Ke manaʻo nei ʻoe i kekahi manawa he ʻūmiʻi iki kou umauma, he paʻakikī ka hanu ʻana, a he luhi paha? Ma hope o kēia mau mea, aia paha kekahi loli a nāwaliwali paha i ke ʻano o ka puʻuwai, ʻo ia hoʻi, ke ʻano o ka puʻuwai, nā paia, nā valves, a i ʻole nā ʻiʻo. I kēia lā ke kamaʻilio nei mākou e pili ana i kekahi mau pilikia i ke ʻano o ka puʻuwai, a nā kauka i kapa ai he `(Structural Heart Disease)`. Hiki i kēia ke lilo i mea i hānau ʻia me ia, a i ʻole hiki ke ulu ma hope me ka ʻelemakule. Inā ʻaʻole mālama pono ʻia, hiki ke kū mai nā pilikia olakino ʻē aʻe i ka hala ʻana o ka manawa.
No laila he aha kēia maʻi puʻuwai kūkulu?
I ka ʻōlelo maʻalahi, ʻo ke ʻano o ka `(Structural Heart Disease)` he ʻano ʻē kekahi i loko o ke ʻano o kou puʻuwai, ʻo ia hoʻi ke ʻano o ka puʻuwai, kona mau paia, nā keʻena, nā valves, a i ʻole nā ʻiʻo puʻuwai. He kumuhana ākea loa kēia. E noʻonoʻo, inā ʻaʻole i hoʻonohonoho pono ʻia nā paia, nā puka, a me nā puka makani o ko mākou hale, ʻaʻole e hana pono kēlā hale. Pēlā nō hoʻi i ka puʻuwai.
He aha kēia mau ʻano maʻi kūkulu puʻuwai?
Hiki iā kākou ke hoʻokaʻawale i kēia mau kūlana i ʻekolu mau māhele nui. E noʻonoʻo, he ʻōkana kupaianaha ko kākou puʻuwai. Loaʻa iā ia nā ʻāpana like ʻole, pono e hana pono nā mea a pau.
- Maʻi kīwila puʻuwai: Ua ʻike anei ʻoe he ʻehā mau kīwila o ko kākou puʻuwai? Ua like kēia me nā puka e kāohi ana i ke kahe o ke koko - ʻae wale lākou i ke koko e kahe i hoʻokahi ʻaoʻao. No laila, inā he pilikia me kēia mau kīwila, no ka laʻana, kahi kīwila i wehe pono ʻole ʻia (stenosis) a i ʻole kahi kīwila i pani pono ʻole ʻia (valvular regurgitation), ua kapa ʻia kēlā he maʻi kīwila puʻuwai.
- Cardiomyopathy: ʻO kēia ka wā e nāwaliwali ai ka ʻiʻo puʻuwai, mānoanoa, a i ʻole e hoʻonui ʻia. Ke hana ʻia kēia, ʻaʻole hiki i ka puʻuwai ke pamu pono i ke koko. E noʻonoʻo e like me ka pamu wai e hiki ʻole ke pamu i ka wai.
- Maʻi puʻuwai hānau: ʻO kēia nā kīnā kūkulu o ka puʻuwai i loaʻa i ka wā hānau. Hiki ke hānau ʻia kekahi mau pēpē me kahi lua i loko o ka puʻuwai a i ʻole kahi pilikia valve. Ua kapa ʻia kēia mau mea he maʻi puʻuwai hānau.
ʻO wai ka mea hiki ke loaʻa i kēia maʻi kūkulu puʻuwai?
ʻO kaʻoiaʻiʻo, hiki i kēia kūlana i kapa ʻia ʻo "Structural Heart Disease" ke ulu i loko o kekahi, me ka nānā ʻole i ke kāne, ka lāhui, a i ʻole ka makahiki. Eia nō naʻe, hiki i kekahi mau mea ke hoʻonui i ka pilikia.
- Moʻolelo ʻohana: Inā loaʻa kekahi o kou ʻohana i kēia ʻano maʻi puʻuwai, ʻoi aku paha kou pilikia o ka loaʻa ʻana.
- Nā mea e hoʻopilikia ana i ka makuahine i ka wā hāpai: I kekahi manawa, hiki i kekahi mau mea e hana ʻia ana i ka makuahine i ka wā o ka pēpē i loko o ka ʻōpū ke kumu i ka maʻi puʻuwai hānau i loko o ka pēpē. Eia kekahi laʻana:
- Ka hoʻopili ʻia ʻana o ka makuahine i nā mea e like me nā mea hoʻoheheʻe ʻoihana i ka wā hāpai.
- Loaʻa i ka makuahine kahi maʻi e like me "Rubella" i nā mahina ʻekolu mua o ka hāpai ʻana.
- Ke hoʻohana nei i kekahi mau lāʻau lapaʻau me ka ʻole o ke aʻo ʻana a ke kauka, ka inu ʻana i ka waiʻona.
- Ka loaʻa ʻana o kekahi mau maʻi viral.
- Ka ʻelemakule ʻana: I ko kākou ʻelemakule ʻana, hiki i ka calcium ke hōʻiliʻili ma nā wahi e like me nā valves o ka puʻuwai. Hiki i kēia ke alakaʻi i nā maʻi puʻuwai. ʻO ka ʻoiaʻiʻo, ʻoi aku ma mua o 10% o ka poʻe ma luna o 75 mau makahiki i loaʻa i kekahi ʻano o ka "Maʻi Puʻuwai Kūkulu".
Pehea ka maʻamau o kēia mau kūlana?
ʻO ka maʻi valve puʻuwai ka mea maʻamau o kēia. Ma ʻAmelika Hui Pū ʻIa wale nō, ma kahi o 2.5% o ka heluna kanaka i loaʻa i kēia maʻi. Hiki ke hana ʻia e ka stenosis a i ʻole ka valvular regurgitation. ʻO ka mitral valve regurgitation a me ka aortic valve stenosis nā mea maʻamau.
ʻO nā maʻi puʻuwai hānau nā kīnā hānau maʻamau maʻamau ma ʻAmelika Hui Pū ʻIa. Ma kahi o 1% o nā pēpē i hānau ʻia i kēlā me kēia makahiki, a i ʻole ma kahi o 40,000 mau pēpē, loaʻa kēia maʻi.
Hoʻopilikia ka Cardiomyopathy (maʻi ʻiʻo puʻuwai) ma kahi o 1 i loko o 500 mau kānaka ma ʻAmelika Hui Pū ʻIa. Nui nā kumu no kēia, me ka maʻi ʻaʻa coronary, nā hopena o nā maʻi viral, nā mea pili i ke kaiapuni e like me ka waiʻona, a me nā mea hoʻoilina.
Pehea ka hopena o nā maʻi puʻuwai kino i koʻu kino?
E noʻonoʻo e like me ka mīkini o ko kākou kino. Hoʻopuka ia i ke koko ma ke kino holoʻokoʻa. Me ke koko e loaʻa ai i ko kākou mau cell ka oxygen a me nā meaʻai e pono ai lākou, a hoʻopau pū ke koko i nā mea ʻōpala mai nā cell. No laila, inā ʻaʻole hiki i ka puʻuwai ke hoʻopuka pono i ke koko ma muli o kahi pilikia me kona ʻano, ʻaʻole lawa ke koko i nā ʻōpū a me nā ʻiʻo ʻē aʻe i loko o ko kākou kino. Hiki i kēia ke hōʻino i nā ʻōpū like ʻole, a hiki mai nā pilikia olakino a me nā hōʻailona ʻē aʻe.
He aha nā kumu o kēia mau maʻi kūkulu puʻuwai?
Aia paha kekahi mau kumu no kēia.
- Congenital: I kekahi manawa, hiki i kekahi mau loli i loko o nā genes o ko mākou kino (DNA a i ʻole genetics) ke hana i nā mea ʻē i ka ulu ʻana o ka puʻuwai.
- Nā kumu e kū mai ana ma hope:
- Ka ʻelemakule: Hiki i kēia ke hana i nā waihona calcium i loko o nā kiwikā o ka puʻuwai.
- Ka ʻona a i ʻole ka lāʻau ʻona.
- ʻO ka aneurysm aorta.
- Nā maʻi Autoimmune, no ka laʻana, lupus a me ka rheumatic fever.
- Maʻi puʻuwai a i ʻole ka hōʻeha puʻuwai (Myocardial infarction).
- Nā maʻi e hōʻino ai i ka puʻuwai, nā laʻana: `(Amyloidosis)`, `(Hemochromatosis)`, `(Sarcoidosis)`.
- ʻO ka maʻi o ka uhi o loko o ka puʻuwai (endocarditis).
- Nā maʻi kelepa endocrine, nā laʻana: Diabetes a me ka maʻi Thyroid.
- Ke koko kiʻekiʻe (Hypertension).
- Ka hōʻike ʻia ʻana i ka radiation nui loa.
- Nā kūlana hoʻoilina e like me ka 'Marfan syndrome'.
- Nā maʻi e pili ana i nā ʻiʻo e like me ka muscular dystrophy.
- Nā waihona momona i loko o nā aʻa (Atherosclerosis).
He aha nā hōʻailona o kēia maʻi?
He mea kupaianaha ka ʻike ʻole ʻia o kekahi poʻe me kēia "Maʻi Puʻuwai Kūkulu". Eia naʻe, i ka holomua ʻana o ka maʻi, e ʻike paha ʻoe i nā hōʻailona e like me:
- ʻEha ka umauma, paʻa, a i ʻole ke kaomi.
- Ka poniuniu, ka māmā o ke poʻo, a i ʻole ka nāwaliwali (Syncope).
- Manaʻo luhi loa (Fatigue).
- Ke koko kiʻekiʻe (Hypertension).
- Puʻuwai kūpono ʻole (Arrhythmia).
- Hana ʻino o ka puʻupaʻa.
- Paʻakikī ka hanu ʻana (Dyspnea).
- Ka pehu ʻana o ka ʻōpū, nā kuʻekuʻe wāwae, a i ʻole nā wāwae (Edema).
Mea nui: Inā loaʻa iā ʻoe kekahi a ʻoi aku paha o kēia mau hōʻailona, e ʻike koke i ke kauka. Hiki ke hana ʻia kēia mau mea e nā kūlana olakino ʻē aʻe, no laila he mea nui e ʻimi i ke kumu pololei.
Pehea e ʻike ʻia ai kēia maʻi?
I ka wā hāpai, hiki i nā kauka ke nānā i kekahi mau ʻano ʻē i loko o ka puʻuwai o ka pēpē me kahi hoʻāʻo i kapa ʻia he "fetal echocardiogram." He hoʻāʻo kēia e hoʻohana ana i nā nalu kani e kiʻi i nā kiʻi o ka puʻuwai o ka pēpē.
No nā keiki a me nā pākeke, ke hoʻolohe kāu kauka i kou puʻuwai me ka stethoscope, lohe paha lākou i kahi leo puʻuwai ʻē (heart murmur). Inā hana ʻia kēia, e kuhikuhi kāu kauka iā ʻoe i kahi cardiologist. Hiki iā lākou ke hana i nā hoʻokolohua e like me kēia:
- Catheterization Cardiac: Ma kēia kaʻina hana, hoʻokomo ʻia kahi paipu liʻiliʻi i loko o ka puʻuwai ma o kahi aʻa ma ka ʻūhā a i ʻole ka lima e ana i ke kaomi i loko o nā keʻena o ka puʻuwai. Hiki iā ia ke kiʻi i nā kiʻi maopopo o ka puʻuwai a me nā kīʻaha koko.
- ʻO ka angiogram coronary: Hana ʻia kēia i ka manawa like me ke catheterization cardiac. Hoʻokomo ʻia kahi dye kūikawā i loko o nā kīʻaha koko a hoʻohana ʻia kahi X-ray e ʻike ai pehea e kahe ai ke koko ma o ka puʻuwai, nā aʻa, a me nā valves.
- Echocardiogram (Echo): He hoʻāʻo kēia e hoʻohana ana i nā nalu kani e hana i nā kiʻi o nā keʻena a me nā valves o ka puʻuwai. Hiki iā ia ke hōʻike pehea e pamu ai ka puʻuwai i ke koko.
- Electrocardiogram (ECG a i ʻole EKG): Ke ana kēia i ka hana uila o ka puʻuwai. Ua ʻike paha ʻoe i ka hoʻāʻo i hana ʻia ma ke kau ʻana i nā pepili ma kou umauma.
- Hoʻāʻo koʻikoʻi hoʻoikaika kino: Ma kēia hoʻāʻo, ua noi ʻia ʻoe e holo a hele paha ma luna o kahi treadmill a ua nānā ʻia kou puʻuwai.
- Nānā Holter: He mea liʻiliʻi kēia e kau ʻia ma kou kino no 24 a 48 mau hola a hoʻopaʻa i ka hana uila o kou puʻuwai ʻoiai ʻoe e hana ana i kāu mau hana o kēlā me kēia lā.
- Nā hoʻokolohua kiʻi ʻē aʻe: Hiki i nā hoʻokolohua e like me ka X-ray umauma, CT scan, a i ʻole MRI cardiac ke ʻike i nā pilikia kūkulu i loko o ka umauma.
ʻO kēia mau mea, ʻo nā hoʻokolohua ʻelua i hoʻohana pinepine ʻia e ʻike ai i nā maʻi puʻuwai ʻo ia ka ECG a me ka Echocardiogram.
Pehea e mālama ʻia ai kēia maʻi?
ʻAʻole pono paha kekahi ʻano o ka `(Structural Heart Disease)` i kekahi lāʻau kūikawā. Eia nō naʻe, pono ʻoe e hoʻomau i ka nānā ʻana i kou kūlana ma lalo o ka nānā ʻana a ke kauka.
No nā ʻano ʻē aʻe, hiki i ke kauka ke ʻōlelo i nā lāʻau lapaʻau e like me:
- Lāʻau lapaʻau: Hiki ke hāʻawi ʻia nā lāʻau lapaʻau e kāohi i nā hōʻailona, hoʻomaikaʻi i ka hana o ka puʻuwai, a pale paha i nā ʻaʻa koko.
- Nā kaʻina hana puʻuwai minimally invasive: Pili kēia i ke hoʻokomo ʻana i nā mea hana ma o kekahi mau lua liʻiliʻi, me ka ʻole o ka hana ʻana i kahi ʻoki nui, e hoʻoponopono i kahi valve hemahema a hoʻololi paha me kahi mea hou.
- ʻO ke ʻoki puʻuwai hāmama: Ma kēia, wehe ke kauka ʻoki i ka umauma a komo i ka puʻuwai e hana i nā mea e like me ke pani ʻana i ka valve, a i kekahi manawa he hoʻoili puʻuwai.
Pehea e hiki ai iaʻu ke hōʻemi i koʻu pilikia o ka loaʻa ʻana o kēia maʻi?
Inā hāpai ʻoe, hiki iā ʻoe ke hana i kēia mau mea e hōʻemi i ka pilikia o kāu pēpē e loaʻa ana i ka maʻi puʻuwai hānau:
- Inā loaʻa iā ʻoe kahi maʻi mau e like me ka maʻi diabetes a i ʻole kahi maʻi e like me ka epilepsy, e kamaʻilio me kāu kauka e pili ana i ka lāʻau lapaʻau āu e lawe ai.
- Inā ʻoe e puhipaka, e hoʻōki. E pale i ka hoʻohana ʻana i nā huahana paka.
- E ho'ōki i ka inu ʻana i ka waiʻona.
- Inā ʻoe e hoʻohana i nā lāʻau lapaʻau no ka leʻaleʻa, e hoʻōki loa i ka hoʻohana ʻana iā lākou.
- E lawe i 400 micrograms o ka folate (folic acid) i kēlā me kēia lā (ʻoi aku ka maikaʻi o ka lawe ʻana i kēia ma mua o kou hāpai ʻana).
E hahai i kēia mau ʻano olakino e hōʻemi i kou pilikia o ka loaʻa ʻana o ka maʻi valve puʻuwai a me kekahi ʻano maʻi ʻiʻo puʻuwai (cardiomyopathy):
- E mālama i ke kaumaha o ke kino kūpono.
- E ʻai i ka meaʻai olakino no ka puʻuwai (haʻahaʻa i ka ʻaila, ka paʻakai, a me ke kō, a kiʻekiʻe i nā huaʻai a me nā mea kanu).
- E hoʻoikaika kino i nā manawa a pau.
- E hōʻemi i ka inu ʻana i ka waiʻona a mai hoʻohana i nā lāʻau lapaʻau no ka leʻaleʻa.
- Inā loaʻa iā ʻoe nā maʻi olakino ʻē aʻe e like me ke koko kiʻekiʻe, ka maʻi diabetes, a i ʻole ka maʻi thyroid, e hahai i nā ʻōlelo aʻoaʻo a kāu kauka a kaohi iā lākou.
- E hōʻemi i ke kaumaha.
Inā loaʻa iaʻu (Structural Heart Disease), pehea lā koʻu wā e hiki mai ana?
Pili maoli kēia i kekahi mau mea:
- ʻEhia ka lōʻihi o kou loaʻa ʻana i kēia maʻi?
- Ka nui o ka maʻi.
- He aha ke ʻano o ka "Maʻi Puʻuwai Kūkulu" āu e loaʻa nei?
- Nā pilikia olakino ʻē aʻe āu e loaʻa nei.
Akā, mai hopohopo! He nui ka poʻe me ka Maʻi Puʻuwai Kūkulu e ola lōʻihi a hauʻoli. Eia nō naʻe, hiki iā ʻoe ke piʻi iki i ka pilikia o nā maʻi puʻuwai. No laila, e kamaʻilio me kāu kauka e pili ana i ka lawe ʻana i nā antibiotics e pale aku i nā maʻi ke loaʻa iā ʻoe nā kaʻina hana niho a i ʻole nā ʻoki ʻē aʻe. Hiki i kēia ke hōʻemi i ka pilikia o nā maʻi e like me ka endocarditis.
Loaʻa iaʻu (Structural Heart Disease), pehea wau e mālama ai iaʻu iho?
Hiki iā ʻoe ke hana i kēia mau mea e mālama i kou puʻuwai olakino a hōʻemi i nā pilikia:
- E hoʻomaopopo i nā kauka a pau e mālama iā ʻoe e pili ana i kou maʻi puʻuwai a me nā lāʻau lapaʻau āu e lawe nei.
- Inā ʻoe e hoʻolālā ana e hāpai, e kamaʻilio me kāu mau kauka ma mua loa. Hiki iā lākou ke loiloi i kou mau pilikia a kōkua iā ʻoe e ʻike i ke ala maikaʻi loa e hoʻokele ai i kou kūlana i ka wā hāpai.
- E ʻike pinepine i kahi kauka puʻuwai e nānā i kou kūlana. Mai ho'ōki i ka lawe ʻana i kāu lāʻau lapaʻau i kuhikuhi ʻia a i ʻole e hōʻole i nā manawa o kāu kauka.
ʻO ka mea hope loa, nā mea e hoʻomanaʻo ai (Leka Lawe-Home)
ʻO ka Maʻi Puʻuwai Kūkulu he pilikia ia me ke ʻano o kou puʻuwai, ʻo ia hoʻi ke ʻano, nā paia, nā kiwikā, a i ʻole nā ʻiʻo. Hiki ke loaʻa i ka wā hānau a i ʻole e ulu aʻe ma hope o ke ola. ʻO nā ʻano nui ka cardiomyopathy, ka maʻi puʻuwai hānau, a me ka maʻi kiwikā puʻuwai.
ʻAʻole paha ʻoe e pono i ka lāʻau lapaʻau, a i ʻole e ʻōlelo paha kāu kauka i ka lāʻau lapaʻau a i ʻole ke ʻoki kino. ʻO ka mea nui loa, ʻo ia ka hahai ʻana i kahi nohona olakino a ʻike pinepine i kahi kauka cardiologist. A laila hiki iā ʻoe ke ola i kahi ola hauʻoli a piha. Inā he mau nīnau hou kāu e pili ana i kēia, mai kānalua e kamaʻilio me kāu kauka.
ʻO ka maʻi puʻuwai, ke ʻano o ka puʻuwai, ka maʻi puʻuwai kūkulu, ka maʻi valve puʻuwai, ka maʻi puʻuwai hānau, Cardiomyopathy, nā hōʻailona maʻi puʻuwai, nā hoʻāʻo maʻi puʻuwai, ka mālama ʻana i ka maʻi puʻuwai











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