He pilikia puʻuwai ko kāu pēpē? E kamaʻilio kākou e pili ana i ka Shone's Complex!

Ke haʻi aku ke kauka iā ʻoe ua loaʻa i kāu keiki liʻiliʻi kahi maʻi puʻuwai i kapa ʻia ʻo "Shone's Complex," e hopohopo paha ʻoe, makaʻu, a huikau . He mea maʻamau loa ia. ʻAʻole paha ʻoe i lohe i kēia inoa ma mua. "He aha kēia maʻi? He aha ka mea e hiki mai ana i kaʻu pēpē?" He nui paha kāu mau nīnau i loko o kou manaʻo. Mai hopohopo. E kamaʻilio kākou e pili ana i kēia me ka maʻalahi a me ka maopopo. He aha ka Shone's Complex? E hoʻomaopopo pono kākou i kāna hana i ka pēpē.

I ka ʻōlelo maʻalahi, he aha kēia Shone's Complex?

He maʻi puʻuwai hānau ʻia ka Shone's Complex. ʻO ka mea e hana ʻia ma kēia, aia kahi mea e ālai ʻia ai ma mua o hoʻokahi wahi ma ke ala kahe koko i ka ʻaoʻao hema o ka puʻuwai o kā mākou pēpē. E noʻonoʻo, ʻo ka ʻaoʻao hema o ko mākou puʻuwai ka mea e lawe i ke koko maʻemaʻe a waiwai i ka oxygen mai nā māmā a hoʻopuehu iā ia i ke kino holoʻokoʻa. E like me ka motika wai. I kēia manawa he aha ka mea e hana ʻia inā he mau mea e ālai ʻia ai a i ʻole nā ​​​​​​ʻeha i loko o kēia ala kahe koko? Lilo ia i mea paʻakikī no ka puʻuwai ke lawe i ke koko, a lilo ia i mea paʻakikī ke hoʻopuehu i ke koko i ke kino. ʻO ia ka mea e hana ʻia ma ka Shone's Complex.

Ua kapa ʻia kēia kūlana ʻo Shone's Complex, ma muli o ke kauka nāna i wehewehe mua iā ia. ʻOiai ua ʻike ʻo ia i ʻehā mau kīnā puʻuwai e pili ana me ia, ua ʻike nā kauka i kēia manawa he nui nā hemahema hou aʻe e pili ana.

He aha nā kīnā o ka puʻuwai e hiki ke hoʻopili ʻia me ka Shone's Complex?

I mea e ʻike ʻia ai me ka Shone's Complex, pono i kahi pēpē ke loaʻa i ʻelua o nā kīnā puʻuwai ʻewalu a mākou e kamaʻilio ai ma lalo nei. E nānā kākou i ke ʻano o lākou. Me he mea lā he paʻakikī iki kekahi o nā huaʻōlelo, akā e wehewehe maʻalahi wau iā lākou.

He aha nā hōʻailona inā loaʻa kēia maʻi i kaʻu pēpē?

Inā koʻikoʻi kekahi mau pēpē me kēia maʻi, e hoʻomaka koke lākou e hōʻike i nā hōʻailona ma hope o ka hānau ʻana . ʻO kēia no ka mea ʻaʻole hiki i ka puʻuwai o ka pēpē ke pamu i ke koko i ke kino. Eia nō naʻe, i kekahi manawa, hiki ke ʻike ʻia nā hōʻailona i ka wā kamaliʻi a i ʻole ka wā ʻōpio.

E nānā i kēia mau hōʻailona i kāu keiki:

• Paʻakikī ke piʻi ʻana o ke kaumaha: ʻAʻole e piʻi pono ke kaumaha.
• Manaʻo luhi i ka wā e inu ana i ka waiū: Ma hope o ka inu ʻana i ka waiū, hoʻomaka ʻoe e hou a paʻakikī i ka hanu ʻana.
• Ka emi ʻana o ka mimi i hoʻopuka ʻia: Ka emi ʻana o ka mimi ma mua o ka maʻamau.
• Ka pulse nāwaliwali: Ua nāwaliwali loa ka pulse, ʻoiai ma nā lima a me nā wāwae.
• ʻOkoʻa ke kaomi koko ma waena o nā lima a me nā wāwae: ʻOi aku ke kiʻekiʻe o ke kaomi koko ma nā lima ma mua o nā wāwae.
• Ka hōʻiliʻili ʻana o ka waikawa lactic i loko o ke koko.

Inā loaʻa i kāu keiki kekahi a ʻoi aku paha o kēia mau hōʻailona, ​​​​he mea nui loa e kamaʻilio me kāu kauka i ka wā hikiwawe loa.

No ke aha i hiki mai ai kēia i kaʻu pēpē? He aha ke kumu o kēia?

I kēia manawa, ke noʻonoʻo nei paha ʻoe, "No ke aha i hana ʻia ai kēia i kaʻu pēpē? Naʻu anei ka hewa?" ʻOiaʻiʻo, ʻaʻole i loaʻa i nā kauka kahi kumu kikoʻī no kēia. ʻO ka hapa nui o ka manawa, hana pinepine ia. ʻAʻole lawa kā mākou ʻike e ʻōlelo maopopo ai inā he kumu hoʻoilina a he kumu kaiapuni paha.

ʻOiai ke kuhikuhi nei kekahi mau noiʻi he mea hoʻoilina paha ia, he paʻakikī loa ke ʻano o kona hoʻoili ʻia ʻana i loko o nā ʻohana. No laila, pono ka noiʻi hou aku e hoʻomaopopo piha i kēia.

He aha nā pilikia e hiki mai ana o kēia maʻi?

Hiki i ka Shone's Complex ke hana i kekahi mau pilikia, ʻo ia ke kumu he mea nui ka mālama koke ʻana a me ka nānā ʻana i ka wā lōʻihi.

• Ke koko kiʻekiʻe o ka pulmonary: He piʻi ʻana o ke koko i loko o nā kīʻaha koko e lawe ana i ke koko i nā māmā.
• Nā ʻano mele puʻuwai ʻē: Nā ʻano mele puʻuwai ʻē.
• Ka hāʻule ʻana o ka puʻuwai: ʻO ke ʻano hiki ʻole i ka puʻuwai ke pamu i ke koko kūpono i ke kino.

Pehea e ʻike ai nā kauka i kēia?

Hoʻohana nā kauka i kekahi mau hoʻokolohua e ʻike ai i kēia maʻi.

• ʻO ka echocardiogram fetal: He scan kūikawā kēia i hana ʻia ʻoiai ke pēpē i loko o ka ʻōpū. Hiki iā ia ke ʻike i nā pilikia o ka puʻuwai ma mua o ka hānau ʻana o ke pēpē.
• ʻO ka transthoracic echocardiogram (TTE): He scan ultrasound o ka puʻuwai i hana ʻia ma hope o ka hānau ʻana o ke pēpē. Hoʻohana nui ʻia kēia hoʻāʻo no ka ʻike ʻana i ka Shone's Complex.
• ʻO ka CT scan Cardiac a i ʻole MRI: ʻAʻole hana pinepine ʻia kēia mau mea no nā mea āpau, akā i kekahi mau hihia, hiki i kēia mau hoʻokolohua ke kōkua i ka hāʻawi ʻana i ka ʻike hohonu e pili ana i ke ʻano o ka puʻuwai.

ʻO ka hapa pinepine, ʻike ʻia ka maʻi ma mua a ma hope paha o ka hānau ʻana. Eia nō naʻe, i kekahi manawa ʻike mua ʻia ka maʻi i ka wā kamaliʻi a i ʻole ka wā ʻōpio, i ka wā e palupalu ai nā hōʻailona a ʻaʻole i koʻikoʻi loa. I ia mau hihia, hiki i ke kauka ke kuhikuhi no ka hoʻāʻo hou ʻana ma muli o kahi leo ʻē (heart murmur) i lohe ʻia i ka wā e hoʻolohe ana i ka puʻuwai.

He aha nā lāʻau lapaʻau no kēia?

ʻO ke ʻoki kino wale nō ke ala e mālama ai i ka Shone's Complex . ʻAʻohe lāʻau lapaʻau i kēia manawa e hiki ke ho'ōla i kēia maʻi. Eia nō naʻe, hiki i ke kauka ke kuhikuhi i ka lāʻau lapaʻau e kāohi i nā hōʻailona o ka pēpē a kākoʻo i ka hana o ka puʻuwai a hiki i ke ʻoki kino.

ʻAʻohe ʻoki kino kūikawā no kēia. Akā, na nā kauka e hoʻoholo i ke ʻoki kino e pono ai ma muli o nā kīnā o ka puʻuwai o kāu keiki a me ke ʻano o ka hana ʻana o ka puʻuwai.

Pono paha kāu keiki i hoʻokahi a ʻoi aku paha o nā ʻoki ʻana:

• Ka wehe ʻana i ke apo ʻiʻo keu a puni ka valve mitral.
• Hoʻoponopono ʻana i ka valve mitral.
• Hoʻololi ʻia ka valve mitral (ʻaʻole kēia i maʻamau).
• Wehe ʻana i nā ʻiʻo keu ma lalo o ka valve aortic.
• Ke hoʻonui nei i ka wehe ʻana o ka valve aortic.
• Ke hoʻoponopono nei i kahi ʻāpana o ka aorta i haiki.

Kaʻina hana ʻoki kino

I kekahi manawa, hana nā kauka i kēia ma ke ʻano hoʻonohonoho . ʻO ia hoʻi, ʻaʻole lākou e hana i ke ʻoki kino i ka manawa hoʻokahi. Hana lākou i ʻelua ʻāpana, i hoʻokaʻawale ʻia e kahi manawa. No ka laʻana, wehe ka ʻoki kino mua i ka mea paʻa i ke ala e kahe ai ke koko mai loko mai o ka puʻuwai. A laila, wehe ka ʻoki kino ʻelua i ka mea paʻa i ke ala e kahe ai ke koko i loko o ka puʻuwai. E wehewehe pono kāu kauka iā ʻoe i ka nui o nā ʻoki kino e pono ai kāu keiki a me ka manawa kūpono e hana ai.

He aha ke ola o ke keiki i ka wā e hiki mai ana a me kona manaʻo no ia mea?

ʻO ke ola a me ke olakino o ke keiki i ka wā e hiki mai ana e hilinaʻi ʻia ma luna o kekahi mau kumu:

• Ke koʻikoʻi o ka maʻi: Pehea ka koʻikoʻi o ke kīnā o ka puʻuwai.
• Ka wikiwiki o ka lāʻau lapaʻau: Pehea ka wikiwiki o ka hoʻomaka ʻana o ka lāʻau lapaʻau.
• Nā pilikia: Inā paha e loaʻa mai nā pilikia ʻē aʻe a i ʻole.
• Ka hana hou ʻana o nā pilikia: E hana hou ʻia anei nā kīnā puʻuwai i mālama ʻia ma mua i ka hala ʻana o ka manawa?

Eia kekahi laʻana, hiki i nā mea e like me ka coarctation o ka aorta ke hana hou i ka hala ʻana o ka manawa. No laila, i ka wā e ulu ai kāu keiki, pono paha ke ʻoki kino hou aku. E hāʻawi kāu kauka iā ʻoe i ka ʻike hou aku e pili ana i kēia ma muli o ke kūlana o kāu keiki.

Ua hōʻike ʻia nā haʻawina he nui ʻoi aku ka nui o ke ola lōʻihi ma hope o ke ʻoki ʻana ma mua o 75%, a hiki i 20 mau makahiki . ʻO ia hoʻi, ʻekolu o nā pēpē ʻehā e ola maikaʻi a olakino ma hope o ka mālama ʻana.