I doctor chuan nangmah emaw, i chhungte emaw thisen chhuak nghal mai tur control turin injection bik a pe em? A hming avang hian i buai deuh mai thei. Mahse, lungngai suh. Vawiin hian chu damdawi chu kan sawi dawn a ni. Acquired Hemophilia A tih hming pu, thisen chhuahna control nan hman a ni tlangpui a, awlsam leh chiang takin sawi ila.
Acquired Hemophilia A hi eng nge ni?
A awlsam zawngin sawi ila, hei hi kan taksa thisen zam (blood clotting process) buaina a ni. A tlangpuiin kan inhliam hian kan thisen a zang a, thisen a chhuak tawh lo. Hei hi kan thisena protein bik, Factor VIII -te hian a pui a ni.
Mahse, Acquired Hemophilia A-ah chuan kan taksa hriselna (immune system) hian tihsual takin he protein Factor VIII an tih hi a rawn bei tan ta a ni. Heng antibodies te hi kan ti bawk . Hei hian thisen a hrual theihna a ti tlem a, a châng chuan chhan awm lovin emaw, hliam tenau emaw avânga thisen chhuah tam lutuk a thlen bawk. Hei hi congenital hemophilia ang a ni lo va, nun chhunga engtik lai pawha lo awm thei dinhmun a ni.
Chuti a nih chuan he vaccine (OBIZUR) hian engtin nge hna a thawh?
Tunah chuan buaina chu kan antibody ngei hian kan Factor VIII ngei hi a bei tih i hrethiam ta. Chuvangin doctor te chuan he vaccine bik hi hei hi solution atan an pe thin.
He damdawi hming hi sei viau mah se, a sawi hi a pawimawh hle a ni:
- Antihemophilic Factor: Hei hian hemophilia natna dotu, emaw thisen zam tipungtu thil tihna a ni.
- Porcine Sequence: Hei hi thil danglam bik a ni. "Porcine" tih hian vawk nena inzawm thil tihna a ni. He vaccine hi vawk thisen zam (blood clotting factor) awm dan (sequence) ang deuha siam a ni. Engvangin nge chutianga tih a nih? A chhan chu, kan taksaa antibodies te hian mihring Factor VIII hi an hre chiang a, an bei laiin, he vawk factor ang chiah hian a structure an hre lo. Chuvangin thisen zam (blood clotting process) chu beih lovin an pui thei a ni.
- Recombinant: Hei hian damdawi hi rannung atanga direct-a lak chhuah ni lovin, biotechnology (recombinant DNA technology) hmanga laboratory-a thianghlim leh him taka siam a ni tihna a ni.
A awlsam zawngin, he vaccine hian a tih chu thisen chhuah tam lutuk control hi a ni a, antibodies-in a nghawng loh nan i taksain a clot a ngai factor a pe a ni.
He damdawi hi i ei hmaa i doctor hnena i hrilh tur thilte
Hei hi damdawi bik a nih avangin enkawlna i tan hmain i doctor hnenah i medical history kimchang hriattir hmasak a pawimawh hle .
| I hriat tur chu | Engvangin nge chu chu? |
|---|---|
| Allergy nei te pawh a awm | He damdawi, vawk sa protein, hamster protein (damdawi thenkhat siamna atana hman), emaw damdawi dang, ei tur emaw, dye emaw i allergy i neih chuan i doctor hnenah hrilh ngei ang che. |
| Naupai emaw, nau hnute pek emaw | Naupai emaw, nau pai tum emaw, nau hnute i pek emaw a nih chuan doctor hriattir a pawimawh hle. |
He damdawi hi engtin nge i hman?
Hei hi damdawi pangngai pill ang maia i ei tur a ni lo. Hei hi thisen kal tlanga injection a ni . He enkawlna hi damdawi inah emaw clinic-ah emaw doctor emaw nurse emaw trained ten an pe tlangpui a ni. Hei hi a chhan chu enkawlna pek chhung hian uluk taka enkawl i mamawh vang a ni.
A tlem hle a, damlo thenkhat chu in lama he vaccine hi dawng turin an hrilh thin. Chutiang a nih chuan a buatsaih dan tur leh a inject dan tur dik tak zirtir i ni ang. Doctor-in a tih aia tam ei ngai suh la, damdawi chu a hun ruat aia hmain ei ngai suh.
Damdawi dose tihpun a nih chuan eng nge tih tur?
Dose pek aia tam i ei nia i hriat chuan Colombo National Hospital-a National Poisons Information Center-ah call nghal la, damdawi in hnai ber Emergency Treatment Unit (ETU)-ah kal nghal rawh.
Dose pakhat ka miss a nih chuan engtin nge ni ang?
He enkawlna chhung hian a hun taka dose ei a pawimawh hle. Damdawi inah appointment i neih loh chuan doctor ko nghal la, thurawn la rawh. In lama damdawi i ei a nih chuan i hriatreng veleh missed dose kha ei nghal rawh. Mahse, dose dang pek hun a nih dawn chuan missed dose chu skip la, a hun ruatah dose dang ei leh rawh. Eng thil vang pawhin double dose ei loh tur.
Enkawl laia ngaihtuah tur thil
- Thisen Test: He damdawi hi i ei lai hian i doctor chuan thisen test mumal tak a ti ang a, a thawk tha em tih te, i thisen a khalh dan te, i taksain damdawi laka antibody thar a siam em tih te a enfiah ang. Heng test te hi skip loh a pawimawh hle.
- Damdawi lam enkawlna: Damdawi ina i awm lai hian damdawi lam thawktute’n uluk takin an lo vil reng ang che. Thisen chhuah leh allergic reaction awm thei te chu an lo thlir reng dawn a ni.
- Medical ID: Hemophilia i vei a nih chuan i dinhmun, damdawi i ei dan, a hman dan tur leh a hun tur te ziakna medical ID card emaw bracelet/chain emaw i keng reng a pawimawh hle. Emergency-a i nunna chhanhimna kawngah a pui thei a ni.
Side effect awm thei te chu engte nge ni?
Damdawi dang ang bawkin he damdawi hian side effect a nei thei a, mi zawng zawngin an vei lo nachungin. A hnuaia symptoms te hi i neih chuan doctor emaw nurse emaw hnenah hrilh nghal rawh.
| Side effect chi hrang hrang | Natna |
|---|---|
| Allergic Reaction na tak tak a awm thei | Skin rash, itching or hives, hmai, hmui, lei emaw ril emaw a hring, thawk harsa. Hengte hi a pawi hle thei a, report nghal tur a ni. |
| Inhibitor Hmasawnna | Damdawi i ei hnuah pawh thisen chhuahna i control thei lo a nih chuan i taksa pawhin he damdawi laka antibody a siam tan tawh mai thei tihna a ni. Hemi chungchang hi i doctor hnenah hrilh rawh. |
He list-a tarlan loh symptom dang danglam tak i neih chuan i doctor nen pawh chutiang lam chu sawipui rawh.
Damdawi dang nena inzawmna
Damdawi dang i ei lai hian he vaccine hi a inzawm thei a, a bik takin Factor VIIa hi a inzawm thei a ni.Hei hi thisen tihthianghlimna damdawi dang nena i hman hunah fimkhur hle tur a ni a, chungte chu:
Chuvangin, i doctor hnenah damdawi i ei zawng zawng (prescription damdawi, vitamin, herbal remedies, leh supplement) list kimchang pe rawh. Tin, zu i in emaw, zu i in emaw chuan doctor hnenah hrilh bawk ang che.
Take-Home Thuchah a ni
- He vaccine hi Acquired Hemophilia A an tih, natna hlauhawm tak, thisen chhuah tam lutuk control nan hman a ni.
- Hei hi enkawlna bik a ni a, thisen zam (vein)-ah inject a ni a, a tlangpuiin damdawi inah an pe thin.
- I allergy zawng zawng leh damdawi dang i ei zawng zawng chu i doctor hnenah hrilh ngei ang che.
- Allergy symptoms na tak (vun vun rawng, vun hring, thawk harsa) i neih chuan doctor rawn nghal rawh.
- Thisen test leh doctor-in appointment a pekte chu skip suh.
- He damdawi hi i tan chauh a ni. Midang hnenah share ngai suh. Zawhna i neih chuan doctor nen inbia ang che.











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