Congenital heart defect chu enkawl loh a nih chuan engtin nge ni ang? Eisenmenger Syndrome chungchang hi zir rawh

Nausen piang, an thinlunga khur neia an pian thu i hre ngai em? A tam zawkah chuan enkawl vat a nih chuan hei hi harsatna a ni lo. Mahse, a chang chuan heng natnate hi enkawl loh chuan hun kal zelah harsatna lian tak takah a chang thei a ni. Chu chu Eisenmenger Syndrome kan tih chu a ni. Hei hi thupui buaithlak deuh ni mahse, vawiinah hian awlsam takin kan sawi dawn a, in hriatthiam theih tur angin.

A awlsam zawngin, Eisenmenger syndrome chu eng nge ni?

Hei hi hrethiam tur chuan thinlung hnathawh dan hi i hre hmasa phawt ang u. Kan thinlung hi pindan pali nei in ang maiin han ngaihtuah teh. Chamber chunglam pahnih leh a hnuai lam chamber pahnih a awm. Thinlung dinglamah hian thisen "bawlhhlawh" a awm a, chu chu taksa pum puiah a kal kual tawh a, oxygen a tlem hle . He thisen hi oxygen pek theih nan lung- ah thawn chhuakin "thianghlim" a ngai a ni. Thinlung veilam ah hian thisen "thianghlim" a awm a, chu chu lung atanga luang chhuak tawh, oxygen khata khat a ni. He thisen hi taksa pum puiah pump chhuah a ni. A tlangpuiin heng lehlam pahnih inkarah hian thisen a inhmeh lo.

Tunah chuan, thinlung pindan inkar (entir nan) bang chhunga khur neia piang i nih angin han mitthla teh. Thinlung veilam a pressure chu dinglam aiin a sang zawk. Chuvangin, a tir lamah chuan oxygen tamna thisen thenkhat chu chu khur atang chuan dinglam lamah a kal a, oxygen tlakchhamna thisen nen a inhmeh ta a ni. Hei hi left-to-right shunt kan ti a ni. Hei hian lung chhunga thisen kal zat chu a tul lovah a tipung a ni.

A tâwpah chuan lung chhûnga pressure a lo pung êm êm a, thinlung dinglamah pressure chu veilam aiin a sang zâwk ta a ni. Chuti a nih chuan eng nge thleng? Thisen kal dan chu a inher chhuak vek a ni. Chumi awmzia chu tunah chuan thisen "bawlhhlawh", oxygen tlakchhamna chu lungah a kal lo va, tihfai a ni tawh lo va, chu khur atang chuan veilam lamah a kal nghal a, taksa pum puiah a pump chhuak ta tihna a ni. Hei hi dinglam atanga veilam shunt kan ti a ni .

Hetianga oxygen tlachham thisen taksaa pump luh avanga symptoms leh complications awmkhawm hi Eisenmenger Syndrome kan tih hi a ni.

Hetiang natna lan chhuah dan hi engte nge ni?

A natna lan chhuah dan ber chu taksaa oxygen tam tawk lo (hypoxemia) avanga lo awm te hi a ni. Heng symptoms te hi tleirawl emaw puitling emaw ah a lang tlangpui a, mahse a chang chuan naupan lai atang pawhin a intan thei bawk.

Engvangin nge hetiang hi a lo awm? Thinlung chhiatna hnuaia awmte chu engte nge ni?

Kan sawi tawh ang khan he natna hi pianpui heart defect enkawl loh avanga lo awm a ni. Entirna thenkhat chu hetiang hi a ni:

• Atrial septal defect ( ASD ): Thinlung chunglam chamber pahnih (atria) inkar bang chhunga khur awm.
• Ventricular septal defect ( VSD ) atanga lo chhuak a ni.Thinlung hnuai lam chamber (chamber) pahnih inkar bang chhunga khur awm.
• Patent ductus arteriosus (PDA): Aorta leh pulmonary artery inzawmna dik lo, nau neih hnua khar tur.
• Atrioventricular septal defect: Thinlung lai takah khur lian tak a awm a, chubakah thinlung valve- ah harsatna a awm bawk .
• Single-ventricle defect: Lung hnuai lam chamber pahnih zinga pakhat chauh hian hna a thawk tha hle.

Hetiang dinhmun avanga harsatna lo awm thei dangte chu:

Eisenmenger syndrome hian thinlung leh lung chauh a nghawng lo. Taksaa oxygen level hniam hian harsatna dang tam tak a thlen thei a ni.

• Secondary erythrocytosis: Taksa hian oxygen thlak nan a mamawh aia tam thisen sen a siam chhuak a , chu chuan thisen a ti thim thei a, thisen zam a tipung thei bawk.
• Thisen chhuak pangngai lo: Thisen khuh, hnar thisen, thlasik rit tak, leh hmui thisen chhuak ang chi thil.
• Heartbeat irregularities (Arrhythmias): Thinlung thawk mumal lo.
• Thisen zam: Heng thisen zamte hi thluaka a kal chuan stroke ang chi natna khirh tak tak a awm thei a ni.
• Thluak ah hian abscesses a awm.
• Kut zungtang clubbed tak tak te.
• Kidney hnathawh that lohna.
• Lung lam chak lohna.
• Lung natna (infective endocarditis) a awm thei.
• Iron tlakchhamna avanga thisen tlakchhamna.

Naupai laiin risk sang tak a ni

Hei hi thil pawimawh tak a ni. Eisenmenger syndrome vei hmeichhia tan naupai hi a hlauhawm hle a, nunna pawh a hlauhawm hle . Naupai lai hian thinlung leh thisen kalna system hian stress a tuar thei lo va, chu chuan nu emaw naute emaw, a pahnih pawhin thihna a thlen thei a ni.

Doctor-te hian engtin nge hei hi an hmuh?

I doctor chuan i symptoms leh medical history a zirin hei hi a ringhlel mai thei. A finfiah nan test eng emaw zat an nei dawn a ni.

• Thisen test dan: 1.1.Red blood cell count leh harsatna dang hriat duh tan.
• Echocardiogram (Echo): Thinlung hnathawh dan, a insiam dan leh a khur awmna hmun enna scan a ni.
• Electrocardiogram (ECG/EKG): Thinlung electric hnathawh leh rhythm enfiah nan.
• Heart Catheterization: Test pawimawh tak a ni a, chu chu thinlung leh lung chhungah tube te tak te dahin chutah chuan pressure dik tak teh a ni.
• Pulse oximetry: Kut zungtang-a hmanraw te tak te hmanga thisen chhunga oxygen awm zat tehna.
• Exercise stress test: Exercise neih laiin thinlung leh oxygen level a inthlak dan enfiah.

Engtin nge enkawl a nih? Hei hi tihdam theih a ni em?

Hetah hian hriatthiam tur pawimawh tak chu Eisenmenger syndrome a lo awm tawh chuan a thlentu thinlung chhiatna (hole) hmasa ber chu surgery hmanga khar theih a ni lo Chutianga tih a nih chuan lungin pressure sang tak, lung chhunga pressure sang tak lo awm tawh chu a tuar thei dawn lo va, harsatna na tak tak leh thihna thlengin a thleng thei a ni.

Chuvangin, enkawlna tum ber chu natna lan chhuah dan control te, nunphung tihchangtlun te, harsatna lo thleng tur venna te a ni.

• Pulmonary hypertension (PAH) therapies: Hengte hi enkawlna bulpui ber a ni. Heng damdawi te hian lung chhunga thisen kalna pressure a tihziaawm a, thawk hah ang chi symptoms te chu a ti reh a ni.
• Antibiotics: Damdawi lam thil thenkhat, ha lak chhuah hmaa antibiotics pek thin a ni a, chu chu thinlunga natna darh zel tur venna atan a ni.
• Damdawi lam enkawlna hnuaia exercise: Hei hian i thawk leh chakna a tichak thei a ni. Doctor rawn hmasa lovin mahni chauha exercise lak ngai suh.
• Iron pill emaw injection emaw: Iron tlakchhamna a awm chuan enkawl nan.
• Supplemental oxygen: Hei hi thisen a oxygen level tihsan nan damlo thlan bik thenkhat tan a tha hle.
• Thisen tithianghlimtu: Hei hi fimkhur tak leh damdawi lam thurawn chauha hman tur a ni.
• Heart emaw heart and lung transplant: End-stage damlo, damdawi hmanga an dinhmun control theih loh tan chuan duhthlan tur a ni.

Engtin nge ka in enkawl ang?

Hetiang dinhmun nena nunpui lai hian i lam atanga i tih tur tlemte a awm.

• Meizial zuk loh vek tur a ni. Hei hian dinhmun a tichhe zual ang.
• Tui tam tak in la, chu chuan dehydration a veng ang.
• Ei leh in tha tak ei rawh.
• Hri kai laka inven nan a hun takah vaccine tul tak tak lak thin ang che.
• Chutiang natna rei tak nena nunpui avanga lungkhamna hmachhawnCounselling dawng rawh .

I dam chhungin cardiologist leh pulmonologist enkawlna hnuaiah i awm dawn a, chuvangin an thupek dik taka zawm a pawimawh hle.