yu pikin gεt prכblεm wit di limf vessel dεm na in intestin? (Primary Intestinal Lymphangiectasia) Lɛ wi tɔk bɔt dis!

Yu dɔn ɛva notis se yu smɔl pikin in leg ɛn an dɛn kin jɔs swel sɔntɛnde? Ɔ bɔku tɛm i kin kɔmplen bɔt in bɛlɛ we de at? Yu tink se i de lɔs in wet we i nɔ de gɛt mɔ wet? Yu kin tink se dis na nɔmal sayn dɛm wae wi nɔr kin pe atɛnshɔn to. כltu, bihayn dεn tin ya, i kin bi se wan kכndyushכn we nכ kin bכku bכt i kin rili kכnsεn we dεn kכl ‘Primary Intestinal Lymphangiectasia’ (PIL) . Di nem de mek yu fred smɔl, nɔto so? Bɔt nɔ wɔri. Lɛ wi tɔk bɔt dis ditayli ɛn rili simpul wan tide.

Wetin na ‘Praymari Intestinal Lymphangiectasia’?

Fɔ tɔk am simpul wan, dis na wan sik we nɔ kin apin so ɔltɛm we kin apin na wi pikin dɛn dijestiv sistɛm, mɔ di smɔl intestinal. Yu no se bɔku pan di it dɛn we wi de it na di tin dɛn we wi kin it kin digest ɛn di tin dɛn we de insay de kin absɔb insay di bɔdi insay dis smɔl intestinal.

naw, insay dis (PIL) kכndishכn, di sכm sכm tכb sistεm we dεn kכl ‘limf vεsεl' na yu pikin in sכmכl intestin dεm dεn dכn pwεl εn dεn nכ de wok fayn. dis limf vεsεl dεm na wan rili fayn nεtwכk fכ chanεl dεm we de spre כlsay na wi bכdi. I tan lɛk ɔda ‘paip sistɛm’ na wi bɔdi. di men wok we dεn de du na fכ kכlekt wata εn protin dεm we de kכmכt na wi tisu dεm (wi kכl dis wata ‘limf’) εn go bak to di sεkyulatri sistεm.

bכt insay pikin we gεt PIL, dεn limf vεsεl dεm ya kin swεla εn ‘lik’. wetin kin apin na dat insted fכ tek di nyutriεnt εn protin dεm frכm dεn limf vessel dεm ya insay di bכdi, dεn de lik bak insay di intestinal dεm. I tan lɛk se wata de lik frɔm paip we de lik.

We tin lik lɛk dis, tu men prɔblɛm dɛn kin kam:

1. di lכw protin lεvεl: di protin na sכmtin we de du wan rili imכtant wok na di bכdi. So we dɛn tin ya lik insay di intestinal, di bɔdi nɔ kin gɛt inof prɔtin. Dis kin mek di wan ol bɔdi swel. wi kin kכl dis kכndyushכn bak ‘protein-losing enteropathy’ insay mεdikal tεm dεm.

2. Nyutrishɔn dɛfisiɛns: Apat frɔm da wata we de lik, impɔtant vaytamɛn ɛn minral dɛn bak de lɔs. If dɛn nɔ tek kia ɔf dis fayn, di pikin kin gɛt difrɛn tin dɛn we i nɔ de it.

(PIL) kin afɛkt yɔŋ pikin dɛn ɛn yɔŋ pipul dɛn mɔ. כltu dεn kin no am bifo i rich 3. כltu, sכmtεm i kin afekt big pipul dεm εn ivin di pikin dεm we de na di bεlε. No mɛrɛsin nɔ de fɔ am yet. Bɔt dɔktɔ dɛn kin kɔntrol di sayn dɛn ɛn ridyus di lik ɛn swel bay we dɛn yuz spɛshal it plan ɛn mɛrɛsin dɛn. Dɛn kin gi di bɔdi bak di vaytamɛn ɛn minral dɛn we i nid.

Dɛn kin kɔl dis (PIL) sityueshɔn sɔm ɔda nem dɛn:

• Intestinal limfangiɛktasia
• Limfangiɛktasia we dɛn kɔl
• Waldmann sik we dɛn kɔl Waldmann sik

Wetin na di sayn dɛm fɔ dis (PIL) kɔndishɔn?

di men εn mכst kכmכn simptom fכ PIL na fכ swel biכs fכ di wata we de rεtεn. Dɔktɔ dɛn kin kɔl dis lymphedema . Yu kin notis dis fɔs na yu pikin in leg ɛn fut. As dis wata de bɔku, yu pikin in fes, in an, ɛn ivin di say we i de na in bɔdi kin bigin fɔ swel.

Imajin, we yu pikin wek na mɔnin, in fut nɔmal, bɔt as di de de go, bay ivintɛm, in fut kin swel so i nɔ kin ivin ebul fɔ wɛr sus. Na dat kin apin insay dis kes.

pan tap dat, di pikin kin gεt wata bak rawnd in at (dεn kכl am pεricarditis ), wata na in chεst (dεn kכl am pleural effusion ), כ wata na in bεlε (dεn kכl am ascites כ abdominal effusion) .

Na sɔm ɔda sayn dɛn ya:

• Pɔsin we de fil pen na di bɛlɛ
• Nɔs ɛn vɔmit
• Dayarɛa (bɛlɛ de at ) .
• Fɔ fil taya ɔltɛm (Fatigue) .
• We yu de lɔs yu wet
• Nɔ gɛt wet ilɛksɛf yu it bɔku it (dis na bikɔs di bɔdi nɔ de tek di nyutriɛnt dɛn fayn fayn wan, we dɛn kɔl ‘malabsorption’ ) .

If yu pikin gɛt wan ɔ mɔ pan dɛn sik ya, i go fayn fɔ mek yu go to dɔktɔ.

Ɛni siriɔs kɔmplikeshɔn de fɔ di (PIL) kɔndishɔn?

Yɛs, pan ɔl we i nɔ kin apin so ɔltɛm, (PIL) kin mek pikin in wan ol bɔdi swel pasmak. Dɛn kɔl dis ‘anasarca’ . Dis na siriɔs sik we kin ivin mek pɔsin in layf de pan denja. So, e fayn fɔ no bɔt de sik.

Wetin na di rizin fɔ dis (PIL) sityueshɔn?

dis kכndyushכn (PIL) de kכz fכ wan abnכmaliti na di pikin in limf chεnal dεm. dis limfatik chanεl dεm, lεk aw wi bin dכn tכk, na wan sistεm fכ tכb dεm we de kכri tin dεm lεk fεt frכm di pikin in sכmכl intestin to di liva εn כda pat dεm na di bכdi.

dis abnכmaliti de mek di limf vessel dεm de blok. Dɔn, dɛn kin ful-ɔp wit limf wata, di vessel dɛn kin swel, ɛn leta dɛn kin bɔs, ɛn di tin dɛn we de insay dɛn vessel dɛn de kin gɛda na di pikin in big intestin (kɔlɔn).

Bɔt, di wan dɛn we sabi bɔt mɛrɛsin stil nɔ no bɛtɛ bɛtɛ wan wetin mek dis sik kin apin. Na dat na di prɔblɛm.

Dis na jenɛtiks? (Na intestinal lymphangiectasia na jɛnɛtiks?)

Na smɔl tɛm nɔmɔ, dɛn dɔn ripɔt se sɔm pipul dɛn na di sem famili dɔn afɛkt di sik. Bɔt di wan dɛn we de stɔdi bɔt dis stil nɔ shɔ if dis na tin we pɔsin kin gɛt frɔm in jɛnɛtiks. Dɛn de du mɔ risach bɔt dis.

Aw dɛn kin no dis (PIL) sik? (Diagnosis) .

Bɔku tɛm, di fɔs tin we dɔktɔ go du na fɔ chɛk yu pikin in bɔdi ɛn aks yu bɔt di sik dɛn we yu pikin gɛt. Sɔntɛnde, we dɛn du ɔltrasɔund bifo di pikin bɔn , we di pikin stil de na di bɛlɛ, kin sho sayn dɛn fɔ swel (ɛdima) na di pikin in leg dɛn, we kin gi yu sɔm aidia bɔt wetin de apin.

afta dεn bכn di pikin, di dכkta go chεk fכ PIL bay we i yuz spεshal instr כmεnt we dεn kכl εndoskop fכ luk insay di pikin in intestכn dεm. Dis na tiub we kin chenj ɛn we dɛn tay kamɛra pan am. Dɛn go put di pikin fɔ slip ɔnda anestezi we dɛn de du dis tɛst, so dɛn nɔ go fil ɛni pen. So nɔ wɔri.

We dɛn de du dis ɛndoskopi, di dɔktɔ kin tek smɔl smɔl tisu dɛn (we dɛn kɔl bayɔpsi ) frɔm sɔm say dɛn na di pikin in intestinal. Dɔn, wan dɔktɔ we de stɔdi bɔt sik dɛn , we na dɔktɔ we spɛshal fɔ chɛk di tisu dɛn, kin luk dɛn tisu sɛmpul dɛn ya ɔnda maykroskɔp fɔ chɛk fɔ si if di limf vesel dɛn nɔ swel.

Apat frɔm dat, blɔd tɛst kin no ɔmɔs prɔtin de na di bɔdi. yu kin tek stכl sεmpl bak fכ si if wata de lik frכm di limf no dεm go insay di sכmכl intestin.

Wetin na di bɛst tritmɛnt fɔ (PIL)?

We yu de trit PIL, di tin we impɔtant pas ɔl na fɔ chenj di it we di pikin de it. Dis na di men wɛpɔn agens PIL. Tink bɔt am lɛk fɔ put ‘plɔg’ fɔ stɔp di nyutriɛnt lik.

Bɔku dɔktɔ dɛn kin gi dɛn tin fɔ it we nɔ gɛt bɔku fat ɛn we gɛt bɔku prɔtin.

Fat kin at fɔ dayjɛst smɔl. So i at fɔ mek yu pikin in gut we de lik fɔ tek di fat fayn fayn wan. So yu nyu it kin gɛt wan spɛshal kayn fat we dɛn kɔl ‘medium-chain triglycerides (MCTs).’ dis dεm (MCT) na wan kayn fεt we di bכdi kin tek izi wan. Dɔn bak, if yu ad mɔ prɔtin to yu it, dat kin mek yu bɔdi tek bɔku tin dɛn.

Bikɔs sɔm tin dɛn we de ɛp am kin lɔs, di dɔktɔ kin tɛl am bak fɔ gi di pikin vaytamɛn ɛn minral sɔpɔtmɛnt fɔ mek shɔ se di pikin in bɔdi de gɛt wetin i nid.

Apat frɔm dat, di dɔktɔ kin gi yu mɛrɛsin dɛn lɛk dis fɔ ɛp wit difrɛn tin dɛn we de apin to di (PIL) sik:

• Diuretics (dεn kin kכl dεm bak wata pil): dεn ya de wok bay we dεn de ridyus di εkstra wata we de kכmכt na di bכdi bikoz fכ di protin we de lik.
• Somatostatin analכg dεm (lεk כktrεotid): dεn mεdikeshכn dεm ya de εp fכ ridyus di lik fכ di sכbstans dεm frכm di limfatik sistεm.

Ɔda tritmɛnt dɛn we yu kin gɛt:

• Ɔpreshɔn: If ɔda tritmɛnt dɛn nɔ ɛp, ɛn nɔto ɔltɛm, dɔktɔ dɛn kin se yu fɔ du ɔpreshɔn fɔ pul di pat we sik na yu pikin in intestinal.
• Ɔda tritmɛnt dɛn we pɔsin kin gɛt: Risach bɔt dis de kɔntinyu. Dɛn de tɛst bɔku nyu mɛrɛsin dɛn lɛk sirolimus fɔ PIL. Dɛn tin ya kin ɛp sɔm tɛm dɛn, bɔt dɛn nɔ de yuz dɛn bɔku bɔku wan yet.

Wetin na di prɔgnosis fɔ di (PIL) sityueshɔn?

As wi bin dɔn tɔk, (PIL) nɔto sik we pɔsin kin mɛn ɔltogɛda. Bɔt di prɔtin we de na di pikin in blɔd fɔ go ɔp insay sɔm wiks afta dɛn bigin fɔ trit am. Bɔt di pikin go nid fɔ it tin dɛn we nɔ gɛt bɔku fat ɛn tek tin dɛn we go mek i gɛt bɛtɛ tin fɔ it fɔ di res ɔf in layf.

Pan ɔl we dis na prɔblɛm, if dɛn de manej di pikin fayn fayn wan, i go ebul fɔ liv nɔmal layf. Di tin we impɔtant pas ɔl na fɔ fala di dɔktɔ in instrɔkshɔn ɛn tek kia ɔf di pikin in it.

Yu tink se dɛn kin ebul fɔ stɔp di (PIL) sityueshɔn?

Bikɔs di wan dɛn we de du risach nɔ no yet wetin kin mek pɔsin gɛt dis (PIL) sik, naw, no we nɔ de fɔ mek dɛn nɔ gɛt dis sik.

Ustɛm mi pikin fɔ go to dɔktɔ?

If yu notis se yu pikin in leg, in fut, ɔ ɛni wan pan di sayn dɛn we de sho se pɔsin gɛt PIL we wi dɔn tɔk bɔt, i go fayn fɔ mek yu kɛr yu pikin go to dɔktɔ wantɛm wantɛm. Di kwik we dɛn no am, na di mɔ dɛn kin bigin fɔ trit am kwik kwik wan.

Us kwɛstyɔn dɛn a fɔ aks mi pikin in dɔktɔ?

If yu pikin gɛt PIL, yu kin gɛt bɔku kwɛstyɔn dɛn fɔ aks yu dɔktɔ. Na sɔm pan dɛn:

• Us it wae fayn fɔ dis (PIL) kɔndishɔn?
• Us supamakit dɛn a fɔ gi mi pikin?
• Wetin ɔda tin a go du fɔ mek a ebul fɔ kɔntrol mi pikin in sik dɛn fayn fayn wan?
• Dis (PIL) situeshɔn siriɔs?
• Us prɔblɛm dɛn a fɔ wach fɔ?

Nɔ fred fɔ aks dɛn kwɛstyɔn ya. Tɔk bɔt ɛnitin we de mɔna yu wit yu dɔktɔ.

Fɔ dɔn, tin dɛn fɔ mɛmba (Take-Home Message) .

We yu fɔs bigin fɔ gɛt sayn dɛm fɔ Primary Intestinal Lymphangiectasia, i kin tranga fɔ yu ɛn yu dɔktɔ dɛm fɔ ɔndastand wetin de apin. I kin rili kɔnfyus ɛn kɔnfyus ɛkspiriɛns. Bɔt yu dɔktɔ dɛn kin wok wit yu fɔ ɛp yu fɔ no wetin de mek yu gɛt dis sik.

Bɔt gud tin na dat, if yu it tin dɛn we nɔ gɛt bɔku fat ɛn yu de it tin dɛn we gɛt bɔku tin fɔ it, yu kin ebul fɔ kɔntrol di sik dɛn we yu pikin gɛt as tɛm de go. Aks yu pikin in dɔktɔ wetin ɔda tin yu kin du fɔ ɛp yu pikin fɔ kɔntrol dis sik. Di lɔv, sɔpɔt, ɛn atɛnshɔn we yu gɛt rili impɔtant to yu pikin insay dis waka.

`Praymari intestinal lymphangiectasia, PIL, limfatik obstrakshכn, bεlε sik dεm na pikin dεm, lεg swεla, protin dεfichεns, dijestiv sistεm sik dεm