I kekahi manawa, hiki iā kākou ke loaʻa nā pilikia i loko o ko kākou kino a kākou e noʻonoʻo ʻole ai, ʻeā? Malia paha ke ʻike nei ʻoe i ke kauka no kekahi mea ʻē aʻe, a i ʻole ke hana nei ʻoe i kahi hoʻāʻo ulia pōpilikia, a ʻike ʻoe aia kekahi mea liʻiliʻi i loko o kou puʻuwai, malia paha he puʻupuʻu liʻiliʻi. Ke lohe ʻoe i ka huaʻōlelo 'puʻupuʻu puʻuwai', lele koke kou puʻuwai a makaʻu ʻoe. Akā, pono ʻoe e hoʻomanaʻo ʻaʻole nā puʻupuʻu āpau he maʻi kanesa . I kēia lā, e kamaʻilio mākou e pili ana i kahi ʻano puʻupuʻu e ulu ana i loko o ka puʻuwai, akā ʻaʻole ia he maʻi kanesa, akā pono kekahi nānā. Kāhea nā kauka i kēia he papillary fibroelastoma . ʻOiai paha he lōʻihi iki ka inoa, e kamaʻilio maʻalahi kākou e pili ana.
He aha ka Papillary Fibroelastoma?
I ka ʻōlelo maʻalahi, ʻo kēia papillary fibroelastoma he puʻupuʻu ʻaʻole kanesa (benign) e kū mai ana i loko o ka puʻuwai. ʻO ke ʻano kēia, ʻaʻole ia he kanesa a ʻaʻole e laha i nā ʻāpana ʻē aʻe o ke kino. Ua kapa ʻia kēia mau mea he mau puʻupuʻu puʻuwai mua no ka mea hoʻomaka lākou i loko o ka puʻuwai ponoʻī. ʻAʻole lākou e hele mai i ka puʻuwai mai kahi ʻē aʻe.
Eia nō naʻe, ʻoiai ʻaʻole ia he maʻi kanesa, ʻaʻole ia he palekana loa. No ka mea, hiki i kēia puʻupuʻu ke lilo i embolic. ʻO ke ʻano o ka embolic, e noʻonoʻo, hiki i kahi ʻāpana liʻiliʻi o kēia puʻupuʻu ke haki a hele pū me ke koko, e paʻa ana i loko o kahi kīʻaha koko ma kahi ʻē aʻe o ke kino. Inā hana ʻia kēlā, aia kahi hiki ke loaʻa nā pilikia koʻikoʻi e like me ka hahau ʻana .
I ka hapanui o ka manawa, ma kahi o ʻewalu o ka ʻumi, e ulu ana nā fibroelastomas papillary ma nā kiwikā o ka puʻuwai. ʻO ka ʻoiaʻiʻo, ʻo ia ke ʻano maʻamau o ka puʻuwai e ulu a puni nā kiwikā o ka puʻuwai.
ʻO wai nā kiwikā puʻuwai e loaʻa pinepine ai kēia mau mea?
Loaʻa pinepine kēia mau puʻupuʻu ma nā kiwikā ma ka ʻaoʻao hema o ka puʻuwai. ʻO ia hoʻi, ma ka kiwikā aortic (ka mea maʻamau) a i ʻole ka kiwikā mitral . I kekahi manawa, hana lākou ma ka kiwikā tricuspid a i ʻole ka kiwikā pulmonary ma ka ʻaoʻao ʻākau o ka puʻuwai.
ʻO ka nūhou maikaʻi, ʻaʻole pinepine nā fibroelastomas papillary e hoʻopilikia nui i ka hana o nā valves puʻuwai. ʻO kēia no ka mea aia kēia mau puʻupuʻu ma ka ʻaoʻao ma lalo o ka valve, ʻo ia hoʻi ka ʻaoʻao kahi e kahe ai ke koko ma mua o ka valve.
ʻO kēia ke kumu i ʻokoʻa ai kēia mau puʻupuʻu mai kekahi ʻano puʻupuʻu puʻuwai i kapa ʻia ʻo cardiac myxoma . ʻOi aku ka nui o nā myxomas a ʻoi aku ka nui o ka hoʻopilikia ʻana i ka hana o nā valves ma mua o nā papillary fibroelastomas. ʻO kekahi mea ʻē aʻe, ʻaʻole pili pinepine nā myxomas i nā valves, ʻaʻole like me nā papillary fibroelastomas.
ʻAuhea maoli kēia nati i loko o ka puʻuwai?
E like me kā mākou i ʻōlelo ai ma mua, aia ka hapa nui o kēia mau puʻupuʻu ma nā valves o ka puʻuwai. Ma kahi o 95 pakeneka (95%) o lākou aia ma ka ʻaoʻao hema o ka puʻuwai.He mea kākaʻikahi loa, ulu kēia mau mea ma ka paia o loko o nā keʻena o ka puʻuwai, ʻoiai ka ventricle hema.
Pehea ka hopena o ka papillary fibroelastoma i ke kino?
ʻO kēia ka mea nui loa e makaʻala ai. Hiki i ka papillary fibroelastoma ke hana i nā ʻūpā koko e hana a hele i loko o ke koko. ʻO nā ʻūpā koko e hele ana ma kēia ʻano ua kapa ʻia ʻo emboli . Hiki i kēia mau emboli ke hele i nā ʻāpana like ʻole o ke kino a paʻa. Eia kekahi laʻana:
- Lolo: Inā hana kēia , hiki ke loaʻa kahi hahau .
- Nā aʻa coronary: Hiki i kēia ke hōʻeha i ka puʻuwai .
- nā puʻupaʻa
- Nā māmā
- Nā retina o nā maka
- ʻO ke kaula iwi kuamoʻo
Ma muli o kēia ʻano koko e paʻa ana a me ke ālai ʻana,
- Maʻi hohola
- Hahau
- Hiki ke hana ʻia nā mea e like me ka ventricular fibrillation (kahi kūlana koʻikoʻi kahi e paʻi ai ka puʻuwai i ka wikiwiki a me ke ʻano kūpono ʻole).
Eia kekahi, inā aia ka puʻupuʻu ma ka valve aortic, hiki iā ia ke ālai i nā aʻa coronary e hoʻolako koko i ka puʻuwai. Hiki i kēia ke hana i ka angina , kahi ʻeha umauma e kū mai ana ke loaʻa ʻole ke koko i ka puʻuwai, i ka wā hoʻoikaika kino. Aia kekahi pilikia o ka make koke ʻana o ka puʻuwai .
ʻO wai ka mea i hoʻopilikia nui ʻia e kēia kūlana?
ʻIke pinepine ʻia nā papillary fibroelastomas i nā pākeke ma luna o 40 mau makahiki. ʻO ka hapa pinepine, ʻike ʻia ka maʻi ma kahi o 60 mau makahiki. He mea kākaʻikahi loa, hiki ke ulu kēia mau puʻupuʻu i nā pēpē a me nā keiki ʻōpio me nā kīnā puʻuwai hānau .
Pehea ka maʻamau o ka papillary fibroelastoma?
ʻO nā puʻupuʻu puʻuwai mua, e hoʻomaka ana i loko o ka puʻuwai, he mea kākaʻikahi loa ia. Hoʻopilikia lākou i ka liʻiliʻi ma mua o hoʻokahi i loko o 2,000 mau kānaka. ʻO kēia mau puʻupuʻu puʻuwai mua, ʻo nā ʻano ʻelua ʻaʻole maʻi kanesa maʻamau ka papillary fibroelastoma a me ka cardiac myxoma. Akā he paʻakikī ke ʻōlelo pololei i ko lākou ʻano maʻamau, no ka mea, ʻike pinepine ʻia lākou ma hope o ka make ʻana o kekahi.
He aha nā hōʻailona?
ʻO ka mea kupanaha, ʻoi aku ma mua o ka hapalua o ka poʻe me kēia maʻi ʻaʻole hōʻike i kekahi mau hōʻailona. ʻO ka poʻe i loaʻa nā hōʻailona e ʻike paha i nā mea e like me:
- Angina: ʻEha a ʻeha paha ka umauma.
- Syncope: Poho o ka ʻike.
- Pōkole o ka hanu.
- ʻO ka Transient Ischemic Attack (TIA) a i ʻole ka Stroke: ʻO ka TIA kahi emi ʻana o ke kahe koko i ka lolo no ka manawa pōkole, e like me ka mini-stroke, me nā hōʻailona e nalowale i loko o kekahi mau minuke.
He aha ke kumu o kēia?
ʻAʻole ʻike ʻia ke kumu kikoʻī o nā fibroelastomas papillary. Eia nō naʻe, manaʻo ka nui o nā kānaka ʻepekema ua hana ʻia lākou e ka hōʻino ʻia ʻana o nā pūnaewele endothelial e uhi ana i loko o ka puʻuwai. Ua manaʻo ʻia e hōʻiliʻili nā ʻōpū koko liʻiliʻi, hele i kahi i hōʻino ʻia, a hana mālie i kahi puʻupuʻu e like me ka puʻupuʻu.
Pehea ʻoe e ʻike ai i kēia?
ʻO ka hapa nui o ka manawa, ʻike ʻia ka papillary fibroelastoma ma ke ʻano ulia. ʻO ia hoʻi, ʻike ke kauka i ka puʻupuʻu i ka wā o kahi hoʻokolohua āu e hana nei no kekahi kumu ʻē aʻe. A i ʻole, hiki ke ʻike ʻia i ka wā e loaʻa ai i kekahi ka hahau a ke hoʻāʻo nei e ʻike i ke kumu.
ʻO ka hoʻāʻo nui e ʻike ai i kēia, ʻo ia ka echocardiography . He scan kēia o ka puʻuwai.
- ʻO ka mea mua, hana pinepine nā kauka i kahi echo transthoracic , ʻo ia hoʻi, hana ʻia ia ma ka ʻili o ka umauma.
- Akā i kekahi manawa, no ka nānā ʻana i nā puʻupuʻu liʻiliʻi loa a i ʻole e ʻike maopopo i ka wahi i hoʻopilikia ʻia , hiki ke hana ʻia kahi transesophageal echo (TEE) . Pili kēia i ka hoʻokomo ʻana i kahi ʻōmole liʻiliʻi i lako me ke kāmela ma o ka esophagus e nānā i ka puʻuwai.
Pehea ke ʻano o kēia puʻupuʻu ma ka Echo?
Ma kahi echocardiogram, ua like kēia papillary fibroelastoma me kahi anemone kai! ʻO ia no ka mea he mau ʻano lālā liʻiliʻi kona i kapa ʻia he mau lau papillary e ʻō aku ana mai kona ʻili.
He liʻiliʻi kēia hua maʻamau (ʻaʻole iʻoi aku ma mua o 1 kenimika). Eia kekahi, ua uhi ʻia e kahi kumu/ʻōpuʻu . ʻAe kēia kumu i ka hua e neʻe maikaʻi a puni, ʻo ia hoʻi, he neʻe ia .
He aha ka lāʻau lapaʻau?
ʻO ke ʻoki ʻana ke ʻano maʻamau no ka papillary fibroelastoma. I ka wā o ke ʻoki ʻana, ʻo ke kauka lapaʻau:
- Hoʻopau ʻia ka puʻupuʻu holoʻokoʻa.
- Nānā lākou i nā ʻāpana ʻē aʻe o ka puʻuwai e ʻike inā he mau puʻupuʻu hou aʻe.
- Inā ua hōʻino ka puʻuwai i kekahi ʻāpana o ka puʻuwai, e hoʻoponopono ʻia nō hoʻi. Hiki i kēia ke komo pū me ka hoʻoponopono ʻana i ka valve a i ʻole ke pani ʻana i ka valve.
ʻO ka mea nui, ʻoiai inā ʻaʻohe ou hōʻailona, hiki i kāu kauka ke ʻōlelo i ke ʻoki ʻana e hōʻemi i nā pilikia e hiki mai ana.
Hana pinepine ʻia ke ʻoki ʻana me ka hoʻohana ʻana i nā ʻano hana open-puʻuwai kuʻuna, akā no kekahi poʻe , hoʻohana ʻia nā ʻano robotic minimally invasive.Hiki iā ʻoe ke hoʻohana. E kamaʻilio me kāu kauka e hoʻoholo i ke ʻano hana kūpono loa iā ʻoe.
Pēlā nō , inā he mea pilikia loa ke ʻoki ʻana iā ʻoe, hiki i kāu kauka ke hoʻoholo e kuhikuhi i nā anticoagulants, a i ʻole nā lāʻau hoʻokahe koko , e hōʻemi i ka pilikia o nā ʻaʻa koko.
Pehea ke kūlana ma hope o ka mālama ʻana? (Prognosis)
He maikaʻi loa ka wānana no ka poʻe i hana ʻia i ke ʻoki ʻana e wehe i kahi papillary fibroelastoma. He haʻahaʻa loa ka pilikia o ka hoʻi hou ʻana mai o ka puʻupuʻu. Eia kekahi, ʻoiai ʻaʻole ia he maʻi kanesa, ʻaʻohe pilikia o ka laha ʻana i nā ʻāpana ʻē aʻe o ke kino.
Āhea wau e ʻike ai i ke kauka?
ʻIke pinepine ʻia kēia ʻano puʻupuʻu i loko o ka puʻuwai ma ke kūlana kūpono. ʻO ia ke kumu he mea nui e mālama i kāu mau manawa lapaʻau a me nā hahai ʻana. ʻOi aku ka maʻalahi o ka mālama ʻana i ka ʻike mua ʻana i nā puʻupuʻu. Inā ʻaʻole mālama ʻia, hiki i nā papillary fibroelastomas ke ulu a hoʻoulu i nā pilikia koʻikoʻi.
Inā loaʻa iā ʻoe kahi ʻoki puʻuwai hāmama e wehe i kahi puʻupuʻu, pono kou kino i ka manawa e ho'ōla ai. E kamaʻilio me kāu kauka e pili ana i nā mea e hana ʻole ai a me nā kapu hana āu e hahai ai no kekahi mau pule ma hope o ke ʻoki ʻana. Hiki ke kuhikuhi ʻia ʻoe i kahi papahana hoʻoponopono puʻuwai e kōkua iā ʻoe e hoʻihoʻi i kou ikaika.
He aha nā nīnau e pono iaʻu e nīnau aku i ke kauka?
Inā ua ʻike ʻia ʻoe me ka papillary fibroelastoma, e nīnau i kāu kauka i kēia mau nīnau:
- Pehea ka nui o ka puʻupuʻu?
- Ma hea ia?
- Pehea kona hopena i koʻu puʻuwai?
- Pono anei au i ke ʻoki kino? Inā pēlā, pehea ka wikiwiki?
- Pehea wau e hoʻomākaukau ai no ke ʻoki kino?
- Pehea ka manawa ho'ōla?
- He aha nā pilikia o ke ʻoki kino?
- Pehea lā koʻu kūlana ma hope o ka mālama ʻia ʻana?
- ʻEhia ka lōʻihi ma mua o koʻu hoʻi ʻana mai no nā hoʻokolohua?
He aha ke ʻano o ka puʻuwai puʻuwai?
ʻO kahi puʻupuʻu ma kou puʻuwai he ulu ʻano ʻē (tumor) i loko o ka puʻuwai. Kāhea nā kauka i kēia mau puʻupuʻu cardiac . Hiki i kēia mau puʻupuʻu puʻuwai ke maʻi kanesa a ʻaʻole paha. Hiki iā lākou ke hoʻomaka i loko o ka puʻuwai (mua) a i ʻole e laha i ka puʻuwai mai kahi ʻē aʻe o ke kino (metastatic).
He mea kākaʻikahi loa ka hoʻomaka ʻana o kahi puʻupuʻu i loko o ka puʻuwai ponoʻī. Akā, ʻo nā puʻupuʻu e hana ana, ʻo ka papillary fibroelastoma ke ʻano maʻamau, me ka cardiac myxoma.
He mea maʻamau ka makaʻu ke haʻi ʻia aku he puʻuwai kou. Akā, ʻo ka nūhou maikaʻi, ʻaʻole he maʻi kanesa ka papillary fibroelastoma, ʻaʻole ia e laha i nā wahi ʻē aʻe o ke kino, a hiki ke ho'ōla pinepine ʻia me ke ʻoki kino. E kamaʻilio me kāu kauka e pili ana i ka hoʻolālā lapaʻau maikaʻi loa nou a me nā mea e manaʻo ai i ka wā e hiki mai ana.
Nā mea nui e hoʻomanaʻo (Leka Lawe-Home)
Ua loaʻa paha iā ʻoe kekahi ʻike i ka Papillary Fibroelastoma a mākou i kamaʻilio ai. ʻOiai ʻaʻole kēia he maʻi kanesa, he ʻano ia e pono ai ka nānā ʻana no ka mea ke halihali nei i ka pilikia o ka hoʻokumu ʻana a me ka hele ʻana o nā ʻōpū koko.
- ʻAʻole hōʻike ka nui o ka poʻe i nā hōʻailona, no laila he mea nui nā hoʻokolohua lapaʻau.
- ʻIke nui ʻia kēia ma o ka hoʻāʻo echocardiography.
- ʻO ke ʻoki pinepine ʻana i ka lāʻau lapaʻau, kahi e hāʻawi ai i nā hopena maikaʻi loa.
- Inā ʻike ʻoe he loaʻa iā ʻoe kēia maʻi , mai hopohopo. E kamaʻilio ākea me kāu kauka, e nīnau i kāu mau nīnau, a e kiʻi i ka ʻike pololei.
ʻO ka mea nui loa, ʻo ia ke noho olakino!
ʻO Papillary Fibroelastoma, maʻi puʻuwai, nā puʻupuʻu puʻuwai, nā valves puʻuwai, hahau, hōʻeha puʻuwai, echocardiogram, ʻoki puʻuwai, puʻupuʻu maikaʻi ʻole, olakino puʻuwai











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