Nitin i chau leh chau zual zel em? Pum natna leh rilru hahna nen hian chaw tui tak ei duhna mak tak i nei fo thin em? Chûngte chu thil pangngai angin lang mah se, hei hi a hnung lamah hian kan hriat tam loh, mahse uluk taka enkawl ngai dinhmun a awm mai thei. Vawiin hian chutiang dinhmun pakhat, Addison natna chungchang kan sawi dawn a ni.
Addison natna hi eng nge ni tak tak?
A awlsam zawngin sawi ila, Addison natna hi kan taksaa adrenal glands-in hormone pawimawh pahnih, cortisol leh aldosterone -te a siam chhuah tlem chuan a awm reng a ni.
Tunah chuan adrenal glands hi eng nge ni tih i ngaihtuah mai thei. Hengte hi kan kal (kidney) chungah hian cap ang maia thut, triangular gland te tak te pahnih an ni. Kan taksa endocrine system-a thil pawimawh tak an ni.
- Cortisol: He hormone hi kan nunah a pawimawh hle. I damloh emaw, accident i neih emaw, operation i neih emaw chuan i taksain stress nasa tak a nei tih han ngaihtuah teh. Chutiang hunah chuan cortisol hormone hian taksa chu chu stress chu a tuar chhuak thei a ni. Chu mai ni lovin, thisen sang, thinlung hnathawh, immune system, leh thisen sugar level control-na atan a pui bawk.
- Aldosterone: He hormone hian kan thisena sodium (salt) leh potassium balance a tidanglam a. Kan kal (kidney) hian zun anga tui a chhuah zat pawh a control bawk. Hei hian kan thisen volume leh blood pressure direct-in a nghawng a ni.
Addison natna hi primary adrenal insufficiency tia hriat a ni bawk. A kaihhnawih natna dang pakhat chu secondary adrenal insufficiency tih a awm bawk . Hetiang dinhmunah hian thluaka pituitary gland hian ACTH tih hormone a siam tling lo. He hormone ACTH hian adrenal glands te chu cortisol siam turin a tichak a.
Addison natna leh Cushing syndrome hi eng nge an danglamna?
An pahnih hi tibuai suh. A awlsam khawp mai.
- Addison natna: Taksaah cortisol (leh aldosterone) a tlem .
- Cushing’s Syndrome: Taksaah cortisol a pung.
He natna hi tuin nge vei tam ber?
Addison natna hi kum eng pawhah a awm thei a, mahse kum 30 leh 50 inkar vel a ni tlangpui.Mite zingah. Hei hi thil awm lo tak a ni.
Tin, autoimmune natna thenkhat nei te pawhin an vei theihna a sang zawk bawk. Autoimmune disease chu kan taksa ngeia immune system-in kan cell hrisel tak takte a rawn beih palh hi a ni. A hnuaia natna vei te hi Addison natna vei theihna a sang zawk a ni:
- Type I zunthlum vei a ni
- Thisen tlakchhamna (pernicious anemia) a awm
- Graves natna a ni
- Thyroiditis natna rei tak a awm
- Dermatitis natna hrik (Herpetiformis) a awm
- Vitiligo a awm
- Myasthenia gravis natna (myasthenia gravis) a ni
Addison natna lan chhuah dan chu engte nge ni?
He natnaah hian adrenal glands chhiatna hi zawi zawiin, hun kal zelah a thleng fo thin. Chuvangin symptoms a lo lang zauh zauh thin. Heng symptoms te hi mi hrang hrangah a inang lo thei.
| Symptom a ni | Hrilhfiahna |
|---|---|
| Chauhna nasa tak nei fo thin | Hei hi a lan chhuah dan tlangpui leh zawi zawiin a pung chho zel a ni. |
| Vunah hmun dum (Hyperpigmentation) . | Vun dum, a bik takin hliam, hliam, vun hrual (elbows, knees), leh gums chhehvel. |
| Pum na, luak chhuak, leh luak chhuak | Digestive system lama harsatna awm thei. |
| Bloating (ril\am) 1.1. | Pum natna leh riltam fo thin. |
| Chaw ei chakna hloh leh taksa rihna tlahniam | A chhan hriat loha taksa rihna tlahniam leh ei duh lohna. |
| Muscle leh ruh natna | Taksa natna leh taksa peng hrang hrang (muscle spasms) ang chi dinhmun. |
| Thisen sang a hniam | Ding laiin luak chhuak leh muhil tih hriat. |
| Chi ei duhna lutuk | Taksa chhunga chi (salt level) tlahniam avanga symptom. |
| Thisen thlum hniam (Hypoglycemia) . | Taksa na leh thawk hah ang chi symptoms a awm thei. |
| Rilru lam inthlak danglamna | Sawifiah theih loh thinrimna, lungngaihna leh ngaihtuahna seng harsa. |
Hmeichhiain he natna hi an neih chuan thlasik hun mumal lo, taksa sam tlakchham, leh mipat hmeichhiatna lama duhna tlahniam te pawh an nei thei bawk.
Emergency: Addisonian Crisis tih hi eng nge ni?
A châng chuan, a bîk takin taksaa lungkhamna nasa tak a awm lai (e.g., natna khirh tak, accident) lai hian, a lan chhuahna chu a zual thut thei a, nunna atana hlauhawm tak a ni thei bawk. Hei hi Addisonian crisis emaw acute adrenal failure emaw an ti a .
Hei hi medical emergency a ni. Enkawl that loh chuan shock leh thihna thlengin a thleng thei a ni.
Nangmah emaw, i hriat miin emaw a hnuaia symptoms te hi an neih chuan damdawi in hnai ber Emergency Department (ETU)-ah hruai nghal rawh.
| Addisonian buaina a awm tih hriattirna chhinchhiahna | |
|---|---|
| 1. 1. A rilru a hah lutuk chuan a rilru a buai em em a. | Sudden extreme hahna leh chak lohna. |
| 2. 2. A rilru a hah lutuk chuan a rilru a buai em em a. | Pum hnuai lam, hnungzang emaw, ke emaw ah natna nasa tak a awm nghal. |
| 3. A rilru a hah lutuk chuan a rilru a buai em em a. | Luak chhuak nasa tak leh riltam, chu chuan tui tlakchhamna a thlen thin. |
| 4. 4. A rilru a hah lutuk chuan a rilru a buai em em a. | Thisen sang tlahniam lutuk. |
| 5. A rilru a hah lutuk. | Rilru buai, rilru hahdam lohna emaw, hlauhna emaw neia inhriatna. |
| 6. 6. A rilru a hah lutuk chuan a rilru a buai em em a. | Thil hriatna hloh. |
Addison natna hi eng nge ni?
Addison natna thlentu ber chu autoimmune response a ni . A awlsam zawngin kan taksa ngeiin kan taksa invenna (immune system) hian kan taksa hrisel tak takte hi a rawn bei sual a ni. He natnaah hian immune system hian adrenal glands pawn lam (adrenal cortex) a bei a. Hei hi cortisol leh aldosterone siamna hmun a ni. Hetiang chhiatna 90% vel a thlen hma chuan symptoms hi a lang lo tlangpui. Hei hian thla tam tak a daih thei a, kum tam tak pawh a daih thei bawk. Hei hi Addison-a damlo 75% awm chhan a ni.
Tun hma chuan TB natna hi a thlentu lian ber a ni a, ram changkang zawkah chuan a thlentu lian tak a la ni reng a ni.
A chhan dang hmuh tur awm lo tak tak a awm bawk:
- HIV/AIDS ang chi hri kai leh fungal infection te.
- Hmun dang atanga cancer cells adrenal glands thlenga darh zel.
- Adrenal glands-a thisen chhuak (hemorrhaging).
- Adrenal glands te chu surgery hmanga lakchhuah a ni.
- Natna te, amyloidosis ang chi te.
He natna hi engtin nge doctor hian a hriat theih ang?
A lan chhuah dan chu a lo lang zauh zauh a, natna dang tam takah a awm fo avangin he natna hi dik taka hriat a harsa thei hle.
Vawi tam tak chu thisen test pangngaia thisenah sodium level hniam emaw, potassium level sang emaw a awm chuan doctor chuan rinhlelhna a nei thin. Vunah hmun dum (dark spots on the skins) hi symptom lian dang pakhat a ni a, chu chuan hei hi rinhlelhna a siam a ni.
I doctor chuan i natna lan chhuah dan a zirin Addison natna a rinhlelh chuan a natna hriat chian nan test eng emaw zat tih belh leh turin an ti ang.
- Thisen test: Hengte hian i thisena sodium, potassium, cortisol, leh ACTH hormone awm zat a teh thin.
- ACTH stimulation test: Hei hian synthetic ACTH hormone inject a, i adrenal glands te hian a chhanna atan cortisol an siam em tih enfiah a ni. Cortisol level hniam hian glands te hi an thawk tha lo tih a tilang thei.
- Insulin-induced hypoglycemia test: Hei hian i harsatna chu pituitary gland nen a inzawm em tih a enfiah thin.
- CT scan: Hei hian adrenal glands a chhiat leh infection a awm leh awm loh a enfiah thei.
Hei hi eng enkawlna nge ni?
Addison natna hi taksaa hormone bo tawhte chu synthetic drugs hmanga thlak a ni.
- Cortisol aiah damdawi hydrocortisone an tih chu pek a ni.
- Aldosterone hi damdawi fludrocortisone tih hmanga thlak a ni .
Addison natna hi natna khirh tak a nih avangin i dam chhung zawng heng damdawi te hi i ei a ngai dawn a ni .
He damdawi hman dan hi mi hrang hrangah a inang lo. Tin, i doctor chuan Addisonian crisis i neih loh nan damdawi chu a tipung thei bawk a, chu chu infection, accident, surgery ang chi stress i neih chuan a ni.
Addison natna i neih chuan engtin nge i in enkawl ang?
He natna hi i vei a nih chuan mahni inenkawl a pawimawh hle.
- ID card emaw medical alert bracelet emaw hmang fo la, chutiang chuan medical professional-te chuan emergency a thlen hunah i dinhmun an hriat theih nan.
- I damloh emaw, i rilru hahna nasa tak i neih hunah emaw i tih tur chungchang chu i doctor nen sawiho rawh, hetiang hunah hian i damdawi hman zat tur chu tihdanglam a ngai mai thei.
- Emergency a nih chuanI doctor hnenah cortisol injection i kuta awm reng chungchang zawt la, chhungkaw member pakhat hnenah pek dan tur zirtir rawh.
Engtikah nge doctor i hmuh ang?
Addison natna i neih chuan i damdawi ei tur chu i tan a dik em tih hriat nan i doctor (endocrinologist a ni fo thin) i pan fo tur a ni.
I rilru hahna lian tak, accident, natna, emaw, i hmangaih tak thihna emaw i neih chuan i damdawi ei tur zat i thlak a ngai mai thei a, a chhan chu i doctor ko rawh.
Addisonian crisis symptoms (chak lohna nasa tak, natna nasa tak ang chi) a lo lang a nih chuan damdawi in Emergency Department (ETU)-ah damdawi lam enkawl nghal tur a ni.
Natna khirh tak i nei tih hriatna chuan rilru lama harsatna a thlen thei a ni. Mahse thu lawmawm tak chu Addison natna hi damdawi hmanga hlawhtling taka enkawl theih a ni. Doctor hmuh fo te, damdawi dose dik tak ei te, leh mahni in enkawl te hian nun hrisel, pangngai takin i nung thei a ni.
Take-Home Thuchah a ni
- Addison natna hi thil awm lo, rei tak a ni a, adrenal glands hian hormone cortisol leh aldosterone te hi a siam chhuak tawk lo a ni.
- A lan chhuah dan ber chu hah lutuk, vunah (a bik takin vun a inzawm khawmna hmunah) dum hring hring, leh ei tur chi (salty foods) duh lutuk te hi a ni.
- Addisonian crisis hi nunna atana hlauhawm thei medical emergency a ni a, symptoms a awm chuan damdawi in emergency department (ETU)-ah i kal nghal tur a ni.
- Enkawlna atan chuan dam chhung zawng hormone thlak danglamna therapy a ngai a ni.
- Damdawi lam thurawn dik tak zawm a, i damdawi ei tur dik tak i ei chuan nun hrisel tak leh pangngai takin i nung thei ang.











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