe, ua ʻike lākou i kekahi mau hoʻololi genetic i ʻike pinepine ʻia me ALCL. Ua manaʻo ʻia e hiki i kēia mau hoʻololi genetic ke hoʻololi i nā cell olakino i nā cell cancer.

Eia kekahi laʻana, ʻo ke ʻano nui o ka ALK-positive ALCL ʻo ia nā mutations i loko o ka gene ALK . Pēlā nō, he mea maʻamau nā mutations gene ʻē aʻe i nā ʻano ALCL ʻē aʻe.

Pehea e ʻike ʻia ai ʻo ALCL? (Diagnosis)

E hana mua kāu kauka i kahi hoʻokolohua kino e nānā i nā hōʻailona o ALCL, e like me nā lymph node pehu. Inā kānalua lākou i kēia, e hana lākou i kekahi mau hoʻokolohua a me nā kaʻina hana like ʻole.

  • Nā kaʻina hana kiʻiHiki i kēia mau mea ke kōkua i ka ʻike ʻana i kahi o ke kanesa. ʻOkoʻa ke ʻano o nā hoʻāʻo kiʻi āu e pono ai ma muli o ke ʻano o ALCL. Hiki i kāu kauka ke hana i kahi X-ray umauma , CT scan , a i ʻole MRI e nānā i nā puʻupuʻu. Hiki i kahi PET/CT scan a i ʻole PET scan ke kōkua i ka hoʻoholo ʻana inā ua pālahalaha ke kanesa ma ke kino holoʻokoʻa. Inā kānalua ʻia ʻo BIA-ALCL, hiki ke hana ʻia kahi ultrasound umauma .
  • Hana Koko : E hana ke kauka i nā hoʻokolohua koko like ʻole, e like me ka helu koko piha (CBC), e nānā i nā hōʻailona o ALCL. Inā ʻaʻole like ka nui o nā hunaola koko (nā hunaola koko ʻulaʻula, nā hunaola koko keʻokeʻo, a i ʻole nā ​​platelets), he hōʻailona paha ia o ALCL. E nānā pū lākou i kekahi mau enzymes a me nā māka ʻē aʻe i loko o ke koko, no ka mea, hiki i kēia mau mea ke lilo i mau hōʻailona o ALCL.
  • Biopsy : ʻO ke ala wale nō e hōʻoia ai i ka ʻike ʻana o ALCL ʻo ia ka loaʻa ʻana o kahi biopsy. I loko o kahi biopsy, lawe ke kauka i kahi laʻana liʻiliʻi o nā ʻiʻo kānalua a nānā iā ia ma lalo o kahi microscope. Ma ke aʻo ʻana i kēia mau cell, hiki i ke kauka ke hoʻoholo pololei i ke ʻano o ALCL āu. Kōkua pū kēia i ka hoʻolālā ʻana i ka lāʻau lapaʻau kūpono loa.

Pehea e mālama ʻia ai ʻo ALCL?

ʻO ka chemotherapy ka lāʻau maʻamau no ka ALCL systemic. ʻO ke ʻoki kino ka lāʻau lapaʻau makemake nui ʻia no ka ALCL ʻili mua a me ka BIA-ALCL.

Ka mālama ʻana i ka ALCL systemic

ʻO ka maʻamau, pane maikaʻi nā lymphomas cell nui anaplastic ALK-positive a me ALK-negative i ka chemotherapy systemic. ʻO ka chemotherapy systemic e pili ana i ka hāʻawi ʻana i nā lāʻau pepehi kanesa ma o kahi aa koko, e hele ana i loko o ke kino ma o ke kahe koko e pepehi i nā hunaola kanesa.

Hoʻohana pinepine ka Chemotherapy no ka ALCL systemic i ka hui pū ʻana o nā lāʻau lapaʻau e hana pū ana e pepehi i nā hunaola kanesa. ʻO kekahi mau laʻana:

  • BV-CHP : Hoʻokomo pū kēia me nā lāʻau lapaʻau ʻo `Brentuximab Vedotin`, `Cyclophosphamide`, `Doxorubicin (Hydroxydaunorubicin)`, a me `Prednisone`.
  • CHOP : Pili kēia i ka hoʻohana ʻana i nā lāʻau i kapa ʻia ʻo 'Cyclophosphamide', 'Doxorubicin (Hydroxydaunorubicin)', 'Vincristine (Oncovin®)', a me 'Prednisone'.
  • CHEOP : Pili kēia i ka hoʻohana ʻana i nā lāʻau lapaʻau i kapa ʻia ʻo 'Cyclophosphamide', 'Doxorubicin (Hydroxydaunorubicin)', 'Etoposide', 'Vincristine (Oncovin®)', a me 'Prednisone'.

Hiki i kēia mau lāʻau lapaʻau ke hoʻopau i nā hōʻailona āpau o ke kanesa i loko o kahi manawa pōkole (kapa mākou i kēia 'remission').(Ua kapa ʻia ʻo ia he "relapse") Eia naʻe, hiki i ke kanesa ke hoʻi hou mai. Inā manaʻo kāu kauka e hoʻi mai ana ke kanesa, hiki iā lākou ke paipai i kahi hoʻoili cell stem i kou wā e hoʻomaha ai. Hoʻololi kahi hoʻoili cell stem i nā cell i luku ʻia e ka chemotherapy me nā cell olakino. A laila hana kēia mau cell olakino i nā cell koko olakino (ʻaʻole cancerous).

Inā hoʻi mai ke kanesa, hiki i kāu kauka ke ʻōlelo i nā ʻano lāʻau chemotherapy ʻē aʻe i hoʻolālā ʻia e mālama i ka lymphoma.

Ka mālama ʻana i ka ALCL ʻili mua

ʻO ke ʻoki kino ka lāʻau lapaʻau maʻamau no kēia. Inā ua pālahalaha ke kanesa i nā lymph nodes, pono paha ʻoe i ka radiation therapy . Hana ka radiation therapy ma ke kuhikuhi ʻana i ka ikehu i nā cell cancer a luku iā lākou.

Hiki i ka ALCL ʻili mua ke hoʻi hou i loko o ʻelima mau makahiki o ka mālama ʻana. Inā hana ʻia kēia, pono hou ke ʻoki kino a me ka radiation therapy.

Inā he mau puʻupuʻu kūloko kou i hiki ʻole ke wehe ʻia me ke ʻoki ʻana, a inā hoʻi hou mai ke kanesa, pono paha ʻoe i nā lāʻau lapaʻau ʻē aʻe. Hiki i kēia mau mea ke komo pū me:

  • ʻO Methotrexate Waha : He lāʻau lapaʻau i hoʻohana ʻia e mālama i ka lymphoma non-Hodgkin.
  • ʻO Bexarotene : He lāʻau lapaʻau i hoʻohana ʻia e mālama i ka lymphoma T-cell e hoʻopilikia ana i ka ʻili.
  • ʻO Brentuximab Vedotin : He lāʻau lapaʻau i hoʻohana ʻia e mālama i ka ALCL systemic a me nā ʻano ʻē aʻe o ka ALCL hou.
  • Interferon : He lāʻau lapaʻau e kōkua ai i kāu ʻōnaehana pale e ʻike a hakakā i nā hunaola kanesa, me ka lymphoma.

Ka mālama ʻana i ka BIA-ALCL

Hiki ke ho'ōla ʻia ʻo BIA-ALCL me ke ʻoki ʻana e wehe i kāu implant umauma a me nā hunaola kanesa a puni ia. Inā ʻaʻole hiki ke ʻoki ʻia, hiki ke hāʻawi ʻia ka radiation therapy e pepehi i nā hunaola kanesa.

Inā hoʻi mai ke kanesa a pālahalaha paha ma ʻō aku o ka umauma, hiki i kāu kauka ke ʻōlelo aku i nā lāʻau lapaʻau chemotherapy e hoʻohana ʻia e mālama ai iā ALK-negative ALCL. Hiki i kēia ke komo pū me ka chemotherapy CHOP a me nā lāʻau lapaʻau e like me Brentuximab Vedotin.

Pehea ke koʻikoʻi o ALCL?

Me ka nānā ʻole i ke ʻano, he maʻi ʻaʻai koʻikoʻi ʻo ALCL e pono ai ka nānā pono ʻana a me ka mālama kūpono. Eia nō naʻe, pili kāu wānana a me ka hoʻolālā mālama i nā mea e like me ke ʻano o ALCL āu, pehea ʻoe e pane ai i ka mālama ʻana, a me kāu helu International Prognostic Index (IPI) .

Ua hoʻomohala ʻia ka IPI e nā kauka oncology e kōkua i ka wānana ʻana i ka hopena o nā lymphomas non-Hodgkin e ulu wikiwiki ana, me ka ALCL systemic. Hoʻokumu ʻia ka helu ma luna o nā kumu aʻe:

  • kou mau makahiki.
  • ʻO kou hiki ke hana i nā hana o kēlā me kēia lā.
  • Pehea ka mamao o ka laha ʻana o kou maʻi kanesa (kahua o ke kanesa).
  • ʻO ka nui o nā kelepa sebaceous i hoʻopilikia ʻia.

Inā loaʻa iā ʻoe ka ALCL systemic, e nīnau i kāu kauka pehea e pili ai kāu helu IPI i kou kūlana o ka ho'ōla ʻana.

He aha ka nui o ke ola no ALCL?

ʻOkoʻa loa nā helu ola no ka ALCL ʻōnaehana. Pili ka ALK-positive ALCL me ka manawa ola lōʻihi ma mua o ka ALK-negative ALCL. Ma muli o nā mea e like me kou ʻano maʻi kanesa a me ka helu IPI, hiki ke piʻi ka helu ola ʻelima makahiki no ka ALK-positive ALCL mai 33% a 90%. Pēlā nō, hiki ke piʻi ka helu ola ʻelima makahiki no ka ALK-negative ALCL mai 13% a 74%.

He maikaʻi loa nā helu ola o ka ALCL ʻili mua a me ka BIA-ALCL. ʻOiai ʻo ka ALCL ʻili mua e hoʻomaha pinepine a hoʻi mai i loko o ʻelima mau makahiki, hiki i nā lāʻau lapaʻau hahai ke hoʻolōʻihi i kou ola. ʻO ka helu ola ma kahi o 80% ʻelima mau makahiki ma hope o ka hōʻoia ʻana. Ma BIA-ALCL, inā e wehe loa ʻia ke kanesa me ke ʻoki ʻana, ua nalowale loa ke kanesa.

He aha nā nīnau e pono iaʻu e nīnau aku i kaʻu kauka?

Eia kekahi mau nīnau koʻikoʻi e nīnau aku i kāu kauka:

  • He aha ke ʻano o ka ALCL iaʻu?
  • Ua kaupalena ʻia koʻu maʻi ʻaʻai i hoʻokahi wahi, a ua laha paha?
  • ʻO wai nā loea ma kaʻu hui mālama?
  • He aha ka lāʻau lapaʻau āu e paipai mai ai iaʻu?
  • Pehea e mālama ai i nā hopena ʻaoʻao o ka lāʻau lapaʻau?
  • He aha kaʻu helu IPI?
  • He aha nā manawa kūpono e komo ai koʻu maʻi kanesa i ke "kala ʻana"?
  • He aha nā manawa kūpono e hoʻi hou mai ai koʻu maʻi kanesa?
  • ʻEhia pinepine e pono ai iaʻu e hele mai no nā kipa hoʻi e nānā i koʻu kūlana?

He mea maʻamau ka makaʻu ke ʻike ʻoe he maʻi kanesa kou. Eia naʻe, ʻo ka mea nui e hoʻomanaʻo ai, ʻaʻole ʻo ALCL he ʻano maʻi kanesa hoʻokahi me ka hopena like . ʻO ke ʻano o ALCL āu e hoʻoholo ai inā laha koke a lohi paha. ʻO ia ka mea e hoʻopili ai i kāu mau koho lapaʻau a me kou manaʻo. Hoʻolaha koke ka ALCL o kekahi poʻe. No kekahi poʻe, ulu lohi ia, e hāʻawi ana iā ʻoe i ka manawa kūpono e loaʻa ai nā lāʻau lapaʻau e hiki ke kōkua i ka kaohi ʻana i ke kanesa. E kamaʻilio me kāu kauka e pili ana i nā hopena hiki ke loaʻa ma muli o kāu hōʻailona.

Nā mea nui e pono ai ʻoe e hoʻomanaʻo (Leka Lawe-Home)

ʻAe, e hōʻuluʻulu kākou i kekahi o nā mea nui e pono ai ʻoe e hoʻomanaʻo mai nā mea a mākou i kamaʻilio ai.

  • He ʻano maʻi kanesa laha ʻole ka ALCL, a he nui nā ʻano like ʻole.
  • ʻAʻole like nā ʻano ALCL āpau. Hoʻolaha koke kekahi, lohi kekahi.
  • ʻOkoʻa ka mālama ʻana a me nā kūlana o ka hoʻōla ʻana ma muli o ke ʻano o ka ALCL āu, kou makahiki, a me kou olakino holoʻokoʻa.
  • ʻOiai ʻoi aku ka pinepine o ka ALK-positive ALCL i ka poʻe ʻōpio, pane maikaʻi ia i ka lāʻau lapaʻau.
  • Hoʻopilikia ka ALK-negative ALCL i nā pākeke he nui a hiki ke paʻakikī iki ka mālama ʻana.
  • ʻO ka wānana no ka skincare ALCL a me ka breast implant-associated ALCL (BIA-ALCL) ma ke ʻano laulā he maikaʻi.
  • Mai hopohopo. Inā he kānalua a he mau hōʻailona paha kāu, e ʻimi koke i ke kōkua lapaʻau.
  • E kamaʻilio ākea me kāu kauka e pili ana i kou kūlana, kāu lāʻau lapaʻau, a me nā nīnau āu e loaʻa ai. ʻO lākou ka poʻe hiki ke kōkua maikaʻi loa iā ʻoe.

E hoʻomanaʻo, ʻaʻole like ke koʻikoʻi o nā maʻi kanesa āpau. ʻOiai me ALCL, me ka ʻike pololei, ka mālama koke ʻana, a me ka nānā pono ʻana, hiki i nā poʻe he nui ke hoʻokō i nā hopena holomua.


ʻO Lymphoma Kelepona Nui Anaplastic, ALCL, Lymphoma, Kanesa, Nā Kelepona T, ALK Gene, Chemotherapy

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

💬 Comments (0)

ʻAʻohe manaʻo i kau ʻia. Hoʻohui i kāu manaʻo ma ʻaneʻi no ka manawa mua.

Hoʻohui i kāu manaʻo

E ʻoluʻolu e helu: 6 + 6 =
E aʻo kākou e pili ana i ka Anaplastic Large Cell Lymphoma (ALCL) ma nā ʻōlelo maʻalahi.

E aʻo kākou e pili ana i ka Anaplastic Large Cell Lymphoma (ALCL) ma nā ʻōlelo maʻalahi.

Ua lohe paha ʻoe i ka Anaplastic Large Cell Lymphoma (ALCL)? Malia paha he ʻano paʻakikī iki kēia inoa. Akā, mai hopohopo, he ʻano maʻi kanesa laha ʻole kēia. I kēia lā, e kamaʻilio mākou e pili ana i ke ʻano o ka ALCL, pehea e ulu ai, he aha nā hōʻailona, ​​he aha nā lāʻau lapaʻau, a me nā mea ʻē aʻe he nui ma ke ʻano maʻalahi loa e hiki ai iā ʻoe ke hoʻomaopopo. E like me ke kamaʻilio ʻana me kahi hoaaloha.

He aha ka ALCL (Anaplastic Large Cell Lymphoma)?

I ka ʻōlelo maʻalahi, he ʻano maʻi kanesa kakaʻikahi a ʻano ʻē ʻole ʻo ALCL no kahi hui nui o nā maʻi kanesa i kapa ʻia ʻo Non-Hodgkin Lymphoma . Ua ʻike anei ʻoe e like me nā Non-Hodgkin Lymphoma āpau, he ʻano maʻi kanesa nō hoʻi ʻo ALCL? Hana ia i ka wā e ulu ai kahi ʻano koko keʻokeʻo i kapa ʻia ʻo lymphocytes i loko o ko mākou kino ma waho o ke kaohi a ma ka wikiwiki ma mua o ka mea e pono ai.

E noʻonoʻo i kēia mau lymphocytes e like me nā koa liʻiliʻi i loko o ko mākou kino. He ʻāpana lākou o kā mākou ʻōnaehana pale, e pale ana iā mākou mai nā germs a me nā maʻi. ʻElua ʻano nui o nā lymphocytes: nā cell B a me nā cell T. I loko o ALCL, ulu kūpono ʻole kāu mau lymphocytes T, a i ʻole nā ​​​​cell T.

I kēia manawa, e nānā kākou i ke ʻano o kēia inoa "anaplastic large cell lymphoma".

  • Anaplastic : ʻO ke ʻano o kēia huaʻōlelo, i ka nānā ʻana ma lalo o kahi microscope, ʻano ʻē loa kēia mau hunaola kanesa a ʻokoʻa hoʻi i ka hoʻohālikelike ʻia me nā hunaola T lymphocyte olakino. Me he mea lā ua hoʻopilikia ʻia ko lākou ʻano a me ke ʻano.
  • Kelepona Nui : ʻO ke ʻano kēia, ʻoi aku ka nui o nā lymphocytes T hana maʻamau ma mua o nā kelepona T maʻamau. ʻIke maopopo ʻia kēia ʻokoʻa ma lalo o kahi microscope.
  • Lymphoma : ʻO ka Lymphoma kahi maʻi ʻaʻai e kū mai ana ma muli o ka ulu ʻole ʻana o nā hunaola koko keʻokeʻo i kapa ʻia ʻo lymphocytes. Hoʻomohala kūikawā ʻia ʻo ALCL mai nā lymphocytes T.

Ua maopopo iaʻu? I ka ʻōlelo maʻalahi, he maʻi ʻaʻai ʻo ALCL kahi e lilo ai nā pūnaewele T i mea nui loa, loli, a ulu me ke kāohi ʻole.

Aia kekahi mau ʻano like ʻole o ALCL?

ʻAe, aia nā ʻano ALCL like ʻole. Ua hoʻokaʻawale ʻia kēia mau mea ma muli o kahi o ke kanesa i loko o kou kino a me nā ʻano o nā hunaola kanesa.

ALCL ʻōnaehana

ʻO kēia ke ʻano nui. ʻO ke ʻano "Systemic" hiki ke hoʻopilikia i ke kino holoʻokoʻa. Hiki iā ia ke hoʻopilikia i kāu mau lymph nodes , a i ʻole "glands" e like me kā mākou e kapa nei iā lākou, a me nā ʻōpū kūloko e like me kou ake a me nā māmā, a i kekahi manawa kou ʻili.

Ua māhele ʻia ka ALCL ʻōnaehana i ʻelua ʻano. Hoʻokumu ʻia kekahi ma muli o ka loaʻa ʻana o kahi mutation i loko o kahi gene i kapa ʻia ʻo ka gene "Anaplastic Lymphoma Kinase (ALK)" . Ua like nā genes me nā puke kuhikuhi liʻiliʻi no kā mākou mau cell, a haʻi kēia mau genes i kahi T lymphocyte pehea e hana ai.

  • ALK-positive ALCL: He ʻano maʻi kanesa kēia nona ka mutation i loko o ka gene ALK. He maʻi kanesa ikaika pinepine kēia. Eia nō naʻe, ʻoi aku ka maʻamau i nā keiki a me nā ʻōpio . ʻO ka mea pōmaikaʻi, pane maikaʻi kēia ʻano i ka chemotherapy .
  • ʻALK-maikaʻi ʻole ALCL : ʻAʻohe o kēia ʻano i ka hoʻololi ʻana o ka gene ALK. He maʻi kanesa ulu wikiwiki (hoʻouka kaua) nō hoʻi kēia. Eia nō naʻe, pili nui ia i ka poʻe ʻelemakule , ʻo ka poʻe ma luna o 60 mau makahiki. Hiki i kēia ʻano ke hoʻomaha ma hope o ka chemotherapy a laila hoʻi hou. No laila, ʻoi aku ka paʻakikī o ka mālama ʻana iā ALK-maikaʻi ʻole ALCL, a ʻoi aku ka maikaʻi ʻole o ka wānana ma mua o ALK-positive ALCL.

Nā ʻano ʻē aʻe o ALCL

Aia kekahi mau ʻano ALCL e ulu lohi ana ma mua o nā ʻano ʻōnaehana.

  • ʻO ka ALCL ʻili mua : He ʻano kēia e hoʻopilikia nui i ka ʻili. Hiki ke loaʻa nā hōʻailona e like me nā pehu, nā puʻupuʻu, a me ka eczema. I ka hapa nui o nā hihia (ma kahi o 90%) ʻaʻole ia e pālahalaha ma waho o ka ʻili.
  • ʻO ka ALCL e pili ana i ka implant umauma (BIA-ALCL) : He ʻano ALCL kēia e ulu a puni nā implant umauma. Hoʻomaopopo pinepine ʻia ma kahi o 10 mau makahiki ma hope o ke kaʻina hana hoʻonui umauma a i ʻole ke kaʻina hana kūkulu hou ʻana i ka umauma.

ʻO wai ka mea e loaʻa ana iā ALCL?

ʻOiai hiki ke ulu aʻe ʻo ALCL i nā kānaka o kēlā me kēia makahiki, ʻoi aku ka hoʻopilikia o kekahi mau ʻano i kekahi mau hui.

  • ʻO ALK-positive ALCL : Hoʻopilikia pinepine kēia i nā keiki ma hope o ke kula kamaliʻi, nā ʻōpio, a me nā mākua ʻōpio i ko lākou mau makahiki 20 a me 30. ʻOi aku ka maʻamau i nā kāne .
  • ALK-maikaʻi ʻole ALCL : Hoʻopilikia nui kēia i ka poʻe ma luna o 60 mau makahiki. ʻOi aku ka maʻamau o ia i nā kāne.
  • ʻO ka ALCL ʻili mua : ʻIke pinepine ʻia kēia i nā pākeke ma luna o 40 mau makahiki. ʻOi aku ka maʻamau i nā kāne a me ka poʻe keʻokeʻo.
  • BIA-ALCL : ʻIke pinepine ʻia kēia i nā poʻe i ko lākou mau makahiki 50. Hiki iā ia ke ulu i loko o ka poʻe i loaʻa nā implants umauma silicone a me saline. Ua ʻike ʻia he pili pono ia me nā implants umauma textured .

Pehea ka maʻamau o ALCL?

He maʻi kanesa laha ʻole ʻo ALCL. Ma kahi o 2% wale nō o nā lymphomas non-Hodgkin i nā pākeke i ʻike ʻia he ALCL. He pakeneka liʻiliʻi loa kēlā.

He aha nā hōʻailona o ALCL?

ʻOkoʻa nā hōʻailona o ALCL ma muli o ke ʻano.

Nā hōʻailona o ka ALCL ʻōnaehana

I loko o nā ALCL ALK-positive a me ALK-negative, he mea maʻamau nā lymph nodes pehu ma kahi e ulu ana ke kanesa. Hiki iā lākou ke manaʻo e like me nā puʻupuʻu ma nā wahi e like me kou ʻāʻī, nā armpits, a i ʻole ka groin . ʻO nā hōʻailona ʻē aʻe:

  • Ka wela pinepine.
  • Manaʻo luhi loa (`Fatigue`).
  • Ka hou ʻana i ka pō ('Night sweats').
  • Ka pohō kaumaha i wehewehe ʻole ʻia.

Ke ʻike ʻia ka hapa nui o nā kānaka, ua pālahalaha iki paha ke kanesa, ʻo ia hoʻi, aia ia i kahi 'paepae holomua' . I kēlā hihia, ua pālahalaha paha ke kanesa i nā ʻōpū e like me kou māmā, ke akepaʻa, a i ʻole nā ​​iwi. A laila, hiki ke ʻike ʻia nā hōʻailona ma muli o ke ʻano i hoʻopilikia ʻia. No ka laʻana, inā he ʻūlū kou umauma a i ʻole ka ʻū pinepine, ua hoʻopilikia paha ka ALCL i ka umauma.

Nā ʻano o ka ALCL ʻili mua

Hiki ke ʻike ʻia nā loli o ka ʻili ma kēia ʻano.

  • ʻIke ʻia nā puʻupuʻu ʻulaʻula a ʻulaʻula paha ma kekahi a ʻoi aku paha mau wahi o ka ʻili, a hiki ke ulu nui aʻe i ka hala ʻana o ka manawa.
  • Nā puʻupuʻu i hāpai ʻia , ʻoi aku ka nui ma mua o ke kālā. Hiki i kēia ke maneʻo i kekahi manawa.
  • Hiki i nā puʻupuʻu ke lilo i ʻeha a laila lilo i ʻōpala .

Nā ʻano o BIA-ALCL (Breast Implant-Associated ALCL)

Ma kēia, hiki ke ʻike ʻia nā loli maopopo i nā umauma.

  • ʻEha umauma.
  • Pehu ʻana o ka umauma.
  • ʻO ka ʻili a i ʻole ka eczema.
  • Ka pehu ʻana a i ʻole ka hōʻiliʻili ʻana o ka wai kokoke i kou implant umauma.
  • He puʻu paʻa kokoke i ke kāpili umauma.

ʻIke pinepine ʻia kēia mau loli ma ka umauma hoʻokahi, akā i kekahi manawa hiki ke ʻike ʻia nā loli ma nā umauma ʻelua.

He aha ke kumu o ALCL?

Hana ʻia ka ALCL i ka wā e hoʻonui nui ʻole ʻia ai nā pūnaewele lymphocyte a mākou i kamaʻilio ai ma mua a hoʻomaka e ulu ma mua o nā ʻiʻo olakino a puni lākou. ʻAʻole maopopo i nā kānaka noiʻi ke kumu e lilo ai kēia mau pūnaewele lymphocyte i maʻi kanesa (nā pūnaewele malignant).

Eia nō naʻe, ua ʻike lākou i kekahi mau hoʻololi genetic i ʻike pinepine ʻia me ALCL. Ua manaʻo ʻia e hiki i kēia mau hoʻololi genetic ke hoʻololi i nā cell olakino i nā cell cancer.

Eia kekahi laʻana, ʻo ke ʻano nui o ka ALK-positive ALCL ʻo ia nā mutations i loko o ka gene ALK . Pēlā nō, he mea maʻamau nā mutations gene ʻē aʻe i nā ʻano ALCL ʻē aʻe.

Pehea e ʻike ʻia ai ʻo ALCL? (Diagnosis)

E hana mua kāu kauka i kahi hoʻokolohua kino e nānā i nā hōʻailona o ALCL, e like me nā lymph node pehu. Inā kānalua lākou i kēia, e hana lākou i kekahi mau hoʻokolohua a me nā kaʻina hana like ʻole.

  • Nā kaʻina hana kiʻiHiki i kēia mau mea ke kōkua i ka ʻike ʻana i kahi o ke kanesa. ʻOkoʻa ke ʻano o nā hoʻāʻo kiʻi āu e pono ai ma muli o ke ʻano o ALCL. Hiki i kāu kauka ke hana i kahi X-ray umauma , CT scan , a i ʻole MRI e nānā i nā puʻupuʻu. Hiki i kahi PET/CT scan a i ʻole PET scan ke kōkua i ka hoʻoholo ʻana inā ua pālahalaha ke kanesa ma ke kino holoʻokoʻa. Inā kānalua ʻia ʻo BIA-ALCL, hiki ke hana ʻia kahi ultrasound umauma .
  • Hana Koko : E hana ke kauka i nā hoʻokolohua koko like ʻole, e like me ka helu koko piha (CBC), e nānā i nā hōʻailona o ALCL. Inā ʻaʻole like ka nui o nā hunaola koko (nā hunaola koko ʻulaʻula, nā hunaola koko keʻokeʻo, a i ʻole nā ​​platelets), he hōʻailona paha ia o ALCL. E nānā pū lākou i kekahi mau enzymes a me nā māka ʻē aʻe i loko o ke koko, no ka mea, hiki i kēia mau mea ke lilo i mau hōʻailona o ALCL.
  • Biopsy : ʻO ke ala wale nō e hōʻoia ai i ka ʻike ʻana o ALCL ʻo ia ka loaʻa ʻana o kahi biopsy. I loko o kahi biopsy, lawe ke kauka i kahi laʻana liʻiliʻi o nā ʻiʻo kānalua a nānā iā ia ma lalo o kahi microscope. Ma ke aʻo ʻana i kēia mau cell, hiki i ke kauka ke hoʻoholo pololei i ke ʻano o ALCL āu. Kōkua pū kēia i ka hoʻolālā ʻana i ka lāʻau lapaʻau kūpono loa.

Pehea e mālama ʻia ai ʻo ALCL?

ʻO ka chemotherapy ka lāʻau maʻamau no ka ALCL systemic. ʻO ke ʻoki kino ka lāʻau lapaʻau makemake nui ʻia no ka ALCL ʻili mua a me ka BIA-ALCL.

Ka mālama ʻana i ka ALCL systemic

ʻO ka maʻamau, pane maikaʻi nā lymphomas cell nui anaplastic ALK-positive a me ALK-negative i ka chemotherapy systemic. ʻO ka chemotherapy systemic e pili ana i ka hāʻawi ʻana i nā lāʻau pepehi kanesa ma o kahi aa koko, e hele ana i loko o ke kino ma o ke kahe koko e pepehi i nā hunaola kanesa.

Hoʻohana pinepine ka Chemotherapy no ka ALCL systemic i ka hui pū ʻana o nā lāʻau lapaʻau e hana pū ana e pepehi i nā hunaola kanesa. ʻO kekahi mau laʻana:

  • BV-CHP : Hoʻokomo pū kēia me nā lāʻau lapaʻau ʻo `Brentuximab Vedotin`, `Cyclophosphamide`, `Doxorubicin (Hydroxydaunorubicin)`, a me `Prednisone`.
  • CHOP : Pili kēia i ka hoʻohana ʻana i nā lāʻau i kapa ʻia ʻo 'Cyclophosphamide', 'Doxorubicin (Hydroxydaunorubicin)', 'Vincristine (Oncovin®)', a me 'Prednisone'.
  • CHEOP : Pili kēia i ka hoʻohana ʻana i nā lāʻau lapaʻau i kapa ʻia ʻo 'Cyclophosphamide', 'Doxorubicin (Hydroxydaunorubicin)', 'Etoposide', 'Vincristine (Oncovin®)', a me 'Prednisone'.

Hiki i kēia mau lāʻau lapaʻau ke hoʻopau i nā hōʻailona āpau o ke kanesa i loko o kahi manawa pōkole (kapa mākou i kēia 'remission').(Ua kapa ʻia ʻo ia he "relapse") Eia naʻe, hiki i ke kanesa ke hoʻi hou mai. Inā manaʻo kāu kauka e hoʻi mai ana ke kanesa, hiki iā lākou ke paipai i kahi hoʻoili cell stem i kou wā e hoʻomaha ai. Hoʻololi kahi hoʻoili cell stem i nā cell i luku ʻia e ka chemotherapy me nā cell olakino. A laila hana kēia mau cell olakino i nā cell koko olakino (ʻaʻole cancerous).

Inā hoʻi mai ke kanesa, hiki i kāu kauka ke ʻōlelo i nā ʻano lāʻau chemotherapy ʻē aʻe i hoʻolālā ʻia e mālama i ka lymphoma.

Ka mālama ʻana i ka ALCL ʻili mua

ʻO ke ʻoki kino ka lāʻau lapaʻau maʻamau no kēia. Inā ua pālahalaha ke kanesa i nā lymph nodes, pono paha ʻoe i ka radiation therapy . Hana ka radiation therapy ma ke kuhikuhi ʻana i ka ikehu i nā cell cancer a luku iā lākou.

Hiki i ka ALCL ʻili mua ke hoʻi hou i loko o ʻelima mau makahiki o ka mālama ʻana. Inā hana ʻia kēia, pono hou ke ʻoki kino a me ka radiation therapy.

Inā he mau puʻupuʻu kūloko kou i hiki ʻole ke wehe ʻia me ke ʻoki ʻana, a inā hoʻi hou mai ke kanesa, pono paha ʻoe i nā lāʻau lapaʻau ʻē aʻe. Hiki i kēia mau mea ke komo pū me:

  • ʻO Methotrexate Waha : He lāʻau lapaʻau i hoʻohana ʻia e mālama i ka lymphoma non-Hodgkin.
  • ʻO Bexarotene : He lāʻau lapaʻau i hoʻohana ʻia e mālama i ka lymphoma T-cell e hoʻopilikia ana i ka ʻili.
  • ʻO Brentuximab Vedotin : He lāʻau lapaʻau i hoʻohana ʻia e mālama i ka ALCL systemic a me nā ʻano ʻē aʻe o ka ALCL hou.
  • Interferon : He lāʻau lapaʻau e kōkua ai i kāu ʻōnaehana pale e ʻike a hakakā i nā hunaola kanesa, me ka lymphoma.

Ka mālama ʻana i ka BIA-ALCL

Hiki ke ho'ōla ʻia ʻo BIA-ALCL me ke ʻoki ʻana e wehe i kāu implant umauma a me nā hunaola kanesa a puni ia. Inā ʻaʻole hiki ke ʻoki ʻia, hiki ke hāʻawi ʻia ka radiation therapy e pepehi i nā hunaola kanesa.

Inā hoʻi mai ke kanesa a pālahalaha paha ma ʻō aku o ka umauma, hiki i kāu kauka ke ʻōlelo aku i nā lāʻau lapaʻau chemotherapy e hoʻohana ʻia e mālama ai iā ALK-negative ALCL. Hiki i kēia ke komo pū me ka chemotherapy CHOP a me nā lāʻau lapaʻau e like me Brentuximab Vedotin.

Pehea ke koʻikoʻi o ALCL?

Me ka nānā ʻole i ke ʻano, he maʻi ʻaʻai koʻikoʻi ʻo ALCL e pono ai ka nānā pono ʻana a me ka mālama kūpono. Eia nō naʻe, pili kāu wānana a me ka hoʻolālā mālama i nā mea e like me ke ʻano o ALCL āu, pehea ʻoe e pane ai i ka mālama ʻana, a me kāu helu International Prognostic Index (IPI) .

Ua hoʻomohala ʻia ka IPI e nā kauka oncology e kōkua i ka wānana ʻana i ka hopena o nā lymphomas non-Hodgkin e ulu wikiwiki ana, me ka ALCL systemic. Hoʻokumu ʻia ka helu ma luna o nā kumu aʻe:

  • kou mau makahiki.
  • ʻO kou hiki ke hana i nā hana o kēlā me kēia lā.
  • Pehea ka mamao o ka laha ʻana o kou maʻi kanesa (kahua o ke kanesa).
  • ʻO ka nui o nā kelepa sebaceous i hoʻopilikia ʻia.

Inā loaʻa iā ʻoe ka ALCL systemic, e nīnau i kāu kauka pehea e pili ai kāu helu IPI i kou kūlana o ka ho'ōla ʻana.

He aha ka nui o ke ola no ALCL?

ʻOkoʻa loa nā helu ola no ka ALCL ʻōnaehana. Pili ka ALK-positive ALCL me ka manawa ola lōʻihi ma mua o ka ALK-negative ALCL. Ma muli o nā mea e like me kou ʻano maʻi kanesa a me ka helu IPI, hiki ke piʻi ka helu ola ʻelima makahiki no ka ALK-positive ALCL mai 33% a 90%. Pēlā nō, hiki ke piʻi ka helu ola ʻelima makahiki no ka ALK-negative ALCL mai 13% a 74%.

He maikaʻi loa nā helu ola o ka ALCL ʻili mua a me ka BIA-ALCL. ʻOiai ʻo ka ALCL ʻili mua e hoʻomaha pinepine a hoʻi mai i loko o ʻelima mau makahiki, hiki i nā lāʻau lapaʻau hahai ke hoʻolōʻihi i kou ola. ʻO ka helu ola ma kahi o 80% ʻelima mau makahiki ma hope o ka hōʻoia ʻana. Ma BIA-ALCL, inā e wehe loa ʻia ke kanesa me ke ʻoki ʻana, ua nalowale loa ke kanesa.

He aha nā nīnau e pono iaʻu e nīnau aku i kaʻu kauka?

Eia kekahi mau nīnau koʻikoʻi e nīnau aku i kāu kauka:

  • He aha ke ʻano o ka ALCL iaʻu?
  • Ua kaupalena ʻia koʻu maʻi ʻaʻai i hoʻokahi wahi, a ua laha paha?
  • ʻO wai nā loea ma kaʻu hui mālama?
  • He aha ka lāʻau lapaʻau āu e paipai mai ai iaʻu?
  • Pehea e mālama ai i nā hopena ʻaoʻao o ka lāʻau lapaʻau?
  • He aha kaʻu helu IPI?
  • He aha nā manawa kūpono e komo ai koʻu maʻi kanesa i ke "kala ʻana"?
  • He aha nā manawa kūpono e hoʻi hou mai ai koʻu maʻi kanesa?
  • ʻEhia pinepine e pono ai iaʻu e hele mai no nā kipa hoʻi e nānā i koʻu kūlana?

He mea maʻamau ka makaʻu ke ʻike ʻoe he maʻi kanesa kou. Eia naʻe, ʻo ka mea nui e hoʻomanaʻo ai, ʻaʻole ʻo ALCL he ʻano maʻi kanesa hoʻokahi me ka hopena like . ʻO ke ʻano o ALCL āu e hoʻoholo ai inā laha koke a lohi paha. ʻO ia ka mea e hoʻopili ai i kāu mau koho lapaʻau a me kou manaʻo. Hoʻolaha koke ka ALCL o kekahi poʻe. No kekahi poʻe, ulu lohi ia, e hāʻawi ana iā ʻoe i ka manawa kūpono e loaʻa ai nā lāʻau lapaʻau e hiki ke kōkua i ka kaohi ʻana i ke kanesa. E kamaʻilio me kāu kauka e pili ana i nā hopena hiki ke loaʻa ma muli o kāu hōʻailona.

Nā mea nui e pono ai ʻoe e hoʻomanaʻo (Leka Lawe-Home)

ʻAe, e hōʻuluʻulu kākou i kekahi o nā mea nui e pono ai ʻoe e hoʻomanaʻo mai nā mea a mākou i kamaʻilio ai.

  • He ʻano maʻi kanesa laha ʻole ka ALCL, a he nui nā ʻano like ʻole.
  • ʻAʻole like nā ʻano ALCL āpau. Hoʻolaha koke kekahi, lohi kekahi.
  • ʻOkoʻa ka mālama ʻana a me nā kūlana o ka hoʻōla ʻana ma muli o ke ʻano o ka ALCL āu, kou makahiki, a me kou olakino holoʻokoʻa.
  • ʻOiai ʻoi aku ka pinepine o ka ALK-positive ALCL i ka poʻe ʻōpio, pane maikaʻi ia i ka lāʻau lapaʻau.
  • Hoʻopilikia ka ALK-negative ALCL i nā pākeke he nui a hiki ke paʻakikī iki ka mālama ʻana.
  • ʻO ka wānana no ka skincare ALCL a me ka breast implant-associated ALCL (BIA-ALCL) ma ke ʻano laulā he maikaʻi.
  • Mai hopohopo. Inā he kānalua a he mau hōʻailona paha kāu, e ʻimi koke i ke kōkua lapaʻau.
  • E kamaʻilio ākea me kāu kauka e pili ana i kou kūlana, kāu lāʻau lapaʻau, a me nā nīnau āu e loaʻa ai. ʻO lākou ka poʻe hiki ke kōkua maikaʻi loa iā ʻoe.

E hoʻomanaʻo, ʻaʻole like ke koʻikoʻi o nā maʻi kanesa āpau. ʻOiai me ALCL, me ka ʻike pololei, ka mālama koke ʻana, a me ka nānā pono ʻana, hiki i nā poʻe he nui ke hoʻokō i nā hopena holomua.


ʻO Lymphoma Kelepona Nui Anaplastic, ALCL, Lymphoma, Kanesa, Nā Kelepona T, ALK Gene, Chemotherapy

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

💬 Comments (0)

ʻAʻohe manaʻo i kau ʻia. Hoʻohui i kāu manaʻo ma ʻaneʻi no ka manawa mua.

Hoʻohui i kāu manaʻo

E ʻoluʻolu e helu: 6 + 6 =