Fibromuscular Dysplasia (FMD) tih natna hi i hre tawh em? A ni lo mai thei. Condition danglam deuh deuh a ni. Mahse a chanchin hriat a pawimawh hle thei. A chhan chu kan taksaa thisen kal dan nen a inzawm tlat a ni. Chuvangin vawiin hian he FMD chungchang hi i hriatthiam theih tur awlsam takin i sawi dawn nia.
Fibromuscular Dysplasia (FMD) hi eng nge ni?
A awlsam zawngin, Fibromuscular Dysplasia , a nih loh leh FMD kan tih ang chi hi kan taksa chhunga thisen kalna kawng (arteries walls)-a cell awm dan pangngai lo taka lo thanglian a ni. Tunah chuan arteries te hi eng nge ni tih i ngaihtuah mai thei. Arteries chu kan thinlung atanga kan taksa chhunga tissue dang zawng zawnga thisen phurtu thisen kalna kawng a ni. Tui dahna atanga in chhung hmun tinah tui phurtu plumbing system ang bawkin heng thisen kalna kawngte hian kan taksaah thisen an pe bawk.
Chuvangin, he FMD dinhmun avang hian i thisen kalna kawng, chu chu thisen kalna kawngte chu a inkhar thei a, a hring thei a, a nih loh leh zungbun hrui ang maiin a lang thei a, hmun thenkhatah a inkhar a, hmun thenkhatah a hring thei bawk Tui pipe chu hmun hrang hrangah a inkhar a, a tikehsawm a nih chuan tui luang tur a tikhawlo ang tih han ngaihtuah teh, he FMD hian thisen kal pawh a tikhawlo thei bawk.
FMD hian eng arteries nge a nghawng theih?
Hetiang dinhmun, FMD an tih hian kan taksa peng hrang hranga thisen kalna kawng (arteries) a nghawng thei a ni. Arteries chi hrang hrang a nghawng thei a, chungte chu:
- Carotid arteries: Hengte hi i kawr chhungah a awm a. Heng arteries te hian i thinlung atanga thisen chu i thluak thlengin an phur a. Heng vessels-ah hian thil a thleng a nih chuan i thluaka thisen kal zat chu a tlahniam thei a ni.
- Renal arteries: Heng arteries te hian i thinlung atanga thisen chu i kal (kidney) thlengin a phur a, chu chu kan taksa atanga bawlhhlawh paih chhuaktu organ pawimawh tak a ni.
- Coronary arteries: Hei hi thinlung chhung ngeia thisen pe chhuaktu thisen kalna kawngte an ni. Heng arteries te hi thinlung hnathawh that nan a hrisel a ngai a ni.
- Mesenteric arteries: Heng arteries te hian thisen chu i intestines ah a phur lut thin. Kan chaw ei tur hi an digest theih nan an function tha a ngai a ni.
- Arteries dang: Hei bakah hian FMD hian i ke, i kut emaw, i taksa peng dang emawa thisen phurtu thisen kalna kawngte pawh a nghawng thei bawk.
Tute nge FMD vei theihna sang zawk?
FMD hian tu pawh a nghawng thei a, mahse mi thenkhat chuan he natna hi an nei tam zawk. Mak tak maiin FMD vei zinga 90% aia tam chu hmeichhia an ni . Kum 40 leh 70 inkar ah pawh a tam ber bawk .
Tin, damdawi lam thil dang thenkhat pawh FMD ang chi symptom nei thei an awm bawk. Chuvangin, doctor-te pawhin heng dinhmunte hi an ngaihtuah hle a ni:
- Ehlers-Danlos natna a ni
- Loeys-Dietz natna a ni
- Neurofibromatosis chi khat a ni
- Williams syndrome tih hi a ni
- Thisen kalna kawng lian tak tak vasculitis (`Large vessel vasculitis`) .
- Atherosclerosis natna a ni
- Systemic arterial mediolysis hmanga tih a ni
FMD hi engtiang chiahin nge a awm?
Dik tak chuan scientist te tan chuan FMD vei engzat nge awm tih chiang taka sawi a harsa hle. Because many people don’t have symptoms , emaw, natna dang test-naah accident-a hmuhchhuah a nih avangin, chu natna chu i nei mai thei a, mahse i hre lo mai thei.
FMD chi hrang hrangte chu engte nge ni?
FMD hi doctor ten an enfiah huna thisen kalna kawng (arteries) a lan dan a zirin chi hnih lian takah then theih a ni.
1. Multifocal FMD: Hei hi a tam ber chi a ni . Hetiang chi-ah hian thisen kalna kawngte chu zungbun hrui ang mai a ni . Chu chu, arteries te chu hmun thenkhatah dilated a ni a, chutah chuan a tawi a, a dilated leh a, a narrow leh a... chutiang pattern-ah chuan.
2. Focal FMD: Hetiang chi hi a tlem zawk hle . Artery block emaw, artery wall-a tissue (lesions) pangngai lo siam emaw a ni.
Eng thilin nge FMD hi a thlen?
Vanduaithlak takin scientist-te chuan FMD thlen chhan chiang tak an la hmu lo a , mahse thil engemaw zat a inrawlh nia ngaih a ni:
- Genetic factors: A then phei chuan hei hi thlahtute atanga lo chhuak a ni thei.
- Hormone: Taksa hormone level inthlak danglamna a awm thei nia rinhlelh a ni a, a bik takin hmeichhiaah a tam zawk avangin.
- Artery wall chhiatna: Arterial walls hi repeated strain ang chi thilin a tichhia thei a ni.
- Thil thenkhat, meizuk ang chi hian FMD a ti na zual thei. Chuvang chuan zu i in a nih chuan bansan a pawimawh hle.
FMD natna lan chhuahna chu engte nge ni?
FMD natna lanchhuah dan hi a natna vei artery a zirin a inang lo . FMD vei thenkhat chuan symptom engmah an nei lo mai thei . Mahse, mi dangte chuan thisen kal dan khap a nih avanga symptoms an nei thei a ni. Chung zingah chuan:
- Bruit: Doctor-in stethoscope hmanga i kawr emaw, i pum emaw a ngaihthlak hian thisen luang ri nen hian ‘swooshing’ thawm danglam tak a ri a.
- Vertigo: I chhehvela inher emaw, inher emaw tih hriatna.
- Thisen sang emaw, thisen sang thunun loh emaw.
- Migraine lu na.
- Kawng a na.
- ‘Swooshing’ ri emaw beng chhunga ri emaw hriat.
Ngaihtuah teh, Nilanthi hi a luak chhuak reng a, a chang chuan a beng atang chuan thawm mak tak mai a hre thin. Hei hi thil pangngai tak niin a ngai a. Mahse doctor chuan a enfiah chuan a kawr atang chuan ``Bruit`` thawm a rawn chhuak tih a hre ta a. Test dang a neih hnuah chauh FMD a vei tih a hmuchhuak ta a ni.
FMD hian eng hriselna lama harsatna lian tak nge a thlen theih?
FMD hi enkawl tha a nih loh chuan hriselna lama harsatna lian tham engemaw zat a thlen thei , chuvangin hei hi hriat a pawimawh.
- Aneurysm: Balloon ang maia bulh chhuak artery chak lohna. Hei hi thluaka thisen kalna kawng (`brain aneurysm`) emaw, pum chhunga thisen kalna (`abdominal artery aneurysm`) emaw-ah a thleng thei a ni. Hei hi a rupture chuan nunna atana hlauhawm tak a ni thei.
- Arterial dissection: Artery chhung lam bang atanga tear chhuak. Entirnan, hei hi carotid artery (carotid dissection) emaw, thinlunga coronary artery (spontaneous coronary artery dissection) emaw-ah a thleng thei a ni.
- Thai.
- Transient ischemic attack (TIA), chu chu mini-stroke an ti bawk.
Hengte hi FMD avanga harsatna awm thei berte chu an ni. Chuvang chuan natna lanchhuahna i neih chuan damdawi lam pan vat a pawimawh hle.
Engtin nge FMD hi hmuhchhuah a nih?
A châng chuan FMD hi doctor-in routine check-up a tih hian (entir nan, ‘bruit’ ri hriat hian) a lo lang chhuak ṭhin. A nih loh leh, natna dang test-naah hmuhchhuah theih a ni bawk.
Doctor-in FMD i vei nia a rinhlelh chuan hetiang test hi a order thei ang:
- CT scan a ni.
- MRI scan (`MRI`) hmanga tih a ni.
- Ultrasound hmanga scan (`Ultrasound`) hmanga tih a ni.
- Angiography: Hei hian thil bik leh X-ray hmangin i thisen kalna kawng (arteries) a en thin.
Heng test te hian arteries inthlak danglamna, blockage leh swelling te chiang takin a hmu thei a ni.
FMD hi a dam kim thei ang em?
Vanduaithlak takin tunah hian FMD damdawi a la awm lo . Chu chu a damdawi a awm lo tihna a ni. Mahse, enkawlna hian natna lan chhuah dan a thunun thei a, harsatna a awm loh nan a pui thei bawk.
FMD enkawlna tur engte nge ni?
FMD enkawlna hi eng artery nge a nghawng tih, natna nasat dan leh i natna lan chhuah dan azirin a inang lo. Enkawlna lian ber berte chu:
- Blood thinners (Antiplatelet drugs or Anticoagulant drugs): Hengte hian thisen a tikhawlo thei lo va, stroke ang chi natna hlauhawmna a ti tlem bawk.
- Thisen sang damdawi: Entirnan, `ACE inhibitors` leh `Angiotensin receptor blockers` ang chi damdawi.
- Lu na leh natna enkawlna: 1.1.A chang chuan aspirin emaw botulinum toxin injection (Botox®) ang chi thil te pawh hman a ni.
- Angioplasty: Hetiang tih danah hian balloon te tak te tak mai chu catheter kaltlangin thisen kalna kawng chhungah an lut a, chu chu an inflated a, a block tawhna hmun chu a inhawng ta a ni.
- Surgery: Aneurysm ang chi thil siam that nan emaw, thisen kalna tur kawng thar siam nan emaw operation neih a ngai mai thei.
I doctor chuan i tana tha ber tur enkawl dan tur a ruat ang.
FMD laka inven dan tur a awm em?
FMD thlen chhan dik tak chu hriat a la nih loh avangin, ven dan tur chiang tak a awm lo . Mahse, nunphung hrisel zawm a pawimawh a, a bik takin meizuk loh hi a pawimawh a, meizuk hian FMD a ti na zual thei a ni.
FMD nen hian dam rei zawng hi eng ang nge ni?
FMD vei tam zawk hi chu nun pangngaiin an hmang thei a ni . Mahse, a tlem berah chuan, a hmaa kan sawi tawh aneurysm zinga pakhat chu a puak a nih chuan thisen chhuahna leh stroke, nerve tichhe reng thei, a châng chuan thihna pawh a thlen thei a ni. Chuvang chuan inenkawlna mumal tak lak a, doctor thupek zawm a pawimawh em em a ni.
FMD i neih chuan engtin nge i in enkawl ang?
FMD i vei tih hmuhchhuah a nih chuan nangmah ngeiin i hriselnaah mawhphurhna i lak a pawimawh. Hengte hi i ti thei ang:
- I thisen sang kha enfiah fo thin ang che.
- Meizial i zuk chuan chawlhsan nghal rawh. Tin, zuk leh hmuam hman pawh bansan rawh. Hengte hian FMD a ti na zual thei a ni.
- Medical checkup leh appointment-ah te pawh tel ve ngei ang che. Kum khatah vawi khat tal arterial blood pressure test neih a ngai mai thei.
- Doctor-in damdawi a pek zawng zawng chu dik tak leh a hun takah ei vek tur a ni.
FMD vei thenkhat chuan he natna vei midangte thil tawn insem theihna tur support group-a tel hi a \angkai hle niin an hria a, FMD zirchianna atana awareness siam hi a \angkai hle.
FMD vei chuan engtikah nge damdawi lam thurawn a lak ang?
I doctor chuan FMD i neih chuan eng symptoms nge doctor pan tur tih a hriattir ang che. Hei hi a natna artery a zirin a danglam thei.
A bik takin FMD vei te chuan stroke symptoms te hi an hriat chian a ngai a ni . Chûngte chu a thleng thut thei a ni:
- Rilru tibuai.
- Luak chhuak, balance hloh emaw, kal harsa emaw.
- Lu na na tak.
- Thusawi emaw, sawi tur hriatthiam harsat.
- Mit hmuhna lama harsatna a awm.
- Hmai, kut, ke (a bik takin taksa sir khatah) chak lohna emaw, rilru hahna emaw.
Heng symptoms zinga pakhat tal i hmuh chuan damdawi in pan nghal rawh.Ni e, a chhan chu stroke hi emergency a nih avangin enkawl vat a ngai a ni.
Kan sawi tawh atanga kan hriat reng tur pawimawh tak tak te chu:
Okay, chuvangin vawiin hian fibromuscular dysplasia (FMD) chungchang kan sawi nasa hle. Thupui buaithlak deuh mahse, awlsam taka in hriatthiam ka beisei.
FMD hi thisen kalna kawngkhar chhunga cell te chu a pangngai lo taka an lo thang lian a, thisen kalna kawng a ti tawi a, a bulh a, a nih loh leh zungbun hrui ang maia lang a ni.
Hei hi a chhan dik tak hriat ni lo mah se, mi thenkhat chu an hlauhawm zawk a, a bik takin hmeichhiate an ni. Mi zawng zawng hian symptoms an nei vek lo a, mahse a neitute chuan luak chhuak, thisen sang leh kawr chhungah thawm mak tak mai an nei thei. A hlauhawm ber chu natna khirh tak tak, aneurysm leh stroke ang chi a thlen thei a ni.
Vanneihthlak takin he natna hi enkawl dan dik leh nunphung thlak danglam a nih chuan tha taka enkawl theih a ni. FMD nena inzawm symptom i neih chuan doctor pan ngei ngei tur a ni. Chumi hnuah chuan test tul tak tak an kalpui thei a, natna lan chhuah dan tihtlem nan leh harsatna awm lo turin enkawlna an pe thei bawk. Meizial zuk bânsan te, thisen sang thunun te, damdawi lam thurawn zawm te hi FMD natna hrisel taka nunpui nan a pawimawh vek a ni.
Zawhna dang i neih chuan i doctor emaw nurse emaw zawh hreh suh. Hrisel takin awm rawh!
` Fibromuscular dysplasia, FMD, arterial disease, thisen kalna kawng, thisen sang, thisen sang, thisen zam, stroke











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