Oluusi omala kuwulira obulumi mu magumba n’ennyondo? Oba owulira ng’omutwe gweyongera obunene katono n’amagulu ne gakendeera katono ng’ogenda okaddiwa? Oyinza okulowooza nti bino bitundu bya bulijjo eby’okukaddiwa. Naye emabega w’ebintu bino, kiyinza okuba embeera enkweke, etayogerwa eyitibwa ‘Obulwadde bwa Paget obw’amagumba’. Erinnya lino liyinza okuba eppya gy’oli. Naye eno mbeera eyinza okukosa obulamu bw’amagumba gaffe mu kasirise. Leero, tugenda kukyogerako mu ngeri ennyangu, mu ngeri gy’osobola okutegeera.
Mu ngeri ennyangu, obulwadde bwa Paget obw’amagumba kye ki?
Kino okukitegeera, ka tusooke tulabe engeri amagumba gaffe gye gakolamu. Amagumba gaffe si bintu byokka ebitali biramu. Zino bitundu biramu ebibeera byezza obuggya buli kiseera, nga biggyawo obutoffaali obukadde ne bikola obupya. Enkola eno tugiyita okuddaabiriza amagumba. Kiba ng’okumenya ennyumba enkadde n’ozimba empya, ey’amaanyi mu kifo kyayo. Kino kikulu nnyo okukuuma amagumba gaffe nga ganywevu.
Kyokka mu muntu alina obulwadde bwa Paget obw’amagumba, enkola eno egenda bubi ddala. Bino bye bigenda mu maaso:
1. Okumenya amangu kw’amagumba amakadde: Obutoffaali bw’amagumba obukadde bumenya mangu okusinga ku bwa bulijjo.
2. Okutondebwa kw’amagumba amapya mu ngeri etategeerekeka: Omubiri gukola mangu eggumba eppya okuziba ekituli. Kyokka eggumba eppya eritondebwawo linafu, teribeera lya bulijjo, ddene era likutuka. Enkula yaayo nayo ya njawulo.
Mu ngeri ennyangu, kiringa ekibaawo ng’omukubi wa baasi alina obumanyirivu agezaako okukola ekintu mu bwangu, ate omuntu atalina ky’amanyi ku kyo n’akikola mu bwangu. Ne bw’ozimba bbugwe, ajja kugolola, anafuye, era ajja kumenya mangu. Ekyo kye kituuka ku magumba gaffe mu bulwadde buno. Olw’ensonga eno , amagumba gakutuka mangu (okumenya) era emikisa gy’okulwala endwadde z’enkizi (arthritis) giri waggulu nnyo. Erinnya eddala eriyitibwa obulwadde buno ye `(Osteitis Deformans)`.
Obulwadde buno kookolo? Tobutabula na 'obulwadde bwa Paget' obulala!
Kino kizibu abantu bangi kye balina. Abantu abamu batya olw’okufaanagana mu linnya.
Jjukira bulungi: Obulwadde bwa Paget obw’amagumba si kookolo.
Kyokka waliwo akatono k’olina okumanya wano. Very rarely , kwe kugamba, n'obusobozi obutono ennyo, waliwo omukisa omutono nti kookolo w'amagumba (`osteosarcoma`) asobola okukula mu ggumba erikoseddwa obulwadde bwa Paget. Naye kikulu okujjukira nti kino tekitera kubaawo nnyo.
Waliwo endwadde endala eziwerako eziyitibwa ‘Paget’s’, naye tezirina kakwate na bulwadde buno obw’amagumba.
- Obulwadde bwa Paget obw’amabeere: Kino kika kya kookolo w’amabeere atatera kulabika era abeera mu kitundu ky’enfuli.
- Obulwadde bwa Paget obw’omumwa gwa nnabaana:Kino kika kya kookolo w’olususu atatera kulabika ng’abeera okwetooloola akamwa k’obukyala mu bakyala.
N’olwekyo, kitegeere nti wadde endwadde zino essatu zirina amannya agafaanagana, zino mbeera za bujjanjabi ssatu ez’enjawulo ddala nga tezirina kakwate na ndala.
Ani ali mu bulabe obw’amaanyi obw’okukwatibwa obulwadde buno?
Bannasayansi tebannaba kuzuula kituufu ekivaako obulwadde buno, naye kirowoozebwa nti buva ku nsonga zombi ez’obuzaale , kwe kugamba, obuzaale, n’obutonde .
Omulongooti guno wansi gulaga ebimu ku bintu ebikulu ebiyinza okuleeta obulwadde buno.
| Ensonga y’akabi | Okunnyonnyola |
|---|---|
| Emyaaka | Abantu abasukka mu myaka 50 bali mu bulabe bwa maanyi okukwatibwa obulwadde buno. Obulabe buno bweyongera n’emyaka. |
| Ebyafaayo by’amaka | Singa omu ku booluganda lwo ab’oku lusegere (maama, taata, muganda wo) alina obulwadde buno, naawe otera okubufuna. |
| Ensibuko y’Eggwanga | Obulwadde buno butera okulabibwa mu bantu mu mawanga ga Bulaaya naddala mu mawanga nga Bungereza, Yitale, ne Spain. |
| Okwegatta | Abasajja batera okukwatibwa obulwadde buno okusinga abakyala. |
Bubonero ki obulaga obulwadde buno? Okitegeera otya?
Ekyewuunyisa ku bulwadde buno abantu bangi tebalina bubonero bwonna . Oba balina obubonero obutonotono ennyo, obutafaayo. Olw’ensonga eno, obulwadde buno butera okuzuulibwa mu butanwa nga bakebereddwa X-ray oba omusaayi olw’ensonga endala.
Kyokka singa obubonero bubaawo, buyinza okwawukana okusinziira ku ggumba erikoseddwa. Obubonero obusinga okulabika mulimu:
- Obulumi bw’amagumba oba mu binywa: Buno bwe bubonero obukulu era obusinga okulabika. Kiyinza okuwulirwa ng’obulumi obutasalako, obw’amaanyi mu ggumba erikoseddwa oba mu kiwanga ekiriraanyewo.
- Obulema bw’amagumba: Ekiseera bwe kigenda kiyitawo, enkula y’amagumba eyinza okukyuka. Okugeza, ssinga ekiwanga kikosebwa, omutwe guyinza okukula katono, oba amagulu bwe gakosebwa, amagulu gayinza okufukamira.
- Okumenya: Olw’okuba amagumba amapya agatondeddwawo ganafu, gasobola okumenya mangu ne bwe gagwa oba akabenje akatono.
- Obulumi bw’omutwe n’okubulwa amatu: Singa obulwadde bukwata amagumba g’ekiwanga, okugonza kw’amagumba ago kuyinza okuvaako okunyigirizibwa kw’obusimu, okulumwa omutwe, n’okubulwa okuwulira.
- Obulumi bw’omugongo: Singa omugongo gukosebwa, obubonero ng’okulumwa omugongo n’okuziyira mu magulu buyinza okulabika.
Omusawo azuula atya obulwadde buno?
Nga bwe kyayogeddwa waggulu, kino kitera okuzuulibwa mu butanwa. Omusawo ayinza okukusindika okukeberebwa kuno singa oba olina obubonero oba singa okukeberebwa olw’ensonga endala kireeta okwekengera.
- Okukebera omusaayi mu Alkaline Phosphatase (ALP): Kuno kwe kukebera okusooka okuwa ekisumuluzo. Enziyiza eno eyitibwa `ALP` ekolebwa ng’obutoffaali bw’amagumba bukola. Mu bulwadde bwa Paget, olw’okuba enkola y’okukola amagumba eyitiridde, omuwendo gwa `ALP` mu musaayi guli waggulu nnyo.
- X-rays: Engeri esinga okukakasa obulwadde buno kwe kukola ``X-ray``. Ebifaananyi bya ``X-ray`` bisobola okwawula obulungi amagumba agakoseddwa ku magumba amalala amalamu. Olaba engeri gye zeeyongedde obuwanvu n’okukyuka mu nkula.
- Bone Scan: Kino kikolebwa okulaba ddala amagumba mu mubiri agakoseddwa obulwadde buno n’obuzibu bwe buba. Dyira entono eya radioactive efuyirwa mu musuwa era ebitundu ebirwadde birabibwa nga ‘bright spots’ nga bikubiddwa sikaani.
Bujjanjabi ki obukolebwa ku kino? Kisobola okuwona ddala?
Ekisooka, amawulire amalungi. Mu kiseera kino tewali ddagala liwonya bulwadde buno. Naye teweeraliikiriranga. Waliwo obujjanjabi obukola ennyo okukendeeza ku kukula kw’obulwadde, okufuga obubonero, n’okuziyiza ebizibu.
Obujjanjabi bwetaagisa eri abo bokka abalina obubonero, oba abo obulwadde bwabwe bwe bukosezza ebitundu ebikulu ng’ekiwanga n’omugongo.
Eddagala
Ekika ky'eddagala ekikulu erikozesebwa mu nsonga eno ye bisphosphonates . Eddagala lino lifuga enkola y’okumenya amagumba amangu.
- Mu kiseera kino lye ddagala erisinga okukola obulungi era erikozesebwa ennyo mu kiti kino.Ekirungo kya Zoledronate . Eno mpiso ntono (`infusion`) eweebwa mu musuwa. Bw’ofuna empiso emu ey’eddagala lino, obulwadde buno busobola okufugibwa okumala emyaka.
- Naye jjukira nti eddagala lino likoma ku kukoma ku bulwadde buno okweyongera okusaasaana, naye teriyinza kutereeza bulema bw’amagumba obubaddewo edda.
Okuloongoosa
Okulongoosebwa kwetaagibwa ku bizibu ebiva ku bulwadde buno. Okugeza nga:
- Bwe wabaawo okumenya, kiteekewo.
- Singa ekiwanga kisaanawo ddala olw’obulwadde, okulongoosa ekinywa ky’okugulu oba eky’ekisambi.
- Okuddamu okusengeka amagumba agatali mu nsengeka.
- Bwe wabaawo okusika omuguwa mu busimu, ggyawo puleesa eyo.
Obulwadde buno gye bukoma okumanyibwa amangu n’okujjanjabibwa, ebizibu ng’okumenya n’endwadde z’enkizi gye bikoma okuziyizibwa amangu. N’olwekyo, kikulu nnyo okumanya obubonero.
Obubaka Obutwala Awaka
- Obulwadde bwa Paget obw’amagumba si kookolo, wabula embeera etawona enafuya amagumba.
- Abantu bangi tebalina bubonero bwonna. Obubonero obukulu buyinza okuba okulumwa amagumba, okulemagana, n’okumenya amagumba okwangu.
- Obulwadde buno busobola bulungi okuzuulibwa nga tuyita mu bungi bwa alkaline phosphatase mu musaayi n’okukeberebwa mu X-ray .
- Wadde obulwadde buno tebusobola kuwona ddala, eddagala nga bisphosphonates liyinza okukozesebwa okubufuga obulungi n’okuziyiza ebizibu.
- Bw’oba olina emyaka egisukka mu 50, ng’olina ebyafaayo by’obulwadde buno mu maka, oba ng’olina obulumi bw’amagumba obutali bwa bulijjo, obutasalako, tobubuusa maaso era mazima ddala laba omusawo akuwe amagezi.











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