Skip to main content

Aia kou puʻuwai ma ka ʻaoʻao ʻākau? E kamaʻilio kākou e pili ana i ka (Dextrocardia)!

Aia kou puʻuwai ma ka ʻaoʻao ʻākau? E kamaʻilio kākou e pili ana i ka (Dextrocardia)!

Ua noʻonoʻo paha ʻoe inā aia kou puʻuwai ma ka ʻaoʻao ʻākau o kou kino, ʻaʻole ma ka hema? ʻĀ, he mea kupanaha, ʻeā? Akā hiki nō paha. ʻO kēia ka mea a mākou e kapa nei he `(Dextrocardia)`. I ka ʻōlelo maʻalahi, aia kou puʻuwai ma ka ʻaoʻao ʻākau o kou umauma, e kū pono ana i ka ʻākau. Ua like ia me ke aniani o ka puʻuwai ma ka hema. ʻO ka maʻamau, aia ko mākou puʻuwai ma ka ʻaoʻao hema o kou umauma, e kū pono ana i ka hema. ʻO kēia kūlana i kapa ʻia ʻo `(Dextrocardia)` ua manaʻo ʻia he kīnā puʻuwai hānau . ʻO ia hoʻi, ua hānau ʻia ʻoe me kēia ʻokoʻa.

I kēia manawa, ke noʻonoʻo nei paha ʻoe, "Auē kuʻu Akua, he mea nui anei kēlā?" ʻOiaʻiʻo, inā loaʻa iā ʻoe wale nō ka `(Dextrocardia)`, ʻo ia hoʻi, aia ka puʻuwai ma ka ʻaoʻao ʻākau, ʻo ka hapa nui o ka manawa ʻaʻole ia he mea koʻikoʻi loa . ʻAʻole ia e hana i kekahi mau hōʻailona, ​​ʻaʻole ia e hoʻoulu i nā pilikia, a ʻaʻole pono ka mālama ʻana. Eia nō naʻe, i kekahi manawa hiki i ka poʻe me `(Dextrocardia)` ke hānau ʻia me nā maʻi olakino ʻē aʻe. Hiki i kēlā mau maʻi ke hoʻoulu i nā pilikia a pono ke mālama ʻia e ke kauka.

He maʻi laha ʻole kēia, e kū ana ma kahi o hoʻokahi i loko o 12,000 mau hāpai ʻana.

He aha nā ʻano nui o `(Dextrocardia)`? ʻO ka puʻuwai wale nō ma ka ʻākau?

ʻAe, hiki i kēia `(Dextrocardia)` ke hele mai i nā ʻano like ʻole. Malia paha ʻo ka puʻuwai wale nō ma ka ʻaoʻao ʻākau, a i ʻole hiki ke hele mai me nā loli i ke kūlana o nā ʻōpū kūloko ʻē aʻe. E nānā kākou i nā ʻano nui:

  • ʻO ka Dextrocardia i hoʻokaʻawale ʻia: ʻO kēia ka manawa e neʻe wale ai kou puʻuwai mai ka ʻaoʻao hema a i ka ʻaoʻao ʻākau. Eia nō naʻe, aia nā ʻāpana ʻē aʻe a pau i kahi kūlana maʻamau. Inā ʻaʻohe maʻi puʻuwai ʻē aʻe, ke hana maʻamau nei ka puʻuwai. ʻAʻohe hōʻailona o kēia.
  • ʻO `Situs Inversus` me `(Dextrocardia)`: Ma kēia, aia kou puʻuwai ma ka ʻaoʻao ʻākau, e like me ke "kiʻi aniani", a aia nā ʻāpana ʻē aʻe i loko o kou umauma a me kou ʻōpū ma ke ʻaoʻao ʻē aʻe. E noʻonoʻo e like me ke akepaʻa ma ka ʻaoʻao hema a aia ka spleen ma ka ʻaoʻao ʻākau. Hiki i kēia kūlana `(Situs Inversu)` ke lilo i hōʻailona o kahi maʻi genetic i kapa ʻia ʻo `(Primary Ciliary Dyskinesia)`. Hiki i kēia maʻi ke hana i nā hōʻailona like ʻole mai ka hānau ʻana.
  • ʻO Dextrocardia me nā kīnā puʻuwai hānau ʻē aʻe: He nui ka poʻe me ka dextrocardia i loaʻa nā maʻi puʻuwai ʻē aʻe e hoʻopilikia ai i ka hana ʻana o ka puʻuwai. Hiki i kēia mau maʻi puʻuwai ke hana i nā hōʻailona, ​​​​nā pilikia, a pono e mālama ʻia.
  • ʻO ka `Heterotaxy Syndrome` me `(Dextrocardia)`: I kēia hihia, aia ka puʻuwai ma ka ʻaoʻao ʻākau, e like me ke "kiʻi aniani". Eia kekahi, aia nā ʻōpū ʻē aʻe ma nā wahi ʻē, ʻaʻole ma kahi e pono ai lākou. Hiki i kēia `(Heterotaxy Syndrome)` ke hana i nā pilikia koʻikoʻi i ka hana ʻana o nā ʻōpū.

He aha nā hōʻailona e hiki ke kū mai ma muli o ka `(Dextrocardia)`?

E like me kā mākou i ʻōlelo ai ma mua, inā ua hoʻokaʻawale ʻia ʻoe ʻo `(Dextrocardia),` ʻo ia hoʻi, aia wale nō ka puʻuwai ma ka ʻaoʻao ʻākau, ʻaʻohe hōʻailona . ʻAʻole paha ʻoe e ʻike aia kou puʻuwai ma ka ʻaoʻao ʻākau, a ua ʻike ʻia ia ma ka hanana i ka wā o kahi `(Imaging Test)` i hana ʻia no kekahi kumu ʻē aʻe.

Eia nō naʻe, inā hui pū ʻia ke kūlana `(Dextrocardia)` me nā kīnā puʻuwai ʻē aʻe a i ʻole nā ​​maʻi genetic, a laila e ʻike ʻia kekahi mau hōʻailona. ʻIke pinepine ʻia kēia mau mea i ka wā ʻōpiopio o ke ola. E nānā i kēia mau hōʻailona:

  • Manaʻo luhi loa.
  • Nā maʻi pinepine o ka māmā a i ʻole nā ​​maʻi sinus.
  • Manaʻo nui i ka luhi a me ka pilikia o ka hanu ʻana i ka wā o ka hana kino.
  • Puʻuwai kūpono ʻole.
  • He uliuli ke ʻano o ka ʻili (ua kapa ʻia kēia he "Cyanosis", ʻo ia hoʻi, ua haʻahaʻa ka oxygen i loko o ke koko).
  • Ke nānā aku nei ka ʻili he keʻokeʻo.
  • Melemele o ka ʻili a me nā maka (e like me ka jaundice).
  • Ka paʻakikī o ka hanu ʻana a i ʻole ka hanu wikiwiki.
  • ʻO ka loaʻa ʻana o ke kaumaha a me nā pilikia ulu (ʻoi aku hoʻi i nā keiki ʻōpio).
  • ʻŪhū me ka huʻa.

He mea nui: Inā loaʻa i kāu keiki kēia mau hōʻailona, ​​​​he mea nui e ʻike koke i ke kauka e ʻike i ke kumu. ʻOiai ʻaʻole i hoʻokumu ʻia kēia mau hōʻailona e ka `(Dextrocardia)` ponoʻī, hiki i nā hoʻokolohua ke ʻike i ke kūlana `(Dextrocardia).`

No ke aha e hana ʻia ai kēia `(Dextrocardia)`? He aha nā kumu?

ʻO ke kumu nui o kēia `(Dextrocardia)` ʻo ia nā loli genetic e kū mai ana i nā wā mua o ka hāpai ʻana . ʻOi aku ma mua o 60 mau genes e kōkua i ka hoʻoholo ʻana i ke ʻano o ke kau ʻana o nā ʻōpū o ko mākou kino. Ke ʻimi nei nā kānaka noiʻi i ka gene pololei e hoʻopilikia ai i `(Dextrocardia)`.

Ma kahi o hoʻokahi o ka ʻehā o ka poʻe me `(Dextrocardia)` he maʻi genetic i kapa ʻia ʻo `(Primary Ciliary Dyskinesia)`. Hiki ke hana ʻia kēia maʻi genetic e nā mutations ma mua o 30 mau genes, e like me `DNAI1` a me `DNAH5`. Hiki i kekahi poʻe ke loaʻa nā mutations i loko o kēia mau genes akā ʻaʻole hōʻike i nā hōʻailona a he `(Carriers)`.

Pehea e ʻike ai nā kauka i kēia maʻi?

I kekahi manawa, hiki i nā kauka ke ʻike i ka `(Dextrocardia)` i ka wā e ulu ana ke keiki . Hoʻohana lākou i kahi hoʻāʻo `(Prenatal Ultrasound)` e hana i kēia. Hiki i kēia ke nānā i ke ʻano o ka ulu ʻana o ka puʻuwai o ke keiki a me nā ʻōpū ʻē aʻe. Hiki i kēia `(Imaging Test)` ke hōʻike i ka `(Dextrocardia)` a i ʻole nā ​​​​​​mea ʻē aʻe i loko o ke keiki. Hana ʻia kekahi hoʻāʻo i kapa ʻia ʻo `(Fetal Echocardiogram)` e nānā pono i ka puʻuwai.

Eia nō naʻe, inā ʻaʻole hōʻike nā hoʻokolohua i hana ʻia i ka wā hāpai i kekahi mau pilikia, hiki ke hana ʻia ka ʻike ma hope o ka hānau ʻana. Hōʻike kekahi mau pēpē i nā hōʻailona o ka maʻi puʻuwai hānau ma hope koke o ka hānau ʻana. A laila hana nā kauka i nā hoʻokolohua e ʻike i ka pilikia.

Eia nō naʻe, inā ʻo `(Dextrocardia)` wale nō ka mea i loaʻa, ʻaʻohe hōʻailona, ​​no laila, ʻaʻole paha e ʻike nā keiki i loaʻa ʻole nā ​​​​pilikia puʻuwai nui a i ʻole nā ​​​​maʻi genetic e pili ana i ia no nā makahiki.

Hana nā kauka i kahi hoʻokolohua kino a me nā hoʻokolohua ʻē aʻe e ʻike ai i ka dextrocardia i nā pēpē, nā keiki, a me nā pākeke. I ka wā o ka hoʻokolohua kino, e hoʻolohe ke kauka i kou puʻuwai me kahi stethoscope. Inā lohe maopopo ʻia ka puʻuwai ma ka ʻaoʻao ʻākau o kou umauma, he hōʻailona paha ia o ka dextrocardia.

Inā kānalua ʻia ka dextrocardia, hiki i nā kauka ke hana i nā hoʻokolohua hou aʻe, e like me:

  • X -ray umauma
  • Nānā CT
  • Echocardiogram (Echo) (Lawe kēia i ke kiʻi o ka puʻuwai)
  • Hoʻāʻo Electrocardiogram (ECG/EKG) (Ke ana kēia i ka hana uila o ka puʻuwai)
  • Hoʻāʻo Genetic
  • MRI o ka puʻuwai

Hiki ke ʻike ʻia ka `(Dextrocardia)` i hoʻokaʻawale ʻia ma o kēia mau hoʻokolohua, ʻoi aku hoʻi ma kahi `(ECG/EKG)`. ʻO ia hoʻi, ʻike pinepine ʻia ia i ka wā e ʻimi ana ke kauka i kahi mea ʻē aʻe.

He aha nā maʻi puʻuwai ʻē aʻe e pili pū ana me ka `(Dextrocardia)`?

ʻIke pinepine ʻia ka poʻe i ʻike ʻia me ka "Dextrocardia" he mau maʻi puʻuwai hānau ʻē aʻe. ʻO kekahi o kēia mau mea:

  • ʻO ka Ventricle hema komo pālua (loaʻa iā ia ʻelua ala no ke koko e komo ai i ka ventricle hema o ka puʻuwai)
  • ʻO ka Ventricle ʻĀkau Puka Pālua (hoʻomaka nā kīʻaha koko nui ʻelua mai ka ventricle ʻākau o ka puʻuwai)
  • "He lua i loko o ka puʻuwai" (ʻAtrial Septal Defect, Ventricular Septal Defect a i ʻole Atrioventricular Septal Defect)
  • ʻO ka Atresia Pulmonary (ʻaʻole i ulu pono ka valve o ke aʻa pulmonary a pani loa ʻia paha)
  • ʻO ka Pulmonary Stenosis (ka hoʻohaiki ʻana o ka valve artery pulmonary)
  • Tetralogy o Fallot (kahi hui pū ʻana o nā kīnā puʻuwai ʻehā)
  • Ke hoʻololi ʻana o nā ʻaʻa nui
  • ʻO ka ʻAtresia Tricuspid (ka ulu pono ʻole ʻana o ka valve tricuspid)

He mea paʻakikī iki paha kēia, akā na nā kauka e wehewehe iā ʻoe.

Pehea e mālama ʻia ai ka `(Dextrocardia)`?

I ka ʻōlelo maʻalahi, ʻaʻole pono ka dextrocardia i hoʻokaʻawale ʻia i kekahi lāʻau lapaʻau . Eia nō naʻe, he mea nui e hoʻomaopopo i kekahi kauka e mālama iā ʻoe he loaʻa iā ʻoe kēia maʻi. ʻO kēia no ka mea he mea kōkua iā lākou ke ʻike i kēia loli kūkulu i loko o kou kino i ka wā e hana ana i kekahi mau hoʻokolohua a i ʻole e hana ana i nā mea e like me ke ʻoki kino.

Eia nō naʻe, inā loaʻa iā ʻoe nā maʻi puʻuwai ʻē aʻe a i ʻole kahi maʻi genetic me ka "(Dextrocardia)", e hoʻoholo kāu kauka i ka lāʻau e pono ai no kēlā mau kūlana. No kēlā mau lāʻau lapaʻauHiki i kēia ke komo pū me nā lāʻau lapaʻau, nā kaʻina hana, a i ʻole nā ​​​​ʻoki kino.

Hoʻomaʻamaʻa pinepine ʻia nā maʻi puʻuwai koʻikoʻi i ka wā kamaliʻi. Maopopo iaʻu inā pono kāu keiki i kekahi mea e like me kēia, hiki ke lilo i mea hopohopo loa iā ʻoe. Eia nō naʻe, e hāʻawi ka hui lapaʻau e mālama ana i kāu keiki iā ʻoe i ke kākoʻo a me ke alakaʻi āu e pono ai. E wehewehe lākou i nā mea āpau iā ʻoe, me nā mea e pono ai kāu keiki a pehea e mālama ai iā lākou ma ka home.

Āhea wau e ʻike ai i ke kauka?

Inā loaʻa i kāu keiki ka `(Dextrocardia),` e kamaʻilio me kā lākou kauka e pili ana i ka mea e manaʻo ai i ka wā e hiki mai ana a me nā hōʻailona e makaʻala ai (ʻoi aku ka poʻe e pili ana i nā maʻi puʻuwai a i ʻole nā ​​​​syndromes).

Inā loaʻa iā ʻoe ʻo '(Dextrocardia),' e kamaʻilio me kāu kauka e aʻo pehea e hoʻopilikia ai nā pilikia olakino ʻē aʻe i kou kino, he aha nā hōʻailona e makaʻala ai, a pehea e mālama ai iā lākou.

ʻEhia ka lōʻihi e ola ai kekahi me ka `(Dextrocardia)`?

Hiki i ke kanaka me `(Dextrocardia)` ke ola lōʻihi . Eia nō naʻe, pili ia i nā maʻi ʻē aʻe. ʻO nā pēpē i hānau ʻia me ka `(Dextrocardia)` i hoʻokaʻawale ʻia (ʻo ia hoʻi, me ka ʻole o nā maʻi puʻuwai a i ʻole nā ​​​​syndromes) he ola maʻamau. Eia nō naʻe, ʻo nā pēpē i hānau ʻia me nā maʻi puʻuwai hānau a i ʻole nā ​​​​syndromes genetic e pono ai ka lāʻau lapaʻau a i ʻole ke ʻoki ʻana e mālama i kēlā mau kūlana. No laila, ʻoi aku ka maikaʻi o ke kamaʻilio ʻana me kāu kauka e pili ana i ka mea e manaʻo ai a me ke ʻano o ka wā lōʻihi.

He maʻi laha ʻole ʻo Dextrocardia, akā ua aʻo nui mākou e pili ana i ia mea i nā makahiki i hala. E noʻonoʻo, ua ʻike nā kānaka ʻepekema e pili ana iā ia mai ka makahiki 1600! ʻO ia hoʻi, ʻo ia kekahi o nā kīnā puʻuwai hānau mua i ʻike ʻia. I kēia lā, ʻike mākou hiki ke hana ia ma kāna iho a i ʻole he hōʻailona o kekahi mau maʻi genetic. He mea maʻamau hoʻi no nā pēpē me ka dextrocardia ke loaʻa nā kīnā puʻuwai hānau ʻē aʻe.

ʻO ka mea hope loa, nā mea e hoʻomanaʻo ai (Leka Lawe-Home)

Inā loaʻa iā ʻoe a i ʻole kāu keiki ka `(Dextrocardia)`, mai hopohopo . E kiʻi i ke alakaʻi e pono ai mai kāu kauka. E wehewehe lākou iā ʻoe inā he mau pilikia ʻē aʻe e pono ai ka mālama ʻana.

ʻO ka mea nui loa, ʻo ia ka hoʻomaopopo ʻana i kēlā me kēia kauka a loea olakino paha e mālama iā ʻoe e pili ana i kēia wahi kikoʻī i loko o kou puʻuwai. He mea nui loa paha iā lākou ke ʻike i kēia ʻike i ka wā e mālama ana iā ʻoe.

Manaʻolana wau he mea pono kēia ʻike iā ʻoe. E ola kino!


ʻO Dextrocardia, puʻuwai ma ka ʻaoʻao ʻākau, Situs Inversus, Congenital Heart Defect, maʻi puʻuwai, maʻi genetic, maʻi hānau

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

💬 Comments (0)

ʻAʻohe manaʻo i kau ʻia. Hoʻohui i kāu manaʻo ma ʻaneʻi no ka manawa mua.

Hoʻohui i kāu manaʻo

E ʻoluʻolu e helu: 8 + 1 =
Aia kou puʻuwai ma ka ʻaoʻao ʻākau? E kamaʻilio kākou e pili ana i ka (Dextrocardia)!

Aia kou puʻuwai ma ka ʻaoʻao ʻākau? E kamaʻilio kākou e pili ana i ka (Dextrocardia)!

Ua noʻonoʻo paha ʻoe inā aia kou puʻuwai ma ka ʻaoʻao ʻākau o kou kino, ʻaʻole ma ka hema? ʻĀ, he mea kupanaha, ʻeā? Akā hiki nō paha. ʻO kēia ka mea a mākou e kapa nei he `(Dextrocardia)`. I ka ʻōlelo maʻalahi, aia kou puʻuwai ma ka ʻaoʻao ʻākau o kou umauma, e kū pono ana i ka ʻākau. Ua like ia me ke aniani o ka puʻuwai ma ka hema. ʻO ka maʻamau, aia ko mākou puʻuwai ma ka ʻaoʻao hema o kou umauma, e kū pono ana i ka hema. ʻO kēia kūlana i kapa ʻia ʻo `(Dextrocardia)` ua manaʻo ʻia he kīnā puʻuwai hānau . ʻO ia hoʻi, ua hānau ʻia ʻoe me kēia ʻokoʻa.

I kēia manawa, ke noʻonoʻo nei paha ʻoe, "Auē kuʻu Akua, he mea nui anei kēlā?" ʻOiaʻiʻo, inā loaʻa iā ʻoe wale nō ka `(Dextrocardia)`, ʻo ia hoʻi, aia ka puʻuwai ma ka ʻaoʻao ʻākau, ʻo ka hapa nui o ka manawa ʻaʻole ia he mea koʻikoʻi loa . ʻAʻole ia e hana i kekahi mau hōʻailona, ​​ʻaʻole ia e hoʻoulu i nā pilikia, a ʻaʻole pono ka mālama ʻana. Eia nō naʻe, i kekahi manawa hiki i ka poʻe me `(Dextrocardia)` ke hānau ʻia me nā maʻi olakino ʻē aʻe. Hiki i kēlā mau maʻi ke hoʻoulu i nā pilikia a pono ke mālama ʻia e ke kauka.

He maʻi laha ʻole kēia, e kū ana ma kahi o hoʻokahi i loko o 12,000 mau hāpai ʻana.

He aha nā ʻano nui o `(Dextrocardia)`? ʻO ka puʻuwai wale nō ma ka ʻākau?

ʻAe, hiki i kēia `(Dextrocardia)` ke hele mai i nā ʻano like ʻole. Malia paha ʻo ka puʻuwai wale nō ma ka ʻaoʻao ʻākau, a i ʻole hiki ke hele mai me nā loli i ke kūlana o nā ʻōpū kūloko ʻē aʻe. E nānā kākou i nā ʻano nui:

  • ʻO ka Dextrocardia i hoʻokaʻawale ʻia: ʻO kēia ka manawa e neʻe wale ai kou puʻuwai mai ka ʻaoʻao hema a i ka ʻaoʻao ʻākau. Eia nō naʻe, aia nā ʻāpana ʻē aʻe a pau i kahi kūlana maʻamau. Inā ʻaʻohe maʻi puʻuwai ʻē aʻe, ke hana maʻamau nei ka puʻuwai. ʻAʻohe hōʻailona o kēia.
  • ʻO `Situs Inversus` me `(Dextrocardia)`: Ma kēia, aia kou puʻuwai ma ka ʻaoʻao ʻākau, e like me ke "kiʻi aniani", a aia nā ʻāpana ʻē aʻe i loko o kou umauma a me kou ʻōpū ma ke ʻaoʻao ʻē aʻe. E noʻonoʻo e like me ke akepaʻa ma ka ʻaoʻao hema a aia ka spleen ma ka ʻaoʻao ʻākau. Hiki i kēia kūlana `(Situs Inversu)` ke lilo i hōʻailona o kahi maʻi genetic i kapa ʻia ʻo `(Primary Ciliary Dyskinesia)`. Hiki i kēia maʻi ke hana i nā hōʻailona like ʻole mai ka hānau ʻana.
  • ʻO Dextrocardia me nā kīnā puʻuwai hānau ʻē aʻe: He nui ka poʻe me ka dextrocardia i loaʻa nā maʻi puʻuwai ʻē aʻe e hoʻopilikia ai i ka hana ʻana o ka puʻuwai. Hiki i kēia mau maʻi puʻuwai ke hana i nā hōʻailona, ​​​​nā pilikia, a pono e mālama ʻia.
  • ʻO ka `Heterotaxy Syndrome` me `(Dextrocardia)`: I kēia hihia, aia ka puʻuwai ma ka ʻaoʻao ʻākau, e like me ke "kiʻi aniani". Eia kekahi, aia nā ʻōpū ʻē aʻe ma nā wahi ʻē, ʻaʻole ma kahi e pono ai lākou. Hiki i kēia `(Heterotaxy Syndrome)` ke hana i nā pilikia koʻikoʻi i ka hana ʻana o nā ʻōpū.

He aha nā hōʻailona e hiki ke kū mai ma muli o ka `(Dextrocardia)`?

E like me kā mākou i ʻōlelo ai ma mua, inā ua hoʻokaʻawale ʻia ʻoe ʻo `(Dextrocardia),` ʻo ia hoʻi, aia wale nō ka puʻuwai ma ka ʻaoʻao ʻākau, ʻaʻohe hōʻailona . ʻAʻole paha ʻoe e ʻike aia kou puʻuwai ma ka ʻaoʻao ʻākau, a ua ʻike ʻia ia ma ka hanana i ka wā o kahi `(Imaging Test)` i hana ʻia no kekahi kumu ʻē aʻe.

Eia nō naʻe, inā hui pū ʻia ke kūlana `(Dextrocardia)` me nā kīnā puʻuwai ʻē aʻe a i ʻole nā ​​maʻi genetic, a laila e ʻike ʻia kekahi mau hōʻailona. ʻIke pinepine ʻia kēia mau mea i ka wā ʻōpiopio o ke ola. E nānā i kēia mau hōʻailona:

  • Manaʻo luhi loa.
  • Nā maʻi pinepine o ka māmā a i ʻole nā ​​maʻi sinus.
  • Manaʻo nui i ka luhi a me ka pilikia o ka hanu ʻana i ka wā o ka hana kino.
  • Puʻuwai kūpono ʻole.
  • He uliuli ke ʻano o ka ʻili (ua kapa ʻia kēia he "Cyanosis", ʻo ia hoʻi, ua haʻahaʻa ka oxygen i loko o ke koko).
  • Ke nānā aku nei ka ʻili he keʻokeʻo.
  • Melemele o ka ʻili a me nā maka (e like me ka jaundice).
  • Ka paʻakikī o ka hanu ʻana a i ʻole ka hanu wikiwiki.
  • ʻO ka loaʻa ʻana o ke kaumaha a me nā pilikia ulu (ʻoi aku hoʻi i nā keiki ʻōpio).
  • ʻŪhū me ka huʻa.

He mea nui: Inā loaʻa i kāu keiki kēia mau hōʻailona, ​​​​he mea nui e ʻike koke i ke kauka e ʻike i ke kumu. ʻOiai ʻaʻole i hoʻokumu ʻia kēia mau hōʻailona e ka `(Dextrocardia)` ponoʻī, hiki i nā hoʻokolohua ke ʻike i ke kūlana `(Dextrocardia).`

No ke aha e hana ʻia ai kēia `(Dextrocardia)`? He aha nā kumu?

ʻO ke kumu nui o kēia `(Dextrocardia)` ʻo ia nā loli genetic e kū mai ana i nā wā mua o ka hāpai ʻana . ʻOi aku ma mua o 60 mau genes e kōkua i ka hoʻoholo ʻana i ke ʻano o ke kau ʻana o nā ʻōpū o ko mākou kino. Ke ʻimi nei nā kānaka noiʻi i ka gene pololei e hoʻopilikia ai i `(Dextrocardia)`.

Ma kahi o hoʻokahi o ka ʻehā o ka poʻe me `(Dextrocardia)` he maʻi genetic i kapa ʻia ʻo `(Primary Ciliary Dyskinesia)`. Hiki ke hana ʻia kēia maʻi genetic e nā mutations ma mua o 30 mau genes, e like me `DNAI1` a me `DNAH5`. Hiki i kekahi poʻe ke loaʻa nā mutations i loko o kēia mau genes akā ʻaʻole hōʻike i nā hōʻailona a he `(Carriers)`.

Pehea e ʻike ai nā kauka i kēia maʻi?

I kekahi manawa, hiki i nā kauka ke ʻike i ka `(Dextrocardia)` i ka wā e ulu ana ke keiki . Hoʻohana lākou i kahi hoʻāʻo `(Prenatal Ultrasound)` e hana i kēia. Hiki i kēia ke nānā i ke ʻano o ka ulu ʻana o ka puʻuwai o ke keiki a me nā ʻōpū ʻē aʻe. Hiki i kēia `(Imaging Test)` ke hōʻike i ka `(Dextrocardia)` a i ʻole nā ​​​​​​mea ʻē aʻe i loko o ke keiki. Hana ʻia kekahi hoʻāʻo i kapa ʻia ʻo `(Fetal Echocardiogram)` e nānā pono i ka puʻuwai.

Eia nō naʻe, inā ʻaʻole hōʻike nā hoʻokolohua i hana ʻia i ka wā hāpai i kekahi mau pilikia, hiki ke hana ʻia ka ʻike ma hope o ka hānau ʻana. Hōʻike kekahi mau pēpē i nā hōʻailona o ka maʻi puʻuwai hānau ma hope koke o ka hānau ʻana. A laila hana nā kauka i nā hoʻokolohua e ʻike i ka pilikia.

Eia nō naʻe, inā ʻo `(Dextrocardia)` wale nō ka mea i loaʻa, ʻaʻohe hōʻailona, ​​no laila, ʻaʻole paha e ʻike nā keiki i loaʻa ʻole nā ​​​​pilikia puʻuwai nui a i ʻole nā ​​​​maʻi genetic e pili ana i ia no nā makahiki.

Hana nā kauka i kahi hoʻokolohua kino a me nā hoʻokolohua ʻē aʻe e ʻike ai i ka dextrocardia i nā pēpē, nā keiki, a me nā pākeke. I ka wā o ka hoʻokolohua kino, e hoʻolohe ke kauka i kou puʻuwai me kahi stethoscope. Inā lohe maopopo ʻia ka puʻuwai ma ka ʻaoʻao ʻākau o kou umauma, he hōʻailona paha ia o ka dextrocardia.

Inā kānalua ʻia ka dextrocardia, hiki i nā kauka ke hana i nā hoʻokolohua hou aʻe, e like me:

  • X -ray umauma
  • Nānā CT
  • Echocardiogram (Echo) (Lawe kēia i ke kiʻi o ka puʻuwai)
  • Hoʻāʻo Electrocardiogram (ECG/EKG) (Ke ana kēia i ka hana uila o ka puʻuwai)
  • Hoʻāʻo Genetic
  • MRI o ka puʻuwai

Hiki ke ʻike ʻia ka `(Dextrocardia)` i hoʻokaʻawale ʻia ma o kēia mau hoʻokolohua, ʻoi aku hoʻi ma kahi `(ECG/EKG)`. ʻO ia hoʻi, ʻike pinepine ʻia ia i ka wā e ʻimi ana ke kauka i kahi mea ʻē aʻe.

He aha nā maʻi puʻuwai ʻē aʻe e pili pū ana me ka `(Dextrocardia)`?

ʻIke pinepine ʻia ka poʻe i ʻike ʻia me ka "Dextrocardia" he mau maʻi puʻuwai hānau ʻē aʻe. ʻO kekahi o kēia mau mea:

  • ʻO ka Ventricle hema komo pālua (loaʻa iā ia ʻelua ala no ke koko e komo ai i ka ventricle hema o ka puʻuwai)
  • ʻO ka Ventricle ʻĀkau Puka Pālua (hoʻomaka nā kīʻaha koko nui ʻelua mai ka ventricle ʻākau o ka puʻuwai)
  • "He lua i loko o ka puʻuwai" (ʻAtrial Septal Defect, Ventricular Septal Defect a i ʻole Atrioventricular Septal Defect)
  • ʻO ka Atresia Pulmonary (ʻaʻole i ulu pono ka valve o ke aʻa pulmonary a pani loa ʻia paha)
  • ʻO ka Pulmonary Stenosis (ka hoʻohaiki ʻana o ka valve artery pulmonary)
  • Tetralogy o Fallot (kahi hui pū ʻana o nā kīnā puʻuwai ʻehā)
  • Ke hoʻololi ʻana o nā ʻaʻa nui
  • ʻO ka ʻAtresia Tricuspid (ka ulu pono ʻole ʻana o ka valve tricuspid)

He mea paʻakikī iki paha kēia, akā na nā kauka e wehewehe iā ʻoe.

Pehea e mālama ʻia ai ka `(Dextrocardia)`?

I ka ʻōlelo maʻalahi, ʻaʻole pono ka dextrocardia i hoʻokaʻawale ʻia i kekahi lāʻau lapaʻau . Eia nō naʻe, he mea nui e hoʻomaopopo i kekahi kauka e mālama iā ʻoe he loaʻa iā ʻoe kēia maʻi. ʻO kēia no ka mea he mea kōkua iā lākou ke ʻike i kēia loli kūkulu i loko o kou kino i ka wā e hana ana i kekahi mau hoʻokolohua a i ʻole e hana ana i nā mea e like me ke ʻoki kino.

Eia nō naʻe, inā loaʻa iā ʻoe nā maʻi puʻuwai ʻē aʻe a i ʻole kahi maʻi genetic me ka "(Dextrocardia)", e hoʻoholo kāu kauka i ka lāʻau e pono ai no kēlā mau kūlana. No kēlā mau lāʻau lapaʻauHiki i kēia ke komo pū me nā lāʻau lapaʻau, nā kaʻina hana, a i ʻole nā ​​​​ʻoki kino.

Hoʻomaʻamaʻa pinepine ʻia nā maʻi puʻuwai koʻikoʻi i ka wā kamaliʻi. Maopopo iaʻu inā pono kāu keiki i kekahi mea e like me kēia, hiki ke lilo i mea hopohopo loa iā ʻoe. Eia nō naʻe, e hāʻawi ka hui lapaʻau e mālama ana i kāu keiki iā ʻoe i ke kākoʻo a me ke alakaʻi āu e pono ai. E wehewehe lākou i nā mea āpau iā ʻoe, me nā mea e pono ai kāu keiki a pehea e mālama ai iā lākou ma ka home.

Āhea wau e ʻike ai i ke kauka?

Inā loaʻa i kāu keiki ka `(Dextrocardia),` e kamaʻilio me kā lākou kauka e pili ana i ka mea e manaʻo ai i ka wā e hiki mai ana a me nā hōʻailona e makaʻala ai (ʻoi aku ka poʻe e pili ana i nā maʻi puʻuwai a i ʻole nā ​​​​syndromes).

Inā loaʻa iā ʻoe ʻo '(Dextrocardia),' e kamaʻilio me kāu kauka e aʻo pehea e hoʻopilikia ai nā pilikia olakino ʻē aʻe i kou kino, he aha nā hōʻailona e makaʻala ai, a pehea e mālama ai iā lākou.

ʻEhia ka lōʻihi e ola ai kekahi me ka `(Dextrocardia)`?

Hiki i ke kanaka me `(Dextrocardia)` ke ola lōʻihi . Eia nō naʻe, pili ia i nā maʻi ʻē aʻe. ʻO nā pēpē i hānau ʻia me ka `(Dextrocardia)` i hoʻokaʻawale ʻia (ʻo ia hoʻi, me ka ʻole o nā maʻi puʻuwai a i ʻole nā ​​​​syndromes) he ola maʻamau. Eia nō naʻe, ʻo nā pēpē i hānau ʻia me nā maʻi puʻuwai hānau a i ʻole nā ​​​​syndromes genetic e pono ai ka lāʻau lapaʻau a i ʻole ke ʻoki ʻana e mālama i kēlā mau kūlana. No laila, ʻoi aku ka maikaʻi o ke kamaʻilio ʻana me kāu kauka e pili ana i ka mea e manaʻo ai a me ke ʻano o ka wā lōʻihi.

He maʻi laha ʻole ʻo Dextrocardia, akā ua aʻo nui mākou e pili ana i ia mea i nā makahiki i hala. E noʻonoʻo, ua ʻike nā kānaka ʻepekema e pili ana iā ia mai ka makahiki 1600! ʻO ia hoʻi, ʻo ia kekahi o nā kīnā puʻuwai hānau mua i ʻike ʻia. I kēia lā, ʻike mākou hiki ke hana ia ma kāna iho a i ʻole he hōʻailona o kekahi mau maʻi genetic. He mea maʻamau hoʻi no nā pēpē me ka dextrocardia ke loaʻa nā kīnā puʻuwai hānau ʻē aʻe.

ʻO ka mea hope loa, nā mea e hoʻomanaʻo ai (Leka Lawe-Home)

Inā loaʻa iā ʻoe a i ʻole kāu keiki ka `(Dextrocardia)`, mai hopohopo . E kiʻi i ke alakaʻi e pono ai mai kāu kauka. E wehewehe lākou iā ʻoe inā he mau pilikia ʻē aʻe e pono ai ka mālama ʻana.

ʻO ka mea nui loa, ʻo ia ka hoʻomaopopo ʻana i kēlā me kēia kauka a loea olakino paha e mālama iā ʻoe e pili ana i kēia wahi kikoʻī i loko o kou puʻuwai. He mea nui loa paha iā lākou ke ʻike i kēia ʻike i ka wā e mālama ana iā ʻoe.

Manaʻolana wau he mea pono kēia ʻike iā ʻoe. E ola kino!


ʻO Dextrocardia, puʻuwai ma ka ʻaoʻao ʻākau, Situs Inversus, Congenital Heart Defect, maʻi puʻuwai, maʻi genetic, maʻi hānau

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

💬 Comments (0)

ʻAʻohe manaʻo i kau ʻia. Hoʻohui i kāu manaʻo ma ʻaneʻi no ka manawa mua.

Hoʻohui i kāu manaʻo

E ʻoluʻolu e helu: 8 + 1 =