Kab mob Evans yog dab tsi? Cia peb tham txog nws!

Koj puas muaj tej lub sij hawm koj xav tias koj nkees? Los yog koj puas muaj teeb meem kom tsis txhob los ntshav txawm tias yog tej yam me me xwb los xij? Tej zaum yog vim koj lub cev tiv thaiv kab mob ua hauj lwm tawm tsam koj. Hnub no peb yuav tham txog ib yam mob uas tsis tshua muaj tab sis tseem ceeb heev uas yuav tsum paub txog. Qhov ntawd yog Evans Syndrome . Tsis txhob txhawj, peb yuav tham txog txhua yam hauv cov lus yooj yim.

Yog li, Evans Syndrome yog dab tsi?

Hais yooj yim xwb, Evans Syndrome yog ib yam kab mob autoimmune . Qhov uas tshwm sim yog cov tub rog uas yuav tsum tiv thaiv peb lub cev, lub cev tiv thaiv kab mob, pib ua yuam kev rhuav tshem qee cov qe ntshav ntawm peb. Nws zoo li peb cov tub rog tawm tsam peb cov neeg. Yog li ntawd, peb lub cev poob cov qe ntshav uas tsim nyog. Qhov kev txo qis ntawm cov qe ntshav no yog qhov peb hu ua cytopenia hauv kev kho mob.

Feem ntau cov neeg uas muaj tus kab mob Evans Syndrome yuav raug kev txom nyem los ntawm cov qe ntshav liab qis (ib yam mob hu ua anemia ) thiab cov platelets (ib yam mob hu ua thrombocytopenia ). Ntxiv rau ob qho tib si, qee tus neeg kuj tseem yuav muaj cov qe ntshav dawb tsawg hu ua neutrophils (ib yam mob hu ua neutropenia ).

Thaum cov hom qe ntshav no qis, ntau yam tseem ceeb hauv peb lub cev, xws li kev tau txais oxygen, kev txhaws, thiab kev tawm tsam kab mob, raug cuam tshuam. Yog vim li ntawd peb thiaj li tsis muaj zog, nkees, pib los ntshav yooj yim, thiab mob ntau zaus .

Tus mob no tuaj yeem cuam tshuam rau qee tus neeg me me xwb, thaum lwm tus tuaj yeem hnyav heev. Thiab nws cov teebmeem tsis kav ntev li qub thoob plaws lub neej. Qhov zoo tshaj plaws yog tias txawm hais tias tsis muaj kev kho rau nws, kev kho mob tuaj yeem pab tswj cov tsos mob thiab txo cov teebmeem .

Cov tsos mob ntawm Evans Syndrome yog dab tsi?

Cov tsos mob ntawm Evans Syndrome muaj peev xwm sib txawv heev. Nws nyob ntawm seb koj muaj hom cytopenia twg thiab nws hnyav npaum li cas. Feem ntau, anemia lossis thrombocytopenia tshwm sim ua ntej, thiab lwm yam tshwm sim tom qab.

Cov tsos mob thaum ntxov ntawm kev tsis muaj cov qe ntshav liab ( anemia ):

Koj puas nkees txawm tias taug kev ib ntus xwb los? Koj puas xav tias nkees thiab ua tsis tau tej yam uas koj tau ua yav dhau los? Tej zaum koj lub ntsej muag zoo li dawb me ntsis. Nov yog qee cov cim qhia tias koj muaj ntshav tsis txaus :

• Tsuas yog xav tias nkees heev xwb.
• Tawv nqaij daj ntseg (pallor) .
• Mob taub hau me ntsis los yog kiv taub hau .
• Ua pa nyuaj (ua tsis taus pa) .
• Lub plawv dhia ceev (tachycardia) .
• Hnov lossis xav tias koj lub plawv dhia tsis zoo li qub (lub plawv dhia tsis xwm yeem) .

Cov tsos mob thaum ntxov ntawm cov ntshav platelet tsis txaus (thrombocytopenia):

Koj puas tau pom tias qee zaum cov pob liab me me tshwm sim ntawm koj daim tawv nqaij? Los yog koj tsuas yog muaj cov qhov txhab thoob plaws koj lub cev xwb? Koj puas xav tias koj cov pos hniav los ntshav ntau dua li qub thaum koj txhuam koj cov hniav? Nov yog cov tsos mob ntawm cov ntshav platelets qis:

• Cov pob me me liab uas los ntshav (petechiae) hauv qab daim tawv nqaij.
• Cov xim av ntawm daim tawv nqaij (purpura) .
• Mob nqaij ntuag (ecchymosis) uas tshwm sim yam tsis muaj laj thawj.
• Los ntshav ntau dhau ntawm cov pos hniav lossis qhov ntswg.
• Los ntshav ntau thaum lub sijhawm muaj hli rau cov poj niam.
• Los ntshav nrog quav los yog zis.

Cov tsos mob ntawm cov qe ntshav dawb tsis muaj zog (tej zaum yuav tshwm sim lossis tsis tshwm sim tom qab):

Nws yog ib txwm muaj mob khaub thuas ib lossis ob zaug hauv ib hlis. Tab sis koj puas feem ntau mob kub taub hau? Koj puas mob qhov ncauj tas li? Puas zoo li lawv siv sijhawm ntev los kho? Nov yog qee yam uas tuaj yeem tshwm sim thaum koj cov neutrophils qis:

• Ua npaws.
• Cov mob qhov ncauj.
• Mob khaub thuas ntau zaus, kub taub hau, thiab mob plab.
• Kab mob pob ntseg rov tshwm sim dua.
• Kev kis kab mob fungal mus sij hawm ntev.
• Kab mob ntawm txoj hlab zis (UTIs) .

Lwm cov tsos mob ntawm Evans Syndrome (cov no yuav tshwm sim qee zaum):

• Cov qog ntshav hauv caj dab o.
• Lub qhov ntswg loj dua .
• Lub siab loj dua .
• Mob daj ntseg .

Vim li cas Evans Syndrome thiaj tshwm sim?

Raws li peb tau hais ua ntej lawm, Evans Syndrome yog ib yam kab mob autoimmune . Qhov no txhais tau tias peb lub cev tiv thaiv kab mob tsis nkag siab qee cov qe ntshav ntawm peb tus kheej ua "yeeb ncuab" thiab pib tawm tsam lawv.

Txoj haujlwm no yog ua los ntawm cov qe ntshav B, ib hom qe ntshav tshwj xeeb hauv peb lub cev tiv thaiv kab mob. Cov qe ntshav B no tsim ib yam dab tsi hu ua cov tshuaj tiv thaiv kab mob . Cov tshuaj tiv thaiv kab mob no mus ntes cov qe ntshav dawb huv thiab rhuav tshem lawv. Feem ntau, lawv pib tawm tsam ib hom qe ntshav ua ntej, thiab tom qab ntawd lawv tuaj yeem pib tawm tsam lwm hom qe ntshav.

Cov txheej txheem no yog qhov ua rau koj muaj qhov tsis txaus ntawm tsawg kawg yog ob hom qe ntshav (cytopenia), thiab qee zaum tag nrho peb hom. Qhov tsis txaus ntawm tag nrho peb hom no hu ua pancytopenia . Peb yam mob tseem ceeb uas cov qe ntshav no qis yog:

• Kab mob ntshav tsis txaus (AIHA)Qhov no yog thaum cov qe ntshav liab raug txo qis. Qhov ntawd yog, lawv raug rhuav tshem sai dua li lub cev ua tau.
• Kab mob ntshav qis hauv lub cev (ITP) : Qhov no yog ib qho mob uas cov ntshav platelets txo qis. Lub cev tiv thaiv kab mob tawm tsam thiab tshem cov ntshav platelets tawm ntawm cov ntshav.
• Kab mob autoimmune neutropenia (AIN) : Qhov no yog ib qho mob uas cov neutrophils, ib hom qe ntshav dawb, txo qis. Lub cev tiv thaiv kab mob tawm tsam thiab rhuav tshem cov neutrophils.

Xav txog nws, muaj ntau yam ua rau cov qe ntshav tsawg (cytopenia). Qee zaum nws tuaj yeem yog vim cov pob txha tsis tsim cov qe ntshav txaus. Txawm li cas los xij, hauv autoimmune cytopenia, lub cev tiv thaiv kab mob rhuav tshem nws cov qe ntshav.

Cov tsos mob dab tsi ua rau muaj Evans syndrome?

Cov kws tshawb fawb tseem tsis tau paub meej tias yog vim li cas cov kab mob autoimmune no thiaj li tshwm sim. Tab sis lawv tau pom tias cov kab mob no feem ntau pib tom qab muaj mob hnyav lossis muaj xwm txheej uas ua rau lub cev tiv thaiv kab mob ntxhov siab. Cov no hu ua cov teeb meem .

Tsis tas li ntawd xwb, yog tias koj muaj ib yam kab mob autoimmune, koj yuav muaj feem ntau dua los muaj lwm yam kab mob. Zoo li tus kab mob tiv thaiv kab mob no kis tau ntawm ib qho ntawm lub cev mus rau lwm qhov.

Kab mob Evans tuaj yeem tshwm sim ntawm nws tus kheej (qhov no hu ua kab mob Evans thawj zaug ), lossis nws tuaj yeem tshwm sim ua tus mob thib ob uas cuam tshuam nrog lwm tus mob (qhov no hu ua kab mob Evans thib ob) . Qee qhov mob uas tuaj yeem cuam tshuam nrog txoj kev no yog:

• Kab mob lupus erythematosus (lupus)
• Kev tiv thaiv kab mob tsis zoo uas tshwm sim ntau zaus
• Kev tsis txaus IgA xaiv
• Kab mob Sjögren
• Cov kab mob lymphoma uas tsis yog Hodgkin
• Kab mob leukemia lymphocytic ntev
• Kab mob siab C ntev
• Kev kis tus kab mob HIV mus ntev

Yog koj muaj tus mob Evans syndrome thawj zaug, tej zaum nws yuav tshwm sim tom qab muaj mob ib ntus, lossis koj yuav tsis muaj yam ua rau mob. Cov kws tshawb fawb faib tus mob Evans syndrome ua ib yam mob uas tsis paub meej . Qhov no txhais tau tias tsis tau pom muaj yam ua rau mob ncaj qha.

Cov teeb meem uas yuav muaj tau ntawm Evans Syndrome yog dab tsi?

Tsis yog txhua tus neeg uas muaj tus kab mob Evans Syndrome yuav muaj teeb meem. Ib txhia neeg tsuas muaj cov tsos mob me me xwb. Txawm li cas los xij, thaum muaj mob hnyav, cov qe ntshav tsis txaus (cytopenias) no tuaj yeem ua rau tuag taus. Piv txwv li:

• Thaum tsis muaj cov qe ntshav liab txaus los nqa oxygen mus rau lub cev, ces yuav tsis muaj oxygen txaus hauv cov ntshav (hypoxemia) . Qhov no nyuaj heev rau lub plawv thiab tuaj yeem ua rau muaj kab mob plawv thiab lub plawv tsis ua haujlwm.
• Thaum koj cov ntshav tsis txaus , uas pab koj cov ntshav txhaws, koj cov ntshav tsis txhaws zoo. Qhov no tuaj yeem ua rau koj los ntshav yooj yim thiab sai. Qhov no tuaj yeem ua rau muaj ntshav tsis txaus.
• Thaum koj lub cev poob cov neutrophils , uas pab tiv thaiv kev kis kab mob, koj yuav muaj feem kis tau kab mob ntau zaus dua, thiab lawv tuaj yeem hnyav thiab kis thoob plaws koj lub cev. Qhov no tuaj yeem ua rau muaj mob txaus ntshai hu ua sepsis .

Cov kws kho mob kuaj mob Evans Syndrome li cas?

Kab mob Evans yog kuaj tau los ntawm kev kuaj ntshav . Tej zaum yuav kuaj tau yog tias koj muaj cov tsos mob ntawm cytopenia, lossis thaum lub sijhawm suav cov qe ntshav thaum lub sijhawm kuaj mob niaj hnub.

Yog koj qhov Kev Ntsuas Ntshav Tag Nrho (CBC) qhia tau tias koj cov qe ntshav liab, cov ntshav platelets, lossis cov neutrophils qis, koj pab neeg kho mob yuav ua ntau qhov kev kuaj ntxiv. Piv txwv li, lawv yuav kuaj koj cov ntshav kom paub txog cov tshuaj tiv thaiv kab mob uas cuam tshuam nrog Evans Syndrome. Lawv kuj tseem yuav kuaj xyuas lwm yam mob uas tuaj yeem ua rau cytopenia, xws li qee yam kev kis kab mob lossis mob qog noj ntshav.

Cov kws kho mob lees paub tias muaj tus mob Evans Syndrome los ntawm kev tshem tawm txhua yam ua rau muaj lwm yam. Qee zaum, lawv kuj yuav tsum tau ua CT scan (computed tomography scan) lossis kuaj pob txha kom paub tseeb tias tsis muaj lwm yam mob.

Puas muaj tshuaj kho tau tag nrho rau tus kab mob Evans Syndrome? Yuav kho nws li cas?

Qhov tseeb, tsis muaj kev kho kom zoo tag nrho rau Evans Syndrome, lossis lwm yam kab mob autoimmune. Cov kws kho mob kho cov kab mob autoimmune no los ntawm kev muab cov tshuaj uas txo qhov kev ua haujlwm ntawm koj lub cev tiv thaiv kab mob.

Tsis tas li ntawd xwb, koj cov tsos mob yuav raug kho cais. Piv txwv li, yog tias koj cov qe ntshav qis heev, koj tus kws kho mob yuav kho tau qhov no los ntawm kev hloov ntshav qee zaus.

Ib yam li ntau yam kab mob autoimmune uas mob ntev, Evans Syndrome tuaj yeem zoo dua thiab phem dua raws sijhawm. Qee zaum cov tsos mob yuav zoo li ploj mus (hu ua kev zam txim) , tab sis tom qab ntawd lawv yuav rov qab los lossis hnyav dua (hu ua kev rov qab mob ).

Tej zaum koj yuav tau sim ntau yam kev kho mob thoob plaws hauv koj lub neej, vim tias lawv txoj kev vam meej tuaj yeem sib txawv raws sijhawm. Koj tus kws kho mob yuav sim tiv thaiv koj ntawm cov teeb meem loj tshaj plaws ntawm Evans Syndrome.

Cov kev kho mob yog dab tsi?

Kev kho mob rau tus mob Evans Syndrome yog siv cov tshuaj uas tiv thaiv kab mob thiab, yog tias tsim nyog, hloov ntshav. Cov tshuaj no ua haujlwm los ntawm kev txo qhov kev tawm tsam yuam kev los ntawm koj lub cev tiv thaiv kab mob.

Cov tshuaj tseem ceeb uas tau muab:

• Cov tshuaj Corticosteroids , xws li prednisone . Qhov no feem ntau yog thawj zaug kho mob.
• Kev kho mob immunoglobulin hauv cov hlab ntsha (IVIg) yog muab cov tshuaj uas muaj cov tshuaj tua kab mob rau tib neeg los ntawm cov hlab ntsha. Cov tshuaj tua kab mob tshiab no tuaj yeem khi rau cov tshuaj tua kab mob autoimmune uas tsis zoo thiab ua rau lawv tsis ua haujlwm.

Yog koj tsis teb zoo rau cov kev kho mob ib txwm muaj, koj tus kws kho mob yuav sim lwm yam kev kho mob. Cov no suav nrog:

• Cov tshuaj monoclonal antibodies , xws li rituximab . Cov no yog cov tshuaj antibodies uas ua nyob rau hauv chav kuaj. Qee zaum cov no tuaj yeem tiv thaiv kev teb ntawm tus kab mob autoimmune. Koj tus kws kho mob yuav qhia cov no yog tias lwm yam tshuaj tsis ua haujlwm.
• Tshem tawm koj lub qhov ntswg . Hauv cov mob hnyav, koj tus kws kho mob yuav pom zoo kom phais koj lub qhov ntswg. Koj lub qhov ntswg yog qhov chaw uas cov qe ntshav qub raug tshem tawm. Yog li thaum tshem tawm lub qhov ntswg, cov txheej txheem qeeb me ntsis.

Puas muaj teeb meem lossis cov kev mob tshwm sim ntawm kev kho mob?

Thaum koj noj cov tshuaj tiv thaiv kab mob, koj lub cev tiv thaiv kab mob tsis kam rau koj tus kab mob autoimmune. Txawm li cas los xij, koj txoj kev tiv thaiv kab mob kuj txo qis . Yog li koj yuav tsum tau ceev faj tshwj xeeb kom tsis txhob muaj mob.

Koj tus kws kho mob yuav pom zoo kom txhaj tshuaj tiv thaiv kab mob ntxiv rau cov uas koj twb tau txhaj lawm. Thaum koj lub cev tiv thaiv kab mob tsis muaj zog (immunocompromised), koj yuav muaj feem yuav mob hnyav dua uas koj feem ntau tsis tau mob.

Puas yog kev nyob nrog Evans Syndrome cuam tshuam rau lub neej?

Kab mob Evans tsis tas yuav cuam tshuam rau koj lub neej. Ib txhia neeg tsuas muaj cov tsos mob me me xwb, qee zaum. Txawm li cas los xij, qee qhov teeb meem, xws li kev los ntshav, kab mob plawv, thiab kev kis kab mob, tuaj yeem ua rau tuag taus.

Yog koj muaj tus mob Evans syndrome theem ob, uas txhais tau tias koj muaj nws nrog lwm yam mob ntev, qhov ntawd kuj tuaj yeem cuam tshuam rau koj lub neej. Tej zaum koj yuav muaj cov teeb meem txaus ntshai uas los nrog koj lwm yam mob.

Yuav ua li cas rau ib tus neeg uas muaj Evans Syndrome?

Cov neeg uas muaj tus kab mob Evans Syndrome muaj ntau yam kev paub sib txawv. Cov tsos mob yuav tsis hnyav heev los yog tsis hnyav heev. Ib txhia neeg xav tias lawv cov tsos mob ploj mus tag (kev zam txim). Lwm tus neeg yuav rov qab muaj dua tom qab (rov qab mob dua).

Muaj coob tus neeg xav tau kev kho mob thiab kev kuaj mob tsis tu ncua. Kev kho mob feem ntau ua haujlwm zoo, tab sis tsis yog txhua lub sijhawm. Qee zaum, qhov ua tau zoo ntawm kev kho mob yuav zoo li txo qis zuj zus. Tej zaum koj yuav tsum sim lwm yam kev kho mob.

Kuv yuav ua li cas thiaj saib xyuas kuv tus kheej thaum kuv tseem muaj tus mob Evans Syndrome?

Yog koj muaj tus mob Evans Syndrome, nws yog ib qho tseem ceeb uas koj yuav tsum mus kuaj mob tsis tu ncua . Txawm tias koj xav tias koj zoo los xij, koj tus kws kho mob yuav xav saib xyuas koj tus mob thiab paub txog nws thaum ntxov yog tias nws hnyav zuj zus.

Tsis tas li ntawd xwb, koj yuav tsum tau ua tib zoo saib xyuas koj tus kheej thiab saib xyuas seb puas muaj cov tsos mob tshiab. Yog tias koj mob khaub thuas uas tsis zoo dua, lossis yog tias koj los ntshav tsis tu ncua, hu rau koj tus kws kho mob tam sim ntawd .

Kuv yuav tsum nug kuv tus kws kho mob li cas?

Tej zaum koj yuav xav nug koj tus kws kho mob cov lus nug zoo li no:

• Kuv tsis muaj cov qe ntshav hom twg?
• Lawv tau txo qis npaum li cas lawm?
• Kuv yuav tsum tau saib xyuas cov tsos mob lossis cov cim ceeb toom twg?
• Kuv yuav paub li cas tias kev kho mob puas ua haujlwm lossis tsis ua haujlwm?
• Yog tias kev kho mob tsis ua haujlwm ces yuav ua li cas?
• Kuv yuav tsum teem sijhawm mus ntsib kws kho mob tom ntej thaum twg?

Kab mob Evans yog ib yam mob tsis tshua muaj uas tej zaum koj yuav tsis tau hnov ​​​​dua li. Cov tsos mob tuaj yeem txawv txawv thiab ntxhov siab. Kev nkag siab txog qhov xwm txheej thiab nws txhais li cas tuaj yeem yog ib qho txheej txheem nyuaj me ntsis.

Txawm hais tias Evans Syndrome yog ib yam mob uas yuav kho tau koj mus ib txhis los xij, nws tsis zoo li qub tas li. Cia siab tias koj yuav zoo dua, tsawg kawg yog qee zaum. Txawm koj xav li cas los xij, koj pab neeg kho mob yuav nyob ntawd los muab kev kho mob uas koj xav tau.

Cov Lus Xaus Kawg coj mus tsev

Zoo, yog li cia peb rov qab qhia koj txog qee yam tseem ceeb tshaj plaws uas peb tau tham txog.

• Evans Syndrome yog dab tsi?Ib yam kab mob tsis tshua muaj uas koj lub cev tiv thaiv kab mob tawm tsam koj cov qe ntshav.
• Qhov no tuaj yeem ua rau cov qe ntshav liab txo qis ( anemia ), platelets (thrombocytopenia), thiab tej zaum neutrophils (neutropenia) .
• Tej zaum yuav muaj cov tsos mob xws li qaug zog heev, ntsej muag dawb paug, mob yooj yim, los ntshav ntau zaus, thiab kis kab mob ntau zaus .
• Txawm hais tias tsis muaj kev kho mob tag nrho rau qhov no, cov tsos mob tuaj yeem tswj tau nrog kev kho mob .
• Nws yog ib qho tseem ceeb heev uas yuav tsum ua raws li cov lus qhia kho mob tsis tu ncua thiab ua tib zoo saib xyuas cov tsos mob.
• Koj tsis nyob ib leeg xwb. Koj cov kws kho mob thiab cov neeg koj hlub yuav pab koj. Nws tseem ceeb heev uas yuav tsum xav txog qhov zoo.

Vam tias cov ntaub ntawv no yuav pab tau koj. Yog tias koj muaj lus nug dab tsi, tsis txhob yig nrog koj tus kws kho mob tham.

Evans syndrome, kab mob autoimmune, cytopenia, anemia, thrombocytopenia, neutropenia, cov kab mob ntshav