Ua manaʻo paha ʻoe ua paʻakikī kāu keikikāne e mimi ? A i ʻole ke manaʻo nei ʻo ia he haiki loa kona urethra a he kahe? ʻOiai ʻaʻole paha e nānā nui kekahi mau mākua i kēia mau mea, he hōʻailona paha kēia o kahi pilikia hānau e pili wale ana i nā keikikāne. I kēia lā ke kamaʻilio nei mākou e pili ana i kekahi ʻano maʻi, ʻo ia hoʻi ʻo Posterior Urethral Valves (PUV).
He aha nā Posterior Urethral Valves (PUV)?
I ka ʻōlelo maʻalahi, ʻo nā Posterior Urethral Valves (PUV) he kīnā hānau e pili wale ana i nā keikikāne. ʻO ka mea e hana ʻia ma kēia hihia, ʻo ia ka ulu ʻana o kahi ʻāpana e like me ka membrane i loko o ka paipu e lawe ana i ka mimi (kapa mākou i kēia he urethra). E noʻonoʻo iā ia me he mea lā i paʻa i loko o kahi paipu wai. Ma kēlā ʻano, ʻaʻole hiki i ka membrane ke kahe pono ma muli o ka mimi.
He aha ka mea e hana ʻia ma muli o kēia? ʻAʻole e hoʻokahe pono ka ʻōpū mimi o ka pēpē. No laila, kahe hope kēia mimi i hōʻiliʻili ʻia a hoʻomaka e hōʻino i ka ʻōpū mimi a me nā puʻupaʻa . Hana ʻia kēia ʻano i ka wā e noho ana ka pēpē i loko o ka ʻōpū. No laila, hiki ke ʻike ʻia i kekahi manawa ma o nā scan ma mua o ka hānau ʻana o ka pēpē, a ma hope paha o ka hānau ʻana, a i ʻole i ka wā kamaliʻi. ʻO kekahi inoa no kēia ʻo `(Congenital Obstructive Posterior Urethral Membrane - COPUM)`.
He kūlana maʻamau loa kēia?
ʻAʻole, ʻaʻole kēia he maʻi e pili ana i nā kānaka a pau. Akā, ʻo kēia kūlana, i kapa ʻia ʻo PUV, ke kumu nui o ka ālai ʻana o ke ala mimi i nā keikikāne ʻōpio.
He aha nā hōʻailona o kēia maʻi?
Hiki ke ʻokoʻa kēia mau hōʻailona mai kēlā pēpē a kēia pēpē. I kekahi manawa, ʻike nā kauka i kēia mau hōʻailona ma nā scan a ka makuahine ma mua o ka hānau ʻana o ke pēpē. I kekahi manawa, ʻike ʻia kēia mau hōʻailona ma hope o ka hānau ʻana o ke pēpē.
| ʻAno | He wehewehe maʻalahi |
|---|---|
| Ka puka ʻana o ka mimi nāwaliwali a palupalu paha | Ke mimi ke keiki, ʻaʻole e puka ikaika mai ka mimi, akā, he liʻiliʻi loa ia o ka mimi e like me ka kulu ʻana. |
| Nā maʻi ʻōpū mimi pinepine (UTIs) | Ma muli o ka hoʻokuʻu pono ʻole ʻia o ka mimi, hiki i ka bacteria ke ulu maʻalahi a hoʻoulu i nā maʻi. |
| Pohō kaumaha o ka pēpē | Hiki ke lohi ka piʻi ʻana o ke kaumaha no ka mea ʻaʻole i loaʻa i ke keiki ka meaʻai kūpono e pono ai no ka ulu ʻana. |
| ʻEha i ka wā o ka mimi ʻana (dysuria) | Inā uē kāu keiki a hōʻike paha i ka ʻoluʻolu ʻole i ka wā e mimi ana , ma muli paha o ka ʻeha. |
| Paʻakikī ke mimi | Inā pono ke keiki e hoʻoikaika e mimi, he hōʻailona nō hoʻi kēlā. |
| Ka wai amniotic haʻahaʻa `(oligohydramnios)` | ʻIke ʻia kēia i ka wā o nā scan i hana ʻia i ka wā o ke pēpē i loko o ka ʻōpū. |
| Pehu ʻana o nā puʻupaʻa (hydronephrosis) | Hiki i nā kauka ke ʻike i kēia ma o nā scan i ka wā hāpai. |
No ke aha lā kēia e hana nei?
ʻAʻole ʻike ʻia ke kumu kikoʻī o kēia, akā ʻike mākou hiki mai ia ma muli o ke ʻano o kēia membrane keu i loko o ka urethra i nā wā mua o ka ulu ʻana o ka pēpē i loko o ka ʻōpū.
ʻO ka mea nui loa, ʻo ia ka hoʻomanaʻo ʻana ʻaʻole kēia he mea āu i hana hewa ai . He ʻāpana wale nō kēia o ka ulu kino o ke keiki.
He aha nā pilikia e hiki ai i kēia ke hana?
Inā ʻaʻole mālama ʻia kēia maʻi i ka manawa kūpono, hiki iā ia ke alakaʻi i nā pilikia olakino koʻikoʻi, no ka mea, ua hōʻino mau ʻia nā puʻupaʻa ma muli o ke kahe hope o ka mimi.
| Ka pilikia | He aha kēlā manaʻo? |
|---|---|
| Kahe hou ʻana o ka mimi i loko o nā puʻupaʻa (vesicoureteral reflux/VUR) | ʻO ka mimi e hoʻopiha ana i ka ʻōpū mimi e hoʻi i luna, ʻo ia hoʻi, i nā puʻupaʻa. Hōʻino kēia i nā puʻupaʻa. |
| ʻAʻole hiki ke hoʻokuʻu loa i ka ʻōpū mimi (paʻa ʻana o ka mimi) | Aia mau kekahi mimi i loko o ka ʻōpū mimi. He kumu nui kēia o nā maʻi. |
| Pehu ʻana o ka puʻupaʻa | Hoʻomaka nā puʻupaʻa e pehu ma muli o ke kaomi o ka mimi. |
| Ka hāʻule ʻana o ka puʻupaʻa | ʻO kēia ke kūlana koʻikoʻi loa e hiki ke hana. I ka wā lōʻihi, hiki i nā puʻupaʻa ke hōʻino ʻia a oki i ka hana. |
Pehea e ʻike ai nā kauka i kēia?
E nānā ke kauka i ke keiki a, inā pono, e paipai i kekahi o kēia mau hoʻokolohua.
| Hoʻāʻo | He aha kāu e hana ai me kēia? |
|---|---|
| ʻO ke nānā ʻana i ka ultrasound o nā puʻupaʻa | E nānā kēia i ke ʻano o nā puʻupaʻa o ke keiki, ka ʻōpū mimi, a me ke ala mimi, a e nānā no nā mea e ālai ana. |
| ʻO ka Voiding Cystourethrogram (VCUG) | He hoʻāʻo X-ray kūikawā kēia e hiki ke hōʻike pololei i ke ʻano o ka piha ʻana a me ka hakahaka ʻana o ka ʻōpū mimi, a me kahi i loaʻa ai kekahi mau mea e ālai ana i ka urethra. |
| ʻO ke ʻano o ka cystoscopy | He hoʻokolohua kahi e hoʻokomo ʻia ai kahi ʻōmole me kahi kāmela liʻiliʻi i lalo o ka urethra a nānā pololei ʻia ka mea i paʻa i loko. |
| Nā hoʻokolohua hana puʻupaʻa | Hoʻomaopopo nā hoʻāʻo koko a me ka mimi i ka maikaʻi o ka hana ʻana o nā puʻupaʻa o ke keiki. |
He aha nā lāʻau lapaʻau no kēia?
ʻO ke ʻano lapaʻau nui no kēia, ʻo ia ke ʻoki ʻana e wehe i ka membrane e ālai ana. Hana pinepine ʻia kēia me ka hoʻohana ʻana i kahi ʻano i kapa ʻia ʻo "fulguration." ʻO ia hoʻi ka hoʻohana ʻana i ka wela mai ka uila e luku ai i nā ʻiʻo keu.
Eia kekahi, hiki i ke kauka ke kuhikuhi i nā lāʻau lapaʻau ʻē aʻe ma muli o ke kūlana o ke keiki.
- Ka catheterization mimi: Hiki ke hoʻokomo ʻia kahi paipu manawa pōkole (catheter) e hoʻokahe i ka mimi mai ka ʻōpū ʻōpū.
- Nā lāʻau lapaʻau: Inā loaʻa iā ʻoe kahi maʻi ʻōpū mimi, e hāʻawi ʻia iā ʻoe nā lāʻau lapaʻau e mālama ai.
- Inā hāʻule ka puʻupaʻa: Inā lilo ke ʻano i mea koʻikoʻi a hāʻule ka puʻupaʻa, pono paha ka dialysis a i ʻole ka hoʻoili puʻupaʻa.
- Nā lāʻau lapaʻau ʻē aʻe: Hiki ke hāʻawi ʻia nā antispasmodics e maʻalahi ai ka mimi ʻana.
He mea kākaʻikahi loa ka hiki ke hana ʻoki kino ʻoiai ke pēpē i loko o ka ʻōpū.
He aha ka mea e hana ʻia ma hope o ka mālama ʻana? He aha ka nānā ʻana?
Pono ke keiki me PUV i ka nānā ʻana o ke kauka no ke ola holoʻokoʻa, ʻoiai ma hope o ka mālama ʻia ʻana. Pono e nānā mau ʻia nā hoʻāʻo koko, nā scan, a me ka hana o nā puʻupaʻa.
Hiki i kekahi mau keiki ke loaʻa i ka incontinence mimi i ka wā kamaliʻi a i ʻole i ka wā makua. Ua hōʻike ʻia nā noiʻi ma kahi o 15% o nā keiki me kēia maʻi e pilikia ana i ka loaʻa ʻana o ka hāʻule ʻana o nā puʻupaʻa. Eia nō naʻe, ʻo ka ʻaoʻao ʻē aʻe , ʻaʻole i loaʻa i ka 85 o 100 mau keiki kēia maʻi koʻikoʻi . No laila, he mea nui loa ka ʻike mua ʻana, ka mālama pono ʻana, a me ka launa pū ʻana me kāu kauka.
Āhea wau e ʻike ai i ke kauka?
Inā kānalua ʻoe ua loaʻa i kāu keiki kekahi o nā hōʻailona a mākou i kūkākūkā ai, mai hoʻokaʻulua.E lawe koke i kāu keiki i ke kauka. Inā ʻaʻole mālama ʻia, hiki i kēia ke hoʻopilikia i ke olakino koʻikoʻi.
He aha nā nīnau āu e nīnau ai i ke kauka?
Ke hele ʻoe e ʻike i ke kauka, he mea kōkua ka nīnau ʻana i kēia mau nīnau.
- He aha nā koho lapaʻau no kēia?
- Pehea pololei e hana ʻia ai kēia lāʻau lapaʻau?
- He aha kāu e manaʻo ai i ka wā hoʻōla ma hope o ka lāʻau lapaʻau?
- Pehea e mālama ai i ke keiki i kēlā manawa?
- Āhea mākou e hele hou ai e ʻike i ke kauka?
He mea maʻamau ka makaʻu ke ʻike ʻoe he pilikia olakino ko kāu pēpē e like me kēia. Akā ʻo ka mea nui loa, ʻo ia ka hoʻomaopopo ʻana ʻaʻole na ʻoe kēia hewa. E kōkua kāu kauka a me ke kime mālama ola iā ʻoe i kēlā me kēia ʻanuʻu. No laila, mai makaʻu. E hahai pono i nā ʻōlelo a kāu kauka, a e nīnau i kāu mau nīnau.
Leka Lawe-Home
- ʻO nā Posterior Urethral Valves (PUV) kahi kīnā hānau e hoʻopilikia wale ana i nā keikikāne a ālai i ke kahe o ka mimi.
- ʻO ka nāwaliwali o ke ala mimi, nā maʻi pinepine o ke ala mimi, a me ka pohō kaumaha o ke keiki paha nā hōʻailona nui.
- Hiki ke ʻike ʻia kēia kūlana ma o nā scan ma mua o ka hānau ʻana o ke pēpē.
- ʻO ka lāʻau nui e mālama ai, ʻo ia ka wehe ʻana i ka mea i ālai ʻia i loko o ka urethra ma o ke ʻoki ʻana.
- ʻOiai ma hope o ka mālama ʻia ʻana, he mea nui loa ka nānā ʻana i ke olakino no ke ola holoʻokoʻa no ka mālama ʻana i ke olakino o nā puʻupaʻa o ke keiki.
- He mea nui e hoʻomaopopo ʻaʻole kēia ka hewa o nā mākua.











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