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Ke ulu nei ʻoe i nā ʻeha ʻeha ma kou ʻili? Hiki paha iā Calciphylaxis!

Ke ulu nei ʻoe i nā ʻeha ʻeha ma kou ʻili? Hiki paha iā Calciphylaxis!

Ua lohe paha ʻoe i kahi maʻi i kapa ʻia ʻo Calciphylaxis? He mea ʻē paha ke kani ʻana o ka inoa. Akā, he ʻano laha ʻole ia, he ʻeha loa, a i kekahi manawa he mea hoʻoweliweli i ke ola. ʻO ka mea e hana ʻia ana, ʻo ia ka hōʻiliʻili ʻana o nā waihona calcium i loko o nā kīʻaha koko liʻiliʻi i loko o kou kino, e ālai ana iā lākou. Ke hana ʻia kēlā, hoʻōki ia i ke kahe ʻana o ke koko a hoʻomaka kou ʻili a me nā ʻiʻo ma lalo e make. Ua like ia me kahi mea kanu e mae ana ke loaʻa ʻole ka wai lawa.

He aha ka Calciphylaxis? E hoʻomaopopo maʻalahi kākou!

I ka ʻōlelo maʻalahi, ʻo Calciphylaxis kahi kūlana kahi e hōʻiliʻili ai nā waihona calcium i loko o kou mau kīʻaha koko, e ālai ana i ke kahe koko a make ai ka ʻili a me nā ʻiʻo ma lalo. E like me ka paipu wai e paʻa ana i ka lepo a pau ke kahe ʻana o ka wai, hōʻiliʻili nā waihona calcium i loko o nā kīʻaha koko liʻiliʻi i loko o ko kākou kino.

ʻO ka hapa pinepine, loaʻa kēia mau waihona calcium i loko o nā kīʻaha koko e hoʻolako ana i ke koko i ka ʻili a me nā ʻiʻo ma lalo o ka ʻili. Eia nō naʻe, he mea kakaikahi loa, hiki i kēia mau waihona calcium ke loaʻa i loko o nā ʻōpū i loko o ke kino, e like me nā maka, nā māmā, ka lolo, nā ʻiʻo, a me nā ʻōpū.

Ke hoʻopilikia kēia ʻano i ka ʻili, hiki ke ʻeha loa . Hiki i ka ʻāpana i hoʻopilikia ʻia ke wehe a hana i kahi ʻeha, e like me ka ʻeha moe. I ka make ʻana o ka ʻili a me nā ʻiʻo a puni ka ʻeha, hiki ke laha ka pōʻino. He lōʻihi ka manawa e ho'ōla ai nā ʻeha Calciphylaxis, a hiki ke alakaʻi i nā pilikia koʻikoʻi.

Inā loaʻa kēia ʻeha i ka maʻi, e laha ka maʻi ma ke kino a hoʻomaka kā mākou ʻōnaehana pale e pane nui. Kāhea mākou i kēia he sepsis . ʻO kēia ka pilikia weliweli loa a make o Calciphylaxis.

Aia kekahi mau ʻano o Calciphylaxis?

ʻAe, ʻelua ʻano nui o ka calciphylaxis, ma muli o ke ʻano o kona ulu ʻana.

1. Ka hoʻokalakikia uremic

ʻO kēia ke ʻano maʻamau . Loaʻa pinepine ia i nā poʻe e dialysis ma muli o ka maʻi puʻupaʻa hope loa (ESKD). ʻO ke ʻano kēia, ʻaʻole hana pono ko lākou mau puʻupaʻa a pono lākou e hoʻopili ʻia i kahi mīkini dialysis e wehe i nā huahana ʻōpala mai ko lākou koko.

2. Calciphylaxis ʻole-uremic

He mea kākaʻikahi loa kēia ʻano. Hiki ke loaʻa i nā poʻe i nā pae mua o ka maʻi puʻupaʻa, i nā poʻe i hōʻino ʻia i kekahi a i ʻole nā ​​puʻupaʻa ʻelua, a i ʻole (kākaʻikahi loa) i nā poʻe ʻaʻohe pilikia puʻupaʻa.

Pehea ka maʻamau o kēia ʻano?

He maʻi laha ʻole ʻo Calciphylaxis.Ma waena o ka poʻe ma ka dialysis, hana ʻia kēia ma kahi o 35 o 10,000 poʻe (ma kahi o hoʻokahi hapakolu o 1%). No ka laʻana, ma ʻAmelika Hui Pū ʻIa, aia ma mua o 1.5 miliona mau kānaka ma ka dialysis, no laila ua hōʻike ʻia ma kahi o 2,000 mau hihia o ka calciphylaxis i kēlā me kēia makahiki. ʻOi aku ka kakaikahi o ke ʻano ma nā ʻāina me ka haʻahaʻa o ka maʻi puʻupaʻa.

Akā, he mea kupanaha, ʻoi aku ka nui o ka pilikia o nā wāhine i ka loaʻa ʻana o kēia maʻi . ʻOi aku ka pālua o ka hiki i nā wāhine ke loaʻa iā ia ma mua o nā kāne.

He aha nā hōʻailona o kēia?

ʻO nā hōʻailona o Calciphylaxis:

  • ʻEha nui: He ʻano ʻeha loa kēia i nā manawa a pau. Hiki ke hoʻomaka ka ʻeha ma mua o ka ʻike ʻia ʻana o kekahi hōʻailona ʻeha a i ʻole nā ​​​​pōʻino ʻē aʻe. Hiki i ka ʻāpana i hoʻopilikia ʻia ke lilo i mea maʻalahi i ke kaomi a i ʻole ka hoʻopā ʻana, e hoʻonui ai i ka ʻeha.
  • Nā loli ʻili (nā pae mua): ʻO kēia nā wahi o ka ʻili e ʻulaʻula, poni, ʻeleʻele, a ʻeleʻele paha. ʻIke pinepine ʻia kēia mau loli e like me ka ʻupena. Aia paha he mau pehu, a hiki i ka ʻili i hoʻopilikia ʻia ke lilo i mānoanoa a ʻili.
  • Nā ʻeha a me nā ʻōpū (pae hope): ʻO ka maʻamau, lilo nā loli ʻili i mau ʻeha, e pālahalaha ana ma ke ʻano hōkū. He ʻala pilau pinepine kēia mau ʻeha. Hiki i ka ʻili make a me ka ʻiʻo ke lilo i ʻeleʻele, ʻili, a hemo.
  • Nā pilikia ʻike, ke kahe koko ʻana o loko, a me ka hōʻino ʻana o nā ʻiʻo: He mea kākaʻikahi loa, hiki ke loaʻa nā waihona calcium ʻaʻole ma lalo o ka ʻili wale nō, akā i loko o ke kino hoʻi, e hana ana i nā pilikia ʻē aʻe. Inā aia nā waihona calcium i loko o nā maka, hiki ke hōʻino ʻia ka ʻike. Inā aia lākou i loko o nā ʻōpū o loko, hiki iā lākou ke kahe ke koko a hōʻino i nā ʻiʻo.
  • Nā waihona kalipuna i loko o nā kīʻaha koko nui a me ka puʻuwai: ʻO kahi pilikia maʻamau o ka maʻi puʻupaʻa hope loa, ʻo ia nā waihona kalipuna i loko o nā kīʻaha koko nui a me nā kiwikā puʻuwai. Hoʻonui ka pilikia o kēia hana ke ulu ka calciphylaxis.

ʻElua mau ʻano nui o nā ʻeha Calciphylaxis e kū mai ana:

Ke loaʻa nā ʻeha, hana pinepine ʻia lākou ma kekahi o nā ʻano ʻelua:

  • Ka hoʻolaha waena: Loaʻa pinepine kēia mau ʻeha ma ka ʻōpū a me nā ʻūhā. ʻOi aku ka maʻamau i nā poʻe me kahi Body Mass Index (BMI) kiʻekiʻe a me nā wahine. Ma kahi o 70% o nā maʻi me ka uremic calciphylaxis i loaʻa kēia mau ʻeha hoʻolaha waena. I nā hihia ʻaʻole uremic, ʻo ka nui o ka hanana ma kahi o 50%. I nā hihia kahi i ʻoi aku ka nui o kēia mau ʻeha waena, ʻoi aku ka kiʻekiʻe o ka make.
  • Ka hoʻolaha ʻana o ka ʻili: ʻO kēia nā ʻeha e kū mai ana ma nā ʻaoʻao o nā lima a me nā wāwae, ʻoi aku hoʻi ma nā manamana lima. Ke koʻikoʻi nā ʻeha ʻili, pono paha ke kauka e ʻoki i kahi manamana lima, manamana wāwae, a i ʻole kekahi ʻāpana o ka lālā e pale ai i ka laha ʻana o ka pōʻino a me ke kumu ʻana i nā pilikia e hoʻoweliweli ai i ke ola.

No ke aha e hana ai ka calciphylaxis? He aha nā kumu?

ʻAʻole ʻike ʻia ke kumu kikoʻī o Calciphylaxis , akā hōʻike ka noiʻi ua hana ʻia e nā kumu he nui. Hoʻohui pū kēia mau mea e hana ai iā Calciphylaxis.

Hiki i kēia mau mea ke komo pū me:

  • Nui loa ka hormone parathyroid: Ke loaʻa iā ʻoe nā pilikia puʻupaʻa, hoʻāʻo kāu mau kelepa parathyroid e mālama i kou pae calcium koko i paʻa. Ke hana lākou i kēia, hana lākou i ka nui o ka hormone e pono ai kou kino. Ua kapa ʻia kēia he hyperparathyroidism . Hiki nō hoʻi kēia ke hana ʻia ke loaʻa ʻole i kou kino ka nui o ka wikamina D a i ʻole ka calcium.
  • Ka hāʻule ʻana o ka puʻupaʻa: ʻO nā puʻupaʻa e hana pono ʻole ana e hoʻopilikia i ke kaulike kemika e kaohi ana i ka calcium a me ka phosphorus i loko o ke kino.
  • Nui loa ka phosphorus: Hoʻohana ko mākou kino i ka phosphorus no nā kaʻina hana kemika like ʻole, a kōkua nā puʻupaʻa i ka kaohi ʻana i nā pae phosphorus.
  • Kekahi mau ʻano maʻi kanesa: ʻIke pinepine ʻia kēia i nā hihia o ka calciphylaxis, kahi mea pili ʻole i ka maʻi puʻupaʻa.
  • ʻEha: Hiki ke hana ʻia kēia e kahi ʻeha, kahi hana lapaʻau e like me ke ʻoki ʻana, a i ʻole kahi laina intravenous (IV).

ʻO wai ka mea i pilikia nui no kēia? (Nā kumu pilikia)

Aia kekahi mau kumu pilikia a me nā kūlana olakino e pili ana paha me Calciphylaxis. ʻO lākou kēia:

  • Nā pilikia puʻupaʻa: ʻO ka hapa nui o ka poʻe e hoʻomohala ana i ka calciphylaxis aia i nā pae hope loa o ka hāʻule ʻana o ka puʻupaʻa, a me ka poʻe ma ka dialysis.
  • Momona: Hoʻonui kēia kūlana i ka pilikia o ka hoʻomohala ʻana i ka calciphylaxis.
  • Maʻi diabetes: Ke hoʻokomo ʻoe i ka insulin i kēlā me kēia lā, hiki ke hōʻino ʻia ka ʻili ma kahi i hoʻokomo ʻia.
  • Nā maʻi Autoimmune: No ka laʻana, nā maʻi e like me Lupus, Ulcerative Colitis, a me Rheumatoid Arthritis.
  • Maʻi akepaʻa: ʻO ka maʻi hepatitis i hoʻokomo ʻia e ka waiʻona, kahi kūlana i hoʻokumu ʻia e ka hoʻohana ʻana i ka waiʻona, hiki ke lilo i mea pilikia.
  • Warfarin: ʻO kēia lāʻau hoʻokahe koko e pale aku i ke kino mai ka hoʻohana ʻana i ka wikamina K. He mea nui ka wikamina K no ke kāpili ʻana o ke koko. Hoʻāla pū ka wikamina K i kahi protein e kaohi ana i nā waihona calcium. ʻAʻole lawa ka wikamina K i ka nui o ka poʻe me ka maʻi puʻupaʻa hope loa. ʻOi aku ka maʻalahi o ka hana ʻana i nā waihona calcium.
  • Corticosteroids: Hāʻawi ʻia kēia mau lāʻau lapaʻau e hōʻemi i ka pehu a me ka mumū. ʻO ka poʻe i loaʻa i ka calciphylaxis ua lawe pinepine lākou i nā corticosteroids.

He aha nā pilikia o ka Calciphylaxis?

Hiki i nā Calciphylaxis ke hana i nā pilikia e like me:

  • ʻAʻole hiki ke hiamoe
  • Ka nalowale o ka makemake
  • Kaumaha
  • Nā ʻeha koʻikoʻi
  • Nā maʻi
  • ʻOki ʻana
  • Sepsis

Pehea e ʻike ai nā kauka i kēia?

Hiki i ke kauka ke kānalua i ka calciphylaxis ma hope o ka loiloi ʻana i kou kūlana, nā hōʻailona, ​​a me kahi hoʻokolohua kino. Hiki i kēia hoʻokolohua kino ke komo pū me ka nānā ʻana i kou ʻili a i ʻole nā ​​​​wahi ma lalo o kou ʻili a me ka nānā ʻana i kekahi mau loli. E nīnau pū lākou e pili ana i kāu mōʻaukala olakino a hoʻāʻo e ʻike i ka calciphylaxis. Ke kānalua ke kauka i kēia, e kauoha lākou i nā hoʻokolohua lapaʻau e ʻike hou aku.

He aha nā hoʻokolohua e hana ʻia nei?

Hiki i ke kauka ke kauoha i kēia mau hoʻokolohua:

  • ʻO ka biopsy ʻili:

ʻO ke ala hilinaʻi loa e ʻike ai i ka calciphylaxis, ʻo ia ka lawe ʻana i kahi laʻana liʻiliʻi (ma kahi o 4 a 5 milimita ka hohonu) o ka ʻili a me nā ʻiʻo ma lalo. E lawe pinepine ke kauka i kahi laʻana mai ka lihi o kahi ʻeha a i ʻole ka ʻeha ʻili. Nānā ʻia kēia laʻana ma lalo o kahi microscope, a hoʻohana ʻia kekahi mau mea e hoʻololi i ke kala a i ʻole nā ​​​​​​loli kemika e kōkua i ka hōʻoia ʻana i ka hōʻailona.

Inā loaʻa iā ʻoe ka maʻi puʻupaʻa hope loa a he mau ʻeha koʻikoʻi me kahi ʻōpala ʻeleʻele, ʻaʻole pono paha kahi biopsy.

  • Hoʻāʻo ʻana ma ka hale hana:

Kōkua nā hoʻāʻo koko a me ka mimi i ka ʻike ʻana i nā maʻi, loiloi i ke koʻikoʻi o ka maʻi, a hoʻoholo i ka lāʻau lapaʻau maikaʻi loa. ʻO nā hoʻāʻo a nā kauka e hoʻohana pinepine ai:

  • Nā hoʻāʻo hana puʻupaʻa: Hoʻopili kēia mau hoʻokolohua i ka mimi e ʻike i ka hana maikaʻi o kāu mau puʻupaʻa.
  • Nā palena mineral a me nā iwi: ʻO ka nānā ʻana i ka calcium, ka phosphorus, ka hormone parathyroid, a me ka wikamina D hiki ke hoʻoholo i ke koʻikoʻi o ka maʻi.
  • Nā hoʻāʻo hana ate: Ke hiki ʻole iā ʻoe ke lawe i nā lāʻau lapaʻau i kānana ʻia e kou mau puʻupaʻa, ʻo ke koho aʻe ka lawe ʻana i nā lāʻau lapaʻau i kānana ʻia e kou ake. Kōkua nā hoʻāʻo hana ate i nā kauka e hoʻoholo inā palekana ke hāʻawi iā ʻoe i nā lāʻau lapaʻau e hilinaʻi nei i ke ake.
  • Nā hōʻailona o ka ʻōnaehana pale:Ke nānā nei kēia hoʻāʻo i nā hōʻailona e hakakā nei kou kino i kahi maʻi. Hiki iā ia ke kōkua i ka ʻike ʻana i nā maʻi autoimmune.
  • Nā māka hoʻopaʻa koko: Ke nānā ʻana i ka maikaʻi o ke kāpili ʻana o kou koko (a i ʻole ke kāpili ʻole ʻana), no ka mea hiki ke hōʻike i ka hiki ke kahe koko i loko a i ʻole nā ​​​​pilikia ʻē aʻe.
  • Nā hoʻāʻo kiʻi:

Hiki i ke kauka ke kauoha i nā hoʻokolohua kiʻi, e like me nā X-ray a i ʻole nā ​​​​scan iwi, akā ʻaʻole maʻamau kēia mau mea. ʻOi aku ka nui o ka hana ʻana i nā hoʻokolohua kiʻi ke hāʻawi ʻole nā ​​​​hoʻokolohua ʻē aʻe i nā pane e hiki ke kōkua i ka hōʻailona.

Pehea e mālama ʻia ai kēia? (Lāʻau lapaʻau)

No ka mea, ʻaʻole maopopo loa i nā kānaka noiʻi ka calciphylaxis, ua kaupalena ʻia ke alakaʻi ʻana i ka lāʻau lapaʻau maikaʻi loa. I kēia manawa, ʻaʻohe lāʻau lapaʻau no kēia maʻi, akā inā holomua ka lāʻau lapaʻau, e nalowale paha kāu mau hōʻailona.

ʻO ka mea maʻamau, nānā nā kauka i kēia mau mea:

Mālama ʻeha

ʻO nā mea nui e pale aku i ka maʻi a kōkua i ka ho'ōla ʻana o ka ʻeha. Hiki i kēia ke komo pū me kekahi mau lāʻau lapaʻau holomua, no ka laʻana:

  • ʻO ka lāʻau lapaʻau oxygen hyperbaric: Pili kēia i ke kau ʻana iā ʻoe i loko o kahi keʻena ea e loaʻa ana he 100% oxygen (ma kahi o ka nui o ka oxygen maʻamau o kahi 20%). ʻOi aku ke kiʻekiʻe o ke kaomi i loko o ke keʻena ma mua o ka maʻamau. He ala kūpono loa kēia e hoʻolaha ai i ka ho'ōla ʻana o ka ʻeha.
  • Debridement: ʻO kēia ka wehe ʻana i nā ʻiʻo make a make paha mai kahi ʻeha. Kōkua kēia i ka pale ʻana i ka maʻi a paipai i ka ʻeha e ho'ōla. I nā hihia koʻikoʻi, pono paha ke ʻoki ʻana.
  • Hoʻopili ʻili a me nā ʻiʻo: I nā hihia i nalowale ai ka nui o nā ʻiʻo, hiki i nā grafts i lawe ʻia mai kahi ʻē aʻe o kou kino ke kōkua i ka hoʻoponopono a me ka ho'ōla ʻana i ka ʻeha.
  • Nā lāʻau lapaʻau antibiotics: Kōkua kēia mau lāʻau lapaʻau i ka hoʻōki ʻana i nā maʻi bacteria.

Kaohi ʻeha

He ʻano ʻeha loa ʻo Calciphylaxis. Hiki iā ia ke paʻakikī iā ʻoe ke hoʻomaha a hoʻōla i kou kino. Hoʻomaʻamaʻa pinepine nā kauka i nā lāʻau ʻeha opioid no Calciphylaxis.

Sodium thiosulfate

Hāʻawi ʻia kēia lāʻau lapaʻau iā ʻoe ma o kahi aʻa koko (IV). Hiki iā ia ke kōkua i ka wehe ʻana i nā waihona calcium mai kou mau kīʻaha koko a i ʻole nā ​​​​ʻiʻo ʻē aʻe.

Ka mālama ʻana i nā pilikia o ka iwi a me nā mineral

He mea nui loa ka mālama ʻana i kāu mau minelala koko i nā pae kūpono a me ke kaulike e pale aku ai i nā pilikia a me nā pilikia. ʻO kēia ka mālama ʻana i kāu mau pae hormone parathyroid mai ka haʻahaʻa loa a kiʻekiʻe loa paha. I kekahi mau hihia, pono paha ke ʻoki ʻana e wehe i hoʻokahi a ʻoi aku paha o kāu mau kelepa parathyroid.

Dialysis

He lāʻau lapaʻau kēia e wehe ai i nā ʻōpala mai ke koko ke hana pono ʻole kou mau puʻupaʻa.

Ka hoʻokele meaʻai

He mea nui loa ka pale ʻana i ka ʻai ʻole a i ʻole nā ​​hemahema o nā meaʻai e hiki ke hana me nā pilikia puʻupaʻa a me nā kūlana pili.

Ka mālama ʻana i nā lāʻau lapaʻau

He mea nui e nānā hou i nā lāʻau lapaʻau āpau āu e lawe ai e pale aku i nā hopena ʻaoʻao a me nā pilikia. He mea nui loa kēia inā ʻoe e lawe ana i ka warfarin a i ʻole nā ​​​​lāʻau lapaʻau ʻē aʻe e hoʻonui ai i ka pilikia o ka calciphylaxis.

Aia kekahi mau hopena ʻaoʻao o ka lāʻau lapaʻau?

Hiki i kāu kauka ke wehewehe pono i nā pilikia a me nā hopena ʻaoʻao. No ka mea he ʻano maopopo ʻole ʻia ka calciphylaxis, hiki ke wānana ʻole ʻia nā pilikia a me nā hopena ʻaoʻao a ʻokoʻa loa mai kēlā kanaka a kēia kanaka.

ʻO kekahi o nā hopena ʻaoʻao a me nā pilikia e hiki ke loaʻa:

  • Nā maʻi: Pili kēia i nā maʻi e hiki ke hana e pili ana i nā kaʻina hana lapaʻau, dialysis, a i ʻole ke ʻoki ʻana, ʻaʻole nā ​​​​maʻi mai nā ʻeha i hoʻokumu ʻia e ka calciphylaxis.
  • Nā hopena ʻaoʻao o ka sodium thiosulfate: ʻO kēia ka nausea, ka luaʻi ʻana, nā pilikia kaulike wai, ke koko haʻahaʻa, a me nā pilikia waikawa koko. Pono nā kauka e makaʻala i kēia mau pilikia, ʻoiai hoʻi i ka poʻe me ka maʻi puʻuwai. I nā hihia he nui, hiki ke mālama ʻia kēia mau mea ma ka hoʻololi ʻana i ka nui o kēia lāʻau lapaʻau a i ʻole ma ka mālama ʻana i nā hopena ʻaoʻao.

ʻAʻole anei hiki ke pale ʻia kēia?

No ka mea, ʻaʻole maopopo loa i nā kānaka noiʻi nā kumu o ka calciphylaxis, he paʻakikī ke pale aku i ke kūlana. Eia nō naʻe, ʻōlelo pinepine nā kauka e hoʻēmi i nā kumu pilikia, e like me ka mālama ʻana i nā pae calcium a me phosphate maʻamau.

He aha ka mea e hiki mai ana inā loaʻa iaʻu ʻo Calciphylaxis? He aha ka wā e hiki mai ana?

ʻO ka mea pōʻino, ma muli o ka nele o ka hoʻomaopopo ʻana i ka maʻi, ʻo ka nānā ʻana no Calciphylaxis he maikaʻi ʻole ia. He nui ka poʻe me Calciphylaxis e nalowale ana ka hiki ke hele a hoʻolilo i ka hapa nui o ko lākou manawa ma kahi noho huila a i ʻole kahi moe.

Ma kahi o ka hapalua o ka poʻe me ka calciphylaxis ʻaʻole ola ma mua o hoʻokahi makahiki. ʻO Sepsis ke kumu nui o ka make.

Eia nō naʻe, ma muli o ke ʻano o ka maʻi, hiki ke piʻi a emi paha ka manawa e ola ai i hoʻokahi makahiki. Eia nā kūlana a me nā manawa kūpono:

  • ʻO ka calciphylaxis non-uremic (ʻaʻole pili i ka maʻi renal hope loa):ʻO ka poʻe i loaʻa i ka calciphylaxis me ka ʻole o ka maʻi puʻupaʻa hope loa, ʻaʻole lākou e make i loko o hoʻokahi makahiki. I nā hihia o ka calciphylaxis non-uremic, ʻo ka pilikia o ka make i loko o hoʻokahi makahiki ma waena o 25% a me 45%. I nā hihia o ka uremic calciphylaxis, ʻo ka pilikia o ka make ma waena o 45% a me 80%.
  • Nā ʻōpū a me nā ʻeha: I nā pae hope loa o ka calciphylaxis, ulu nā loli ʻili i nā ʻōpū a me nā ʻeha. ʻO ka lohi o ka hōʻoia ʻana, ʻoi aku ka ʻino o ka nānā ʻana. Ma kahi o 20% wale nō o ka poʻe me nā ʻōpū a i ʻole nā ​​ʻeha e ola ana ma mua o ʻeono mahina.
  • Ka wehe ʻana i nā ʻiʻo make ma nā ʻeha: Aia nā hōʻike e hoʻonui ana kēia ʻano mālama ʻeha i ke ola. ʻO ka nui o ke ola ʻana no hoʻokahi makahiki no ka poʻe i hana ʻia ka debridement ma luna iki o 61%, ke hoʻohālikelike ʻia me kahi 27% no ka poʻe i hana ʻole.

ʻEhia ka lōʻihi o kēia kūlana?

He maʻi mau loa ʻo Calciphylaxis no ke ola holoʻokoʻa ʻaʻohe ona lāʻau lapaʻau i kēia manawa . Eia nō naʻe, i kekahi mau hihia, hiki i ka maʻi ke hoʻomaha ma hope o ka mālama ʻana. ʻAʻole ʻike ka poʻe noiʻi i ka lōʻihi o kona hiki ke mālama ʻia i ke kala ʻana.

Pehea wau e mālama ai iaʻu iho?

He mea nui loa ia e hahai pono i nā ʻōlelo a kāu kauka me ka hiki ke hiki me ka calciphylaxis. Pono ʻoe e makaʻala loa e pili ana i ka mālama ʻana i nā ʻeha, e mālama i nā ʻeha a i ʻole nā ​​​​ʻeha i maʻemaʻe a pale ʻia mai ka maʻi. Pono ʻoe e kamaʻilio me kāu kauka e pili ana i nā meaʻai āu e ʻai ai, nā lāʻau lapaʻau āu e lawe ai, a me nā mea hoʻohui hou a i ʻole nā ​​​​lāʻau lapaʻau home āu e noʻonoʻo nei.

Āhea wau e ʻike ai i ke kauka?

E kamaʻilio me kāu kauka ma kēia mau hihia:

  • Inā manaʻo ʻoe a ʻike paha ʻoe e pilikia ana ʻoe i ka loaʻa ʻana o Calciphylaxis, ua maikaʻi kēlā.
  • Inā ua ʻike mua ʻoe ua loaʻa iā ʻoe kēia maʻi.
  • Inā ʻike ʻoe i kekahi mau wahi ʻeha hou a i ʻole nā ​​​​wahi ʻeha.
  • Inā ʻike ʻoe i kahi loli i ke kala o kou ʻili.
  • Inā ʻike ʻoe i kekahi mau loli i kou ʻili a i ʻole ma lalo o kou ʻili.

ʻO kāu kauka ke kumu maikaʻi loa o ka ʻike e pili ana i kāu mau kumu pilikia, he aha nā hōʻailona āu e makaʻala ai, a me ka wā e ʻimi ai i ke aʻo lapaʻau. Hiki iā lākou ke ʻike i ka calciphylaxis i ka wā mua, hiki ke kōkua i kāu mālama ʻana.

Āhea wau e hele ai i ka lumi pilikia?

Inā loaʻa iā ʻoe ʻo Calciphylaxis, e alakaʻi kāu kauka iā ʻoe i ka wā e kelepona ai i ko lākou keʻena e pili ana i ka mālama ʻeha a i ʻole ka wā e ʻimi ai i ke kōkua lapaʻau wikiwiki. ʻO nā mea nui e makaʻala ai, ʻo ia nā hōʻailona o ka maʻi a i ʻole nā ​​​​pilikia a puni kahi ʻeha. ʻO kēia mau mea:

  • He mea maikaʻi ka pehu ʻana a i ʻole ka ʻulaʻula a puni ka ʻeha.
  • Inā ʻoe e manaʻo i ka wela ke hoʻopā ʻoe i ka ʻāpana a puni ka ʻeha.
  • Inā he wai e puka mai ana mai kahi ʻeha a/a i ʻole kahi ʻala maikaʻi ʻole.
  • Inā kū mai kahi ʻili ʻeleʻele ma luna o ka ʻeha.

He aha nā nīnau e pono iaʻu e nīnau aku i ke kauka?

ʻO kekahi mau nīnau āu e noʻonoʻo ai e nīnau aku i kāu kauka:

  • He aha ke ʻano o ka Calciphylaxis iaʻu?
  • He aha ka lāʻau lapaʻau maikaʻi loa noʻu?
  • Hiki iā ʻoe ke hoʻohui iaʻu i nā kumuwaiwai e hiki ke kōkua iaʻu i koʻu wā maʻi?
  • He aha ka manaʻolana no kekahi i loko o koʻu kūlana?

Leka Lawe-Home

Hiki ke paʻakikī ke hoʻomaopopo iā Calciphylaxis, no ka mea, he palena wale nō ka noiʻi a me ka ʻike e pili ana i ia mea. Hiki i ke kamaʻilio ʻana me kāu kauka ke kōkua iā ʻoe e hoʻomaopopo maikaʻi iā ia a ʻike i ka mea e manaʻo ai. Hiki i ka Calciphylaxis ke lilo i maʻi paʻakikī a paʻakikī ke mālama, akā aia nā koho lapaʻau e hiki ke kōkua. Inā ʻoe e hopohopo nei no ia mea, hiki i ke kamaʻilio ʻana me kahi kākāʻōlelo ke kōkua iā ʻoe e hoʻokele i kou mau manaʻo. E hoʻomanaʻo, ʻaʻole ʻoe hoʻokahi, a he mea nui e loaʻa ka ʻōlelo aʻoaʻo lapaʻau kūpono a me ke kākoʻo.


ʻO Calciphylaxis, maʻi puʻupaʻa, maʻi ʻili, nā kīʻaha koko, calcium, dialysis, nā ʻeha

Frequently Asked Questions (FAQ)

He aha nā hoʻokolohua e hana ʻia nei?

Hiki i ke kauka ke kauoha i kēia mau hoʻokolohua:

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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Ke ulu nei ʻoe i nā ʻeha ʻeha ma kou ʻili? Hiki paha iā Calciphylaxis!

Ke ulu nei ʻoe i nā ʻeha ʻeha ma kou ʻili? Hiki paha iā Calciphylaxis!

Ua lohe paha ʻoe i kahi maʻi i kapa ʻia ʻo Calciphylaxis? He mea ʻē paha ke kani ʻana o ka inoa. Akā, he ʻano laha ʻole ia, he ʻeha loa, a i kekahi manawa he mea hoʻoweliweli i ke ola. ʻO ka mea e hana ʻia ana, ʻo ia ka hōʻiliʻili ʻana o nā waihona calcium i loko o nā kīʻaha koko liʻiliʻi i loko o kou kino, e ālai ana iā lākou. Ke hana ʻia kēlā, hoʻōki ia i ke kahe ʻana o ke koko a hoʻomaka kou ʻili a me nā ʻiʻo ma lalo e make. Ua like ia me kahi mea kanu e mae ana ke loaʻa ʻole ka wai lawa.

He aha ka Calciphylaxis? E hoʻomaopopo maʻalahi kākou!

I ka ʻōlelo maʻalahi, ʻo Calciphylaxis kahi kūlana kahi e hōʻiliʻili ai nā waihona calcium i loko o kou mau kīʻaha koko, e ālai ana i ke kahe koko a make ai ka ʻili a me nā ʻiʻo ma lalo. E like me ka paipu wai e paʻa ana i ka lepo a pau ke kahe ʻana o ka wai, hōʻiliʻili nā waihona calcium i loko o nā kīʻaha koko liʻiliʻi i loko o ko kākou kino.

ʻO ka hapa pinepine, loaʻa kēia mau waihona calcium i loko o nā kīʻaha koko e hoʻolako ana i ke koko i ka ʻili a me nā ʻiʻo ma lalo o ka ʻili. Eia nō naʻe, he mea kakaikahi loa, hiki i kēia mau waihona calcium ke loaʻa i loko o nā ʻōpū i loko o ke kino, e like me nā maka, nā māmā, ka lolo, nā ʻiʻo, a me nā ʻōpū.

Ke hoʻopilikia kēia ʻano i ka ʻili, hiki ke ʻeha loa . Hiki i ka ʻāpana i hoʻopilikia ʻia ke wehe a hana i kahi ʻeha, e like me ka ʻeha moe. I ka make ʻana o ka ʻili a me nā ʻiʻo a puni ka ʻeha, hiki ke laha ka pōʻino. He lōʻihi ka manawa e ho'ōla ai nā ʻeha Calciphylaxis, a hiki ke alakaʻi i nā pilikia koʻikoʻi.

Inā loaʻa kēia ʻeha i ka maʻi, e laha ka maʻi ma ke kino a hoʻomaka kā mākou ʻōnaehana pale e pane nui. Kāhea mākou i kēia he sepsis . ʻO kēia ka pilikia weliweli loa a make o Calciphylaxis.

Aia kekahi mau ʻano o Calciphylaxis?

ʻAe, ʻelua ʻano nui o ka calciphylaxis, ma muli o ke ʻano o kona ulu ʻana.

1. Ka hoʻokalakikia uremic

ʻO kēia ke ʻano maʻamau . Loaʻa pinepine ia i nā poʻe e dialysis ma muli o ka maʻi puʻupaʻa hope loa (ESKD). ʻO ke ʻano kēia, ʻaʻole hana pono ko lākou mau puʻupaʻa a pono lākou e hoʻopili ʻia i kahi mīkini dialysis e wehe i nā huahana ʻōpala mai ko lākou koko.

2. Calciphylaxis ʻole-uremic

He mea kākaʻikahi loa kēia ʻano. Hiki ke loaʻa i nā poʻe i nā pae mua o ka maʻi puʻupaʻa, i nā poʻe i hōʻino ʻia i kekahi a i ʻole nā ​​puʻupaʻa ʻelua, a i ʻole (kākaʻikahi loa) i nā poʻe ʻaʻohe pilikia puʻupaʻa.

Pehea ka maʻamau o kēia ʻano?

He maʻi laha ʻole ʻo Calciphylaxis.Ma waena o ka poʻe ma ka dialysis, hana ʻia kēia ma kahi o 35 o 10,000 poʻe (ma kahi o hoʻokahi hapakolu o 1%). No ka laʻana, ma ʻAmelika Hui Pū ʻIa, aia ma mua o 1.5 miliona mau kānaka ma ka dialysis, no laila ua hōʻike ʻia ma kahi o 2,000 mau hihia o ka calciphylaxis i kēlā me kēia makahiki. ʻOi aku ka kakaikahi o ke ʻano ma nā ʻāina me ka haʻahaʻa o ka maʻi puʻupaʻa.

Akā, he mea kupanaha, ʻoi aku ka nui o ka pilikia o nā wāhine i ka loaʻa ʻana o kēia maʻi . ʻOi aku ka pālua o ka hiki i nā wāhine ke loaʻa iā ia ma mua o nā kāne.

He aha nā hōʻailona o kēia?

ʻO nā hōʻailona o Calciphylaxis:

  • ʻEha nui: He ʻano ʻeha loa kēia i nā manawa a pau. Hiki ke hoʻomaka ka ʻeha ma mua o ka ʻike ʻia ʻana o kekahi hōʻailona ʻeha a i ʻole nā ​​​​pōʻino ʻē aʻe. Hiki i ka ʻāpana i hoʻopilikia ʻia ke lilo i mea maʻalahi i ke kaomi a i ʻole ka hoʻopā ʻana, e hoʻonui ai i ka ʻeha.
  • Nā loli ʻili (nā pae mua): ʻO kēia nā wahi o ka ʻili e ʻulaʻula, poni, ʻeleʻele, a ʻeleʻele paha. ʻIke pinepine ʻia kēia mau loli e like me ka ʻupena. Aia paha he mau pehu, a hiki i ka ʻili i hoʻopilikia ʻia ke lilo i mānoanoa a ʻili.
  • Nā ʻeha a me nā ʻōpū (pae hope): ʻO ka maʻamau, lilo nā loli ʻili i mau ʻeha, e pālahalaha ana ma ke ʻano hōkū. He ʻala pilau pinepine kēia mau ʻeha. Hiki i ka ʻili make a me ka ʻiʻo ke lilo i ʻeleʻele, ʻili, a hemo.
  • Nā pilikia ʻike, ke kahe koko ʻana o loko, a me ka hōʻino ʻana o nā ʻiʻo: He mea kākaʻikahi loa, hiki ke loaʻa nā waihona calcium ʻaʻole ma lalo o ka ʻili wale nō, akā i loko o ke kino hoʻi, e hana ana i nā pilikia ʻē aʻe. Inā aia nā waihona calcium i loko o nā maka, hiki ke hōʻino ʻia ka ʻike. Inā aia lākou i loko o nā ʻōpū o loko, hiki iā lākou ke kahe ke koko a hōʻino i nā ʻiʻo.
  • Nā waihona kalipuna i loko o nā kīʻaha koko nui a me ka puʻuwai: ʻO kahi pilikia maʻamau o ka maʻi puʻupaʻa hope loa, ʻo ia nā waihona kalipuna i loko o nā kīʻaha koko nui a me nā kiwikā puʻuwai. Hoʻonui ka pilikia o kēia hana ke ulu ka calciphylaxis.

ʻElua mau ʻano nui o nā ʻeha Calciphylaxis e kū mai ana:

Ke loaʻa nā ʻeha, hana pinepine ʻia lākou ma kekahi o nā ʻano ʻelua:

  • Ka hoʻolaha waena: Loaʻa pinepine kēia mau ʻeha ma ka ʻōpū a me nā ʻūhā. ʻOi aku ka maʻamau i nā poʻe me kahi Body Mass Index (BMI) kiʻekiʻe a me nā wahine. Ma kahi o 70% o nā maʻi me ka uremic calciphylaxis i loaʻa kēia mau ʻeha hoʻolaha waena. I nā hihia ʻaʻole uremic, ʻo ka nui o ka hanana ma kahi o 50%. I nā hihia kahi i ʻoi aku ka nui o kēia mau ʻeha waena, ʻoi aku ka kiʻekiʻe o ka make.
  • Ka hoʻolaha ʻana o ka ʻili: ʻO kēia nā ʻeha e kū mai ana ma nā ʻaoʻao o nā lima a me nā wāwae, ʻoi aku hoʻi ma nā manamana lima. Ke koʻikoʻi nā ʻeha ʻili, pono paha ke kauka e ʻoki i kahi manamana lima, manamana wāwae, a i ʻole kekahi ʻāpana o ka lālā e pale ai i ka laha ʻana o ka pōʻino a me ke kumu ʻana i nā pilikia e hoʻoweliweli ai i ke ola.

No ke aha e hana ai ka calciphylaxis? He aha nā kumu?

ʻAʻole ʻike ʻia ke kumu kikoʻī o Calciphylaxis , akā hōʻike ka noiʻi ua hana ʻia e nā kumu he nui. Hoʻohui pū kēia mau mea e hana ai iā Calciphylaxis.

Hiki i kēia mau mea ke komo pū me:

  • Nui loa ka hormone parathyroid: Ke loaʻa iā ʻoe nā pilikia puʻupaʻa, hoʻāʻo kāu mau kelepa parathyroid e mālama i kou pae calcium koko i paʻa. Ke hana lākou i kēia, hana lākou i ka nui o ka hormone e pono ai kou kino. Ua kapa ʻia kēia he hyperparathyroidism . Hiki nō hoʻi kēia ke hana ʻia ke loaʻa ʻole i kou kino ka nui o ka wikamina D a i ʻole ka calcium.
  • Ka hāʻule ʻana o ka puʻupaʻa: ʻO nā puʻupaʻa e hana pono ʻole ana e hoʻopilikia i ke kaulike kemika e kaohi ana i ka calcium a me ka phosphorus i loko o ke kino.
  • Nui loa ka phosphorus: Hoʻohana ko mākou kino i ka phosphorus no nā kaʻina hana kemika like ʻole, a kōkua nā puʻupaʻa i ka kaohi ʻana i nā pae phosphorus.
  • Kekahi mau ʻano maʻi kanesa: ʻIke pinepine ʻia kēia i nā hihia o ka calciphylaxis, kahi mea pili ʻole i ka maʻi puʻupaʻa.
  • ʻEha: Hiki ke hana ʻia kēia e kahi ʻeha, kahi hana lapaʻau e like me ke ʻoki ʻana, a i ʻole kahi laina intravenous (IV).

ʻO wai ka mea i pilikia nui no kēia? (Nā kumu pilikia)

Aia kekahi mau kumu pilikia a me nā kūlana olakino e pili ana paha me Calciphylaxis. ʻO lākou kēia:

  • Nā pilikia puʻupaʻa: ʻO ka hapa nui o ka poʻe e hoʻomohala ana i ka calciphylaxis aia i nā pae hope loa o ka hāʻule ʻana o ka puʻupaʻa, a me ka poʻe ma ka dialysis.
  • Momona: Hoʻonui kēia kūlana i ka pilikia o ka hoʻomohala ʻana i ka calciphylaxis.
  • Maʻi diabetes: Ke hoʻokomo ʻoe i ka insulin i kēlā me kēia lā, hiki ke hōʻino ʻia ka ʻili ma kahi i hoʻokomo ʻia.
  • Nā maʻi Autoimmune: No ka laʻana, nā maʻi e like me Lupus, Ulcerative Colitis, a me Rheumatoid Arthritis.
  • Maʻi akepaʻa: ʻO ka maʻi hepatitis i hoʻokomo ʻia e ka waiʻona, kahi kūlana i hoʻokumu ʻia e ka hoʻohana ʻana i ka waiʻona, hiki ke lilo i mea pilikia.
  • Warfarin: ʻO kēia lāʻau hoʻokahe koko e pale aku i ke kino mai ka hoʻohana ʻana i ka wikamina K. He mea nui ka wikamina K no ke kāpili ʻana o ke koko. Hoʻāla pū ka wikamina K i kahi protein e kaohi ana i nā waihona calcium. ʻAʻole lawa ka wikamina K i ka nui o ka poʻe me ka maʻi puʻupaʻa hope loa. ʻOi aku ka maʻalahi o ka hana ʻana i nā waihona calcium.
  • Corticosteroids: Hāʻawi ʻia kēia mau lāʻau lapaʻau e hōʻemi i ka pehu a me ka mumū. ʻO ka poʻe i loaʻa i ka calciphylaxis ua lawe pinepine lākou i nā corticosteroids.

He aha nā pilikia o ka Calciphylaxis?

Hiki i nā Calciphylaxis ke hana i nā pilikia e like me:

  • ʻAʻole hiki ke hiamoe
  • Ka nalowale o ka makemake
  • Kaumaha
  • Nā ʻeha koʻikoʻi
  • Nā maʻi
  • ʻOki ʻana
  • Sepsis

Pehea e ʻike ai nā kauka i kēia?

Hiki i ke kauka ke kānalua i ka calciphylaxis ma hope o ka loiloi ʻana i kou kūlana, nā hōʻailona, ​​a me kahi hoʻokolohua kino. Hiki i kēia hoʻokolohua kino ke komo pū me ka nānā ʻana i kou ʻili a i ʻole nā ​​​​wahi ma lalo o kou ʻili a me ka nānā ʻana i kekahi mau loli. E nīnau pū lākou e pili ana i kāu mōʻaukala olakino a hoʻāʻo e ʻike i ka calciphylaxis. Ke kānalua ke kauka i kēia, e kauoha lākou i nā hoʻokolohua lapaʻau e ʻike hou aku.

He aha nā hoʻokolohua e hana ʻia nei?

Hiki i ke kauka ke kauoha i kēia mau hoʻokolohua:

  • ʻO ka biopsy ʻili:

ʻO ke ala hilinaʻi loa e ʻike ai i ka calciphylaxis, ʻo ia ka lawe ʻana i kahi laʻana liʻiliʻi (ma kahi o 4 a 5 milimita ka hohonu) o ka ʻili a me nā ʻiʻo ma lalo. E lawe pinepine ke kauka i kahi laʻana mai ka lihi o kahi ʻeha a i ʻole ka ʻeha ʻili. Nānā ʻia kēia laʻana ma lalo o kahi microscope, a hoʻohana ʻia kekahi mau mea e hoʻololi i ke kala a i ʻole nā ​​​​​​loli kemika e kōkua i ka hōʻoia ʻana i ka hōʻailona.

Inā loaʻa iā ʻoe ka maʻi puʻupaʻa hope loa a he mau ʻeha koʻikoʻi me kahi ʻōpala ʻeleʻele, ʻaʻole pono paha kahi biopsy.

  • Hoʻāʻo ʻana ma ka hale hana:

Kōkua nā hoʻāʻo koko a me ka mimi i ka ʻike ʻana i nā maʻi, loiloi i ke koʻikoʻi o ka maʻi, a hoʻoholo i ka lāʻau lapaʻau maikaʻi loa. ʻO nā hoʻāʻo a nā kauka e hoʻohana pinepine ai:

  • Nā hoʻāʻo hana puʻupaʻa: Hoʻopili kēia mau hoʻokolohua i ka mimi e ʻike i ka hana maikaʻi o kāu mau puʻupaʻa.
  • Nā palena mineral a me nā iwi: ʻO ka nānā ʻana i ka calcium, ka phosphorus, ka hormone parathyroid, a me ka wikamina D hiki ke hoʻoholo i ke koʻikoʻi o ka maʻi.
  • Nā hoʻāʻo hana ate: Ke hiki ʻole iā ʻoe ke lawe i nā lāʻau lapaʻau i kānana ʻia e kou mau puʻupaʻa, ʻo ke koho aʻe ka lawe ʻana i nā lāʻau lapaʻau i kānana ʻia e kou ake. Kōkua nā hoʻāʻo hana ate i nā kauka e hoʻoholo inā palekana ke hāʻawi iā ʻoe i nā lāʻau lapaʻau e hilinaʻi nei i ke ake.
  • Nā hōʻailona o ka ʻōnaehana pale:Ke nānā nei kēia hoʻāʻo i nā hōʻailona e hakakā nei kou kino i kahi maʻi. Hiki iā ia ke kōkua i ka ʻike ʻana i nā maʻi autoimmune.
  • Nā māka hoʻopaʻa koko: Ke nānā ʻana i ka maikaʻi o ke kāpili ʻana o kou koko (a i ʻole ke kāpili ʻole ʻana), no ka mea hiki ke hōʻike i ka hiki ke kahe koko i loko a i ʻole nā ​​​​pilikia ʻē aʻe.
  • Nā hoʻāʻo kiʻi:

Hiki i ke kauka ke kauoha i nā hoʻokolohua kiʻi, e like me nā X-ray a i ʻole nā ​​​​scan iwi, akā ʻaʻole maʻamau kēia mau mea. ʻOi aku ka nui o ka hana ʻana i nā hoʻokolohua kiʻi ke hāʻawi ʻole nā ​​​​hoʻokolohua ʻē aʻe i nā pane e hiki ke kōkua i ka hōʻailona.

Pehea e mālama ʻia ai kēia? (Lāʻau lapaʻau)

No ka mea, ʻaʻole maopopo loa i nā kānaka noiʻi ka calciphylaxis, ua kaupalena ʻia ke alakaʻi ʻana i ka lāʻau lapaʻau maikaʻi loa. I kēia manawa, ʻaʻohe lāʻau lapaʻau no kēia maʻi, akā inā holomua ka lāʻau lapaʻau, e nalowale paha kāu mau hōʻailona.

ʻO ka mea maʻamau, nānā nā kauka i kēia mau mea:

Mālama ʻeha

ʻO nā mea nui e pale aku i ka maʻi a kōkua i ka ho'ōla ʻana o ka ʻeha. Hiki i kēia ke komo pū me kekahi mau lāʻau lapaʻau holomua, no ka laʻana:

  • ʻO ka lāʻau lapaʻau oxygen hyperbaric: Pili kēia i ke kau ʻana iā ʻoe i loko o kahi keʻena ea e loaʻa ana he 100% oxygen (ma kahi o ka nui o ka oxygen maʻamau o kahi 20%). ʻOi aku ke kiʻekiʻe o ke kaomi i loko o ke keʻena ma mua o ka maʻamau. He ala kūpono loa kēia e hoʻolaha ai i ka ho'ōla ʻana o ka ʻeha.
  • Debridement: ʻO kēia ka wehe ʻana i nā ʻiʻo make a make paha mai kahi ʻeha. Kōkua kēia i ka pale ʻana i ka maʻi a paipai i ka ʻeha e ho'ōla. I nā hihia koʻikoʻi, pono paha ke ʻoki ʻana.
  • Hoʻopili ʻili a me nā ʻiʻo: I nā hihia i nalowale ai ka nui o nā ʻiʻo, hiki i nā grafts i lawe ʻia mai kahi ʻē aʻe o kou kino ke kōkua i ka hoʻoponopono a me ka ho'ōla ʻana i ka ʻeha.
  • Nā lāʻau lapaʻau antibiotics: Kōkua kēia mau lāʻau lapaʻau i ka hoʻōki ʻana i nā maʻi bacteria.

Kaohi ʻeha

He ʻano ʻeha loa ʻo Calciphylaxis. Hiki iā ia ke paʻakikī iā ʻoe ke hoʻomaha a hoʻōla i kou kino. Hoʻomaʻamaʻa pinepine nā kauka i nā lāʻau ʻeha opioid no Calciphylaxis.

Sodium thiosulfate

Hāʻawi ʻia kēia lāʻau lapaʻau iā ʻoe ma o kahi aʻa koko (IV). Hiki iā ia ke kōkua i ka wehe ʻana i nā waihona calcium mai kou mau kīʻaha koko a i ʻole nā ​​​​ʻiʻo ʻē aʻe.

Ka mālama ʻana i nā pilikia o ka iwi a me nā mineral

He mea nui loa ka mālama ʻana i kāu mau minelala koko i nā pae kūpono a me ke kaulike e pale aku ai i nā pilikia a me nā pilikia. ʻO kēia ka mālama ʻana i kāu mau pae hormone parathyroid mai ka haʻahaʻa loa a kiʻekiʻe loa paha. I kekahi mau hihia, pono paha ke ʻoki ʻana e wehe i hoʻokahi a ʻoi aku paha o kāu mau kelepa parathyroid.

Dialysis

He lāʻau lapaʻau kēia e wehe ai i nā ʻōpala mai ke koko ke hana pono ʻole kou mau puʻupaʻa.

Ka hoʻokele meaʻai

He mea nui loa ka pale ʻana i ka ʻai ʻole a i ʻole nā ​​hemahema o nā meaʻai e hiki ke hana me nā pilikia puʻupaʻa a me nā kūlana pili.

Ka mālama ʻana i nā lāʻau lapaʻau

He mea nui e nānā hou i nā lāʻau lapaʻau āpau āu e lawe ai e pale aku i nā hopena ʻaoʻao a me nā pilikia. He mea nui loa kēia inā ʻoe e lawe ana i ka warfarin a i ʻole nā ​​​​lāʻau lapaʻau ʻē aʻe e hoʻonui ai i ka pilikia o ka calciphylaxis.

Aia kekahi mau hopena ʻaoʻao o ka lāʻau lapaʻau?

Hiki i kāu kauka ke wehewehe pono i nā pilikia a me nā hopena ʻaoʻao. No ka mea he ʻano maopopo ʻole ʻia ka calciphylaxis, hiki ke wānana ʻole ʻia nā pilikia a me nā hopena ʻaoʻao a ʻokoʻa loa mai kēlā kanaka a kēia kanaka.

ʻO kekahi o nā hopena ʻaoʻao a me nā pilikia e hiki ke loaʻa:

  • Nā maʻi: Pili kēia i nā maʻi e hiki ke hana e pili ana i nā kaʻina hana lapaʻau, dialysis, a i ʻole ke ʻoki ʻana, ʻaʻole nā ​​​​maʻi mai nā ʻeha i hoʻokumu ʻia e ka calciphylaxis.
  • Nā hopena ʻaoʻao o ka sodium thiosulfate: ʻO kēia ka nausea, ka luaʻi ʻana, nā pilikia kaulike wai, ke koko haʻahaʻa, a me nā pilikia waikawa koko. Pono nā kauka e makaʻala i kēia mau pilikia, ʻoiai hoʻi i ka poʻe me ka maʻi puʻuwai. I nā hihia he nui, hiki ke mālama ʻia kēia mau mea ma ka hoʻololi ʻana i ka nui o kēia lāʻau lapaʻau a i ʻole ma ka mālama ʻana i nā hopena ʻaoʻao.

ʻAʻole anei hiki ke pale ʻia kēia?

No ka mea, ʻaʻole maopopo loa i nā kānaka noiʻi nā kumu o ka calciphylaxis, he paʻakikī ke pale aku i ke kūlana. Eia nō naʻe, ʻōlelo pinepine nā kauka e hoʻēmi i nā kumu pilikia, e like me ka mālama ʻana i nā pae calcium a me phosphate maʻamau.

He aha ka mea e hiki mai ana inā loaʻa iaʻu ʻo Calciphylaxis? He aha ka wā e hiki mai ana?

ʻO ka mea pōʻino, ma muli o ka nele o ka hoʻomaopopo ʻana i ka maʻi, ʻo ka nānā ʻana no Calciphylaxis he maikaʻi ʻole ia. He nui ka poʻe me Calciphylaxis e nalowale ana ka hiki ke hele a hoʻolilo i ka hapa nui o ko lākou manawa ma kahi noho huila a i ʻole kahi moe.

Ma kahi o ka hapalua o ka poʻe me ka calciphylaxis ʻaʻole ola ma mua o hoʻokahi makahiki. ʻO Sepsis ke kumu nui o ka make.

Eia nō naʻe, ma muli o ke ʻano o ka maʻi, hiki ke piʻi a emi paha ka manawa e ola ai i hoʻokahi makahiki. Eia nā kūlana a me nā manawa kūpono:

  • ʻO ka calciphylaxis non-uremic (ʻaʻole pili i ka maʻi renal hope loa):ʻO ka poʻe i loaʻa i ka calciphylaxis me ka ʻole o ka maʻi puʻupaʻa hope loa, ʻaʻole lākou e make i loko o hoʻokahi makahiki. I nā hihia o ka calciphylaxis non-uremic, ʻo ka pilikia o ka make i loko o hoʻokahi makahiki ma waena o 25% a me 45%. I nā hihia o ka uremic calciphylaxis, ʻo ka pilikia o ka make ma waena o 45% a me 80%.
  • Nā ʻōpū a me nā ʻeha: I nā pae hope loa o ka calciphylaxis, ulu nā loli ʻili i nā ʻōpū a me nā ʻeha. ʻO ka lohi o ka hōʻoia ʻana, ʻoi aku ka ʻino o ka nānā ʻana. Ma kahi o 20% wale nō o ka poʻe me nā ʻōpū a i ʻole nā ​​ʻeha e ola ana ma mua o ʻeono mahina.
  • Ka wehe ʻana i nā ʻiʻo make ma nā ʻeha: Aia nā hōʻike e hoʻonui ana kēia ʻano mālama ʻeha i ke ola. ʻO ka nui o ke ola ʻana no hoʻokahi makahiki no ka poʻe i hana ʻia ka debridement ma luna iki o 61%, ke hoʻohālikelike ʻia me kahi 27% no ka poʻe i hana ʻole.

ʻEhia ka lōʻihi o kēia kūlana?

He maʻi mau loa ʻo Calciphylaxis no ke ola holoʻokoʻa ʻaʻohe ona lāʻau lapaʻau i kēia manawa . Eia nō naʻe, i kekahi mau hihia, hiki i ka maʻi ke hoʻomaha ma hope o ka mālama ʻana. ʻAʻole ʻike ka poʻe noiʻi i ka lōʻihi o kona hiki ke mālama ʻia i ke kala ʻana.

Pehea wau e mālama ai iaʻu iho?

He mea nui loa ia e hahai pono i nā ʻōlelo a kāu kauka me ka hiki ke hiki me ka calciphylaxis. Pono ʻoe e makaʻala loa e pili ana i ka mālama ʻana i nā ʻeha, e mālama i nā ʻeha a i ʻole nā ​​​​ʻeha i maʻemaʻe a pale ʻia mai ka maʻi. Pono ʻoe e kamaʻilio me kāu kauka e pili ana i nā meaʻai āu e ʻai ai, nā lāʻau lapaʻau āu e lawe ai, a me nā mea hoʻohui hou a i ʻole nā ​​​​lāʻau lapaʻau home āu e noʻonoʻo nei.

Āhea wau e ʻike ai i ke kauka?

E kamaʻilio me kāu kauka ma kēia mau hihia:

  • Inā manaʻo ʻoe a ʻike paha ʻoe e pilikia ana ʻoe i ka loaʻa ʻana o Calciphylaxis, ua maikaʻi kēlā.
  • Inā ua ʻike mua ʻoe ua loaʻa iā ʻoe kēia maʻi.
  • Inā ʻike ʻoe i kekahi mau wahi ʻeha hou a i ʻole nā ​​​​wahi ʻeha.
  • Inā ʻike ʻoe i kahi loli i ke kala o kou ʻili.
  • Inā ʻike ʻoe i kekahi mau loli i kou ʻili a i ʻole ma lalo o kou ʻili.

ʻO kāu kauka ke kumu maikaʻi loa o ka ʻike e pili ana i kāu mau kumu pilikia, he aha nā hōʻailona āu e makaʻala ai, a me ka wā e ʻimi ai i ke aʻo lapaʻau. Hiki iā lākou ke ʻike i ka calciphylaxis i ka wā mua, hiki ke kōkua i kāu mālama ʻana.

Āhea wau e hele ai i ka lumi pilikia?

Inā loaʻa iā ʻoe ʻo Calciphylaxis, e alakaʻi kāu kauka iā ʻoe i ka wā e kelepona ai i ko lākou keʻena e pili ana i ka mālama ʻeha a i ʻole ka wā e ʻimi ai i ke kōkua lapaʻau wikiwiki. ʻO nā mea nui e makaʻala ai, ʻo ia nā hōʻailona o ka maʻi a i ʻole nā ​​​​pilikia a puni kahi ʻeha. ʻO kēia mau mea:

  • He mea maikaʻi ka pehu ʻana a i ʻole ka ʻulaʻula a puni ka ʻeha.
  • Inā ʻoe e manaʻo i ka wela ke hoʻopā ʻoe i ka ʻāpana a puni ka ʻeha.
  • Inā he wai e puka mai ana mai kahi ʻeha a/a i ʻole kahi ʻala maikaʻi ʻole.
  • Inā kū mai kahi ʻili ʻeleʻele ma luna o ka ʻeha.

He aha nā nīnau e pono iaʻu e nīnau aku i ke kauka?

ʻO kekahi mau nīnau āu e noʻonoʻo ai e nīnau aku i kāu kauka:

  • He aha ke ʻano o ka Calciphylaxis iaʻu?
  • He aha ka lāʻau lapaʻau maikaʻi loa noʻu?
  • Hiki iā ʻoe ke hoʻohui iaʻu i nā kumuwaiwai e hiki ke kōkua iaʻu i koʻu wā maʻi?
  • He aha ka manaʻolana no kekahi i loko o koʻu kūlana?

Leka Lawe-Home

Hiki ke paʻakikī ke hoʻomaopopo iā Calciphylaxis, no ka mea, he palena wale nō ka noiʻi a me ka ʻike e pili ana i ia mea. Hiki i ke kamaʻilio ʻana me kāu kauka ke kōkua iā ʻoe e hoʻomaopopo maikaʻi iā ia a ʻike i ka mea e manaʻo ai. Hiki i ka Calciphylaxis ke lilo i maʻi paʻakikī a paʻakikī ke mālama, akā aia nā koho lapaʻau e hiki ke kōkua. Inā ʻoe e hopohopo nei no ia mea, hiki i ke kamaʻilio ʻana me kahi kākāʻōlelo ke kōkua iā ʻoe e hoʻokele i kou mau manaʻo. E hoʻomanaʻo, ʻaʻole ʻoe hoʻokahi, a he mea nui e loaʻa ka ʻōlelo aʻoaʻo lapaʻau kūpono a me ke kākoʻo.


ʻO Calciphylaxis, maʻi puʻupaʻa, maʻi ʻili, nā kīʻaha koko, calcium, dialysis, nā ʻeha

Frequently Asked Questions (FAQ)

He aha nā hoʻokolohua e hana ʻia nei?

Hiki i ke kauka ke kauoha i kēia mau hoʻokolohua:

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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