I taksaah hian thil mak tak tak awm angin i inhria a, mahse eng nge a nih i hre chiang thei lo em ni? Natna thenkhat chu i taksaah a lo lang fo thin a, mahse i hriat chian chuan i thunun thei a ni. Sarcoidosis hi chutiang natna pakhat a ni. Vawiin hian he thu hi awlsam takin, i hriatthiam theih angin kan sawi dawn a ni.
Sarcoidosis hi eng nge ni?
A awlsam zawngin sawi ila, sarcoidosis hi i taksa immune system a overactive a, taksa hmun hrang hrangah lump te te a siam thin a ni. Heng lumps te hi granulomas an ti a . Heng granulomas te hi khawiah nge an lo awm tih leh an lian leh teah hian a natna lan chhuah dan a innghat a ni. A châng chuan natna lan chhuahna a awm lo thei a, a nih loh leh natna tlem aṭanga chhinchhiahna na tak thlengin a awm thei bawk. A hlauhawm zawk chu a chang chuan heng granulomas te hian tissue scarring a siam thei a, chu chu fibrosis an ti a, chu chuan lung a tichhe vek thei a, entirnan.
Heng granulomas te hi taksa khawi hmunah pawh a lo awm thei tak tak a ni. Mahse lung leh lymph node ah an awm tam ber . Hei bakah hian vun, mit leh taksa peng hrang hrangah te pawh an lo piang thei a, natna lanchhuahna a thlen thei bawk.
Granuloma tih hi eng nge ni?
I taksa chhungah indona tlemte a awm tih i ngaihtuah thei em? Granuloma chu chutiang chiah chu a ni. I immune system chuan i taksaah thil tha lo a lut niin a ngai. Chuvangin, chu thil tha lo chu thisen var (white blood cells) te chuan an lo pungkhawm a, an hual vel a, i taksa dang zawng zawng atang chuan an inthen darh ta a ni. Hmelma trap ang mai a ni. He thisen var (white blood cell mass) tang hian a chhehvelah fibrous tissue layer a siam a. Chuvangin granuloma hi i khawih chuan lump te tak te ang maiin a lang.
He dinhmun hian tute nge a nghawng ber?
Sarcoidosis hian tu pawh a nghawng thei a, mahse mi thenkhat chuan an vei tam zawk. Entirnan, he natna hi mipa hring aiin mipa hring zingah a tam zawk. Hmeichhia pawh mipa aiin tlemin a nghawng nasa zawk bawk. Kum 25 leh 40 inkar ah a awm tam ber .
Hei hi thlahtu natna a ni lo. Chu chu nu atanga pa hnena direct-a inthlunzawm thil a ni lo tihna a ni. Mahse, i chhungte zinga i chhungte hnai tak (nu leh pa, fate, unau) in he natna hi a neih chuan nang pawhin i vei theihna tur hlauhawmna engemaw chen i nei a ni.
Sarcoidosis hi natna hlauhawm takah ngaih a ni . Entirnan, United States-ah hian engtik lai pawhin damlo sanghnih aia tlem an awm a.
Sarcoidosis natna lan chhuah dan chu engte nge ni?
Ka sawi tawh ang khan a natna lan chhuah dan chu taksa chhunga khawiah nge granulomas hi a lo awm tih a innghat a ni. Mi tam zawk chuan lungah hian symptoms an nei thin. Mahse, heng symptoms te hi taksa khawi hmunah pawh a lang thei a, vunah, mit lamah, ruhkawr ah te, a nihna takah chuan. A châng chuan a lan chhuah dân tlangpui chauh a awm thei a, chu chu chak lohna leh hahna ang chi a ni a, a lan dân pawh a awm lo thei bawk.
A lan chhuah dan tlangpui:
- Khawsik
- Chau reng reng, chau reng reng
- Joint natna
- Muscle na emaw chak lohna emaw
- Zanah thawk hah
- Lymph node a lo hring chhuak
- Chhan awm lovin taksa rihna tihtlem
- Kidney lung (kidney stone) siam chhuah
Lung nena inzawm natna lan chhuah dan:
- Khuh (a tam zawkah chuan khuh hring) .
- Thâwk harsa, thawk hah (dyspnea) .
- A rilru a na
- Thâwk chhuah laiin thawk hah (whistling).
Mit nena inzawm natna lan chhuah dan:
- Mit hmuh lohna emaw, mit hmuhna hloh vek emaw (optic neuritis ang chi dinhmun avang) .
- Mit na a na
- Mit sen emaw, a hring emaw (`uveitis` emaw `conjunctivitis` ang chi natna) .
- Eng laka sensitivity (eng pakhat en theih lohna) .
Vun nena inzawm natna lan chhuah dan:
- Vun hnuaia lumps awm chu hliam emaw tattoo emaw vel a ni
- Vunah hmun eng emaw, dum emaw a awm
- Hnar emaw hmui emaw-ah hian red-purple bumps emaw lesions (`lupus pernio`) a awm a.
- Groin area-a hnah sen, hring hring (erythema nodosum) .
Lung lam natna lan chhuah dan: 1.1.
- A rilru a na
- I thinlung a na lutuk tih hriat (palpitations) .
- Lung lam natna (arrhythmia) .
- Lung lam chak lohna
- Thâwk harsa
Nervous system nena inzawm natna lan chhuah dan:
- Tuihâl tam emaw, zun tam lutuk emaw (Diabetes insipidus) .
- Hmai ruh chak lohna emaw, a chak lohna emaw (Bell’s palsy) .
- Lu na
- Seizures a awm thin
Pulmonary sarcoidosis hi eng stage nge awm?
Sarcoidosis, lung natna vei hi a then chuan stage hrang hranga sawi a ni. Hei hi Siltzbach classification system an ti a .
Mahse hriat reng a pawimawh: Heng stage te hian natna nasat zia a tilang hauh lo. Chu zawng zawng chu i paltlang vek a ngai lo. Chest X-ray-a i lung a lan dan a zirin classified an ni. Chu chu granulomas awmna hmun a ni.
Sarcoidosis vei chu heng stage inkarah hian a kal leh chhuak thei a, a nih loh leh granulomas te hi a bo vek thei bawk. Stage tihdanglam theih loh awmchhun chu stage palina a ni. Hei hi lung chhunga chhiatna awm reng a awm hun a ni a, chu chu pulmonary fibrosis an ti a ni.
- Stage 0-naah chuan:X-ray enfiahnaah chuan lungah sarcoidosis a awm tih hmuhchhuah a ni lo. Lung leh lymph node te chu a pangngai angin a lang.
- Stage 1: Granulomas hi lymph node-ah chauh a awm.
- Stage 2: Granulomas hi lymph node leh lung-ah te a awm a.
- Stage 3: Granulomas hi lung chhungah chauh a awm.
- Stage 4: X-ray-ah chuan pulmonary fibrosis a awm a, chu chu lungah hliam awm reng tihna a ni.
Eng thilin nge sarcoidosis hi a thlen?
Hetiang dinhmun hi a chhan dik tak hi hriat a la ni lo. Research atanga a lan dan chuan genetic factors leh environmental factors inkawp avanga lo awm a ni. Chumi awmzia chu mi thenkhat immune system chuan antigens thenkhat , bacteria leh virus te chu a overreact thei tihna a ni. Immune system hi inrawlh mahse, sarcoidosis hi autoimmune disorder anga ngaih a ni lo .
Eng gene leh trigger nge inzawmkhawmin hetiang hi a thlen tih kan hriat chian loh avangin tuin nge hetiang hi a thlen dawn tih sawi a harsa hle.
Löfgren syndrome tih hi eng nge ni?
Löfgren syndrome hi sarcoidosis lo awm nghal mai a ni. Taksa hmun engemaw zat nghawng thei symptom hrang hrang inzawmkhawm a ni a:
- Arthritis hi ruh engemaw zatah a awm.
- Khawsik.
- Groin area-ah hian a sen, a hring (erythema nodosum) a awm.
- A rilru a hah lutuk chuan a rilru a buai em em a.
Thu lawmawm tak chu Löfgren syndrome hi thla 6 atanga kum 2 chhungin a reh tlangpui.
Engtin nge sarcoidosis hi an hriat theih?
Sarcoidosis hi doctor-in a enfiah fo thin (`physical exam`), imaging test te, chest X-ray ang chi te , granuloma rinhlelh awm tak sample tlem te chu enfiah (biopsy) atan a la thin Natna hian natna dang ang bawkin a lan chhuah dan a neih theih avangin, i doctor chuan natna dang a awm loh nan test dang neih belh turin thu a pe thei bawk.
Diagnostic test te hi engte nge ni?
Imaging test leh biopsies hi sarcoidosis hriat theihna atana hman tlanglawn ber a ni a, mahse i doctor chuan i symptoms a zirin test dang a order thei bawk.
- Imaging test: Hengte hian machine bik hmangin i taksa chhunga thil awmte thlalak an la thin. I doctor chuan chest X-ray, CT scan, emaw MRI emaw a ti thei ang.
- Biopsies te chu:Biopsy tih chi hi granuloma rinhlelhna hmun azirin a inang lo. Vun, mit leh lymph node thenkhat atanga biopsies lak hi chu thil lian tak a ni lo va, incision lian tak siam lovin tih theih a ni.
A châng chuan lung atanga tissue piece pakhat lak chhuah tur chuan a buaithlak zawk hman a ngai thin. Hei hi hnar emaw, kawr emaw hmanga tube te te, camera leh biopsy hmanrua te dahin, a nih loh leh incision te tak te siamin tih a ni. Entirnan:
- ``Endobronchial ultrasound hmanga kaihhruaina hmanga transbronchial fine needle aspiration (EBUS-TBNA)'' tih a ni.
- ``Bronchoscopic transbronchial biopsy hmanga tih a ni'' tih a ni.
- `Mediastinoscopy` (Hengte hi damdawi lam thil buaithlak deuh a ni a, a tul chuan doctor-in a tih mai thin)
Test dangte chu:
- Pulmonary function tests: Hengte hian i lung hnathawh that dan a enfiah thin. Hengte hi test awlsam tak a ni.
- Thisen leh zun test (`Lab tests`): Organ dang, thin leh kal te hnathawh dan enfiah thin ang che.
- Electrocardiogram (EKG emaw ECG): I thinlung electric hnathawh dan enfiahna pangngai test a ni.
- Nuclear imaging test: Heng zingah hian PET scan leh gallium scan te pawh a tel. Heng test-ah hian radioactive material tlemte hmangin taksaah inflammation an zawng a ni.
- Purified protein derivative (PPD) test: Hei hi vun test awlsam tak a ni. Tuberculosis (TB) kai leh kai loh a enfiah thin. Hei hi a pawimawh a, a chhan chu a chang chuan TB hi sarcoidosis angin a lang thei a ni.
- Slit-lamp examination: Doctor chuan i mit chhung lam a en a, sarcoidosis hian mit harsatna a thlen em tih a en a.
Sarcoidosis hi engtin nge enkawl a nih?
Sarcoidosis hi a natna lan chhuah dan control nan leh taksa peng hrang hrang tihchhiat loh nan enkawl a ni fo. Granulomas hi immune cells avanga inflammation avanga lo awm a ni tih hre reng ang che. Chuvangin, enkawlnaah hian taksa hriselna tidanglam emaw, thunun thei emaw damdawi a tel a ni. Taksa chhunga granuloma awmna hmun azirin enkawl dan a inang lo.
Sarcoidosis hi damdawi chiang tak a awm lo . Mahse a mah chauhin a tha chho fo thin . A natna lan chhuah dan hi a tibuai lutuk lo emaw, nunna atana hlauhawm lutuk emaw a nih loh chuan a chang chuan sarcoidosis hi enkawl nghal a ni lo. Chu ai chuan nang leh i doctor chuan in symptoms te enfiah turin in thawk ho ang.
Sarcoidosis damdawi hi engte nge ni?
Heng damdawi te hian immune system tihdanglam emaw control emaw leh inflammation tihziaawmna hmangin hna an thawk a ni. Damdawi hman tlanglawn tak tak thenkhat chu:
- Corticosteroids te hi a hnuaia mi ang hian a ni.Damdawi prednisone leh cortisone ang chi te. Chungte chuan taksaa inflammation a tihziaawm. Pill ei tur angin an awm a, ka chhunga spray tur inhaler angin an awm a, topical cream angin (vun emaw mit tan emaw) an awm bawk.
- Immunosuppressants: Hengte hian immune system-in taksa peng hrang hrang a tihchhiat leh inflammation a thlen loh nan a titawp thei a ni. Methotrexate hi sarcoidosis natna atana hman tlanglawn damdawi chi khat a ni.
- Anti-tumor necrosis factor-alpha antibodies (anti-TNF-alpha antibodies): Damdawi infliximab ang chi. Hengte hian immune system-a chemical bik pakhat block-in inflammation tihziaawmna hmangin hna an thawk a ni. Heng damdawi te hi doctor chuan vein chhungah infusion (saline solution ang chi) angin a pe thin.
- Nonsteroidal Anti-Inflammatory Drugs (NSAIDs): Hengte hian inflammation avanga natna lanchhuahna atanga rei lo te chhung a tidam thei a, mahse hun rei tak chhung atan an pe lo tlangpui.
Enkawlna avanga harsatna/side effects awmte chu engte nge ni?
Corticosteroids hian natna i neih theihna a tipung thei a ni. Side effect engemaw zat an nei thei bawk. Entirnan:
- A lian lutuk.
- Mu thei lo.
- Acne a awm.
- Zunthlum vei duhtute zingah zunthlum vei.
- Thisen sang a sang.
- Glaucoma natna (Glaucoma) a awm.
- Mit (cataract) a awm.
- Ruh a hring (Osteoporosis) a ni.
- Depression leh rilru natna thunun harsa.
- Vun a hliam awlsam.
Heng avang hian doctor-te chuan sarcoidosis damdawi hi a hlawknain a hlauhawmna aiin a tam zawk a nih chauhvin an rawt thin.
Engtiang chiahin nge enkawl hnuah ka dam leh thuai ang?
Sarcoidosis enkawl tan hnuah a natna lan chhuahna a lo ṭhat theih nan kar engemaw zat aṭanga thla engemaw zat a ngai thei. I doctor chuan a enkawl ang che a, enkawlna a thawk tha em tih enfiah turin follow-up test a nei thei bawk.
Sarcoidosis i neih lai hian eng ei tur nge ei tur tha lo?
Research thenkhat chuan ei leh in dan thenkhat hian taksaa inflammation a tihziaawm thei niin an sawi. Thlai leh thei ang chi thlai chi hrang hrang ei tam te, sa leh cheese tihtlem te, leh carbohydrates sugar leh chhang te tihtlem te hian i sarcoidosis symptoms te chu a tidam thei a ni. Mahse diet thar i tan hmain doctor zawt hmasa phawt ang che .
Sarcoidosis hi ven theih a ni em?
A chhan dik tak hriat a nih loh avangin sarcoidosis venna tur emaw, a vei theihna tihziaawmna tur emaw a awm lo. Mahse, doctor-in a tih angin damdawi ei hian granulomas vanga taksa peng hrang hrang tihchhiatna chu a tihziaawm thei a ni.
Sarcoidosis hi eng nge a nih?
Sarcoidosis hi a nasat dan a inang lo. Mi tam zawk tan chuan hun eng emaw chen atana natna a ni a, a mah chauhin emaw, enkawlna nen emaw a dam leh thin. Mi thenkhat tan chuan hun rei tak chhung natna (`chronic illness`) a lo ni thei a, chatuan atan chhiatna a thlen thei bawk.
Hei hi han ngaihtuah teh: Sarcoidosis vei hmun thuma ṭhena hmun hnih vel chu kum hnih aṭanga kum thum chhungin an dam kim vek ang (i.e., natna chu `remission`-ah a kal ang). A hmaa kan sawi tawh Löfgren syndrome vei te hian an dam leh theihna chance a tha zawk hle a, a tam zawkah chuan thla 6 atanga kum 2 chhungin an dam leh thei a ni.
Kum thum hnua sarcoidosis la nei te chuan hun rei tak chhung natna an vei tam zawk. Mahse, hun rei tak chhung sarcoidosis vei te zingah pawh mi 10% atanga 20% chauhvin taksa peng hrang hrang a tichhe vek a ni. Complication awm tam ber chu lung scarring a ni.
Sarcoidosis vei tam zawk hi dam chhung pangngaiin an hmang thin. Za zela tlemte chauh (1% - 5%) chauh an thi. Chuvangin, ngaihtuahawm tur a awm lo, hei hi manageable condition a ni.
Sarcoidosis natna vei lai hian engtin nge ka in enkawl ang?
I tih theih tha ber chu i doctor thupek zawm hi a ni. I symptoms te chu a danglamna a awm leh awm loh enfiah fo ang che. I damdawi ei tur chu a tih ang chiah khan ei rawh. Tin, thlamuang taka awm a pawimawh bawk.
Engtikah nge Doctor ka hmuh ang?
Symptom thar i neih chuan, i symptoms te chu a buaithlak a nih chuan emaw, damdawi i ei a, side effects i neih chuan i doctor hmu nghal emaw, biak emaw nghal rawh.
Doctor hnenah eng zawhna nge ka zawh ang?
I doctor i tlawh hunah heng zawhnate hi zawh hi a \angkai thei ang:
- Enkawlna zawng emaw, ka natna lan chhuah dan enfiah emaw hi ka tan a hlawk zawk em?
- Symptoms a that theih nan eng chen nge hun a duh?
- Engtin nge ka enkawlna hian hna a thawk em tih ka hriat theih ang?
- Ka nunphung tihdanglam ka ngai em?
- Engtikah nge ka rawn hmu leh ang che?
A tawi zawngin (Take-Home Message) .
Sarcoidosis hi natna hlauhawm tak a ni a, symptom hrang hrang a thlen thei a ni. Lungngai suh, a tam zawkah chuan a mah chauhin emaw, enkawlna nen emaw a bo vek ang. Hun rei tak chhung daih thei mah se, damdawi leh damdawi lam thurawn hmangin a enkawl tha thei a ni. Thil engemaw takah chuan enkawlna tel lovin i natna lan chhuah dan enfiah mai mai a tha zawk thei tih hre reng ang che. Nang leh i doctor chuan i tana tha ber tur chu i rel thei ang. Chuvangin, chak takin awm la, i doctor thurawn zawm rawh.
` Sarcoidosis, granuloma, immune system, lung natna, vun natna, mit natna, thinlung natna, Sarcoidosis, granuloma, immune system, lung natna, vun natna, mit natna, thinlung natna











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