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Loaʻa iā ʻoe kahi puʻupuʻu e like me kēia i loko o kou puʻupaʻa? (Angiomyolipoma) Mai hopohopo, e kamaʻilio kākou e pili ana i kēia!

Loaʻa iā ʻoe kahi puʻupuʻu e like me kēia i loko o kou puʻupaʻa? (Angiomyolipoma) Mai hopohopo, e kamaʻilio kākou e pili ana i kēia!

Ua manaʻo paha ʻoe he puʻupuʻu liʻiliʻi kou e ulu ana i loko o kou puʻupaʻa? I kekahi manawa, hiki ke loaʻa kēia mau mea me ka ʻole o nā hōʻailona. I kēia lā, e kamaʻilio mākou e pili ana i kahi ʻano puʻupuʻu e hiki ke hana i loko o ka puʻupaʻa. Ua kapa ʻia ʻo angiomyolipoma , a kapa pū kekahi poʻe iā ia he renal angiomyolipoma. He lōʻihi iki ke kani ʻana o ka inoa, ʻeā? Akā, mai hopohopo, e mālama kākou i ka maʻalahi.

He aha maoli ka Angiomyolipoma?

I ka ʻōlelo maʻalahi, ʻo ka angiomyolipoma kahi ulu ʻana e kū mai ana i ka wā e ulu kūpono ʻole ai kekahi o nā cell i loko o kou puʻupaʻa. Ua kapa pū nā kauka iā ia he tumor a he neoplasm paha . Akā ʻo ka nūhou maikaʻi, ʻaʻole ka hapa nui o nā angiomyolipomas he maʻi kanesa (benign) . ʻO ia hoʻi, ʻaʻole paha lākou e hoʻoulu i nā pilikia koʻikoʻi.

Ua hana ʻia kēia mau nati i ʻekolu mau ʻāpana nui:

  • ʻO ka ʻiʻo adipose , e like me kahi papa o ka ʻaila.
  • ʻIʻo laumania .
  • He mau ʻōmole liʻiliʻi nā kīʻaha koko e lawe ana i ke koko.

Eia nō naʻe, inā e ulu nui kēia puʻupuʻu, e ʻike ʻia paha kekahi mau hōʻailona. Eia kekahi laʻana, hiki ke loaʻa ke kahe koko , ka anemia , ke kuni , a i ʻole ka ʻeha ma kahi o ka puʻupaʻa .

ʻO wai ka mea i ʻoi aku ka paʻakikī o ka loaʻa ʻana o ka angiomyolipoma?

Hiki iā ia ke hana maoli i kekahi. Eia nō naʻe, ua ʻike ʻia e ka noiʻi he ʻoi aku ka nui o ka loaʻa ʻana o kēia maʻi i nā wahine , ʻoiai ka poʻe ma waena o 40 a me 60 mau makahiki .

Eia kekahi, ʻoi aku ka nui o ka poʻe me kekahi mau kūlana olakino e loaʻa i nā angiomyolipomas. ʻElua mau kūlana penei:

  • ʻO ka Lymphangioleiomyomatosis (LAM)
  • ʻO ka Tuberous Sclerosis Complex (TSC)

He mea paʻakikī iki kēia, akā inā loaʻa iā ʻoe kēia maʻi, he mea nui loa ia e kamaʻilio me ke kauka a aʻo e pili ana i ia mea.

Pehea ka maʻamau o nā angiomyolipomas o nā puʻupaʻa?

ʻIke ʻia nā angiomyolipomas ma lalo o 1% o ka heluna kanaka maʻamau. ʻAʻole ia he manaʻo he mea kakaikahi lākou, akā ʻaʻole lākou e hiki i nā kānaka a pau. Eia nō naʻe, ʻo lākou ke ʻano maʻamau o ka puʻupaʻa benign.

He mea maʻamau loa kēia i waena o ka poʻe me ka tuberous sclerosis complex (TSC) i ʻōlelo ʻia ma luna. ʻO ke ʻano kēia, ʻoi aku ma mua o ka hapalua o ka poʻe me TSC hiki ke loaʻa i nā angiomyolipomas.

Aia kekahi mau ʻano angiomyolipomas like ʻole?

ʻAe, hiki ke hoʻokaʻawale ʻia nā angiomyolipomas i ʻekolu mau ʻano nui e pili ana i nā ʻano o nā pūnaewele a me nā ʻiʻo i loko o kēia puʻupuʻu:

1.Nā AML Kuʻuna (triphasic): ʻO kēia ke ʻano maʻamau. Loaʻa iā lākou nā ʻano ʻekolu o nā cell i ʻōlelo ʻia ma mua: nā kīʻaha koko, nā ʻiʻo momona, a me nā ʻiʻo laumania .

2. Nā AML Monophasic: Loaʻa i kēia ʻano puʻupuʻu hoʻokahi ʻano ʻiʻo . No ka laʻana, loaʻa paha iā lākou ka ʻiʻo laumania wale nō, a i ʻole ka ʻiʻo momona wale nō.

3. Nā epithelioid angiomyolipomas: Hoʻokumu nui ʻia kēia mau mea mai nā pūnaewele epithelioid e uhi ana i loko o nā kīʻaha koko o ka puʻupaʻa. ʻOi aku ka nui o ka pilikia o kēia ʻano puʻupuʻu e lilo i maʻi kanesa ma mua o nā mea ʻē aʻe . No laila, ua uku ʻia ka nānā kūikawā i kēia.

Pehea ke koʻikoʻi o ka angiomyolipoma?

I ka manawa pinepine, ʻaʻole ʻike ka nui o ka poʻe me nā angiomyolipomas he hoʻokahi ko lākou. ʻO ia no ka mea ʻaʻole lākou e hōʻike pinepine i kekahi mau hōʻailona.

Eia nō naʻe, inā ulu kēia puʻupuʻu ma mua o 4 kenimika (ʻo ia ka nui o ka walnut a mākou e ʻai mau ai), a laila hiki ke hoʻomaka ke kahe koko (hemorrhage) . Hiki i ke kahe koko e like me kēia ke hoʻoweliweli i ke ola inā ʻaʻole mālama ʻia i ka manawa. No laila he mea nui e makaʻala me kēia mau puʻupuʻu.

Pehea ka wikiwiki o ka ulu ʻana o ka angiomyolipoma?

ʻAʻole ulu iki ka hapa nui o nā angiomyolipomas maʻamau. A i ʻole, inā ulu lākou, lohi loa ko lākou ulu ʻana. Ma ka awelika, ulu kēia mau puʻupuʻu ma kahi o 0.19 kenimika (ma kahi o hoʻokahi ʻumikumamāono o ka ʻīniha) i kēlā me kēia makahiki.

Eia nō naʻe, hiki i kēia mau puʻupuʻu ke ulu wikiwiki i ka wā hāpai . No laila, inā loaʻa iā ʻoe ka angiomyolipoma a ke hāpai nei i kahi pēpē, he mea naʻauao paha ke mālama ʻia ka puʻupuʻu ma mua o kou hāpai ʻana . ʻOi aku ka maikaʻi o ke kamaʻilio ʻana me kāu kauka e pili ana i kēia.

He aha ke kumu o ka angiomyolipoma?

ʻAʻole maopopo i nā kauka ke kumu e hōʻiliʻili ai kēia ʻiʻo a hana i kahi puʻupuʻu puʻupaʻa. Eia nō naʻe, manaʻoʻiʻo nā kānaka noiʻi he kuleana ko kekahi mau loli (nā mutations) i loko o kā mākou mau genes .

He aha nā hōʻailona o ka angiomyolipoma?

E like me kā mākou i ʻōlelo ai ma mua, ʻaʻole ʻike ka hapa nui o ka poʻe me ka angiomyolipoma i kekahi mau hōʻailona . Eia nō naʻe, i ka ulu ʻana o ka puʻupuʻu, hiki ke ʻike ʻia kekahi mau hōʻailona. ʻO kēia mau mea:

  • ʻO ka anemia i hoʻokumu ʻia e ke kahe koko .
  • Kuni .
  • ʻEha ma ka ʻaoʻao o ka puʻupaʻa a i ʻole ka ʻeha o ka puʻupaʻa ma muli o ke kahe ʻana o ke koko a puni ka puʻupaʻa.
  • Ke koko kiʻekiʻe (hypertension) .
  • Ka luaʻi a me ka luaʻi .

Inā loaʻa iā ʻoe kekahi a ʻoi aku paha o kēia mau hōʻailona, ​​​​he mea nui loa e ʻike koke i ke kauka.

Pehea e ʻike ai inā loaʻa iā ʻoe ka angiomyolipoma?

I kekahi manawa, loaʻa paha i kāu kauka ka puʻupuʻu ma kahi ulia ka wā e loaʻa ai iā ʻoe nā hoʻokolohua kiʻi , e like me nā scans, no kekahi maʻi olakino ʻē aʻe. A i ʻole, inā loaʻa iā ʻoe nā hōʻailona i ʻōlelo ʻia ma luna, hiki i kāu kauka ke kauoha i kēia mau hoʻokolohua e ʻike i ke kumu.

He aha ke ʻano o nā hoʻokolohua e ʻike ai i kēia?

Hoʻomaopopo pinepine nā kauka i nā hoʻokolohua kiʻi e like me kēia:

  • Nānā CT
  • MRI
  • Ultrasound

Eia nō naʻe, hiki i kekahi mau ʻano angiomyolipomas ke like me ke kanesa puʻupaʻa ma kēia mau scan. No laila, i mea e maopopo ai, hiki i kāu kauka ke ʻōlelo aku i kahi biopsy puʻupaʻa, ʻo ia hoʻi ka lawe ʻana i kahi ʻāpana liʻiliʻi o ka puʻupaʻa a hoʻāʻo iā ia.

Pehea e ʻike ai inā pono ka mālama ʻana i kaʻu angiomyolipoma?

ʻAʻole pono ka lāʻau lapaʻau i nā kānaka a pau me ka angiomyolipoma. Inā pono ʻoe i ka lāʻau lapaʻau, pili ia i ka nui o ka puʻupuʻu , inā he mau hōʻailona kou , a inā paha ʻoe e hoʻolālā ana e hāpai i ka wā e hiki mai ana .

ʻO ka maʻamau, pono ʻoe e ʻike i kāu kauka ma kahi o hoʻokahi manawa i ka makahiki e nānā i ka ulu ʻana o ka puʻupuʻu. Inā ʻoi aku ka nui o ka puʻupuʻu ma mua o 4 kenimika , hiki i kāu kauka ke ʻōlelo i ka lāʻau lapaʻau.

Pehea e mālama ʻia ai nā angiomyolipomas?

Hiki i ke kauka ke ʻōlelo i nā lāʻau lapaʻau e hoʻōki i ka ulu ʻana o ka puʻupuʻu a wehe paha. ʻO kekahi o kēia mau mea:

  • Lapaʻau ablation: Ma kēia lāʻau lapaʻau, hoʻohana nā kauka i ka ikehu (no ka laʻana , nā nalu radiofrequency ), ka wela nui, a i ʻole ka ea anuanu loa e hoʻopau i ka angiomyolipoma.
  • ʻO ka embolization arterial: Ma kēia kaʻina hana, hana ʻia kahi ʻoki liʻiliʻi ma loko o kou ʻūhā, hoʻokomo ʻia kahi ʻōmole lahilahi (catheter) , a hoʻokomo ʻia nā momi liʻiliʻi ma loko. Hoʻōki kēia mau momi i ke kahe koko i ka angiomyolipoma. Hoʻemi kēia i ka puʻupuʻu, hoʻemi i ke kahe koko, a hoʻemi i ka pilikia o ke kahe ʻana o ke koko.
  • ʻO ka nephrectomy piha: Hoʻopau kēia ʻoki i ka puʻupaʻa holoʻokoʻa i loaʻa ka angiomyolipoma.
  • ʻO ka nephrectomy hapa: ʻAʻole kēia e wehe i ka puʻupaʻa holoʻokoʻa. ʻO ka ʻāpana wale nō o ka puʻupaʻa i loaʻa ka angiomyolipoma e wehe ʻia . Hiki ke hana ʻia kēia ma ke ʻano he nephrectomy hapa hāmama a i ʻole he nephrectomy hapa robotic .

ʻO ka mea nui loa, ʻo ke kamaʻilio ʻana me kāu kauka e koho i ke ʻano lapaʻau kūpono loa iā ʻoe.

Aia kekahi mau pilikia a i ʻole nā ​​​​hopena ʻaoʻao ma hope o ka mālama ʻana?

Aia paha kekahi mau pilikia ma hope o ke ʻoki ʻana i nā puʻupaʻa a me nā lāʻau lapaʻau angiomyolipoma ʻē aʻe. Eia kekahi laʻana:

  • Ke kahe ʻana o ke koko
  • Maʻi
  • Nā ʻōpala

I kekahi manawa, hiki ke loaʻa ka hemahema o ka puʻupaʻa ma hope o ka mālama ʻana i nā puʻupaʻa. Akā, he mea kākaʻikahi loa kēia. E kamaʻilio kāu kauka me ʻoe e pili ana i kēia mau pilikia ma mua o ka mālama ʻana a e hana i nā hana e hōʻemi ai iā lākou. Inā loaʻa ka hemahema o ka puʻupaʻa, e hana kāu kauka i kahi hoʻolālā lapaʻau e kōkua iā ʻoe e hoʻokele i kāu mau hōʻailona a noho olakino e like me ka hiki.

ʻEhia ka lōʻihi e hoʻōla ai ma hope o ka lāʻau lapaʻau?

Inā ua loaʻa iā ʻoe kahi nephrectomy piha a hapa paha , pono ʻoe e noho ma ka haukapila no kekahi mau lā. E nānā pū nā kauka i ka hana o kou puʻupaʻa a e hōʻoia e ho'ōla maikaʻi ana ʻoe.

Inā loaʻa iā ʻoe ka ablation therapy a i ʻole ka arterial embolization , pono ʻoe e noho i ka haukapila no kekahi mau hola a i ʻole ka pō.

Hiki ke pale ʻia ka angiomyolipoma?

ʻO kaʻoiaʻiʻo, ʻaʻohe ala kikoʻī e pale aku ai i ka ulu ʻana o nā angiomyolipomas. Hoʻopuka pinepine kēia mau puʻupuʻu me ka manaʻo ʻole, me ke kumu ʻole . ʻO ia hoʻi, he paʻakikī ke ʻōlelo i ke kumu kikoʻī o ka AML.

Aia kekahi mau kūlana ʻē aʻe e hoʻonui ai iaʻu i ka pilikia o ka loaʻa ʻana o ka angiomyolipoma?

ʻAe. Inā loaʻa iā ʻoe ka tuberous sclerosis complex (TSC) a i ʻole lymphangioleiomyotosis (LAM) , aia ʻoe i ka nui o ka pilikia o ka hoʻomohala ʻana i ka angiomyolipoma. No laila, e kamaʻilio me kāu kauka e pili ana i ka nānā ʻana i kou olakino a me ka hana ʻana i nā hana e hōʻemi ai i kou pilikia.

Inā loaʻa iaʻu kahi angiomyolipoma, he aha kaʻu e manaʻo ai?

Inā loaʻa iā ʻoe kahi angiomyolipoma akā ʻaʻole ʻoe e ʻike i kekahi mau hōʻailona , ​​​​pono ʻoe e ʻike i kāu kauka ma kahi o hoʻokahi manawa i ka makahiki . Pono paha ʻoe e loaʻa nā hoʻokolohua kiʻi e ʻike ai inā e ulu ana ka puʻupuʻu.

Inā loaʻa iā ʻoe nā hōʻailona , ​​​​hiki i kāu kauka ke ʻōlelo i ka lāʻau e pale ai i ka pilikia o ke kahe ʻana o ke koko.

Hiki i nā angiomyolipomas ke hana i nā hopena lōʻihi?

Inā ulu nui nā angiomyolipomas, hiki iā lākou ke kahe ke koko a poha paha . No laila, e nānā mau kāu kauka i ka nui o ka puʻupuʻu a paipai i ka lāʻau lapaʻau inā ʻoe i ka pilikia.

Hiki iaʻu ke loaʻa i ka angiomyolipoma ma mua o hoʻokahi manawa?

ʻAe , hiki i ka angiomyolipoma ke ulu hou ma hope o ka mālama ʻia.Eia kekahi, hiki ke loaʻa ma mua o hoʻokahi angiomyolipoma , a hiki i nā AML ke ulu i nā puʻupaʻa ʻelua .

Hiki i ka angiomyolipoma ke lilo i maʻi ʻaʻai?

ʻO kēlā ʻano puʻupuʻu a mākou i kamaʻilio ai ma mua, i kapa ʻia ʻo epithelioid angiomyolipoma, hiki ke lilo i ka maʻi kanesa . Inā hana ʻia kēlā, e nānā pono kāu kauka iā ʻoe a kamaʻilio pū me ʻoe e pili ana i ka mea e hana ai ma hope.

Inā loaʻa iaʻu ka angiomyolipoma, ehia mau manawa e pono ai iaʻu ke ʻike i ke kauka?

E hana pū me kāu kauka e hoʻomohala i kahi hoʻolālā lapaʻau . E mālama i nā manawa hoʻopaʻa a pau e nānā ai i ka ulu ʻana o ka puʻupuʻu.

Āhea wau e kāhea aku ai i kaʻu kauka?

E kāhea koke aku i kāu kauka inā loaʻa iā ʻoe kekahi o kēia mau hōʻailona hou :

  • ʻEha ʻōpū
  • ʻEha hope
  • kuni
  • Ka luaʻi a me ka luaʻi
  • Hematuria - ke koko i loko o ka mimi

ʻO ka mea hope loa, nā mea e hoʻomanaʻo ai (Leka Lawe-Home)

He puʻupuʻu maikaʻi ʻole ka Angiomyolipoma e ulu pinepine ana i loko o ka puʻupaʻa. ʻAʻole paha ʻoe e loaʻa i kekahi mau hōʻailona. E nānā kāu kauka i ka puʻupuʻu i kēlā me kēia makahiki e ʻike inā e ulu ana. Pono paha nā puʻupuʻu i ʻoi aku ma mua o 4 kenimika e mālama ʻia e pale aku i ke kahe ʻana o ke koko.

ʻO ka mea nui loa, inā loaʻa iā ʻoe kekahi mau hōʻailona, ​​mai hopohopo a kamaʻilio koke me kāu kauka. E hāʻawi lākou iā ʻoe i ka lāʻau lapaʻau a me ke alakaʻi maikaʻi loa āu e pono ai.


ʻAngiomyolipoma , nā cysts o ka puʻupaʻa, ka maʻi puʻupaʻa, nā puʻupuʻu maikaʻi ʻole, ka ʻeha o ka puʻupaʻa, ka anemia, ka sclerosis tuberous

Frequently Asked Questions (FAQ)

He aha ke ʻano o nā hoʻokolohua e ʻike ai i kēia?

Hoʻomaopopo pinepine nā kauka i nā hoʻokolohua kiʻi e like me kēia:

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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Loaʻa iā ʻoe kahi puʻupuʻu e like me kēia i loko o kou puʻupaʻa? (Angiomyolipoma) Mai hopohopo, e kamaʻilio kākou e pili ana i kēia!

Loaʻa iā ʻoe kahi puʻupuʻu e like me kēia i loko o kou puʻupaʻa? (Angiomyolipoma) Mai hopohopo, e kamaʻilio kākou e pili ana i kēia!

Ua manaʻo paha ʻoe he puʻupuʻu liʻiliʻi kou e ulu ana i loko o kou puʻupaʻa? I kekahi manawa, hiki ke loaʻa kēia mau mea me ka ʻole o nā hōʻailona. I kēia lā, e kamaʻilio mākou e pili ana i kahi ʻano puʻupuʻu e hiki ke hana i loko o ka puʻupaʻa. Ua kapa ʻia ʻo angiomyolipoma , a kapa pū kekahi poʻe iā ia he renal angiomyolipoma. He lōʻihi iki ke kani ʻana o ka inoa, ʻeā? Akā, mai hopohopo, e mālama kākou i ka maʻalahi.

He aha maoli ka Angiomyolipoma?

I ka ʻōlelo maʻalahi, ʻo ka angiomyolipoma kahi ulu ʻana e kū mai ana i ka wā e ulu kūpono ʻole ai kekahi o nā cell i loko o kou puʻupaʻa. Ua kapa pū nā kauka iā ia he tumor a he neoplasm paha . Akā ʻo ka nūhou maikaʻi, ʻaʻole ka hapa nui o nā angiomyolipomas he maʻi kanesa (benign) . ʻO ia hoʻi, ʻaʻole paha lākou e hoʻoulu i nā pilikia koʻikoʻi.

Ua hana ʻia kēia mau nati i ʻekolu mau ʻāpana nui:

  • ʻO ka ʻiʻo adipose , e like me kahi papa o ka ʻaila.
  • ʻIʻo laumania .
  • He mau ʻōmole liʻiliʻi nā kīʻaha koko e lawe ana i ke koko.

Eia nō naʻe, inā e ulu nui kēia puʻupuʻu, e ʻike ʻia paha kekahi mau hōʻailona. Eia kekahi laʻana, hiki ke loaʻa ke kahe koko , ka anemia , ke kuni , a i ʻole ka ʻeha ma kahi o ka puʻupaʻa .

ʻO wai ka mea i ʻoi aku ka paʻakikī o ka loaʻa ʻana o ka angiomyolipoma?

Hiki iā ia ke hana maoli i kekahi. Eia nō naʻe, ua ʻike ʻia e ka noiʻi he ʻoi aku ka nui o ka loaʻa ʻana o kēia maʻi i nā wahine , ʻoiai ka poʻe ma waena o 40 a me 60 mau makahiki .

Eia kekahi, ʻoi aku ka nui o ka poʻe me kekahi mau kūlana olakino e loaʻa i nā angiomyolipomas. ʻElua mau kūlana penei:

  • ʻO ka Lymphangioleiomyomatosis (LAM)
  • ʻO ka Tuberous Sclerosis Complex (TSC)

He mea paʻakikī iki kēia, akā inā loaʻa iā ʻoe kēia maʻi, he mea nui loa ia e kamaʻilio me ke kauka a aʻo e pili ana i ia mea.

Pehea ka maʻamau o nā angiomyolipomas o nā puʻupaʻa?

ʻIke ʻia nā angiomyolipomas ma lalo o 1% o ka heluna kanaka maʻamau. ʻAʻole ia he manaʻo he mea kakaikahi lākou, akā ʻaʻole lākou e hiki i nā kānaka a pau. Eia nō naʻe, ʻo lākou ke ʻano maʻamau o ka puʻupaʻa benign.

He mea maʻamau loa kēia i waena o ka poʻe me ka tuberous sclerosis complex (TSC) i ʻōlelo ʻia ma luna. ʻO ke ʻano kēia, ʻoi aku ma mua o ka hapalua o ka poʻe me TSC hiki ke loaʻa i nā angiomyolipomas.

Aia kekahi mau ʻano angiomyolipomas like ʻole?

ʻAe, hiki ke hoʻokaʻawale ʻia nā angiomyolipomas i ʻekolu mau ʻano nui e pili ana i nā ʻano o nā pūnaewele a me nā ʻiʻo i loko o kēia puʻupuʻu:

1.Nā AML Kuʻuna (triphasic): ʻO kēia ke ʻano maʻamau. Loaʻa iā lākou nā ʻano ʻekolu o nā cell i ʻōlelo ʻia ma mua: nā kīʻaha koko, nā ʻiʻo momona, a me nā ʻiʻo laumania .

2. Nā AML Monophasic: Loaʻa i kēia ʻano puʻupuʻu hoʻokahi ʻano ʻiʻo . No ka laʻana, loaʻa paha iā lākou ka ʻiʻo laumania wale nō, a i ʻole ka ʻiʻo momona wale nō.

3. Nā epithelioid angiomyolipomas: Hoʻokumu nui ʻia kēia mau mea mai nā pūnaewele epithelioid e uhi ana i loko o nā kīʻaha koko o ka puʻupaʻa. ʻOi aku ka nui o ka pilikia o kēia ʻano puʻupuʻu e lilo i maʻi kanesa ma mua o nā mea ʻē aʻe . No laila, ua uku ʻia ka nānā kūikawā i kēia.

Pehea ke koʻikoʻi o ka angiomyolipoma?

I ka manawa pinepine, ʻaʻole ʻike ka nui o ka poʻe me nā angiomyolipomas he hoʻokahi ko lākou. ʻO ia no ka mea ʻaʻole lākou e hōʻike pinepine i kekahi mau hōʻailona.

Eia nō naʻe, inā ulu kēia puʻupuʻu ma mua o 4 kenimika (ʻo ia ka nui o ka walnut a mākou e ʻai mau ai), a laila hiki ke hoʻomaka ke kahe koko (hemorrhage) . Hiki i ke kahe koko e like me kēia ke hoʻoweliweli i ke ola inā ʻaʻole mālama ʻia i ka manawa. No laila he mea nui e makaʻala me kēia mau puʻupuʻu.

Pehea ka wikiwiki o ka ulu ʻana o ka angiomyolipoma?

ʻAʻole ulu iki ka hapa nui o nā angiomyolipomas maʻamau. A i ʻole, inā ulu lākou, lohi loa ko lākou ulu ʻana. Ma ka awelika, ulu kēia mau puʻupuʻu ma kahi o 0.19 kenimika (ma kahi o hoʻokahi ʻumikumamāono o ka ʻīniha) i kēlā me kēia makahiki.

Eia nō naʻe, hiki i kēia mau puʻupuʻu ke ulu wikiwiki i ka wā hāpai . No laila, inā loaʻa iā ʻoe ka angiomyolipoma a ke hāpai nei i kahi pēpē, he mea naʻauao paha ke mālama ʻia ka puʻupuʻu ma mua o kou hāpai ʻana . ʻOi aku ka maikaʻi o ke kamaʻilio ʻana me kāu kauka e pili ana i kēia.

He aha ke kumu o ka angiomyolipoma?

ʻAʻole maopopo i nā kauka ke kumu e hōʻiliʻili ai kēia ʻiʻo a hana i kahi puʻupuʻu puʻupaʻa. Eia nō naʻe, manaʻoʻiʻo nā kānaka noiʻi he kuleana ko kekahi mau loli (nā mutations) i loko o kā mākou mau genes .

He aha nā hōʻailona o ka angiomyolipoma?

E like me kā mākou i ʻōlelo ai ma mua, ʻaʻole ʻike ka hapa nui o ka poʻe me ka angiomyolipoma i kekahi mau hōʻailona . Eia nō naʻe, i ka ulu ʻana o ka puʻupuʻu, hiki ke ʻike ʻia kekahi mau hōʻailona. ʻO kēia mau mea:

  • ʻO ka anemia i hoʻokumu ʻia e ke kahe koko .
  • Kuni .
  • ʻEha ma ka ʻaoʻao o ka puʻupaʻa a i ʻole ka ʻeha o ka puʻupaʻa ma muli o ke kahe ʻana o ke koko a puni ka puʻupaʻa.
  • Ke koko kiʻekiʻe (hypertension) .
  • Ka luaʻi a me ka luaʻi .

Inā loaʻa iā ʻoe kekahi a ʻoi aku paha o kēia mau hōʻailona, ​​​​he mea nui loa e ʻike koke i ke kauka.

Pehea e ʻike ai inā loaʻa iā ʻoe ka angiomyolipoma?

I kekahi manawa, loaʻa paha i kāu kauka ka puʻupuʻu ma kahi ulia ka wā e loaʻa ai iā ʻoe nā hoʻokolohua kiʻi , e like me nā scans, no kekahi maʻi olakino ʻē aʻe. A i ʻole, inā loaʻa iā ʻoe nā hōʻailona i ʻōlelo ʻia ma luna, hiki i kāu kauka ke kauoha i kēia mau hoʻokolohua e ʻike i ke kumu.

He aha ke ʻano o nā hoʻokolohua e ʻike ai i kēia?

Hoʻomaopopo pinepine nā kauka i nā hoʻokolohua kiʻi e like me kēia:

  • Nānā CT
  • MRI
  • Ultrasound

Eia nō naʻe, hiki i kekahi mau ʻano angiomyolipomas ke like me ke kanesa puʻupaʻa ma kēia mau scan. No laila, i mea e maopopo ai, hiki i kāu kauka ke ʻōlelo aku i kahi biopsy puʻupaʻa, ʻo ia hoʻi ka lawe ʻana i kahi ʻāpana liʻiliʻi o ka puʻupaʻa a hoʻāʻo iā ia.

Pehea e ʻike ai inā pono ka mālama ʻana i kaʻu angiomyolipoma?

ʻAʻole pono ka lāʻau lapaʻau i nā kānaka a pau me ka angiomyolipoma. Inā pono ʻoe i ka lāʻau lapaʻau, pili ia i ka nui o ka puʻupuʻu , inā he mau hōʻailona kou , a inā paha ʻoe e hoʻolālā ana e hāpai i ka wā e hiki mai ana .

ʻO ka maʻamau, pono ʻoe e ʻike i kāu kauka ma kahi o hoʻokahi manawa i ka makahiki e nānā i ka ulu ʻana o ka puʻupuʻu. Inā ʻoi aku ka nui o ka puʻupuʻu ma mua o 4 kenimika , hiki i kāu kauka ke ʻōlelo i ka lāʻau lapaʻau.

Pehea e mālama ʻia ai nā angiomyolipomas?

Hiki i ke kauka ke ʻōlelo i nā lāʻau lapaʻau e hoʻōki i ka ulu ʻana o ka puʻupuʻu a wehe paha. ʻO kekahi o kēia mau mea:

  • Lapaʻau ablation: Ma kēia lāʻau lapaʻau, hoʻohana nā kauka i ka ikehu (no ka laʻana , nā nalu radiofrequency ), ka wela nui, a i ʻole ka ea anuanu loa e hoʻopau i ka angiomyolipoma.
  • ʻO ka embolization arterial: Ma kēia kaʻina hana, hana ʻia kahi ʻoki liʻiliʻi ma loko o kou ʻūhā, hoʻokomo ʻia kahi ʻōmole lahilahi (catheter) , a hoʻokomo ʻia nā momi liʻiliʻi ma loko. Hoʻōki kēia mau momi i ke kahe koko i ka angiomyolipoma. Hoʻemi kēia i ka puʻupuʻu, hoʻemi i ke kahe koko, a hoʻemi i ka pilikia o ke kahe ʻana o ke koko.
  • ʻO ka nephrectomy piha: Hoʻopau kēia ʻoki i ka puʻupaʻa holoʻokoʻa i loaʻa ka angiomyolipoma.
  • ʻO ka nephrectomy hapa: ʻAʻole kēia e wehe i ka puʻupaʻa holoʻokoʻa. ʻO ka ʻāpana wale nō o ka puʻupaʻa i loaʻa ka angiomyolipoma e wehe ʻia . Hiki ke hana ʻia kēia ma ke ʻano he nephrectomy hapa hāmama a i ʻole he nephrectomy hapa robotic .

ʻO ka mea nui loa, ʻo ke kamaʻilio ʻana me kāu kauka e koho i ke ʻano lapaʻau kūpono loa iā ʻoe.

Aia kekahi mau pilikia a i ʻole nā ​​​​hopena ʻaoʻao ma hope o ka mālama ʻana?

Aia paha kekahi mau pilikia ma hope o ke ʻoki ʻana i nā puʻupaʻa a me nā lāʻau lapaʻau angiomyolipoma ʻē aʻe. Eia kekahi laʻana:

  • Ke kahe ʻana o ke koko
  • Maʻi
  • Nā ʻōpala

I kekahi manawa, hiki ke loaʻa ka hemahema o ka puʻupaʻa ma hope o ka mālama ʻana i nā puʻupaʻa. Akā, he mea kākaʻikahi loa kēia. E kamaʻilio kāu kauka me ʻoe e pili ana i kēia mau pilikia ma mua o ka mālama ʻana a e hana i nā hana e hōʻemi ai iā lākou. Inā loaʻa ka hemahema o ka puʻupaʻa, e hana kāu kauka i kahi hoʻolālā lapaʻau e kōkua iā ʻoe e hoʻokele i kāu mau hōʻailona a noho olakino e like me ka hiki.

ʻEhia ka lōʻihi e hoʻōla ai ma hope o ka lāʻau lapaʻau?

Inā ua loaʻa iā ʻoe kahi nephrectomy piha a hapa paha , pono ʻoe e noho ma ka haukapila no kekahi mau lā. E nānā pū nā kauka i ka hana o kou puʻupaʻa a e hōʻoia e ho'ōla maikaʻi ana ʻoe.

Inā loaʻa iā ʻoe ka ablation therapy a i ʻole ka arterial embolization , pono ʻoe e noho i ka haukapila no kekahi mau hola a i ʻole ka pō.

Hiki ke pale ʻia ka angiomyolipoma?

ʻO kaʻoiaʻiʻo, ʻaʻohe ala kikoʻī e pale aku ai i ka ulu ʻana o nā angiomyolipomas. Hoʻopuka pinepine kēia mau puʻupuʻu me ka manaʻo ʻole, me ke kumu ʻole . ʻO ia hoʻi, he paʻakikī ke ʻōlelo i ke kumu kikoʻī o ka AML.

Aia kekahi mau kūlana ʻē aʻe e hoʻonui ai iaʻu i ka pilikia o ka loaʻa ʻana o ka angiomyolipoma?

ʻAe. Inā loaʻa iā ʻoe ka tuberous sclerosis complex (TSC) a i ʻole lymphangioleiomyotosis (LAM) , aia ʻoe i ka nui o ka pilikia o ka hoʻomohala ʻana i ka angiomyolipoma. No laila, e kamaʻilio me kāu kauka e pili ana i ka nānā ʻana i kou olakino a me ka hana ʻana i nā hana e hōʻemi ai i kou pilikia.

Inā loaʻa iaʻu kahi angiomyolipoma, he aha kaʻu e manaʻo ai?

Inā loaʻa iā ʻoe kahi angiomyolipoma akā ʻaʻole ʻoe e ʻike i kekahi mau hōʻailona , ​​​​pono ʻoe e ʻike i kāu kauka ma kahi o hoʻokahi manawa i ka makahiki . Pono paha ʻoe e loaʻa nā hoʻokolohua kiʻi e ʻike ai inā e ulu ana ka puʻupuʻu.

Inā loaʻa iā ʻoe nā hōʻailona , ​​​​hiki i kāu kauka ke ʻōlelo i ka lāʻau e pale ai i ka pilikia o ke kahe ʻana o ke koko.

Hiki i nā angiomyolipomas ke hana i nā hopena lōʻihi?

Inā ulu nui nā angiomyolipomas, hiki iā lākou ke kahe ke koko a poha paha . No laila, e nānā mau kāu kauka i ka nui o ka puʻupuʻu a paipai i ka lāʻau lapaʻau inā ʻoe i ka pilikia.

Hiki iaʻu ke loaʻa i ka angiomyolipoma ma mua o hoʻokahi manawa?

ʻAe , hiki i ka angiomyolipoma ke ulu hou ma hope o ka mālama ʻia.Eia kekahi, hiki ke loaʻa ma mua o hoʻokahi angiomyolipoma , a hiki i nā AML ke ulu i nā puʻupaʻa ʻelua .

Hiki i ka angiomyolipoma ke lilo i maʻi ʻaʻai?

ʻO kēlā ʻano puʻupuʻu a mākou i kamaʻilio ai ma mua, i kapa ʻia ʻo epithelioid angiomyolipoma, hiki ke lilo i ka maʻi kanesa . Inā hana ʻia kēlā, e nānā pono kāu kauka iā ʻoe a kamaʻilio pū me ʻoe e pili ana i ka mea e hana ai ma hope.

Inā loaʻa iaʻu ka angiomyolipoma, ehia mau manawa e pono ai iaʻu ke ʻike i ke kauka?

E hana pū me kāu kauka e hoʻomohala i kahi hoʻolālā lapaʻau . E mālama i nā manawa hoʻopaʻa a pau e nānā ai i ka ulu ʻana o ka puʻupuʻu.

Āhea wau e kāhea aku ai i kaʻu kauka?

E kāhea koke aku i kāu kauka inā loaʻa iā ʻoe kekahi o kēia mau hōʻailona hou :

  • ʻEha ʻōpū
  • ʻEha hope
  • kuni
  • Ka luaʻi a me ka luaʻi
  • Hematuria - ke koko i loko o ka mimi

ʻO ka mea hope loa, nā mea e hoʻomanaʻo ai (Leka Lawe-Home)

He puʻupuʻu maikaʻi ʻole ka Angiomyolipoma e ulu pinepine ana i loko o ka puʻupaʻa. ʻAʻole paha ʻoe e loaʻa i kekahi mau hōʻailona. E nānā kāu kauka i ka puʻupuʻu i kēlā me kēia makahiki e ʻike inā e ulu ana. Pono paha nā puʻupuʻu i ʻoi aku ma mua o 4 kenimika e mālama ʻia e pale aku i ke kahe ʻana o ke koko.

ʻO ka mea nui loa, inā loaʻa iā ʻoe kekahi mau hōʻailona, ​​mai hopohopo a kamaʻilio koke me kāu kauka. E hāʻawi lākou iā ʻoe i ka lāʻau lapaʻau a me ke alakaʻi maikaʻi loa āu e pono ai.


ʻAngiomyolipoma , nā cysts o ka puʻupaʻa, ka maʻi puʻupaʻa, nā puʻupuʻu maikaʻi ʻole, ka ʻeha o ka puʻupaʻa, ka anemia, ka sclerosis tuberous

Frequently Asked Questions (FAQ)

He aha ke ʻano o nā hoʻokolohua e ʻike ai i kēia?

Hoʻomaopopo pinepine nā kauka i nā hoʻokolohua kiʻi e like me kēia:

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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