I fate chu doctor-in pianpui thinlung natna a neih thu a hrilh hian hlauhna leh mangang taka awm hi thil pangngai a ni. Mahse, lungngai suh. Vawiina kan sawi tur dinhmun, Coarctation of the Aorta tih hi i hre chiang a nih chuan hlawhtling takin i tuar thei ang. Eng nge a nih, engvangin nge a lo awm tih leh eng nge tih theih tih hi awlsam takin han thlir ila.
Coarctation of the Aorta (CoA) tih hi eng nge ni?
A awlsam zawngin sawi ila, Coarctation of the Aorta (CoA) hi pianpui thinlung natna a ni. Kan thinlung atanga kan taksa peng dang thlenga oxygenated thisen phurtu thisen kalna bulpui aorta hmun thenkhat a zim chuan a thleng thin. “Coarctation” tih thumal hi a awmzia tak chu “narrowing” tihna a ni.
Colombo-Galle Road-a lirthei tlan tam lutuk laiin kawngpui lane pakhat kha khar nghal a nih chuan eng nge thleng ang tih han ngaihtuah teh? Lirthei zawng zawng chu an kal tan vek ang a, traffic jam lian tak a awm ang. Chu chu kan taksaa thisen kalna kawng lian ber pakhat a inkharkhip chuan a thleng thin. Thisen chu a luang tha thei dawn lo.
He blockage hi taksa hnuai lam panna thisen phurtu vein te inthen hmain a thleng tlangpui. Hei hian thinlung atanga a chunglam (kut, lu) thlenga thisen sang a tisang a, thisen atanga taksa hnuai lam (ke) thlenga thisen sang a ti tlahniam bawk. Dik tak chuan, he inthlauhna lian tak hi doctor-in i naute kut leh kea thisen sang a enfiah hunah a hmuh tur hi he natna hriat theihna atana clue lian ber pakhat a ni.
Eng nge a lan chhuah dan? Nausen leh naupang upa zawkte hi an danglamna a awm em?
Blockage nasat dan azirin symptoms a inang lo. Blockage a nasat chuan naute hian a pian atanga kar khat emaw kar hnih emaw chhungin symptoms a lantir tan thei a ni. Mahse, blockage a tlem hle a nih chuan naupan lai thlengin symptoms a lang lo thei a, a awm lo thei bawk.
| Kum hrang hrang | A lan chhuah dan tlangpui |
|---|---|
| Nausen piang thar (Nausen) . |
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| Naupang leh Puitling tan |
|
Naupang thenkhat chuan symptom engmah an hmu lo mai thei. A chang chuan, he harsatna hi an hmuhchhuah hmasak ber chu doctor-in an thisen sang chu damdawi in pangngaiah a enfiah a, a sang tih a hmuh hian a ni.
Engvangin nge hetiang hi a lo awm? A chhan engte nge ni?
Hei hi a chhan dik tak hriat ni lo mah se, doctor-te chuan genetic component a nei niin an ngai . Chumi awmzia chu nausen pum chhunga a lo seilian laia genetic change thenkhat lo awm hian aorta chu a siam tha thei lo thei tihna a ni.
Hei hi a chhan ber pakhat chu thisen kalna kawng te tak te , ductus arteriosus an tih khar dan inthlak danglam vang a ni.
Ngaihtuah teh, naute chu nu pum chhunga a awm lai chuan lungte hian hna a thawk lo. Tichuan thisen kalna kawng bik a awm a, chu chuan naute chu oxygen a hmu thei a ni. Naute a pian a, thawk a tan chuan he vessel hi a ngai tawh lo va, ni rei lo te chhungin a inkhar nghal vek a ni. Mahse a chang chuan hei hi a khar chuan a chhunga tissue thenkhat pawh aorta chhungah a hruai lut thei a, aorta pawh a inzawm khawm thei bawk.
Tin, naute genetic condition thenkhat, Turner syndrome ang chi te pawhin he CoA condition hi an vei theihna a sang hle bawk.
Enkawl loh chuan eng harsatna nge awm thei?
He natna hi a hmaa hriatchhuah leh enkawl a nih loh chuan hun kal zelah harsatna hrang hrang a awm thei a ni.
- Taksa pumpuiah thisen sang (Hypertension) a awm.
- Lung ruh a thim lutuk (left ventricular hypertrophy) .
- Lung (coronary artery disease)-a thisen pe chhuaktu arteries-a thau awm zat (coronary artery disease) chu a tlangpui aia hmaa awm.
- Aorta-a balloon ang maia bulge (aneurysm) emaw thluaka thisen kalna kawng emaw a awm.
- Thinlung hian thisen a pump tling thei lo dinhmun(heart failure) a lo awm thin.
Pawimawh tak chu heng harsatna tam tak hi natna hi a hmaa hriatchhuah leh enkawl a nih loh chuan a thleng chauh a ni. Chuvang chuan a rang thei ang bera Doctor hmuh a pawimawh hle.
Engtin nge doctor-te hian he natna hi dik taka an hriat theih?
Naupang cardiologist te hian he natna hi an hmuchhuak tlangpui. Hei hi naute taksa enfiahna hmanga tih a ni ber.
- Kut leh kea thisen sang inthlauhna enfiah .
- Neck leh groin-a pulse enfiah.
- Heart murmur tih hi a rilru leh hnungzang chunga stethoscope dah a nih chuan a ri danglam tak hriat theih a ni.
Hei bakah hian Echocardiogram (echo) , thinlung scan chu tih a ni a, chu chuan a natna hmuhchhuah chu a finfiah a, a blockage nasat zia hriat a ni bawk. A châng chuan CT emaw MRI scan emaw pawh a ngai mai thei.
Hemi nena lo awm thei thinlung natna dang
CoA vei naute 45% atanga 75% vel pawhin bicuspid aortic valve tih natna an nei bawk. Chumi awmzia chu thinlung atanga aorta thlenga thisen phurtu valve hian cusp pathum ni lovin pahnih chauh a nei tihna a ni. Chu bakah, thinlunga khur (atrial septal defect emaw ventricular septal defect) ang chi dinhmun pawh he natna nen hian hmuh theih a ni bawk.
Enkawlna kawng hrang hrangte chu engte nge ni?
Naupang kum zat, aortic stenosis zau zawng leh thinlung natna dang a awm leh awm loh a zirin enkawl dan tur a ni.
Inzai
Nausen leh naupang tê tête enkawlna ṭha ber chu zai hi a ni.
- End-to-end anastomosis hmanga resection: Hei hian a blockage te tak te chu cut chhuakin, a hrisel pahnih chu inzawm tir leh a ni.
- Resection with extended end-to-end anastomosis: Aorta bend-ah blockage a awm chuan he surgery buaithlak zawk hi tih a ni.
Naute pian tirh atanga natna lanchhuahna na tak nei te chu operation hmaa naute dinhmun tihngheh nan damdawi prostaglandin (PGE-1) te pek a ngai mai thei.
Cardiac Catheter hmanga tih a ni
Hei hi surgery aiin a awlsam zawk. Hetiang method hi blockage a tlem a nih chuan, emaw, operation hnua blockage a lo awm leh chuan hman thin a ni.
- Balloon angioplasty: Balloon ang chi hmanraw te tak te chu thisen kalna kawngah dahin a inkharkhipna hmun zau zawka tihzauh nan inflated a ni.
- Balloon angioplasty with stent placement: A block lai chu balloon hmangin an tizau a, a chhungah chuan mesh ang chi tube (stent) te tak te dahin, chu chu a block leh loh nan an dah a ni.
Ka fa hmalam hun chu eng ang nge ni ang?
Tunlai diagnostic method leh treatment hmasawn tak tak hmang hian CoA vei naupang chu nun pangngai, hrisel takin a nung thei a ni. Tun hma chuan heng damlote dam rei zawng chu kum 35 vel a nih laiin, tunah chuan kum 60 emaw a aia rei emaw chhung chu hrisel takin an nung thei tawh a ni.
A pawimawh ber chu, enkawl hnuah pawh i dam chhung zawng cardiologist clinic- ah i kal a ngai a ni.
Tichuan, Doctor, .
- Naupang thisen sang hi enfiah reng a ni.
- Scan ang chi test te hi thinlung hnathawh dan enfiah nan an ti thin.
- Lung hrisel ei leh in leh exercise chungchangah thurawn a pe.
- A tul chuan damdawi a pe thin.
I fain he natna hi a nei tih i hriat chuan zawhna tam tak i nei thei a ni. Engvangin nge hetiang hi a lo awm tih i ngaihtuah mai thei. Hei hi i sualna a ni lo tih hre reng ang che. I doctor leh medical team te chuan nang leh i fate tanpui nan theihtawp an chhuah ang. Zawhna zawt hreh suh la, i hlauhthawnna te sawi rawh.
Take-Home Thuchah a ni
- Coarctation of the Aorta (CoA) hi pianpui lung natna a ni a, taksa thisen kalna bulpui peng pakhat a inkharkhip a, a lo awm thin.
- Nausen piang tharte hian chaw pek harsa, mut tam lutuk, thawk harsa tih ang chi natna lanchhuahna a nei thei.
- He natna chhinchhiahna lian tak chu kut leh ke inkara thisen sang inthlauhna nasa tak a ni.
- Hei hi i sualna a ni lo. Lungngai suh, Doctor hmu rawh.
- He natna hi surgery leh tunlai enkawlna dang hmangin hlawhtling takin enkawl theih a ni.
- Naupang chu enkawl hnuah nun pangngai, hrisel tak hmang thei mah se, dam chhung zawng damdawi in tlawh chu tih ngei ngei tur a ni.
Coarctation of the Aorta Sinhala, Coarctation of the Aorta, Congenital heart disease, Naute thinlung natna, Naupang thinlung natna, Thisen sang, Congenital heart defect Sinhala











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