Ua manaʻo paha ʻoe e like me ʻoe e pupule ana, ʻeha kou mau hono, a i ʻole e loaʻa ana i kou ʻili nā ʻano ʻulaʻula a i ʻole nā kiko? Hoʻopoina pinepine mākou i kēia mau mea, me ka manaʻo he mea maʻamau lākou. Akā i kekahi manawa, ma hope o kēia mau hōʻailona liʻiliʻi, aia paha kahi maʻi koʻikoʻi a mākou i lohe ʻole ai. I kēia lā, e kamaʻilio mākou e pili ana i kekahi maʻi like ʻole, ʻo ia hoʻi ʻo Vasculitis . He mea hou paha kēia inoa iā ʻoe. Akā he mea nui loa ia e makaʻala i kēia.
He aha ka Vasculitis? E hoʻomaopopo maʻalahi kākou.
I ka ʻōlelo maʻalahi, ʻo Vasculitis kahi mumū a pehu paha o kou mau kīʻaha koko, ʻo ia hoʻi, nā kīʻaha koko . I kēia manawa ke noʻonoʻo nei paha ʻoe i ke ʻano o kēia mau kīʻaha koko. E wehewehe iki kākou i kēlā.
E noʻonoʻo i ka ʻōnaehana aʻa koko i loko o ko kākou kino e like me kahi pūnaewele o nā alanui ma Sri Lanka. Lawe kēia mau alanui i ka oxygen a me nā meaʻai i kēlā me kēia cell i loko o ko kākou kino. ʻEkolu mau ʻano nui o kēia pūnaewele o nā alanui:
- Nā aʻa koko: Ua like kēia me nā alaloa nui. Lawe kēia mau aʻa koko nui i ke koko maʻemaʻe mai ka puʻuwai a puni ke kino.
- Nā aʻa koko: ʻO kēia nā ala e hoʻihoʻi mai i ke koko i hoʻohana ʻia, ʻo ia hoʻi, ke koko lepo, i ka puʻuwai.
- Nā Capillaries: ʻO kēia nā ala liʻiliʻi e hoʻohui i nā alaloa a me nā alanui ʻē aʻe. Loaʻa i kēlā me kēia cell i loko o ke kino nā meaʻai mai ke koko ma o kēia mau kīʻaha koko liʻiliʻi.
I kēia manawa, ua maopopo iā ʻoe? Hoʻopilikia ka Vasculitis i ka pūnaewele o nā kīʻaha koko. Ke hiki mai kēia maʻi, pehu a mānoanoa nā paia o nā kīʻaha koko. E like me ke alanui e lilo ai i haiki a paʻakikī no nā kaʻa e hele ai, lilo ia i mea paʻakikī no ke kahe ʻana o ke koko ma o kēia mau kīʻaha koko i haiki.
Ke hoʻopilikia ʻia ke kahe koko ma kēia ʻano, hoʻomaka ka hōʻino ʻia o nā ʻōpū e hānai ʻia e kēlā mau kīʻaha koko (no ka laʻana, nā puʻupaʻa, nā māmā, ka ʻili). I kekahi manawa hiki i nā paia o nā kīʻaha koko ke nāwaliwali a puʻupuʻu e like me ka pōpō. Kāhea mākou i kēia he aneurysm . He kūlana weliweli loa ia.
Hiki i nā kānaka he nui ke kāohi i kēia mau hōʻailona me ka lāʻau lapaʻau. Eia nō naʻe, inā ʻoki ʻia ke kahe koko i nā ʻōpū koʻikoʻi, hiki i kēia ke lilo i mea hoʻoweliweli i ke ola .
Ma hea kahi e hoʻopilikia ai ka vasculitis i ke kino?
ʻO kaʻoiaʻiʻo, hiki iā ia ke hoʻopilikia i kekahi ʻāpana o ke kino me nā kīʻaha koko. ʻO ia hoʻi, hiki iā ia ke hoʻopilikia i kekahi ʻōkana mai ke poʻo a i nā wāwae.
Eia kekahi o nā wahi nui kahi e hiki ai ke loaʻa nā hopena:
- ʻIli
- Nā māmā
- Puʻuwai
- Nā aʻalolo
- Nā maka
- nā puʻupaʻa
- lolo
- Nā Sinus
- ʻŌpū a me nā ʻōpū (ʻŌpū)
- Nā lima a me nā wāwae
He aha nā hōʻailona maʻamau o ka vasculitis?
Hiki ke ʻokoʻa loa nā hōʻailona o kēia maʻi mai kēlā kanaka a kēia kanaka. Aia ia i ke ʻano o ka ʻōpū i hoʻopilikia ʻia ai nā kīʻaha koko a me ke koʻikoʻi o ka mumū. No ka laʻana, inā loaʻa i kekahi nā kīʻaha koko i loko o ko lākou ʻili, hiki iā lākou ke loaʻa kahi ʻulaʻula a me nā kiko ʻulaʻula ma ko lākou ʻili. Inā loaʻa i kekahi maʻi puʻupaʻa, hiki iā lākou ke loaʻa ke koko i loko o ko lākou mimi.
Eia nō naʻe, aia kekahi mau hōʻailona maʻamau ʻaʻole i pili pono i kēia maʻi. Inā ʻike ʻoe i kekahi o kēia mau hōʻailona i ka manawa like, pono ʻoe e ʻike i ke kauka.
| Hōʻailona | I ka ʻōlelo maʻalahi... |
|---|---|
| Nā ʻano laulā | Kuni, luhi, pohō kaumaha, ʻeha kino. |
| Nā hōʻailona pili i ka ʻili | Nā kiko ʻulaʻula a poni paha ma ka ʻili, eczema, a me nā ʻeha paha. |
| Nā hōʻailona e pili ana i ke aʻalolo | ʻO ka mae, ke ʻūlū, ka nāwaliwali o nā lālā. |
| Nā hōʻailona e pili ana i ka ʻōnaehana hanu | Paʻakikī ka hanu ʻana, ka ʻūhū (hiki paha me ke koko). |
| Nā hōʻailona e pili ana i nā puʻupaʻa | Ka ʻeleʻele o ka mimi, ke koko i loko o ka mimi. |
| Nā hiʻohiʻona ʻē aʻe | Nā kūlana e like me ka ʻeha o ke hono, ka ʻeha o ka ʻōpū, a me ka hahau ʻana. |
No ke aha e hana ai kēia vasculitis?
He nīnau paʻakikī kēia. He maʻi autoimmune ka Vasculitis. He aha ke ʻano o kēia?
He ʻōnaehana pale akamai loa ko ko kākou kino. Kapa mākou iā ia he ʻōnaehana pale. ʻO kāna hana ke pale iā kākou mai nā maʻi ma ke kaua ʻana i nā germs (viruses, bacteria) e komo i loko o ke kino. Eia nō naʻe, i loko o kahi maʻi autoimmune, lilo kēia ʻōnaehana pale i hewa a hoʻomaka e hoʻouka i kā kākou mau cell olakino ponoʻī ma kahi o kahi mea hoʻouka kaua haole.
I ka vasculitis, hoʻouka kāu ʻōnaehana pale i kou mau kīʻaha koko ponoʻī . ʻAʻole maopopo i nā kānaka ʻepekema ke kumu o kēia.
Eia nō naʻe, ua ʻike ʻia hiki i kekahi mau mea ke hoʻoulu i kēia ʻano.
- Nā maʻi: Hiki ke hana ʻia kēia ʻano ma hope o kekahi mau maʻi viral a bacteria paha.
- Nā maʻi autoimmune ʻē aʻe: Inā loaʻa iā ʻoe kekahi maʻi autoimmune ʻē aʻe, e like me ka rheumatoid arthritis, ʻoi aku ka nui o ka pilikia o ka hoʻomohala ʻana i ka vasculitis.
- Kekahi mau lāʻau lapaʻau: I kekahi manawa pinepine, hiki ke hana ʻia kēia ma ke ʻano he hopena i kekahi mau lāʻau lapaʻau.
- Kekahi ʻano maʻi ʻaʻai: Hiki ke hana ʻia kēia ʻano e nā mea e like me nā maʻi ʻaʻai koko.
Aia kekahi mau ʻano o kēia maʻi?
ʻAe, aia ma mua o 30 mau ʻano o kēia. Hoʻokaʻawale nui ʻia lākou e like me ka nui o nā kīʻaha koko i hoʻopilikia ʻia (nui, waena, liʻiliʻi) a me ko lākou wahi. Inā mākou e kamaʻilio e pili ana i kēia mau ʻano āpau, e nalowale kāua. No laila e ʻike kākou i nā inoa o kekahi o nā ʻano nui i kūkākūkā ʻia.
- ʻO ka vasculitis e pili ana iā ANCA: He nui nā ʻano like ʻole o kēia.
- ʻO ka arteritis cell nui: He ʻano kēia e hoʻopilikia pinepine ai i ka poʻe ma luna o 50 mau makahiki a hoʻopilikia i nā aʻa nui ma ke poʻo a me ka ʻāʻī.
- ʻO Takayasu arteritis: He ʻano kēia e hoʻopilikia ai i nā aʻa nui.
- ʻO ka polyarteritis nodosa
- Maʻi Kawasaki: He ʻano kēia e kū pinepine ai i nā keiki ʻōpio.
- ʻO ka vasculitis IgA (Henoch-Schönlein purpura): He mea maʻamau kēia i waena o nā keiki.
ʻAʻole pono ʻoe e hoʻomanaʻo i kēia mau inoa. ʻO ka mea nui loa, ʻo ia ke ʻike pono o ke kauka i ke ʻano āu i loaʻa ai, no ka mea, e pili ana ka lāʻau lapaʻau i kēlā ʻano.
Pehea e ʻike ai ke kauka i kēia maʻi?
Hiki ke paʻakikī iki ka ʻike ʻana i ka vasculitis no ka mea ua like kona mau hōʻailona me nā maʻi ʻē aʻe he nui. No laila, ʻaʻole e kapa koke ke kauka iā ia he vasculitis.
Ke hele ʻoe e ʻike i ke kauka, e hoʻolohe mua ʻo ia i kāu mau hōʻailona a aʻo e pili ana iā lākou. A laila e nānā ʻo ia i kou kino. Eia kekahi, e kauoha ʻo ia i kekahi mau hoʻokolohua e hōʻoia i ka maʻi.
- Nā hoʻāʻo koko: Kōkua kēia i ka nānā ʻana i ka mumū i loko o ke kino (nā hoʻāʻo e like me ESR, CRP), a no nā antibodies kikoʻī e like me ANCA.
- Nā hoʻāʻo mimi: Hiki i kēia ke kōkua i ka hoʻoholo ʻana inā ua hoʻopilikia ʻia nā puʻupaʻa.
- Biopsy: ʻO kēia ke ala maikaʻi loa e hōʻoia ai i ka maʻi. Pili kēia i ka lawe ʻana i kahi ʻāpana liʻiliʻi loa o ka ʻiʻo mai kahi ʻāpana i hoʻopilikia ʻia (e like me ka ʻili, ka puʻupaʻa) a nānā iā ia ma lalo o kahi microscope.
- Angiogram: He hoʻāʻo kūikawā kēia e like me ke kiʻi X-ray e nānā ana i loko o kou mau kīʻaha koko. Hiki iā ia ke nānā inā ua haiki a pehu paha kou mau kīʻaha koko.
Ma hope o kēia mau hoʻokolohua, e hoʻouna ʻia paha ʻoe i kahi kauka i loea i nā maʻi mumū e like me kēia, he rheumatologist .
He aha nā lāʻau lapaʻau no ka vasculitis?
ʻElua mau pahuhopu nui i ka mālama ʻana i ka vasculitis.
1. Ke kāohi nei i ka mumū.
2. Ke hoʻōki nei i ka hana hewa ʻana o ka ʻōnaehana pale.
Hoʻohana nui ʻia nā lāʻau lapaʻau no kēia.
- Corticosteroids: He mau lāʻau lapaʻau ikaika kēia e kāohi koke i ka mumū. ʻO Prednisolone ka lāʻau lapaʻau i hoʻohana nui ʻia ma kēia papa.
- Nā Immunosuppressants: Hoʻomalu kēia mau lāʻau i ka hana o ka ʻōnaehana pale, ka mea e hoʻouka hewa i ke kino.
E hoʻoholo ʻia kēia ʻano lapaʻau e kāu kauka ma muli o ke ʻano a me ke koʻikoʻi o kou kūlana. I kekahi manawa, inā he pōʻino nui i nā kīʻaha koko, pono paha ke ʻoki ʻana e hoʻoponopono iā ia.
ʻO ka mea nui loa, ʻo ia ka lawe ʻana i ka lāʻau lapaʻau i kuhikuhi ʻia e ke kauka, ma ke ana kūpono a me ka manawa kūpono. ʻO ka hoʻōki ʻana i ka hapalua hiki ke hana i ka pōʻino nui.
Āhea wau e ʻimi ai i ke aʻo lapaʻau?
ʻO kēia ka ʻāpana koʻikoʻi loa o kēia ʻatikala. E hoʻolohe pono i kou kino. Inā ʻike ʻoe i kekahi mau loli a i ʻole nā mea ʻē aʻe, mai hoʻowahāwahā iā lākou.
| Nā kūlana e pono ai ka nānā koke ʻana | |
|---|---|
| E ʻike i kāu kauka... |
|
| E hele koke i ka Emergency Treatment Unit (ETU) o ka haukapila... |
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Leka Lawe-Home
- He mumū nā kīʻaha koko ka Vasculitis. He maʻi autoimmune ia.
- He ʻokoʻa loa nā hōʻailona o kēia maʻi. Hiki iā lākou ke ʻano mai nā hōʻailona maʻamau e like me ke kuni a me ka malaise i nā hōʻailona koʻikoʻi e like me ka ʻili ʻulaʻula a me ka paʻakikī o ka hanu ʻana.
- ʻAʻole hiki ke ho'ōla loa ʻia kēia maʻi. Eia nō naʻe, me ka mālama pono ʻana, hiki ke kaohi ʻia nā hōʻailona a hiki ke alakaʻi ʻia kahi ola maʻamau.
- Mai hoʻowahāwahā i nā hōʻailona hou a i ʻole e ʻoi aʻe ana paha i loko o kou kino. E hoʻomaopopo koke i kāu kauka.
- Inā pilikia ʻoe i ka hanu ʻana, nā hōʻailona o ka hāʻule puʻuwai, a i ʻole ka nalowale koke ʻana o ka ʻike, e hele i ka ʻOihana Pilikia (ETU) o ka haukapila kokoke loa me ke kānalua ʻole.











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