He aha ka Eisenmenger Syndrome? E kamaʻilio kākou e pili ana i ia mea me nā kikoʻī?

Ua lohe paha ʻoe e hiki i kekahi mau kīnā puʻuwai hānau ke alakaʻi i nā maʻi koʻikoʻi ma hope o ke ola? ʻO kekahi o ia mau maʻi paʻakikī ʻo ia ka maʻi Eisenmenger. He mea hou paha ka inoa iā ʻoe, akā he mea nui e ʻike e pili ana i ia mea, ʻoiai inā he maʻi puʻuwai hānau kekahi o kou ʻohana. E kamaʻilio kākou e pili ana i kēia me nā kikoʻī hou aku, no ka mea, he mea nui loa ka ʻike mua ʻana a me ka ʻike ʻana i kēia maʻi.

He aha maoli ka Eisenmenger Syndrome?

I ka ʻōlelo maʻalahi, ʻo ka Eisenmenger Syndrome kahi maʻi e kū mai ana i ka wā e kahe nui ai ke koko ma o nā kīʻaha koko (nā aʻa) e lawe ana i ke koko mai kou puʻuwai a i kou mau māmā. E noʻonoʻo e like me ka wai e kahe wikiwiki ana ma o kahi faucet. ʻO kēia ka hopena i ke koko kiʻekiʻe i loko o nā kīʻaha koko o kou mau māmā a ma ka ʻaoʻao ʻākau o kou puʻuwai, kahi maʻi i kapa ʻia ʻo Pulmonary Hypertension . Ua like ia me ka hoʻāʻo ʻana e hoʻokuke i kahi nui o ka wai ma o kahi paipu liʻiliʻi, kahi e hana ai i ka nui o ke kaomi i loko o ka paipu.

Eia kekahi, hoʻomaka ke koko e kahe pono ʻole ma waena o nā ʻaoʻao hema a me ka ʻākau o ka puʻuwai ('blood shunting`). ʻO ke ʻano kēia ma muli o kahi pilina kūpono ʻole (e like me ka lua i loaʻa i ka wā hānau), kahe ke koko mai ka ʻaoʻao hema o ka puʻuwai (waiwai i ka oxygen) i ka ʻaoʻao ʻākau (haʻahaʻa i ka oxygen). I ka hala ʻana o ka manawa, hiki ke hoʻohuli ʻia kēia kūlana, ʻo ia hoʻi ke kahe nei ke koko me ka oxygen liʻiliʻi mai ka ʻaoʻao ʻākau a i ka hema.

ʻO kēia kūlana, i kapa ʻia ʻo Eisenmenger syndrome, e kū pinepine ana i ka wā e waiho ʻole ʻia ai kekahi a ʻoi aku paha nā kīnā puʻuwai hānau ʻole a ʻike ʻole ʻia paha . Inā hoʻomau kēia kūlana no ka manawa lōʻihi, hiki iā ia ke hōʻeha mau i ka māmā a me nā pilikia ʻē aʻe e hoʻoweliweli ana i ke ola. ʻO ia ke kumu he kūlana kēia e pono ai ka nānā pono ʻana.

ʻO wai ka mea i ʻoi aku ka paʻakikī o ka loaʻa ʻana o kēia maʻi?

ʻO ka maʻi Eisenmenger kahi maʻi e kū pinepine ana i nā keiki a me nā ʻōpio i hānau ʻia me ka Ventricular Septal Defect (VSD), he lua ma ka paia ma waena o nā keʻena pumping ʻelua o lalo o ka puʻuwai (nā ventricles hema a me ka ʻākau).

Eia kekahi, hiki ke loaʻa ka maʻi Eisenmenger ke mālama ʻole ʻia kekahi mau kīnā puʻuwai hānau ʻē aʻe. Eia kekahi mau laʻana:

• ʻO ke kīnā o ke kahawai atrioventricular
• ʻO ke kīnā septal atrial
• ʻO ka maʻi puʻuwai cyanotic (kahi e polū ai ke kino)
• ʻO ka patent ductus arteriosus (kahi kīʻaha koko i manaʻo ʻia e pani ma hope o ka hānau ʻana)
• Tetralogy o Fallot (kahi hui pū ʻana o nā kīnā puʻuwai ʻehā)
• Truncus arteriosus `(Truncus arteriosus)`

ʻO kekahi mea ʻē aʻe, ʻo ia ka Down syndrome.ʻOi aku ka nui o ka pilikia o nā keiki me Down syndrome i ka loaʻa ʻana o ka maʻi puʻuwai hānau. ʻO ka hopena, ʻoi aku ka maʻalahi o lākou i ka maʻi Eisenmenger. ʻO ka ʻoiaʻiʻo, hōʻike nā helu helu ma waena o 25% a me 50% o nā pākeke me Eisenmenger syndrome he Down syndrome nō hoʻi.

Pehea ka maʻamau o ka maʻi Eisenmenger?

ʻO ka mea pōmaikaʻi, he maʻi laha ʻole ka maʻi Eisenmenger. Hoʻopilikia ia ma waena o 1% a me 6% o nā pākeke i hānau ʻia me kahi kīnā puʻuwai hānau. Eia nō naʻe, ʻoiai he mea laha ʻole ia, he mea nui e makaʻala iā ia ma muli o kona koʻikoʻi.

He aha ke kumu o ka maʻi Eisenmenger?

I mea e maopopo pono ai ke kumu o kēia, pono ʻoe e loaʻa kahi manaʻo iki pehea e kahe ai ke koko i loko o ko kākou puʻuwai. E noʻonoʻo ʻoe ua like ko kākou puʻuwai me kahi hale me ʻehā lumi.

ʻO ke kahe koko i loko o ka puʻuwai olakino e hana ʻia penei:

1. Atrium ʻākau: ʻO ke koko i hoʻohana ʻia a nele i ka oxygen o ke kino e hele mua mai a hōʻiliʻili ma ʻaneʻi. A laila hoʻopuka ʻia kēia koko i ka ventricle ʻākau.

2. Ventricle ʻākau: ʻO kēia kahi e hoʻouna ʻia ai ke koko nele i ka oxygen i nā māmā e loaʻa ai ka oxygen hou.

3. Atrium hema: ʻO ke koko maʻemaʻe i hoʻopiha ʻia me ka oxygen i loko o nā māmā e hoʻi i ka puʻuwai ma ʻaneʻi. A laila hoʻouna ʻia kēia koko i ka ventricle hema.

4. Ventricle hema: ʻO kēia ka pamu nui o ka puʻuwai. Maanei e hoʻolaha ʻia ai ke koko waiwai i ka oxygen ma ke kino holoʻokoʻa.

I kēia manawa, e noʻonoʻo he kīnā kūkulu ko ka puʻuwai, e like me ka lua ma ka paia ma waena o nā ventricles ʻākau a me hema (VSD). He aha ka mea e hana ʻia? Hoʻomaka ke koko i waiwai i ka oxygen (ma ka ʻaoʻao hema) a me ke koko i nele i ka oxygen (ma ka ʻaoʻao ʻākau) e hui pū. ʻO ka hopena, nui ke koko e kahe ana i nā māmā. ʻO kēia ke kumu o ka hypertension pulmonary i ʻōlelo ʻia ma luna. Eia kekahi, ua emi ka nui o ke koko waiwai i ka oxygen e pono ai ke hele i ke koena o ke kino. ʻO kēia ka pilikia nui o ka maʻi Eisenmenger.

He aha nā hōʻailona o ka maʻi Eisenmenger?

Hiki ke ʻokoʻa nā hōʻailona o ka maʻi Eisenmenger mai kēlā kanaka a kēia kanaka. Aia lākou i ke ʻano o ka hemahema o ka puʻuwai a me nā ʻōpū i hoʻopilikia ʻia. ʻO ka pinepine, ʻaʻole ʻike ʻia kēia mau hōʻailona i ka manawa hoʻokahi. Hoʻomaka pinepine lākou e ʻike ʻia i ka wā ʻōpio a i ʻole ka wā ʻōpiopio. A laila, e ʻoi aku ka ʻino o nā hōʻailona.

Eia kekahi o nā hōʻailona i ʻike pinepine ʻia:

• ʻEha a paʻa paha ka umauma (Angina)
• Puʻuwai kūpono ʻole (Arrhythmias) - ʻO ke ʻano kēia, ke kuʻi nei ka puʻuwai ma nā ʻano like ʻole ma kahi o hoʻokahi ʻano.
• Ka hoʻonui ʻia ʻana o nā wēlau o nā kui lima a me ke kūlou ʻana o nā kui (Clubbing) - e like me ka wēlau o ka lāʻau pahu.
• Ke ʻū ʻana i ke koko.
• ʻO ke kala ʻili polū a hina paha (Cyanosis) - Hoʻokumu ʻia kēia e ka emi ʻana o ka nui o ka oxygen i loko o ke koko.
• Ka poniuniu a i ʻole ka māʻule ʻana.
• Ka pehu ʻana o nā wāwae, nā kuʻekuʻe wāwae, nā wāwae, a i ʻole ka ʻōpū (edema).
• Ke manaʻo nei e kuʻi wikiwiki ana kou puʻuwai, ke lohe nei i ke kani o kou umauma e kuʻi ana (heart palpitations).
• Luhi nui a me ka nele i ka ikaika (Lethargy).
• Dyspnea - Paʻakikī ka hanu ʻana ʻoiai me ka hoʻoikaika iki ʻana.

Inā loaʻa iā ʻoe kekahi a ʻoi aku paha o kēia mau hōʻailona, ​​​​he mea nui loa e ʻimi koke i ke kōkua lapaʻau.

He aha nā pilikia e hiki ke loaʻa mai ka maʻi Eisenmenger?

ʻO ka mea pōʻino, ʻaʻole ka maʻi Eisenmenger he maʻi e noho mau ana ma kahi hoʻokahi. Hiki iā ia ke alakaʻi i nā pilikia olakino like ʻole. ʻO kekahi o lākou:

• Ke kahe nei ke koko i loko o ka lolo.
• ʻŌpū lolo ma muli o ka maʻi.
• ʻAʻole lawa ka lako koko i ka lolo (Cerebral vascular insufficiency).
• ʻO ka ʻōpū.
• Maʻi hohola.
• Ka hāʻule ʻana o ka puʻuwai.
• Nā maʻi puʻuwai, no ka laʻana, endocarditis.
• Ka mānoanoa o ke koko (Hyperviscosity syndrome).
• Ka hāʻule ʻana o nā puʻupaʻa.
• Nā pilikia i ka wā hāpai (he mea weliweli loa kēia).
• Hahau.
• Make koke.

Ke nānā nei i kēia mau pilikia, hiki iā ʻoe ke ʻike i ke koʻikoʻi o kēia kūlana, ʻeā? ʻO ia ke kumu e pono ai mākou e makaʻala kūikawā i kēia.

Pehea e ʻike ʻia ai ka maʻi Eisenmenger?

E nānā pinepine ke kauka i nā hōʻailona o ka maʻi Eisenmenger i ka wā o ka hoʻokolokolo kino. Eia kekahi laʻana, inā he uliuli kou ʻili, inā ua ʻūlū ʻia kou mau manamana lima, a inā lohe ʻoe i nā leo ʻē i ka wā e hoʻolohe ana i kou puʻuwai.

A laila, hiki i ke kauka ke kauoha i hoʻokahi a ʻoi aku paha o nā hoʻokolohua aʻe e hōʻoia i ka hōʻailona:

• Ke nānā nei i ka pae oxygen i loko o ke koko.
• Catheterization Cardiac: Hoʻokomo kēia i ka hoʻokomo ʻana i kahi ʻōmole liʻiliʻi i loko o ka puʻuwai e ana i ke kaomi a nānā i kona ʻano.
• X-ray umauma.
• Helu koko piha (CBC).
• ʻEchocardiogram (Echocardiogram - echo): He scan ultrasound kēia o ka puʻuwai. Hiki iā ia ke nānā i nā keʻena o ka puʻuwai, nā valves, a me ke kahe ʻana o ke koko.
• Electrocardiogram (EKG/ECG): Hoʻāʻo kēia i ka hana uila o ka puʻuwai.
• He hoʻāʻo MRI puʻuwai.
• Hoʻāʻo hana puʻuwai.

Hiki i ke kauka ke ʻike pololei i ka maʻi ma muli o ka ʻike i loaʻa mai kēia mau hoʻokolohua.

Pehea e mālama ʻia ai ka maʻi Eisenmenger?

ʻO ka pahuhopu nui o ka mālama ʻana i ka maʻi Eisenmenger ʻo ia ke kāohi i nā hōʻailona a pale i ka hōʻino hou ʻana i ka puʻuwai a i ʻole nā ​​​​māmā.

Hiki ke hoʻohana ʻia kēia mau mea ma ke ʻano he lāʻau lapaʻau:

• Nā lāʻau antibiotic: Kāohi i nā maʻi bacteria i loko o ka puʻuwai a me nā māmā.
• Nā Anticoagulants: Hoʻēmi i ke kūkulu ʻia ʻana o nā clots koko i loko o nā kīʻaha koko.
• Diuretics (nā lāʻau wai): E hōʻemi i ka nui o ka wai keu e hōʻiliʻili ana i loko o ke kino.
• ʻO nā antagonists receptor endothelin pālua: He ʻano lāʻau lapaʻau kūikawā kēia i hāʻawi ʻia e hōʻemi i ke koko kiʻekiʻe i loko o nā māmā.
• Nā mea hoʻohui hao: E mālama i ka anemia i hoʻokumu ʻia e ka nele i ka hao.
• Oxygen pākuʻi: E maʻalahi ka hanu ʻana a hoʻonui i nā pae oxygen i loko o ke koko.

ʻO ka mea nui, i ka wā e ulu ai ka maʻi Eisenmenger, ua lohi pinepine ka hoʻoponopono ʻana i ke kīnā puʻuwai hānau ma ke ʻoki kino, no ka mea, i kēlā manawa ua hana mua ʻia ka hōʻino ʻana i nā māmā.

Eia nō naʻe, pono paha i kekahi poʻe me nā hōʻailona koʻikoʻi loa a me ka hōʻino nui ʻana o nā kino i kahi hoʻoili puʻuwai a māmā paha. Akā he hana paʻakikī a pilikia hoʻi kēlā.

Hiki ke pale ʻia ka maʻi Eisenmenger?

ʻAe, ʻo ke ala wale nō e pale aku ai i ka maʻi Eisenmenger, ʻo ia ka ʻike ʻana i nā kīnā puʻuwai hānau i ka wā hikiwawe loa, i ka wā ʻōpiopio o ke ola, a mālama pono iā lākou, a inā pono, e hana i ke ʻoki kino. Inā ʻike ʻia a mālama ʻia kēia mau kīnā i ka wā kamaliʻi, aia kahi manawa kūpono e pale aku ai i kahi maʻi koʻikoʻi e like me ka maʻi Eisenmenger.

He aha ke kūlana o ke ola no nā kānaka me ka maʻi Eisenmenger?

ʻOi aku ka pōkole o ke ola o ka poʻe me ka maʻi Eisenmenger ma mua o ka heluna kanaka maʻamau. ʻO kēia ma muli o nā pilikia e hele mai me ke ʻano. Eia nō naʻe, ola kekahi poʻe a hiki i ka makahiki waena. ʻO ka lōʻihi o ka manawa e hiki ai iā lākou ke ola ma muli o nā mea e like me ke koʻikoʻi o kā lākou mau hōʻailona, ​​​​ke ʻano o ka hemahema puʻuwai hānau, a pehea lākou e pane ai i ka lāʻau. No laila, he mea nui e hahai i ka ʻōlelo aʻo a kāu kauka a mālama i kou olakino.

Inā loaʻa iaʻu ka maʻi Eisenmenger, hiki iaʻu ke hāpai?

He nīnau koʻikoʻi loa kēia. He mea weliweli loa ka hāpai ʻana no kekahi me ka maʻi Eisenmenger. Hiki iā ia ke alakaʻi i nā pilikia koʻikoʻi e like me ka hāʻule ʻana o ka puʻuwai, nā ʻūpā koko, a me ka make koke. Inā loaʻa iā ʻoe kēia maʻi a ke noʻonoʻo nei e hāpai, pono ʻoe e ʻike i kahi loea i nā maʻi puʻuwai hānau makua (`(specialist in adult congenital heart conditions)`) e kūkākūkā i kēia mau pilikia. ʻO ia ka mea hiki ke hāʻawi iā ʻoe i ka ʻōlelo aʻoaʻo maikaʻi loa.

Pehea e hiki ai iaʻu ke mālama iaʻu iho me ka maʻi Eisenmenger?

Inā loaʻa iā ʻoe ka maʻi Eisenmenger, aia kekahi mau mea hiki iā ʻoe ke hana e hōʻemi i kou pilikia o nā pilikia. ʻO ka hahai ʻana i kēia mau ʻanuʻu e kōkua i ka hoʻomaikaʻi ʻana i kou ola a me ke ʻano o ke ola.

Nā mea e hana ai:

• E ʻai i ka meaʻai sodium-controlled: ʻO ka ʻai ʻana i ka paʻakai nui e hiki ke hoʻopaʻa i ka wai a hoʻonui i ke koko.
• E kiʻi i nā lāʻau pale kūpono: E pale iā ʻoe iho mai nā maʻi e like me ka niumonia a me ka maʻi palū.
• E inu i ka wai he nui a mai hoʻokuʻu i kou kino e maloʻo (`(Noho hydrated)`) : Akā ma ka nui wale nō i ʻōlelo ʻia e kāu kauka.
• E hahai pono i nā lāʻau lapaʻau a pau a me nā lāʻau lapaʻau ʻē aʻe i kuhikuhi ʻia e kāu kauka puʻuwai. Mai poina i hoʻokahi mahele lāʻau.
• E lawe i nā lāʻau antibiotic ma mua o ka mālama ʻana i nā niho a i ʻole ke ʻoki ʻana: Hiki i kēia ke kōkua i ka pale ʻana i nā maʻi puʻuwai. E nīnau i kāu kauka e pili ana i kēia.

Nā mea pono ʻole e hana:

• Mai hele i nā wahi kiʻekiʻe loa ma luna o ka ʻilikai (`(Nā wahi kiʻekiʻe)`): Hiki ke hoʻonui ʻia nā pilikia hanu ma muli o ka nele o ka oxygen ma nā wahi kiʻekiʻe.
• E hōʻalo i ka hoʻohana ʻana i nā sauna, nā lumi mahu, a i ʻole nā ​​​​ʻauʻau wela: Hiki i kēia ke hoʻoulu i ka hāʻule koke o ke koko.
• E hōʻalo loa i ka puhipaka a i ʻole ka hoʻohana ʻana i nā huahana paka.
• E hōʻalo i ka hoʻoikaika kino: E hana wale i ka hoʻoikaika kino māmā ma kahi pae i ʻae ʻia e kāu kauka.

Leka Lawe-Home

ʻO ka maʻi Eisenmenger kahi kūlana i loaʻa ai ke koko kiʻekiʻe i loko o nā kīʻaha koko o nā māmā a me ka ʻaoʻao ʻākau o ka puʻuwai. Hoʻokumu pinepine ʻia ia e nā kīnā puʻuwai hānau i mālama ʻole ʻia. Hoʻomaka pinepine nā hōʻailona e ʻike ʻia i ka wā ʻōpio a i ʻole ka wā makua ʻōpio. ʻO nā hōʻailona e komo pū me ka ʻili polū (cyanosis), ka pōkole o ka hanu i ka wā hoʻoikaika kino, a me ka puʻuwai puʻuwai kūpono ʻole.

ʻO ke kumu nui o ka mālama ʻana no kēia maʻi, ʻo ia ka hōʻoluʻolu ʻana i nā hōʻailona a me ka hōʻemi ʻana i ka hōʻino ʻana i ka puʻuwai a me nā māmā. Ua lohi loa ka hoʻōla ʻana i kēia maʻi me ke ʻoki kino. No laila, ʻoi aku ka maikaʻi o ka ʻike ʻana a me ka mālama ʻana i nā kīnā puʻuwai hānau i ka wā hikiwawe loa.

Inā he mau nīnau hou aku kāu e pili ana i kēia, mai makaʻu e kamaʻilio me kāu kauka. E kōkua lākou iā ʻoe.

ʻO ka maʻi Eisenmenger, maʻi puʻuwai, ke koko kiʻekiʻe o ka pulmonary, cyanosis, nā kīnā puʻuwai hānau ʻia, nā pilikia hanu, ke olakino puʻuwai