He mea maʻamau ka makaʻu a me ka haʻalulu ke haʻi aku ke kauka o kāu keiki iā ʻoe he lua i loko o ko lākou puʻuwai. Ke noʻonoʻo nei paha ʻoe, "Auē kuʻu Akua, he aha ka mea i hana ʻia i kaʻu keiki?" Akā, mai hopohopo. He mea maʻamau kēia maʻi i ka lāʻau lapaʻau. I kēia lā, e kamaʻilio mākou e pili ana i kēia lua i loko o ka puʻuwai, ʻo ia ka mea a mākou e kapa nei he `(Atrial Septal Defect - ASD)` i ka lāʻau lapaʻau, a me ka lāʻau lapaʻau i hoʻohana ʻia e ho'ōla iā ia, ʻo ia hoʻi `(ASD Closure)`.
I ka ʻōlelo maʻalahi, he aha ka ASD?
ʻEhā keʻena nui o ko kākou puʻuwai. Ua kapa ʻia nā keʻena ʻelua o luna ʻo ka atria. Aia kahi paia (septum) ma waena o kēia mau atria ʻelua. ʻO kahi Atrial Septal Defect (ASD) he lua kūpono ʻole ia ma kēia paia.
E noʻonoʻo e pili ana i ia mea, aneane kēlā me kēia pēpē i hānau ʻia me kahi lua liʻiliʻi ma kēia paia. He mea maʻamau kēlā. Pani ʻia kēia lua ma kona iho i loko o kekahi mau pule a i ʻole mau mahina ma hope o ka hānau ʻana o ke pēpē. Akā i kekahi manawa, hiki i kēia lua ke nui iki aʻe, a i ʻole hiki ʻole ke pani iā ia iho. ʻO ia ka manawa a mākou e kapa ai iā ia he ASD.
Pono anei e pani ʻia kēia lua? ʻO wai ka mea e pono ai kēia lāʻau lapaʻau?
Inā liʻiliʻi loa ka lua, ʻaʻole paha e pilikia. ʻAʻole paha e pono ka mālama ʻana. Akā inā nui ka lua, hiki ke lilo i pilikia.
ʻO ka mea e hana ʻia ana, ma muli o kēia lua, hoʻomaka ke koko mai kekahi keʻena o ka puʻuwai e kahe i loko o ke keʻena kūpono ʻole. A laila pono ka puʻuwai a me nā māmā e hana ikaika ma mua o ka mea maʻamau. I ka hala ʻana o ka manawa, hiki i kēia ke alakaʻi i nā pilikia like ʻole.
ʻO ka mea nui loa, ʻo ia ka mālama ʻana i kēia ma mua o ka puka ʻana mai o nā pilikia. No laila, inā ʻōlelo kāu kauka i kēia ʻoki kino, mai makaʻu.
ʻO nā pilikia nui e hiki ke kū mai ma muli o kēia ʻano:
- Nā ʻano puʻuwai kūpono ʻole, i ʻike ʻia hoʻi ʻo nā kūlana `(Arrhythmia)`. No ka laʻana, `(Atrial Fibrillation)` a i ʻole `(Atrial Flutter)`.
- Ka hoʻonui ʻia ʻana o ka puʻuwai.
- Ka pilikia o ka hāʻule ʻana o ka puʻuwai.
- Ke koko kiʻekiʻe i loko o nā māmā (Pulmonary Hypertension).
- Paʻakikī ka hanu ʻana.
- Ka pilikia o ka hahau ʻana.
Inā ʻoe a i ʻole kāu keiki i ka pilikia o kēia mau pilikia, hiki i kāu kauka ke ʻōlelo aku e pani i ka lua (ASD Closure). Eia kekahi, inā ʻoe e hana ʻia ana i ke ʻoki no kekahi maʻi puʻuwai ʻē aʻe, hiki i kāu kauka ke hoʻoholo e pani i ka lua i ka manawa like. Hana pinepine ʻia kēia ʻoki ma nā keiki ʻōpio e pale aku i ka hōʻino ʻana o ka puʻuwai i ka wā e hiki mai ana.
Pehea e pani ai i ka lua? ʻElua mau ʻano nui!
ʻElua mau ʻano hana nui i hoʻohana ʻia e pani i kēia lua: ke ʻoki puʻuwai hāmama a me nā ʻano hana ʻoki ʻole me ka hoʻohana ʻana i kahi catheter. Na kāu kauka puʻuwai e hoʻoholo i ke ʻano hana kūpono loa no kou kūlana.
| ʻAno lapaʻau | Wehewehena |
|---|---|
| 1. ʻOki Puʻuwai Hāmama (Pani ʻoki) | Ma kēia, hana ʻia kahi ʻoki ma ka ʻāpana umauma, e komo pololei ana i ka puʻuwai a pani i ka lua. Hiki ke hoʻohana ʻia kahi ʻāpana hana, nā ʻiʻo ʻē aʻe mai ke kino, a i ʻole nā humuhumu e pani i ka lua. Hana ʻia kēia ma lalo o ka anesthesia laulā. |
| 2. Pani ʻana o ka Transcatheter | ʻAʻole pono kēia i kahi ʻoki nui. Hoʻokomo ʻia kahi ʻōmole lahilahi loa (catheter) ma o kahi kīʻaha koko ma ka ʻāpana groin i ka puʻuwai, a hoʻokomo ʻia kahi mea hana kūikawā (mea pani) ma o ia mea e pani ai i ka lua. He pōkole ka manawa ho'ōla, a ʻaʻohe ʻeha nui i koe. |
He mea hou aʻe e pili ana i ka pani ʻana o Transcatheter
Inā liʻiliʻi ka lua i loko o kou puʻuwai a ʻaʻohe ou maʻi puʻuwai ʻē aʻe, koho pinepine ʻia kēia ʻano hana. Ma kēia ʻano hana, ʻaʻole hiamoe loa ka mea maʻi. Hoʻohana ʻia ka hoʻomaha māmā. Hoʻohana ke kauka i kahi catheter i hoʻokomo ʻia ma o kahi ʻoki liʻiliʻi ma ka ʻūhā, nā X-ray a me ka "(Echocardiogram)" e alakaʻi i ka catheter i loko o ka puʻuwai. A laila, ua kau pono ʻia ka mea e pani ana i ka lua a ua wehe ʻia ka catheter. He wikiwiki loa ka hoʻōla ʻana ma kēia ʻano hana.
He aha ka mea e hana ʻia ma hope o ka lāʻau lapaʻau? Pehea ka lōʻihi e hoʻōla ai?
Ma muli o ka lāʻau lapaʻau āu e loaʻa ai, pono paha ʻoe e noho ma ka haukapila no hoʻokahi lā a ʻoi aku paha. E nānā pono ke kime lapaʻau iā ʻoe.
- Inā ua hana ʻia ʻoe i ke ʻoki hāmama , pono ʻoe e pale i nā hana ikaika e like me ka hāpai kaumaha no kekahi mau pule.
- Inā ua loaʻa iā ʻoe ke kaʻina hana catheter , hiki iā ʻoe ke hoʻi i kāu mau hana maʻamau i loko o hoʻokahi pule.
Ma hope o ka mālama ʻana, ka lāʻau lapaʻau e pale ai i nā ʻōpū koko no kahi o 6 mau mahinaPono ʻoe e lawe. Eia kekahi, ʻoiai inā ʻoe e mālama ana i nā niho, e aʻo aku kāu kauka iā ʻoe e lawe i nā antibiotics e pale aku i ka maʻi.
ʻO ka mea nui loa, ʻo ia ka hōʻoia ʻana e hele ʻoe i ke kauka i nā lā i hoʻonohonoho ʻia. Pono ʻoe e hana i kekahi mau hoʻokolohua, e like me ka "Echocardiogram" a me ka "Electrocardiogram - ECG", e ʻike ai inā ua holomua ka lāʻau lapaʻau.
Aia kekahi mau pilikia i kēia lāʻau lapaʻau?
E like me nā lāʻau lapaʻau āpau, aia kekahi mau pilikia liʻiliʻi. Eia nō naʻe, he lāʻau palekana a maikaʻi loa ia. ʻO nā pilikia hiki ke loaʻa:
- Nā maʻi ʻaleka i nā mea i hoʻohana ʻia i ka lāʻau lapaʻau.
- Nā ʻano like ʻole o ka puʻuwai (Arrhythmia).
- Ke kahe ʻana o ke koko.
- Ka hōʻino ʻana i nā ʻiʻo puʻuwai a i ʻole nā kīʻaha koko (he mea kākaʻikahi loa kēia).
- Ka maʻi a puni ka ʻoki a i ʻole ka mea hana i pani ai i ka lua.
- Hahau a i ʻole ka Hoʻouka Ischemic Kuikilana.
E kamaʻilio kāu kauka me ʻoe e pili ana i kēia mau pilikia. ʻAʻohe mea e hopohopo ai, ʻo ka hapa nui o ka manawa ʻaʻole kēia mau mea e hana ʻia.
I nā kūlana hea e pono ai ʻoe e ʻike koke i ke kauka?
Inā ʻike ʻoe i kekahi mau hōʻailona hōʻailona ma hope o kāu lāʻau lapaʻau, pono ʻoe e kāhea koke i kāu kauka a i ʻole e hele i ka Emergency Department (ETU) o ka haukapila kokoke loa.
| Nā hōʻailona hōʻike e makaʻala ai | |
|---|---|
| - Ke kahe ʻana o ke koko, ka pus, a i ʻole kekahi wai ʻē aʻe mai ka ʻoki. | - ʻEha ka umauma. |
| - Ka nalowale ʻana o ka ʻike a i ʻole ka huikau. | - Ke kuni. |
| - ʻAʻole e hoʻonui a emi paha ka ʻeha ʻoiai ke lawe nei i nā mea hoʻomaha ʻeha. | - Paʻakikī ka hanu ʻana. |
| - Nā loli i ke kuʻi ʻana o ka puʻuwai (manaʻo e like me ke kuʻi ʻana i ka umauma). | |
I ka hopena, he lāʻau koʻikoʻi loa ka ASD Closure e pale ana i ke olakino o ka puʻuwai a me nā māmā, e kōkua ana iā ʻoe a i ʻole kāu keiki e ola i ke ola lōʻihi a olakino.
Leka Lawe-Home
- ʻO kahi kīnā septal atrial (ASD) he lua ia ma ka paia ma waena o nā keʻena ʻelua o luna o ka puʻuwai.
- Ma muli o ke kaumaha o nā lua nui ma ka puʻuwai a me nā māmā, he mea nui e pani iā lākou e pale ai i nā pilikia e hiki mai ana.
- Aia nā ʻoki puʻuwai hāmama a me nā ʻano hana ʻoki ʻole e hoʻohana ana i kahi catheter e pani ai i kēia. Na kāu kauka e hoʻoholo i ke ʻano hana kūpono loa iā ʻoe.
- Ma hope o ka lāʻau lapaʻau, he mea nui loa e hahai pololei i nā ʻōlelo a ke kauka a hele i nā keʻena lapaʻau i nā lā i hoʻonohonoho ʻia.
- Hoʻonui kēia lāʻau i ka manaʻolana ola a kōkua nui i ke ola ʻana i kahi ola olakino.











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