Qee zaum, thaum koj nkees heev, lossis thaum koj hnov ib yam dab tsi loj hauv koj lub siab, xws li kev zoo siab, kev tu siab, lossis kev ntshai, koj lub plawv puas dhia ceev dua thiab koj lub hauv siab xav tias nruj? Tej zaum koj lub qhov muag tig xiav thiab koj kiv taub hau? Tsis txhob xav tsis thoob, tej yam no tuaj yeem tshwm sim rau ib tug menyuam yaus me. Hnub no peb yuav tham txog ib qho mob tshwj xeeb uas tshwm sim hauv lub plawv dhia, uas yog qhov tsis tshua muaj tab sis tseem ceeb heev uas yuav tsum paub txog.
CPVT (Catecholaminergic Polymorphic Ventricular Tachycardia) yog dab tsi?
Hais yooj yim xwb, CPVT (Catecholaminergic Polymorphic Ventricular Tachycardia) yog ib yam mob uas tshwm sim hauv lub plawv dhia. Hauv qhov no, cov seem qis ntawm koj lub plawv, uas yog, cov chav qis ntawm lub plawv, lossis raws li cov kws kho mob hu lawv, cov ventricles , mam li pib dhia ceev heev thiab tsis zoo li qub thaum koj tawm dag zog, ua si, lossis xav tias muaj kev ntxhov siab ntau, xws li kev zoo siab heev, kev ntshai, lossis kev zoo siab.
Xav txog nws li no: peb lub siab zoo li lub twj tso dej. Nws yog lub uas tso cov ntshav thoob plaws lub cev. Yog li, thaum lub plawv no dhia ceev dhau, uas yog, thaum lub plawv dhia tsis zoo, nws muaj teeb meem tso cov ntshav kom raug thiab xa mus rau txhua qhov ntawm lub cev. Qhov no yog qhov tshwm sim hauv CPVT.
Tus mob no hu ua CPVT feem ntau npaum li cas?
Qhov tseeb, tus mob no hu ua CPVT yog qhov tsis tshua muaj . Raws li cov kws kho mob hais, kwv yees li ntawm ib ntawm kaum txhiab (10,000) tus neeg muaj tus mob no. Yog li, tsis yog txhua tus neeg yuav tau hnov txog nws.
Vim li cas qhov CPVT no thiaj tshwm sim? Dab tsi yog qhov ua rau?
Muaj coob tus neeg muaj ib lo lus nug, "Vim li cas qhov no thiaj tshwm sim?" Qhov laj thawj tseem ceeb rau CPVT yog kev hloov pauv hauv peb cov noob caj noob ces, kev hloov pauv . Koj paub, txhua yam hauv peb lub cev yog tswj hwm los ntawm cov noob caj noob ces no.
- Feem ntau, koj tuaj yeem tau txais qhov kev hloov pauv caj ces no los ntawm koj niam lossis koj txiv, lossis ob qho tib si.
- Tab sis tsis tshua muaj, uas yog, tsis tshua muaj, qhov kev hloov pauv caj ces no tuaj yeem tshwm sim hauv tus neeg tshiab lub cev yam tsis muaj kev cuam tshuam caj ces los ntawm niam txiv.
Yog li, qhov kev hloov pauv caj ces no ua rau muaj teeb meem hauv txoj kev uas cov calcium ions raug tswj hwm hauv cov hlwb plawv. Qhov ntawd yog qhov laj thawj tseem ceeb uas ua rau lub plawv dhia nrawm dua thaum lub plawv ntxhov siab lossis thaum lub sijhawm ua si.
Cov tsos mob ntawm CPVT yog dab tsi? Peb yuav paub nws li cas ?
Cov tsos mob ntawm CPVT feem ntau pib thaum yau, feem ntau yog nruab nrab ntawm hnub nyoog 7 thiab 12. Cov tsos mob feem ntau tshwm sim tom qab khiav thiab ua si ntau , lossis thaum ib tus neeg muaj kev xav zoo , xws li kev xyiv fab, kev ntshai, kev npau taws, lossis kev zoo siab.
Nov yog qee yam uas yuav yog cov cim qhia ntawm CPVT:
- Ntau tshaj li ib tug neeg ib txwmTej zaum koj yuav tsaus muag tas li, lossis kiv taub hau lossis qaug zog. Tej zaum koj yuav poob siab tam sim ntawd yam tsis muaj laj thawj thiab ntog.
- Lub plawv dhia ceev yog qhov kev xav sai sai, nrawm heev, thiab dhia nrawm zoo li muaj ib tug neeg khiav hauv koj lub hauv siab.
- Tej zaum yuav muaj tej yam mob xws li qaug dab peg . Qhov no tshwm sim vim tias cov ntshav uas mus txog lub hlwb txo qis thaum lub plawv tsis tso cov ntshav kom zoo.
Tseem Ceeb: Yog tias koj tus menyuam cia li kiv taub hau thaum ua si, khiav, lossis dhia, lossis yog tias lawv yws tias ua pa nyuaj, tsis txhob tsis quav ntsej nws. Nws yog ib qho tseem ceeb uas yuav tsum nrhiav kev pab kho mob tam sim ntawd.
Tus kws kho mob yuav kuaj mob CPVT li cas kom raug?
Yog koj lossis koj tus menyuam muaj cov tsos mob no, tus kws kho mob yuav ua ntau qhov kev kuaj mob kom paub tseeb tias koj puas muaj CPVT.
- Echocardiogram - kev kuaj echo: Qhov no zoo li kev ntsuas ultrasound ntawm lub plawv. Nws siv cov suab nthwv dej los pom meej meej txog koj lub plawv lub duab, seb phab ntsa plawv ua haujlwm zoo li cas, seb cov qhov valve puas ua haujlwm zoo, thiab ntshav ntws li cas.
- ECG (Electrocardiogram): Qhov kev kuaj no siv daim duab ntawm koj lub plawv cov teeb liab hluav taws xob, lossis lub plawv dhia. Ib tus neeg uas muaj CPVT yuav tsis pom muaj kev hloov pauv tseem ceeb ntawm ECG thaum lawv nyob hauv lub xeev ib txwm.
- Kev Ntsuas Kev Nyuaj Siab Thaum Ua Si: Qhov no yog ib qho kev xeem tseem ceeb heev los nrhiav CPVT. Thaum koj khiav ntawm lub treadmill lossis caij tsheb kauj vab, koj lub plawv dhia thiab ECG raug saib xyuas tas li. Cov neeg uas muaj CPVT feem ntau yuav muaj lub plawv dhia ceev tsis zoo thaum lub sijhawm ua si no.
- Lwm yam kev kuaj duab: Qee zaum, koj tus kws kho mob yuav pom zoo kom saib koj lub plawv kom tob dua, xws li MRI (Magnetic Resonance Imaging ), kev siv catheter rau lub plawv , lossis kev kuaj mob plawv .
- Kev Kuaj Genetic: Cov kev kuaj no nrhiav cov kev hloov pauv tshwj xeeb ntawm cov noob caj noob ces (kev hloov pauv) uas ua rau muaj CPVT hauv cov ntshav kuaj. Qhov no tuaj yeem lees paub tus kab mob thiab txiav txim siab seb lwm tus neeg hauv tsev neeg puas muaj kev pheej hmoo.
Qee zaum koj tus kws kho mob yuav muab ib lub tshuab me me rau koj uas koj tuaj yeem hnav tau ob peb hnub lossis ob peb lub lis piam. Qhov no hu ua lub tshuab saib xyuas kev mob lossis lub tshuab saib xyuas Holter.Nws sau cov hluav taws xob ntawm koj lub plawv thoob plaws hnub (24, 48, lossis ntev dua) thaum koj mus ua koj cov dej num txhua hnub thiab ua koj cov haujlwm hauv tsev ib txwm muaj. Qhov no muab rau koj tus kws kho mob lub tswv yim zoo txog koj lub plawv dhia li cas, txawm tias thaum koj tsis muaj tsos mob dab tsi los xij.
Cov kev kho mob rau CPVT yog dab tsi?
Yog tias lub plawv dhia sai sai, uas yog, yog tias nws mus rau hauv lub xeev ventricular tachycardia (Ventricular Tachycardia) , nws tuaj yeem ua rau tuag taus. Hauv cov xwm txheej zoo li no, yuav tsum tau siv hluav taws xob (Cardioversion lossis Defibrillation) los kho lub plawv dhia kom rov qab zoo li qub. Qhov no feem ntau ua raws li kev kho mob thaum muaj xwm txheej ceev.
Tiam sis rau lub sijhawm ntev, lub hom phiaj tseem ceeb ntawm kev kho mob CPVT yog tiv thaiv kom lub plawv dhia tsis txhob nrawm dhau thiab kom tswj tau lub plawv dhia ib txwm. Koj txoj kev npaj kho mob yuav suav nrog ib lossis ntau yam hauv qab no:
- Cov tshuaj kho mob:
- Cov tshuaj Beta-blockers: (piv txwv li Lopressor®, Corgard®) Cov tshuaj no ua haujlwm los ntawm kev txo cov teebmeem ntawm cov tshuaj hormones xws li adrenaline rau lub plawv. Qhov no pab tswj lub plawv dhia kom tsis txhob nce ntxiv thaum lub sijhawm ua si lossis kev ntxhov siab. Qhov no yog hom tshuaj tseem ceeb uas muab rau CPVT.
- Cov Tshuaj Calcium Channel Blockers: (piv txwv li Cardizem®, Procardia®) Qee zaum cov tshuaj no tuaj yeem muab nrog rau cov beta-blockers.
- Lwm cov tshuaj tswj lub plawv dhia: Tej zaum yuav muaj ib txhia neeg tau txais lwm cov tshuaj, xws li flecainide.
- Lub Tshuab Ua Pa Hluav Taws Xob Rau Lub Plawv (ICD): Qhov no yog ib lub tshuab me me, siv roj teeb uas raug phais muab tso rau hauv qab daim tawv nqaij ntawm lub hauv siab. Nws saib xyuas lub plawv dhia tas li. Yog tias lub plawv dhia tsis xwm yeem, lub tshuab yuav xa hluav taws xob los kho nws. Cov kws kho mob feem ntau pom zoo kom siv ICD rau cov neeg uas muaj kev pheej hmoo siab thiab lawv lub plawv dhia nyuaj tswj nrog tshuaj xwb.
- Kev phais plawv sab laug (LCSD): Qhov no yog ib txoj kev phais uas tshem tawm qee cov hlab ntsha uas mus rau lub plawv. Qhov no tuaj yeem txo qhov kev txhawb nqa ntawm lub plawv thiab txo qhov kev pheej hmoo ntawm kev mob plawv dhia ceev. Kev phais no yuav raug txiav txim siab rau cov neeg uas muaj ICD uas feem ntau poob siab lossis cov neeg uas tsis teb zoo rau cov tshuaj.
Tsis tas li ntawd xwb, koj yuav tsum tau hloov qee yam tseem ceeb rau koj txoj kev ua neej .
- Kev tawm dag zog hnyav xws li khiav ceev lossis tsa cov hnyav, yuav tsum raug txwv.
- Rau ib tug me nyuam yaus uas muaj CPVT, nws yog qhov zoo tshaj plaws kom tsis txhob koom nrog kev ua si sib tw , vim tias kev zoo siab thiab kev nyuaj siab ntawm kev yeej kev sib tw tuaj yeem ua rau lub plawv dhia ceev dua.
- Nws tseem ceeb heev rau kev xyaum ua kom txo tau kev ntxhov siab.
Peb puas tuaj yeem tiv thaiv qhov CPVT no kom tsis txhob tshwm sim?
Vim tias CPVT yog tshwm sim los ntawm kev hloov pauv caj ces, yeej tsis muaj txoj hauv kev los tiv thaiv nws kom tsis txhob tshwm sim . Vim tias nws tsis yog ib yam dab tsi uas peb tuaj yeem tswj tau.
Txawm li cas los xij, thaum pom tias muaj CPVT lawm, yog tias tswj tau zoo, uas yog, yog tias cov tshuaj uas tus kws kho mob sau tseg siv tau zoo, hloov pauv txoj kev ua neej raws li tau sau tseg, thiab mus ntsib kws kho mob tsis tu ncua, txawm tias tus neeg uas muaj CPVT kuj tuaj yeem ua neej zoo li qub.
Yog tias ib tug neeg hauv koj tsev neeg tau kuaj pom tias muaj CPVT, nws yog ib qho tseem ceeb uas yuav tsum xav txog kev kuaj noob caj noob ces thiab kev sab laj txog noob caj noob ces rau lwm tus neeg hauv tsev neeg, tshwj xeeb tshaj yog cov menyuam yaus. Tus kws pab tswv yim txog noob caj noob ces tuaj yeem pab koj nkag siab txog tus mob zoo dua, tham txog qhov muaj feem uas koj cov menyuam yuav tau txais nws, thiab tham txog cov teeb meem tseem ceeb xws li koj tuaj yeem ua dab tsi txog nws.
Yuav ua li cas thiaj li tsis txhob muaj teeb meem uas yuav tshwm sim vim yog CPVT?
Yog tias CPVT tsis raug tswj kom zoo, qee qhov teeb meem txaus ntshai tuaj yeem tshwm sim. Koj tuaj yeem ua cov no kom txo koj qhov kev pheej hmoo:
- Tham nrog koj tus kws kho mob thiab tsim kom muaj ib txoj kev npaj ua kom lub cev muaj kev nyab xeeb uas ua haujlwm rau koj. Koj tsis tas yuav tsum tsis txhob ua kom lub cev muaj kev nyab xeeb kiag li, tab sis koj yuav tsum paub tias cov kev tawm dag zog twg zoo thiab cov kev tawm dag zog twg tsis zoo.
- Txwv cov dej haus uas muaj caffeine xws li kas fes, tshuaj yej, qee cov chocolates, thiab qee cov dej qab zib kom ntau li ntau tau, vim caffeine yog ib yam khoom ua rau lub plawv dhia ceev thiab tuaj yeem ua rau koj lub plawv dhia ceev.
- Nco ntsoov ua tib zoo saib xyuas koj cov tsos mob . Yog tias koj kiv taub hau, mob hauv siab, lossis ua pa nyuaj, tsis txhob tsis quav ntsej cov tsos mob no. Hu rau koj tus kws kho mob tam sim ntawd.
- Tsis txhob nco ib hnub ntawm cov tshuaj uas koj tus kws kho mob tau sau tseg, noj nws raws sijhawm thiab raws li qhov ntau npaum li cas .
- Nws yog ib qho tseem ceeb heev uas yuav tsum mus ntsib kws kho mob raws sijhawm thiab mus kuaj mob uas tsim nyog. Qhov no yog ib yam dab tsi uas koj yuav tsum ua thoob plaws koj lub neej.
Ib tug neeg uas muaj CPVT yuav cia siab tau yav tom ntej zoo li cas?
Yog tias tsis kho, CPVT tuaj yeem ua rau muaj teeb meem kev noj qab haus huv thiab teeb meem. Qee qhov teeb meem, xws li lub plawv nres tam sim ntawd , tuaj yeem ua rau tuag taus.
Tiam sis, qhov xov xwm zoo yog tias nrog kev kho mob kom zoo thiab kev ua neej noj qab haus huv, feem ntau cov neeg uas muaj CPVT tuaj yeem tswj tau lub plawv dhia ib txwm muaj, txo qhov kev pheej hmoo ntawm cov teeb meem no, thiab ua neej zoo siab thiab txaus siab.
Yog koj muaj CPVT, koj yuav tsum tau saib xyuas tas mus li kom paub tseeb tias koj lub plawv dhia zoo li qub.Nws yog qhov tsim nyog. Qhov ntawd txhais tau tias koj yuav tsum mus ntsib kws kho mob tsis tu ncua thiab tau txais kev kuaj mob tsim nyog. Yog tias cov tsos mob CPVT rov tshwm sim, xws li kiv taub hau tom qab ua si, hu rau koj tus kws kho mob tam sim ntawd yam tsis muaj kev ncua.
Tej yam uas yuav tsum nug koj tus kws kho mob
Yog tias koj lossis koj tus menyuam muaj cov tsos mob no, lossis yog tias koj twb tau kuaj pom tias muaj CPVT lawm, nws yuav pab tau heev rau koj nug koj tus kws kho mob kom meej meej txog cov hauv qab no:
- Qhov ua rau muaj cov tsos mob no yog dab tsi? Qhov no puas yog CPVT?
- Kuv lossis kuv tus menyuam yuav tsum tau kuaj dab tsi ntxiv kom paub tseeb tias kuv muaj CPVT?
- Cov kev kho mob zoo tshaj plaws rau CPVT yog dab tsi? Kev kho mob twg zoo tshaj plaws rau kuv/kuv tus menyuam?
- Cov txiaj ntsig thiab cov kev mob tshwm sim ntawm cov kev kho mob no yog dab tsi?
- Koj yuav tsum ua li cas thaum mus ntsib kws kho mob, kom tswj tau cov tsos mob hauv tsev, lossis thaum muaj xwm txheej ceev?
- Kuv yuav tsum hloov dab tsi hauv kuv txoj kev ua neej (kev noj zaub mov, kev tawm dag zog)?
- Puas muaj lwm cov neeg hauv tsev neeg uas muaj kev pheej hmoo? Puas yuav tsum kuaj lawv thiab?
Thaum kawg, yuav tsum nco ntsoov li cas (Cov Lus Coj Mus Tsev)
Yog li, txawm hais tias tus mob uas peb tau tham txog ntev lawm, CPVT (Catecholaminergic Polymorphic Ventricular Tachycardia), yuav zoo li txaus ntshai me ntsis, qhov tseem ceeb tshaj plaws yog kom paub txog nws thaum ntxov thiab kho nws kom zoo.
Yog tias kuaj pom zoo, kho raws li koj tus kws kho mob tau hais, thiab hloov qee yam kev ua neej yooj yim, txawm tias ib tus neeg uas muaj CPVT tuaj yeem ua neej nyob zoo li qub, nquag, thiab txaus siab. Nco ntsoov, yog tias koj muaj cov tsos mob, nws yog ib qho tseem ceeb uas yuav tsum mus ntsib kws kho mob sai li sai tau yam tsis quav ntsej lawv. Koj tsis yog tib tug neeg hauv txoj kev no, thiab muaj cov kws kho mob txawj ntse thiab cov kws tshaj lij kev kho mob uas tuaj yeem pab thiab saib xyuas koj. Yog li ntawd, tsis txhob ntshai, ntsib qhov no nrog kev ua siab loj.
` CPVT, lub plawv dhia ceev, lub plawv dhia ceev, lub plawv dhia ceev ceev, kev hloov pauv ntawm cov noob caj noob ces, mob hlwb, lub plawv nres tam sim ntawd, kev noj qab haus huv ntawm menyuam yaus











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Tsis muaj lus teb tau muab tso tawm. Ntxiv koj cov lus tawm ntawm no thawj zaug.
Ntxiv koj cov lus