Ke manaʻo nei ʻoe i kekahi manawa he pōkole iki ka hanu, he ʻūlū paha i loko o kou umauma? A i ʻole he ʻūlū kou i ʻoi aku ka ʻino i ke kakahiaka, a i ʻole ua luhi ʻoe? ʻAʻole paha kēia he mau hōʻailona o ke anu wale nō. He mau hōʻailona paha ia o kahi maʻi māmā i kapa ʻia ʻo Bullous Emphysema , kahi mea āu e hopohopo ai. No laila, e kamaʻilio kākou e pili ana i kēia me nā kikoʻī hou aku i kēia lā, me he mea lā e kamaʻilio ana ʻoe me kahi hoaaloha, ʻae?
He aha ka Bullous Emphysema?
I ka ʻōlelo maʻalahi, ʻo Bullous Emphysema kahi ʻano maʻi māmā i kapa ʻia ʻo emphysema . Hana ʻia ka emphysema i ka wā e hōʻino ʻia ai nā paia o nā ʻeke ea liʻiliʻi i loko o kou mau māmā, i kapa ʻia ʻo alveoli . E hoʻomanaʻo, ʻo kēia mau alveoli nā mea e hana i ka hana koʻikoʻi o ka lawe ʻana i ka oxygen a me ka hoʻokuʻu ʻana i ke kalapona dioxide i ka wā e hanu ai mākou.
I kēia manawa, i ka emphysema bullous, ʻo ka mea e hana ʻia, ʻo ia ka hōʻino ʻia ʻana o nā paia o kēlā mau alveoli, a pehu lākou a hana i nā ʻeke ea nui, e like me nā balloons. Kāhea mākou i kēia mau bullae . Hiki i kēia mau bullae ke ʻoi aku ka nui ma mua o hoʻokahi kenimika.
Ke hoʻokumu ʻia kēia cyst, hoʻopilikia ia i ka hiki o nā māmā ke hana pono. Lilo ia i mea paʻakikī no nā alveoli ke hoʻololi i ka oxygen a me ke kalapona ʻokikene. Hiki ke loaʻa kēia ʻano ma kekahi a i ʻole nā māmā ʻelua. Eia nō naʻe, inā hoʻokumu ʻia kēia cyst ma kekahi māmā, hiki iā ia ke hoʻopilikia i ka hiki o kekahi māmā ke pehu, ʻo ia hoʻi ka hanu ʻana. I kekahi manawa, inā nui loa kēia cyst, hiki i ka māmā ke hiolo, e hana ana i kahi ʻano i kapa ʻia ʻo Vanishing Lung Syndrome . ʻOiai hiki i kēia ke hōʻeha mau loa i nā māmā, hiki i ka mālama kūpono ke kāohi i kēia ʻano a hoʻonui i kou ola.
ʻO wai ka mea i ʻoi aku ka paʻakikī o ka loaʻa ʻana o kēia maʻi?
ʻO ka ʻoiaʻiʻo, hiki i kekahi ke loaʻa i ka bullous emphysema, me ka nānā ʻole i ka makahiki, ka lāhui, a i ʻole ke kāne. Eia nō naʻe, pili pinepine ia me ka maʻi pulmonary obstructive chronic (COPD) , kahi maʻi māmā i hoʻokumu ʻia e ka puhipaka. Eia kekahi, inā loaʻa iā ʻoe kekahi mau kūlana genetic, ʻoi aku ka kiʻekiʻe o kou pilikia. Eia kekahi laʻana:
- Ka hemahema o ka Alpha-1 antitrypsin
- ʻO ka maʻi ʻo Ehlers-Danlos
- ʻO ka maʻi Marfan
Eia kekahi, ʻo ka poʻe i loaʻa i ka Human Immunodeficiency Virus (HIV) e pilikia nui ana hoʻi i ka hoʻomohala ʻana i ka bullous emphysema.
Pehea ka maʻamau o kēia? No ke aha e hana ʻia ai kēia?
Ma ka honua holoʻokoʻa, ʻoi aku ma mua o 5% o ka heluna kanaka a ʻoi aku ma mua o 12% o nā pākeke ma luna o 30 mau makahiki i hōʻike ʻia he bullous emphysema. ʻO ia kekahi ke kumu nui ʻekolu o ka make ma nā ʻāina e like me ʻAmelika Hui Pū ʻIa. No laila, ʻaʻole kēia he mea e lawe māmā ʻia.
I kēia manawa, e nānā kākou i ke kumu o kēia hana.
ʻO ke kumu nui o ka emphysema bullous ka puhipaka . ʻO ka mumū mau i hoʻokumu ʻia e ka uahi o ka cigarette e hōʻino i nā paia o kou alveoli. Hoʻonui kēia i nā ʻeke ea, e ālai ana i ka neʻe ʻana o ka oxygen a me ke kalapona ʻokikene.
Ma waho aʻe o ka puhi paka, aia kekahi mau kumu ʻē aʻe:
- Ka puhi ʻana i ka cocaine crack a i ʻole ka mariuana.
- Ka hoʻohana ʻana i ka lāʻau lapaʻau intravenous.
- Hiki i nā kūlana genetic i ʻōlelo ʻia ma luna nei ke hana i nā paia alveolar e lilo i mea nāwaliwali a hōʻino ʻia, e alakaʻi ana i ka bullous emphysema.
He aha nā hōʻailona o kēia?
ʻO ka hōʻailona nui a maʻamau o ka bullous emphysema ka pōkole o ka hanu . ʻO ke ʻano kēia, ua pōkole kou hanu, ʻaʻole wale i ka wā e luhi iki ai ʻoe, i ka wā e piʻi ai i ke alapiʻi, akā i kekahi manawa ʻoiai ʻoe e kū mālie ana.
Aia kekahi mau hōʻailona maʻamau ʻē aʻe:
- Manaʻo o ka ʻeha o ka umauma a i ʻole ka ʻūmiʻi.
- Loaʻa ka ʻū (ʻoi aku ka ʻino o kēia i ke kakahiaka).
- Manaʻo luhi a luhi mau i nā manawa a pau (Fatigue).
- ʻAʻohe ʻono o ka meaʻai.
- Ka luaʻi.
- Pilikia ka hanu ʻana.
Eia nō naʻe, loaʻa paha i kekahi poʻe ka bullous emphysema akā ʻaʻole hōʻike i kekahi mau hōʻailona. Inā lilo nā bullae i mea nui loa, kapa mākou iā lākou he mau bullae nunui , a laila e ʻoi aku ka koʻikoʻi o nā hōʻailona.
Ke ʻike ʻoe i ke kauka, e ʻimi ʻo ia i nā hōʻailona e like me kēia i kou nānā ʻana iā ʻoe:
- He umauma ʻano barela.
- Nā manamana lima i hoʻopaʻa ʻia.
- Ke lohe nui nei i kou puʻuwai ma muli o ke koko kiʻekiʻe o ka pulmonary.
- Pehu (Edema).
- Hanu ʻū.
Pehea ʻoe e ʻike pono ai i kēia?
E nīnau mua kāu kauka iā ʻoe e pili ana i kāu mau hōʻailona, kou mōʻaukala olakino, a inā paha ua loaʻa i kekahi o kou ʻohana nā kūlana like. A laila e hana lākou i kahi hoʻokolokolo kino.
Inā kānalua ʻia ka emphysema bullous, e kauoha kāu kauka i ka hoʻāʻo ʻana i ka hana pulmonary (PFT) . Nānā kēia mau hoʻokolohua i ka maikaʻi o ka neʻe ʻana o kou mau māmā i ka ea a inā paha e ālai ana nā bullae i ke kahe o ka ea.
Ma ke ʻano he ʻāpana o kēia mau hoʻokolohua, ʻo ka spirometryHiki iā ʻoe ke hoʻāʻo ʻia. Pili kēia i kou hanu ʻana ma o kahi ʻōmole i loko o kahi mīkini (spirometer). Ana kēia i ka nui o ka ea e neʻe ana i loko a i waho o kou mau māmā ke hanu ʻoe i loko a i waho.
Eia kekahi, hiki i kāu kauka ke kuhikuhi i nā hoʻokolohua kiʻi e nānā i nā alveoli i hoʻonui ʻia a hōʻino ʻia paha. Hiki i kēia mau mea ke komo pū me:
- ʻO X-ray umauma: Hiki i kēia ke kōkua i ka hoʻoholo ʻana inā he mau bullae a me ko lākou wahi i loko o nā māmā.
- CT scan: Hiki i kēia ke kōkua i ka hoʻoholo ʻana i ka wahi kikoʻī, ka helu, a me ka nui o ka cyst.
Hiki ke hāpai ʻia nā hoʻokolohua ʻē aʻe, no ka laʻana:
- Nā hoʻāʻo koko: E nānā i ka hōʻiliʻili ʻana o ke kalapona ʻokikene i loko o nā māmā, e hoʻolilo ana i ke koko i waikawa (ua kapa ʻia kēia he acidosis respiratory ), a i ʻole nā pae oxygen haʻahaʻa.
- Helu koko piha (CBC): Nānā i nā pae hemoglobin haʻahaʻa.
- Electrocardiogram (EKG): No ka nānā ʻana i nā hopena o ka puʻuwai i hoʻokumu ʻia e ka maʻi māmā, e like me ka hypertrophy ventricular ʻākau a i ʻole ka hoʻonui ʻia ʻana o ka atrial ʻākau.
Hiki i kāu kauka ke nānā inā loaʻa iā ʻoe ka hemahema o Alpha-1 antitrypsin ma o nā hoʻāʻo koko.
Aia kekahi lāʻau lapaʻau piha no kēia?
ʻO ka mea pōʻino, ʻaʻohe lāʻau lapaʻau no ka bullous emphysema. ʻO ke ʻano kēia, ke ulu aʻe, ʻaʻole hiki ke hoʻohuli ʻia. Akā, mai hopohopo! Aia nā lāʻau lapaʻau e hiki ke kōkua iā ʻoe e ola me nā hōʻailona a pale i ka maʻi mai ka ʻino ʻana.
No laila he aha nā lāʻau lapaʻau?
I mea e kōkua ai i ka kaohi ʻana i kāu mau hōʻailona, hiki i kāu kauka ke kuhikuhi i nā lāʻau lapaʻau i kapa ʻia ʻo bronchodilators . Hoʻomoʻa pinepine ʻia kēia mau mea ma o kahi inhaler . Hana nā Bronchodilators ma ka hoʻomaha ʻana i nā ʻiʻo i loko o kou mau ala ea, e maʻalahi ai ka ea e hele i loko o kou mau māmā, a me ka hōʻemi ʻana i ka pōkole o ka hanu.
E noʻonoʻo, hana kēia mau lāʻau lapaʻau e like me ka hoʻonui iki ʻana i kahi alanui paʻapū, e maʻalahi ai ka hele ʻana o nā kaʻa.
Inā loaʻa iā ʻoe nā hōʻailona koʻikoʻi a i ʻole kahi maʻi māmā, hiki ke hāʻawi ʻia iā ʻoe nā antibiotics a i ʻole corticosteroids no kahi manawa pōkole.
Inā haʻahaʻa kou pae oxygen, hiki i kāu kauka ke kuhikuhi i ka lāʻau lapaʻau oxygen hou , ʻo ia hoʻi ka hāʻawi ʻana i kou kino i ka oxygen keu ma o kahi ʻōmole i kau ʻia i loko o kou mau puka ihu a i ʻole kahi pale maka i kau ʻia ma kou alo.
I kekahi manawa, ʻoiai ke ʻōlelo ʻoe i kēlāInā he mau bullae nunui, inā paʻakikī loa ka hanu ʻana, a inā he mau pilikia ʻē aʻe ma muli o kēia maʻi, no ka laʻana:
- Pūmāmā hiolo (Pneumothorax)
- Ke ʻū ʻana i ke koko (Hemoptysis)
- Nā maʻi puʻupaʻa
Inā hana ʻia nā mea e like me kēia, pono paha ʻoe i ke ʻoki ʻana.
Nā ʻano hana no ka emphysema bullous:
- Bullectomy: Ma kēia kaʻina hana, wehe ke kauka lapaʻau i ka bulla (ʻeke ea) mai kou māmā. Hiki ke hana ʻia kēia ma ke ʻano he ʻoki hāmama (Thoracotomy) a i ʻole he kaʻina hana minimally invasive (Video-assisted thoracic surgery - VATS).
- Ka hoʻemi ʻana o ka nui o ka māmā Bronchoscopic (BLVR): Ma kēia kaʻina hana minimally invasive, hoʻokomo ke kauka lapaʻau i kahi valve i loko o kou māmā a hoʻemi pono i kahi ʻāpana o ka māmā.
- ʻO ke ʻoki hoʻemi nui o ka māmā (LVRS): Ma kēia, wehe ke kauka ʻoki i ka ʻiʻo māmā i hōʻino ʻia i hiki ai i ke kino i koe ke hana maikaʻi.
Inā ʻaʻohe o kēia mau lāʻau lapaʻau e holo pono, a inā kūpono, hiki i kāu kauka ke kuhikuhi iā ʻoe no kahi hoʻoili māmā .
Pehea e hiki ai ke hoʻēmi ʻia kēia pilikia?
ʻO ka mea maikaʻi loa hiki iā ʻoe ke hana e hōʻemi i kou pilikia o ka loaʻa ʻana o ka bullous emphysema, ʻo ia ka puhi ʻole ʻana, a inā ʻoe e puhipaka ana, e haʻalele. E kamaʻilio me kāu kauka e pili ana i nā ala e kōkua ai iā ʻoe e haʻalele i ka puhipaka. Ua ʻike mākou ʻaʻole ia he mea maʻalahi, akā he mea kūpono ia no ke olakino o kou mau māmā.
He aha kāu e manaʻo ai i ka wā e noho ai me kēia maʻi?
He maʻi olakino ola ka bullous emphysema. ʻO ke ʻano kēia, i ka wā e hōʻino ʻia ai kou mau māmā, ʻaʻole loa lākou e ola piha. Eia nō naʻe, ʻo ka wikiwiki o kou hoʻomaka ʻana i ka lāʻau lapaʻau, ʻo ka nui o kou hiki ke pale i ka ʻino ʻana o ke ʻano. No laila, he mea nui e ʻimi koke i ke kōkua lapaʻau inā loaʻa iā ʻoe nā hōʻailona.
Pehea wau e mālama ai iaʻu iho?
Hiki iā ʻoe ke hoʻokele i kāu mau hōʻailona a ola maikaʻi. ʻO ka loaʻa ʻana o ka lāʻau kūpono nou hiki ke hoʻomaikaʻi nui i kou ʻano ola.
He mea nui hoʻi e noho olakino a pale i nā pilikia olakino koʻikoʻi. No laila, e kamaʻilio me kāu kauka e pili ana i nā ʻano lāʻau pale āu e pono ai, e like me ka lāʻau pale maʻi flu, ka lāʻau pale COVID, a me ka lāʻau pale Pneumococcus .
I ka manawa hea e pono ai iaʻu ke ʻike i ke kauka?
Inā ʻike ʻoe i kekahi mau hōʻailona o ka emphysema bullous, a inā paha e loaʻa iā ʻoe nā hōʻailona hou, e ʻike pono i ke kauka.
Inā loaʻa iā ʻoe nā hōʻailona ma lalo nei, he mea nui e ʻimi koke i ke kōkua lapaʻau:
- He kala polū a hina paha i kou mau lehelehe a i ʻole nā manamana lima (cyanosis).
- Ka paʻakikī e noho makaʻala noʻonoʻo.
- Ke piʻi nei ka paʻakikī o ka hanu ʻana.
- Ka wikiwiki o ka puʻuwai (Tachycardia).
Hiki i ka hanu ʻole ke lilo i mea weliweli. Inā loaʻa iā ʻoe ka bullous emphysema, manaʻo paha ʻoe e hakakā mau ana ʻoe i ka hanu ʻana. E hoʻomanaʻo, ʻo ka puhipaka ke kumu nui. Eia kekahi, hiki i kekahi mau kūlana genetic ke hoʻonui i kou pilikia. ʻO ka haʻalele ʻana i ka puhipaka ka mea maikaʻi loa hiki iā ʻoe ke hana e pale aku i ka bullous emphysema mai ka ʻino ʻana. Hiki i kāu kauka ke kuhikuhi i nā lāʻau lapaʻau e hiki ke kōkua iā ʻoe e hanu maʻalahi a hoʻolilo i kou ola o kēlā me kēia lā i mea maʻalahi.
E hoʻomanaʻo i ka mea nui loa (Leka Lawe-Home)
ʻAe, eia kekahi o nā mea nui a mākou i kamaʻilio ai i kēia lā e kōkua iā ʻoe e hoʻomanaʻo:
- ʻO ka emphysema bullous kahi kūlana i hōʻino ʻia ai nā ʻeke ea i loko o nā māmā a hana ʻia nā ʻeke ea nui (bullae).
- ʻO ka puhipaka ke kumu nui o kēia, no laila he mea nui loa ka pale ʻana i ka puhipaka.
- Inā loaʻa iā ʻoe nā hōʻailona e like me ka paʻakikī o ka hanu ʻana, ke kuʻi mau, a i ʻole ka ʻeha o ka umauma, e ʻimi pono i ke kōkua lapaʻau.
- ʻOiai ʻaʻohe lāʻau lapaʻau piha no kēia, aia nā lāʻau lapaʻau kūpono e kaohi i nā hōʻailona a pale i ka maʻi mai ka ʻoi aku ka ʻino.
- Hiki i ka ʻike mua ʻana a me ka mālama ʻana ke hoʻomaikaʻi i kou ola maikaʻi.
No laila, inā loaʻa iā ʻoe a i ʻole kekahi āu i ʻike ai kēia mau hōʻailona, mai hopohopo a e ʻike i ke kauka no ka ʻōlelo aʻo. E noho olakino!
ʻO ka emphysema bullous, ka maʻi māmā, ka pilikia hanu, ka puhipaka, COPD, bullae, alveoli











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