Ua lohe paha ʻoe i kahi maʻi ʻē e hoʻopilikia ai i ka lolo a me ka hoʻomanaʻo? I kekahi manawa, ʻaʻole mākou i ʻike i ka wā e nele ai ko mākou kino i kekahi mau huaora, ʻoiai ka huaora B1 i kapa ʻia ʻo "Thiamine", hiki ke hōʻino nui ʻia ko mākou lolo. ʻO kekahi o ia mau maʻi koʻikoʻi ʻo Wernicke-Korsakoff Syndrome (WKS) . He ʻano maʻi kēia e pono ai ka mālama koke. E kamaʻilio maʻalahi anei kākou e pili ana i kēia, ma ke ʻano e hiki ai iā ʻoe ke hoʻomaopopo?
He aha maoli ka Wernicke-Korsakoff syndrome (`WKS`)?
I ka ʻōlelo maʻalahi, he maʻi kēia e hoʻopilikia ai i ko kākou lolo a me ka hoʻomanaʻo. ʻO ke kumu nui o kēia, ʻo ia ka emi nui ʻana o ko kākou kino i ka 'Thiamine' (`Thiamine`) a i ʻole ka huaora B1 . E noʻonoʻo e pili ana, ua like ko kākou kino me ke kaʻa. ʻO ka ʻenekini o kēia kaʻa, ʻo ia ka lolo. Pono ka ʻenekini i ka ʻaila e holo ai. Pēlā nō, he mea nui ka huaora i kapa ʻia ʻo 'Thiamine` (`Thiamine`) no ka hana ʻana o ko kākou lolo a me ka ʻōnaehana nerve. ʻO kēia huaora ka mea e hoʻololi i ka meaʻai a kākou e ʻai ai i ikehu. No laila, ke emi kēia 'Thiamine` (`Thiamine`), ʻaʻole loaʻa i ka lolo ka ikehu e pono ai, a laila hoʻomaka nā hunaola o ka lolo e hōʻino ʻia.
ʻElua mau pae nui ma kēia `WKS`:
1. Wernicke encephalopathy: ʻO kēia ka ʻeha mua, koke, a koʻikoʻi o ka lolo. Pono ia i ka mālama koke ʻia.
2. Korsakoff syndrome: He kūlana lōʻihi kēia e hoʻopilikia nui ana i ka hoʻomanaʻo.
Ua kapa ʻia ʻo ia ma muli o ke kauka neurologist Kelemania ʻo Carl Wernicke a me ke kauka neurologist Lūkini ʻo Sergei Korsakoff, nāna i ʻike mua i ke ʻano.
He aha ka pilina ma waena o ka 'Wernicke's encephalopathy' a me ka 'Korsakoff syndrome'?
He pili nā mea ʻelua. I ka pololei, ʻo kahi kūlana i kapa ʻia ʻo "Wernicke encephalopathy", inā ʻaʻole mālama ʻia i ka manawa, ʻo ia ka mea e ulu mālie ai i kahi pilikia hoʻomanaʻo koʻikoʻi i kapa ʻia ʻo "Korsakoff syndrome".
ʻEkolu mau hōʻailona nui o ka Wernicke encephalopathy:
- Huikau: Nalowale o ka ʻike, nalowale o ka wahi a me ka manawa.
- ʻO ka nalowale o ke kaulike a me ka hiki ʻole ke kāohi i nā neʻe ʻana (`Ataxia`): Lilo ka hele wāwae i mea paʻakikī ke kāohi i nā lālā.
- Nā loli o ka ʻike a me nā pilikia maka: Nā neʻe maka maʻamau ʻole, e like me ka ʻike pālua.
Eia kekahi, i kekahi manawa hiki i nā ʻiʻo ke lilo i mea nāwaliwali.
Inā hoʻomau kēia mau hōʻailona no ka manawa lōʻihi, e hōʻino mau ʻia ka lolo a me nā hunaola nerve. ʻO kēia ka wā e nalowale nui ai ka hoʻomanaʻo a ʻaʻole hiki ke hoʻomanaʻo ʻia nā hoʻomanaʻo hou. Ua kapa ʻia kēia ʻo "Korsakoff syndrome".
ʻO ka Wernicke-Korsakoff Syndrome (WKS) kahi maʻi e hiki ke lilo i mea ʻino aʻe i ka hala ʻana o ka manawa a hiki ke hoʻoweliweli i ke ola. No laila, he mea nui ka mālama wikiwiki ʻana me ka thiamine. ʻO ka hana ʻana pēlā e hiki ke kōkua i ka hōʻoluʻolu ʻana i nā hōʻailona a pale i ka hōʻino mau loa ʻana i ka hoʻomanaʻo a me nā hana ʻē aʻe o ka lolo.
Inā loaʻa iā ʻoe a i ʻole kekahi mea kokoke iā ʻoe kēia mau hōʻailona, pono ʻoe e ʻike koke i ke kauka a i ʻole e hele i ka haukapila kokoke loa.
ʻO wai ka mea i hoʻopilikia nui ʻia e kēia kūlana?
ʻOi aku ka maʻamau o ka maʻi Wernicke-Korsakoff (WKS) i nā kāne ma mua o nā wahine. Loaʻa pinepine ia i nā poʻe ma waena o 30 a me 70 mau makahiki. ʻO ka hapa nui o ka poʻe e loaʻa ana iā WKS ma muli o ka hoʻohana ʻana i ka waiʻona he mau kāne ma luna o 40 mau makahiki. Eia nō naʻe, hiki i nā wahine a me nā poʻe ʻōpio ke loaʻa i ke kūlana no nā kumu ʻē aʻe ma mua o ka waiʻona. Kākaʻikahi ka hōʻike ʻia ʻana i nā keiki ʻōpio.
ʻO wai ka mea i ʻoi aku ka nui o ka pilikia o ka hoʻomohala ʻana i ka maʻi Wernicke-Korsakoff?
ʻO ka Wernicke encephalopathy kahi maʻi i ʻike nui ʻia i ka poʻe e hoʻohana nui ana i ka waiʻona (alcohol use disorder). Ke inu ʻia ka waiʻona no ka manawa lōʻihi, hōʻino ia i ka ʻōpū a me ka ʻōnaehana hoʻoheheʻe. Hoʻopilikia pū ia i ka hiki o ke kino ke omo i nā huaora (malabsorption). Ua ʻōlelo ʻia ma kahi o 80% o ka poʻe ʻona ʻona ʻaʻole hiki ke omo a mālama paha i ka thiamine lawa.
Eia kekahi, hiki i ka poʻe hiki ʻole ke omo pono i ka meaʻai ma muli o kekahi mau kūlana olakino ke loaʻa i ka `WKS`. No ka laʻana, hiki ke hana ma hope o ke ʻoki pohō kaumaha (`bariatric surgery`) a i ʻole he hopena ʻaoʻao o ka `chemotherapy` no ka maʻi ʻaʻai.
Eia kekahi mau kumu pilikia ʻē aʻe:
- Nā maʻi ʻōpū, no ka laʻana, ka maʻi ʻōpū mumū a i ʻole ka gastropathy.
- Ka maʻi ʻaʻai (ʻoi aku hoʻi i nā hihia koʻikoʻi).
- Ke piʻi nui nei ka nui o nā hormones thyroid (thyrotoxicosis).
- ʻO kekahi mau hoʻololi genetic.
- Ka hoʻohana ʻana i ka diuretic therapy no ka pohō o ka naʻau no ka manawa lōʻihi.
- Nā maʻi nele o ka Thiamine e like me ka HIV/AIDS.
- ʻO ka hāʻule ʻana o nā puʻupaʻa, no ka mea, ʻo ka mālama ʻana i ka dialysis lōʻihi e hōʻemi ana i ka hiki o ke kino ke omo i ka thiamine.
- ʻO ka nele i ke komo ʻana i nā hale lapaʻau a i ʻole ka meaʻai momona.
- ʻO ka luaʻi nui a me ka nausea i ka wā hāpai (hyperemesis gravidarum).
He aha nā kumu o ka "Wernicke-Korsakoff syndrome"?
ʻO ke kumu nui o kēia, ʻo ia ka nele o ka "Thiamine". ʻO kēia huaora koʻikoʻi ka mea e hoʻololi i ke kō a mākou e ʻai ai i ikehu. No laila, ke lawa ʻole ka "Thiamine", ʻaʻole i loaʻa i ko mākou lolo ka ikehu e pono ai e hana pono.
ʻO ke kumu nui o ka nele o ka thiamineʻO ka inu nui ʻana i ka waiʻona no ka manawa lōʻihi. Hoʻopilikia ka waiʻona i ke kino e omo i ka thiamine a mālama iā ia i loko o ke ake. Hoʻopilikia pū ka waiʻona i ka hoʻohana ʻana o ka wikamina B1 no nā hana koʻikoʻi ʻē aʻe.
Aia kekahi mau kumu ʻē aʻe:
- ʻAi kūpono ʻole: ʻAi ʻole i ka papaʻai kaulike.
- Nā maʻi ʻai: e like me ka anorexia a me ka bulimia.
- Nā maʻi maʻi mau.
- Nā ʻoki kino: ʻOi aku nā ʻoki kino e like me ke ʻoki bypass gastric no ka pohō kaumaha.
- ʻEha lolo traumatic: Akā, he mea kakaikahi kēia.
He aha nā hōʻailona o ka maʻi ʻo "Wernicke-Korsakoff syndrome"?
Hiki i kēia ke hōʻike ʻia ma nā ʻano hōʻailona like ʻole. ʻO kekahi o nā hōʻailona maʻamau i ʻike ʻia i nā hihia koʻikoʻi ʻo ia ka 'confabulation' . ʻO ia hoʻi, ke haku moʻolelo ʻana i loko o kou manaʻo e uhi i nā mea āu e hoʻomanaʻo ʻole ai. E noʻonoʻo, ʻaʻole hoʻomanaʻo kekahi i kahi mea a lākou i hana ai i nehinei, akā haʻi wahaheʻe lākou e uhi ai, akā ʻaʻole lākou e wahaheʻe no ka mea ua manaʻo lākou ua hana maoli ʻia. Manaʻoʻiʻo lākou i ka moʻolelo.
Hiki i ka poʻe me kēia maʻi ke manaʻo pinepine i ka huikau a i ʻole ka pioloke. ʻO kēia huikau e paʻakikī ai iā lākou ke ʻike he hewa kekahi mea me lākou a e ʻimi i ka lāʻau lapaʻau.
ʻO nā hōʻailona maʻamau o ka encephalopathy Wernicke:
- Ka nalowale o ke kaulike a i ʻole ka hiki ʻole ke kāohi i nā neʻe ʻana (ataxia).
- 'Hoʻohuihui'.
- Huikau, delirium.
- Ka paʻakikī o ka hele wāwae, ka hele wāwae paʻa ʻole.
- Hiamoe.
- Haʻahaʻa loa ka mahana o ke kino (hypothermia).
- Nā pilikia o ka puʻuwai: piʻi ka nui o ka puʻuwai (tachycardia) a i ʻole ke koko haʻahaʻa (hypotension).
- Ka nalowale ʻana o ka hoʻonohonoho ʻana o nā ʻiʻo (ataxia).
He mea maʻamau nō hoʻi nā pilikia o ka maka:
- Nā neʻe ʻana o nā maka maʻamau ʻole (nystagmus).
- ʻIke pālua.
- Ke kulou ʻana o ka lihilihi o luna (ptosis).
- Ka nāwaliwali a i ʻole ka hana ʻino o nā ʻiʻo maka (ophthalmoplegia).
Inā ʻaʻole mālama ʻia ka Wernicke encephalopathy, hiki iā ia ke holomua i ka Korsakoff syndrome, kahi maʻi hoʻomanaʻo lōʻihi. ʻO kāna mau hōʻailona:
- Ka nalowale piha ʻana o ka hoʻomanaʻo (ʻAmnesia) a i ʻole ka hiki ʻole ke hoʻomanaʻo i kekahi mea hou.
- Nā loli o ke ʻano: huhū, huhū wikiwiki.
- 'Hoʻohuihui'.
- Delirium a me ka disorientation.
- Luhi a palaualelo paha.
- ʻO nā hallucinations, ʻoiai i ka wā e haʻalele ai i ka waiʻona.
- ʻAʻole hiki ke noʻonoʻo pono.
- Ka hele wāwae paʻa ʻole.
ʻAʻole e hoʻomaikaʻi piha kekahi mau hōʻailona me ka mālama ʻia. I nā hihia koʻikoʻi, hiki ke nalowale ka ʻike (`coma`). Inā nalowale ʻoe a i ʻole kekahi mea kokoke iā ʻoe i ka ʻike, a inā he mau hōʻailona kou o ka `Wernicke-Korsakoff syndrome`, e ʻike koke i ke kauka a i ʻole e hele i kahi lumi pilikia.
Pehea e ʻike ʻia ai ka maʻi ʻo Wernicke-Korsakoff syndrome?
He mea nui ka ʻike mua ʻana i kēia maʻi `WKS` no ka mālama pono ʻana. Hoʻoponopono nā kauka iā ia ma ka hana ʻana i kahi hoʻokolokolo kino, nīnau e pili ana i kāu mau hōʻailona, a nīnau e pili ana i kou mōʻaukala ʻohana. Eia nō naʻe, hiki ke paʻakikī ke ʻike i ka wā e huikau ai kekahi a nalowale paha ka hoʻomanaʻo.
E nānā pono ke kauka i kēia mau mea:
- Aia kekahi mau pilikia hoʻohana waiʻona ('Alcohol use disorder')?
- Aia ka ʻai ʻole i ka meaʻai?
- Aia kekahi hemahema o ka thiamine?
He aha nā hoʻokolohua e kōkua i ka ʻike ʻana i ka maʻi Wernicke-Korsakoff?
E kauoha aku kāu kauka i nā hoʻāʻo koko e nānā i kou kō koko a me nā pae thiamine. Hiki iā lākou ke kauoha i kahi hoʻāʻo waiʻona koko e nānā i ka hoʻohana ʻana i ka waiʻona a me kahi hoʻāʻo hana ate e nānā i ka hana ate, no ka mea, he hōʻailona paha kēia i ka hōʻino ʻia o ke ake.
Hiki ke hana ʻia nā hoʻokolohua hou aʻe e nānā i nā kumu ʻē aʻe:
- ʻO ka hoʻāʻo kinoea koko arterial (ABG), e nānā ana i nā pae o ke kalapona ʻokikene a me ka oxygen i loko o ke koko.
- 'Helu koko piha' ('Helu koko piha - CBC').
- Ka nānā ʻana i ka toxicology.
Pono paha ʻoe e loaʻa nā hoʻokolohua kiʻi e like me kēia:
- ʻO ke kiʻi CT.
- ʻO ka MRI (MRI)
- ʻElectrocardiogram (Electrocardiogram - EKG)
Hiki ke ho'ōla ʻia ka maʻi Wernicke-Korsakoff? Pehea e mālama ʻia ai?
ʻO ka ʻoiaʻiʻo, ʻaʻole hiki ke ho'ōla loa ʻia. Eia nō naʻe, inā hoʻomaka mua ʻia ka lāʻau lapaʻau, hiki ke hoʻomaha ʻia nā hōʻailona a hiki ke hoʻohuli ʻia kekahi o lākou. ʻO ke ʻano kēia, hiki ke hoʻōki i ke kūlana "Wernicke encephalopathy" mai ka ʻino ʻana a i ka "Korsakoff syndrome".
I ka hapanui o nā hihia, hiki i ka lāʻau lapaʻau ke kaohi a hoʻomaikaʻi paha i nā hōʻailona e like me ka huikau, nā pilikia maka, a me ka nalowale o ke kaulike. E hoʻomohala kāu kauka i kahi hoʻolālā lapaʻau kūpono iā ʻoe.
Hana pinepine ʻia kēia mau mea ma ke ʻano he lāʻau lapaʻau:
- ʻO ka hāʻawi ʻana i ka wikamina B1 ma o nā pila a i ʻole nā inikini.
- Inā maloʻo ke kino, e hāʻawi i ka saline ma o nā "wai IV".
- Ka mālama ʻana i nā pilikia e pili ana i ka hoʻohana ʻana i ka waiʻona.
- Ke hāʻawi nei i ke kākoʻo meaʻai.
- E hoʻolako i nā lāʻau lapaʻau ʻē aʻe inā pono.
Pehea e hiki ai iā ʻoe ke hōʻemi i ka pilikia o ka hoʻomohala ʻana i kēia maʻi?
I ka hapanui o nā hihia, ʻo ka hoʻōki ʻana a i ʻole ka palena ʻana i ka inu ʻona ka mea nui loa hiki iā ʻoe ke hana e hōʻemi i kou pilikia o ka hoʻomohala ʻana i ka maʻi Wernicke-Korsakoff. Eia kekahi, ʻo ka loaʻa ʻana o ka meaʻai maikaʻi a, inā pono, ʻo ka lawe ʻana i nā mea hoʻohui thiamine ma ke ʻano o nā inikini a i ʻole nā pile e hiki ke kōkua i ka hōʻemi ʻana i kou pilikia, ʻoi aku hoʻi no ka poʻe i hoʻopili ʻia i ka waiʻona.
He aha ka wānana no kekahi kanaka me ka maʻi Wernicke-Korsakoff?
Inā loaʻa iā ʻoe a i ʻole kekahi mea kokoke iā ʻoe kēia maʻi, pili ka prognosis i ke koʻikoʻi o nā hōʻailona a me ka wikiwiki o ka ʻike ʻia ʻana a me ka mālama ʻia ʻana o ka maʻi. Hiki i ka mālama mua ke hoʻohuli i nā hōʻailona a pale i nā pilikia lōʻihi. Eia nō naʻe, inā ʻaʻole mālama ʻia, hiki iā ia ke alakaʻi i ke kīnā a me ka make.
I ka manawa hea ʻoe e ʻimi ai i ke aʻo lapaʻau no kēia maʻi?
Inā loaʻa iā ʻoe a i ʻole kekahi āu i ʻike ai nā hōʻailona o ka maʻi Wernicke-Korsakoff, e ʻimi koke i ke kōkua lapaʻau. Pono paha ʻoe e kāhea i kāu kauka a i ʻole e hele i ka lumi pilikia o ka haukapila kokoke loa no ka mālama ʻana i ka pilikia.
Pehea wau e mālama ai iaʻu iho?
ʻAʻole he hana maʻalahi ka loaʻa ʻana o kahi hōʻoia o ka maʻi Wernicke-Korsakoff. Pono paha ʻoe e hoʻokomo ʻia i ka haukapila a loaʻa ka lāʻau lapaʻau. ʻO ka mea nui loa, ʻo ia ka hahai ʻana i nā ʻōlelo aʻoaʻo a kāu kauka, e like me ka hoʻemi ʻana i kāu inu ʻona (a i ʻole ka hōʻoki loa ʻana) a me ka ʻai ʻana i ka meaʻai momona. E kākoʻo nui kēia mau mea i kou ho'ōla ʻana.
E hahai pono i nā ʻōlelo a kāu kauka e hoʻokele i nā pilikia a mālama i nā hōʻailona. E hana ʻo ia i kahi hoʻolālā mālama pilikino e kūpono iā ʻoe a kōkua iā ʻoe e hoʻi i kou olakino.
He maʻi hoʻomanaʻo kakaʻikahi akā koʻikoʻi ka maʻi Wernicke-Korsakoff. Pono ia i ka mālama wikiwiki e hōʻoluʻolu i nā hōʻailona a pale i nā pilikia. I ka holomua ʻana o ka maʻi, ʻike ʻia nā hōʻailona o ka ʻōnaehana nerve, e like me ka huikau nui a me ka disorientation. Hiki i kēia mau hōʻailona ke paʻakikī iā ʻoe a i ʻole kekahi mea kokoke iā ʻoe ke ʻike i kou kūlana. No laila, he mea nui e ʻike mua i ka maʻi. E paipai kāu kauka i kahi hoʻolālā lapaʻau i hoʻopilikino ʻia i kāu mau pono.
Nā mea nui e hoʻomanaʻo (Leka Lawe-Home)
ʻAe, eia nā mea nui e hoʻomanaʻo e pili ana i ka 'Wernicke-Korsakoff Syndrome' a mākou i kamaʻilio ai:
- He kūlana koʻikoʻi kēia e hoʻopilikia ai i ka lolo a me ka hoʻomanaʻo ma muli o ka nele o ka thiamine (vitamin B1).
- ʻO ke kumu nui o ka pilikia, ʻo ia ka hoʻohana nui ʻana i ka waiʻona.
- ʻO ke kahua mua ʻo Wernicke encephalopathy, a inā ʻaʻole mālama ʻia, hiki ke alakaʻi i kahi pilikia hoʻomanaʻo lōʻihi i kapa ʻia ʻo Korsakoff syndrome.
- ʻO ka huikau, ka paʻakikī i ka hele wāwae, nā pilikia ʻike, a me ka nalowale o ka hoʻomanaʻo paha nā hōʻailona nui.
- He mea nui ka ʻike wikiwiki ʻana a me ka mālama koke ʻana me ka thiamine.
- ʻOiai ʻaʻole hiki ke ho'ōla piha ʻia, hiki i ka mālama mua ʻana ke kaohi i nā hōʻailona a pale i ka hōʻino mau loa.
- Inā ʻoe a i ʻole kekahi āu i ʻike ai e hōʻike ana i kēia mau hōʻailona, e ʻimi koke i ke kōkua lapaʻau.
Manaʻolana wau he mea pono kēia ʻike iā ʻoe. E ola kino!
ʻO ka maʻi Wernicke-Korsakoff, ka hemahema o ka thiamine, ka wikamina B1, ka hoʻohana ʻana i ka waiʻona, ka hemahema o ka hoʻomanaʻo, nā maʻi lolo, nā maʻi neurological











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