Ua loaʻa koke iā ʻoe kahi ʻeha poʻo nui a me ka ʻeha ke neʻe ʻoe i kou mau maka? A i ʻole ke manaʻo nei ʻoe ʻaʻole hiki iā ʻoe ke kāohi pono i kou mau maka? Inā loaʻa iā ʻoe nā hōʻailona e like me kēia, hiki ke kumu o kahi maʻi laha ʻole i kapa ʻia ʻo Tolosa-Hunt Syndrome, a mākou e kamaʻilio nei i kēia lā. Mai hopohopo, e kamaʻilio mākou e pili ana i nā mea āpau ma ke ʻano maʻalahi hiki iā ʻoe ke hoʻomaopopo.
He aha ka Tolosa-Hunt Syndrome?
I ka ʻōlelo maʻalahi, he maʻi laha ʻole ka maʻi Tolosa-Hunt. Hoʻoulu ia i nā ʻeha poʻo koke a koʻikoʻi a me ka ʻeha i ka neʻe ʻana i kou mau maka, a i ʻole ka nalowale o ka hiki ke hoʻoneʻe i kou mau maka. Hiki i kēia mau hōʻailona ke hele mai a hele i loko o kou ola. Ua like ia me ka loaʻa ʻana o kahi malihini i kono ʻole ʻia i loko o kou hale. Hoʻopilikia lākou i kou lā a hoʻoluhi iā ʻoe. Akā, ʻo ka mea pōmaikaʻi, ʻaʻole pinepine kēia mau malihini e hele mai.
Ua hōʻike ʻia e ka noiʻi ʻo ke kumu o kēia kūlana paha ka pehu ʻana ma hope o ka maka, ʻo ia ka pane mai ka ʻōnaehana pale o ko mākou kino (ka mumū).
Ua lohe paha ʻoe i kāu kauka e kapa ana i kēia maʻi ma nā inoa ʻē aʻe. Eia kekahi laʻana:
- ʻO ka maka (Ophthalmoplegia)
- `(Ophthalmoplegia Hoʻi Hou)` (ʻO ia hoʻi, hoʻi hou ia)
- ʻO ka maʻi ʻeha o ka maka (Ophthalmoplegia Syndrome)
ʻOiai he aha ka inoa i kapa ʻia ai, ʻo ia hoʻi ke ʻano like: ʻo Tolosa-Hunt syndrome.
Pehea ka maʻamau o kēia kūlana?
He mea kākaʻikahi loa kēia. Inā ʻoe e nānā i nā helu helu a puni ka honua, hōʻike nā haʻawina e pili ana i hoʻokahi i loko o hoʻokahi miliona mau kānaka e loaʻa i ka maʻi Tolosa-Hunt. No laila, ʻaʻole kēia he maʻi e hoʻopilikia i nā mea āpau.
He aha nā hōʻailona o ka maʻi Tolosa-Hunt?
ʻIke koke ʻia kēia mau hōʻailona. ʻO nā hōʻailona nui e ʻike ʻia:
- ʻEha poʻo nui: ʻAʻole like kēia me ke poʻo poʻo maʻamau. Loaʻa kēia ʻeha ma ka ʻaoʻao o luna o ka maka, ʻoi aku hoʻi a puni nā maka (he 'ʻeha poʻo periorbital'). Manaʻo paha kekahi poʻe he ʻeha ʻoi, e like me ka ʻō ʻana o ka pahi. Manaʻo paha kekahi he ʻeha palupalu a he ʻeha palupalu paha .
- ʻIke pālua: Ke nānā ʻoe i hoʻokahi mea, ʻike ʻia ia he ʻelua mau mea kaʻawale. Me he mea lā ʻaʻole i kālele pono nā maka ʻelua. He hōʻailona hoʻopilikia loa kēia.
- Ka nāwaliwali a i ʻole ka hiki ʻole ke hoʻoneʻe i nā ʻiʻo a puni nā maka a me ke alo: Lilo i mea paʻakikī ke hoʻoneʻe i nā maka, i kekahi manawa a i kekahi ʻaoʻao. Hiki ke hoʻopilikia ʻia nā ʻiʻo o ke alo.
- Luhi mau loa: E luhi paha ʻoe i ka lā a pau, me he mea lā ʻaʻole hiki iā ʻoe ke hoʻopau i ka luhi me ka nānā ʻole i ka nui o kāu hiamoe ʻana.
Ma waho aʻe o kēia mau mea nui, hiki ke ʻike ʻia kekahi mau mea ʻē aʻe:
- Ka puka ʻana o nā maka (proptosis): Hiki i kekahi a i ʻole nā maka ʻelua ke ʻike ʻia e puka iki i mua.
- Ke kulou ʻana o ka lihilihi o luna (ptosis):ʻAʻole paha e hiki ke hāpai pono ʻia ka lihilihi o luna o kekahi a i ʻole nā maka ʻelua a me he mea lā e kulou ana.
- Poho ʻike: Hiki i kekahi poʻe ke nalowale iki ka ʻike.
Hoʻopilikia pinepine kēia mau hōʻailona i hoʻokahi ʻaoʻao o ka maka. Hiki iā lākou ke ʻike koke ʻia a nalo koke i loko o kekahi mau lā (remission spontaneous). Eia naʻe, hiki iā lākou ke hana hou.
He aha ke kumu o ka maʻi Tolosa-Hunt?
ʻO kaʻoiaʻiʻo, ʻaʻole mākou i ʻike pono i ke kumu . Akā, aia ʻelua mau mea nui a nā kauka a me nā mea noiʻi e manaʻo nei he hiki ke hana:
1. Pane autoimmune maʻamau ʻole: ʻO kēia ka manawa e hoʻouka hewa ai kā mākou ʻōnaehana pale kino - ka ʻōnaehana e pale ai iā mākou mai ka maʻi - i kā mākou mau ʻiʻo olakino ponoʻī. I ka maʻi Tolosa-Hunt, hana ʻia kēia hoʻouka ma nā wahi ʻelua koʻikoʻi loa ma hope o ka maka. ʻO kekahi ʻo ka "Cavernous Sinus" , kahi ʻāpana e like me ke lua i loaʻa nā aʻa koko koʻikoʻi a me nā aʻalolo e hoʻolako i ke koko i ka lolo. ʻO kekahi ʻo ka "Orbital Fissure" , kahi puka e hele ai nā aʻalolo a me nā kīʻaha koko e pili ana i ka maka. Hoʻouka kā mākou ʻōnaehana pale kino ponoʻī i kēia mau wahi, e hoʻoulu ai i ka pehu ma laila.
2. Ka pehu ʻana a i ʻole ka hāiki ʻana o nā kīʻaha koko: ʻO kekahi manaʻo ʻē aʻe, ʻo ia ka loaʻa ʻana o kēia mau hōʻailona no ka mea, ua pehu a ʻūmiʻi nā kīʻaha koko ma kēia mau wahi i kapa ʻia ʻo "Cavernous Sinus" a me "Orbital Fissure", e hōʻemi ana i ke kahe koko i kekahi mau ʻāpana o ka lolo a me nā aʻalolo e pili ana i ka maka.
Aia nō kēia mau mea ʻelua i ke kahua noiʻi, no laila he paʻakikī ke ʻōlelo i kahi kumu kikoʻī.
He aha nā kumu pilikia no kēia?
Hiki i kekahi mau mea ke hoʻonui i ka pilikia o ka loaʻa ʻana o nā hōʻailona o ka maʻi Tolosa-Hunt. Ua kapa ʻia kēia mau mea he 'triggers'. ʻO lākou kekahi:
- Loaʻa i kahi maʻi viral .
- He ʻeha lolo traumatic .
- Loaʻa kahi puʻupuʻu ma kekahi wahi o ke kino, ʻoi aku hoʻi ma ke poʻo.
- ʻO ke kūlana e like me ka hoʻonui ʻana a i ʻole ka puʻupuʻu (aneurysm) o kahi kīʻaha koko.
ʻAʻole e loaʻa i nā kānaka a pau kēia maʻi no ka mea wale nō he mau mea kēia iā lākou, akā, e hoʻonui iki ʻia paha ka pilikia.
He aha nā pilikia e hiki ai i kēia ke hana?
ʻO ka hapa nui o ka manawa, ʻaʻole ia he maʻi hoʻoweliweli ola ka maʻi Tolosa-Hunt. Eia nō naʻe, i kekahi mau hihia koʻikoʻi, hiki iā ia ke hoʻopilikia i kou ʻike. Hana ʻia kēia i ka wā e pālahalaha ai ka pehu ma ka "Cavernous Sinus" a me ka "Orbital Fissure" ma hope o ka maka i ka "Optic Nerve", ke aʻalolo nui e hāʻawi mai iā mākou i ka ʻike. Inā hana ʻia kēia, hiki ke nalowale ka ʻike a i ʻole nā hemahema ʻike ʻē aʻe. No laila, he mea nui e ʻimi i ka lāʻau lapaʻau i ka wā e ʻike ʻia ai nā hōʻailona.
Pehea e ʻike ʻia ai kēia?
E ʻike ke kauka i kēia ma hope o ka hoʻolohe pono ʻana i kāu mau hōʻailona, e nānā iā ʻoe, a me ka lawe ʻana i kāu mōʻaukala olakino piha. He hana paʻakikī iki kēia, ʻoiai hiki ke ʻike ʻia kēia mau hōʻailona i nā kūlana olakino ʻē aʻe.
No laila, hana ʻia nā hoʻokolohua koko a me nā hoʻokolohua kiʻi e hōʻoia i ka hōʻailona a kāpae i nā kūlana ʻē aʻe me nā hōʻailona like (no ka laʻana, kahi puʻupuʻu lolo a i ʻole ka maʻi). ʻO nā hoʻokolohua kiʻi ʻelua nui i hoʻohana ʻia no kēia:
- ʻO ke kiʻi Computed Tomography (CT): Hoʻohana kēia i nā kukuna X a me ke kamepiula e hana i kahi kiʻi ʻekolu-dimensional (3D) o nā ʻiʻo palupalu a me nā iwi i loko o kou kino. Hiki i kēia ke kōkua i ka nānā ʻana i nā mea e like me ka pehu ʻana ma ka ʻāpana sinus cavernous.
- ʻIke Resonance Magnetic (MRI): Hoʻohana kēia i kahi magnet nui, nā nalu lekiō, a me kahi kamepiula e hana i nā kiʻi maopopo loa o loko o kou kino, ʻoiai nā wahi o ka lolo a me nā maka. ʻOi aku ka kikoʻī ma mua o ka CT scan.
Hoʻohana nā kauka i kēia mau scan e nānā pono i ka pehu ʻana ma nā wahi ma hope o nā maka i kapa ʻia ʻo "Cavernous Sinus" a me "Orbital Fissure." Kōkua pū kēia mau hoʻokolohua e hōʻoia ʻaʻohe kumu ʻē aʻe.
I ka manawa hea e ʻike pinepine ʻia ai ka maʻi Tolosa-Hunt?
ʻOiai hiki ke hoʻopilikia kēia maʻi i nā kānaka o kēlā me kēia makahiki, ʻike pinepine ʻia ia ma kahi o 40 mau makahiki .
Pehea e mālama ʻia ai kēia?
Hoʻōla ʻia kēia me ke ʻano lāʻau lapaʻau pōkole '(Steroid)' . ʻOi aku ka hoʻohana ʻia ʻana o ke ʻano lāʻau lapaʻau '(Corticosteroids)' . ʻO ka hana a kēia mau lāʻau lapaʻau, ʻo ia ka hōʻemi ʻana i kēlā pehu ('inflammation'). No ka mea, ʻo ke kumu nui o kou mau hōʻailona, ʻo ia kēia pehu ma hope o ka maka.
Ke lawe ʻoe i kēia lāʻau lapaʻau i kapa ʻia ʻo "Corticosteroids," e emi ana ka pehu, e hoʻomaha ʻia ke kaomi ma luna o nā aʻalolo, a e hoʻomaikaʻi koke ʻia kou mau hōʻailona.
Aia kekahi mau hopena ʻaoʻao o ka lāʻau lapaʻau?
ʻAe, e like me nā lāʻau lapaʻau āpau, hiki i ka `(Corticosteroids)` ke loaʻa kekahi mau hopena ʻaoʻao. No laila, pono ʻoe e kūkākūkā i kēia me kāu kauka ma mua o ka hoʻomaka ʻana i kēia lāʻau lapaʻau. A laila hiki iā ʻoe ke loaʻa kahi ʻike maopopo e pili ana i ia mea. ʻO kekahi o nā hopena ʻaoʻao hiki ke loaʻa:
- Pehu wāwae
- Hoʻonui ʻia ka makemake
- Nā loli o ke ʻano
- ʻEha maʻalahi
- ʻIke pōwehiwehi iki
ʻAʻole hiki kēia i nā kānaka a pau, a i ka hapanui o nā hihia, e emi ana lākou ke pau ka lāʻau lapaʻau.
Pehea ka wikiwiki o koʻu ho'ōla ʻana ma hope o ka lāʻau lapaʻau?
ʻO kēia ka nūhou maikaʻi loa. Ma hope o ka lawe ʻana i ka lāʻau steroid e like me ke kauoha, hiki iā ʻoe ke hoʻomaka e ʻike i ka hōʻoluʻolu nui i loko o kahi manawa pōkole, e like me hoʻokahi a ʻekolu paha lā. Hoʻemi ʻia ka ʻeha, lilo ia i mea maʻalahi ke hoʻoneʻe i kou mau maka, a nalowale mālie kēlā mau hōʻailona hoʻonāukiuki.
E noʻonoʻo wale, inā ʻaʻole ʻoe e loaʻa i ka lāʻau lapaʻau, hiki i nā hōʻailona ke emi iho i loko o 15 a 20 mau lā. Eia naʻe, ʻaʻole ʻoe makemake e ʻeha no ia manawa lōʻihi. Eia kekahi, ma hope o ka nalowale ʻana o nā hōʻailona, hiki iā lākou ke ʻike hou ʻia me ka manaʻo ʻole. No laila, ʻoi aku ka maikaʻi o ka loaʻa ʻana o ka lāʻau lapaʻau.
He kūlana koʻikoʻi anei kēia?
ʻAʻole he maʻi hoʻoweliweli ola ka maʻi Tolosa-Hunt. Eia nō naʻe, ke ʻike ʻia nā hōʻailona, hiki ke paʻakikī ke hana i nā hana maʻamau o kēlā me kēia lā, ʻoiai me nā ʻeha poʻo nui a me nā pilikia maka.
Eia nō naʻe, me ka mālama ʻana, maikaʻi loa ka wānana. ʻOiai ʻo nā steroids e hōʻemi i nā hōʻailona i loko o 24 a 72 mau hola, e ʻoluʻolu koke ʻoe a hiki iā ʻoe ke hoʻi hou i kāu mau hana maʻamau.
Hiki ke ho'ōla loa ʻia ka maʻi Tolosa-Hunt?
ʻO ka mea pōʻino, ʻaʻohe lāʻau lapaʻau no kēia maʻi. ʻO ka manaʻo o ka lāʻau lapaʻau ka kaohi ʻana i nā hōʻailona a me ka hōʻemi koke ʻana iā lākou. Hiki ke hoʻi hou mai nā hōʻailona, no laila pono paha ka lāʻau lapaʻau.
Hiki ke pale ʻia kēia?
ʻAʻohe ala i ʻike ʻia e pale aku ai i kēia maʻi i kēia manawa. No ka mea, e like me kā mākou i kūkākūkā ai ma mua, ʻaʻole i ʻike ʻia ke kumu pololei, he paʻakikī ke ʻōlelo pehea e pale aku ai.
Āhea ʻoe e ʻike ai i ke kauka?
Inā manaʻo ʻoe he mau hōʻailona kou o ka maʻi Tolosa-Hunt - e like me ka ʻeha poʻo koke a koʻikoʻi, ka ʻeha a puni nā maka, ka ʻike pālua, a me ka paʻakikī i ka neʻe ʻana i kou mau maka - e ʻike koke i ke kauka. Mai hoʻokaʻulua.
A laila e kuhikuhi ke kauka i nā steroids pōkole e mālama i kāu mau hōʻailona. Ma muli o ka hana wikiwiki ʻana o kēia mau mea, e ʻoluʻolu koke ʻoe a hiki ke hoʻi i kou ola maʻamau.
He aha nā nīnau āu e nīnau ai i kāu kauka?
Ke hele ʻoe e ʻike i ke kauka, he mea maikaʻi ke nīnau i kekahi mau nīnau e like me kēia:
- Hiki i ka maʻi Tolosa-Hunt ke hoʻopilikia i koʻu ʻike?
- Pono maoli anei iaʻu e lawe i nā steroids ma ke ʻano he lāʻau lapaʻau no kēia?
- Pehea e lawe ai au i ka lāʻau lapaʻau '(Steroid)'? Pehea ka lōʻihi e lawe ai au?
- He aha nā hopena ʻaoʻao o kēia mau lāʻau lapaʻau? He aha kaʻu e hana ai e pale aku iaʻu iho mai ia mau mea?
- He aha kaʻu e hana ai inā hoʻi mai nā hōʻailona?
Ma ka nīnau ʻana i nā nīnau e like me kēia, e loaʻa iā ʻoe kahi ʻike maikaʻi aʻe i ka maʻi a me kona mālama ʻana.
ʻO ka mea hope loa, e hoʻomanaʻo i kēia (Leka Lawe-Home)
ʻO ka Tolosa-Hunt Syndrome kahi maʻi e hiki koke mai ana a hoʻoulu i nā hōʻailona ʻoluʻolu ʻole. Hiki i nā ʻeha poʻo koʻikoʻi ke paʻakikī i ka hana ʻana i kāu mau hana o kēlā me kēia lā. Hiki ke hoʻopilikia ʻia ka ʻike. Hiki i kēia mau hōʻailona ke hele mai a hele a hala i ke ola holoʻokoʻa.
Akā e hoʻomanaʻo, ʻaʻole kēia he mea hoʻoweliweli i ke ola, a aia nā lāʻau lapaʻau.Hiki i ka hoʻohana pōkole ʻana i nā steroids ke hōʻemi i nā hōʻailona i loko o hoʻokahi a ʻekolu mau lā. No laila, inā ʻoe e ʻike i ke kauka i ka wā e ʻike ʻia ai nā hōʻailona a loaʻa ka lāʻau lapaʻau, hiki iā ʻoe ke hoʻōla koke a hoʻi i ka hana ʻana i nā mea āu e makemake ai. Mai makaʻu, e kamaʻilio me kāu kauka e pili ana i kekahi mea.
ʻO ka maʻi Tolosa-Hunt, ʻeha poʻo, ʻeha maka, ʻike pālua, Steroids, MRI, CT scan, Ophthalmoplegia, Cavernous Sinus











💬 Comments (0)
ʻAʻohe manaʻo i kau ʻia. Hoʻohui i kāu manaʻo ma ʻaneʻi no ka manawa mua.
Hoʻohui i kāu manaʻo