Koj puas tau muaj mob taub hau thiab mob heev thaum koj txav koj ob lub qhov muag? Los yog koj puas xav tias koj tswj tsis tau koj ob lub qhov muag kom zoo? Yog tias koj muaj cov tsos mob zoo li no, nws yuav yog vim muaj ib yam mob tsis tshua muaj hu ua Tolosa-Hunt Syndrome, uas peb yuav tham txog hnub no. Tsis txhob txhawj, peb yuav tham txog txhua yam hauv txoj kev yooj yim uas koj nkag siab.
Tolosa-Hunt Syndrome yog dab tsi?
Hais yooj yim xwb, tus mob Tolosa-Hunt syndrome yog ib yam mob tsis tshua muaj. Nws ua rau mob taub hau thiab mob hnyav thaum koj txav koj lub qhov muag, lossis tsis txav koj lub qhov muag. Cov tsos mob no tuaj yeem tshwm sim thiab ploj mus thoob plaws hauv koj lub neej. Zoo li muaj ib tug qhua uas tsis tau caw tuaj rau hauv koj lub tsev. Lawv cuam tshuam koj hnub thiab ua rau koj tsis xis nyob. Tab sis hmoov zoo, cov qhua no tsis tuaj ntau zaus.
Kev tshawb fawb qhia tias qhov ua rau muaj tus mob no tej zaum yuav yog o tom qab lub qhov muag, uas yog ib qho lus teb los ntawm peb lub cev tiv thaiv kab mob (mob o).
Tej zaum koj yuav tau hnov koj tus kws kho mob hu tus kab mob no ua lwm lub npe. Piv txwv li:
- `(Ophthalmoplegia)`
- `(Kev mob qhov muag rov qab tshwm sim dua)` (Qhov ntawd txhais tau tias nws rov tshwm sim dua)
- `(Ophthalmoplegia Syndrome)`
Txawm nws hu ua lub npe dab tsi los xij, feem ntau nws txhais tau tib yam: Tolosa-Hunt syndrome.
Qhov teeb meem no feem ntau tshwm sim li cas?
Qhov no yeej tsis tshua muaj . Yog koj saib cov ntaub ntawv thoob plaws ntiaj teb, kev tshawb fawb qhia tias muaj li ib ntawm ib lab tus tib neeg uas muaj tus mob Tolosa-Hunt syndrome. Yog li qhov no tsis yog ib yam kab mob uas cuam tshuam rau txhua tus.
Cov tsos mob ntawm Tolosa-Hunt syndrome yog dab tsi?
Cov tsos mob no feem ntau tshwm sim sai sai. Cov tsos mob tseem ceeb uas pom tau yog:
- Mob taub hau hnyav: Qhov no tsis zoo li mob taub hau ib txwm muaj. Qhov mob no hnov nyob rau sab saud ntawm lub ntsej muag, tshwj xeeb tshaj yog nyob ib puag ncig lub qhov muag ('mob taub hau periorbital'). Ib txhia neeg yuav hnov nws zoo li mob ntse, zoo li riam chob. Lwm tus yuav hnov nws zoo li mob tsis tu ncua lossis mob tsis tu ncua .
- Pom ob sab: Thaum koj saib ib yam, nws zoo li ob yam khoom sib cais. Zoo li ob lub qhov muag tsis tsom ntsoov zoo. Qhov no yog ib qho tsos mob uas ua rau koj ntxhov siab heev.
- Tsis muaj zog lossis tsis muaj peev xwm txav cov leeg nqaij nyob ib puag ncig lub qhov muag thiab lub ntsej muag: Nws nyuaj rau txav lub qhov muag, qee zaum txawm tias mus rau ib sab. Cov leeg nqaij ntawm lub ntsej muag kuj tuaj yeem raug cuam tshuam.
- Kev qaug zog ntev: Tej zaum koj yuav xav tias nkees tag nrho hnub, zoo li koj tsis tuaj yeem tshem tawm qhov kev qaug zog txawm tias koj pw tsaug zog npaum li cas los xij.
Ntxiv rau cov yam ntxwv tseem ceeb no, qee lwm yam ntxwv kuj tseem tuaj yeem pom:
- Qhov muag tawm (proptosis): Ib lossis ob lub qhov muag yuav zoo li tawm me ntsis mus tom ntej.
- Qaug zog ntawm lub qhov muag sab saud (ptosis):Lub qhov muag sab saud ntawm ib lossis ob lub qhov muag yuav tsis tuaj yeem tsa tau zoo thiab yuav zoo li poob qis.
- Kev Poob Qhov Muag: Qee tus neeg kuj tseem yuav muaj kev poob qhov muag me ntsis.
Cov tsos mob no feem ntau tsuas yog tshwm sim rau ib sab ntawm lub ntsej muag xwb. Lawv kuj tseem tuaj yeem tshwm sim sai sai thiab ploj mus yam tsis muaj kev kho mob (spontaneous remission). Txawm li cas los xij, lawv tuaj yeem rov tshwm sim dua.
Dab tsi ua rau muaj tus mob Tolosa-Hunt syndrome?
Yog hais qhov tseeb, peb tseem tsis tau paub meej tias yog dab tsi ua rau nws . Tiam sis muaj ob yam tseem ceeb uas cov kws kho mob thiab cov kws tshawb fawb xav tias ua tau:
1. Kev teb tsis zoo ntawm lub cev tiv thaiv kab mob: Qhov no yog thaum peb lub cev tiv thaiv kab mob - lub cev uas tiv thaiv peb ntawm kab mob - ua yuam kev tawm tsam peb cov nqaij noj qab haus huv. Hauv Tolosa-Hunt syndrome, qhov kev tawm tsam no tshwm sim hauv ob qho chaw rhiab heev tom qab lub qhov muag. Ib qho yog "Cavernous Sinus" , ib qho chaw zoo li qhov uas muaj cov leeg ntshav tseem ceeb thiab cov hlab ntsha uas muab ntshav rau lub hlwb. Qhov thib ob yog "Orbital Fissure" , ib qho qhib uas cov hlab ntsha thiab cov hlab ntsha uas txuas rau lub qhov muag hla mus. Peb lub cev tiv thaiv kab mob tawm tsam cov chaw no, ua rau o.
2. Cov hlab ntsha o los yog nqaim: Lwm txoj kev xav yog tias cov tsos mob no tshwm sim vim tias cov hlab ntsha hauv cov cheeb tsam no hu ua "Cavernous Sinus" thiab "Orbital Fissure" o thiab nqaim, txo cov ntshav ntws mus rau qee qhov ntawm lub hlwb thiab cov hlab ntsha ntsig txog lub qhov muag.
Ob qho tib si ntawm cov ntsiab lus no tseem nyob rau theem tshawb fawb, yog li nws nyuaj rau hais qhov laj thawj tshwj xeeb.
Cov yam ua rau muaj kev pheej hmoo no yog dab tsi?
Muaj tej yam uas ua rau muaj cov tsos mob ntawm Tolosa-Hunt syndrome. Cov no hu ua 'triggers'. Lawv suav nrog:
- Muaj tus kab mob viral .
- Kev raug mob hlwb .
- Muaj ib qho qog nyob qhov twg hauv lub cev, tshwj xeeb tshaj yog nyob rau thaj tsam taub hau.
- Ib qho mob xws li kev nthuav dav lossis o (aneurysm) ntawm cov hlab ntsha.
Tsis yog txhua tus neeg yuav muaj tus mob no tsuas yog vim lawv muaj cov no xwb, tab sis qhov kev pheej hmoo yuav nce ntxiv me ntsis.
Qhov no ua rau muaj teeb meem dab tsi?
Feem ntau, Tolosa-Hunt syndrome tsis yog ib qho mob uas yuav ua rau tuag taus. Txawm li cas los xij, qee zaum mob hnyav, nws tuaj yeem cuam tshuam rau koj qhov pom kev. Qhov no tshwm sim thaum qhov o ntawm "Cavernous Sinus" thiab "Orbital Fissure" tom qab lub qhov muag nthuav mus rau "Optic Nerve", lub paj hlwb tseem ceeb uas muab kev pom kev rau peb. Yog tias qhov no tshwm sim, kev poob qhov muag lossis lwm yam kev tsis pom kev tuaj yeem tshwm sim. Yog li ntawd, nws yog ib qho tseem ceeb uas yuav tsum nrhiav kev kho mob sai li sai tau thaum cov tsos mob tshwm sim.
Yuav kuaj mob li cas?
Tus kws kho mob yuav kuaj mob no tom qab mloog koj cov tsos mob, kuaj koj, thiab sau tag nrho koj cov keeb kwm kev kho mob. Qhov no yog ib qho txheej txheem nyuaj me ntsis, vim tias cov tsos mob no kuj tuaj yeem pom hauv lwm yam mob.
Yog li ntawd, kev kuaj ntshav thiab kev kuaj duab yog ua los xyuas kom meej tias muaj mob thiab tshem tawm lwm yam mob uas muaj cov tsos mob zoo sib xws (piv txwv li, mob qog hauv hlwb lossis muaj kab mob). Ob qho kev kuaj duab tseem ceeb uas siv rau qhov no yog:
- Kev Siv Tshuab X-ray (CT): Qhov no siv cov duab X-ray thiab lub khoos phis tawj los tsim ib daim duab peb-seem (3D) ntawm cov nqaij mos thiab cov pob txha hauv koj lub cev. Qhov no tuaj yeem pab nrhiav tej yam xws li o ntawm thaj chaw qhov ntswg.
- Kev Siv Duab Xam Xaj Sib Nqus (MRI): Qhov no siv lub hlau nplaum loj, cov nthwv dej xov tooj cua, thiab lub khoos phis tawj los ua cov duab meej heev ntawm sab hauv koj lub cev, tshwj xeeb tshaj yog lub hlwb thiab thaj chaw qhov muag. Nws muaj cov duab ntxaws dua li CT scan.
Cov kws kho mob siv cov kev ntsuas no los nrhiav qhov o ntawm cov cheeb tsam tom qab lub qhov muag hu ua "Cavernous Sinus" thiab "Orbital Fissure." Cov kev kuaj no kuj pab kom paub tseeb tias tsis muaj lwm yam ua rau.
Feem ntau yuav kuaj pom tus mob Tolosa-Hunt thaum twg?
Txawm hais tias tus mob no tuaj yeem cuam tshuam rau cov neeg txhua lub hnub nyoog, feem ntau nws raug kuaj pom thaum muaj hnub nyoog 40 xyoo .
Qhov no kho li cas?
Qhov no kho nrog cov tshuaj "(Steroid)" luv luv. Tshwj xeeb, siv cov tshuaj "(Corticosteroids)" . Cov tshuaj no ua rau txo qhov o ("mob"). Vim tias, qhov ua rau koj cov tsos mob tseem ceeb yog qhov o tom qab lub qhov muag.
Thaum koj noj cov tshuaj no hu ua "Corticosteroids," qhov o yuav txo qis, qhov kev nyem rau ntawm cov hlab ntsha yuav txo qis, thiab koj cov tsos mob yuav zoo sai sai.
Puas muaj tej yam tshwm sim ntawm kev kho mob?
Yog, ib yam li lwm yam tshuaj, '(Corticosteroids)' muaj qee yam kev phiv. Yog li ntawd, koj yuav tsum tham nrog koj tus kws kho mob ua ntej pib siv cov tshuaj no. Tom qab ntawd koj tuaj yeem nkag siab meej txog nws. Qee qhov kev phiv uas yuav tshwm sim yog:
- Ceg o
- Kev ntshaw zaub mov ntau ntxiv
- Kev hloov pauv ntawm lub siab
- Kev mob yooj yim
- Pom kev tsis meej me ntsis
Cov no tsis tshwm sim rau txhua tus, thiab feem ntau lawv ploj mus thaum tsis noj tshuaj lawm.
Kuv yuav zoo sai npaum li cas tom qab kho tas?
Qhov no yog xov xwm zoo tshaj plaws. Tom qab noj cov tshuaj steroid raws li tau qhia, koj tuaj yeem pib hnov qhov kev nplij siab zoo hauv lub sijhawm luv luv, zoo li ib lossis peb hnub. Qhov mob tau txo qis, nws yooj yim dua rau koj txav koj lub qhov muag, thiab cov tsos mob tsis zoo ntawd maj mam ploj mus.
Xav txog seb, yog koj tsis kho, cov tsos mob yuav ploj mus li ntawm 15 txog 20 hnub. Txawm li cas los xij, koj tsis xav raug kev txom nyem ntev npaum li ntawd. Tsis tas li ntawd, txawm tias tom qab cov tsos mob ploj mus lawm, lawv kuj yuav rov tshwm sim tsis tau xav txog. Yog li ntawd, nws yog qhov zoo tshaj plaws kom tau txais kev kho mob.
Qhov no puas yog ib qho teeb meem loj heev?
Kab mob Tolosa-Hunt tsis yog ib yam mob uas ua rau tuag taus. Txawm li cas los xij, thaum muaj cov tsos mob, nws yuav nyuaj rau ua tej yam niaj hnub, tshwj xeeb tshaj yog thaum muaj mob taub hau hnyav thiab teeb meem qhov muag.
Txawm li cas los xij, nrog kev kho mob, qhov kev kwv yees zoo heev. Vim tias cov tshuaj steroids txo cov tsos mob hauv 24 txog 72 teev, koj yuav zoo dua sai sai thiab rov qab ua tau koj cov dej num ib txwm.
Puas kho tau tus mob Tolosa-Hunt syndrome kom zoo tag nrho?
Tu siab kawg li, tsis muaj tshuaj kho tau tus kab mob no. Kev kho mob yog tsom rau kev tswj cov tsos mob thiab txo lawv sai sai. Cov tsos mob tuaj yeem rov tshwm sim dua, yog li ntawd tej zaum yuav xav tau kev kho mob.
Qhov no puas tiv thaiv tau?
Tam sim no tseem tsis tau muaj txoj kev paub los tiv thaiv tus kab mob no. Vim tias, zoo li peb tau tham ua ntej lawm, tseem tsis tau paub meej tias yog vim li cas, nws nyuaj rau hais tias yuav tiv thaiv nws li cas.
Thaum twg koj yuav tsum mus ntsib kws kho mob?
Yog koj xav tias koj muaj cov tsos mob ntawm Tolosa-Hunt syndrome - xws li mob taub hau sai sai, mob ib ncig ntawm lub qhov muag, pom ob sab, thiab nyuaj rau txav koj lub qhov muag - nco ntsoov mus ntsib kws kho mob tam sim ntawd. Tsis txhob ncua sijhawm.
Tom qab ntawd tus kws kho mob yuav sau ntawv kom siv cov tshuaj steroids luv luv los kho koj cov tsos mob. Vim tias cov tshuaj no ua haujlwm sai, koj yuav zoo dua sai sai thiab rov qab mus rau koj lub neej ib txwm.
Koj yuav tsum nug koj tus kws kho mob li cas?
Thaum koj mus ntsib kws kho mob, nws yog ib lub tswv yim zoo los nug qee cov lus nug zoo li no:
- Puas muaj mob Tolosa-Hunt uas cuam tshuam rau kuv qhov muag?
- Kuv puas yuav tsum tau noj tshuaj steroids los kho qhov no tiag?
- Kuv yuav tsum noj tshuaj '(Steroid)' li cas? Kuv yuav tsum noj nws ntev npaum li cas?
- Cov kev kho mob no muaj tej yam tshwm sim tsis zoo li cas? Kuv yuav tsum ua li cas thiaj li tiv thaiv tau kuv tus kheej ntawm tej yam no?
- Yog tias cov tsos mob rov qab los, kuv yuav tsum ua li cas?
Thaum koj nug cov lus nug zoo li no, koj yuav nkag siab zoo dua txog tus kab mob thiab nws txoj kev kho mob.
Thaum kawg, nco ntsoov qhov no (Cov Lus Coj Mus Tsev)
Kab mob Tolosa-Hunt yog ib yam mob uas tshwm sim sai sai thiab ua rau muaj cov tsos mob tsis xis nyob heev. Mob taub hau hnyav tuaj yeem ua rau koj ua tsis tau koj cov dej num txhua hnub. Qhov muag kuj tseem yuav raug cuam tshuam. Cov tsos mob no tuaj yeem tshwm sim thiab ploj mus thoob plaws hauv koj lub neej.
Tiam sis nco ntsoov, qhov no tsis yog qhov txaus ntshai rau lub neej, thiab muaj kev kho mob.Kev siv cov tshuaj steroids luv luv tuaj yeem txo cov tsos mob hauv ib mus rau peb hnub. Yog li ntawd, yog tias koj mus ntsib kws kho mob sai li sai tau thaum cov tsos mob tshwm sim thiab tau txais kev kho mob, koj tuaj yeem rov zoo sai sai thiab rov qab ua cov yam koj nyiam. Tsis txhob ntshai, tham nrog koj tus kws kho mob txog txhua yam.
Tolosa -Hunt Syndrome, Mob taub hau, Mob qhov muag, Pom ob sab, Tshuaj Steroids, MRI, CT scan, Ophthalmoplegia, Cavernous Sinus











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Tsis muaj lus teb tau muab tso tawm. Ntxiv koj cov lus tawm ntawm no thawj zaug.
Ntxiv koj cov lus