Yu pikin de gɛt bɔku bɔku tin dɛn we nɔ kɔmɔn na in bɔdi? Dis kin bi sayn fɔ Kɔmpleks Limfatik Anomali (CLA)!

Sɔntɛnde, wi kin rili fred we wi si smɔl chenj dɛn na wi pikin dɛn bɔdi, nɔto so? Ɛspɛshali if wi nɔ no di rayt tin dɛn tin dɛn de. Tide wi go tɔk bɔt wan rare bɔt rili impɔtant kɔndishɔn fɔ no bɔt. Dɛn kɔl dis Complex Lymphatic Anomalies , ɔ (CLA) fɔ shɔt tɛm. Sɔm pipul dɛn kin kɔl am bak (Lymphangiomatosis) bifo. So yu go yɛri dɛn tu nem ya.

Fɔs, lɛ wi si, wetin na Kɔmpleks Limfatik Anomali (CLA)?

Fɔ tɔk am simpul wan, Kɔmpleks Limfatik Anɔmal (CLA) na wan sik we nɔ kin apin so ɔltɛm bɔt we kin apin we pikin kin gɛt fayn fayn tɔŋ dɛn we dɛn kɔl limfatik malfɔmeshɔn ɔ limfanjɔm na di pikin in limfatik sistɛm. Dɛn tumbu ya kin gro insay di pikin in bon, di kɔnektiv tisu, ɛn ɔda pat dɛn, ɛn dis kin mek i pwɛl.

Jɔs tink bɔt, ivin if wi pikin gɛt dis sik we dɛn bɔn am, bɔku tɛm di sik kin bigin fɔ sho we i dɔn big smɔl, sɔntɛm afta sɔm ia. Na dat mek sɔntɛnde i kin let fɔ no dis.

So, wetin na dis Limfatik Sistem?

Okay, naw yu go mɔs de wɔnda wetin na di limfatik sistɛm. Fɔ tɔk am simpul wan, na wɔndaful difens sistɛm na wi bɔdi. I tan lɛk di sojaman dɛn na wi kɔntri. Dis limfatik sistɛm de ɛp wi bɔdi fɔ mek wi nɔ gɛt sik ɛn fɛt dɛn if dɛn du am. Na impɔtant pat pan wi imyun sistɛm.

di limf sistεm na wan nεtwכk fכ sכm sכm tכb dεm we dεn kכl limfatik vεsεl dεm, gland dεm lεk limf no dεm, εn כgan dεm lεk di splin. dis limfatik vεsεl dεm lεk sכm sכm tכb dεm. Dɛn kin gɛda limf wata frɔm di tisu dɛn na di bɔdi, filta am, klin am, dɔn dɛn kin gi am bak to di blɔd. Yu nɔ tink se dis na wɔndaful wok?

Tu kayn CLA de: Isolated ɛn Systemic.

Komplex Limfatik Anomali dεm kin sheb to tu men tכp dεm:

1. Isolated CLAs: Dis na we di tכmכro dεm de kכnfyus na wan εria na di pikin in bכdi. Fɔ ɛgzampul, dɛn kin jɔs afɛkt di chɛst kaviti. insay dis kes, di lכng dεm εn di sכft tisu dεm na di chεst (mediastinum) de afekt mכst.

2. Sistem CLA dεm: insay dis kes, dεn tכmכro dεm ya kin apin na bכku ples dεm na di pikin in bכdi, lεk di bon dεm, chεst, εn bεlε.

Dis we ya, di sayn dɛm ɛn di tritmɛnt dɛm kin difrɛn difrɛn wan fɔ di say we di sik afɛkt.

Wetin na di men kayn Kɔmpleks Limfatik Anomali (CLA)?

Fo men kayn CLA de. Pan ɔl we ɛni kayn sik gɛt sɔm pan di sem sayn dɛm, dɛn na difrɛn tin dɛm. Ɛn di chenj dɛn we de apin na di jin we kin mek dɛn gɛt dɛn, dɛnsɛf difrɛn.

• Jɛnɛralized Limfatik Anomali (GLA): .Dis kכndyushכn kin afekt difrεn pat dεm na di pikin in bכdi. fכ egzampl, dεn tכmכro dεm ya kin apin na di bon dεm, splin, liva, lכng, εn sכft tisu dεm na di chεst (mediastinum).
• Kaposiform Lymphangiomatosis (KLA): Dis na di kayn CLA we kin rili bad ɛn we kin skata kwik kwik wan. insay KLA, di limf vεsεl dεm we de kכri limf fכluid כlsay na di pikin in bכdi de big. Dis kin mek dɛn kam insay ɛn pwɛl di ɔgan dɛn, bon dɛn, ɛn tisu dɛn we de rawnd dɛn.
• Sεntri Kכndukshכn Limfatik Anomali (CCLA): Pikin dεm we gεt CCLA kin gεt big limf vεsεl dεm bak. כltu, insay CCLA, dεn bכku bכku dεm ya we dεn big kin de mכst na di torso. Dis kin afɛkt di dijestiv sistɛm ɛn mek di pikin nɔ ebul fɔ pul di limf wata fayn fayn wan na di bɔdi.
• Gorham-Stout Disease (GSD): Dɛn kin kɔl am bak Gorham’s disease, dis kכndyushכn kin mek bכku bon dεm sכlv bikoz fכ di fכmeshכn fכ di limfatik vεsεl dεm insay di bon dεm. Dɛn kin kɔl am bak "vanishing bone disease." I kin afɛkt ɛni bon. Bɔt pikin dɛn we gɛt GSD kin gɛt bon dɛn we kin lɔs na dɛn rib, skel, kɔlabɔn, ɛn sɛvikal spayna.

Aw kɔmɔn dis CLA kɔndishɔn?

Kɔmpleks Limfatik Anomali na rili wan sik we nɔ kin apin so ɔltɛm . Bikɔs dɛn nɔ kin bɔku, sɔntɛnde i kin at fɔ lɛ dɔktɔ dɛn no di rayt we. So, if yu gɛt sɔm sayn dɛm, i rili impɔtant fɔ go to spɛshal dɔktɔ kwik kwik wan.

Wetin kin mek dis CLA de?

Dɔktɔ ɛn risach pipul dɛn stil de tray fɔ no wetin kin mek pɔsin gɛt CLA. כltu, rεsכch we dεn jכs du sho se di kכndyushכn kin kכz fכ כl tu di hεridita jin mכtεshכn dεm we de pas dכn frכm mama εn papa to pikin dεm, εn bak di somatik jin mכtεshכn dεm we de apin afta dεn bכn am. Dis min se i gɛt sɔntin fɔ du wit in jɛnɛtiks.

Udat de pan denja fɔ gɛt CLA?

Kɔmpleks Limfatik Anomali kin afɛkt ɛnibɔdi. Spɛshal wan, di sayn dɛm fɔ dis sik kin apia na di let pikin ɔr yɔŋ pipul dɛm. So, ivin if de sik de wae dεn bכn am, i kin tek sכm tεm fכ di sayn dεm fכ sho.

So, wetin na di sayn dɛm fɔ CLA?

Di sayn dɛm kin difrɛn frɔm wan pikin to ɔda pikin wae gɛt dis sik. Dɔn bak, di sayn dɛm kin difrɛn difrɛn wan bay us ɔgan sistɛm de afɛkt ɛn aw i tranga. Bɔrku tɛm, dis sik kin go bifo smɔl smɔl. So, wi nɔ kin pe atɛnshɔn tumɔs pan sɔm pan di sayn dɛm, ɔr wi kin tink se na bikɔs ɔf ɔda sik.

If di we aw yu pikin de blo dɔn afɛkt:

Dis tɛm, sɔm kayn sayn dɛm wae tan lɛk asma kin apia.

• Kɔf we de kɔntinyu fɔ kɔf.
• I nɔ izi fɔ blo (dyspnea).
• Wiz ( wan sawnd we de wis ) we yu de blo.

If yu pikin in skel sistɛm afɛkt:

• Pen na bon ɔ jɔyn dɛn.
• Ivin smɔl fɔdɔm kin mek pɔsin brok .
• Di limb dɛn we de na di an ɛn fut dɛn kin swɛla.
• Pen ɔ wik we pɔsin kin gɛt we i de kɔmprɛs di nerv .

If yu pikin in dijestiv sistɛm afɛkt:

• Abdominal distension ɛn bɛlɛ pen .
• Anemia ɛn taya ɔltɛm.
• Rɔnbɛlɛ.
• Di it nɔ de te.
• Nɔs ɛn vɔmit.
• We yu de lɔs yu wet fɔ natin.

If yu pikin in urinary system afɛkt:

• Blɔd we de na di urine (hematuria).
• Flank pen .
• Ay blɔd prɛshɔn na pikin dɛn.

If yu pikin gɛt wan ɔ mɔ pan dɛn sik ya, duya go to dɔktɔ. Dis nɔto sayn dɛm we de sho se na CLA, bɔt i impɔtant fɔ mek dɛn du tɛst.

Aw dɔktɔ dɛn kin no dis CLA kɔndishɔn?

Bikɔs CLA na sik we nɔ kin apin so ɔltɛm ɛn di sayn dɛm kin difrɛn, sɔntɛnde i kin at fɔ mek dɔktɔ dɛn no di rayt sik. Bikɔs bɔku tɛm i kin afɛkt pikin dɛn lɔng ɛn bon, yu pikin in dɔktɔ kin ɔda fɔ du tɛst dɛn lɛk:

• Bronchoscopy: Fɔ chɛk fɔ si if infɛkshɔn ɔ ɔda tin dɛn we nɔ fayn na di say dɛn we di briz de blo.
• Pulmonary function testing: Mek yu no aw yu lכng dεm de wok fayn fayn wan.
• Whole-body MRI: Fɔ chɛk fɔ tin dɛn lɛk di ɔgan dɛn we afɛkt, bon lɛsin, ɔ wata we de na di bɛlɛ.
• X-ray: Fɔ chɛk mɔ bon dɛn we tan lɛk se dɛn de sɔprayz ɔ wund pan di MRI. di chεst εks-ray kin luk bak fכ abnכmal tin dεm na di lכng dεm.

Sɔntɛnde, dɔktɔ dɛn kin tek smɔl smɔl limf no ɛn tisu (bayopsi) ɛn chɛk am ɔnda maykroskɔp. pan tap we dis tεst kin dεfinitiv fכ no CLA, sכmtεm i kin mek komplikεshכn dεm, lεk we dεn kכlekt limf fכluid rawnd di lכng dεm (chylothorax). Bikɔs ɔf dis, bɔku tɛm dɔktɔ dɛn kin abop pan tɛst dɛn we nɔ kin tek bɔku tɛm fɔ no if pɔsin gɛt di sik.

Aw dɛn kin trit CLA?

Bikɔs CLA kin afɛkt bɔku say dɛn na di pikin in bɔdi, dɔktɔ dɛn kin wok togɛda, dat min se dɛn kin yuz bɔku tin dɛn fɔ plan tritmɛnt we fit di pikin. We dɛn de trit CLA, di men tin we dɛn kin pe atɛnshɔn pan na fɔ kɔntrol di pikin in sik dɛn. Fɔ du dis, yu kin du tin dɛn lɛk:

• Bon graftin: Fɔ bon damej na kɔndishɔn lɛk GSD.
• wan it we gεt hכy protin כ intravenכs nyutrishכn (tכtal parenteral nyutrishכn כ TPN).
• Sklerotɛrapi: Fɔ shrink ɔ deaktiv di tumor ɔ limf vessel dɛn.
• כpεrayshכn: fכ pul di tכmכro dεm כ fכ put sכm sכm tכb dεm (shunt) fכ mek i izi fכ fכlכ di limf fכ fכlכ.
• Radieshɔn tɛrapi ɔ kemotɛrapi: Fɔ shrink di tɔŋ dɛn we nɔ gɛt kansa (dɛn kin yuz dɛn tin ya nɔmɔ pan kes dɛn we rili siriɔs, we kin mek pɔsin in layf de pan denja).

Dis biɛn tɛm, dɛn dɔn yuz bak di tritmɛnt dɛn we dɛn kin tɔch we de tɔch di jɛnɛtik muteshɔn dɛn we kin mek pɔsin gɛt dis sik. Dɛn dɔn sho bak se dɛn tritmɛnt ya kin wok fayn as fɔs layn tritmɛnt fɔ CLA.

Dɛn kin ebul fɔ mek dɛn nɔ gɛt Kɔmpleks Limfatik Anomali (CLA)?

Bɔt i sɔri fɔ no se, nɔ . CLA kin apin we uman gɛt bɛlɛ, ɛn wi nɔ no di rayt tin we kin mek i apin. So, natin nɔ bin de we yu go du fɔ mek yu pikin nɔ gɛt dis sik.

Wetin na di prɔblɛm dɛn we kin apin we CLA kin gɛt?

CLA kin put yu pikin pan denja fɔ:

• Ascites: Fluid we de gɛda na di bɛlɛ.
• Bɔn dɛn we kin brok.
• Chylothorax εn Chylopericardium: na wan kכlekshכn fכ wan milky fluid (chyle) we gεt limf fluid εn fεt na di mεmbran we de kכba di lכng dεm (pleura) כ di sak we de rawnd di at (pericardium).
• Di lɔng we dɔn kol / nyumotɔraks.
• Liva nɔ de wok fayn.
• Paralayz we pɔsin kin gɛt.
• Pɛrikardia efyushɔn.
• Pleural efyushכn εn kadyojεnik pulmonari εdima.

Sɔm pan dɛn prɔblɛm ya kin rili siriɔs, so i impɔtant fɔ no bɔt di sayn dɛm ɛn fala yu dɔktɔ in instrɔkshɔn.

Wetin na di fiuja fɔ pɔsin we gɛt CLA?

Nɔr mɛrɛsin nɔ de fɔ Kɔmpleks Limfatik Anomali (CLA). Yu pikin in fiuja dipen pan us bɔdi sistɛm dɛn de afɛkt ɛn aw di sik dɛn kin tranga.

Pleural effusions na di big tin we kin mek pipul dɛn we gɛt CLA day. Bɔt if dɛn trit pikin fayn ɛn mɛn am, dɛn go ebul fɔ ɛp am fɔ liv nɔmal layf.

Ustɛm a fɔ go to dɔktɔ?

If yu pikin gɛt ɛni wan pan dɛn sik ya, go to dɔktɔ wantɛm wantɛm:

• Pen na di bɛlɛ ɔ di intestinal.
• If blɔd de na di urine.
• Kɔf ɔltɛm, swɛt, ɔ i nɔ kin izi fɔ blo.
• Nɔs, taya, ɔ we yu nɔ gɛt bɔku bɔku bɔdi we yu nɔ ebul fɔ ɛksplen.

If yu gɛt ɛni wan pan dɛn tin ya, duya go to dɔktɔ ɛn nɔ de te.

Wetin a fɔ aks di dɔktɔ?

Yu kin aks yu pikin in dɔktɔ kwɛstyɔn dɛn lɛk dɛn wan ya:

• Us pat na mi pikin in bɔdi dis sik dɔn afɛkt?
• Us tritmɛnt dɛn de fɔ mi pikin?
• Yu tink se dɛn nid fɔ du ɔpreshɔn pan mi pikin?
• A fɔ no bɔt di sayn dɛn we de sho se a gɛt prɔblɛm dɛn?

I rili impɔtant fɔ aks dɛn kwɛstyɔn ya ɛn ɔndastand di tin we de apin klia wan.

Fɔ dɔn, a fɔ se...

We yu kam fɔ no se yu pikin gɛt CLA (lymphangiomatosis), i nɔmal fɔ mek yu fred ɛn wɔri bɔt aw i go afɛkt dɛn wɛlbɔdi ɛn tumara bambay. Bɔku pan wi nɔ go ɛva yɛri bɔt dis sik bifo. Ɛn natin nɔ de we yu bin fɔ dɔn du fɔ mek i nɔ apin.

Di fɔs tin we yu fɔ du fɔ ɛp yu pikin na fɔ no gud gud wan bɔt dis sik, di sayn dɛn we i kin gɛt, ɛn aw fɔ trit am. Si dɔktɔ we spɛshal pan sik dɛn we gɛt fɔ du wit di limfatik sistɛm. Dɛn kin ansa yu kwɛstyɔn dɛn ɛn gi yu di patikyula mɛrɛsin we yu pikin nid.

Pan ɔl we no mɛrɛsin nɔ de fɔ CLA, di rayt tritmɛnt ɛn manejmɛnt kin ɛp yu pikin fɔ liv gladi ɛn wɛlbɔdi layf. So, kɔntinyu fɔ strɔng ɛn du di bɛst we yu ebul fɔ yu pikin.

` Komplex Limfatik Anomali, Limfanjiomatosis, Limfatik Sistem Sik, Pikin Tכmכro, Osteomalacia, Pulmonari Simptom, Rare Pikin Sik