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Lwaki Puleesa y’amawuggwe (PH) ya bulabe nnyo? Kiki ekituuka ku mubiri gwaffe?
Lowooza ku kiki ekibaawo nga puleesa eri munda mu misuwa egitwala omusaayi mu mawuggwe yeeyongedde. Nga payipu y’amazzi bw’ezibiddwa, kizibuwalira amazzi okukulukuta, emisuwa gino gifuuka mifunda, oluusi ne gigonvuwa. Olwo, omutima gulina okukola ennyo okusobola okusindika omusaayi mu mawuggwe. Oludda olwa ddyo olw’omutima (right ventricle) naddala lwe lusinga okuwulira okunyigirizibwa kuno. Ekiseera bwe kigenda kiyitawo, omutima gutandika okunafuwa nga bwe gweyongera okukola ennyo. Embeera eno era esobola okuleeta ebizibu eby’enjawulo mu mubiri. Okugeza nga:- Okukendeera kwa hemoglobin mu musaayi ( Anemia ).
- Omutima okukuba obutasalako (Arrhythmias).
- Omusaayi guzimba mu misuwa gy'amawuggwe .
- Okukung’aanya amazzi okwetoloola omutima ( Pericardial effusion ).
Bika ki ebikulu ebya puleesa y’amawuggwe (PH)?
Ekitongole ky’ebyobulamu mu nsi yonna (WHO) kyawuddemu embeera eno eya Pulmonary Hypertension (PH) mu biti bitaano ebikulu okusinziira ku bivaako. Ka tulabe kye bali. 1. Ekika 1: PH ereetebwa Pulmonary Arterial Hypertension (PAH). Mu kino, emisuwa egitambuza omusaayi mu mawuggwe (emisuwa gy'amawuggwe) gifunda, ne gigonvuwa, oba ne gikaluba. Kino kiyinza okuba n’ensonga ez’enjawulo. Embeera z’obujjanjabi ezimu, wadde eddagala erimu, ziyinza okukosa kino. 2. Ekika 2: PH ereetebwa obuzibu ku ludda olwa kkono olw’omutima. Oludda olwa kkono olw’omutima gwaffe lwe luyiwa omusaayi mu mubiri gwonna. Kale, singa wabaawo obuzibu ku ludda olwa kkono olw’omutima, bukosa oludda olwa ddyo n’enkola etambuza omusaayi mu mawuggwe. Omusaayi tegutambula bulungi ne guzibikira, era puleesa mu misuwa gy’amawuggwe yeeyongera. 3. Ekika 3: PH ereetebwa obulwadde bw’amawuggwe oba obutaba na mukka gwa oxygen (hypoxia).Endwadde z’amawuggwe ezimu zireetera emisuwa mu mawuggwe okufunda. Kino kireetera omusaayi okulemesebwa, ne puleesa okulinnya. 4. Ekika 4: PH ereetebwa ebiziyiza mu mawuggwe. Okuzimba omusaayi mu mawuggwe oba enkovu eziva ku zo ziremesa omusaayi okutambula. Kino kyongera okunyigirizibwa ku ludda olwa ddyo olw’omutima, ne kyongera puleesa mu mawuggwe. 5. Ekika 5: PH ereetebwa endwadde endala. Embeera eno eya PH esobola okubaawo n’endwadde endala, gamba ng’endwadde ezimu ez’omusaayi n’obuzibu mu nkyukakyuka y’emmere. Wabula tekinnategeerekeka bulungi ngeri ndwadde zino gye zireeta PH.Ani asinga okukosebwa embeera eno Pulmonary Hypertension (PH)?
Puleesa y’amawuggwe (PH) esobola okukwata abantu abakulu ab’emyaka gyonna. Abantu abalina obulwadde bw’omutima oba amawuggwe bali mu bulabe bwa maanyi okubufuna. Era kiyinza okusinga okubeera mu bantu abalina embeera endala. Okugeza nga:- Kumpi abantu 100% abalina obulwadde obw’amaanyi obwa mitral valve.
- Abantu nga 65% abalina obulwadde bwa aortic valve (obulwadde obulala obw’omutima).
- Abantu nga 30% abalina Scleroderma (obulwadde bw'okukaluba kw'olususu n'ebitundu ebiyunga ).
- Abantu nga 20% - 40% abalina obulwadde bwa sickle cell .
- Abantu nga omu ku buli 200 abakwatibwa akawuka ka siriimu .
Bubonero ki obusooka obulaga puleesa y’amawuggwe (PH)?
Ebiseera ebisinga akabonero akasooka kwe kussa obubi, oba okuwunya . Oyinza okufuna okussa kuno okutono ng’okola emirimu egya bulijjo egya bulijjo, gamba ng’okulinnya amadaala, okusitula eby’okulya oba okukola dduyiro. Oyinza obutaba na bubonero bwonna mu kusooka. Obubonero bwe bulabika, buyinza okuba nga butono nnyo. Kyokka ekiseera bwe kigenda kiyitawo, obubonero buno buyinza okweyongera okukaluubiriza okukola emirimu gyo egya bulijjo.Bubonero ki obulabika ng’obulwadde buno bweyongera?
pH bw’egenda yeeyongera, oyinza okussa obubi ne bw’oba oyimiridde buyimiridde. Kino kiyinza okuwerekerwako obubonero nga:- Emimwa gya bbululu oba olususu.
- Obulumi mu kifuba oba okunyiga.
- Okuwulira ng’oziyira oba ng’ozirika.
- Okuwulira nga okooye buli kiseera (Obukoowu ).
- Emmere tewooma.
- Obulumi mu ludda olwa waggulu olwa ddyo olw’olubuto.
- Okuwulira ng’omutima gwo gukuba nnyo.
- Okuzimba enkizi, amagulu, oba olubuto (Edema).
Waliwo emitendera gya Puleesa y’Amawuggwe (PH)?
Yee, ekitongole ky’ebyobulamu mu nsi yonna (WHO) kizudde emitendera ena emikulu egy’obulwadde bwa PH. Bino biyitibwa "ebibinja ebikola." Bino bisalibwawo obubonero bw’olaba n’obungi bw’osobola okukola emirimu gyo egya bulijjo. Obulwadde bwe bugenda bweyongera, obubonero bweyongera okulabika era ne butaataaganya obulamu bwo obwa bulijjo.- Ekibiina 1: Tewali bubonero.
- Ekibiina 2: Tewali bubonero nga buwummudde, wabula obutabeera bulungi oba obulumi obumu mu biseera by’emirimu egya bulijjo, gamba ng’okukola emirimu gy’awaka oba okulinnya amadaala.
- Ekibiina 3: Oyinza okuba ng’okyawulira bulungi ng’otudde butudde. Naye kizibu nnyo okukola emirimu egya bulijjo kati. Oli mukoowu nnyo ate nga oli ku situleesi.
- Ekibiina 4: Obubonero bubaawo ne bw’oba oyimiridde buyimiridde. Obubonero bweyongera bw’ogezaako okukola omulimu gwonna ogwa bulijjo.
Biki ebivaako puleesa y’amawuggwe (PH)?
Waliwo ebintu bingi eby’enjawulo ebivaako PH. Kisinziira ku kika kya PH gy’olina. Endwadde ez’enjawulo, embeera z’obulamu ezisibukako, n’ensonga z’obutonde (obutwa, eddagala erimu) bisobola okubuleeta.Ekika 1: Ebivaako Pulmonary Arterial Hypertension (PAH)
- Obulwadde bw'omutima obuzaalibwa nabwo .
- Eddagala erimu erikendeeza ku buzito (e.g., eddagala "fen-phen," eriyinza okuleeta PAH ne bwe liba limaze emyaka nga likozesebwa).
- Enkyukakyuka mu buzaale .
- Endwadde z'okutereka glycogen.
- Okukwatibwa akawuka ka siriimu.
- Obulwadde bw'ekibumba .
- Obulwadde bwa Lupus.
- Portal hypertension (okweyongera kwa puleesa mu misuwa egigenda mu kibumba).
- Endwadde z’emisuwa gy’amawuggwe ezitatera kulabika nga Pulmonary capillary hemangiomatosis ne Pulmonary veno-occlusive disease.
- Schistosomiasis (obulwadde obuva ku kiwuka).
- Obulwadde bwa Scleroderma.
- Okukozesa eddagala nga Methamphetamine.
Ekika 2: Ebivaako PH ebiva ku buzibu ku ludda olwa kkono olw’omutima
Obulwadde bw’omutima butera okuvaako PH. Olw’okuba oludda olwa kkono ne ddyo olw’omutima bikolagana, ekizibu ekiri ku ludda olwa kkono kijja kukosa n’oludda olwa ddyo.- Obulwadde bwa aortic valve: Kino kizibu ku vvaalu wakati w’ekisenge ekikulu eky’omutima ekipampagira (left ventricle) ne aorta (omusuwa gw’omusaayi ogusinga obunene mu mubiri).
- Omutima okulemererwa ku ludda olwa kkono : Oludda olwa kkono olw’omutima terusobola kusiba musaayi bulungi.
- Left ventricular hypertrophy (okugonza ebisenge by’omusuwa gwa kkono) : Kino kizibuwalira omutima okukuba omusaayi obulungi.
- Obulwadde bwa Mitral valve : Obuzibu ku valve esobozesa omusaayi okukulukuta okuva mu atrium ya kkono okutuuka mu ventricle ya kkono ey’omutima.
Ekika 3: Ebivaako PH ebiva ku bulwadde bw’amawuggwe oba obutaba na mukka gwa oxygen (hypoxia) .
- Obulwadde bw’amawuggwe obutawona (COPD) : Kuno kw’ogatta endwadde nga chronic bronchitis ne emphysema. Bino bikaluubiriza okussa.
- Obulwadde bw’amawuggwe obuyitibwa interstitial lung disease : Enkovu (fibrosis) ebaawo mu bitundu by’amawuggwe.
- Obstructive sleep apnea : Kino kireetera omukutu gw’empewo okuzibikira buli luvannyuma lwa kiseera nga weebase, ekikendeeza ku mukka gwa oxygen omubiri gwe gufuna.
Ekika 4: Ebivaako PH olw’okuzibikira mu mawuggwe
Kino kisinga kuva ku mbeera eyitibwa Chronic Thromboembolic Pulmonary Hypertension (CTEPH) . Kino we wabaawo ebizimba by’omusaayi ne bikola enkovu mu misuwa gy’amawuggwe. Oluusi, embeera eno eyinza okuva ku nkovu ezireetebwa pulmonary embolism (omusaayi oguzimba mu mawuggwe).Ekika 5: Ebivaako PH ereetebwa endwadde endala
PH esobola okuva ku ndwadde endala eziwerako, era bannassaayansi n’okutuusa kati tebategedde bulungi ngeri gye kibaawo.- Obulwadde bwa Gaucher (obulwadde obuva mu nkyukakyuka y’emmere).
- Obulwadde bw’ekibumba.
- Langerhans cell histiocytosis (obulwadde obuleeta enkovu n’ebizimba mu mawuggwe g’abantu abakulu).
- Sarcoidosis (embeera y’okuzimba, esinga kukosa mawuggwe n’ennywanto).
- Obulwadde bwa thyroid.
- Ebizimba : Ebizimba, ka bibeere bya kookolo oba ebitali bya bulabe, bisobola okuleeta puleesa ku misuwa mu mawuggwe.
Puleesa y’amawuggwe (PH) ezuulibwa etya ?
Omusawo ajja kukukebera era bwe kiba kyetaagisa, akole ebigezo ebiwerako okuzuula oba olina PH. Okusooka, omusawo wo ajja kukukebera omubiri . Awo,- Babuuza ku byafaayo by’obulamu bwo n’obubonero bwo.
- Kebera oba emisuwa gy’omu bulago gigaziye (kino kiyinza okuba akabonero k’okulemererwa kw’omutima ku ludda olwa ddyo).
- Okukebera obunene bw’ekibumba, wulira oludda olwa waggulu olwa ddyo olw’olubuto.
- Omutima n’amawuggwe biwulirwa n’ekyuma ekiwuliriza.
- Kebera olubuto, enkizi n’amagulu oba bizimba (edema).
- Puleesa epimibwa.
- Ekipima pulse oximeter kipima omukka gwa oxygen mu musaayi.
Bikebere ki ebikozesebwa okuzuula PH?
- Okusiba omutima ogwa ddyo: Era kiyitibwa okukuba emisuwa gy’amawuggwe, kino kipima puleesa mu misuwa gy’amawuggwe n’omuwendo gw’omusaayi omutima gwe gusobola okusiba buli ddakiika. Kino kye kigezo ekikulu okukakasa PH.
- Doppler echocardiogram: Eno sikaani nga ekozesa amaloboozi. Kiyinza okulaga engeri ventricle eya ddyo ey’omutima gy’ekola n’engeri omusaayi gye guyitamu mu valve. Kino kisobozesa omusawo okubala puleesa y’emisuwa gy’amawuggwe (systolic pulmonary artery pressure).
- Okukebera omusaayi: Bino bikebera ebintu ng’enkola y’ebitundu by’omubiri, obusimu obuyitibwa hormone, ne yinfekisoni. Mu bino mulimu okukebera nga Complete metabolic panel ne complete blood count.
- Chest CT scan: Ekebera oba omusaayi guzimba n’ebizibu ebirala eby’amawuggwe.
- X-ray y’ekifuba: Kino osobola okukikozesa okulaba oba oludda olwa ddyo olw’omutima oba emisuwa gy’amawuggwe minene okusinga ku gya bulijjo.
- Okukebera otulo (Polysomnogram - PSG): Okukebera ekiro okulaba oba olina sleep apnea.
- Pulmonary ventilation/perfusion (VQ) scan: Ekebera oba omusaayi guzimba mu mawuggwe.
Bujjanjabi ki obujjanjaba puleesa y’amawuggwe (PH)?
Obujjanjabi bwa PH businziira ku kika kya PH gy’olina n’embeera z’obulamu bwo endala. Ttiimu yo ey’abasawo ejja kukola enteekateeka y’obujjanjabi ekusinga obulungi. Mu kiseera kino, waliwo ebika bya PH bibiri byokka ebiyinza okujjanjabibwa butereevu:- Peesa y'emisuwa gy'amawuggwe (PAH)''.
- Pleesa y'amawuggwe etali ya bulijjo (CTEPH)''.
- Ebiziyiza emikutu gya Calcium: Eddagala lino liyamba okukendeeza puleesa mu misuwa gy’amawuggwe ne mu mubiri gwonna.
- Eddagala erifulumya amazzi ("empeke z'amazzi"): Liyamba okuggya amazzi agasukkiridde mu mubiri.
- Obujjanjabi bwa okisigyeni: Kino kiyinza okwetaagisa singa mu musaayi temuli mukka gwa oxygen gumala.
- Ebigaziya emisuwa gy’amawuggwe:Eddagala lino liwummuza emisuwa mu mawuggwe ne giggulawo bulungi. Kino kitereeza entambula y’omusaayi n’okukendeeza ku mirimu ku mutima.
- Anticoagulants (eddagala eriziyiza omusaayi okuzimba).
- Balloon atrial septostomy (BAS): Wadde nga kino kitera okukolebwa ku balongo abalina obuzibu obw’amaanyi ku mutima, era kikozesebwa okutebenkeza abantu abakulu abalina PH okutuusa nga basobola okusimbuliza amawuggwe.
- Balloon pulmonary angioplasty (BPA): Eno nkola ekozesa ekituli okugaziya emisuwa gy’amawuggwe. Kikolebwa ku bantu abatasobola kulongoosebwa nnyo.
- Eddagala: Eddagala eriyitibwa Soluble guanylate cyclase stimulator (SGCS) liyinza okuyamba okufuga okukula kw'obulwadde.
- Pulmonary endarterectomy (PEA): Kuno kulongoosa. Kiggya omusaayi mu mawuggwe. Mu kiseera kino eno y’engeri yokka ey’okuwonya ddala PH. Wabula kisobola okukolebwa mu bantu abalina CTEPH bokka.
Jjukira nti olina okwogera n’omusawo wo n’osalawo obujjanjabi obusinga okukuyamba.Abantu abamu abalina PH ey’amaanyi bayinza okwetaaga okukyusibwa amawuggwe ng’ekisembayo.
Oddukanya otya eddagala eriweweeza ku puleesa y’amawuggwe (PH)?
Oyinza okuba ng’omira eddagala eriwera ku PH n’embeera endala. Kiyinza okuba ekizibu okujjukira bino byonna n’okubikola obulungi. Wano waliwo obukodyo obutonotono:- Manya amannya g’eddagala lyonna ly’omira n’engeri gye likola. Kola olukalala era bulijjo lukuume naawe.
- Eddagala lyo limira mu kiseera kye kimu buli lunaku. Bw’oba weerabira ddoozi, tomira ddoozi bbiri okugikola. Kuba omusawo wo omubuuze eky’okukola.
- Tomira ddagala lyonna eritali ku ddagala nga tewebuuzizza ku musawo. Eddagala erimu ery’omusujja, okusesema n’omusujja, awamu n’eddagala eriweweeza ku bulumi, liyinza okuleeta obuzibu eri abantu abalina obulwadde bw’omutima.
- Tomira ddagala lyonna eriwandiikiddwa nti terisaanira bantu abalina puleesa.
- Tolekera awo kumira ddagala lyonna oba okukyusa eddagala nga toyogedde na musawo wo.
- Weewale okukozesa eddagala eriweweeza ku muddo ne caayi ow’omuddo. Ziyinza okukwatagana n’eddagala erimu ly’omira.
Endowooza etya eri omuntu alina puleesa y’amawuggwe (PH)?
Kino kyawukana okusinziira ku muntu. Kisinziira ku:- Ekivaako PH.
- Engeri obulwadde gye bwazuulibwamu amangu.
- Obuzibu bw’obubonero.
- Endwadde endala ezikwatagana.
Bintu ki ebyongera ku bulabe bw’okulwala puleesa y’amawuggwe (PH)?
- Okukwatibwa asibesito.
- Okubeera n’ebyafaayo by’amaka eby’okuzimba omusaayi.
- Okubeera n’omuntu w’omu maka alina puleesa y’amawuggwe (PH).
- Okubeera ku buwanvu obuwanvu waggulu w’obugulumivu bw’ennyanja.
- Okunywa sigala n’okukozesa ebintu ebikolebwa mu taaba.
- Eddagala erimu erikozesebwa okugejja (e.g. "fen-phen" - dexfenfluramine ne phentermine).
- Eddagala erimu eriwonya kookolo n’okwennyamira.
- Okukozesa ebiragalalagala.
- Omusaayi guzimba mu misuwa gy’amawuggwe.
- Obulwadde bw’ebitundu ebiyunga.
- Obulwadde bwa wansi.
- Obulwadde bwa Gaucher.
- Obulwadde bw’omutima.
- SIriimu.
- Obulwadde bw’ekibumba.
- Endwadde z’amawuggwe.
Puleesa y’amawuggwe (PH) esobola okuziyizibwa?
PH tesobola kuziyizibwa bulijjo. Ebimu ku bintu eby’akabi tetusobola kubifuga. Bw’oba olina ebintu ebikuviirako akabi, omusawo ayinza okukuwa amagezi okukeberebwa okumu okukebera omutima n’amawuggwe gy’okola. Osobola okukendeeza ku bulabe bwo obwa PH ng’okola kyonna ekisoboka okuziyiza oba okufuga embeera endala ez’obujjanjabi.- Kola enteekateeka y’okukola dduyiro. Buuza omusawo wo dduyiro ki ataliiko bulabe gy’oli.
- Goberera emmere eyamba omutima. Weewale emmere erimu omunnyo omungi, amafuta, ssukaali n’emmere ey’obutonde.
- Mulekere awo okunywa sigala n’okukozesa taaba. Bino bye bintu ebikulu ebiyinza okuvaako endwadde z’omutima n’amawuggwe.
- Mumira eddagala eriweweeza ku puleesa n’endwadde endala ddala nga omusawo bw’akulagidde.
Obulabirizi bwa ngeri ki obw‟okugoberera bwe nnina okufuna?
Yogerako n’omusawo wo ku ngeri y’okuddukanyaamu n’okulondoola embeera yo. Omusawo ajja kukubuulira ddi lw’olina okuyingira okwekebejjebwa n’okukeberebwa. Buulira omusawo wo amangu ago singa ofuna obubonero obupya oba singa obubonero bwo bukyuka. Ate era, yogerako n’omusawo wo ku bino:- Enkola z’okuteekateeka amaka n’okumanya oba olubuto terulina bulabe. Olubuto lwa bulabe eri abantu abalina PH.
- Zimba ekintu eky’amangu. Abantu abalina PH balina okukuuma ebintu ebimu n’amawulire nga biri kumpi buli kiseera.
- Dduyilo.Buuza kiki ekikukuuma, engeri y’okuyingizaamu dduyiro mu bulamu bwo obwa bulijjo, ne dduyiro ki gw’olina okwewala.
- Eddagala erigema mu sizoni (nga ssennyiga, ekifuba).
- Ebibiina ebiwagira oba okubudaabudibwa. Oyinza okufuna enneewulira ez’enjawulo nga bw’omanyiira okubeera ne PH.
- Enteekateeka z’okutambula. Oyinza okwetaaga okwegendereza okw’enjawulo bw’oba otambula mu nnyonyi. Era olina okwegendereza ng’ogenda ku buwanvu.
Nkyukakyuka ki mu mmere gye nsaanidde okukola?
Omusawo wo ajja kukuwa amagezi ebitongole. Ekikulu ekimu kwe kukendeeza ku munnyo (sodium) gw’onywa. Kino kitegeeza nti:- Lekera awo okuteeka omunnyo ku mmeeza n'okukozesa "omunnyo ogusiiga."
- Weewale ennyama n’ebyennyanja ebifumbiddwa mu ssigala, omunnyo, n’ebibbo.
- Londa emmere ewandiikiddwako "low sodium" (omunnyo omutono).
- Komya emmere ey’amangu n’emmere gy’otwala ebweru.
- Lya emmere erimu ebiwuziwuzi bingi (empeke enzijuvu, ebikuta, ebibala, enva endiirwa).
- Lya emmere erimu ekirungo kya potassium (zabbibu, ebijanjaalo, emicungwa).
- Lya emmere erimu ekirungo kya magnesium (entangawuuzi, tofu, broccoli).
- Kkomya emmere erimu ssukaali omulongooseemu, amasavu amangi, ne kolesterol.
Ddi lwe nnina okulaba omusawo?
Yogerako n’omusawo wo bw’oba olina ekimu ku bibuuzo bino:- Omutima okukuba amangu (okukuba emirundi egisukka mu 120 buli ddakiika).
- Bw’oba olina obulwadde bw’okussa oba okusesema okweyongera.
- Bw’oba otera okuwulira ng’oziyira oba ng’ozirika.
- Obulumi mu kifuba oba obutabeera bulungi olw’okukola emirimu gy’omubiri.
- Okukoowa ennyo oba obutasobola kukola mirimu gya bulijjo.
- Okuziyira oba obutayagala mmere.
- Obutawummula oba okutabulwa.
- Bw’oba weeyongedde okussa obubi naddala ng’ozuukuse ku makya.
- Singa wabaawo okuzimba okweyongera mu bisambi, amagulu oba mu lubuto.
- Bw’oba okaluubirirwa okussa ng’okola emirimu egya bulijjo oba wadde ng’oyimiridde buyimiridde.
- Okugejja (kkiro nga emu mu lunaku, oba kkiro nga 2.5 mu wiiki).
Ddi lwe nnina okugenda mu kisenge ky’abalwadde ab’amangu (ER)?
Singa ekintu nga kino kibaawo, genda mu kisenge ky’abalwadde ab’amangu mu bwangu, oba kuba 1990:- Singa omutima gukuba mangu nnyo (okukuba 120-150 buli ddakiika) ate nga tegukendeera.
- Singa ozirika n’ozirika.
- Bw’oba omira eddagala eriweebwa mu misuwa nga prostacyclins ng’oyita mu kasengejja ka Hickman, waliwo obulabe ng’okukwatibwa yinfekisoni, okutambula kw’akasuwa, okukulukuta kw’eddagala, okuvaamu omusaayi, oba ppampu ya IV okulemererwa.
- Singa okussa obubi tekukendeera ne bw’oba oyimiridde buyimiridde.
- Singa ofuna obulumi obw’amaanyi mu kifuba mu bwangu.
- Singa ofuna omutwe ogw’amaanyi mu bwangu.
- Singa ofuna obunafu oba okuziyira mu bwangu mu bitundu byo.
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