Yu dɔn ɛva notis se sɔm pipul dɛn tit gɛt strenj kɔlɔ smɔl, sɔntɛm blu-grey kɔlɔ, ɔ yɔlɔ-brawn kɔlɔ? Ɔ yu gɛt tit we wik so dat i kin brok ɔ west ivin we yu it smɔl tin? Yu go tink se dat na nɔmal tin. כltu dis kin bi bak fכ wan rare kכndishכn we de apin we di tut de divεlכp we dεn kכl `(Dentinogenesis Imperfecta)`. Mek wi tok abaut dis likl bit tide, okay?
Wetin na `(Dentinogenesis Imperfecta)`? Lɛ wi ɔndastand am simpul wan, nɔto so?
Fɔ tɔk am simpul wan, `(Dentinogenesis Imperfecta)` na prɔblɛm we kin apin we di tit dɛn fɔm, dat na we di tit dɛn de gro. Wetin kin apin pan dis kes na dat yu tit kin wik bad bad wan ɛn brok izi wan . Lɛk biskit, if yu brok am ivin smɔl, i go brok. Dɔn bak, di tit dɛn fɔ pipul dɛn we gɛt dis sik kin shayn smɔl . Di kɔlɔ na bak, lɛk aw a bin dɔn tɔk , blu-grey ɔ yɔlɔ-brawn .
dis kכndyushכn we dεn kכl ``Dentinogenesis Imperfecta,'' kin afekt yu praymar tit dεm εn yu pεrmanεnt tit dεm . Dis min se di sayn dɛm kin bigin we dɛn yɔŋ, ɔr kin apin leta na layf.
Naw luk, we wi tek tut, i gɛt sɔm layers. di pat we de shayn, strכng pan tap dεn kכl am `(Enamel)`. dכn dכn dat `(Enamel)` wan כda layt de, we dεn kכl `(Dentin)`. dis `(Dentin)` pat na in de mεnli gi di tut trεnk εn kכla. wetin de apin na `(Dentinogenesis Imperfecta)` na dat di `(Dentin)` pat nכ de divεlכp fayn fayn wan. Wetin kin apin da tɛm de? biכs di `(Dentin)` wik, di `(Enamel)` we de pan tap nכ de atak di tut fayn fayn wan. Na dat mek di `(Enamel)` izi fɔ flɛk ɛn west.
Impɔtant: `(Dentinogenesis Imperfecta)` difrɛn frɔm `(Amelogenesis Imperfecta)`. insay `(Amelogenesis Imperfecta)`, di `(Enamel)` na di tut de afekt dairekt wan. insay `(Dentinogenesis Imperfecta)`, di prכblεm de na di `(Dentin)`.
Dɛn se dis na tin we nɔ kin apin so ɔltɛm . Bɔrku tɛm, dis sik kin apun pan lɛk wan pan ɔl 6,000 to 8,000 pipul dɛm.
Yu tink se ɛni kayn `(Dentinogenesis Imperfecta)` de?
yes, wi de tכk bכt tri men tכp dεm fכ `(Dentinogenesis Imperfecta)`. Lɛ wi si wetin dɛn bi.
1. `(Dentinogenesis Imperfecta)` Tayp 1 (Tayp I): Dis na spɛshal tin. biכs dis kayn kin apin wit wan sik we dεn kכl `(Osteogenesis Imperfecta)`. `(Osteogenesis Imperfecta)` na jכs sik we de mek di bon dεm rili fraylayz (brittle bon disease). So, wit dɛn tit prɔblɛm, dɛn pipul ya kin gɛt bon prɔblɛm bak. di rizin fכ dis na biכs sכm chenj dεm de na di `(Genes)` fכ di `(COL1A1)` כ `(COL1A2)` jin dεm. dεn tu jin dεm ya de εp fכ mek di protin `(Kכlagen)` insay wi bכdi.
2. `(Dentinogenesis Imperfecta)` Tayp 2 (Type II): Dis tכp de kכmכn pas pεrmanεnt tit dεm.I kin mɔs bi na di pikin in tit. Bɔku tɛm, dɛn pipul ya nɔ kin gɛt bɔku ɔda sik dɛn we dɛn kin gɛt frɔm dɛn mama ɛn papa. Bɔt dɛn dɔn si se sɔntɛnde, i kin izi fɔ mek pɔsin nɔ yɛri fayn bikɔs i dɔn ol .
3. `(Dentinogenesis Imperfecta)` Tayp 3 (Tayp III): Dis na di kayn we we nɔ kin bɔku . I kin afɛkt di tit dɛn we kin de sote go pas di pikin dɛn tit. Risach pipul dεm dכn ripot dis kayn mכst pan pipul dεm we kכmכt na Ju we dεn kכl `(Ashkenazi Jewish)`, εn insay sεvεra famili dεm we de na di sawt pat na Merilan.
Wetin na di sayn dɛm fɔ `(Dentinogenesis Imperfecta)`? Aw fɔ no am?
As a bin dɔn tɔk, di men tin dɛn we kin mek pɔsin gɛt kɔlɔ na we di tit kin chenj ɛn di tit we wik ɛn we kin brok . Bɔku tɛm, di tit dɛn kin shayn, ɛn dɛn kin gɛt yɔlɔsh-brawn ɔ blu-grey kɔlɔ .
Apat frɔm dat, yu kin si ɔda sayn dɛn bak lɛk:
- di pikin in tit dεm we de lכs let: di pikin in tit dεm de fכl leta pas aw i nכmal.
- Enamel Hypoplasia: Dis min se di enamel layεr we de na di tכp pan di tit dεm dכn lכs inof.
- Joint Hypermobility: Sɔm pipul dɛn kin bɛn dɛn joyn, lɛk dɛn finga ɛn ɛlb, bak ɛn go bak pasmak.
- Tut Agenesis: Dis min se dɛn bɔn yu we yu nɔ gɛt sɔm tit.
- Di tut inɛmel we wik: Di ɛnamel wik ɛn i kin west kwik kwik wan.
Jɔs tink bɔt, if yɔŋ pikin in bebi tit dɛn gɛt strenj kɔlɔ, dɛn gɛt bluish tint, ɔ dɛn kin brok izi wan, yu fɔ rili wɔri bɔt dɛn.
Wetin mek dis `(Dentinogenesis Imperfecta)` kin apin? Wetin na di kɔz?
Di men rizin fɔ dis na we wi jin dɛn chenj. in patikyula, wan chenj na di jin we dεn kכl `(DSPP) ` de mek `(Dentinogenesis Imperfecta). dis `(DSPP)` jin de gi di instrכkshכn fכ mek `(Dentin)`, di midul layεr fכ wi tit dεm. So we prכblεm de wit dis jin, `(Dentin)` nכ de fכm fayn fayn wan.
Dis jεnεtik vεryush כn kin kכmכt frכm mama εn papa , כ i kin apin randomly .
di wan dεm we gεt Dentinogenesis Imperfecta tayp 1, lεk aw a bin se, gεt mכtεshכn na di COL1A1 כ COL1A2 jin dεm. dis na di sem jεnεtik mכtεshכn dεm we dεn kin si bak pan dεn wan dεm we gεt Osteogenesis Imperfecta (wan sik we de mek dεn bon dεm brok).
Aw dɔktɔ dɛn kin no bɔt dis?
If yu ɔ yu pikin gɛt ɛni wan pan dɛn sik ya, yu fɔ go to dɛntist fɔs . Fɔs, i go du in bɔdi ɛgzam ɛn aks if ɛnibɔdi na yu famili dɔn gɛt ɛni wan pan dɛn sik ya..
Apat frɔm dat, if yu tink se yu gɛt Dentinogenesis Imperfecta, dɛn kin du dɛn tɛst ya fɔ kɔnfirm di sik:
- Fɔ tek ɛks-ray fɔ yu tit.
- Sɔntɛm yu kin du CT skan .
bay we di dכkta luk dεn imej dεm ya, i kin gεt gud aidia fכ di kכndishכn fכ di insay pan di tit dεm, di nεchכr fכ di ``Dentin''.
Sɔntɛnde, yu dɔktɔ kin se yu fɔ tɛst yu jɛnɛtiks fɔ no ustɛm di chenj dɛn we de apin na yu DNA kin mek yu gɛt dentinogenesis imperfecta.
Wetin na di tritmɛnt dɛm fɔ dis? (Tritmɛnt)
Di men tin we dɛn de pe atɛnshɔn pan fɔ tritmɛnt fɔ Dentinogenesis Imperfecta na fɔ mek di tit dɛn we wik strɔng . Dɛntist dɛn kin yuz difrɛn we dɛn fɔ mek dɛn tit bak fɔ du dis.
Fɔ ɛgzampul:
- Filin: Fil di gap ɛn krak krak na di tit.
- Vinɛs: Dɛn tin ya na tint shel dɛn we dɛn kin put na di fɔs pat pan di tut. Dɛn kin mek di tut fayn bak.
- Krawn: Krawn tan lɛk kap we dɛn kin put pan tut. I de kɔba di wan ol tut ɛn mek i strɔng.
Dɛn tritmɛnt ya kin yuz tin dɛn we gɛt tut kɔlɔ, so dat yu go ebul fɔ mek yu smayl fayn.
We yu gɛt Dentinogenesis Imperfecta, yu kin lɔs yu tit as yu de ol. If yu tit lɔs, yu kin put dɛn tit ɔ dɛnt fɔ chenj dɛn tit .
Us kayn op yu go gɛt we yu de liv wit dis sityueshɔn? (Autluk) .
Di we aw yu de si tin dipen pan bɔku tin dɛn:
- Yu ej we dɛn bin no se yu gɛt dis sik.
- Aw kwik yu bigin fɔ trit.
- Us kayn Dentinogenesis Imperfecta yu gɛt?
Di impɔtant tin na dat Dentinogenesis Imperfecta nɔ kin mɛn . Bɔt if yu kia fɔ yu tit fayn ɛn yu gɛt gud abit fɔ klin yu mɔt, yu kin ɛp fɔ mek yu tit nɔ pwɛl mɔ ɛn mek dɛn strɔng. Di kwik we dɛn no di sik ɛn trit am, na di mɔ i go fayn.
Yu tink se dɛn kin ebul fɔ mek dɛn nɔ gɛt Dentinogenesis Imperfecta?
I sɔri fɔ no se dɛn nɔ kin ebul fɔ stɔp Dentinogenesis Imperfecta bikɔs na di chenj dɛn we de apin na di jɛnɛtiks we wi nɔ ebul fɔ kɔntrol kin mek i apin. Bɔt if yu bigin tritmɛnt kwik kwik wan , dat kin mek yu nɔ pwɛl di tit fɔ lɔng tɛm.
Aw a kin tek kia ɔf mi tit? (We yu de kia fɔ yusɛf) .
If yu gɛt `(Dentinogenesis Imperfecta)`, gud ɔral hajɛns impɔtant.I impɔtant fɔ mek dɛn mek di say dɛn we dɔn pwɛl. Fɔ mek yu tut nɔ rɔtin ɛn nɔ pwɛl, du dɛn tin ya:
- Aks yu dɛntist bɔt di tritmɛnt dɛn we gɛt fluoride fɔ mek yu tit dɛn strɔng.
- Brush yu tit tu ɔ tri tɛm insay di de wit tut brɔsh we gɛt saf brist ɛn tut paste we gɛt fluoride .
- Limit it dɛn we gɛt shuga ɛn we gɛt asid.
- Rinse yu mɔt wit fluoride mɔt rins wan tɛm insay di de.
- Go to di dɛntist ɔltɛm fɔ mek dɛn chɛk am ɛn klin am .
Wetin gud fɔ it ɛn drink we yu gɛt `(Dentinogenesis Imperfecta)`?
Di bɛst tin fɔ du na fɔ pik it ɛn drink dɛn we nɔ gɛt bɔku shuga ɛn asid . Dis min se yu fɔ kɔt drink lɛk soda, sitrus frut lɛk laym, ɛn tomato sos as yu ebul. I fayn bak fɔ stɔp fɔ it tin dɛn we yu nid fɔ it ɛn we at ɔ we krach .
Na sɔm gud it dɛn fɔ it fɔ pɔsin we gɛt Dentinogenesis Imperfecta:
- Fish we dɛn dɔn bek
- Tayp dɛn fɔ Kasrɔl
- Vegjetabul dɛn we dɛn dɔn kuk
- Oatmil we dɛn kin mek
- Pasta wit krim-based sos
- Skrambl eg dɛn
- Smoothies we dɛn kin mek
Dis na it wae izi fɔ it ɛn nɔr de kɔz bɔrku damej pan yu tit.
Ustɛm a fɔ go to dɔktɔ?
If yu ɔ yu pikin notis ɛnitin we nɔ kɔmɔn ɔ we difrɛn bɔt dɛn tit, i go fayn fɔ tɛl yu dɔktɔ wantɛm wantɛm . Mɛmba se, di sayn dɛm fɔ DGI kin apia pan ɛni ej. If yu pikin in fɔs pikin tit dɛn tan lɛk blu, grey, ɔ brawn , mek shɔ se yu go to pikin dɛn dɛntist fɔ advays.
Us kwɛstyɔn dɛn yu fɔ aks di dɔktɔ?
If dɛn no se yu gɛt Dentinogenesis Imperfecta, yu kin aks yu dɔktɔ kwɛstyɔn dɛn lɛk:
- Us kayn `(DGI)` a gɛt?
- Us kayn tritmɛnt a nid?
- Aw lɔng di tritmɛnt dɛn go tek? Aw lɔng di tritmɛnt dɛn go las?
- Aw ɔltɛm a fɔ klin mi tit?
- Us tin dɛn we a kin du fɔ mek mi tut nɔ west ɛn nɔ pwɛl?
Fɔ dɔn sɔntin... (Tek-Home Message)
Fɔ gɛt wik tit we kin brok izi wan, kin rili mek yu vɛks. I kin taya bak fɔ gɛt fɔ tek tɛm ɛvri tɛm we yu de it. We yu gɛt `(Dentinogenesis Imperfecta)`, yu kin shem fɔ di we aw yu tit dɛn de luk. Bikɔs ɔf dis, yu nɔ go want fɔ fes di sosayti.
Bɔt mɛmba se nɔto yu wangren de.. Dɔktɔ dɛn de we go ɛp yu. Dɛn kin tɛl yu bɔt tritmɛnt fɔ mek yu tit strɔng, fɔ mek yu smayl fayn, ɛn fɔ mek yu gɛt kɔnfidɛns pan yusɛf. So, nɔ wɔri bɔt ɛnitin, ɛn fala yu dɔktɔ in advays.
If yu no di sik kwik kwik wan, gɛt di rayt tritmɛnt, ɛn fala gud abit fɔ klin yu mɔt, yu kin liv wɛl, gladi layf ivin wit di kɔndishɔn `(Dentinogenesis Imperfecta).'
` dentinogenesis imperfecta, tit sik, wik tit, tut dεm we de kכla, jεnεtik sik, tit hεlth, pikin tit











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