ʻAʻole anei e ulu pono ana nā māmā o kāu pēpē? (Pulmonary Hypoplasia) E aʻo kākou e pili ana i ia mea!

ʻAʻole hiki ke wehewehe ʻia ka hauʻoli āu e ʻike ai ke nānā aku ʻoe i kahi pēpē hānau hou, ʻeā? Akā i kekahi manawa, me kēlā hauʻoli, hiki mai kahi makaʻu iki i ka noʻonoʻo, ʻoiai inā ʻike ʻoe e paʻakikī ana ka pēpē i ka hanu ʻana. I kēlā mau manawa, ʻo kekahi o nā nīnau e kū mai ana i ka manaʻo o nā mākua, "Aia kekahi mea hewa me kaʻu pēpē?". I kēia lā e kamaʻilio mākou e pili ana i kēlā ʻano koʻikoʻi, akā he mea nui loa e makaʻala. ʻO ia hoʻi, ʻaʻole ulu pono nā māmā o ka pēpē, kahi ʻano a mākou e kapa nei ma ke ʻano lapaʻau he `(Pulmonary Hypoplasia)`.

He aha ka `(Pulmonary Hypoplasia)`? E hoʻomaopopo maʻalahi kākou.

I ka ʻōlelo maʻalahi, ʻo ka Pulmonary Hypoplasia ka wā ʻaʻole i ulu nā māmā o kāu pēpē e like me ka mea i manaʻo ʻia i ko lākou wā i loko o ka ʻōpū. He kūlana hānau kēia, ʻo ia hoʻi, aia lākou i ka wā hānau. ʻO ka hapa pinepine, ua hoʻokumu ʻia e kekahi kūlana olakino ʻē aʻe. ʻO ia hoʻi, ʻaʻole lawa ka lumi o nā māmā e ulu ai i loko o ka ʻōpū. I kekahi manawa, ʻike nā kauka i kēia kūlana ma mua o ka hānau ʻana o ka pēpē, i ka wā hāpai, ma o nā scan ultrasound. I kekahi manawa, ʻike ʻia ma hope koke o ka hānau ʻana o ka pēpē a i ʻole kekahi mau lā ma hope.

I kēia manawa, e nānā, i loko o ko kākou mau māmā he mau ʻeke ea liʻiliʻi i kapa ʻia ʻo alveoli. ʻO kēia nā mea e hoʻohui i ka oxygen a kākou e lawe ai i loko o ke koko. A laila lawe ke koko i kēia oxygen i nā ʻiʻo ma ke kino holoʻokoʻa. No laila, inā ʻaʻole i hoʻomohala pono ʻia nā māmā, e emi ana hoʻi kēia mau ʻeke ea. He aha ka mea e hana ai? ʻAʻole lawa ka oxygen i nā ʻōpū a me nā ʻiʻo ʻē aʻe o ke kino. Hoʻoikaika kēia i ka puʻuwai, a hiki ke piʻi aʻe ke koko i loko o nā māmā (pulmonary hypertension). E noʻonoʻo e pili ana iā ia, e like me ka hiki ʻole i kahi mea kanu liʻiliʻi ke ulu pono inā nele i ka wai, ka hakahaka, a me ka meaʻai.

He aha nā hōʻailona e hōʻike ai ka pēpē?

Inā loaʻa i kahi pēpē hānau hou ka Pulmonary Hypoplasia, hiki iā ia ke hōʻike i nā hōʻailona e like me:

• He kala polū i ka ʻili, nā lehelehe, a i ʻole nā ​​​​kui lima (`(cyanosis)`) . Hana ʻia kēia i ka wā ʻaʻole lawa ka oxygen i nā ʻiʻo o ke kino. ʻO ke kikoʻī, hana ʻia kēia kala polū i ka wā e emi ai ka oxygen i loko o ke koko.
• Ka puka ihu e pālahalaha ana . ʻO ke ʻano kēia e hoʻāʻo nui nei ke pēpē e hanu no ka mea he paʻakikī. E like me ka wā e holo ai a hāʻule, puhi mākou i ko mākou ihu a hanu.
• Paʻakikī ka hanu ʻana. Hiki i ka pēpē ke hana i kahi leo wheezing a i ʻole gasping i ka wā e hanu ana.
• Ka piʻi ʻana o ka hanu ʻana (tachypnea) . Inā ʻoi aku ka wikiwiki o ka hanu ʻana o ka pēpē ma mua o ka maʻamau, he hōʻailona nō hoʻi kēlā.

Inā loaʻa i kāu pēpē kekahi a ʻoi aku paha o kēia mau hōʻailona, ​​ʻoi aku ka maikaʻi o ka ʻike koke ʻana i ke kauka. Hiki i kēia ke lilo i mau hōʻailona o nā maʻi hanu ʻē aʻe, no laila he mea nui e loaʻa koke kahi hōʻailona kūpono.

No ke aha e hana ʻia ai kēia? He aha nā kumu nui o ka `(Pulmonary Hypoplasia)`?

Hoʻokumu pinepine ʻia ka Pulmonary Hypoplasia e nā maʻi olakino ʻē aʻe e pale ai i ka ulu pono ʻana o nā māmā i loko o ka ʻōpū. ʻO kēia mau maʻi e waiho i nā māmā me ka ʻole o kahi e pono ai lākou e ulu. ʻO kēia nā maʻi maʻamau:

• Ka wai amniotic haʻahaʻa (oligohydramnios) : Ke emi ka wai amniotic a puni ka pēpē, hiki iā ia ke kau i ke kaomi ma luna o nā māmā a hoʻoulu iā lākou e ulu maikaʻi ʻole. Hana kēia wai ma ke ʻano he uluna no ka pēpē a kōkua i ka ulu ʻana o nā māmā.
• ʻO Congenital Diaphragmatic Hernia (CDH) : ʻO ka diaphragm kahi ʻiʻo e hoʻokaʻawale i ka umauma a me ka ʻōpū. Inā he lua i loko a puka kekahi o nā ʻōpū o ka ʻōpū (e like me nā ʻōpū a me ke akepaʻa) i loko o ka umauma, ua emi ka wahi no nā māmā. A laila ʻaʻole hiki i nā māmā ke pehu a ulu pono.
• ʻOmphalocele : Ma kēia kūlana, puka kekahi o nā ʻōpū o ka pēpē ma o ke kaula umbilical, i uhi ʻia e kahi membrane. Hiki i kēia ke hoʻololi i ke kaomi i loko o ka ʻōpū o ka pēpē a hoʻopilikia i ka ulu ʻana o ka māmā.
• ʻO ka haki mua ʻana o nā membrane i ka wā hāpai (PROM) : Ke haki ka ʻeke amniotic ma mua o ka hānau ʻana o ke pēpē, i ʻike ʻia ʻo PROM, hiki ke emi nā pae wai a hoʻopilikia i ka ulu ʻana o ka māmā.
• ʻO ka maʻi māmā Cystic : ʻO kēia nā ʻōpū ʻaʻole kanesa e lawe i kahi i loko o nā māmā a hoʻopilikia i ka ulu ʻana o ka ʻiʻo māmā maʻamau.
• Ka hoʻonui ʻia ʻana o ka puʻuwai ma muli o nā pilikia o ka puʻuwai : No ka laʻana, ke hoʻonui ʻia ka puʻuwai ma muli o nā maʻi puʻuwai hānau e like me ka "tricuspid atresia" a i ʻole ka "Ebstein's anomaly", hiki iā ia ke kau i ke kaomi ma luna o nā māmā.
• Diaphragm hana ʻole a hana ʻole paha : ʻO ka diaphragm kahi ʻiʻo e pono ai no ka hana pono ʻana o nā māmā. Inā he pilikia me kāna hana, hiki iā ia ke hoʻopilikia i ka ulu ʻana o ka māmā.

Eia nō naʻe, i kekahi manawa, ʻaʻole hiki i nā kauka ke loaʻa kahi kumu kikoʻī no ka "Pulmonary Hypoplasia." Kāhea mākou iā ia he hypoplasia pulmonary mua . Hana ʻia kēia ma kahi o 10% a 15% o nā hihia.

ʻO wai ka mea i pilikia nui no kēia maʻi?

Hiki i kekahi mau kūlana i ka wā hāpai ke hoʻonui i ka pilikia o ka fetus no ka hypoplasia pulmonary, e like me oligohydramnios a me ka hānau mua ʻana. ʻO kēia mau mea:

• Nā maʻi : ʻO nā maʻi i laha ʻia e ke moekolohe (STI) a i ʻole nā ​​​​maʻi bacteria e like me ka bacterial vaginosis hiki ke hana i kou wai e haki i ka wā ʻōpiopio.
• Pōkole ka lōʻihi o ka ʻōpū . Hiki i kēia ke kumu o ka hānau mua ʻana a me ka PROM.
• Ke manaʻo nei i nā keiki he nui, e like me nā māhoe a i ʻole nā ​​māhoe ʻekolu . Hiki i kēia ke hana i nā pilikia e like me ka palena o ka hakahaka i loko o ka ʻōpū a me nā pae wai haʻahaʻa.
• Amniocentesis : He hoʻāʻo kēia i hana ʻia i ka wā hāpai. Eia nō naʻe, he mea kakaikahi loa, hiki ke hōʻino ʻia ka ʻeke wai a hiki ke liki ka wai.
• Ke koko kiʻekiʻe a i ʻole ka preeclampsia i ka wā hāpai. Hiki i kēia mau mea ke hoʻopilikia i ka hana o ka placenta, e hōʻemi ana i ka meaʻai a me ka oxygen o ka pēpē, a hiki nō hoʻi ke kumu o ka nalowale ʻana o ka wai.
• Maʻi diabetes : Inā loaʻa ka maʻi diabetes i ka makuahine, hiki iā ia ke hana i kekahi mau pilikia.
• Ka maloʻo ʻana o ka wai : Inā ʻaʻole inu ka makuahine i ka wai lawa, e emi paha ka nui o ka wai amniotic.

ʻO ia ke kumu he mea nui loa ka hahai pono ʻana i nā ʻōlelo a kāu kauka a hele i nā keʻena lapaʻau i ka manawa kūpono i ka wā hāpai. ʻO ka mālama ʻana i kou olakino e pili pono ana i ke olakino o kāu pēpē.

He aha nā pilikia ʻē aʻe e hiki ai i kēia ke hana?

ʻO ka ʻoiaʻiʻo ʻaʻole i ulu pono nā māmā hiki ke hoʻopilikia i nā ʻāpana ʻē aʻe o ke kino o ka pēpē. Eia nā pilikia e hiki ke kū mai ma muli o ka `(Pulmonary Hypoplasia):`

• ʻO ka pae oxygen haʻahaʻa i loko o ke koko (hypoxemia) : ʻO kēia ka pilikia nui. Hiki iā ia ke hōʻino i ka lolo a me nā ʻōpū ʻē aʻe.
• Ke koko kiʻekiʻe i loko o nā māmā o ka pēpē (pulmonary hypertension) : Hoʻololi nā kīʻaha koko i loko o nā māmā, e kau ana i ke kaomi hou ma ka puʻuwai.
• Ka nāwaliwali a i ʻole ka ulu kūpono ʻole o ka trachea (tracheomalacia) : Hiki i kēia ke hoʻopili i ka trachea i ka wā e hanu ai.
• Pneumothorax : Puka ka ea mai loko mai o nā māmā, hōʻiliʻili a puni ka māmā, a hiolo ka māmā.
• Nā pilikia hanu : No ka laʻana, bronchopulmonary dysplasia. Hiki i kēia ke ulu ma hope, ʻoi aku hoʻi i nā pēpē hānau mua ʻole, ke hoʻopili ʻia lākou i kahi ventilator.
• ʻO nā pilikia ʻē aʻe e hiki mai ana ma muli o ke kūlana kumu i hoʻokumu ai i ka hypoplasia pulmonary. Eia kekahi laʻana, nā pilikia hānai, ka hemahema o ka lohe, a me nā lohi o ka ulu ʻana .

"E makaʻu paha ʻoe ke lohe ʻoe i kēia mau mea a pau. Akā e hoʻomanaʻo, ʻo ka ʻike ʻana ke kaʻina hana maikaʻi loa e kū ai i kahi kūlana e like me kēia. E kamaʻilio me kāu mau kauka a nīnau i kāu mau nīnau a pau."

Pehea e ʻike ai nā kauka i kēia maʻi?

ʻO ka hapa pinepine, ʻike ke kauka i ka Pulmonary Hypoplasia i ka wā o ka ultrasound scan maʻamau i ka wā hāpai. Ana ke scan i ka nui o nā māmā o ka pēpē a me ke anapuni o ka umauma. Hiki ke hana ʻia kahi scan MRI (magnetic resonance imaging) e hōʻoia i ka hōʻailona. Hiki i kahi MRI ke hāʻawi i kahi kiʻi maopopo o ka nui o nā māmā.

I kekahi manawa, e ʻike ke kauka i kēia maʻi i ka wā hānau a i ʻole kekahi mau lā ma hope o ka hānau ʻana. Inā pilikia kāu pēpē i ka hanu ʻana, e hana ke kauka i kahi X-ray umauma e nānā no ka hypoplasia pulmonary a i ʻole kekahi maʻi māmā ʻē aʻe. Hiki i ka X-ray ke hōʻike i ka nui a me ke kūlana o nā māmā.

He aha nā lāʻau lapaʻau no kēia?

ʻO ka mālama ʻana no ka Pulmonary Hypoplasia e pili ana i ke kumu, ke koʻikoʻi o ke kūlana, a inā paha i ʻike ʻia i ka wā hāpai a ma hope paha o ka hānau ʻana. ʻO ka pahuhopu nui o ka mālama ʻana, ʻo ia ka hāʻawi ʻana i ka pēpē i ka oxygen e pono ai lākou e ola a kōkua i ko lākou mau māmā e ulu i ka hiki. Inā hānau ʻia kāu pēpē me ka Pulmonary Hypoplasia, pono ʻoe e kōkua iā lākou e hanu a hiki i ka ulu ʻana o ko lākou mau māmā e hanu iā lākou iho, a i ʻole a hiki i ka hiki i nā kauka ke hāʻawi i ka mālama hou aku.

Eia kekahi o nā lāʻau lapaʻau a ke kauka hānau keiki a i ʻole ka neonatologist e hoʻohana ai:

• ʻAmnioinfusion : Inā he haʻahaʻa ka pae o ka wai amniotic i ka wā hāpai, hoʻokomo kēia kaʻina hana i ka wai. Hiki i kēia ke kōkua i ka hōʻemi ʻana i ke kaomi ma luna o nā māmā a kōkua i ka ulu ʻana.
• ʻO ke ʻoki ʻana i ka ʻōpū a i ʻole ke ʻoki ʻana ma hope o ka hānau ʻana : No ka laʻana, inā he kūlana i kapa ʻia ʻo CDH, hiki ke hana ʻia ke ʻoki ʻana e hoʻoponopono iā ia. I kekahi manawa hana ʻia kēia ʻoki ʻana i ka wā e noho ana ke pēpē i loko o ka ʻōpū.
• Hoʻōla oxygen : Hāʻawi ʻia ka oxygen i ka pēpē ma o ka cannula ihu a i ʻole kahi pale maka i kau ʻia ma luna o ka maka.
• Hoʻoulu ea mīkini : Pili kēia i ka hoʻopili ʻana i kahi ventilator i kahi mīkini a me ke kōkua ʻana i ka hanu hana. Hana ʻia kēia ma ke komo ʻana i kahi ʻōmole i loko o ka ʻōpū makani.
• ʻO ka Extracorporeal Membrane Oxygenation (ECMO) : He lāʻau lapaʻau kūikawā a paʻakikī kēia. Hoʻohui kahi mīkini i ka oxygen i ke koko a hoʻoneʻe i ke kalapona dioxide me ka hāʻawi ʻana i ka hoʻomaha i nā māmā a me ka puʻuwai o ka pēpē. Hoʻohana ʻia ia i nā hihia koʻikoʻi loa ke hāʻule nā ​​​​lāʻau lapaʻau ʻē aʻe.

He aha ka mea e hana ai inā hānau ʻia kāu pēpē me ka Pulmonary Hypoplasia?

Inā hānau ʻia kāu pēpē me nā māmā i ulu pono ʻole, e nānā ʻia ʻo ia e kahi neonatologist (he kauka loea i nā pēpē hānau hou) a me kahi hui o nā loea ʻē aʻe. Ma muli o ke koʻikoʻi o ke kūlana a me nā kino ʻē aʻe i hoʻopilikia ʻia, hiki i ka hui lapaʻau ke komo pū me:

• Nā Kauka Lapaʻau Puʻupaʻa (Nā Nephrologists)
• Nā Pulmonologists (nā loea hanu)
• Nā kauka ʻokiʻoki Cardiothoracic (Nā kauka ʻokiʻoki Cardiothoracic)
• Nā Gastroenterologists (nā loea i ka ʻōnaehana hoʻoheheʻe)

Hoʻomaʻamaʻa pinepine ʻia nā pēpē me ka "(Pulmonary Hypoplasia)" meMa ka ʻāpana mālama koʻikoʻi neonatal (NICU), loaʻa i nā pēpē ka mālama kūikawā a me ka nānā mau ʻana. Loaʻa pinepine iā lākou nā pilikia māmā lōʻihi a me nā kūlana olakino ʻē aʻe. Hoʻokomo pū kēia me nā maʻi hanu pinepine, nā kūlana e like me ka hānō, a me nā lohi o ka ulu ʻana. Eia nō naʻe, ʻaʻole paha e loaʻa i kekahi mau pēpē me ka Pulmonary Hypoplasia kahi kūlana koʻikoʻi i ko lākou wā ʻelemakule, a hiki ke hoʻomau ka ulu ʻana o ko lākou mau māmā a hiki ke hoʻomaikaʻi ʻia ko lākou mau hōʻailona.

Pehea lā e hiki ai ke ola me kēia kūlana?

He ʻoiaʻiʻo nō hiki i nā pēpē me nā māmā i ulu pono ʻole ke ola. Akā, ʻokoʻa ke kūlana o kēlā me kēia kanaka. ʻO ke ʻano o ka hiki ke ola me ka `(Pulmonary Hypoplasia)` e pili ana i kēia mau mea:

• Ke koʻikoʻi o ke kūlana. Pehea ka lōʻihi o ka ulu ʻana o nā māmā.
• Ke kumu kumu. He aha ka maʻi kumu i hoʻoulu ai i ka `(Pulmonary Hypoplasia)` a pehea kona koʻikoʻi.
• Inā paha i ʻike ʻia i ka wā hāpai a ma hope paha o ka hānau ʻana. Inā ʻike mua ʻia, i kekahi manawa hiki ke hana koke ʻia.
• Aia kekahi mau pilikia ʻē aʻe?

Ma keʻano holoʻokoʻa, ua ʻōlelo ʻia ʻo ka nui o ka make ma muli o ka Pulmonary Hypoplasia ma luna o 55%. He mea paʻakikī ke ola me nā hihia koʻikoʻi loa o ka Pulmonary Hypoplasia. He mea kaumaha ke ʻōlelo ʻana i kēia, akā he mea nui e ʻike i ka ʻoiaʻiʻo. Eia nō naʻe, me ka holomua o ka ʻepekema lapaʻau, ua hoʻomaikaʻi nui ʻia nā ʻano hana e kōkua ai i kēlā mau pēpē i kēia lā.

Hiki iā kākou ke hana i kekahi mea e pale aku ai i kēia?

ʻAʻohe ala hoʻokahi e pale aku ai i ka Pulmonary Hypoplasia, no ka mea, he hopena pinepine ia o kahi maʻi ʻē aʻe. Eia nō naʻe, ʻo ke ala maikaʻi loa e hōʻemi ai i ka pilikia o nā pilikia olakino ke hānau ʻia kāu pēpē, ʻo ia ke hahai i nā ʻōlelo aʻo a kāu kauka hānau no ka hāpai kino olakino. Hiki iā ʻoe ke mālama iā ʻoe iho ma:

• E mālama i kāu mau maʻi mau loa, e like me ka maʻi diabetes a me ke koko kiʻekiʻe.
• E hele i kāu kauka i kēlā me kēia lā i kou wā hāpai. Ma kēlā ala, inā he mau pilikia, hiki iā ʻoe ke ʻike mua iā lākou.
• E pale loa i ka puhipaka a me ka inu ʻona. He hopena maikaʻi ʻole kēia i ka ulu ʻana o ka pēpē.
• E inu i ka nui o ka wai. He mea nui loa e inu ma ka liʻiliʻi he 2-3 lita o ka wai i ka lā.
• E pale iā ʻoe iho mai nā maʻi i laha ma ke moekolohe (STI) a me nā maʻi lele ʻē aʻe.

Hiki i nā nānā mau ʻana me kāu kauka hānau keiki a me ke kauka wahine ke kōkua i ka ʻike mua ʻana i nā pilikia. I kekahi manawa, hiki i nā kauka ke mālama i ke kumu kumu o ka Pulmonary Hypoplasia i ka wā hāpai. Hiki i kēia ke kōkua i ka pale ʻana i kāu pēpē mai ka hānau ʻana me nā māmā i ulu pono ʻole.

ʻO ka mea hope loa, pono ʻoe e ʻōlelo ...

Inā hānau ʻia kāu pēpē me ka Pulmonary Hypoplasia, e hele pū ana kahi hui o nā kauka me ʻoe i kēlā me kēia ʻanuʻu o ke ala. E wehewehe lākou i ke koʻikoʻi o ke kūlana, kāu mau koho lapaʻau, a me nā mea e hiki mai ana. Mai kānalua e nīnau i nā nīnau āu e loaʻa ai i hiki iā ʻoe ke hoʻoholo i nā hoʻoholo e pili ana i ka mālama ʻana i kāu pēpē - a i ʻole kou olakino ponoʻī.

"Inā hiki, e hana i kāu hui kākoʻo pilikino ponoʻī o nā poʻe āu e hilinaʻi ai a aloha ai. ʻO ia hoʻi, ʻo nā poʻe e like me kāu kāne, makuahine, makuakāne, mau kaikaina, a me nā hoaaloha maikaʻi loa. ʻO kā lākou kākoʻo he ikaika nui ia e kū ai i nā pilikia e hiki mai ana iā ʻoe. He mea nui loa ia e noho ikaika. Mai haʻalele i ka manaʻolana."

Lana ko mākou manaʻo he kōkua kēia ʻike iā ʻoe. E hoʻomanaʻo, e nīnau mau i ke kauka kūpono no ka ʻōlelo aʻo lapaʻau. No ka ʻike laulā wale nō kēia ʻatikala.

ʻO ka Hypoplasia Pulmonary, ka ulu ʻole ʻana o nā māmā, nā pēpē hānau hou, ka pilikia hanu, nā maʻi hānau, NICU, olakino pēpē, nā pilikia hāpai