Yu dɔn ɛva notis wan smɔl bɔmp ɔ di kɔlɔ we de na yu skin? Sɔntɛnde, wi nɔ kin pe atɛnshɔn to am bɛtɛ, nɔto so? Bɔt sɔntɛnde ivin sɔntin we smɔl lɛk dis kin bi sɔntin we pɔsin fɔ wɔri bɔt. Tide, wi go tɔk bɔt wan kayn kansa na yu skin we nɔ kin bɔku bɔt we impɔtant. Dɛn kɔl am Dermatofibrosarcoma Protuberans , ɔ DFSP fɔ shɔt.
Wetin na DFSP (Dermatofibrosarcoma Protuberans)?
Fɔ tɔk am simpul wan, DFSP na wan kayn kansa na di skin we de gro sloslo, bɔt we nɔ kin bɔku. I kin bigin na di midul layt na wi skin, we na di dɛmis . Yu kin yɛri bak dɔktɔ kɔl am DFSP.
Bikɔs dis na kansa we de gro sloslo, i nɔ kin pas na ɔda pat dɛn na di bɔdi. Bɔt, i nɔ fayn fɔ lɛ wi nɔ pe atɛnshɔn to am. I rili impɔtant fɔ gɛt di rayt tritmɛnt ɛn pul dis tumbu. Na da tɛm de nɔmɔ dɛn go ebul fɔ mek di kansa stɔp fɔ kam bak (we i de kam bak) ɔ i go skata to ɔda pat dɛn na di bɔdi (mɛtastas kansa). If pɔrsin gɛt di rayt tritmɛnt, pɔrsin wae gɛt DFSP kin gɛt bɔrku chans fɔ wɛl.
Dis DFSP na jɔs wan tumbu? Ɔ na kansa?
Nɔ, DFSP nɔto jɔs wan benign tumor. Na wan bad bad sik. Fɔ tɔk di kɔrɛkt tin, na wan kayn kansa we gɛt sɔft tisu, we na wan kayn sɔft tisu sarkoma . Sarkoma na kansa wae de fכm na say dεm lεk mכsul, fεt, εn skin. Sɔntɛnde, dɛn kin afɛkt di bon dɛn bak.
DFSP kin spre (mεtastasayz) to כda pat dεm na di bכdi?
DFSP nɔ kin bi wan kayn kansa we kin skata kwik kwik wan ɔlsay na di bɔdi. Bɔt, na smɔl tɛm nɔmɔ, lɛk wan pan ɛvri 20 pipul dɛn we gɛt DFSP kin gɛt di kansa we go skata pas usay i bigin. Dɛn kɔl dis mɛtastas kansa .
Dis kin pas pasmak if dɛn nɔ trit am, ɔ if di kansa dɔn skata dip dip wan insay di skin, insay di fat tisu ɛn mɔsul.
כda tin na, pan כl we dεn nכ no di εksakεt kכz, if DFSP de divεlכp we uman bεlε, i kin bi mכr siriכs.
Dɔn bak, smɔl nɔmba pan pipul dɛn we gɛt DFSP kin gɛt wan kayn we we kin mek dɛn gɛt mɔ agresiv, we kin skata kwik kwik wan we dɛn kɔl fibrosarcomatous dermatofibrosarcoma protuberans (DFSP-FS) . Ivin if dεn כpכt dεn DFSP-FS tכmכro dεm ya, dεn kin kam bak εn kin spre to כda εria dεm.
Aw kכmכn dεn kכl dis kכndyushכn DFSP?
DFSP na wan kayn kansa we nɔ kin bɔku. Ɔlsay na di wɔl, na lɛk 4 pipul dɛn nɔmɔ de afɛkt pan ɛvri milyɔn pipul dɛn ɛvri ia. DFSP de akכnt fכ bitwin 1% εn 6% pan כl di sכft tisu sarkoma dεm.
Dis kansa kin kam pan big pipul dɛm wae ol bitwin 20 ɛn 50. Bɔt yɔŋ pikin dɛm kin gɛt dis kansa na dɛn skin bak. Sɔm pikin dɛn kin gɛt DFSP we dɛn bɔn dɛn. Risach dɔn sho se blak pipul dɛn kin gɛt am smɔl pas pipul dɛn we kɔmɔt na ɔda trayb.
Wetin na di men kayn DFSP dɛn?
Pathologist, dכkta dεm we de egzamin di bכdi tisu dεm כnda maykroskכp, kin tεl yu εksεkshכn us kayn DFSP yu gεt bay we dεn de egzamin di sεl dεm. Bɔku men kayn dɛn de:
- Bednar tumor (we dεn kכl bak pigmented DFSP): dεn kayn sεl dεm ya gεt bכku melanin , di pigment we de gi di skin in kכla. Dis na di rizin we mek dɛn tumbu ya kin apia wit difrɛn kɔlɔ dɛn lɛk rɛd, brawn, blu, ɛn pepul. Dis kayn de mek lɛk 5% pan di DFSP diagnosis dɛm.
- Jaynt sel fibroblastoma: Dis kayn we de sho se jayant sεl dεm de. Dɛn kin kɔl dis kayn tin bak juvenile DFSP bikɔs i kin apin mɔ pan pikin ɛn yɔŋ pipul dɛn.
- Fibrosarcomatous dermatofibrosarcoma protuberans (DFSP-FS): As wi bin dɔn tɔk, dis na wan kayn sɔft tisu sarkoma we rili agresiv, we de skata kwik kwik wan.
- di myxoid DFSP dεm: dεn mek dεm wit wan abnכmal tכp kכnektiv tisu we dεn kכl myxoid stroma. Dis kayn DFSP nɔ kin bɔku.
Wetin kin mek DFSP?
I sɔprayz fɔ no se 9 pan ɛvri 10 pipul dɛn we gɛt DFSP gɛt wan jɛnɛtik muteshɔn we kin mek dɛn gɛt dis sik . dis jin mכtεshכn de apin na wi sεl dεm afta dεn bכn wi. Dis min se DFSP nɔto bikɔs ɔf wan jenɛtik difrɛns we wi mama ɛn papa gɛt.
Wetin na di risk factor dɛm fɔ divɛlɔp DFSP?
Apat frɔm di rays, fɔ gɛt ɛni kayn injuri ɔ skata na yu skin kin mek yu gɛt DFSP. Bɔku we dɛn de we di skin kin wund:
- Bɔn dɛn
- We dɛn de du redyushɔn tɛrapi
- Di say dɛn we dɛn kin kɔt di bɔdi we dɛn kin du ɔpreshɔn
- Tatu dɛn we dɛn kin mek
Imajin se yu dɔn ɛva bɔn bad bad wan ɛn big skata. Ɔ, yu dɔn gɛt redyushɔn tritmɛnt fɔ ɔda sik. we tin dεm lεk dis dεn dכn pwεl di skin, sכm chans de fכ mek wan kכndyushכn lεk DFSP go divεlכp insay di fכs tεm, pan כl we i nכ kin apin sכmtεm. Na dat mek wi fɔ no ɔltɛm bɔt di chenj dɛn we de apin na di skin.
Wetin na di sayn dɛm fɔ DFSP?
Di fɔs sayn dɛm fɔ DFSP kin so klia dat wi nɔr kin notis dɛm ɔr ivin si dɛm. Dɛn tumbu ya kin apin mɔ na di chɛst, bak, sholda, bɛlɛ, ɔ di bɔdi. Dɛn kin kam bak na di an, leg, skel, ɛn insay di mɔt.
Fɔs, yu kin si wan smɔl say we tan lɛk brus na di skin.I flat ɛn i nɔ de mek pɔsin fil pen. I kin fil lɛk se i rɔf smɔl we yu tɔch am, ɛn di kɔlɔ kin chenj smɔl.
pan bebi dεm εn yכŋ pikin dεm, DFSP kin luk lεk bכn mak . Dɛn spat ya kin waid lɛk af inch to tu inch (1 to 5 sɛntimita).
Di simptom dɛm fɔ DFSP kin bi klia as di kansa de gro. as di tכmכro de gro, i de push insay di tכp layεr na di skin (epidamis). Dis kin mek had lump (nodul) de apia na di skin . Di wɔd "protuberance" min "protruding."
Yu kin si dɛn sayn ya na dɛn bɔmp ya:
- I kin krak ɔ blɔd izi wan.
- i tay fayn fayn wan pan di skin (dεn nכ kin muv am rawnd).
- As yu de ol, yu skin de strɛch.
- I kin fil at fɔ tɔch, ɔ lɛk rɔba.
- Di kɔlɔ kin bi rɛd-brawn, pepul, blu, ɔ rɛd.
- I kin tan lɛk se i tan lɛk smɔl we yu tɔch am.
Ɔda tin dɛn de we kin mek pɔsin gɛt sayn dɛn we fiba DFSP?
Yɛs, wan sik de we nɔ gɛt kansa na di skin we dɛn kɔl sɛlular dɛmatofibroma . Dis kin luk rili fiba DFSP, mɔ we i de bigin. Sεlyul dεrmatofibromas na benign sכft tisu tכmכro dεm. Dɛn kin apin mɔ na di leg dɛn. Sɔntɛnde, dɛn kin it ɛn mek dɛn fil pen. Mɔs pan di dɛmatofibromas nɔ nid tritmɛnt. Bɔt i fayn fɔ mek yu nɔ kɔnfyus dɛn tu tin ya, so i go fayn fɔ go to dɔktɔ if yu notis ɛni nyu tin na yu skin.
Aw dɛn kin no se dɛn gɛt DFSP (Dermatofibrosarcoma Protuberans)?
DFSP na dermatologists , we na dɔktɔ dɛn we gɛt spɛshal trenin fɔ kansa na di skin ɛn sik dɛn na di skin. Yu dɔktɔ go fɔs tek smɔl sampul pan di skin lump ɔ spat ɛn sɛn am to lab fɔ tɛst (wan skin biopsy) . Dɛn kin pul di wan ol lump ɛn sɛn am na lɛb. Dɔn di wan dɛn we de stɔdi bɔt di sik go luk di tisu ɔnda maykroskɔp fɔ si if i gɛt kansa sɛl dɛn.
If di skin bayɔpsi kɔnfyus se yu gɛt DFSP, dɛn kin aks yu fɔ du MRI skan . Dis go ɛp fɔ no di rayt saiz fɔ di tumbu ɛn aw dip i dɔn spre insay di skin. Dis infɔmeshɔn rili impɔtant fɔ plan tritmɛnt.
Wetin na di tritmɛnt fɔ DFSP (Dermatofibrosarcoma Protuberans)?
di men εn bεst tritmεnt fכ DFSP na fכ pul di tכmכro wit כpεrayshכn. Di dɔktɔ dɛn we de mɛn di bɔdi kin yuz wan spɛshal we we dɛn kɔl Mohs ɔpreshɔn fɔ pul di DFSP tɔŋ dɛn. Na dis na wetin kin apin we dɛn de du dis ɔpreshɔn:
- Fɔs, dɛn kin injɛkt wan lokal anestetik na di say we dɛn de trit yu, so dat yu nɔ go fil ɛni pen.
- Dɔn, di dɔktɔ kin kɔt di tumbu we gɛt kansa ɛn pul am. Bɔt nɔto di tumbu nɔmɔ, bɔt na smɔl eria we gɛt wɛlbɔdi skin rawnd am. Dɛn kɔl dis di margin .
- nεks, dεn de egzamin di ed dεm (bכda dεm) fכ di tisu we dεn pul כnda maykroskכp fכ si if εni kεnsar sεl dεm stil de.
- If kansa sɛl dɛn stil de na di ed dɛn, di dɔktɔ go pul sɔm mɔ tisu dɛn na di say we dɛn du di ɔpreshɔn bak.
- dis we ya, dεn de kכntinyu fכ pul di tisu te dεn nכ fכnshכn kεnsar sεl dεm na di margin dεm.
- Afta dɛn dɔn pul di kansa kpatakpata, dɛn kin du ɔpreshɔn fɔ mek di kansa bak if nid de.
Ɔda tritmɛnt dɛn de fɔ DFSP we nɔ gɛt ɔpreshɔn?
Ivin if dɛn du ɔpreshɔn fɔ pul di DFSP tumbu dɛn, sɔntɛnde dɛn kin kam bak. afta wan tipik waid εksizishכn, 20% to 30% chans de fכ mek dεn kam bak insay tri ia. Afta Mohs ɔpreshɔn, dis risk kin ridyus to 4% to 5%. Bɔt i impɔtant fɔ de wach, bikɔs di tumbu kin kam bak ivin 10 ia ɔ mɔ afta dat.
Sɔntɛnde, if di kansa dɔn skata to ɔda pat dɛn na di bɔdi (metastatic DFSP), ɔ if di tumbu tu big ɔ tu say fɔ pul am fɔ ɔpreshɔn, dɔktɔ dɛn kin yuz wan mɛrɛsin we dɛn kɔl Imatinib . Dis drɔg kin mek di tumbu smɔl bak, ɛn dis kin mek i izi fɔ pul am we dɛn de du ɔpreshɔn.
Dɔn bak, if ɔpreshɔn nɔ ebul fɔ pul di kansa kpatakpata, ɔ if ɔpreshɔn nɔ pɔsibul atɔl, dɛn kin yuz redyushɔn tɛrapi .
Wetin na di lukin-grɔn fɔ pɔsin we gɛt DFSP?
Dis na nyus we rili kɔrej wi. Bikɔs DFSP na kansa we de gro sloslo, we nɔ de wok, wit di rayt tritmɛnt, pas 99% pan pipul dɛn go liv fɔ 10 ia ɔ mɔ. So, di tin we impɔtant pas ɔl na fɔ nɔ panik ɛn fala yu dɔktɔ in advays.
Wetin a go du fɔ mek a tink gud wan?
Bɔku tin dɛn de we yu kin du fɔ mek yu tink gud wan:
- Du yu skin sɛlf-ɛgzam ɔltɛm. Luk fɔ ɛni nyu chenj, spat, ɔ lumps na yu skin. If yu notis ɛnitin, tɛl yu dɔktɔ wantɛm wantɛm.
- Afta yu dɔn gɛt tritmɛnt, go to yu dɔktɔ fɔ chɛk yu skin at le ɛvri tri to siks mɔnt fɔ di fɔs tri ia. Dɔn go fɔ chɛk-ap wan tɛm insay di ia, ɔ lɛk aw yu dɔktɔ tɛl yu.
- Nɔ mek di san nɔ bɔku. UV rayt we de kɔmɔt na di san kin mek pɔsin gɛt ɔda kansa dɛn na di skin. So, wɛr sanskrin we yu de go na do na di san, wɛr klos we go protɛkt yu , ɛn nɔ spɛn bɔku tɛm fɔ de na do di tɛm we di ples kin wam pas ɔl.
Ustɛm a fɔ go to dɔktɔ?
If yu notis ɛni nyu chenj na yu skin, mɔ if yu gɛt ɛni wan pan dɛn tin ya, mek shɔ se yu go to dɔktɔ:
- Nyu, bɔmp ɔ spat we nɔ de dɔn, ɔ nyu skin we de gro.
- Chenj na di wɔt, bɔn mak, ol skata, ɔ tatu.
- If di bɔmp dɛn we de na di skin de blɔd izi wan.
Mɛmba se bɔku tɛm, we pɔsin chenj in skin, i nɔ kin ambɔg am. Bɔt sɔm chenj dɛn kin bi sayn fɔ gɛt kansa na yu skin. So, if yu gɛt ɛni dawt, i bɛtɛ fɔ go to dɔktɔ fɔ mek dɛn sɔlv am.
Wetin a fɔ aks mi dɔktɔ?
If dɛn no se yu gɛt DFSP, yu kin aks yu dɔktɔ kwɛstyɔn dɛn lɛk:
- Wetin mek a gɛt dis kansa na mi skin?
- A de pan denja fɔ gɛt ɔda kayn kansa na mi skin?
- Wetin na di bɛst tritmɛnt fɔ mi?
- Risk de fɔ mek dis kansa go na ɔda pat dɛn na di bɔdi?
- Aw ɔltɛm a fɔ kam fɔ mek dɛn chɛk mi kansa?
If yu no di ansa to dɛn kwɛstyɔn ya, dat go ɛp yu fɔ ɔndastand di sik fayn fayn wan ɛn i go ɛp yu fɔ no klia wan bɔt yu tritmɛnt ɛn di tin dɛn we yu go plan fɔ du tumara bambay.
Fɔ dɔn, tin dɛn we wi fɔ mɛmba
Pan ɔl we DFSP na kansa we nɔ kin bɔku na di skin, i nɔ kin izi fɔ mek i go ɔda pat dɛn na di bɔdi. Bɔt i impɔtant fɔ mek dɛn nɔ gɛt ɔpreshɔn fɔ mek i nɔ gro. If yu no am kwik ɛn trit yu di rayt we, dat kin rili ɛp yu fɔ si tin. So, tek tɛm wit yu skin ɛn go to dɔktɔ if yu notis ɛnitin we nɔ kɔmɔn. Nɔto yu wan de, ɛn dɔktɔ dɛn de we go ɛp yu fɔ du dis waka.
` DFSP, skin kansa, skin kansa, skin lumps, Mohs ɔpreshɔn, kansa simptom, skin sik











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