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Puas muaj teeb meem nrog koj lub plawv lub aorta? Cia peb tham txog Aortopathy!

Puas muaj teeb meem nrog koj lub plawv lub aorta? Cia peb tham txog Aortopathy!

Koj puas tau xav txog seb cov hlab ntsha loj tshaj plaws thiab tseem ceeb tshaj plaws hauv peb lub cev yog dab tsi? Nws yog lub aorta, lossis aorta . Nws zoo li txoj kev loj hauv peb lub cev. Nws khiav ntawm lub plawv mus txog rau lub plab. Nws yog qhov uas nqa cov ntshav uas muaj oxygen thiab huv si uas lub plawv nqus mus rau tag nrho lub cev. Yog li, yog tias muaj qee yam tsis raug nrog lub aorta no, nws tuaj yeem cuam tshuam rau tag nrho lub cev. Ntawd yog pawg kab mob uas cuam tshuam rau lub aorta, uas peb hu ua Aortopathy .

Aortopathy yog dab tsi? Cia peb nkag siab yooj yim.

Hais yooj yim xwb, aortopathy yog ib pawg ntawm cov mob uas ua rau cov phab ntsa ntawm koj lub aorta tsis muaj zog lossis puas tsuaj. Tam sim no xav txog, koj lub plawv tso cov ntshav ncaj qha mus rau hauv lub aorta no txhua zaus nws dhia. Yog li, cov phab ntsa ntawm cov hlab ntsha no yuav tsum muaj zog heev kom tiv taus qhov kev nyuaj siab ntawd. Tab sis, yuav ua li cas yog tias cov phab ntsa no tsis muaj zog? Lawv tuaj yeem tawg lossis txiav. Qhov no txaus ntshai heev. Hom aortopathy uas koj muaj yuav cuam tshuam rau lub aorta sib txawv.

Cov hom aortopathy tseem ceeb yog dab tsi?

Muaj ntau hom kab mob aortopathy sib txawv. Cia peb tham txog qee hom tseem ceeb.

Mob plawv hauv plab (AAA)

Qhov no yog thaum phab ntsa ntawm koj lub aorta, uas khiav hla koj lub plab, ua rau tsis muaj zog thiab tawm zoo li lub npas. Peb kuj hu qhov no ua aneurysm . Qhov mob no feem ntau cuam tshuam rau cov neeg hnub nyoog tshaj 65 xyoo, cov neeg haus luam yeeb, lossis cov neeg uas muaj lwm yam kev pheej hmoo rau kab mob plawv. Qhov "(AAA)" no txaus ntshai vim tias nws tuaj yeem tawg tam sim ntawd thiab ua rau muaj kev hem thawj rau lub neej.

Kev Mob Aneurysm ntawm Lub Plawv Aortic (TAA)

Qhov no yog qhov qaug zog lossis nthuav dav ntawm qhov aorta uas khiav hla lub hauv siab. Tus mob '(TAA)' tsis tshua muaj ntau npaum li '(AAA)'. Txawm li cas los xij, nws yuav khiav hauv tsev neeg ntau dua, txhais tau tias nws tuaj yeem kis mus rau ntau tiam neeg. Ib yam li '(AAA)', qhov kev pheej hmoo tseem ceeb ntawm '(TAA)' yog tias nws yuav tawg.

Qhov mob txaus ntshai hu ua Aortic Dissection

Qhov no nyuaj me ntsis. Qhov tshwm sim ntawm no yog tias txheej sab hauv ntawm phab ntsa ntawm aorta rhuav tshem. Qhov no tshwm sim qhov twg phab ntsa ntawm aorta tsis muaj zog. Qee zaum, raws li tau hais ua ntej, nws tuaj yeem tshwm sim qhov twg muaj aneurysm. Txawm li cas los xij, nws kuj tuaj yeem tshwm sim yam tsis muaj aneurysm. Muaj ob hom tseem ceeb ntawm qhov no. Hom A dissection yog kev rhuav tshem hauv qhov ntawm aorta ze tshaj plaws rau lub plawv (piv txwv li, ua ntej aortic arch). Hom B dissection yog kev rhuav tshem tom qab aortic arch, hauv siab lossis plab. Qhov "(Aortic Dissection)" no yog ib qho mob uas hem lub neej uas xav tau kev lees paub thiab kev kho mob tam sim ntawd .

Cia peb kawm txog Familial Aortopathy?

Familial Aortopathy yog ib yam mob caj ces uas khiav hauv tsev neeg.Kab mob aortopathy hauv tsev neeg yog ib yam kab mob ntawm cov hlab ntsha loj uas cuam tshuam nrog keeb kwm tsev neeg muaj kab mob aortic. Cov neeg no muaj ib qho kev hloov pauv ntawm cov noob caj noob ces uas ua rau lawv muaj feem yuav mob aortic. Feem ntau, qhov kab mob aortopathy no cuam tshuam rau cov hlab ntsha loj hauv lub hauv siab, tshwj xeeb tshaj yog cov hauv paus aortic lossis ascending aorta.

Kuj muaj ob pawg tseem ceeb hauv qhov no:

Syndromic Aortopathy yog dab tsi?

Peb kuj hu qhov no tias '(Syndromic hereditary thoracic aortic disease)'. Hais yooj yim xwb, koj muaj ib qho genetic syndrome uas cuam tshuam rau koj lub aorta thiab ua rau muaj lwm yam kev hloov pauv hauv koj lub cev. Qee cov syndromes uas ua rau muaj kab mob aorta yog:

  • Kab mob Loeys-Dietz
  • 'Marfan syndrome'
  • 'Turner syndrome'
  • Kab mob Ehlers-Danlos hauv cov hlab ntsha

Cia peb kuj paub txog Non-syndromic Aortopathy

Qhov no hu ua "Kab mob aortic hauv lub plawv uas tsis yog ib yam kab mob uas muaj feem cuam tshuam." Hauv qhov no, koj tsis muaj ib qho mob caj ces tshwj xeeb, tab sis koj muaj ib qho kev hloov pauv ntawm cov noob caj ces uas ua rau koj muaj feem yuav mob aortic ntau ntxiv. Cov kws tshawb fawb tau txuas ntau dua 50 qhov kev hloov pauv ntawm cov noob caj ces rau qhov mob aortopathy no. Qee cov noob caj ces uas tau txuas nrog zoo heev yog:

  • `ACTA2` (Qhov no yog qhov feem ntau pom)
  • `FOXE3`
  • `LOX`
  • `MYH11`
  • `MYLK`

Nco ntsoov tias, yog tias muaj leej twg hauv koj tsev neeg tau muaj aneurysm lossis dissection ntawm aorta, tham nrog koj tus kws kho mob txog kev kuaj noob caj noob ces . Yog tias koj raug kuaj pom tias muaj kab mob aortic, koj yuav tsum tau kuaj noob caj noob ces kom pom tias lwm tus tswv cuab hauv koj tsev neeg kuj muaj kev pheej hmoo.

Bicuspid Aortopathy yog dab tsi?

Qhov no kuj hu ua '(Bicuspid valve-associated aortopathy)'. Qhov no txhais tau tias, nrog rau aortic stenosis, koj kuj muaj mob plawv txij thaum yug los hu ua Bicuspid Aortic Valve (BAV) . Qhov '(BAV)' no yog ib qho mob plawv txij thaum yug los, cuam tshuam kwv yees li ib ntawm 50 tus menyuam mos.

Tam sim no, koj lub aortic valve yog ib qho ntawm plaub "rooj vag" uas tswj cov ntshav ntws hauv koj lub plawv. Nws tswj cov ntshav ntws los ntawm sab laug ventricle, lub plawv lub chamber tseem ceeb, mus rau hauv aorta. Lub aortic valve noj qab haus huv muaj peb daim nplooj uas qhib thiab kaw los tswj cov ntshav ntws. Txawm li cas los xij, lub bicuspid aortic valve tsuas muaj ob daim nplooj xwb. Qhov no yuav tsis ua rau muaj teeb meem loj rau ib ntus, tab sis nws tuaj yeem ua rau muaj teeb meem dhau sijhawm.

Yog koj muaj mob bicuspid aortopathy, koj lub aortic valve muaj ob daim leaflets, thiab koj lub aorta dav dua li qub (dilated). Rau cov neeg uas muaj bicuspid aorta, qhov kev nthuav dav feem ntau tshwm sim hauv cov hauv paus aortic lossis ascending aorta. Cov no yog cov feem ntawm aorta ze tshaj plaws rau lub plawv.

Cov Teeb Meem ntawm Bicuspid Aortopathy

Ib qho aorta loj me ntsis yuav tsis yog teeb meem loj. Txawm li cas los xij, yog tias nws loj dhau, aneurysm tuaj yeem tshwm sim. Qhov aneurysm no muab kev nyuaj ntxiv rau ntawm phab ntsa ntawm aorta, uas tuaj yeem ua rau nws tawg lossis dissection. Cov neeg uas muaj bicuspid aortopathy muaj feem yuav muaj aortic dissection li cuaj npaug ntau dua li cov neeg uas tsis muaj mob.

Cov kab mob aortopathy no muaj ntau npaum li cas?

Nws txawv nyob ntawm hom kab mob. Aortic aneurysm (AAA) yog hom aortopathy uas feem ntau pom, thiab nws kuj yog hom aneurysm uas feem ntau pom. Tsuas yog hauv Tebchaws Meskas xwb, muaj li ntawm 200,000 tus neeg raug kuaj pom tias muaj AAA txhua xyoo. Thoob ntiaj teb, muaj li ntawm 47,000 tus neeg tuag txhua xyoo los ntawm txhua hom aortopathy.

Cov tsos mob ntawm Aortopathy yog dab tsi? Tsis txhob tsis quav ntsej txog cov no!

Feem ntau cov kab mob plawv tsis muaj tsos mob . Qhov ntawd yog qhov txaus ntshai tshaj plaws. Yog vim li cas nws thiaj li tseem ceeb kom mus kuaj mob tsis tu ncua yog tias koj muaj cov yam ntxwv uas ua rau muaj kev pheej hmoo.

Muaj qee cov tsos mob uas yuav tshwm sim thaum lub aneurysm yuav tawg. Cov cim ceeb toom uas yuav tshwm sim ua ntej nws tawg suav nrog:

  • Txawm tias noj me ntsis lawm los kuj tseem xav tias puv npo.
  • Mob nraub qaum, pob tw, qhov chaw mos, ceg, lossis plab tas li.
  • Hnov lub plawv dhia hauv thaj tsam plab.
  • Ua pa nyuaj.

Kev tawg ntawm cov hlab ntsha hauv lub plawv thiab kev tawg ntawm cov hlab ntsha hauv lub plawv yog qhov xwm txheej ceev uas ua rau tuag taus! Yog tias koj muaj cov tsos mob hauv qab no , hu rau 1990 tam sim ntawd kom tau txais lub tsheb thauj neeg mob, lossis mus rau chav kho mob ceev hauv tsev kho mob ze tshaj plaws:

  • Mob plab hnyav heev tam sim ntawd.
  • Mob sai sai, ntse, thiab mob heev hauv lub hauv siab lossis sab nraub qaum. Qhov no tuaj yeem zoo li nws raug dua los ntawm sab hauv, zoo li riam chob, lossis zoo li nws raug chob.
  • Tawv nqaij nplaum los yog hws ntau dhau.
  • Kev tsis meej pem.
  • Kiv taub hau los yog tsaus muag.
  • Lub plawv dhia nce ntxiv.
  • Xeev siab thiab ntuav.
  • Ua pa nyuaj.
  • Nyuaj siab hais lus.
  • Tsis pom kev.
  • Tsis muaj zog los yog loog ntawm ib sab ntawm lub cev.

Dab tsi yog cov ua rau mob aortopathy?

Muaj ntau yam ua rau muaj aortopathy. Ib txhia tshwm sim thaum yug los, thaum lwm tus tshwm sim tom qab lub neej.

  • Cov noob caj noob ces: Raws li tau hais ua ntej lawm, cov tsos mob ntawm cov noob caj noob ces thiab cov noob caj noob ces sib txawv tuaj yeem ua rau muaj kab mob aortic. Feem ntau cov aortopathy hauv tsev neeg tau txais los ntawm kev yug los ntawm autosomal dominant. Qhov no txhais tau tias yog tias ib tug niam txiv muaj cov noob caj noob ces, lawv tus menyuam muaj 50% feem pua ​​​​​​ntawm kev tau txais nws.
  • Kab mob plawv yug los: Cov no yog txuam nrog aortopathy. Qhov no tsis tau txhais hais tias aortopathy yog tshwm sim los ntawm kab mob plawv yug los, tab sis ob qho no feem ntau pom ua ke. Piv txwv li: `Bicuspid aortic valve`, `Coarctation of the aorta`, `Pulmonary atresia with ventricular septal defect (VSD)`, `Tetralogy of Fallot`, `d-Transposition of the great arteries`, `Truncus arteriosus`. Aortopathy kuj tseem tuaj yeem tshwm sim tom qab phais rau qee yam kab mob plawv yug los. Piv txwv li: `Arterial switch (ASO) operation`, `Atrial baffle (Mustard/Senning) operation`, `The staged Norwood, Glenn thiab Fontan surgeries`.
  • Kab mob Atherosclerosis: Qhov no yog qhov uas cov rog sib sau ua ke (plaque) hauv cov hlab ntsha, ua rau lawv nqaim zuj zus. Kab mob Atherosclerosis ntawm lub aorta yog qhov ua rau muaj kab mob aortopathy tom qab hauv lub neej.

Leej twg muaj feem yuav mob aortopathy ntau dua?

Muaj ntau yam ua rau muaj kev pheej hmoo ntawm aortopathy:

  • Haus luam yeeb thiab siv luam yeeb: Qhov no yog ib qho tseem ceeb uas ua rau muaj kev pheej hmoo . Feem ntau ntawm cov hlab ntsha aneurysm tshwm sim rau cov neeg uas haus luam yeeb lossis tau haus luam yeeb yav dhau los.
  • Ntshav Siab (Tshuaj Ntshav Siab): Qhov mob no tuaj yeem ua rau cov phab ntsa ntawm cov hlab ntsha qaug zog dhau sijhawm.
  • Kev laus: Qhov kev pheej hmoo ntawm kev tsim aneurysm nce ntxiv tom qab hnub nyoog 65 xyoos.
  • Keeb kwm tsev neeg: Yog tias ib tug tswv cuab ntawm tsev neeg tau muaj aneurysm lossis dissection, koj muaj kev pheej hmoo ntau dua.
  • Cov roj cholesterol ntau lossis triglycerides ntau: Cov roj (lipids) ntau ntxiv hauv cov ntshav ua rau muaj kev pheej hmoo ntawm cov rog hauv cov hlab ntsha.
  • Cov kab mob autoimmune: Cov kab mob autoimmune xws li 'Giant cell arteritis' thiab 'Takayasu arteritis' tuaj yeem ua rau o ntawm phab ntsa ntawm cov hlab ntsha loj, ua rau lawv qaug zog.
  • Kev kis kab mob: Tsis tshua muaj, kev kis kab mob xws li mob syphilis, lossis kev kis kab mob ntawm phab ntsa ntawm cov hlab ntsha loj, tuaj yeem ua rau nws qaug zog.

Yuav kuaj mob aortopathy li cas ?

Feem ntau cov hlab ntsha aneurysm thiab cov hlab ntsha tawg tsis muaj tsos mob lossis cov cim ceeb toom, yog li ntawd tej zaum yuav tsis pom lawv kom txog thaum muaj teeb meem loj tshwm sim. Txawm li cas los xij, yog tias koj muaj cov yam txaus ntshai, koj tus kws kho mob yuav kuaj koj lub aorta kom paub txog cov cim ntawm tus kab mob.

Cov txheej txheem siv los kuaj mob aortopathy yog:

  • Kev kuaj lub cev: Koj tus kws kho mob yuav kuaj txhua yam ntawm koj txoj kev noj qab haus huv. Nws kuj tseem yuav soj ntsuam koj cov yam uas ua rau muaj kab mob plawv. Qhov no yuav suav nrog kev nug txog koj keeb kwm kev kho mob, cov yam ntxwv ntawm kev ua neej (xws li kev haus luam yeeb), thiab keeb kwm tsev neeg.
  • Kev kuaj noob caj noob ces: Koj tus kws kho mob yuav pom zoo kom kuaj noob caj noob ces. Qhov no yuav qhia seb koj puas muaj kev hloov pauv noob caj noob ces uas cuam tshuam nrog kab mob ntawm cov hlab ntsha hauv lub plawv.
  • Kev kuaj duab: Koj tus kws kho mob yuav xaj cov kev kuaj no los xyuas qhov loj thiab kev noj qab haus huv ntawm koj lub aorta. Cov kev kuaj no ntsuas txoj kab uas hla ntawm koj lub aorta thiab saib seb nws puas dav dua li qub.

Cov kev kuaj twg siv los kuaj mob Aortopathy?

  • Kev kuaj mob computer (CT scan)
  • Kev siv tshuab magnetic resonance imaging (MRI)
  • Kev kuaj lub plawv los ntawm lub qhov ntswg (Transthoracic echocardiogram - TTE)
  • Kev kuaj plawv los ntawm txoj hlab pas (transesophageal echocardiogram - TEE) (kev ntsuas plawv los ntawm txoj hlab pas)
  • Kev kuaj mob plab ultrasound (kev kuaj mob plab ultrasound)

Txhua qhov kev kuaj mob muaj nws cov txiaj ntsig thiab qhov tsis zoo. Koj tus kws kho mob yuav piav qhia seb koj xav tau qhov kev kuaj mob twg thiab yog vim li cas. Koj tus kws kho mob kuj tseem yuav siv ib lossis ntau qhov kev kuaj mob no los saib xyuas koj lub aorta dhau sijhawm. Tej zaum koj yuav tsum tau thaij cov duab no tsis tu ncua (piv txwv li, ib xyoos ib zaug). Koj yuav tsum tau kuaj mob no ntau npaum li cas nyob ntawm koj cov yam ntxwv uas ua rau muaj kev pheej hmoo thiab kev noj qab haus huv tam sim no ntawm koj lub aorta.

Cov kev kho mob rau Aortopathy yog dab tsi?

Kev kho mob nyob ntawm koj tus mob tshwj xeeb thiab koj qhov kev pheej hmoo ntawm cov teeb meem. Koj tus kws kho mob yuav kho koj txoj kev kho mob kom haum rau koj tus mob thiab cov kev xav tau. Cov kev xaiv kho mob suav nrog kev hloov pauv hauv lub neej, tshuaj, kev kho mob, thiab phais.

Cia peb pib nrog kev hloov pauv hauv lub neej!

Kev hloov pauv hauv lub neej yuav pab qeeb qeeb qee yam kab mob aortic thiab txo qhov kev pheej hmoo ntawm aneurysm tawg. Yog tias koj muaj kab mob aortic, nws yog ib qho tseem ceeb uas yuav tsum ua cov hauv qab no:

  • Tsis txhob haus dej cawv.
  • Tsis txhob haus luam yeeb thiab txhua yam khoom haus luam yeeb.
  • Noj zaub mov kom lub plawv noj qab nyob zoo.
  • Ua si nawv tsis tu ncua (raws li koj tus kws kho mob hais).
  • Tswj koj qhov hnyav kom noj qab nyob zoo.
  • Tswj cov yam uas ua rau muaj kab mob plawv xws li ntshav siab thiab roj cholesterol ntau.

Yog tias tsim nyog, kuj muaj cov tshuaj zoo li no.

Koj tus kws kho mob yuav sau ntawv kom noj tshuaj los pab txo koj cov ntshav siab. Cov tshuaj ntshav siab txo cov ntshav siab rau koj cov phab ntsa ntawm cov hlab ntsha. Qhov no tuaj yeem txo qhov kev pheej hmoo ntawm kev tawg lossis kev txiav ntawm cov hlab ntsha loj. Cov hom tshuaj uas koj tuaj yeem noj suav nrog:

  • Cov tshuaj ACE inhibitors (angiotensin converting enzyme)
  • Cov tshuaj Angiotensin receptor blockers (ARBs)
  • Cov tshuaj beta-blockers
  • Cov tshuaj calcium channel blockers
  • Cov tshuaj diuretics (cov tshuaj uas ua rau koj tso zis ntau dua)

Kev phais thiab lwm yam kev kho mob

Muaj ib txhia neeg xav tau kev kho mob lossis phais mob rau cov kab mob aortopathy. Cov no suav nrog:

  • Kev phais mob aneurysm (kev phais qhib ib txwm muaj)
  • Kev phais hloov cov hauv paus aorta
  • Kho cov hlab ntsha hauv lub hlwb (EVAR) - Qhov no yog kev kho mob uas siv ib lub raj ntxig los ntawm ib qho kev phais me me.
  • Kho cov hlab ntsha hauv lub qhov ntswg (TEVAR) - Qhov no kuj yog kev kho mob zoo sib xws rau cov hlab ntsha hauv lub qhov ntswg.

Peb ua tau dab tsi los txo qhov kev pheej hmoo ntawm aortopathy?

Koj tuaj yeem txo koj txoj kev pheej hmoo ntawm kev mob aortopathy los ntawm kev ua neej noj qab haus huv rau lub plawv. Nov yog qee cov lus qhia:

  • Tsis txhob haus tshuaj yeeb: Luam yeeb, tshuaj yeeb, thiab cawv tsis zoo rau koj lub plawv. Qhov tseeb, lawv tuaj yeem ua rau koj lub plawv thiab cov hlab ntsha puas tsuaj. Tsum haus luam yeeb thiab siv tshuaj yeeb tag nrho. Thaum nws los txog rau cawv, paub meej tias 'dej haus' yog dab tsi thiab txwv qhov ntau. Cov kws kho mob pom zoo tias cov poj niam tsis txhob haus ntau tshaj ib 'dej haus' ib hnub thiab cov txiv neej tsis txhob haus ntau tshaj ob 'dej haus' ib hnub.
  • Noj zaub mov zoo rau lub plawv: Qhov no suav nrog kev noj cov zaub mov uas muaj roj saturated tsawg, trans fat, sodium (ntsev), thiab qab zib. Txo cov carbohydrates refined (xws li mov ci dawb) thiab noj ntau cov nplej tag nrho (xws li mov ci tag nrho, mov xim av). Tsis tas li ntawd, yuav tsum paub txog kev noj haus cuam tshuam li cas rau koj cov roj cholesterol.
  • Kev Ua Si: Tsis muaj ib txoj kev uas haum rau txhua tus neeg. Ua yam koj nyiam. Tsis tas li ntawd, ua raws li koj tus kws kho mob cov lus qhia txog yam kev ua si twg uas muaj kev nyab xeeb rau koj. Feem ntau cov kws kho mob pom zoo kom ua 150 feeb ntawm kev ua si nruab nrab hauv ib lub lim tiam. Qhov no tuaj yeem suav nrog kev taug kev sai, caij tsheb kauj vab, lossis ua luam dej.
  • Tswj kev ntxhov siab: Nws tsis yooj yim li nws suab. Tab sis nws yog ib qho tseem ceeb uas yuav tsum sim kawm cov txoj hauv kev tshiab los pab koj daws kev ntxhov siab hauv koj lub neej txhua hnub. Tsis tas li ntawd, tham nrog koj tsev neeg thiab cov phooj ywg txog cov txheej txheem uas ua haujlwm rau lawv.

Yuav ua li cas rau ib tus neeg uas muaj Aortopathy? (Outlook)

Tus neeg zoo tshaj plaws los nug txog koj lub neej yav tom ntej yog koj tus kws kho mob. Nws yuav xav txog ntau yam, piv txwv li:

  • Koj tus mob tshwj xeeb.
  • Tus nqi ntawm kev nce qib ntawm koj tus kab mob.
  • Koj lub hnub nyoog thiab poj niam txiv neej.
  • Koj cov yam ntxwv uas ua rau muaj kab mob plawv.
  • Koj tsev neeg keeb kwm kev kho mob.
  • Koj cov keeb kwm kho mob tag nrho.

Tham nrog koj tus kws kho mob txog yam uas yuav tshwm sim rau yav tom ntej.

Yog tias kuv muaj Aortopathy, kuv yuav tsum saib xyuas kuv tus kheej li cas?

Koj tus kws kho mob yuav muab cov lus qhia rau koj txog kev saib xyuas koj tus kheej. Ua raws li cov lus qhia ntawd kom meej, thiab nug koj tus kws kho mob yog tias koj muaj lus nug dab tsi. Koj yuav tsum ua cov hauv qab no:

  • Tsis txhob ua si nawv hnyav lossis ua kis las uas kov cov khoom sib chwv.
  • Txwv lossis tsum tsis txhob haus cawv kiag li.
  • Hloov koj cov zaub mov noj.
  • Tsum haus luam yeeb los yog siv cov khoom luam yeeb.
  • Noj koj cov tshuaj raws li tau qhia.

Cev Xeeb Tub thiab Aortopathy

Kev cev xeeb tub tuaj yeem ua rau muaj kev phom sij yog tias koj muaj kab mob plawv. Tham nrog koj tus kws kho mob ua ntej koj npaj yuav cev xeeb tub kom paub tseeb tias nws muaj kev nyab xeeb rau koj. Tej zaum koj yuav xav tau kev saib xyuas tshwj xeeb thaum cev xeeb tub (xws li kev kuaj duab ntau zaus) kom txo koj qhov kev pheej hmoo ntawm cov teeb meem. Tsis txhob siv cov tshuaj uas tsis muaj kev nyab xeeb thaum cev xeeb tub. Koj tus kws kho mob yuav tsum hloov koj cov tshuaj.

Kuv yuav tsum mus ntsib kws kho mob thaum twg?

Mus ntsib koj tus kws kho mob kom tau txais kev kuaj mob txhua xyoo, thiab mus rau txhua qhov kev teem caij rov qab. Koj tus kws kho mob yuav qhia rau koj tias koj yuav tsum tuaj kuaj mob ntau zaus npaum li cas.

Yog tias koj tau kuaj pom tias muaj kab mob plawv txij thaum yug los thaum koj tseem yog menyuam yaus, tej zaum koj yuav muaj ib tug kws kho mob plawv menyuam yaus uas saib xyuas koj tus mob. Tab sis, tom qab koj muaj 18 xyoo, tej zaum koj yuav tsis tau pom ib tug kws tshwj xeeb tshiab. Kev tshawb fawb qhia tau hais tias ntau tus neeg tsis meej pem thaum lawv hloov ntawm kev saib xyuas menyuam yaus mus rau kev saib xyuas neeg laus. Yog tias koj tau kho mob plawv txij thaum yug los thaum koj tseem yog menyuam yaus, nws yog ib qho tseem ceeb uas yuav tsum txuas ntxiv ua haujlwm nrog ib tug kws kho mob plawv thaum koj laus. Qhov no muaj tseeb txawm tias koj tsis hnov ​​​​​​muaj teeb meem dab tsi los xij. Koj tus kws kho mob plawv yuav qhia koj txog koj qhov kev pheej hmoo rau aortopathy thiab lwm yam mob thaum koj laus zuj zus.

Thaum kawg, tej yam tseem ceeb tshaj plaws uas yuav tsum nco ntsoov (Cov Lus Coj Mus Tsev)

Kab mob plawv Aortopathy yog ib yam mob hnyav uas yuav ua rau koj tuag taus yog tias tsis paub thiab kho. Yog tias ib tug neeg hauv koj tsev neeg tau muaj kab mob aneurysm lossis kev txiav ntawm lub aorta, tham nrog koj tus kws kho mob txog koj qhov kev pheej hmoo. Qee tus neeg muaj kev pheej hmoo siab dua vim yog cov mob caj ces, kab mob plawv txij thaum yug los, lossis cov yam ntxwv ntawm kev ua neej xws li kev haus luam yeeb. Kev ua neej noj qab haus huv rau lub plawv tuaj yeem txo koj qhov kev pheej hmoo ntawm aortopathy thiab ua kom koj lub cev muaj zog.Saib xyuas koj lub siab, vim nws yog lub plawv dhia ntawm koj lub neej!

👩🏽‍⚕️ Cov Lus Nug Ntxiv (FAQs)

💬 Aortopathy puas yog kab mob plawv?

Tsis yog ntawm lub plawv, qhov no yog ib qho kab mob ntawm 'cov hlab ntsha loj tshaj plaws' uas los ntawm lub plawv. Lub npe no yog muab rau txhua yam kab mob uas tshwm sim hauv cov hlab ntsha loj thiab loj tshaj plaws (Aorta) uas nqa cov ntshav los ntawm peb lub plawv mus rau tag nrho lub cev. Feem ntau, qhov tshwm sim yog tias cov phab ntsa ntawm cov hlab ntsha no dhau los ua nyias thiab tsis muaj zog.

💬 Yuav ua li cas thaum cov leeg ntshav no qaug zog?

Thaum qhov no qaug zog lawm, cov hlab ntsha yuav tsis tuaj yeem tiv taus qhov siab ntawm cov ntshav uas lub plawv tso tawm, thiab cov hlab ntsha yuav pib loj zoo li lub pob (Aortic aneurysm). Yog tias nws tseem loj hlob zoo li no, cov hlab ntsha yuav tawg tam sim ntawd yam tsis muaj lus ceeb toom ua ntej (Aortic dissection / Rupture). Tom qab ntawd tus neeg mob yuav tuag hauv ob peb feeb.

💬 Koj puas nrhiav tau qhov no ua ntej nws tawg?

Feem ntau, tus neeg mob tsis hnov ​​​​​​mob lossis tsis xis nyob los ntawm qhov kev loj hlob ntawm cov hlab ntsha no (ib yam kab mob ntsiag to). Vim tias qhov no feem ntau yog los ntawm noob caj noob ces (genetic - zoo li Marfan syndrome), yog tias ib tug neeg hauv tsev neeg muaj lub aorta tawg, nws yog ib qho tseem ceeb uas lwm tus tau txais Echocardiogram lossis CT scan los xyuas qhov no thiab noj qhov kev phais lossis tshuaj ntshav siab.


` Aortopathy, Aorta, Kab Mob Plawv, Aneurysm, Aortic Dissection, Cov Kab Mob Genetic, Mob Hauv Siab, Ntshav Siab, Haus Luam Yeeb, Kev Noj Qab Haus Huv Plawv

Frequently Asked Questions (FAQ)

Syndromic Aortopathy yog dab tsi?

Peb kuj hu qhov no tias '(Syndromic hereditary thoracic aortic disease)'. Hais yooj yim xwb, koj muaj ib qho genetic syndrome uas cuam tshuam rau koj lub aorta thiab ua rau muaj lwm yam kev hloov pauv hauv koj lub cev. Qee cov syndromes uas ua rau muaj kab mob aorta yog:

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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Tsis muaj lus teb tau muab tso tawm. Ntxiv koj cov lus tawm ntawm no thawj zaug.

Ntxiv koj cov lus

Thov xam: 1 + 9 =
Puas muaj teeb meem nrog koj lub plawv lub aorta? Cia peb tham txog Aortopathy!

Puas muaj teeb meem nrog koj lub plawv lub aorta? Cia peb tham txog Aortopathy!

Koj puas tau xav txog seb cov hlab ntsha loj tshaj plaws thiab tseem ceeb tshaj plaws hauv peb lub cev yog dab tsi? Nws yog lub aorta, lossis aorta . Nws zoo li txoj kev loj hauv peb lub cev. Nws khiav ntawm lub plawv mus txog rau lub plab. Nws yog qhov uas nqa cov ntshav uas muaj oxygen thiab huv si uas lub plawv nqus mus rau tag nrho lub cev. Yog li, yog tias muaj qee yam tsis raug nrog lub aorta no, nws tuaj yeem cuam tshuam rau tag nrho lub cev. Ntawd yog pawg kab mob uas cuam tshuam rau lub aorta, uas peb hu ua Aortopathy .

Aortopathy yog dab tsi? Cia peb nkag siab yooj yim.

Hais yooj yim xwb, aortopathy yog ib pawg ntawm cov mob uas ua rau cov phab ntsa ntawm koj lub aorta tsis muaj zog lossis puas tsuaj. Tam sim no xav txog, koj lub plawv tso cov ntshav ncaj qha mus rau hauv lub aorta no txhua zaus nws dhia. Yog li, cov phab ntsa ntawm cov hlab ntsha no yuav tsum muaj zog heev kom tiv taus qhov kev nyuaj siab ntawd. Tab sis, yuav ua li cas yog tias cov phab ntsa no tsis muaj zog? Lawv tuaj yeem tawg lossis txiav. Qhov no txaus ntshai heev. Hom aortopathy uas koj muaj yuav cuam tshuam rau lub aorta sib txawv.

Cov hom aortopathy tseem ceeb yog dab tsi?

Muaj ntau hom kab mob aortopathy sib txawv. Cia peb tham txog qee hom tseem ceeb.

Mob plawv hauv plab (AAA)

Qhov no yog thaum phab ntsa ntawm koj lub aorta, uas khiav hla koj lub plab, ua rau tsis muaj zog thiab tawm zoo li lub npas. Peb kuj hu qhov no ua aneurysm . Qhov mob no feem ntau cuam tshuam rau cov neeg hnub nyoog tshaj 65 xyoo, cov neeg haus luam yeeb, lossis cov neeg uas muaj lwm yam kev pheej hmoo rau kab mob plawv. Qhov "(AAA)" no txaus ntshai vim tias nws tuaj yeem tawg tam sim ntawd thiab ua rau muaj kev hem thawj rau lub neej.

Kev Mob Aneurysm ntawm Lub Plawv Aortic (TAA)

Qhov no yog qhov qaug zog lossis nthuav dav ntawm qhov aorta uas khiav hla lub hauv siab. Tus mob '(TAA)' tsis tshua muaj ntau npaum li '(AAA)'. Txawm li cas los xij, nws yuav khiav hauv tsev neeg ntau dua, txhais tau tias nws tuaj yeem kis mus rau ntau tiam neeg. Ib yam li '(AAA)', qhov kev pheej hmoo tseem ceeb ntawm '(TAA)' yog tias nws yuav tawg.

Qhov mob txaus ntshai hu ua Aortic Dissection

Qhov no nyuaj me ntsis. Qhov tshwm sim ntawm no yog tias txheej sab hauv ntawm phab ntsa ntawm aorta rhuav tshem. Qhov no tshwm sim qhov twg phab ntsa ntawm aorta tsis muaj zog. Qee zaum, raws li tau hais ua ntej, nws tuaj yeem tshwm sim qhov twg muaj aneurysm. Txawm li cas los xij, nws kuj tuaj yeem tshwm sim yam tsis muaj aneurysm. Muaj ob hom tseem ceeb ntawm qhov no. Hom A dissection yog kev rhuav tshem hauv qhov ntawm aorta ze tshaj plaws rau lub plawv (piv txwv li, ua ntej aortic arch). Hom B dissection yog kev rhuav tshem tom qab aortic arch, hauv siab lossis plab. Qhov "(Aortic Dissection)" no yog ib qho mob uas hem lub neej uas xav tau kev lees paub thiab kev kho mob tam sim ntawd .

Cia peb kawm txog Familial Aortopathy?

Familial Aortopathy yog ib yam mob caj ces uas khiav hauv tsev neeg.Kab mob aortopathy hauv tsev neeg yog ib yam kab mob ntawm cov hlab ntsha loj uas cuam tshuam nrog keeb kwm tsev neeg muaj kab mob aortic. Cov neeg no muaj ib qho kev hloov pauv ntawm cov noob caj noob ces uas ua rau lawv muaj feem yuav mob aortic. Feem ntau, qhov kab mob aortopathy no cuam tshuam rau cov hlab ntsha loj hauv lub hauv siab, tshwj xeeb tshaj yog cov hauv paus aortic lossis ascending aorta.

Kuj muaj ob pawg tseem ceeb hauv qhov no:

Syndromic Aortopathy yog dab tsi?

Peb kuj hu qhov no tias '(Syndromic hereditary thoracic aortic disease)'. Hais yooj yim xwb, koj muaj ib qho genetic syndrome uas cuam tshuam rau koj lub aorta thiab ua rau muaj lwm yam kev hloov pauv hauv koj lub cev. Qee cov syndromes uas ua rau muaj kab mob aorta yog:

  • Kab mob Loeys-Dietz
  • 'Marfan syndrome'
  • 'Turner syndrome'
  • Kab mob Ehlers-Danlos hauv cov hlab ntsha

Cia peb kuj paub txog Non-syndromic Aortopathy

Qhov no hu ua "Kab mob aortic hauv lub plawv uas tsis yog ib yam kab mob uas muaj feem cuam tshuam." Hauv qhov no, koj tsis muaj ib qho mob caj ces tshwj xeeb, tab sis koj muaj ib qho kev hloov pauv ntawm cov noob caj ces uas ua rau koj muaj feem yuav mob aortic ntau ntxiv. Cov kws tshawb fawb tau txuas ntau dua 50 qhov kev hloov pauv ntawm cov noob caj ces rau qhov mob aortopathy no. Qee cov noob caj ces uas tau txuas nrog zoo heev yog:

  • `ACTA2` (Qhov no yog qhov feem ntau pom)
  • `FOXE3`
  • `LOX`
  • `MYH11`
  • `MYLK`

Nco ntsoov tias, yog tias muaj leej twg hauv koj tsev neeg tau muaj aneurysm lossis dissection ntawm aorta, tham nrog koj tus kws kho mob txog kev kuaj noob caj noob ces . Yog tias koj raug kuaj pom tias muaj kab mob aortic, koj yuav tsum tau kuaj noob caj noob ces kom pom tias lwm tus tswv cuab hauv koj tsev neeg kuj muaj kev pheej hmoo.

Bicuspid Aortopathy yog dab tsi?

Qhov no kuj hu ua '(Bicuspid valve-associated aortopathy)'. Qhov no txhais tau tias, nrog rau aortic stenosis, koj kuj muaj mob plawv txij thaum yug los hu ua Bicuspid Aortic Valve (BAV) . Qhov '(BAV)' no yog ib qho mob plawv txij thaum yug los, cuam tshuam kwv yees li ib ntawm 50 tus menyuam mos.

Tam sim no, koj lub aortic valve yog ib qho ntawm plaub "rooj vag" uas tswj cov ntshav ntws hauv koj lub plawv. Nws tswj cov ntshav ntws los ntawm sab laug ventricle, lub plawv lub chamber tseem ceeb, mus rau hauv aorta. Lub aortic valve noj qab haus huv muaj peb daim nplooj uas qhib thiab kaw los tswj cov ntshav ntws. Txawm li cas los xij, lub bicuspid aortic valve tsuas muaj ob daim nplooj xwb. Qhov no yuav tsis ua rau muaj teeb meem loj rau ib ntus, tab sis nws tuaj yeem ua rau muaj teeb meem dhau sijhawm.

Yog koj muaj mob bicuspid aortopathy, koj lub aortic valve muaj ob daim leaflets, thiab koj lub aorta dav dua li qub (dilated). Rau cov neeg uas muaj bicuspid aorta, qhov kev nthuav dav feem ntau tshwm sim hauv cov hauv paus aortic lossis ascending aorta. Cov no yog cov feem ntawm aorta ze tshaj plaws rau lub plawv.

Cov Teeb Meem ntawm Bicuspid Aortopathy

Ib qho aorta loj me ntsis yuav tsis yog teeb meem loj. Txawm li cas los xij, yog tias nws loj dhau, aneurysm tuaj yeem tshwm sim. Qhov aneurysm no muab kev nyuaj ntxiv rau ntawm phab ntsa ntawm aorta, uas tuaj yeem ua rau nws tawg lossis dissection. Cov neeg uas muaj bicuspid aortopathy muaj feem yuav muaj aortic dissection li cuaj npaug ntau dua li cov neeg uas tsis muaj mob.

Cov kab mob aortopathy no muaj ntau npaum li cas?

Nws txawv nyob ntawm hom kab mob. Aortic aneurysm (AAA) yog hom aortopathy uas feem ntau pom, thiab nws kuj yog hom aneurysm uas feem ntau pom. Tsuas yog hauv Tebchaws Meskas xwb, muaj li ntawm 200,000 tus neeg raug kuaj pom tias muaj AAA txhua xyoo. Thoob ntiaj teb, muaj li ntawm 47,000 tus neeg tuag txhua xyoo los ntawm txhua hom aortopathy.

Cov tsos mob ntawm Aortopathy yog dab tsi? Tsis txhob tsis quav ntsej txog cov no!

Feem ntau cov kab mob plawv tsis muaj tsos mob . Qhov ntawd yog qhov txaus ntshai tshaj plaws. Yog vim li cas nws thiaj li tseem ceeb kom mus kuaj mob tsis tu ncua yog tias koj muaj cov yam ntxwv uas ua rau muaj kev pheej hmoo.

Muaj qee cov tsos mob uas yuav tshwm sim thaum lub aneurysm yuav tawg. Cov cim ceeb toom uas yuav tshwm sim ua ntej nws tawg suav nrog:

  • Txawm tias noj me ntsis lawm los kuj tseem xav tias puv npo.
  • Mob nraub qaum, pob tw, qhov chaw mos, ceg, lossis plab tas li.
  • Hnov lub plawv dhia hauv thaj tsam plab.
  • Ua pa nyuaj.

Kev tawg ntawm cov hlab ntsha hauv lub plawv thiab kev tawg ntawm cov hlab ntsha hauv lub plawv yog qhov xwm txheej ceev uas ua rau tuag taus! Yog tias koj muaj cov tsos mob hauv qab no , hu rau 1990 tam sim ntawd kom tau txais lub tsheb thauj neeg mob, lossis mus rau chav kho mob ceev hauv tsev kho mob ze tshaj plaws:

  • Mob plab hnyav heev tam sim ntawd.
  • Mob sai sai, ntse, thiab mob heev hauv lub hauv siab lossis sab nraub qaum. Qhov no tuaj yeem zoo li nws raug dua los ntawm sab hauv, zoo li riam chob, lossis zoo li nws raug chob.
  • Tawv nqaij nplaum los yog hws ntau dhau.
  • Kev tsis meej pem.
  • Kiv taub hau los yog tsaus muag.
  • Lub plawv dhia nce ntxiv.
  • Xeev siab thiab ntuav.
  • Ua pa nyuaj.
  • Nyuaj siab hais lus.
  • Tsis pom kev.
  • Tsis muaj zog los yog loog ntawm ib sab ntawm lub cev.

Dab tsi yog cov ua rau mob aortopathy?

Muaj ntau yam ua rau muaj aortopathy. Ib txhia tshwm sim thaum yug los, thaum lwm tus tshwm sim tom qab lub neej.

  • Cov noob caj noob ces: Raws li tau hais ua ntej lawm, cov tsos mob ntawm cov noob caj noob ces thiab cov noob caj noob ces sib txawv tuaj yeem ua rau muaj kab mob aortic. Feem ntau cov aortopathy hauv tsev neeg tau txais los ntawm kev yug los ntawm autosomal dominant. Qhov no txhais tau tias yog tias ib tug niam txiv muaj cov noob caj noob ces, lawv tus menyuam muaj 50% feem pua ​​​​​​ntawm kev tau txais nws.
  • Kab mob plawv yug los: Cov no yog txuam nrog aortopathy. Qhov no tsis tau txhais hais tias aortopathy yog tshwm sim los ntawm kab mob plawv yug los, tab sis ob qho no feem ntau pom ua ke. Piv txwv li: `Bicuspid aortic valve`, `Coarctation of the aorta`, `Pulmonary atresia with ventricular septal defect (VSD)`, `Tetralogy of Fallot`, `d-Transposition of the great arteries`, `Truncus arteriosus`. Aortopathy kuj tseem tuaj yeem tshwm sim tom qab phais rau qee yam kab mob plawv yug los. Piv txwv li: `Arterial switch (ASO) operation`, `Atrial baffle (Mustard/Senning) operation`, `The staged Norwood, Glenn thiab Fontan surgeries`.
  • Kab mob Atherosclerosis: Qhov no yog qhov uas cov rog sib sau ua ke (plaque) hauv cov hlab ntsha, ua rau lawv nqaim zuj zus. Kab mob Atherosclerosis ntawm lub aorta yog qhov ua rau muaj kab mob aortopathy tom qab hauv lub neej.

Leej twg muaj feem yuav mob aortopathy ntau dua?

Muaj ntau yam ua rau muaj kev pheej hmoo ntawm aortopathy:

  • Haus luam yeeb thiab siv luam yeeb: Qhov no yog ib qho tseem ceeb uas ua rau muaj kev pheej hmoo . Feem ntau ntawm cov hlab ntsha aneurysm tshwm sim rau cov neeg uas haus luam yeeb lossis tau haus luam yeeb yav dhau los.
  • Ntshav Siab (Tshuaj Ntshav Siab): Qhov mob no tuaj yeem ua rau cov phab ntsa ntawm cov hlab ntsha qaug zog dhau sijhawm.
  • Kev laus: Qhov kev pheej hmoo ntawm kev tsim aneurysm nce ntxiv tom qab hnub nyoog 65 xyoos.
  • Keeb kwm tsev neeg: Yog tias ib tug tswv cuab ntawm tsev neeg tau muaj aneurysm lossis dissection, koj muaj kev pheej hmoo ntau dua.
  • Cov roj cholesterol ntau lossis triglycerides ntau: Cov roj (lipids) ntau ntxiv hauv cov ntshav ua rau muaj kev pheej hmoo ntawm cov rog hauv cov hlab ntsha.
  • Cov kab mob autoimmune: Cov kab mob autoimmune xws li 'Giant cell arteritis' thiab 'Takayasu arteritis' tuaj yeem ua rau o ntawm phab ntsa ntawm cov hlab ntsha loj, ua rau lawv qaug zog.
  • Kev kis kab mob: Tsis tshua muaj, kev kis kab mob xws li mob syphilis, lossis kev kis kab mob ntawm phab ntsa ntawm cov hlab ntsha loj, tuaj yeem ua rau nws qaug zog.

Yuav kuaj mob aortopathy li cas ?

Feem ntau cov hlab ntsha aneurysm thiab cov hlab ntsha tawg tsis muaj tsos mob lossis cov cim ceeb toom, yog li ntawd tej zaum yuav tsis pom lawv kom txog thaum muaj teeb meem loj tshwm sim. Txawm li cas los xij, yog tias koj muaj cov yam txaus ntshai, koj tus kws kho mob yuav kuaj koj lub aorta kom paub txog cov cim ntawm tus kab mob.

Cov txheej txheem siv los kuaj mob aortopathy yog:

  • Kev kuaj lub cev: Koj tus kws kho mob yuav kuaj txhua yam ntawm koj txoj kev noj qab haus huv. Nws kuj tseem yuav soj ntsuam koj cov yam uas ua rau muaj kab mob plawv. Qhov no yuav suav nrog kev nug txog koj keeb kwm kev kho mob, cov yam ntxwv ntawm kev ua neej (xws li kev haus luam yeeb), thiab keeb kwm tsev neeg.
  • Kev kuaj noob caj noob ces: Koj tus kws kho mob yuav pom zoo kom kuaj noob caj noob ces. Qhov no yuav qhia seb koj puas muaj kev hloov pauv noob caj noob ces uas cuam tshuam nrog kab mob ntawm cov hlab ntsha hauv lub plawv.
  • Kev kuaj duab: Koj tus kws kho mob yuav xaj cov kev kuaj no los xyuas qhov loj thiab kev noj qab haus huv ntawm koj lub aorta. Cov kev kuaj no ntsuas txoj kab uas hla ntawm koj lub aorta thiab saib seb nws puas dav dua li qub.

Cov kev kuaj twg siv los kuaj mob Aortopathy?

  • Kev kuaj mob computer (CT scan)
  • Kev siv tshuab magnetic resonance imaging (MRI)
  • Kev kuaj lub plawv los ntawm lub qhov ntswg (Transthoracic echocardiogram - TTE)
  • Kev kuaj plawv los ntawm txoj hlab pas (transesophageal echocardiogram - TEE) (kev ntsuas plawv los ntawm txoj hlab pas)
  • Kev kuaj mob plab ultrasound (kev kuaj mob plab ultrasound)

Txhua qhov kev kuaj mob muaj nws cov txiaj ntsig thiab qhov tsis zoo. Koj tus kws kho mob yuav piav qhia seb koj xav tau qhov kev kuaj mob twg thiab yog vim li cas. Koj tus kws kho mob kuj tseem yuav siv ib lossis ntau qhov kev kuaj mob no los saib xyuas koj lub aorta dhau sijhawm. Tej zaum koj yuav tsum tau thaij cov duab no tsis tu ncua (piv txwv li, ib xyoos ib zaug). Koj yuav tsum tau kuaj mob no ntau npaum li cas nyob ntawm koj cov yam ntxwv uas ua rau muaj kev pheej hmoo thiab kev noj qab haus huv tam sim no ntawm koj lub aorta.

Cov kev kho mob rau Aortopathy yog dab tsi?

Kev kho mob nyob ntawm koj tus mob tshwj xeeb thiab koj qhov kev pheej hmoo ntawm cov teeb meem. Koj tus kws kho mob yuav kho koj txoj kev kho mob kom haum rau koj tus mob thiab cov kev xav tau. Cov kev xaiv kho mob suav nrog kev hloov pauv hauv lub neej, tshuaj, kev kho mob, thiab phais.

Cia peb pib nrog kev hloov pauv hauv lub neej!

Kev hloov pauv hauv lub neej yuav pab qeeb qeeb qee yam kab mob aortic thiab txo qhov kev pheej hmoo ntawm aneurysm tawg. Yog tias koj muaj kab mob aortic, nws yog ib qho tseem ceeb uas yuav tsum ua cov hauv qab no:

  • Tsis txhob haus dej cawv.
  • Tsis txhob haus luam yeeb thiab txhua yam khoom haus luam yeeb.
  • Noj zaub mov kom lub plawv noj qab nyob zoo.
  • Ua si nawv tsis tu ncua (raws li koj tus kws kho mob hais).
  • Tswj koj qhov hnyav kom noj qab nyob zoo.
  • Tswj cov yam uas ua rau muaj kab mob plawv xws li ntshav siab thiab roj cholesterol ntau.

Yog tias tsim nyog, kuj muaj cov tshuaj zoo li no.

Koj tus kws kho mob yuav sau ntawv kom noj tshuaj los pab txo koj cov ntshav siab. Cov tshuaj ntshav siab txo cov ntshav siab rau koj cov phab ntsa ntawm cov hlab ntsha. Qhov no tuaj yeem txo qhov kev pheej hmoo ntawm kev tawg lossis kev txiav ntawm cov hlab ntsha loj. Cov hom tshuaj uas koj tuaj yeem noj suav nrog:

  • Cov tshuaj ACE inhibitors (angiotensin converting enzyme)
  • Cov tshuaj Angiotensin receptor blockers (ARBs)
  • Cov tshuaj beta-blockers
  • Cov tshuaj calcium channel blockers
  • Cov tshuaj diuretics (cov tshuaj uas ua rau koj tso zis ntau dua)

Kev phais thiab lwm yam kev kho mob

Muaj ib txhia neeg xav tau kev kho mob lossis phais mob rau cov kab mob aortopathy. Cov no suav nrog:

  • Kev phais mob aneurysm (kev phais qhib ib txwm muaj)
  • Kev phais hloov cov hauv paus aorta
  • Kho cov hlab ntsha hauv lub hlwb (EVAR) - Qhov no yog kev kho mob uas siv ib lub raj ntxig los ntawm ib qho kev phais me me.
  • Kho cov hlab ntsha hauv lub qhov ntswg (TEVAR) - Qhov no kuj yog kev kho mob zoo sib xws rau cov hlab ntsha hauv lub qhov ntswg.

Peb ua tau dab tsi los txo qhov kev pheej hmoo ntawm aortopathy?

Koj tuaj yeem txo koj txoj kev pheej hmoo ntawm kev mob aortopathy los ntawm kev ua neej noj qab haus huv rau lub plawv. Nov yog qee cov lus qhia:

  • Tsis txhob haus tshuaj yeeb: Luam yeeb, tshuaj yeeb, thiab cawv tsis zoo rau koj lub plawv. Qhov tseeb, lawv tuaj yeem ua rau koj lub plawv thiab cov hlab ntsha puas tsuaj. Tsum haus luam yeeb thiab siv tshuaj yeeb tag nrho. Thaum nws los txog rau cawv, paub meej tias 'dej haus' yog dab tsi thiab txwv qhov ntau. Cov kws kho mob pom zoo tias cov poj niam tsis txhob haus ntau tshaj ib 'dej haus' ib hnub thiab cov txiv neej tsis txhob haus ntau tshaj ob 'dej haus' ib hnub.
  • Noj zaub mov zoo rau lub plawv: Qhov no suav nrog kev noj cov zaub mov uas muaj roj saturated tsawg, trans fat, sodium (ntsev), thiab qab zib. Txo cov carbohydrates refined (xws li mov ci dawb) thiab noj ntau cov nplej tag nrho (xws li mov ci tag nrho, mov xim av). Tsis tas li ntawd, yuav tsum paub txog kev noj haus cuam tshuam li cas rau koj cov roj cholesterol.
  • Kev Ua Si: Tsis muaj ib txoj kev uas haum rau txhua tus neeg. Ua yam koj nyiam. Tsis tas li ntawd, ua raws li koj tus kws kho mob cov lus qhia txog yam kev ua si twg uas muaj kev nyab xeeb rau koj. Feem ntau cov kws kho mob pom zoo kom ua 150 feeb ntawm kev ua si nruab nrab hauv ib lub lim tiam. Qhov no tuaj yeem suav nrog kev taug kev sai, caij tsheb kauj vab, lossis ua luam dej.
  • Tswj kev ntxhov siab: Nws tsis yooj yim li nws suab. Tab sis nws yog ib qho tseem ceeb uas yuav tsum sim kawm cov txoj hauv kev tshiab los pab koj daws kev ntxhov siab hauv koj lub neej txhua hnub. Tsis tas li ntawd, tham nrog koj tsev neeg thiab cov phooj ywg txog cov txheej txheem uas ua haujlwm rau lawv.

Yuav ua li cas rau ib tus neeg uas muaj Aortopathy? (Outlook)

Tus neeg zoo tshaj plaws los nug txog koj lub neej yav tom ntej yog koj tus kws kho mob. Nws yuav xav txog ntau yam, piv txwv li:

  • Koj tus mob tshwj xeeb.
  • Tus nqi ntawm kev nce qib ntawm koj tus kab mob.
  • Koj lub hnub nyoog thiab poj niam txiv neej.
  • Koj cov yam ntxwv uas ua rau muaj kab mob plawv.
  • Koj tsev neeg keeb kwm kev kho mob.
  • Koj cov keeb kwm kho mob tag nrho.

Tham nrog koj tus kws kho mob txog yam uas yuav tshwm sim rau yav tom ntej.

Yog tias kuv muaj Aortopathy, kuv yuav tsum saib xyuas kuv tus kheej li cas?

Koj tus kws kho mob yuav muab cov lus qhia rau koj txog kev saib xyuas koj tus kheej. Ua raws li cov lus qhia ntawd kom meej, thiab nug koj tus kws kho mob yog tias koj muaj lus nug dab tsi. Koj yuav tsum ua cov hauv qab no:

  • Tsis txhob ua si nawv hnyav lossis ua kis las uas kov cov khoom sib chwv.
  • Txwv lossis tsum tsis txhob haus cawv kiag li.
  • Hloov koj cov zaub mov noj.
  • Tsum haus luam yeeb los yog siv cov khoom luam yeeb.
  • Noj koj cov tshuaj raws li tau qhia.

Cev Xeeb Tub thiab Aortopathy

Kev cev xeeb tub tuaj yeem ua rau muaj kev phom sij yog tias koj muaj kab mob plawv. Tham nrog koj tus kws kho mob ua ntej koj npaj yuav cev xeeb tub kom paub tseeb tias nws muaj kev nyab xeeb rau koj. Tej zaum koj yuav xav tau kev saib xyuas tshwj xeeb thaum cev xeeb tub (xws li kev kuaj duab ntau zaus) kom txo koj qhov kev pheej hmoo ntawm cov teeb meem. Tsis txhob siv cov tshuaj uas tsis muaj kev nyab xeeb thaum cev xeeb tub. Koj tus kws kho mob yuav tsum hloov koj cov tshuaj.

Kuv yuav tsum mus ntsib kws kho mob thaum twg?

Mus ntsib koj tus kws kho mob kom tau txais kev kuaj mob txhua xyoo, thiab mus rau txhua qhov kev teem caij rov qab. Koj tus kws kho mob yuav qhia rau koj tias koj yuav tsum tuaj kuaj mob ntau zaus npaum li cas.

Yog tias koj tau kuaj pom tias muaj kab mob plawv txij thaum yug los thaum koj tseem yog menyuam yaus, tej zaum koj yuav muaj ib tug kws kho mob plawv menyuam yaus uas saib xyuas koj tus mob. Tab sis, tom qab koj muaj 18 xyoo, tej zaum koj yuav tsis tau pom ib tug kws tshwj xeeb tshiab. Kev tshawb fawb qhia tau hais tias ntau tus neeg tsis meej pem thaum lawv hloov ntawm kev saib xyuas menyuam yaus mus rau kev saib xyuas neeg laus. Yog tias koj tau kho mob plawv txij thaum yug los thaum koj tseem yog menyuam yaus, nws yog ib qho tseem ceeb uas yuav tsum txuas ntxiv ua haujlwm nrog ib tug kws kho mob plawv thaum koj laus. Qhov no muaj tseeb txawm tias koj tsis hnov ​​​​​​muaj teeb meem dab tsi los xij. Koj tus kws kho mob plawv yuav qhia koj txog koj qhov kev pheej hmoo rau aortopathy thiab lwm yam mob thaum koj laus zuj zus.

Thaum kawg, tej yam tseem ceeb tshaj plaws uas yuav tsum nco ntsoov (Cov Lus Coj Mus Tsev)

Kab mob plawv Aortopathy yog ib yam mob hnyav uas yuav ua rau koj tuag taus yog tias tsis paub thiab kho. Yog tias ib tug neeg hauv koj tsev neeg tau muaj kab mob aneurysm lossis kev txiav ntawm lub aorta, tham nrog koj tus kws kho mob txog koj qhov kev pheej hmoo. Qee tus neeg muaj kev pheej hmoo siab dua vim yog cov mob caj ces, kab mob plawv txij thaum yug los, lossis cov yam ntxwv ntawm kev ua neej xws li kev haus luam yeeb. Kev ua neej noj qab haus huv rau lub plawv tuaj yeem txo koj qhov kev pheej hmoo ntawm aortopathy thiab ua kom koj lub cev muaj zog.Saib xyuas koj lub siab, vim nws yog lub plawv dhia ntawm koj lub neej!

👩🏽‍⚕️ Cov Lus Nug Ntxiv (FAQs)

💬 Aortopathy puas yog kab mob plawv?

Tsis yog ntawm lub plawv, qhov no yog ib qho kab mob ntawm 'cov hlab ntsha loj tshaj plaws' uas los ntawm lub plawv. Lub npe no yog muab rau txhua yam kab mob uas tshwm sim hauv cov hlab ntsha loj thiab loj tshaj plaws (Aorta) uas nqa cov ntshav los ntawm peb lub plawv mus rau tag nrho lub cev. Feem ntau, qhov tshwm sim yog tias cov phab ntsa ntawm cov hlab ntsha no dhau los ua nyias thiab tsis muaj zog.

💬 Yuav ua li cas thaum cov leeg ntshav no qaug zog?

Thaum qhov no qaug zog lawm, cov hlab ntsha yuav tsis tuaj yeem tiv taus qhov siab ntawm cov ntshav uas lub plawv tso tawm, thiab cov hlab ntsha yuav pib loj zoo li lub pob (Aortic aneurysm). Yog tias nws tseem loj hlob zoo li no, cov hlab ntsha yuav tawg tam sim ntawd yam tsis muaj lus ceeb toom ua ntej (Aortic dissection / Rupture). Tom qab ntawd tus neeg mob yuav tuag hauv ob peb feeb.

💬 Koj puas nrhiav tau qhov no ua ntej nws tawg?

Feem ntau, tus neeg mob tsis hnov ​​​​​​mob lossis tsis xis nyob los ntawm qhov kev loj hlob ntawm cov hlab ntsha no (ib yam kab mob ntsiag to). Vim tias qhov no feem ntau yog los ntawm noob caj noob ces (genetic - zoo li Marfan syndrome), yog tias ib tug neeg hauv tsev neeg muaj lub aorta tawg, nws yog ib qho tseem ceeb uas lwm tus tau txais Echocardiogram lossis CT scan los xyuas qhov no thiab noj qhov kev phais lossis tshuaj ntshav siab.


` Aortopathy, Aorta, Kab Mob Plawv, Aneurysm, Aortic Dissection, Cov Kab Mob Genetic, Mob Hauv Siab, Ntshav Siab, Haus Luam Yeeb, Kev Noj Qab Haus Huv Plawv

Frequently Asked Questions (FAQ)

Syndromic Aortopathy yog dab tsi?

Peb kuj hu qhov no tias '(Syndromic hereditary thoracic aortic disease)'. Hais yooj yim xwb, koj muaj ib qho genetic syndrome uas cuam tshuam rau koj lub aorta thiab ua rau muaj lwm yam kev hloov pauv hauv koj lub cev. Qee cov syndromes uas ua rau muaj kab mob aorta yog:

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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