Qee zaum peb hnov, 'Auj, kuv tus menyuam muaj teeb meem me me ntawm lub plawv, nws yug los nrog lub suab plawv tsis meej'? Los yog, thaum ib tug tub ntxhais hluas ua pa nyuaj lossis mob hauv siab, cov kws kho mob hais tias, 'Muaj teeb meem me me nrog lub plawv valve.' Yog li ntawd peb yuav tham txog tus mob plawv uas tsis tshua muaj, tab sis tseem ceeb heev uas yuav tsum paub txog.
Lub plawv aortic ib daim nplooj ('Unicuspid Aortic Valve') no yog dab tsi?
Hais yooj yim xwb, lub plawv aortic valve hauv koj lub plawv tsuas muaj ib daim nplooj xwb es tsis yog peb daim uas nws ib txwm muaj. Lo lus "unicuspid" txhais tau tias "ib daim nplooj xwb." Xav txog nws zoo li lub qhov rooj uas tsuas muaj ib lub xauv xwb es tsis yog ob lub.
Cov ntawv me me no zoo li lub qhov rooj me me. Lawv qhib thiab kaw kom cov ntshav huv thiab muaj oxygen ntau dhau los ntawm lub plawv sab laug - lub plawv sab laug hauv qab - mus rau lub plawv aorta . Lub plawv aorta mam li tso cov ntshav mus thoob plaws lub cev. Yog li, thaum cov ntawv me me hauv lub valve no txo qis, tej zaum yuav muaj tej yam me me uas cuam tshuam rau cov ntshav ntws.
Ib txhia neeg uas muaj tus mob no, Unicuspid Aortic Valve, kuj tseem yuav muaj lwm yam teeb meem plawv. Piv txwv li:
- Aortopathy : Qhov no txhais tau tias tsis muaj zog hauv phab ntsa ntawm aorta.
- Kab Mob Ventricular Septal Defect (VSD) : Ib lub qhov hauv phab ntsa ntawm ob lub chav hauv qab ntawm lub plawv.
- Patent Ductus Arteriosus (PDA) : Cov hlab ntsha uas yuav tsum tau kaw tom qab yug los tseem qhib.
- Kev Hloov Pauv ntawm Cov Hlwb Ntshav Hauv Lub Plawv : Qee qhov kev hloov pauv hauv cov hlab ntsha uas muab ntshav mus rau lub plawv.
Qhov no yog ib qho mob tsis tshua muaj. Nws cuam tshuam txog li 0.02% ntawm cov pej xeem. Tsis tas li ntawd, nws feem ntau tshwm sim rau cov txiv neej.
Puas muaj cov hom no?
Yog, muaj ob hom tseem ceeb ntawm "Unicuspid Aortic Valve". Qhov txawv ntawm ob hom no yog qhov sib txawv uas ob daim nplooj (leaflets) txuas rau phab ntsa valve, uas hu ua "Commissure" . Koj tuaj yeem nkag siab qhov no zoo li no. Xav txog tias koj daim di ncauj txuas mus tas li rau koj lub ntsej muag, tab sis lawv tuaj yeem sib sau ua ke thiab sib cais, puas yog? Ntawd yog qhov "Commissure" yog.
Ob hom no yog:
1. Hom Acommissural: Qhov no yog hom hnyav tshaj plaws . Hauv qhov no, tsis muaj commissure, uas yog, tsis muaj qhov sib txawv. Thiab nws tsis txuas nrog aorta. Cov ntawv me me txhua daim lo ua ke, zoo li lawv tau vuam ua ke. Cov ntshav tsuas ntws los ntawm lub qhov me me, zoo li lub qhov pinhole.
2. Hom kev sib koom ua ke:Qhov no tsis hnyav npaum li lwm qhov, thiab nws kuj yog hom uas pom ntau tshaj plaws . Nws muaj ib qho "Commissure" uas yog, ib qho qhov sib txawv. Nws kuj txuas nrog lub aorta. Thaum hom valve no qhib, nws zoo li ib txoj kab. Ib txhia neeg piv rau lub qhov ncauj ntawm tus ntses.
Koj pom cov tsos mob dab tsi?
Yog tias ib tug neeg laus muaj tus mob no (Unicuspid Aortic Valve), cov tsos mob uas feem ntau pom tau yog:
- Ua tsis taus pa : Thaum koj nkees me ntsis, koj yuav xav tias koj yuav tsaus muag thaum nce ntaiv.
- Kab mob kiv taub hau : Thaum koj sawv ntsug tam sim ntawd, koj yuav xav tias kiv taub hau.
- Angina : Qhov no yog qhov mob lossis nruj hauv siab. Rau qee tus neeg, qhov no tuaj yeem kis mus rau lub puab tsaig, caj dab, lossis txawm tias caj npab.
- Tsaus muag/tsaus muag : Tam sim ntawd poob siab.
Cov menyuam yaus uas muaj tus mob no feem ntau muaj cov mob xws li lub plawv tsis ua haujlwm sab laug . Lawv kuj feem ntau poob phaus zoo li lwm cov menyuam yaus hnub nyoog li lawv, txhais tau tias lawv nce phaus me ntsis.
Hom "Acommissural" uas tau hais ua ntej lawm, uas yog hom mob hnyav, qhia cov tsos mob rau cov menyuam mos . Tab sis cov neeg uas muaj hom "Unicommissural" yuav tsis qhia cov tsos mob kom txog thaum lawv muaj hnub nyoog 20 lossis 30 xyoo, uas yog, kom txog thaum lawv loj hlob mus txog thaum lawv tseem hluas.
Vim li cas qhov no thiaj tshwm sim? Yog vim li cas?
Qhov mob no, hu ua "Unicuspid Aortic Valve", tshwm sim thaum peb daim nplooj uas feem ntau yuav tsum tsim pib tsim thaum tus menyuam tseem nyob hauv plab, thiab tom qab ntawd es tsis txhob sib cais, lawv sib koom ua ke thiab ua ib qho. Qhov no tshwm sim ua ntej tus menyuam yug los .
Txawm hais tias cov kws tshawb fawb tseem tsis tau ua pov thawj tseeb los xij, lawv xav tias qhov no yuav yog "mob uas tau txais los ntawm noob caj noob ces." Qhov ntawd txhais tau tias tej zaum yuav muaj kev cuam tshuam los ntawm noob caj noob ces.
Qhov no ua rau muaj teeb meem dab tsi?
Ib tug neeg uas muaj lub qhov ntswg aortic unicuspid yuav muaj ntau yam teeb meem raws sijhawm. Cov teeb meem tseem ceeb yog:
- Aortic valve stenosis : Qhov no tshwm sim thaum lub valve tsis qhib kom zoo, thaiv cov ntshav ntws. Qhov no ua rau lub plawv ua haujlwm hnyav dua los tso ntshav.
- Kev rov qab qhib lub plawv aortic: Lub plawv tsis kaw zoo, ua rau qee cov ntshav uas tau nqus rov qab mus rau hauv lub plawv.
- Kab mob Endocarditis uas kis tau los ntawm kev sib kis : Kev kis kab mob rau ntawm daim ntaub ntawm lub plawv, tshwj xeeb tshaj yog cov qhov valve. Cov neeg uas muaj cov qhov valve tsis zoo li qub muaj feem yuav kis tau kab mob ntau dua.
- Kev pheej hmoo ntawm Aortic Dissection : Qhov no yog ib qho mob tam sim ntawd thiab hnyav uas phab ntsa ntawm aorta rhuav tshem los ntawm sab hauv.
Tseem Ceeb: Nws yog ib qho tseem ceeb heev uas yuav tsum kuaj mob thiab kho tus kab mob kom raws sijhawm, ua ntej cov teeb meem no tshwm sim.
Koj nrhiav tau qhov no li cas?
Thaum koj mus ntsib kws kho mob, nws yuav mloog koj lub plawv nrog lub stethoscope thaum koj kuaj lub cev . Yog tias tus kws kho mob hnov lub suab plawv tsis zoo (lub suab "lub plawv nrov") ze ntawm koj lub aorta, nws yuav xav tias qhov no. Tom qab ntawd, nws yuav pom zoo kom kuaj ntxiv.
Cov kev ntsuam xyuas twg tab tom ua?
Cov kev ntsuam xyuas tseem ceeb uas tau ua los xyuas kom meej tias muaj qhov mob "Unicuspid Aortic Valve" no yog:
- Transthoracic Echocardiogram (TTE) : Qhov no zoo li kev ntsuas ultrasound ntawm lub plawv. Nws ua rau ntawm qhov chaw ntawm lub hauv siab. Nws tuaj yeem soj ntsuam zoo dua qhov zoo li ntawm lub plawv thiab kev ua haujlwm ntawm nws cov li qub.
- Kev kuaj lub plawv Echocardiogram (TEE) : Qhov no kuj yog echocardiogram. Txawm li cas los xij, ib lub raj me me raug ntxig los ntawm caj pas thiab lub plawv raug saib los ntawm txoj hlab pas. Qhov no tuaj yeem tsim cov duab meej dua li TTE.
- Kev Ntsuas Tomography Hauv Lub Plawv (CT) : Qhov no tuaj yeem tsim cov duab 3D uas hla ntawm lub plawv thiab aorta.
- MRI ntawm lub plawv (Magnetic Resonance Imaging) : Qhov no kuj tseem tuaj yeem muab cov ntaub ntawv qhia txog cov qauv thiab kev ua haujlwm ntawm lub plawv.
Yuav kho li cas?
Kev kho rau qhov no sib txawv raws li hnub nyoog thiab qhov hnyav ntawm cov tsos mob.
Cov kev kho mob uas feem ntau siv rau cov menyuam yaus yog:
- Kev Phais Mob Valvotomy : Qhov no suav nrog kev phais kom txiav cov ntaub so ntswg ntawm lub valve uas lo ua ke thiab tsim cov ntawv tshiab.
- Valvuloplasty : Qhov no suav nrog kev siv ib yam dab tsi zoo li lub npas los qhib lub valve.
- Commissurotomy : Phais cais cov cheeb tsam hu ua "Commissures" uas ob lub qhov muag txuas ua ke.
- Kev Kho Mob Ross : Qhov no yog ib qho kev phais mob nyuaj me ntsis. Peb mam li tham ntxiv txog qhov no tom qab.
Rau cov neeg laus , feem ntau yuav tsum tau phais kho lub plawv dhia (Unicuspid Aortic Valve kho) lossis hloov nws nrog lub plawv dhia tshiab (hloov chaw) .
Puas muaj tej yam kev mob tshwm sim/teeb meem ntawm kev kho mob?
Ib yam li lwm yam kev phais mob, tej zaum yuav muaj qee yam teeb meem nrog kev kho mob no. Tab sis tsis yog txhua tus yuav muaj cov teeb meem no. Tsis txhob txhawj, koj tus kws kho mob yuav qhia koj txog cov no.
Qee qhov teeb meem uas feem ntau tshwm sim yog:
- Kev kis kab mob
- Cov ntshav txhaws
- Los ntshav ntau dhau ('Bleeding')
- Endocarditis (kev kis kab mob ntawm lub valve)
- Teeb meem nrog daim ntaub uas siv rau hauv kev kho lub valve.
- Kev Thaiv Lub Plawv Tag Nrho : Kev cuam tshuam ntawm kev xa hluav taws xob ntawm lub plawv.
- Mob plawv nres
- Ntshav ntws los ntawm lub valve mus rau sab tsis yog.
- Lub plawv dhia tsis zoo li qub
Yuav siv sijhawm ntev npaum li cas thiaj kho tau?
Qhov no yuav txawv nyob ntawm seb koj tau ua dab tsi. Nws yuav siv sijhawm li ib lub lim tiam mus txog ob peb lub hlis kom rov zoo. Koj tus kws kho mob yuav qhia koj tias koj yuav tsum so ntev npaum li cas thiab thaum twg koj thiaj rov ua tau tej yam li qub.
Lub neej yuav zoo li cas nrog qhov xwm txheej no?
Yog tias koj muaj lub Unicuspid Aortic Valve, tej zaum koj yuav xav tau phais . Qhov tseeb, koj yuav tsum tau kho lossis hloov koj lub valve ntau dua ib zaug thaum koj tseem muaj sia nyob. Koj kuj tseem yuav muaj lwm yam teeb meem plawv. Koj kuj tseem yuav tsum tau noj cov tshuaj thinning ntshav (anticoagulants) tom qab phais, nyob ntawm seb koj muaj hom valve twg.
Tiam sis yuav tsum tau hais tias qhov "Unicuspid Aortic Valve" no tsis yog ib yam dab tsi uas yuav zoo dua . Tus mob tseem zoo li qub kom txog thaum koj phais kom kho nws.
Muaj xov xwm zoo. Ib txoj kev tshawb fawb pom tias 97% ntawm cov neeg uas tau phais lub plawv aortic rau ib qho mob hu ua "Unicuspid Aortic Valve" tseem muaj sia nyob 10 xyoo tom qab .
Txawm li cas los xij, kuj muaj kev xav tias yog tias ib tus neeg hnub nyoog qis dua 65 xyoo tau txais lub qhov ntswg prosthetic aortic vim yog qhov mob no, nws tuaj yeem txo qhov kev cia siab ntawm lub neej ntau dua 10 xyoo. Yog vim li cas cov kws tshawb fawb hais tias Ross Procedure yog qhov zoo tshaj plaws rau cov tub ntxhais hluas, cov neeg nquag. Hauv qhov "Ross procedure" no, koj coj koj tus kheej lub qhov ntswg thiab hloov nws mus rau qhov chaw uas muaj kab mob aortic valve. Tom qab ntawd, ib qho pulmonary homograft los ntawm tus neeg tuag tau hloov mus rau qhov chaw uas lub qhov ntswg tshem tawm tau siv los. Txawm hais tias qhov no nyuaj me ntsis, cov txiaj ntsig tau hais tias zoo.
Koj xav ua dab tsi ntawm koj ib sab?
Tom qab phais lawm, koj yuav tsum ua raws li koj tus kws kho mob cov lus qhia kom zoo txog yuav ua li cas saib xyuas koj cov qhov txiav/qhov txiav . Nws kuj tseem yuav qhia koj tias koj yuav tsum so ntev npaum li cas thiab thaum twg koj tuaj yeem pib tsav tsheb thiab lwm yam dej num txhua hnub.
Tsis txhob hnov qab: Nws yog ib qho tseem ceeb heev uas yuav tsum noj koj cov tshuaj raws sijhawm, raws li tus kws kho mob tau hais, thiab mus rau chaw kho mob raws li hnub teem tseg.
Muaj tej lub sij hawm koj xav tias, "Auj, kuv tseem tsis tau laus txaus kom muaj kab mob plawv," tiam sis koj tseem mob hauv siab thiab ua pa nyuaj.Yog koj muaj ib qho ntawm cov hauv qab no, nco ntsoov mus ntsib kws kho mob. Tom qab phais rau Unicuspid Aortic Valve, koj yuav txuas ntxiv mus ntsib koj tus kws kho mob. Yog tias muaj teeb meem (xws li kev kis kab mob) tshwm sim tom qab phais, koj yuav xav tau kev kho mob ceev.
Koj yuav tsum nug tus kws kho mob li cas?
Thaum koj mus ntsib kws kho mob, tsis txhob ntshai nug tej lus nug uas koj muaj. Nov yog qee cov lus nug uas koj tuaj yeem nug tau:
- Kev kho mob zoo tshaj plaws rau kuv yog dab tsi?
- Qhov txawv ntawm ntau hom kev hloov pauv lub valve yog dab tsi? (piv txwv li, lub valve dag vs. biovalve)
- Kuv yuav tsum tau phais sai npaum li cas?
- Lub valve tshiab uas tau teeb tsa ntev npaum li cas?
Thaum koj hnov tias muaj qee yam hauv koj lub siab tsis ua haujlwm zoo, nws tsis yooj yim. Txawm li cas los xij, dhau sijhawm, cov kws kho mob tau tsim cov kev kho mob zoo dua rau qhov mob no. Tham nrog koj tus kws kho mob txog qhov zoo tshaj plaws rau koj. Vim tias qhov no yog ib qho mob tsis tshua muaj , nws yog qhov zoo tshaj plaws rau koj kom nrhiav tau tus kws kho mob uas muaj kev paub txog nws. Piv txwv li, cov kws tshawb fawb hais tias tus kws phais yuav tsum ua tsawg kawg 15 Ross cov txheej txheem ib xyoos.
Thaum kawg, qhov tseem ceeb tshaj plaws uas yuav tsum nco ntsoov (Cov Lus Qhia Coj Mus Tsev)
Zoo, yog li kuv vam tias koj tam sim no muaj kev nkag siab zoo txog tus kab mob plawv no hu ua '(Unicuspid Aortic Valve)' uas peb tau tham txog hnub no. Nco ntsoov, qhov no yog ib yam dab tsi uas yug los nrog thiab tsis tshua pom. Txawm li cas los xij, yog tias kuaj pom zoo thiab kho raws sijhawm, koj tuaj yeem ua neej zoo . Yog tias koj lossis ib tus neeg koj paub muaj cov tsos mob no, tsis txhob ntshai mus ntsib kws kho mob thiab tau txais kev qhia. Tshwj xeeb, nws yog ib qho tseem ceeb heev kom tau txais kev txhawb nqa ntawm pab pawg kws kho mob uas muaj kev paub dhau los thaum kho cov mob tsis tshua muaj no. Saib xyuas koj lub siab. Nws yog qhov khoom muaj nqis tshaj plaws hauv koj lub neej!
Kab Mob Plawv, Aortic Valve, Unicuspid Aortic Valve, Phais Plawv, Kab Mob Plawv Txij Thaum Yug Los, Ua Tsis Taus, Mob Hauv Siab











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Tsis muaj lus teb tau muab tso tawm. Ntxiv koj cov lus tawm ntawm no thawj zaug.
Ntxiv koj cov lus