I ha enamel-ah pawh harsatna i nei em? (Amelogenesis Imperfecta) chungchang hi han sawi ila!

Engvangin nge i ha chu a rawng a danglam em em, a nih loh leh awlsam taka a chip emaw, a chhe emaw tih i ngaihtuah ngai em? A châng chuan a chhan i hriat loh pawhin i ha-a enamel awm vangin harsatna a awm thei bawk. Chu chu vawiinah kan sawi dawn a ni. A buaithlak deuh a, mahse awlsam taka sawifiah tum ila.

(Amelogenesis Imperfecta) tih hi eng nge ni? A awlsam zawngin i zawng chhuak ang u!

A awlsam zawngin, (Amelogenesis Imperfecta) hi thlahtute atanga lo chhuak natna a ni . Hetianga thil thleng chu i ha chunglama venhimna khauh khuhna, enamel an tih chu a lo thang tha lo a ni. Ngaihtuah teh, he enamel hian kan ha chhunga thil nalh tak takte chu a venghim a ni. (Amelogenesis Imperfecta) i neih chuan enamel siam chhuah zat a tling lo emaw, enamel siam chhuah zat chu a chak tawk lo emaw a ni thei. Hei hian i ha a tidanglam thei a , a chak lo thei bawk . A dik tak chuan he enamel hi ha chhunga venhimna thal ang maia thawktu a ni. Chuvangin a harsatna a awm chuan ha chungah nghawng lian tak a nei thin.

Hetiang dinhmun hian i nuihzatthlakzia a ti zak thei a, i ha nena accident tlemte pawh i neih chuan doctor pan pawh i hlau thei bawk. A tam hle mai. Mahse dawhtheihna leh hun hman chuan i ha tichaktu leh a lan dan titha thei tur enkawlna a awm. Beiseina bansan suh!

(Amelogenesis Imperfecta) chi hrang hrangte chu engte nge ni?

Hetiang dinhmun hi chi li a awm a. Eng nge an nih hi han en ila, chipchiar deuhin:

• Type 1 — Hypoplastic: Hei hi enamel hypoplasia an tih a ni. Hei hian enamel a siam tlem tihna a ni. I enamel chu a hring thei a, glass te tak te ang maiin a hring thei bawk. Hei hian i ha chu a tlangpui aia te zawkin a siam thei a, a chunglam chu a hrual thei a, khur pawh a awm thei bawk.

• Type 2 — Hypomaturation: Hetiang chi hi i enamel tihpunna tura puitu proteins te a lo thang tha lo a nih chuan a lo awm thin. In sak laiin cement a dam tha lo ang maiin han ngaihtuah teh. I enamel chu a thickness pangngai hnaih ni mahse, a nem hle thei a, awlsam takin a chhe thei bawk . Chalk chi khat ang maiin.

• Type 3 — Hypocalcified: Hetiang chi hi i enamel-in a tichak thei tur, emaw, a tihkhauh theih nan calcium a siam tlem chuan a lo awm thin. Enamel hi a thuk dan pangngai a ni thei a, mahse a chhe thei a, a chhe thei bawk. Pressure tlemte pawhin a chhe thei a, biscuit ang maiin a chhe thei.

• Type 4 — Hypomaturation/hypoplasia/taurodontism: Hetiang type-ah hian i ha enamel-ah harsatna i hmu thei a, chu chu type 1 leh 2-ah a awm fo a, hei hian enamel chu a hring leh nem thei tihna a ni. Tin, taurodontism pawh a awm bawkHei hi "protrusion of the jaw" tih natna nen pawh a inzawm thei bawk. Hei hi i ha taksa a lian lutuk a, a zung a tawi lutuk lai a ni. Hetianga ha ratio danglam tak hian doctor-te tan chuan enkawlna tur thlan chu a ti harsa deuh thei a ni.

Hetiang dinhmun hi engtiang chiahin nge a awm?

(Amelogenesis Imperfecta) hi a awm lo hle a ni . Entirnan, United States-ah chuan mi 14,000 zinga pakhat chauh a nghawng a ni. Sri Lanka-ah pawh a hluar vak lo. Chuvângin, chu chu i hre thiam lo mai thei.

(Amelogenesis Imperfecta) natna lan chhuah dan chu engte nge ni?

Amelogenesis Imperfecta i neih chuan i ha ah heng symptoms te hi i hmu mai thei. Heng zinga pakhat emaw a aia tam emaw i neih leh neih loh en rawh:

• Coloration: Ha chu opaque, chalky white, gray, yellow, brown emaw a lo ni thei. A châng chuan, a hring emaw, a rawng emaw a awm thei bawk.
• A tlangpuiin a te: Hei hian i ha inkarah gap a siam thei.
• A chunglam chu a hrual, a pitted emaw, grooved emaw a ni. Hetiang roughness hi khawih chuan hriat theih a ni.
• Brittleness leh awlsam taka chhe leh wear. Thil tenau tak i seh thlak pawhin ha pakhat chu a chhuak thei a ni.
• Thil lum leh vawt laka sensitivity. Ice cream i ei emaw, tea lum i in emaw hian i ha a hring chhuak tih i hre mai thei.
• Misalignment: Open bite i nei thei a, chutah chuan i hmui i khar hian i ha chunglam leh hnuailam a inhmu lo. Hei hian i hmui khar lai pawhin i hmalam ha inkarah gap a awm tihna a ni.

(Amelogenesis Imperfecta) hi eng nge a chhan?

Amelogenesis Imperfecta hi i ha enamel lo pian chhuahna control tu gene pakhat emaw, a aia tam emaw-a mutation , a nih loh leh inthlak danglamna a awm hian a thleng thin. Heng genetic changes te hian i naute ha leh i puitling ha te pawh hmasawnna kawngah harsatna a thlen thei a ni. Mi tam zawk chuan he mutation hi nu leh pa pakhat emaw, an pahnih emaw hnen atangin an rochun thin.

Enamel siam hi thil buaithlak tak a ni. Gene engemaw zatin a nghawng a ni. A bik takin, protein leh mineral te inzawmkhawmin enamel siam dan tur control tu gene a awm a. Heng genes te hi harsatna tlemte a awm chuan amelogenesis imperfecta a awm thei a ni. Amelogenesis imperfecta-a ​​mutation awm tam ber ṭhenkhat chu heng genes te nen hian a inzawm a ni:

• `(FAM83H)` tih a ni
• `(ENAM)` tih a ni
• `(MMP20)` tih a ni
• `(AMELX)` tih a ni

Heng hmingte hi a tricky deuh a, mahse hengte hi doctor ten he natna chungchang an sawi hian an gene hming thenkhat an ni.

Engtin nge hei hi thlah khat atanga chhuan dangah a lo inher chhuah?

Genetic mutations hi a takin a thleng thei a, chu chu chhan awm lovin a awm thei a, mahse Amelogenesis Imperfecta vei tam zawk chuan he natna hi an rochun thin. Amelogenesis Imperfecta chi hrang hrang a zirin inheritance pattern chu hetiang hi a ni thei:

• Autosomal dominant: Hetiang a nih chuan Amelogenesis Imperfecta i neih theih nan i nu leh pa pakhat chauh hnen atangin mutated gene i inherit a ngai a ni. Chumi awmzia chu nu emaw pa emaw hian gene a neih chuan naupang pawhin a nei thei tihna a ni. Hei hi Amelogenesis Imperfecta chi tam zawk hi rochun dan a ni.
• Autosomal recessive: Hetiang a nih chuan Amelogenesis Imperfecta lo awm tur chuan nu leh pa pahnih atanga mutated gene i inherit a ngai a ni. Nu leh pa pahnihin gene an rochun chauhvin he natna hi a lo awm ang.
• X-linked: Hetiang a nih chuan mutation hi X chromosome kaltlangin a inherit a, Y chromosome kaltlangin a inherit a ni. I hriat angin hmeichhia hian X chromosome pahnih (XX) an nei a, mipa chuan X chromosome pakhat leh Y chromosome pakhat (XY) an nei bawk. X-linked (Amelogenesis Imperfecta) nei mipa naupangte hian hmeichhe naupang aiin harsatna leh symptom an nei tam zawk .

Amelogenesis Imperfecta avanga harsatna awm thei te chu engte nge ni?

Ha enamel chungchanga harsatna awm hian a hnuaia sensitive tissue, dentine tia koh chu a pholang a, ha lama harsatna awm theihna a tipung bawk. (Amelogenesis Imperfecta) hian hetiang hi a tipung a:

• Cavities emaw ha hring emaw. Enamel a chak loh avangin awlsam takin natna hrik a lut thei a ni.
• Ha a hring chhuak.
• Gum natna. Gum infection hi a awm thei a, a chhan chu i ha tihfai that a harsat vang a ni.
• Ha na.
• Lungkhamna: I ha lan dan tur chungchangah mualpho leh lungkhamna i nei thei. Mipui hmaa nuih pawh i hlau mai thei.

Engtin nge (Amelogenesis Imperfecta) hi kan hriat theih ang?

Ha enkawltu chuan ha enfiahnaah amelogenesis imperfecta a nei tih a hmuchhuak thei a ni. Doctor chuan i ha awm dan, a rawng leh a hmin dan enin a dinhmun chu a hre thei a ni. Hetiang dinhmun hi chhungkaw hrang hrangah a kal zel avangin, i chhungkaw history-a ha lama harsatna i neihte, i nu, i pa, a nih loh leh i unaute pawhin chutiang harsatna an tawh leh tawh loh te chu a zawt thei a ni.

Nang emaw i fa emaw chuan ha X-ray neih a ngai mai thei . Hei hian doctor chuan i emaw i fa emaw ha insiam dan, entirnan, enamel chu engtiang taka sei nge a nih tih leh ha zung pianzia te chu a hre belh thei ang.

A châng chuan, genetic testing hmangin natna chi hrang hrang (specific mutation) leh chi hrang hrang chu a dik tih finfiah theih a ni. Hei hian enkawlna ruahmannaah pawh a pui thei bawk.

Amelogenesis Imperfecta hi engtin nge enkawl a nih?

I ha dinhmun leh naute ha emaw, ha nghet emaw a nih dan azirin i ha enkawltu chuan enkawlna engemaw zat a rawt thei ang. Amelogenesis Imperfecta vei tam tak chuan an ha venhim leh tihchangtlun nan enkawlna chi hrang hrang an mamawh a ni. Hei hi hun rei tak chhunga thil tih theih a ni.

Enkawlna hrang hrangte chu:

• Restorative treatments: Heng treatment te hian ha chhia te chu a siam tha thin. Entirnan, i ha khuh tur leh venhim nan ha lallukhum pakhat emaw a aia tam emaw i mamawh mai thei. Chûngte chu i ha chunga in fit ang mai a ni. A then phei chuan i ha a chhiat nasa hle a nih chuan ha thlak dan kimchang tak tak, implants ( ha siam chhuah) leh ha lem (ha siam chhuah set) te hi a tha ber.
• Cosmetic treatment: Heng treatment te hian i hmel a ti tha hle. Entirnan, amelogenesis imperfecta avanga i ha a rawng a danglam, a chhe emaw, a chhe emaw a nih chuan, ha bonding ( ha rawng hmanga ha siam thar leh) leh veneer (ha hmalam a khuh te tak te) te hian a pui thei ang. Crown hian ha a tihngheh theih nan a pui bakah ha hmel a ti tha bawk. Whitening treatment hian ha hring (mottled teeth) a pui thei a ni.
• Orthodontic treatment: Amelogenesis Imperfecta avanga ha i hrual a nih chuan, emaw, i seh harsatna i neih chuan, ha enkawlna hmanrua braces emaw aligners emaw i bun a ngai mai thei

A pawimawh ber chu i ha enkawltu nen inbia a, i tana tha tur treatment plan siam hi a ni.

(Amelogenesis Imperfecta) i neih chuan eng nge beisei tur?

Amelogenesis Imperfecta neih (a nih loh leh he natna nei naupang neih) hi a lungchhiatthlak thei a, a lungchhiatthlak thei bawk. Chutiang chu hriatthiam theih a ni. Ha enamel lama harsatna hian ha lama harsatna engemaw zat i neih theihna a tipung a ni. Hun kal zelah enkawlna engemaw zat i neih a ngai mai thei. Enkawlna kimchang tihfel nan pawh kum tam tak a ngai thei.

I ha tan eng enkawlna nge tha ber tih i dentist zawt rawh. Enkawl dan tur pawh zawt bawk ang che, mi hrang hrangah a inang lo thei a ni. Chutiang chuan eng ang hmasawnna nge i beisei theih tih leh engtikah nge a lo thlen dawn tih i hre thei ang. Hetah hian dawhtheihna hi a pawimawh ber a ni.

Engtin nge ka in enkawl ang? A nih loh leh engtin nge ka fa ka enkawl ang?

Amelogenesis Imperfecta i neih chuan i ha venhim nan fimkhur zual a ngai a ni. Hei hian a huam tel a ni:

• I ha tihfai fo thin:Kum khatah vawi hnih tal i ha enkawltu hnena check-up neih hi hloh suh la, i kal fo a ngai mai thei bawk.
• Oral hygiene habit tha tak vawng reng rawh: Ni khatah vawi hnih i ha i silfai tur a ni a, nitin floss i hmang tur a ni a, ha sensitivity venna atan desensitising toothpaste leh tui lum tak i hmang tur a ni
• I ha tana tha ei tur: Vitamin A leh D tamna chaw (carrot, butter, leh fish oil ang chi) te hi i ha enamel atan a tha hle. Calcium tamna ei tur (bawnghnute, yogurt, cheese, leh sangha te tak te, a hnah nei ang chi) te pawh hi duhthlan tur tha tak a ni.
• I ha tichhe thei ei leh in te pumpelh rawh: Ei leh in tur, sugar emaw acid tamna (toffee, chocolate, soft drinks) ei loh tum ang che. Tin, ei tur harsa tak tak, ei harsa tak tak (candy, ice cubes) ei kha tihtlem bawk ang che. Tin, caramel ang chi ei tur sticky tak tak atanga inthiarfihlim a tha bawk.
• A tul chuan natna tidamtu damdawi ei rawh: Ha na i neih chuan i ha enkawltu hmu turin appointment siam rawh. Chutih lai chuan, over-the-counter painkillers acetaminophen (or paracetamol) leh ibuprofen te chu i ei thei bawk. Mahse heng natna tidamtu damdawi hi doctor emaw healthcare provider emaw nena inbiakna nei lovin vawi khatah ni 10 aia tam ei suh.

Engtikah nge Doctor ka hmuh ang?

Amelogenesis Imperfecta an tih natna lan chhuahna, ha rawng danglam, chak lo, awlsam taka chhe thei ang chi i hmuh chuan ha enkawltu hnenah hma la nghal vat rawh. Enkawlna hian i ha a humhim thei a, a siam tha thei a, a hmel a ti tha thei bawk – mahse vawi khat enamel a bo tawh chuan a siam thar leh thei tawh lo. Chuvangin, enkawlna i hmuh hma poh leh i ha hrisel taka awm theihna chance a sang zawk.

Doctor hnenah eng zawhna nge ka zawh ang?

Hetiang dinhmun hi doctor nen inbiakna neih a pawimawh. Zawhna i zawh theih ṭhenkhat chu hetiang hi a ni:

• Eng ang Amelogenesis Imperfecta nge kei (or ka fa) hian ka neih?
• Eng ang enkawlna nge kei (a nih loh leh ka fa) hian ka mamawh?
• Ka (or ka fa) enkawlna hun tur chu eng ang nge ni ang? Eng chen nge a daih ang?
• Ka (or ka fa) ha enkawl nan eng thil bik nge ka practice theih ang?
• Hetiang dinhmun avang hian nakin lawkah eng harsatna dang nge lo awm thei ang?

He thuziak atanga hriat reng tur pawimawh ber chu!

Okay, chuti a nih chuan tunah chuan kan sawi tawh (Amelogenesis Imperfecta) kha i hre chiang zawk tawh ang. Hetiang dinhmun hi i neih chuan i ha enkawltu ha enkawltu nen hnaih taka thawh dun a ngai a ni. I ha venhimna atana fimkhur zual a ngai chu a lungchhiatthlak hle a, mahse, i ha venhimna atana pui thei tur enkawlna a awm tih hre reng ang che. Tin, i nuihzatnaah i lungawi loh chuan a hmel titha thei tur enkawlna a awm bawk. Hun engemaw chen a la ngai thei a, mahse nang leh i ha enkawltu chuan i ha enkawl turin hma i la thei a ni. Ngaihtuah buai suh, okay? Hriatna leh enkawlna dik tak nen chuan he natna hi enkawl theih a ni.

` Amelogenesis Imperfecta, Ha Enamel, Genetic Diseases, Ha rawng thlak danglam, Ha enkawl dan, Ha hriselna, Ha harsatna