I ṭhiante nêna in nuih lai a, rang takin i hmui chu a rawn inhawng a, a nih loh leh i kawr chu hma lamah a inbeng nghal mai ang tih han ngaihtuah teh. A nih loh leh thinrim taka mi i biak lai hian i khup chu a chhuak thut a, leiah i thut a ngai a ni. Hetiang thil hi i tawng tawh em? Hlau suh. Vawiin hian he dinhmun hi sawi turin ka rawn kal a ni. Damdawi lamah chuan hei hi cataplexy kan ti thin.
Cataplexy hi eng nge ni tak tak?
A awlsam zawngin, cataplexy chu i harh laiin taksa peng hrang hrang hnathawh a hloh nghal vat a, rei lo te chhunga i taksa ruh hnathawh a hloh a, nuih, phurna, thinrim ang chi rilru natna nasa tak i neih hian a ni. Hei hi a takah chuan mutna lama harsatna narcolepsy an tih chhinchhiahna pawimawh tak a ni. Narcolepsy hi chronic (lifelong) condition a ni a, nitin mutthilh theih loh a thlen thin.
Cataplexy hian taksa ruh chak lohna a thlen thei a, chu chu a nasat loh atanga na tak thlengin a awm thei. Entîr nân, i hmai ruhte chu i thunun thei lo chauh thei a, chu chuan i hmui a ti tla a, i kawr chu hma lam hawiin tlem a hrual thei bawk. A nasat chuan i taksa thunun theihna zawng zawng i hloh a, leiah i tlu thei bawk.
Mahse hetah hian a pawimawh ber chu hetiang thil a thlen hian i fully conscious tih hi a ni . Syncope emaw seizure emaw lai angin i hriatna i hloh lo.
Hetiang dinhmun hi second tlemte atanga minute tlemte chauh a awm tlangpui. Chutah chuan a mah chauhin a tha leh ta a ni. Mi thenkhat chuan ni khatah vawi eng emaw zat an dawng a, thenkhat erawh chuan kum khatah vawi khat emaw vawi hnih emaw an dawng thung.
Cataplexy leh narcolepsy hi eng nge an danglamna?
Mi tam tak chuan an pahnih hi an ti buai hle. Cataplexy hi narcolepsy symptom pakhat chauh a ni. Narcolepsy hi chi hnih a awm a. Cataplexy awm leh awm loh a zirin an pahnih hian an thliar hrang a ni.
| Narcolepsy chi hrang hrang | Cataplexy a awm em? | Hrilhfiahna |
|---|---|---|
| Narcolepsy chi hrang hrang 1 | Ni e, a awm. | Heng mite hian cataplexy an nei a. An thluaka neurotransmitter orexin (hypocretin) level hniam tak an nei a. Hetiang dinhmun hi nitin mutthilh lutuk nen a inzawm a ni. |
| Narcolepsy chi 2 a ni | Aih. | Heng mite hian cataplexy an nei lo. An thluaka orexin level hi a level dik takah a awm tlangpui. |
Hetiang thil a thlen hian engtin nge naupangte hian an tuar?
Naupangte zingah Cataplexy hi a danglam deuh hlek a. A tam zawk chu hmai, hmui leh mitmeng ruh te a nghawng a ni. Natna nei emaw, huatna avanga nuihzatthlak emaw ang maiin a lang thei. Naupang thenkhat phei chuan he hun chhung hian an lei an chhuah chhuak ang.
Vawi tam tak chu naupang tê tê chunga hetiang thil a thlen hian, nu leh pate emaw, mi dangte emaw chuan ngaihsak lohna chhinchhiahna, rilru hahna, thinrimna, a nih loh leh ngaihven hlawh theihna kawng mai mai niin an ngai . Chuvangin, i fate nungchangah hetiang hriat theih loh inthlak danglamna i hmuh chuan doctor hnena hruai nghal a pawimawh hle .
Engvangin nge hetiang hi a lo awm? Eng nge a chhan?
Cataplexy thlentu ber chu narcolepsy type 1 a ni a , thluaka chemical (neurotransmitter ) orexin tih tlakchham vang a ni. He orexin hian kan harh reng theih nan a pui a, kan mut laiin REM sleep (kan mumang mutna thuk tak) a control bawk.
Tunah chuan REM mut kan neih hian kan taksa ruh thenkhat chu paralysis state-ah an kal hi thil pangngai a ni. Hei hi kan mumang ang thilte kan tih tak tak loh nan leh kan tan harsatna kan thlen loh nan a ni. Mahse Orexin a hniam chuan, kan harh lai pawhin, nuih ang chi emotion chak tak kan neih chuan kan thluak hian REM mutnaah kan awm niin a ngai. Tichuan chu mut chhunga paralysis lo awm chu kan la harh laiin a lo awm ta a ni. Chu chu cataplexy an ti a.
Engtin nge enkawl a nih?
He natna hi damdawi hmanga enkawl a ni ber. Damdawi i harh theihna tur leh cataplexy symptoms control nana hman thin damdawi ang chiah hi narcolepsy enkawlna atan hman a ni. I doctor chuan a enfiah ang che a, i tana tha ber tur damdawi a rawn pe ang che.
Cataplexy atana damdawi chi hrang hrang phalsak a awm a:
- Sodium oxybate a awm a
- Sodium hniam zawk oxybate a awm
- Pitolisant a ni
Hei bakah hian doctor ten hemi atan hian damdawi dang an pe thei bawk. Hei hian damdawi chu natna dang atana siam tak tak ni mah se, cataplexy tan pawh a thawk tha hle tihna a ni. Entirnan, antidepressant thenkhat (SSRI, SNRI, TCA) chu hemi atan hian an hmang thin.
A pawimawh ber chu enkawlna i tan tawh chuan i damdawi ei tur chu i doctor-in a hrilh ang chiah khan i ei a pawimawh hle a ni . I damdawi ei kha i chawlhsan nghal chuan i cataplexy chu a na hle thei a ni. Chuvangin i damdawi ei chungchangah zawhna i neih chuan i doctor nen inbia ang che.
Hetiang dinhmun hi ka nunpui lai hian engtin nge ka in enkawl theih ang?
Cataplexy hi ven theih a ni lo mai thei a, mahse mi tam tak chuan an chau lutuk ni-ah a thleng tam zawk niin an sawi. Chuvângin, mut ṭhat chuan a thunun theih nân kawng thui tak a zawh thei a ni.
A ṭangkai thei tûr thil tih dân awlsam ṭhenkhat chu hetiang hi a ni:
- Nitin hun khatah mut la, a rualin harh bawk ang che.
- I mutna pindan chu a reh ang a, thim la, temperature nuam takah dah rawh.
- Mutna hmun atang hian electronic devices TV, computer, leh phone te chu la chhuak rawh.
- Mut hma darkar hnih tal chaw rit tak tak, coffee leh zu ei loh tur a ni.
- Nitin exercise engemaw zat nei rawh. Zanah i mut that theih nan a pui ang che.
Chu bâkah, thil dang i tih theihte chu:
- Hriselna lam ngaihtuah rawh: Hriatna hloh nghal mai chu a hlauhawm thei hle a, a bik takin lirthei khalh emaw, hmun sang taka hnathawh emaw i nih chuan. Hemi chungchang hi i doctor nen sawiho la, inven dan tur zir rawh.
- Hemi chungchang hi midangte hrilh rawh: I chhungte, i thiante, leh hnathawhna hmuna mite hnenah he thu hi hrilh rawh. Chutiang chuan i chungah thil a lo thleng thut a nih chuan thil awmdan chu an hre chiang a, an hlau lo.
- Ṭanpuina dawng rawh: Hetiang dinhmun nena nun hi rilru lamah a harsa thei hle. Hetiang natna vei midang hmuh theihna tur support group-ah te tel ve rawh. Tin, hei hian lungkhamna emaw, lungkhamna emaw nasa tak a thlen che a nih chuan, i doctor emaw, rilru lam hriselna lama mithiam emaw, rilru lam doctor emaw, biak pawh hlau suh.
Nangmah emaw, i fa emaw hian heng symptoms te hi i neih chuan doctor pan hmasa phawt ang che. Hengte hi enkawlna hmanga control tha thei dinhmunte an ni.
Take-Home Thuchah a ni
- Cataplexy hi emotion chak tak karah taksa ruh hnathawh hloh a ni. Hei hi seizure emaw convulsion emaw a ni lo, i la hriatchhuah avangin.
- Hei hi Narcolepsy Type 1 chhinchhiahna pawimawh tak a ni a, thluaka chemical orexin tlahniam vang a ni.
- Naupangteah chuan hei hi kawng hrang hrangin a lang thei a, chu chu hmai hring emaw, lei chhuak emaw a ni thei. Heng symptoms te hi i hriat chuan doctor rawn la nghal rawh.
- He natna hi damdawi hmangin hlawhtling takin a control theih a ni. Doctor thupek zawm a pawimawh hle.
- Mut that a pawimawh hle a, i hnaih berte hnenah i dinhmun hriattir reng a, him taka awm a pawimawh hle.











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