Yu dɔn ɛva yɛri se di retina we de insay yu yay, we na di pat we tan lɛk skrin we de mek di pikchɔ dɛn we wi de si, kin split wantɛm wantɛm to tu ɔ mɔ layers? Dat na wan strenj bɔt impɔtant kɔndishɔn fɔ no bɔt. Dis na wetin dɔktɔ dɛn kin kɔl `(Retinoschisis)`. Nɔ wɔri, lɛ wi tɔk bɔt am simpul wan.
Wetin na Retinoschisis? Lɛ wi ɔndastand am simpul wan.
fכ sכmtεm, `(Retinoschisis)` na we di rεtina insay yu yay split insay layεr dεm. Fɔ tɔk di kɔrɛkt tin, i kin split to tu ɔ mɔ layers. Yu no se wi retina na wan rili kɔmpleks mɛmbran. i gεt wan layεr we de sεnsitiv to layt, εn wan layεr fכ sεl dεm we de kכri signal to di bren tru di `optik nεv`. So, we dɛn layers ya split lɛk dis, i kin afɛkt yu vishɔn. Tink bɔt am lɛk se dɛn nɔ glu di pej dɛn na buk ɛn dɛn nɔ de sheb dɛn. dis split dεm kin apin na di midul pan di rεtina, bכt bכku tεm dεn kin apin na di ed dεm, dat na, na di `pεrifεri`.
Wetin na di men kayn retinoschisis?
Dis kכndyushכn, ``Retinoschisis'', na sכm tεm. Bɔt tu men kayn we dɛn de fɔ dis. Wan na tin we pɔsin kin gɛt , ɛn di ɔda wan na pɔsin we dɛn bɔn wit .
Retinoschisis we kin bigin leta (Akwyayz Retinoschisis) .
dis dεn kכl am bak `dijεnεraytiv rεtinoschisis` . Dat min se na sɔntin we kin apin wit di ej, sɔntin we gɛt fɔ du wit smɔl smɔl we aw pɔsin kin west. Bɔrku tɛm, dɛn kin si dis arawnd di ej 50, 60, ɔ 70. Na dat mek sɔm pipul dɛn kin kɔl am bak `senile retinoschisis` . Bɔt sɔntɛnde, yɔŋ pipul dɛnsɛf kin gɛt dis sik.
Tu kayn degenerative retinoschisis de. Wan na di tipik tayp, ɛn di ɔda wan na di bullous ɔ reticular tayp. insay di bulכs tכp, sכm sכm wata blista dεm de fכm na di rεtina. I at smɔl fɔ no difrɛns bitwin di tu kayn dɛn. כltu di bulכs tכp kin divεlכp di rεtina ol dεm εn di rεtina dεtachmεnt.
Wan ɔda kayn mayopik makyula skisis de . Dɛn kin kɔl am bak mayopik trakshɔn makulopati ɔ mayopik foveoschisis . i kin apin na di sεntri pat pan di rεtina, we dεn kכl di makula , εn spεshal wan na di sεntrכm pan di makula, we dεn k כl fכvia . Bɔrku tɛm, dɛn kin si am pan pipul dɛm wae gɛt siriɔs myopia ɔr wae nɔr de si fayn fayn wan.
Retinoschisis we dɛn bɔn wit
Yu no, we wi se sɔntin we wi bɔn wit, i min sɔntin we de na wi bɔdi we dɛn bɔn wi. dis kayn `(Retinoschisis)` dεn kכl am `juvenile X-linked retinoschisis`.Na wan sik we kin bigin we i yɔŋ, ɔ we i smɔl, ɛn i kin gɛt fɔ du wit di X kromozom. Bɔku tɛm, i kin afɛkt ɔl tu di yay dɛn.
dis kכndishכn, `juvenile X-linked retinoschisis`, de afekt bכy pikin dεm mכst. Dɛn mama dɛn kin kɛr di jin fɔ am, bɔt bɔku tɛm, mama dɛn nɔ kin gɛt dis sik.
Wetin na di difrɛns bitwin Retina Detachment ɛn Retinoschisis?
Pan ɔl we dɛn tu tin ya kin tan lɛk, smɔl difrɛns de. Tink bɔt am, di rεtina detachmεnt na we di rεtina kכmplit wan sεparayt frכm di sכpכt tisu εn kכmכt. I tan lɛk posta we de kɔmɔt na wan wɔl.
rεtinoschisis nכto di rεtina dεtachmεnt, bכt na fכ separet di rεtina insay layεr dεm. Sɔntɛnde, i kin at fɔ no bɔt dis sik, ivin fɔ dɔktɔ we de mɛn yu yay. Bɔt spɛshal tɛst kin ɛp yu dɔktɔ fɔ no ustɛm i bi.
sכmtεm dεn tu kכndyushכn dεm ya, we na `(Retinal detachment)` εn `(Retinoschisis)`, kin apin di sem tεm. dis risk de hכy spεshal if yu gεt di `(congenital)` tכp `(Retinoschisis)` we de de we yu bכn.
Aw kɔmɔn dis sik we dɛn kɔl Retinoschisis?
Risach pipul dεm se di kכndyushכn we dεn bכn wit `juvenile X-linked retinoschisis` de apin pan lεk wan pan 5,000 כ wan pan 25,000 pipul dεm. Dat na wan pasɛnt we rili smɔl.
Dijeneretiv retinoschisis, na wan sik we kin apin wit di ej, dɛn se i kin afɛkt lɛk 4% pan pipul dɛn we dɔn pas 40. Wan ɔda sɔv sho se i kin afɛkt bitwin 1% ɛn 4% pan pipul dɛn we dɔn pas 50 ia.
Wetin na di sayn dɛm fɔ Retinoschisis? Yu gɛt dɛn tin ya bak?
Di wɔndaful tin na dat sɔmtɛm yu kin gɛt dis sik ɛn nɔr gɛt ɛni sayn . Bɔt if yu gɛt sɔm sayn dɛn, lɛ wi si wetin dɛn bi.
If yu gɛt congenital `juvenile X-linked retinoschisis`, yu kin si simptom dɛm lɛk dis:
- di yay dεm de sho se dεn tכn to di nos (lεk `kכros yay`).
- di yay dεm nכ de de na wan ples εn de muv bak εn go bifo (nystagmus).
- dipכnt pan di say we di rεtina tear de, i kin bi se di sεntri כ fכvial vishכn כ pεrifεral vishכn kin lכs.
- Prɔblɛm wit distans vishɔn (bɔku tɛm fɔ si fa).
If yu dɔn gɛt retinoschisis, yu kin gɛt dɛn tin ya:
- we yu nכ ebul fכ si klia wan na di tu dεyshכn dεm (dεn de lכs di pεrifεral vishכn).
- Sɔntɛnde, no sayn nɔ kin apin.
Bɔt if yu retinoschisis kam bad bad wan, ɔ if i kam wit di retina we de kɔmɔt, yu kin gɛt sɔm sayn dɛn lɛk:
- We yu si smɔl blak tin dɛn we de flɔt bifo yu yay (`floaters`) ɛn we yu de si layt we de flash wantɛm wantɛm (`flashers`).
- Fɔ si tin dɛn we dɛn strɛch ɛn distɔrj (`distorted images`).
- dipכnt pan di say we di rεtina tear de, i kin bi se di sεntri כ pεrifεral vishכn kin lכs.
Impɔtant: If yu gɛt ɛni wan pan dɛn sayn ya, go to ay dɔktɔ wantɛm wantɛm. Bikɔs tritmɛnt kwik kwik wan rili impɔtant fɔ di prɔblɛm dɛn we pɔsin kin si.
Wetin mek Retinoschisis kin apin? Wetin na di tin dɛn we kin mek i apin?
Bɔku tɛm di rεtinoschisis we dεn bכn kin kכz bay wan jεnεtik mכtεshכn . Wi bin dɔn tɔk bifo tɛm se i gɛt X-link, we min se i gɛt fɔ du wit di jin dɛn we di mama gɛt.
Bɔt sayɛnsman dɛn nɔ dɔn fɛn yet di rayt kɔz fɔ di sik ``acquired retinoschisis.`` Bɔt dɛn dɔn si se di risk fɔ gɛt am kin go ɔp wit di ej, mɔ afta di ej fɔ 40 ia.
Aw yu go no fɔ tru if yu gɛt Retinoschisis? (Diagnosis) .
Bɔku tɛm, na pɔsin we sabi bɔt yay (ɔftalmɔlɔjis) kin no bɔt dis sik . Afta dɛn dɔn du di ay ɛgzam gud gud wan (we dɛn kin du kɔmprɛhɛnsif ay ɛgzam), dɛn kin du dɛn tɛst ya fɔ kɔnfirm di sik:
- Oftalmoskopi ɔ fundoskopi: Insay dis prɔsidyu, di dɔktɔ kin yuz spɛshal inschrumɛnt (ɔftalmoskɔpi) fɔ chɛk insay yu yay, mɔ di retina.
- Optical Coherence Tomography (OCT): Dis na test we nɔ de invayd we de yuz layt fɔ mek klia pikchɔ dɛn fɔ di insay ɛn bak pat na yu yay. I kin si klia wan di layers na di retina.
- B-scan ultrasonography: Dis na bak wan non-invasive ultrasound test we de yuz sawnd wev fɔ tek pikchɔ fɔ di insay pat na di yay.
- Ilɛktrorɛtinografi (ERG): Dis tɛst de sho aw yu yay de ansa we layt flash wantɛm wantɛm. Dis de ɛp fɔ no aw di retina de wok.
- Angiography: Dis tɛst de tek pikchɔ fɔ di blɔd vesel dɛn na yu retina. I de yuz spɛshal day dɛn lɛk fluorescein ɔ indocyanine grin.
- Jɛnɛtik tɛst: If yu dɔktɔ sɔprayz se yu gɛt wan sik we yu bɔn wit we dɛn kɔl juvenile X-linked retinoschisis, dɛn kin tɛl yu fɔ du dis tɛst.
Wetin na di tritmɛnt dɛm fɔ Retinoschisis? Yu tink se dɛn kin mɛn am?
Fɔ bi ɔnɛs, di kɔndishɔn `(Retinoschisis)`I nɔ go ebul fɔ mɛn am kpatakpata. Bɔt, dɛn kin ebul fɔ kɔntrol am. Dɔktɔ dɛn kin tɛl yu fɔ yuz glas ɔ ɔda tin dɛn we go ɛp yu fɔ si fayn.
- If yu dɔn gɛt retinoschisis , yu nɔ go nid ɛni tritmɛnt. Yu dɔktɔ kin tek dis as bad bad sik we nɔ nid tritmɛnt. Bɔt if yu gɛt mistek dɛn we de mek yu nɔ ebul fɔ si tin, lɛk we yu de si nia ɔ we yu de si fa, yu go nid fɔ gɛt glas.
- If yu gɛt congenital `juvenile X-linked retinoschisis` , yu go nid fɔ yuz glas bak fɔ prɔblɛm wit yu yay.
Sɔntɛnde, di blɔd vesel dɛn na di retina kin brok ɛn mek blɔd kɔmɔt insay di yay. If dis apin, yu dɔktɔ kin tɛl yu fɔ yuz krayoablation ɔ laser therapy fɔ stɔp di blɔd.
di tin we impɔtant pas ɔl na dat if yu gɛt wan retina we de kɔmɔt, yu go mɔs nid ɔpreshɔn fɔ mek yu atak di retina bak.
Risach pipul dɛn stil de tray fɔ fɛn nyu tritmɛnt fɔ juvenile X-linked retinoschisis, lɛk jin tɛrapi , stem-sɛl tɛrapi , ɛn wan mɛrɛsin we dɛn kɔl dorzolamide .
Wan we de fɔ mek yu nɔ gɛt retinoschisis?
כnכfכs, i nכ pכsibul fכ mek di divεlכpmεnt fכ ``Retinoschisis'' .
Nɔbɔdi nɔr no bɔt de kɔz fɔ akwyayz retinoschisis, so no we nɔr de fɔ avɔyd am. Bɔt if pɔsin na yu famili gɛt histri bɔt juvenile X-linked retinoschisis, i go fayn fɔ aks yu dɔktɔ bɔt fɔ tɔk to pɔsin we de advays yu bɔt yu jɛnɛtiks.
Wetin yu kin ɛkspɛkt if yu gɛt retinoschisis?
As wi bin dɔn tɔk, no mɛrɛsin nɔ de fɔ dis sik. Sɔntɛnde, i kin mek pɔsin nɔ ebul fɔ si bɛtɛ igen, sɔntɛnde i kin mek i blaynd bay lɔ. Bɔt sɔm pipul dɛn nɔ kin nid ɛni tritmɛnt atɔl. E kin dipen pan aw yu sik kin tranga ɛn aw yu sik.
Aw a fɔ tek kia ɔf misɛf if a gɛt retinoschisis?
If yu gɛt `(Retinoschisis)`, sɔm impɔtant tin dɛn de we yu kin du:
- Gɛt ɛgzam fɔ yu yay ɔltɛm. Dis na di tin we impɔtant pas ɔl. Mek dɛn chɛk yu yay ɔltɛm , lɛk aw yu dɔktɔ se.
- Yuz tin dɛn we de ɛp yu fɔ si smɔl.Dɔn bak, lan bɔt adaptiv teknɔlɔji we go ɛp yu fɔ du ɛvride wok izi wan. Dis impɔtant fɔ yu ɛn yu pikin if dɛn gɛt dis sik.
- If yu notis ɛni chenj na yu yay, tɛl yu dɔktɔ wantɛm wantɛm. Nɔ ignore ivin smɔl chenj.
If yu nɔ ebul fɔ si ivin smɔl, dat kin mek yu fred. Bɔt mɛmba se yu nɔ nid fɔ manej am yu wan. Stay in kɔntakt wit yu ay dɔktɔ. Aks yu mɛdikal tim bɔt sɔpɔt grup ɛn ɔda tin dɛn. Tek advantej pan di savis dɛn we dɛn de gi. Dɛn kin gi yu ɛdyukeshɔn, tɛl ɔda pipul dɛn bɔt ɛkspiriɛns, ɛn ɛp yu wit tɛknikal.
Di impɔtant tin we yu nid fɔ mɛmba frɔm wetin wi dɔn tɔk bɔt (Take-Home Message)
Okay, so, frɔm wetin wi dɔn tɔk bɔt, dɛn tin ya na di impɔtant tin dɛn we wi fɔ mɛmba:
- rεtinoschisis na wan kכndyushכn we di rεtina de split insay layεr dεm, we kin afekt di vishכn.
- Tu men kayn dis de: we i kam pan di ej ɛn we pɔsin bɔn wit.
- Sɔm pipul nɔr kin gɛt ɛni sayn , bɔt ɔda pipul kin gɛt sɔm kayn sik lɛk wae yu nɔr de si fayn ɛn yu yay de twitch.
- Pan ɔl we no kɔmplit mɛrɛsin nɔ de fɔ dis, dɛn kin ebul fɔ kɔntrol am. Fɔ dis, i impɔtant fɔ gi di rayt advays to dɔktɔ ɛn tɛst.
- If yu ɔ sɔmbɔdi na yu famili gɛt dis sik, i rili impɔtant fɔ go to dɔktɔ fɔ yu yay ɔltɛm ɛn fala dɛn advays .
- If yu notis ɛni chenj na yu yay, go to dɔktɔ wantɛm wantɛm. If yu no di sik kwik kwik wan ɛn trit am, dat kin mek i nɔ wɔs.
- Nɔto yu wan, ples ɛn we dɛn de fɔ gɛt ɛp.
So, a op se dis infɔmeshɔn go yusful to yu. Tek kia ɔf yu yay!
` Rεtinoschisis, rεtina dεtachmεnt, yay sik, yay lכs, yay hεlth, jεnεtik sik, yay tεst











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