Ua ʻike paha ʻoe i kahi ʻeha ʻōpū i kāu keiki liʻiliʻi, a i ʻole he puʻupuʻu ma ka ʻāʻī a i ʻole ka lima, a ua hopohopo iki paha ʻoe. ʻO ka hapa nui o ka manawa, he mea maʻamau kēia. Eia nō naʻe, aia kekahi ʻano maʻi kanesa kakaikahi loa e hiki ke laha koke i loko o ke kino . ʻO ia ka mea a mākou e kamaʻilio ai i kēia lā. Ua kapa ʻia ʻo Burkitt Lymphoma. Mai makaʻu i kou lohe ʻana i ka inoa, no ka mea, ʻo ka mea nui loa, ʻo ia ka ʻike pono e pili ana i ia mea.
He aha maoli ka Burkitt Lymphoma?
I ka ʻōlelo maʻalahi, ʻo Burkitt lymphoma kahi maʻi kanesa e ulu wikiwiki ana i loko o nā cell-B , kahi ʻano o ke koko keʻokeʻo i loko o ko mākou kino. No ka hui o nā maʻi kanesa i kapa ʻia ʻo lymphoma, a he ʻano lymphoma non-Hodgkin . ʻIke pinepine ʻia i nā keiki ʻōpio a me nā mākua ʻōpio. Kapa pū kekahi poʻe iā ia ʻo ka maʻi Burkitt, ka lymphoma Burkitt, a i ʻole ka puʻupuʻu Burkitt.
Hoʻomaka pinepine ia ma nā lymph nodes i loko o kou ʻōpū a i ʻole pelvis. Akā hiki iā ia ke laha koke i nā ʻāpana ʻē aʻe o kou kino, e like me:
- ʻŌpū (wahi ʻōpū)
- ʻIwi iwi
- ʻAla ʻōpū
- ʻĀpana ʻauwae
- ʻŌpū
- ʻĀʻī
- Nā ʻōpū tonsil
Ma muli o ka wikiwiki o kona holomua ʻana, hiki i kekahi manawa ke hoʻoweliweli i ke ola. Akā ʻo ka mea maikaʻi loa, inā hoʻomaka mua ʻia ka lāʻau lapaʻau, hiki ke ho'ōla loa ʻia ka hapa nui o ka poʻe . ʻO ia hoʻi, e nalowale nā hōʻailona a hiki iā ʻoe ke noho olakino me ka ʻole o ka hoʻi hou ʻana mai. Kāhea mākou i kēia e hele ana i ke 'hoʻomaha lōʻihi'.
He aha nā ʻano nui o ka Burkitt Lymphoma?
ʻEkolu mau ʻano nui o kēia:
1. ʻAno Endemic: ʻO kēia ka mea maʻamau ma nā ʻāpana o ʻApelika. Ua ʻike ʻia ua pili ia me kahi maʻi i kapa ʻia ʻo Epstein-Barr virus (EBV) .
2. ʻAno sporadic: ʻIke ʻia kēia ma nā ʻāina e like me ʻAmelika Hui Pū ʻIa, ʻoi aku hoʻi i waena o nā kamaliʻi ʻōpio. ʻOi aku ma mua o 40% o ka lymphoma non-Hodgkin i nā keiki kēia ʻano.
3. Pili i ka pale ʻana i ka maʻi: Hana ʻia kēia i nā poʻe i nāwaliwali ko lākou ʻōnaehana pale, ma muli paha o nā maʻi e like me ka HIV/AIDS a i ʻole nā kumu ʻē aʻe.
Pehea ka maʻamau o kēia? ʻO wai ka mea i loaʻa pinepine?
He maʻi kanesa laha ʻole ka maʻi lymphoma ʻo Burkitt. No ka laʻana, ma ʻAmelika Hui Pū ʻIa, ʻike ʻia ke ʻano sporadic ma kahi o ʻehā o kēlā me kēia miliona mau keiki ma lalo o ka makahiki 16. ʻO ia ka helu ma waena o 1% a me 2% o nā lymphoma āpau i nā pākeke.
ʻO kēia ka mea maʻamau i waena o nā keiki ʻōpio , ma waena o nā makahiki 3 a me 12.
He aha nā hōʻailona? Pehea ʻoe e ʻike ai i kēia?
Hiki ke ʻike koke ʻia nā hōʻailona. ʻO lākou kekahi:
- ʻEha ʻōpū, nausea, luaʻi
- Kuni, malaise, hou o ka pō
- Ka nalowale o ka makemake a me ka pohō kaumaha i manaʻo ʻole ʻia
- Nā ʻōpū lymph pehu (hiki ke ʻike ʻia he mau puʻupuʻu ma nā wahi e like me ka ʻāʻī, nā armpits, a me ka ʻūhā)
E noʻonoʻo ua hoʻopiʻi kāu keiki i ka ʻeha ʻōpū no kekahi mau lā, ʻaʻole hiki iā ia ke ʻai, a ke hou nui nei ʻo ia i ka pō. Manaʻo paha ʻoe he kuni viral maʻamau kēia. Akā inā e ʻoi aʻe kēia mau hōʻailona i kēlā me kēia lā, pono ʻoe e ʻike i ke kauka. No ka mea, hiki i nā ʻōpū lymphoma Burkitt ke pālua i ka nui i loko o kekahi mau lā wale nō. ʻO ia ke kumu he mea nui e hana wikiwiki.
No ke aha i loaʻa ai kēia maʻi? He aha nā kumu?
ʻAʻole maopopo loa i nā kauka ke kumu o ka lymphoma Burkitt. Eia nō naʻe, ua ʻike lākou ua pili ia i nā loli i loko o kahi gene i kapa ʻia ʻo MYC, ka mea e kāohi ana i ka ulu ʻana o kā mākou mau cell. Hiki i kēia gene MYC ke lilo i overactive ma muli o kahi kīnā genetic kūikawā i kapa ʻia ʻo translocation .
Ma Sri Lanka, e like me nā ʻāina ʻē aʻe a puni ka honua, loaʻa i kekahi poʻe i loaʻa i ka maʻi Epstein-Barr (EBV) ka lymphoma Burkitt. Eia nō naʻe, he mea nui e hoʻomanaʻo ʻaʻole e loaʻa i nā kānaka a pau i loaʻa i ka EBV kēia maʻi kanesa.
He aha nā pilikia e hiki ke kū mai mai kēia maʻi?
Hiki i kēia maʻi kanesa ke hana i kekahi mau pilikia, e like me:
- Ka emi ʻana o ka helu o nā hunaola koko (anemia, helu o nā hunaola koko keʻokeʻo, helu o nā platelet). Pono paha kēia i ka hoʻoili koko.
- ʻO ka Tumor Lysis Syndrome : He kūlana pilikia kēia kahi e hoʻopilikia ʻia ai ke kaulike kemika o ke kino e ka hoʻokuʻu ʻia ʻana o nā mea mai nā hunaola kanesa i ko lākou make koke ʻana.
- Ka nāwaliwali o ke kūpaʻa ʻole (maʻalahi ke loaʻa i ka maʻi).
Inā pilikia ʻoe a i ʻole kāu keiki i ka kaohi ʻana i kēia mau hōʻailona, e haʻi koke aku i kāu kauka.
Pehea e hoʻomaopopo pono ai nā kauka i kēia?
No ka ʻike pono ʻana inā he Burkitt Lymphoma kou, e hana mua paha kāu kauka i kahi biopsy lymph node , ʻo ia hoʻi ka lawe ʻana i kahi hāpana liʻiliʻi o kahi lymph node pehu a nānā iā ia ma lalo o kahi microscope.
Eia kekahi, hiki ke hana ʻia nā hoʻokolohua aʻe:
- CT scan: No ka nānā ʻana i nā ʻōpū ma ka umauma, ka ʻōpū, a me ka ʻāpana pelvic.
- Nānā PET: Hōʻike kikoʻī kēia scan i nā wahi o ke kino kahi i loaʻa ai ka maʻi kanesa.
- ʻO ka biopsy iwi: No ka ʻike ʻana inā ua pālahalaha ke kanesa i ka iwi.
- ʻUku lumbar: No ka nānā ʻana i nā hunaola kanesa i loko o ke kinowai i loko o ke kaula kuamoʻo.
Pehea e hoʻoholo ʻia ai nā pae o ka maʻi kanesa?
Hoʻohana nā kauka i kēia mau pae e ʻike ai i ka mamao o ka laha ʻana o ke kanesa:
- Pae I (1): Aia ke kanesa ma kahi hoʻokahi wale nō, a i ʻole ma hoʻokahi wale nō lymph node.
- Pae II (2): Aia ke kanesa ma ʻelua a ʻoi aku paha mau wahi ma ka ʻaoʻao like o ka diaphragm , kahi ʻiʻo e kōkua iā mākou e hanu.
- Pae III (3): Aia ke kanesa ma nā ʻaoʻao ʻelua o ka diaphragm.
- Pae IV (4): Ua pālahalaha ke kanesa ma waho o ka ʻōnaehana lymphatic, i nā wahi e like me ke akepaʻa, nā māmā, a me ka iwi iwi.
He aha nā lāʻau lapaʻau?
Ma muli o ka laha wikiwiki ʻana o ka Burkitt Lymphoma, pono e hoʻomaka koke ʻia ka lāʻau lapaʻau. ʻO nā koho lapaʻau nui i loaʻa:
- Kemoterapia: ʻO kēia ka lāʻau lapaʻau nui. ʻO ka hapa nui, hāʻawi ʻia ka chemotherapy ikaika loa, a hoʻomaka ʻia i ka wā e ʻike ʻia ai ka maʻi.
- Immunotherapy: Hana kēia ma ke kōkua ʻana i ka ʻōnaehana pale ponoʻī o kou kino e ʻimi a luku i nā hunaola kanesa.
- Lapaʻau radiation: I kekahi manawa hoʻohana ʻia me ka chemotherapy, akā hāʻawi pinepine ʻia i nā pākeke.
- Hoʻoili pūnaewele kumu: Hiki i kēia ke kōkua inā hoʻi mai ke kanesa ma hope o ka mālama ʻana.
- ʻO ke ʻoki kino: Hoʻohana pinepine ʻole ʻia kēia. No ka laʻana, i nā hihia kahi e ālai ai kahi puʻupuʻu i nā ʻōpū.
Āhea ʻoe e pono ai e ʻike i ke kauka?
E hoʻonohonoho kāu kauka i nā hoʻokolohua e nānā i kou olakino. I loko o kēia mau manawa, hiki iā ia ke hana i nā hoʻokolohua koko a me nā scan CT.
Inā loaʻa iā ʻoe a i kāu keiki paha kekahi o kēia mau hōʻailona, e ʻike koke i ke kauka :
- ʻEha umauma a paʻakikī paha ka hanu ʻana
- Inā ʻoi aku ke kuni ma mua o 38 kekelē Celsius (100.4 Fahrenheit)
- Ke kahe koko ʻana o ka ihu a i ʻole ke kahe ʻana o nā ʻāʻī
- ʻEha mau
- ʻIli keʻokeʻo a i ʻole ka palapū maʻalahi
He aha nā nīnau āu e nīnau ai i ke kauka?
Ke ʻike ʻoe he Burkitt Lymphoma kou a i ʻole kāu keiki, makemake paha ʻoe e nīnau i kāu kauka e like me kēia:
- Aia i hea ke kanesa?
- I ke kahua hea kēia?
- He aha ka lāʻau lapaʻau āu e paipai nei?
- E hiki anei iaʻu/kaʻu keiki ke hele i ka hana/kula?
- Pono ʻoe e hana i nā hoʻokolohua hou aʻe?
- He aha kā mākou e manaʻo ai no ka wā e hiki mai ana (nānā)?
He aha kāu e manaʻo ai inā loaʻa iā ʻoe ka Burkitt Lymphoma?
ʻO ka Burkitt Lymphoma kahi maʻi ʻaʻai e hiki ke ho'ōla ʻia i ka hapanui o nā hihia.. Pane maikaʻi ia i ka lāʻau lapaʻau, ʻoi aku hoʻi i waena o nā kamaliʻi ʻōpio a me nā mākua ʻōpio. Hoʻomanawanui maikaʻi nā keiki i ka chemotherapy ma mua o nā pākeke. Loaʻa paha i nā pākeke nā pilikia olakino ʻē aʻe, no laila ʻoi aku ka paʻakikī o ka lāʻau lapaʻau.
He aha ka helu ho'ōla?
ʻOiai he maʻi koʻikoʻi a laha wikiwiki ka Burkitt Lymphoma, pane maikaʻi ka hapa nui o ka poʻe i ka lāʻau lapaʻau. ʻO ka awelika o ka ola ola penei:
- Ke kahua mua: ʻOi aku ma mua o 90% o nā keiki e ho'ōla i ka wā lōʻihi.
- I nā keiki i ke kahua holomua: Ma waena o 80% a me 90% e ho'ōla hou ana.
- Nā mākua: Ua nalo aku ma mua o 50% o nā hōʻailona ma hope o ka mālama ʻana ('remission').
He mau helu awelika wale nō kēia. ʻOkoʻa paha kou kūlana. No laila, e kamaʻilio me kāu kauka e aʻo hou e pili ana i kou kūlana ponoʻī. Mai makaʻu, he mea nui loa ka wiwo ʻole.
He aha kekahi mau mea hiki iā ʻoe ke hana? (Nā ʻōlelo aʻoaʻo no ka mālama ponoʻī)
Hiki ke paʻakikī iki ka manawa lapaʻau, akā aia kekahi mau mea e hiki ke kōkua iā ʻoe e hoʻomanawanui:
- E ʻimi i ke kākoʻo: ʻO ke kamaʻilio ʻana me nā poʻe i loaʻa i nā ʻike like hiki ke lilo i kumu ikaika nui. Aia nā hui kākoʻo kahi e hiki ai i nā poʻe e like me ʻoe ke loaʻa ke kākoʻo.
- E hoʻomaha nui: E hāʻawi i kou kino i ka manawa e ho'ōla ai.
- ʻAi maikaʻi: E ʻimi i ka ʻōlelo aʻo mai kahi meaʻai meaʻai a ʻai i nā meaʻai e hāʻawi i kou kino i ka ikehu i ka wā o ka mālama ʻana.
- E hoʻolālā i mua: E nīnau i kāu kauka i ka mea e manaʻo ai.
- E kiʻi i ke kōkua mai ka poʻe aloha: Ua mākaukau ka ʻohana a me nā hoaaloha e kōkua iā ʻoe.
- E kākoʻo i kāu keiki: Aia nā loea e hiki ke kōkua i nā keiki e hoʻoponopono i ka ʻaoʻao naʻau o kēia maʻi (e laʻa, he loea ola keiki).
ʻO ka mea hope loa, nā mea e hoʻomanaʻo ai
He mea maʻamau ke kaumaha a hopohopo ke ʻike ʻoe ua loaʻa iā ʻoe a i ʻole kāu keiki ka Burkitt Lymphoma. Nui paha kāu mau nīnau a me nā makaʻu. Akā, ʻaʻole ʻoe hoʻokahi.
ʻOiai ke pālahalaha koke nei kēia maʻi ʻaʻai, he kūpono loa nā koho lapaʻau. E hoʻomaka koke kāu hui lapaʻau i ka lāʻau a kākoʻo iā ʻoe i kēlā me kēia ʻanuʻu o ke ala. No laila, he mea nui loa ka noʻonoʻo maikaʻi a hahai i nā ʻōlelo aʻoaʻo a kāu mau kauka.
ʻO Burkitt lymphoma, maʻi ʻaʻai, maʻi ʻaʻai kamaliʻi, lymphoma, nā hōʻailona, lāʻau lapaʻau, nā pūnaewele B











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