Ua kuhikuhi ʻia anei ʻoe a i ʻole kāu keiki i ka Triheptanoin? E kamaʻilio maʻalahi kākou e pili ana i kēia.

I kekahi manawa, kuhikuhi nā kauka i nā lāʻau lapaʻau kūikawā loa a mākou i lohe ʻole ai. ʻO Triheptanoin kekahi o ia mau lāʻau wai kūikawā. ʻAʻole ia e hāʻawi pinepine ʻia i nā mea āpau. Hoʻohana kūikawā ʻia ia no ka poʻe e ʻeha nei i kahi maʻi genetic laha ʻole i kapa ʻia ʻo LC-FAOD, a i ʻole nā ​​​​maʻi oxidation acid fatty Long-chain. No laila, inā ua kuhikuhi kāu kauka i kēia lāʻau lapaʻau nou a i ʻole kāu keiki, e kōkua nui kēia ʻatikala iā ʻoe i ka hoʻomaopopo ʻana i nā nīnau, nā hopohopo, a me nā makaʻu e pili ana i ia mea ma ke ʻano maʻalahi.

He aha ka mea e hana maoli me kēia lāʻau lapaʻau?

E ʻōlelo maʻalahi kākou. Pono nā ʻāpana o ko kākou kino i ka ikehu e hana ai. No ka hoʻoulu ʻana i kēia ikehu, hoʻohana nui ko kākou kino i nā kalapona a me ka momona mai ka meaʻai a kākou e ʻai ai. Eia nō naʻe, i ka poʻe me kahi maʻi genetic i kapa ʻia ʻo LC-FAOD, ʻaʻole hiki i ke kino ke wāwahi i nā waikawa momona kaulahao lōʻihi e hoʻoulu ai i ka ikehu. He nāwaliwali ia i loko o ko lākou mau genes.

ʻO kēia kahi e komo mai ai ʻo Triheptanoin. ʻOi aku ia he mea hoʻohui momona ma mua o ka lāʻau lapaʻau. Loaʻa iā ia kahi ʻano momona kūikawā e hiki i ke kino ke omo maʻalahi a hoʻololi i ka ikehu. I nā huaʻōlelo ʻē aʻe, hāʻawi kēia lāʻau i ka ikehu a me nā calorie i hiki ʻole i ke kino ke loaʻa ma muli o LC-FAOD ma o kekahi ala ʻē aʻe.

Nā mea e pono ai ʻoe e haʻi i kāu kauka ma mua o ka lawe ʻana i kēia lāʻau lapaʻau

Ma mua o ke kau ʻana i kēia lāʻau lapaʻau, he mea nui loa i kāu kauka ke ʻike i kou mōʻaukala olakino piha. E hōʻoia e haʻi iā lākou e pili ana i kekahi o kēia mau mea:

Pehea e pono ai iaʻu ke hoʻohana i kēia lāʻau lapaʻau?

He mea nui loa ia e ʻike pono pehea e hoʻohana ai i kēia lāʻau.

• E hahai i nā ʻōlelo a kāu kauka: E lawe i ka lāʻau lapaʻau e like me ke kauoha, ma ka nui i kauoha ʻia, a i ka manawa kūpono. Mai hoʻololi i ka nui ma kāu manaʻo ponoʻī.
• E lawe pū me ka meaʻai: Pono e lawe ʻia kēia lāʻau lapaʻau me ka ʻai a ma hope paha o ka ʻai ʻana.
• E heluhelu i nā kuhikuhi: E heluhelu pono i nā KUHI NO KA HOʻOHANA ʻANA e hele mai me ka lāʻau lapaʻau. Inā ʻaʻole maopopo kekahi mea, mai hilahila e noi i kāu kauka e wehewehe.
• Ke hāʻawi ʻia i nā keiki: Hiki ke hāʻawi ʻia kēia lāʻau lapaʻau i nā pēpē hānau hou i kekahi mau hihia kūikawā. Eia nō naʻe, ʻo ke kauka o kāu keiki wale nō ke hoʻoholo i kēia. No laila, e hana e like me kāu kauka e ʻōlelo ai iā ʻoe.

He aha inā lawe nui wau i ka lāʻau lapaʻau?

Inā manaʻo ʻoe ua lawe ʻoe ma mua o ka nui i kuhikuhi ʻia, ma ke kuhihewa a i ʻole ma ka ulia pōpilikia, e kelepona koke i ke Kikowaena ʻIke Poisons Lahui ma ka Halemai Lahui ʻo Colombo. A i ʻole, mai hoʻonele i ka manawa a hele i ka Emergency Treatment Unit (ETU) o ka haukapila kokoke loa.

He aha kāu e hana ai inā e poina ʻoe i kahi mahele o ka lāʻau lapaʻau?

Inā poina iā ʻoe ke lawe i kahi lāʻau, e lawe koke iā ia i kou hoʻomanaʻo ʻana. E waiho i 3 a 4 mau hola ma waena o kēlā me kēia lāʻau. Eia nō naʻe, inā ʻaʻole lawa ka manawa e lawe ai i ka lāʻau piha no ka lā (no ka laʻana, inā kokoke i ka manawa no ka lā aʻe), e kāpae i ka lāʻau i hala ʻole a lawe i ka lāʻau aʻe i ka manawa maʻamau. Mai lawe i ʻelua mau lāʻau i ka manawa hoʻokahi e hoʻopiha ai i kahi lāʻau i hala ʻole.

Nā hopena ʻaoʻao paha o ka lawe ʻana i ka lāʻau lapaʻau

E like me nā lāʻau lapaʻau āpau, hiki i ka triheptanoin ke hana i nā hopena ʻaoʻao i kekahi poʻe. He koʻikoʻi kekahi o kēia mau mea, a he akahai kekahi.

Ka mālama ʻana a me ka hoʻolei ʻana i nā lāʻau lapaʻau

Ma hea wau e waiho ai?

• E mālama pono iā ia mai ka hiki ʻana aku o nā keiki a me nā holoholona .
• E mālama ma ka mahana o ka lumi (ma waena o 20 a me 25 kekelē Celsius). Mai hoʻopaʻahau.
• E mālama i ka lāʻau lapaʻau i loko o ka ʻōmole kumu i hoʻokomo ʻia ai.
• E hoʻolei i kekahi lāʻau lapaʻau i koe 9 mau mahina ma hope o ka wehe ʻana i ka ʻōmole a i ʻole ma hope o ka lā pau (ʻo ka mea e hiki mua mai).

Pehea ʻoe e hoʻopau ai i nā lāʻau lapaʻau pono ʻole?

Mai hoʻolei wale i nā lāʻau lapaʻau i pau ka manawa a i ʻole i hoʻohana ʻole ʻia i loko o ka ʻōpala.

• ʻO ka mea maikaʻi loa e hana ai, ʻo ia ke hāʻawi iā lākou i kahi papahana lawe-hoʻihoʻi lāʻau. Hiki iā ʻoe ke nīnau i kāu hale kūʻai lāʻau lapaʻau kūloko a i ʻole ka haukapila e pili ana i ia mau wahi.
• Inā ʻaʻole hiki iā ʻoe ke loaʻa i ia ʻano polokalamu, e lawe i ka lāʻau lapaʻau mai loko mai o ka ʻōmole, e kāwili maikaʻi me kahi mea e like me nā lau kī i hoʻohana ʻia, nā ʻōpala kope, a i ʻole ka lepo, e hoʻokomo i loko o kahi ʻeke palakiko i hoʻopaʻa pono ʻia, a e hoʻolei i loko o ka ʻōpala.
• Inā ʻaʻole ʻoe maopopo pehea e wehe ai, e nīnau i kāu kauka.