Yu dɔn ɛva fil wan smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl smɔl. Sɔntɛm i bin apin afta we dɛn dɔn wok fayn fayn wan. Yu dɔn ɛva ɛkspiriɛns sɔntin lɛk dis? So, na wan sik wae yu nɔr no bɔt wae kin impɔtant to yu.
Wetin na Eosinophilic Fasciitis?
Fɔ tɔk am simpul wan, Eosinophilic Fasciitis na wan kɔndishɔn we di tisu we de kɔba wi mɔsul ɛn tisu dɛn we de ɔnda wi skin – we wi kɔl am fascia insay mɛrɛsin – wantɛm wantɛm i kin inflam, tik, ɛn tayt. Tink bɔt am lɛk di mɛsh we de ol wi skin ɛn mɔsul dɛn togɛda ɛn ɛp dɛn fɔ muv rawnd, jɔs lɛk di mɛsh we wi kin put na di trɔnk na wi motoka we wi de go shop.
Dɛn kin klas dis as `ɔtoimyun sik` . Dis min se di difɛns sistɛm we wi bɔdi de fɛt, we na di imyun sistɛm, kin mistek bigin fɔ atak di pat dɛn we gɛt wɛlbɔdi na wi yon bɔdi. I tan lɛk se wi de atak wi yon famili mɛmba dɛn we dɛn tink se dɛn dɔn tif dɛn.
If dɛn nɔ no am ɛn trit am kwik, i kin mek di skin chenj fɔ ɔltɛm ɛn i kin mek di jɔyn dɛn nɔ ebul fɔ muv igen . So, i rili impɔtant fɔ go to dɔktɔ jɔs lɛk aw di sik dɔn sho.
Aw dis tin kin afɛkt mɔ? Udat dɛn i kin afɛkt?
Eosinophilic Fasciitis kin afɛkt di fascia ɛnisay na di bɔdi, bɔt i kin afɛkt di an ɛn fut mɔ . Fɔ bɔku pipul dɛn, di sayn dɛn lɛk pen ɔ swɛlin, kin fɔs apia afta dɛn dɔn du ɛksɛsayz tranga wan ɔ dɛn dɔn du wok we dɛn fɔ tinap ɔl di de.
Dɛn sayn ya lɛk we yu de fil pen na yu mɔsul ɛn swɛlin kin tan lɛk ɔda sik dɛn we yu kin gɛt, so i impɔtant fɔ go to dɔktɔ wantɛm wantɛm if yu notis ɛni nyu chenj ɔ pen na yu skin, mɔsul, ɔ jɔyn dɛn. Yu kin nid bak fɔ go to dɔktɔ we de mɛn yu bɔdi, dɔktɔ we spɛshal pan jɔyn ɛn ɔda sik dɛn we kin mek yu bɔdi wam.
Naw, no mɛrɛsin nɔ de fɔ dis sik. Bɔt di gud nyus na dat fɔ bɔku pipul dɛn, di sik kin dɔn insay sɔm ia, we min se di sik kin go na `rɛmishɔn`, ɔr wan stet we dɛn kin slip. Bɔt sɔm pipul dɛn kin gɛt dis sik bak.
Difrɛns Bitwin Eosinophilic Fasciitis ɛn Scleroderma
We dɛn de tɔk bɔt dɛn tu sik ya, sɔm pipul dɛn kin kɔnfyus dɛn wit ɔda sik we dɛn kɔl `Scleroderma`. `Eosinophilic Fasciitis` εn `Scleroderma` dεn tu na dεn tu sik dεm we rili rare `autoimmune`. Dɔn bak, pan dɛn tu sik ya, di tisu dɛn na di bɔdi kin tik ɛn stif.
So wetin na di difrɛns? di difrεns de pan di kayn tisu dεm we dεn afekt.
- insay Eosinophilic Fasciitis, lεk aw wi bin dכn tכk bכt, di fascia, we na wan tin, εlastik kכnektiv tisu we de dכn di skin, de afekt. As tεm de go, dis fascia de tik εn i de pan, we de mek i at fכ muv di pat na di bכdi we afekt.
- bכt insay `Scleroderma`, di imyun sistεm de mek כda sεl dεm fכ prodyuz mכr protin we dεn kכl `kolagen` (sכmtin we de gi trεnk to wi skin εn tisu dεm). dis kolagen we pasmak de put insay di skin εn di insay כgan dεm, we de mek dεn tik εn at, lεk ol ska. Bɔt instead fɔ mɛn wund, dis kolagen we pasmak kin pwɛl di wɛlbɔdi tisu bak.
Eosinophilic Fasciitis ɛn KƆvid-19
Dɛn kin tek pipul dɛn we gɛt ɔtoimyun sik lɛk Eosinophilic Fasciitis as dɛn kin gɛt smɔl ay risk fɔ gɛt COVID-19 pas di jenɛral pipul dɛn.
Di masta sabi pipul dɛn stil nɔ shɔ if pipul dɛn we gɛt dis sik kin gɛt siriɔs sik frɔm COVID-19. So, i bɛtɛ fɔ fala wetin di wan dɛn we de wok fɔ di wɛlbɔdi biznɛs, lɛk di Sɛntral fɔ Kɔntrol ɛn Prɛvenshɔn fɔ Sik (CDC) dɔn tɛl yu fɔ protɛkt yusɛf frɔm di sik.
Udat kin gɛt dis sik pas ɔlman?
Eosinophilic Fasciitis kin afɛkt ɛnibɔdi, bɔt i kin afɛkt pipul dɛn we ol bitwin 30 ɛn 60 ia.
Apat frɔm dat, pipul dɛm wae gɛt sɔm kayn wɛl bɔdi sik kin gɛt dis sik. Sɔm pan dɛn tin ya na:
- Aplastic anemia (aplastic anemia - na wan anemia we di blɔd sɛl dɛn we de mek di blɔd sɛl dɛn de go dɔŋ) .
- Hemolytic anemia (na wan anemia we di rɛd blɔd sɛl dɛn kin brok kwik kwik wan) .
- Limfoma (kansa na di limfatik sistɛm) .
- Lukimiya (kansa na di blɔd sɛl) .
- Sɔm kayn `Thyroid disease`
Aw kɔmɔn tin dis?
Eosinophilic Fasciitis na rili wan sik we nɔ kin bɔku . Te naw, na smɔl pipul dɛn nɔmɔ we gɛt di sik, we na lɛk 300, dɛn dɔn ripɔt na sayɛns magazin dɛn ɔlsay na di wɔl. Bɔt sɔntɛm bikɔs dɛn nɔ no di sik ɔ dɛn nɔ kin ripɔt bɛtɛ, di nɔmba fɔ di wan dɛn we gɛt di sik kin bɔku pasmak.
Aw Eosinophilic Fasciitis de afɛkt mi bɔdi?
as wi bin dכn tכk bכt, dis kכndyushכn de kכz fכ inflameshn na di fascia, we na wan tin, fleksibul kכnektiv tisu dεm we de dכn di skin. dis layt fכ fascia de kכba εn protεkt wi mכsul dεm εn sכm insay כgan dεm. I de ol di skin ɛn di mɔsul dɛn bak ɛn sɔpɔt dɛn we dɛn de muv.
Tink bɔt am, dis fascia de ɛp fɔ mek wi an ɛn fut dɛn ebul fɔ chenj, bɔt nɔto jɔs fɔ hang dɔŋ. bכt pan pכsin we gεt `Eosinophilic Fasciitis`, dis fascia mεmbran de inflam, sכmtεm i de tik, εn i de stif. Dɔn, dis inflamɛns kin mek i nɔ izi fɔ muv di skin ɛn di mɔsul dɛn we de rawnd am. If dɛn nɔ trit dis fascia, i kin stɔp na wan ples ɛn tayt. Sɔntɛnde dɛn kin kɔl dis `kɔntrakt`. Dat min se, wan kɔndishɔn we wan jɔyn nɔ kin ebul fɔ ɛkstɛnd ɔ bɛn.
insted fכ di nכmal elastik fכ di fascia, di pat dεm na di bכdi we afekt kin fil pen כ i at fכ muv.
Di pat dɛm na di bɔdi we kin afɛkt mɔ na:
- An (especially di palm, dat na di insay pat pan di an) .
- Leg (especially di front, rayt na di hip bon) .
- Jɔyn ɔ di say dɛn we de rawnd am
Pan ɔl we dis sik nɔ kin apin so ɔltɛm, i kin afɛkt di skin bak na di fes, chɛst, ɛn bɛlɛ.
Sɔm pasɛnt dɛn we gɛt Eosinophilic Fasciitis kin gɛt jɔyn inflamɛns bak we fiba Rheumatoid Arthritis. If dɛn nɔ kɔntrol dis jɔyn inflamɛns, di katilej we de na di jɔyn dɛn kin pwɛl, we kin mek pɔsin gɛt at at fɔ lɔng tɛm.
Dɔn bak, if dis sik afɛkt di fascia na yu an ɔ yu an, di inflamɛns kin mek di midyan nɛv, we na wan pan di men nerv dɛn na di an, kɔmprɛs, ɛn dis kin mek yu gɛt wan sik we dɛn kɔl Carpal Tunnel Syndrome (we yu nɔ gɛt bɛtɛ trɛnk, yu kin fil pen, ɛn yu kin wik).
Di impɔtant tin na dat Eosinophilic Fasciitis na wan sik we kin chenj ɛn divɛlɔp kwik kwik wan. Yu kin bigin fɔ notis di tin dɛn we yu kin si insay shɔt tɛm, lɛk sɔm wiks. So, if yu notis ɛni sayn ɔ chenj na yu bɔdi, go to dɔktɔ wantɛm wantɛm.
Wetin na di sayn dɛm fɔ Eosinophilic Fasciitis?
So, aw yu fɔ saspek dis sik? Na sɔm pan di men sayn dɛm wae de sho se yu gɛt dis sik:
- Mɔsul dɛn kin pen .
- Tɛnda skin.
- Inflameshɔn ɔ swel .
- di simptom dεm fכ `Carpal Tunnel Syndrome` (lεk fכ sכm, pen, wik na di an).
- Atraytis (atraytis - joyn de swel, pen, stiffness na mɔnin).
- Di skin kin fil tik ɛn tayt pas aw i kin fil.
- na sכm εria dεm, di skin kin luk pכk εn rכf, lεk di sεl fכ כrεnj (`puckered skin` כ "peau d'orange" apinans).
Wetin na di rizin fɔ dis?
Fɔ tɔk tru, masta sabi pipul dɛn stil nɔ no di rayt tin we kin mek pɔsin gɛt Eosinophilic Fasciitis. Lɛk bɔku sik dɛn we pɔsin kin gɛt we i de fɛt insɛf, i kin kam wantɛm wantɛm, sɔntɛnde fɔ no rizin.
כltu, sכm stכdi dεn fכnshכn se dεn כtoimyun sik ya kin ``trigεr`` bay sכm tin dεm. Dat min se, dis sik kin kam bikɔs ɔf ɔda tin. Fɔ ɛgzampul:
- Sɔm kayn infekshɔn dɛn .
- Sɔm alɛji riakshɔn dɛn.
- Yuz sɔm mɛrɛsin dɛn .
- Yuz sɔm drɔgs dɛn .
Sɔm pipul dɛm wae gɛt Eosinophilic Fasciitis se dɛn fɔs simptom kin apin afta dɛn dɔn du bɔku tin fɔ du , lɛk fɔ rɔn, fɔ es wet, ɔr fɔ du ɛksɛsayz, ɔr wae dɛn de du wok wae nid fɔ tray tranga wan pan dɛn an ɔr leg.
I fayn fɔ tɔk to yu dɔktɔ bɔt yu risk factor fɔ gɛt ɔtoimyun sik lɛk dis.
Aw dɔktɔ dɛn kin no bɔt dis sik? (Diagnosis) .
If yu gɛt dɛn sik ya, dɔktɔ kin du sɔm tɛst fɔ no if yu gɛt Eosinophilic Fasciitis:
1. Fascia Biopsy: Bayopsi na we yu dɔktɔ tek smɔl sampul pan yu tisu ɛn sɛn am to lab fɔ luk am ɔnda maykroskɔp. Dis involv fɔ tek smɔl pat pan di skin we afɛkt ɛn di fascia we de ɔnda am ɛn chɛk am. Bɔrku tɛm, dis na di we we pɔsin kin abop pan fɔ no di sik.
2. Blɔd tɛst: If yu gɛt Eosinophilic Fasciitis, yu kin gɛt ay lɛvɛl pan wan kayn wayt blɔd sɛl we dɛn kɔl Eosinophils na yu blɔd (na de di sik gɛt in nem). Bɔt, blɔd tɛst nɔmɔ nɔ go ebul fɔ no if pɔsin gɛt di sik. Bɔku tɛm, dɛn kin nid fɔ tek bayɔpsi.
3. Imej tεst: tεst lεk MRI (Magnetic Resonance Imaging) kin εp fכ no di inflameshn insay di bכdi, spεshal wan na di fascia εn di tisu dεm we de rawnd. Bɔt lɛk blɔd tɛst, dɛn nɔ kin spɛshal lɛk bayɔpsi fɔ no di sik.
Tritmɛnt fɔ Eosinophilic Fasciitis
Na smɔl tɛm nɔmɔ, di sayn dɛm kin go fɔ dɛnsɛf if dɛn nɔr gɛt ɛni tritmɛnt. Bɔt bɔku tɛm, dɔktɔ dɛn kin trit Eosinophilic Fasciitis wit wan kayn mɛrɛsin we dɛn kɔl kɔtikosterɔyd . Dis na wan kayn stɛroyd.
di kכtikostεroyd dεm de wok bay we dεn de ridyus di inflameshn na di bכdi εn sכpres di כva aktiv imyun sistεm. Prɛdnison na di kɔtikosterɔyd we dɛn kin gi mɔ.
Yu dɔktɔ kin gi yu ɔda tritmɛnt dɛn bak apat frɔm kɔtikosterɔyd, lɛk:
- `NSAID`: Nɔn-steroidal anti-inflammatory drugs (NSAID) we de na di famasi – fɔ ɛgzampul, ibuprofen ɛn diclofenac – kin ridyus di simptom dɛm lɛk pen ɛn swel. Bɔt if yu dɔn ɔlrɛdi de tek `kɔtikosterɔyd`, tɔk to yu dɔktɔ bifo yu tek `NSAID`. Nɔ tek `NSAIDs` fɔ pas 10 dez wan tɛm if yu dɔktɔ nɔ gri fɔ tek am.
- Mεdikeshכn dεm we de sכpres di imyun sistεm: Dipכnt pan aw yu kכndyushכn siriכs, yu dכkta kin gi yu כda mεdikeshכn dεm (e.g., Methotrexate) we de sכpres di כva aktiv imyun sistεm we de mek yu gεt Eosinophilic Fasciitis.
- Fizik tritmɛnt: Fizik tritmɛnt kin ɛp fɔ strɛch ɛn lɔs yu fascia we i tayt, ɛn ɛp fɔ mek yu jɔyn dɛn kɔntinyu fɔ muv. Yu dɔktɔ ɔr fizik thɛrapist go tich yu fɔ du ɛksɛsayz ɛn strɛch wae fayn fɔ yu sayn dɛm.
- Fɔ trit ɔda sik dɛn: Yu kin fil fayn if yu trit di sayn dɛm fɔ ɔda sik dɛm, lɛk carpal tunnel syndrome ɔr at at sik.
- Ɔpreshɔn: If yu Eosinophilic Fasciitis siriɔs fɔ mek yu gɛt kɔntrakt, yu kin nid fɔ du ɔpreshɔn fɔ rilis ɔ pul pat pan yu fascia (fascial release). Bɔku tɛm, dis na las tin we dɛn kin du.
Aw fɔ kɔntrol di sayn dɛm?
- I rili impɔtant fɔ tek di mɛrɛsin jɔs lɛk aw di dɔktɔ se, fɔ di tɛm we dɛn tɛl yu fɔ tek am.
- If yu dɔktɔ ɔr fyzikal tritmɛnt gi yu strɛch ɔ ɔda ɛksesaiz, du am bɔku tɛm lɛk aw dɛn tɛl yu fɔ ɛp fɔ strɛch di fascia we dɔn afɛkt. Pan ɔl we dis kin tranga, i kin bɛnifit yu if yu kɔntinyu fɔ du dɛn.
- If yu gɛt Carpal Tunnel Syndrome, yu kin nid fɔ wɛr bres fɔ mek yu an de na in ples we yu de slip. Yuz am lɛk aw yu dɔktɔ tɛl yu fɔ du am.
Aw kwik a go fil fayn afta dɛn dɔn trit mi?
di inflameshn we Eosinophilic Fasciitis de mek fכ bigin fכ sכb insay fכ awa afta dεn tek di fכs doz fכ kכtikostεroyd. Dis rilif kin bi fɔ sɔm tɛm, ɛn di sayn dɛn kin kam bak as di mɛrɛsin de west. So, i impɔtant fɔ tek di mɛrɛsin fɔ di ful tɛm we yu dɔktɔ tɛl yu fɔ tek.
Yu tink se dɛn kin ebul fɔ protɛkt Eosinophilic Fasciitis?
Bɔt i sɔri fɔ no se, no patikyula we nɔ de fɔ mek dɛn nɔ gɛt dis sik. Di masta sabi pipul dɛm nɔr no bɛtɛ bɛtɛ wan wetin kin mek yu gɛt ɔtoimyun sik ɔ aw dɛn kin kam, so dɛn nɔr kin ebul fɔ tɔk ustɛm ɔr wetin mek yu go gɛt wan.
Wetin pɔsin we gɛt dis sik fɔ ɛkspɛkt?
If dɛn no se yu gɛt Eosinophilic Fasciitis, yu fɔ ɛkspɛkt fɔ manej yu sik fɔ sɔm tɛm. If yu notis ɛni chenj na yu sik, mɔ if dɛn de wɔs, tɔk to yu dɔktɔ wantɛm wantɛm.
As wi don tok bifo, no mɛrɛsin nɔ de fɔ dis. Bɔrku pipul kin liv wit am fɔ sɔm ia, dɔn de sik kin go (go insay `rɛmishɔn`). Sɔm pipul nɔr kin ɛva gɛt am igen, bɔt ɔda pipul kin gɛt sɔm kayn sik kam bak leta (`recur`).
Yu nɔ go ebul fɔ go wok ɔ skul?
If yu kin du yu wok ɔ skul wok we yu nɔ put tumɔs strɛs pan yu fascia we dɔn afɛkt, yu fɔ ebul fɔ go bak na wok ɔ skul te yu wɛl frɔm Eosinophilic Fasciitis. Bɔt yu dɔktɔ go tɛl yu wetin yu fɔ avɔyd te yu wɛl. I impɔtant fɔ fala dɛn instrɔkshɔn ya.
Mek shɔ se yu tɔk to yu dɔktɔ ɛn gɛt rayt bifo yu bigin fɔ du tin dɛn we yu kin du we yu de du bɔku bɔku tin dɛn lɛk fɔ rɔn, fɔ es wet, ɔ fɔ du ɛksɛsayz.
Ustɛm yu fɔ go to dɔktɔ?
- If yu notis ɛni nyu sayn na yu an, fut, ɔr jɔyn – mɔ if yu gɛt pen ɔ swel we nɔ de go afta sɔm dez we yu dɔn rɛst – go to dɔktɔ wantɛm wantɛm.
- If dɛn dɔn ɔlrɛdi no se yu gɛt Eosinophilic Fasciitis, tɛl yu dɔktɔ wantɛm wantɛm if yu sik dɛn de wɔs, ɔ if yu notis se ɛni pat na yu bɔdi de stif ɔ nɔ de fil fayn.
Ustɛm yu fɔ go na Imejɛnsi Tritmɛnt Yunit (ETU) ?
If yu nɔ ebul fɔ muv ɔ yuz wan pat na yu bɔdi wantɛm wantɛm, ɔ if yu fil pen we yu nɔ go ebul fɔ bia, go na di imejensi rum we de nia yu wantɛm wantɛm .
Us kwɛstyɔn dɛn yu fɔ aks di dɔktɔ?
We yu go si dɔktɔ, yu kin aks kwɛstyɔn dɛn lɛk dɛn wan ya:
- A gɛt Eosinophilic Fasciitis, ɔ na ɔda tin?
- Aw kwik mi sik kin wɔs?
- Us kayn tritmɛnt a nid? Aw lɔng a go nid tritmɛnt?
- Yu tink se a go nid ɔpreshɔn?
- Ustɛm a go ebul fɔ du di nɔmal bɔdi wok bak?
- Aw dis tin kin afɛkt mi ɛvride layf?
Sɔm pan di impɔtant tin dɛn we wi nid fɔ mɛmba frɔm dis stori na
Eosinophilic fasciitis na wan sik wae nɔr kin bɔrku bɔt wae kin gɛt siriɔs sik wae kin afɛkt yu kwik kwik wan. If yu notis nyu pen, swel, ɔ tayt na yu an ɔ fut, mɔ if i nɔ go insay sɔm dez, nɔ delay fɔ go to dɔktɔ. Bikɔs dis sik kin kam kwik kwik wan , di mɔ yu de chɛk yu sik dɛn kwik kwik wan, na di mɔ yu dɔktɔ go ebul fɔ fɛn di tin we de mek yu sik ɛn bigin di tritmɛnt we yu nid.
Yu dɔktɔ go ad kɔtikosterɔyd ɛn ɔda tritmɛnt dɛn if nid de fɔ ɛp fɔ kɔntrol yu sik dɛn. Nɔ panik, bɔt no bɔt di sayn dɛm we yu gɛt ɛn fala yu dɔktɔ in instrɔkshɔn dɛn gud gud wan. Wi de wish yu fɔ wɛl kwik kwik wan!
` Eosinophilic Fasciitis, Eosinophilic Fasciitis, Skin Disizin, Fascia, Jɔyn Pen, Mɔsul Pen, Ɔtoimyun Sik











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