I taksaah hian hliam pakhat emaw pahnih emaw chu rang takin i hmu a, "Wow, khawiah nge he thil hian a rawn deng?" Chutiang chuan a chang chuan hliam tenau te chu a awm fo thin. Mahse, chhan awm lovin i taksa pum puiah hliam i tuar a nih chuan, ha i sil laiin i hmuiah thisen a chhuak a nih chuan, emaw, i hliam tenau pawhin thisen a chhuah loh chuan ngaihtuah tur a ni. Vawiin hian natna lan chhuah dan ang chi kan sawi dawn a, mahse mi tam tak chuan an hre lo. Chu chu ITP a ni.
A awlsam zawngin ITP chu eng nge ni?
He natna hming kimchang, ITP tia tawifel chu Immune Thrombocytopenia tih a ni. Hei hi thisen kaihhnawih natna awm lo tak a ni.
Ngaihtuah teh, kan thisenah hian cell part te tak te, ``Platelets`` an tih te hi a awm a. Kan taksaah sipai te tak te ang mai an ni. Khawi emaw laiah hliam emaw hliam emaw a awm chuan heng platelet te hna ber chu chutah chuan tlan chak a, inzawm khawm a, thisen chhuah tihtawp a ni.
Tunah chuan, ITP vei mi pakhat chunga thil thleng chu hetiang hi a ni. Kan taksa natna laka humhimtu immune system chu a kal nghal vat a. Chu buaina avang chuan immune system chuan kanmahni ‘sipai’ tha tak tak, platelet te chu pawn lam atanga hmêlma angin a hre sual a ni. Tichuan, chu signal dik lo avang chuan immune system chuan heng platelet te hi a tichhia tan ta a ni.
A awlsam zawngin, ITP chu mahni invenna system-in kan thisen tichhe thei platelet a tihchhiat hian a ni. Hei hian thisena platelet count chu a pangngai aia hniam takin a ti tlahniam a ni.
Platelet a tlahniam chuan thisen chhuah tihtawp theihna pawh a tlahniam bawk. Chuvangin a tul lovah i hliam tan a, thisen a chhuak tan bawk.
ITP chi hrang hrangte chu engte nge ni?
ITP hi eng chen nge a daih tih a zirin chi thumah then a ni. Hei hi i hriat a pawimawh hle.
| ITP chi hrang hrang | Hrilhfiahna |
|---|---|
| Acute ITP (hun rei lote chhunga ITP) 1.1. | Hei hi thla 3 aia rei lo a ni. Naupang tê tê (a bik takin kum 2-5 inkar)-ah virus infection, khawsik emaw flu emaw atanga an dam leh hnuah a awm fo thin. Vanneihthlak takin enkawl ngai lovin a reh fo thin. |
| ITP awm reng | Hetiang chi hi thla 3 leh thla 12 inkar a ni. |
| ITP rei tak awm tawh | Hei hi kum khat chuang a daih a ni. Hetiang chi hi puitlingah a lo awm tlangpui. A châng chuan naupang tê têah pawh a lo awm thei bawk. Hun rei tak enkawl a ngai mai thei. |
ITP natna lan chhuah dan chu engte nge ni?
Platelet count a hniam lutuk hian symptoms a lang chhuak thin. Mi thenkhat chuan a tir lamah symptom an nei lo mai thei.
- Sudden bruising: Sudden, blue-purple bruises taksaah hian engmah trauma awm lovin a lo lang thin.
- Vunah a sen: Pinprick te tak te ang maia lang, a bik takin ke hnuai lam ah chuan sen-purple (`petechiae`) a awm. Hengte hi a takah chuan vun hnuaia thisen kalna kawng te tak te atanga thisen chhuak an ni.
- Hmun lian tak tak: A chang chuan a sen, sen, a sen (`Purpura`) lian tak tak a lo lang thin.
- Ha kha thisen chhuak: I ha i ha sil lai leh i ding mai mai lai pawhin i hmui a thisen a chhuak thei.
- Hnar thisen: Hnar thisen a lo chhuah tan tawh chuan tihtawp a harsa thei hle.
- Zun emaw, ek emaw-a thisen: Hei hi a nasat deuh deuh a ni.
- Hmeichhiaah thlasik laiin thisen chhuak nasa: Ni 7 aia rei thlasik hun leh thisen chhuak nasa.
- Chauhna danglam tak: Chauh lutuk leh hah lutuk chu chhan awm lovin hriat theih a ni.
ITP awm chhante chu engte nge ni?
Kan sawi tawh ang khan ITP awm chhan ber chu immune system lama harsatna vang a ni. Amaherawhchu, he harsatna lo awm chhan a zirin ITP hi chi hnih ah then theih a ni.
1. Primary ITP: Hetiang ITP-ah hian pawn lam atanga chhan chiang tak a awm lo. Immune system chu a thawk tha lo mai mai a ni.
2. Secondary ITP: Hetiang a nih chuan ITP hi damdawi lam thil dang emaw, hri kai emaw avanga lo awm a ni. Entir nan:
- Viral infection `HIV` emaw `Hepatitis C` emaw ang chi te.
- Bacterial infection te ang chi `H. pylori` tih a ni.
- Autoimmune natna dang lupus ang chi te.
- Hetiang dinhmun hi damdawi thenkhat vang pawh a ni thei.
Diagnosis leh enkawl dan
Hetiang symptoms i neih chuan, .I tih hmasak ber tur chu doctor pan a, thurawn lak hi a ni. Hlau suh. Doctor chuan i medical history a zawt ang che a, i taksa a enfiah ang.
Tichuan, heng symptoms awm chhan dang a awm leh awm loh enfiah turin test thenkhat an order ang.
- Full Blood Count (FBC/CBC): Hei hian i platelet count a hniam zia chiang takin a hrilh che a ni.
- Peripheral Blood Smear: Hetah hian thisen tla khat lak a ni a, microscope hmangin platelet awm dan enfiah a ni.
- Test dang: HIV leh Hepatitis C ang chi infection te pawh test i ni thei bawk.
Engtin nge enkawl a nih?
ITP vei zawng zawng hian enkawlna an tan nghal vek dawn lo. I doctor chuan i platelet count, i symptoms nasat dan leh thisen chhuah theihna i neih dan a zirin enkawlna i tan leh tan loh tur chu a rel ang.
Enkawlna a ngai a nih chuan enkawlna bulpui engemaw zat a awm a, chungte chu:
- Corticosteroids: Hengte hi damdawi chi hrang hrang pek hmasak ber a ni. Heng damdawi te hian immune system hnathawh control-in leh platelet tihchhiatna a titawp a ni.
- Intravenous Immunoglobulin (IVIG): Hei hi vein (saline solution ang chi) hmanga enkawlna a ni. Thisen chhuak nasa tak a awm chuan i platelet count a tipung nghal vat thei a ni.
- Platelet Transfusion: Thisen chhuak na tak, nunna atana hlauhawm (entir nan, thluaka thisen chhuak) a awm chuan, mi hrisel atanga platelet lak chu emergency angin pek a ni.
- Damdawi dang: Enkawlna hmasa berin natna a thunun loh chuan platelet siam chhuah tipung thei damdawi (`Eltrombopag`, `Romiplostim`) emaw, kawng danga immune system control thei (`Rituximab` ang chi) emaw pek thin a ni.
- Splenectomy: Kan taksaa platelet tihchhiatna hmun lian ber chu kan taksa a ni. Damdawi hmanga natna hi tihreh theih a nih loh chuan doctor-te chuan mi thenkhat tan chuan surgery hmanga an ril (spleen) lakchhuah an rawt a ni.
ITP nena kan khawsak huna ngaihtuah tur thil
Chronic ITP hi i bulah rei tak a awm thei a ni. Chuvangin, nun pangngaia i nun ruala chetsualna leh thisen chhuah laka inven nan thil tenawm te i enkawl a ngai a ni.
A pawimawh ber chu, Doctor nen inbia lovin natna tidamtu damdawi emaw, damdawi dang emaw ei loh tur a ni. A bik takin damdawi `Aspirin` leh `Ibuprofen` te hian thisen chhuah theihna a tipung.
- Hrisel takin awm rawh: Rugby leh football ang chi contact sports te hi pumpelh rawh. Bike i khalh chuan helmet vuah ngei ngei tur a ni.
- Tothbrush nem tak hmang rawh: Hei hian hah hliam a veng thei a ni.
- Thil hriam tak i hman hunah fimkhur rawh: Knife leh nail clipper ang chi thil i hman hmain vawi hnih ngaihtuah hmasa phawt ang che.
- Stress tihziaawm: Yoga leh meditation ang chi thil hmanga i rilru tih hahdam hi a pawimawh hle.
Take-Home Thuchah a ni
- ITP hi nangmah ngeiin i immune system hian platelet a tichhia a, chu chuan thisen a tichhe thei a ni.
- Chhan awm lova i hliam emaw, thisen chhuak fo emaw i nih chuan ngaihthah suh la , doctor pan nghal rawh.
- ITP hi cancer a ni lo va, kai theih a ni lo bawk.
- Mi tam zawk chuan damdawi hmangin he natna hi an enkawl tha thei a, nun pangngai an hmang thei bawk. Mi thenkhat tan, a bik takin naupang tan chuan a mah chauhin a reh thin.
- ITP i neih chuan i doctor thurawn lo chuan damdawi (a bik takin natna tidamtu) engmah ei loh tur a ni.











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