Oluusi owulira ng’olususu lwo lunyirira katono ate nga lunywezeddwa okusinga bulijjo? Oba olina obulumi mu binywa oba okukaluba ku makya? Bino bye bintu bye tuyinza obutafaayo nnyo. Kyokka era ziyinza okuba obubonero bw’embeera etali ya bulijjo eyitibwa Scleroderma . Kino ka twogere mu bujjuvu katono leero, nedda?
Scleroderma kye ki?
Mu ngeri ennyangu, Scleroderma mbeera etali ya bulijjo ng’ebitundu by’omubiri mu mubiri gwo bifuuka ebinene era nga bikaluba okusinga ebya bulijjo. Ebiseera ebisinga, bukosa olususu. Naye oluusi, embeera eno esobola okukosa ebitundu ebirala byonna mu mubiri.
Kino mu butuufu bulwadde bwa autoimmune disorder . Kati oyinza okuba nga weebuuza ‘obuzibu bw’abaserikale b’omubiri’ kye ki. Omubiri gwaffe gulina enkola eringa eggye etukuuma obutakwatibwa ndwadde, eyitibwa abaserikale b’omubiri. Naye mu mbeera eno, enkola eyo egenda bubi, era mu kifo ky’okulwanyisa obuwuka obugwira, etandika okulumba obutoffaali bwaffe obulungi. Kiringa nga tetusobola kumanya ani waffe era ani omulabe. N’abasawo n’okutuusa kati tebasobola kuzuula ddala lwaki kino kibaawo.
Bw’oba olina obulwadde bwa scleroderma, abaserikale b’omubiri bo bawa obubonero eri obutoffaali bw’omubiri gwo okukola puloteyina eyitibwa kolagini omungi ennyo . Mu butuufu emibiri gyaffe gyetaaga kolagini. Kye kifuula ebitundu ebiyunga eby’amaanyi era ebiramu ebiwanirira ebitundu byaffe. Naye bwe kizimba ekisusse, olususu n’ebitundu ebirala bifuuka bigonvu ate nga bibaamu ebiwuzi okusinga ebya bulijjo.
Scleroderma bulwadde obutawona . Kino kitegeeza nti oyinza okubeera n’obubonero buno okumala ebbanga, mpozzi obulamu bwo bwonna. Ate era singa kikosa ebitundu by’ebitundu byo eby’omunda, kiyinza okuleeta ebizibu ebiyinza okutta obulamu bwo. Bw’oba owulira ng’olina obulwadde bw’omutima, ng’olina obuzibu mu kussa, oba ng’olina obuzibu mu kumira, kuba 911 (oba ennamba y’amangu mu kitundu kyo) mu bwangu, oba genda mu kisenge ky’abalwadde ab’amangu mu ddwaaliro.
Bw’oba olina obulumi oba okukaluba mu binywa naddala okwetooloola engalo n’ebigere, mazima ddala olina okulaba omusawo.
Bika ki ebikulu ebya Scleroderma?
Abasawo bagabanyaamu obulwadde bwa scleroderma mu bika bibiri ebikulu:
1. Localized Scleroderma: ‘Ekifo’ kitegeeza okukoma mu kitundu kimu. Ekika kino kikwata ekitundu kimu kyokka eky’omubiri (ebiseera ebisinga olususu). Kivaako ebitundutundu oba emisono gy’olususu olugonvu era olulimu waxy. Ekisinga obulungi kiri nti localized scleroderma oluusi esobola okugonjoola ku bwayo . Era tebutera kusaasaana mu bitundu by’omubiri ebirala.
2. 2. .Systemic Sclerosis: Ekika kino kiyinza okukwata ebitundu ebirala ng’oggyeeko olususu. Kiyinza okukosa enkola yo ey’okussa (ekitundu ekikuyamba okussa n’okuwunyiriza) n’enkola yo ey’okugaaya emmere (ekitundu ekifuula emmere gye tulya amaanyi). Singa obulwadde bwa scleroderma bukosa obusobozi bwo obw’okussa oba okunyiga ebiriisa, otera okufuna ebizibu eby’amaanyi. Kiyinza n’okutta omuntu. Systemic Sclerosis nayo erina ebika ebitono bisatu – diffuse, limited, ne sine sclerosis.
Obulwadde bw’okusannyalala (Diffuse Sclerosis).
‘Okusaasaana’ kitegeeza ‘okubunye’. Mu mbeera eno, obulwadde bwa diffuse sclerosis bubaawo mu bwangu ku bitundu ebinene eby’omubiri. Okugeza nga:
- Ekifuba
- Olubuto
- Ebisambi
- Emikono
- Amagulu
- Feesi
Ate era, kiyinza okukwata ebitundu by’omubiri ebiwerako omulundi gumu. Ekyo kitegeeza nti:
- Enkola y’okugaaya emmere (Enkola y’okugaaya emmere - GI tract) .
- Ensigo
- Omutima
- Amawuggwe
Obulwadde bw’okuzimba emisuwa obutono (CREST syndrome) .
Abasawo batera okuyita Limited Scleroderma nga CREST syndrome . Buli nnukuta mu CREST eyimiridde ku kabonero akava ku yo:
- C - Calcinosis: Calcium ayitiridde mu lususu. Kiyinza okulabika ng’obutundutundu obutono obweru ku lususu.
- R - Obulwadde bwa Raynaud: Okukyuka langi n’okuzimba engalo n’ebigere. Ziyinza okufuuka enzirugavu, bbululu oba emmyufu bwe zibeera mu nnyonta.
- E - Obutakola bulungi mu nnywanto: Okukaluubirirwa okumira n’okuddamu okufulumya asidi.
- S - Sclerodactyly: Okunyiga olususu ku ngalo, ekizibu okufukamira n’okugolola engalo.
- T - Telangiectasias: Obutundutundu obutono, obumyufu oba obukyuse langi ku lususu. Bino biyinza okufaanana ng’emikutu gy’enjuki.
Obulwadde bw’okusannyalala kw’emisuwa
Mu mbeera y’obulwadde bwa Sine Sclerosis, obubonero bw’obulwadde bwa Limited Sclerosis obwogeddwako emabegako bubaawo, naye olususu terukosebwa . Kwe kugamba, oyinza okuba n’obubonero obumu obwogeddwako mu bulwadde bwa CREST syndrome, naye nga tewali kugonza kulabika ku lususu.
Scleroderma etera etya?
Scleroderma bulwadde ddala obutatera kulabika.Abakugu bateebereza nti abantu nga 250 ku buli bukadde mu Amerika balina ebika byonna ebisatu eby’obulwadde bwa scleroderma. Ku bano, abantu nga 100,000 balina obulwadde bwa systemic sclerosis.
Bubonero ki obulaga obulwadde bwa Scleroderma?
Abantu abamu abalina obulwadde bwa scleroderma bayinza obutaba na bubonero bwonna mu ntandikwa. Wabula bangi, akabonero akakulu kwe kulabika ng’ebitundu ebigonvu, ebiringa wax oba emisono ku lususu. Okugatta ku ekyo, waliwo obubonero obulala obuwerako obutera okulabika:
- Obulumi mu binywa
- Okukaluba , naddala ng’ozuukuse ku makya
- Obukoowu (okuwulira ng’okooye nnyo buli kiseera) .
- Okugejja mu ngeri etategeerekeka
Obubonero obulala bw’olaba (ne we bukukwata) businziira ku kika ky’obulwadde bwa scleroderma bw’olina.
Obubonero bw’obulwadde bwa Localized Scleroderma
Abantu abalina obulwadde bwa localized scleroderma batera okufuna olususu lwokka okugonza . Okugonza kuno kuyinza okuba mu kitundu kimu oba kuyinza okubaawo mu bitundutundu. Kiyinza okukosa ebitundu by’olususu bino wammanga:
- Ekifuba
- Olubuto (ekitundu ekyetoolodde olubuto) .
- Emikono n’amagulu (Emikono n’amagulu go) .
- Emikono n’engalo
- Ebigere n’obugere
Kyokka, obulwadde bwa localized scleroderma, obukosa ebitundu by’omunda, tebutera nnyo .
Obubonero bw’obulwadde bwa Systemic Sclerosis
Obulwadde bwa systemic sclerosis busobola okuleeta obubonero obw’enjawulo. Kino nakyo kireetera olususu okugonza, naye ebiseera ebisinga mu bitundu ebinene ne mu bitundutundu. Naddala ku maaso ne mu ngalo. Olususu olugonvu luyinza okutandikira mu ngalo n’ebigere oluvannyuma ne lusaasaana mu mubiri gwonna. Bw’oba olina obulwadde bwa Raynaud’s syndrome , engalo n’obugere mu kitundu ekikoseddwa biyinza okukyusa langi ng’ofunye embeera ennyogovu (ebiseera ebisinga langi njeru, emmyufu, oba langi ya bbululu eya kakobe).
Obulwadde bwa systemic sclerosis era busobola okuleeta obubonero mu bitundu byo ebirala n’ebitundu byo. Okugeza nga:
- Ebinywa: Okuzimba n’okuzimba naddala mu ngalo n’ebigere (enkomerero z’ebitundu byo).
- Ennyondo: Okukaluba, okuzimba, n’obutasobola kutambula.
- Amawuggwe: Okusesema n’okukaluubirirwa okussa (dyspnea).
- Enkola y’okugaaya emmere: Okubulwa emmere, okulumwa omutima, okuzimba, okuziyira n’ekiddukano.
- Omutima:Omutima okukuba mu ngeri etaali ya bulijjo (arrhythmia), okukuŋŋaanyizibwa kw’amazzi okwetoloola omutima (pericardial effusion), n’okugonza kw’ebinywa by’omutima (fibrosis).
- Ensigo: Ekibumba okulemererwa (kino kiyinza okutta obulamu).
- Ebitundu by’ekyama: Obuzibu bw’okusituka (ED) mu basajja n’obukyala okukala.
Kiki ekivaako Scleroderma?
Mu butuufu, abasawo n’okutuusa kati tebamanyi kituufu ekivaako obulwadde bwa scleroderma.
Okunoonyereza okumu kuzudde nti esobola okutambulira mu maka okutuuka ku ddaala eritali limu (ekitegeeza nti esobola okusiigibwa okuva mu bazadde okudda mu baana), naye tekitera kubaawo nnyo ne kiba nti tewali bujulizi bumala kukakasa bulungi nti buzibu bwa buzaale .
Ensonga ezireeta akabi mu Scleroderma
Omuntu yenna asobola okulwala obulwadde bwa scleroderma, naye ebibinja ebimu biri mu bulabe bwa maanyi:
- Abakyala batera okukwatibwa obulwadde buno emirundi nga ena okusinga abasajja.
- Businga kubeera mu bantu abali wakati w’emyaka 30 ne 50. Obulwadde bwa Scleroderma butono nnyo mu bantu abali wansi w’emyaka 30.
- Abantu abaddugavu batera okulwala obulwadde bwa scleroderma. Era batera okufuna obulwadde buno nga bukyali, batera okufuna obubonero obukosa amawuggwe, ate nga balina obubonero obw’amaanyi obw’olususu.
Bizibu ki ebiyinza okuva mu Scleroderma?
Abantu abalina obulwadde bwa scleroderma bali mu bulabe bwa maanyi obw’okufuna embeera endala bbiri: Raynaud’s syndrome ne Sjögren’s syndrome .
Obulwadde bwa Raynaud bukosa emisuwa emitono mu ngalo zo n’ebigere (digito zo). Abantu abalina embeera eno bafuna ebiseera by’obubonero (oluusi obuyitibwa ‘obulumbaganyi’). Wano emisuwa gy’omusaayi mu ngalo zo bwe ginyiganyiga ennyo mu bwangu. Kino kiyinza okuvaako olususu mu ngalo ezikoseddwa okufuuka olumyufu, oba okutangaala okusinga langi y’olususu lwo olw’obutonde. Oluusi, kiyinza n’okulabika nga kya bbululu.
Obulwadde bwa Sjögren buleetera ezimu ku nseke z’omubiri gwo okukola obunnyogovu obutono – emirundi mingi endwadde z’amalusu mu kamwa ko n’endwadde z’amaziga mu maaso go. Abantu abamu abalina obulwadde bwa Sjögren nabo balumwa ebinywa n’ennyondo.
Ebika ebimu eby'obulwadde bwa scleroderma bisobola okuleeta ebizibu eby'amaanyi . Ebimu ku byo mulimu:
- Okulemererwa kw’ekibumba
- Puleesa y’amawuggwe (puleesa mu misuwa egitambuza omusaayi okuva ku mutima okutuuka mu mawuggwe) .
- Obulwadde bw’amawuggwe (okulumwa enkovu mu bitundu by’amawuggwe) .
- Obulwadde bw’emisuwa (ebizibu ebikosa omutima gwo n’emisuwa) .
- Okulemererwa kw’omutima okuzimba, embeera y’omutima
- Obutaba na busimu obuziyiza endwadde
- Endwadde z’omu lubuto (embeera ezikosa engeri omubiri gye gukolamu emmere n’okunyiga ebiriisa) .
- Kookolo
Ebimu ku bizibu bino biyinza okutta omuntu . Bw’olaba obubonero obupya oba obukyuka, laba omusawo amangu ddala nga bwe kisoboka. Bw’oba olowooza nti olina obubonero bw’okulwala omutima, gamba ng’okukaluubirirwa okussa oba okumira, kuba 911 (oba ennamba y’amangu mu kitundu kyo) mu bwangu, oba genda mu kisenge ky’abalwadde ab’amangu mu ddwaaliro.
Scleroderma ezuulibwa etya?
Omusawo azuula obulwadde bwa scleroderma ng’ayita mu kukeberebwa omubiri n’okukeberebwa okulala okuwerako.
Oyinza n’okukwetaagisa okulaba omusawo w’endwadde z’enkizi , omusawo omukugu mu kujjanjaba endwadde z’abaserikale b’omubiri. Ajja kukukebera era akubuuze ku bubonero bwo. Olina okubuulira omusawo obubonero bwo bwe buli, ddi lwe bwasooka okutandika, era oba waliwo ekirabika ng’ekisinga okubwonoona.
Era ojja kwetaaga okukeberebwa okuwerako okukakasa nti tolina mbeera ndala ezireeta obubonero obufaananako bwe butyo.
Bikebere ki abasawo bye bakozesa okuzuula obulwadde bwa Scleroderma?
Okuzuula obulwadde bwa scleroderma ebiseera ebisinga kiba kitundu ku nkola eyitibwa ‘differential diagnosis.’ Kino kitegeeza nti omusawo wo ajja kugaana embeera endala n’akola okukeberebwa okuwerako okuzuula ekikuleetera obubonero nga tannakuzuula nti olina obulwadde bwa scleroderma. Bino bye bimu ku bigezo by’oyinza okuba nabyo:
- Okukebera omusaayi okulaba engeri abaserikale b’omubiri gy’akola.
- Okukebera enkola y’amawuggwe okulaba oba amawuggwe oba enkola y’okussa ekosebwa.
- Okukebera ebitundu by’omubiri (biopsy) nkola nga mu lususu olukoseddwa oba ebitundu ebirala ebikoseddwa okuggyibwako akatundu akatono ne kakeberebwa mu laboratory.
- Bw’oba olina obubonero bw’okugaaya emmere (GI), endoscopy kwe kukebera okutunula wansi mu mumiro oba olubuto nga kkamera entono eyungiddwa ku ttanka empanvu ennyogovu.
Okugatta ku ekyo, ojja kwetaaga okukeberebwa ebifaananyi ebiwerako okusobola okukuba ebifaananyi by’omubiri gwo munda. Mu bino mulimu:
- Okukebera omutima mu byuma (ECG) .
- Echocardiogram (Ekifaananyi ky’omutima - Echo) .
- X-ray y’ekifuba
- Okukebera CT (Computed Tomography - Okukebera CT) .
Scleroderma ejjanjabwa etya?
There is no cure for scleroderma , naye omusawo wo asobola okukuyamba okufuna obujjanjabi obw’omugatte obuyinza okuyamba okufuga obubonero bwo n’okukendeeza ku buzibu bwe bukwata ku bulamu bwo obwa bulijjo.
Ekika ky’obujjanjabi bwe weetaaga kisinziira ku bubonero bwo we buli n’obuzibu bwe buli. Wano waliwo obujjanjabi obutera okukozesebwa ku bulwadde bwa scleroderma:
- Enzijanjaba y’olususu: Ojja kwetaaga okukozesa ebizigo n’ebifukirira okuziyiza olususu lwo okukala.
- Eddagala eriziyiza obusimu obuziyiza endwadde: Eddagala lino liremya abaserikale b’omubiri gwo okwonoona obutoffaali n’ebitundu ebiramu.
- Eddagala eriyinza okufuga obubonero obw’enjawulo: Ng’ekyokulabirako, kiyinza okwetaagisa okumira eddagala erifuga puleesa yo, okukwanguyira okussa, okuddukanya okulemererwa kw’ekibumba oba okumalawo obubonero bw’okugaaya emmere.
- Obujjanjabi bw’omubiri: Omusawo akola ku by’omubiri asobola okukuyamba okulongoosa entambula yo ey’omubiri.
- Obujjanjabi bw’ekitangaala: Kino kizingiramu okukozesa ekitangaala ekimasamasa era ekitunuuliddwa ennyo ekya ultraviolet (UV) okujjanjaba embeera z’olususu. Kino kiyinza okuyamba okujjanjaba olususu olugonvu.
- Okusimbuliza obutoffaali obusibuka mu mubiri: Abantu abamu abalina obubonero obw’amaanyi bayinza okwetaaga okusimbuliza obutoffaali obusibuka mu mubiri. Kino kizingiramu okukyusa obutoffaali bw’omusaayi obwonooneddwa n’ossaamu obutoffaali obugaba omusaayi obulungi.
Bwemba nnina obulwadde bwa Scleroderma, kiki kye nsuubira?
Olina okusuubira okuddukanya obulwadde bwa scleroderma n'obubonero bwayo obulamu bwo bwonna . Wadde nga tewali ddagala lya lubeerera, abantu bangi bafuna obujjanjabi n’enkyukakyuka mu bulamu ebiyinza okukendeeza ku buzibu obubonero bwabwe bwe bukwata ku bulamu bwabwe obwa bulijjo.
Okubeera n’obulwadde obumaze ebbanga eddene kiyinza okukunyiiza ennyo ebiseera ebimu. Buuza omusawo wo ku bibiina ebiyamba oba emikisa gy‟okusoma okukuyamba okuddukanya situleesi yo n‟obulamu bw‟obwongo.
Scleroderma esobola okuziyizibwa?
Olw’okuba ekizibu ekituufu tekimanyiddwa, tewali ngeri yonna gye tuyinza kuziyiza bulwadde bwa scleroderma .
Nze nneerabirira ntya? (Okwefaako) .
Ng’oggyeeko obujjanjabi bwo obwa bulijjo, oyinza okusobola okuddukanya obubonero obumu ng’okola enkyukakyuka ezimu mu bulamu bwo obwa bulijjo. Ebimu ku bino mulimu:
- Okugoberera enteekateeka y’endya ennungi n’okukola dduyiro ekusaanira.
- Okwewala okukola emirimu gy’omubiri ennyo ng’owulira bulungi.
- Kuuma olususu lwo ng’oyambala mu ngeri esaanira embeera gy’obeera n’okusiiga eddagala eriziyiza omusana ery’omutindo omulungi ng’ofuluma ebweru.
- Lambula omusawo w’amannyo (omusawo w’amannyo) okuyonja amannyo buli kiseera n’okukeberebwa.
Ddi lwe nnina okulaba omusawo wange?
Scleroderma esobola okuleeta obubonero obw’enjawulo, n’olwekyo oluusi kiyinza okuba ekizibu okutegeera mu kusooka. Bw’oba olina obulumi obupya oba obubonero obulala naddala bwe bugenda bweyongera, laba omusawo. Obubonero ne bwe buba buva ku kintu kirala, omusawo asobola okuzuula ekivaako n’akuwa amagezi ku bujjanjabi bw’olina okubufuga.
Singa obujjanjabi bwo obwa scleroderma bulabika nga tebukola bulungi, oba singa obubonero bwo bukyuka oba bweyongera – naddala nga bukosa obusobozi bwo obw’okussa oba okumira – yogerako n’omusawo wo.
Ddi lwe nnina okugenda mu kitongole ekijjanjaba abalwadde ab’amangu (ETU) ?
Bw’oba olina obubonero bw’okulwala omutima , gamba ng’okulumwa mu kifuba, okukaluubirirwa okussa, oba bw’oba owulira nga tosobola kumira, kuba 911 (oba ennamba yo ey’amangu mu kitundu kyo) amangu ddala, oba genda mu kitongole ky’abalwadde ab’amangu mu ddwaaliro.
Bibuuzo ki bye nnina okubuuza omusawo wange?
Tewerabira okubuuza ebibuuzo bino ng'olaba omusawo:
- Nnina Scleroderma oba obulwadde obulala?
- Nnina kika ki ekya Scleroderma?
- Bujjanjabi bwa ngeri ki bwe nneetaaga?
- Bizibu ki bye nsaanidde okwegendereza naddala?
Omuntu alina Scleroderma awangaala ki?
Abantu abasinga obungi abalina obulwadde bwa scleroderma tebafuna bizibu ebiyinza okutta obulamu bwabwe .
Wabula bw’oba olina obulwadde bwa systemic sclerosis, obukosa ebitundu by’omubiri eby’omunda, oba mu bulabe bwa maanyi obw’okufuna ebizibu eby’amaanyi. Omusawo ajja kukubuulira ky’osuubira n’okumanya oba oli mu bulabe bwa maanyi obw’okufuna ebizibu ebitta.
Scleroderma bulwadde bwa maanyi?
Okufaananako n’obulwadde bwonna obutawona, scleroderma mbeera ya maanyi era ya maanyi.. Kino kiri bwe kityo kubanga kirabika ojja kuba olina okukola ku bubonero obwo obulamu bwo bwonna. Wabula ekyo tekitegeeza nti Scleroderma ajja kufuga obulamu bwo. Buli muntu by’ayitamu bya njawulo. Yogerako n’omusawo wo ku bintu by’otya, by’obuusabuusa, n’ebikweraliikiriza.
Scleroderma eyinza okuba embeera enyiiza ennyo okubeera nayo. Olw’okuba abasawo tebakakasa kiki ekibuleeta ate nga tewali bujjanjabi bumu, kiyinza okukutwalira ekiseera okufuna obujjanjabi obujja okufuga obulungi obubonero bwo. Omusawo wo ajja kukuyamba buli ddaala ly’ogendako.
Wesige gut feeling yo, era wesige ekyo ekiwulira nti ‘si kituufu’. Ne bwe wabaawo enkyukakyuka entono mu bubonero eyinza okuba akabonero k’ekizibu ekyetaaga okukeberebwa omusawo wo. Totya kubuuza bibuuzo n’okugabana endowooza yo ku bubonero bwo oba obujjanjabi bwo.
Okubeera n’obulwadde obutawona kiyinza okukukooya ennyo. Twala obudde weewa ekitiibwa n’okusiima olw’omulimu omunene gw’okola mu kuddukanya obubonero bwo.
Ebimu ku bintu ebikulu by’osaanidde okujjukira (Take-Home Message) .
Okay, twogedde nnyo ku Scleroderma kati. Mu kumaliriza, bino bye bimu ku bintu ebikulu by’olina okujjukira:
- Scleroderma bulwadde obutatera kulabika, obuziyiza endwadde nga omubiri gukola kolagini omungi, ekivaako olususu n’oluusi ebitundu by’omunda okugonza.
- Kino kirina ebika bibiri ebikulu: eby’omu kitundu n’eby’enkola. Ekika ky’ensengekera (systemic type) kya bulabe katono kubanga era kiyinza okukosa ebitundu by’omubiri eby’omunda.
- Obubonero bwa njawulo. Ebikulu mulimu okugonza olususu, okulumwa ennyondo, okukoowa n’obulwadde bwa Raynaud.
- Wadde nga tewali ddagala lya lubeerera, waliwo obujjanjabi obulungi okufuga obubonero. Yogerako n’omusawo wo okole enteekateeka y’obujjanjabi ekukolera.
- Okuzuula amangu n’okujjanjaba kikulu nnyo, n’olwekyo bw’oba olina ekimu ku bubonero buno, kakasa nti onoonya amagezi g’omusawo.
- Okuva bwe kiri nti embeera eno ewangaala, kikulu okusigala ng’oli mugumu mu birowoozo. Bwe kiba kyetaagisa, noonya obuyambi okuva mu bibiina ebiwagira.
Tofaayo, toli wekka. Bw’oba olina okumanya okutuufu n’okubuulirira kw’abasawo, osobola okubeera obulungi n’embeera eno.
` Scleroderma, Scleroderma, Okugonza olususu, Endwadde z’abaserikale b’omubiri, Collagen, Raynaud’s syndrome, Systemic sclerosis, Endwadde z’olususu











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