I thinlung a na, a na, a nih loh leh i rilruah thil mak tak a awm tih i hre fo thin em? Hengte hi a chang chuan kan ngaihven vak loh thil a ni a, mahse thinlung natna hmuh tur awm lo thenkhat chhinchhiahna a ni thei. Vawiin hian chutiang thinlung natna hmuh tur awm lo, mahse na tak thei tur pakhat chu kan sawi dawn a ni. A hming chu Giant Cell Myocarditis, a nih loh leh Mizo tawngin `(Giant Cell Myocarditis)` tih a ni.
Giant Cell Myocarditis hi eng nge ni? A awlsam zawngin i hrethiam ang u.
A awlsam zawngin, Giant Cell Myocarditis hi heart muscle inflammation chi khat a ni lo hle a ni . Inflammation hi a hring chi khat a ni. He natnaah hian thil thleng chu kan taksa ‘inflammatory cells’ thenkhat chu an inzawm khawm a, ‘Giant Cells’ an tih chu cell lian chi khat an siam thin a ni. Heng cell lian tak takte hian hmelma ang bawkin i thinlung ruh chu an bei a, hliam an siam thin.
Ngaihtuah teh, kan thinlung hi tui pump ang mai a ni. Taksa pum puia thisen pump chhuaktu a ni. Chuvangin, heng cell lian tak takte hian thinlung ruh an tihchhiat hian thinlung hian hna a thawk tha thei lo. Chumi awmzia chu:
- Thisen pump a harsa chho zel .
- Thinlung a na chuan a peng zawng zawng chu a rualin a inzawm khawm vek lo .
- Heartbeat control tu electrical signals te chu a disrupted , chu signal te chu heartbeat kaltlangin a kal tha lo hle.
He natna hi a nasat thuai theih avangin, he natna vei te hian thinlung thlak (heart transplant) an neih a ngai fo thin .
Myocarditis leh Giant Cell Myocarditis hi eng nge an danglamna?
Myocarditis hi heart muscle a inflammation a ni bawk. Mahse, giant cell myocarditis hi myocarditis chi khat, a awm lo hle a, a bik takin a awm a ni. Myocarditis chi dang ang bawkin heart rhythm abnormalities, emaw arrhythmias emaw a thlen thei bawk.
Viral infection hi myocarditis thlentu ber a ni tlangpui. Mahse, zirchiangtute chuan he giant cell myocarditis (GCM) hi engvangin nge a lo awm tih hi an la chhui chhuak zel a ni.
He natna hian tute nge a nghawng ber? Engtiang chiahin nge a hluar?
Giant cell myocarditis (GCM) hi naupang hrisel leh kum chanve velah a awm tam ber . Amaherawhchu, mipa leh hmeichhia thliar lovin kum eng pawhah a awm thei.
Hei hi engtiang chiahin nge a awm fo tih erawh chu a tlem hle, a tlem hle. Doctor ten he natna hi kum khatah mi 100,000 zinga pakhat aia tlem lovah an hmuchhuak thin. Chu chu mi 100,000 zingah 0.13 velin an report tihna a ni .
Eng nge a lan chhuah dan? Engtin nge kan hriat chian?
Giant cell myocarditis (GCM) natna lan chhuah hmasak ber chu:
- Heart palpitations (i thinlung a na lutuk emaw, i rilru a na emaw ang maia hriat) .
- A rilru a na
- Thâwk harsaemaw Thâwk hahna emaw
- A ke ruh a hring
- Chau lutuk
Vawi tam tak chu heng symptoms te hi a intan nghal vat thin . Nakinah chuan heart rhythm abnormalities a lo awm thei bawk. He natna vei zinga a chanve aia tam chuan heart rhythm irregularities hlauhawm tak (`Ventricular arrhythmias`) an nei a, chu chu heart chambers atanga tan a ni Chûngte chuan thinlung chu a titawp thut thei a ni.
Tin, heart rate pawh a rang thei hle a, a slow hle thei bawk. I lu a buai emaw i muhil emaw pawh a ni thei . Mi thenkhat chuan natna khirh tak ``cardiogenic shock,'' tih pawh an nei thei a, chutah chuan thinlungin thisen a pump tha thei lo.
Engvangin nge hetiang hi a lo awm? A chhan engte nge ni?
Zirchiangtute chuan giant cell myocarditis (GCM) hi eng nge a thlen tih chiang takin an la hre lo . Thil chi hrang hrang an thlir kual mek a ni. Entîr nân, natna hrik ṭhenkhat, i taksa chakna (immune system) dik lo, a nih loh leh i gene-a thil engemaw chuan natna i vei theihna a tipung thei em tih an enfiah a ni.
Thil dang chu he natna vei zinga 20% velin autoimmune disorder an nei tih hmuhchhuah a ni bawk . Autoimmune natna hi kan taksa invenna, chu chu immune system-in kan taksa cell-te a beih hian a ni. Chuvangin, heng natna chi hrang hrangte hi GCM lo awm chhan emaw, risk factor emaw pawh a ni thei bawk.
Engtin nge he natna hi dik taka i hriat theih?
Giant cell myocarditis (GCM) tih hriat chian nan i doctor chuan i thinlung ruh sample tlemte a lak a ngai ang . Hei hi heart biopsy an ti a. Sample hi laboratory-ah thawn a ni a, cardiac pathologist-in a enfiah a ni.
Hetiang specialist-in sample hi enfiah tir a pawimawh a, a chhan chu giant cell myocarditis biopsy result hi heart muscle inflammation thlentu natna dang, cardiac sarcoidosis ang chi result nen a inang thei a ni. Chuvangin, enkawl dan tur ruahmanna siam tur chuan diagnosis dik tak a pawimawh hle.
He `(Biopsy)` test hi risky tak a ni a, mahse he natna hi i vei em tih chiang taka hriat theihna awmchhun a ni. Heart muscle `(Biopsy)` avanga harsatna awm thei thenkhat chu:
- Pericardial effusion (thinlung chhehvela membrane-a tui awmkhawm) .
- Cardiac tamponade a ni
- Heart chamber (ventricular wall) bang chhunga perforation awm .
He sample lak hian doctor chuan i kawr emaw, i kawr chhungah emaw thisen kalna kawng lian tak hmangin i thinlungah tube te tak te tak, catheter an tih chu a dah lut thin. He catheter hi hmanraw bik (`Imaging`) hmangin thinlung chhungah hruai lut a ni. Tichuan, catheter chhunga hmanraw bik pakhat chuan thinlung ruh te tak te a la a.
A chang chuan `(Biopsy)` pakhat aia tam a ngai mai thei. Hei hi a chhan chu `(GCM)` hian thinlung peng zawng zawng a nghawng dan inang lo mai thei a ni. Thinlung `(MRI)` scan ang chi thil tih hian doctor chuan `(Biopsy)` lakna tur hmun dik tak a siam thei ang.
Eng test dang nge i tih thin?
Lung natna dang i neih loh nan i doctor chuan test dang a ti thei bawk. Chung zinga ṭhenkhat chu:
- Electrocardiogram (EKG) hmanga tih a ni.
- Echocardiogram hmanga tih a ni
- Cardiac catheter hmanga tih a ni
Enkawlnate chu engte nge ni?
I doctor chuan he natna enkawlna atan hian damdawi chi hrang hrang a pe thei ang. Heng damdawi te hi:
- Inflammation a tihziaawm thei .
- Heart rhythm pangngai lo emaw, heart failure emaw a awm loh nan a pui thin.
- Heart transplant i mamawh hma loh chuan hun tam zawk pek i ni thei.
- Nun ti sei turin a pui .
Giant cell myocarditis (GCM) enkawlna dangte hian heart failure leh heart rhythm pangngai lo control-naah a pui a ni. Heng enkawlnate hi a hnuaia mi ang hian a ni thei:
- Damdawi chi hrang hrang
- Catheter hmanga tihbo a ni
- Pacemaker a ni
- Implantable cardioverter defibrillator (ICD) hi taksaah dahin heart rate tihreh leh shock a ni.
- Lung thlak (Heart transplant) a ni
Heart transplant nghah lai hian left ventricular assist device (LVAD) i mamawh mai thei. Heart transplant i mamawh a nih chuan chutiang atana hmanraw nei damdawi inah test leh enkawlna i neih a ngai dawn a ni.
Eng ang damdawi nge hman thin?
Giant cell myocarditis (GCM) enkawlnaah hian i taksa hriselna (immune system) control thei damdawi (immunosuppressants) te a tel a ni. Chu chu, taksa hriselna tichhe thei damdawi tihna a ni. Chung zinga ṭhenkhat chu:
- Cyclosporine (e.g. Gengraf®, Neoral®) hmanga siam chhuah a ni.
- Corticosteroids te hi prednisone ang chi (e.g. Sterapred®, Rayos®) te hi a ni.
- Azathioprine (e.g. Imuran®, Azasan®) te hi a tha ber pawl a ni.
Heng damdawi te hi a rang thei ang bera tan a pawimawh hle. Heng damdawi te hi tel lo chuan a lan chhuah atanga thla thum chhungin heart transplant a ngai thei a, a nih loh leh natna hi a thihpui thei bawk. Mahse, immune system control thei damdawi ei thinte chu thla 12 vel an dam tlangpui.
Enkawlna hian side effect a nei em?
Damdawi i ei chi hrang hrang a zirin side effect a inang lo thei. Side effects langsar zual thenkhat chu:
- Muscle na emaw chak lohna emaw
- Lu na
- Thisen sugar sang
- Kawthalo
- Mu thei lo
Hetiang thil i hriat chuan doctor hnenah hrilh theihnghilh suh.
He natna nen hian nun hi eng ang nge ni ang?
Giant cell myocarditis (GCM) i neih chuan heart failure emaw heart block emaw a thlen thei a ni . Heng dinhmunte hi a nasat chuan (a tlangpuiin thla nga vel chhungin) thinlung thlak a ngai mai thei, i tlin chuan. Mi tam tak chu thinlung thar an dawn hnuah symptom nei lo an ni a, mahse thinlung thar thlawp turin damdawi thar tam tak an ei a ngai dawn a ni.
Giant cell myocarditis hi a veng thei ang em?
Mite chu giant cell myocarditis (GCM) vei hian an dam rei thei a, mahse, heart transplant tel lo chuan natna hlauhawm tak a la ni reng a ni . Kum 1900 chho vela a tam zawk chu GCM vei te hi thla thum aia rei lo an dam a ni. Mahse tunlai hian he natna hi hriat hmasak a nih a, immune system control thei damdawi hmanga enkawl a nih chuan GCM vei zinga 90% chu kum khat tal an dam thei a ni. Heng damdawi te hian heart transplant i mamawh thlengin thla emaw kum tam tak emaw a lei thei che a ni.
Natna hi eng prognosis nge ni?
Heart transplant hnuah giant cell myocarditis (GCM) vei zinga 71% vel chu kum nga chhung an dam (zirchianna dangah 82%) . Heart transplant atanga kum sawm hnuah damchhuah zat chu 68% vel a ni.
Mahse, thinlung thar dawngtu zinga 10% leh 50% inkarah hian cell lian tak tak a lo lang leh thei a ni . Hei hi transplant hnu kar tlemte atanga kum kua thlengin khawi hmunah pawh a thleng thei. Chutiang a nih chuan thla engemaw zat chhung chu steroid i ei a ngai dawn a ni.
Engtin nge ka in enkawl ang?
Giant cell myocarditis (GCM) i neih chuan thla thum atanga thla ruk tal inelna infiamna i pumpelh tur a ni . I GCM a stable tawh chuan i doctor hnenah zawi zawiin exercise lama kir leh chu a him em tih zawt rawh.
Engtikah nge Doctor i hmuh a ngaih?
I damdawi ei avanga side effect nasa tak i neih chuan, emaw, i symptoms a na zual ang tih i hriat chuan doctor pan nghal rawh . I dinhmun enfiah turin doctor pan fo a pawimawh bawk.
Engtikah nge Emergency Treatment Unit (ETU) ah i kal a ngaih ?
I rilru na tak emaw, thawk harsa i tih chuan 911 call emaw, emergency room-ah emaw kal nghal rawh. Hei hi a pawimawh hle a, hengte hi natna khirh tak chhinchhiahna a nih theih avangin.
Doctor hnenah eng zawhna nge ka zawh ang?
Doctor i hmuh hunah heng zawhnate hi zawh theihnghilh suh:
- Follow-up appointment atan engzat nge ka lo kal ngai?
- He natna vei te hian an zawm theihna tur support group a awm em?
- Heart transplant ka mamawh dawn i ti em?
A tawp berah chuan hriat reng tur pawimawh ber
Chuvangin, tunah chuan Giant Cell Myocarditis hi thinlung natna hlauhawm tak, mahse na tak a ni tih i hrethiam tawh mai thei. A pawimawh ber chu a natna lan chhuah dan hriat hmasak a, damdawi lam thurawn la a, enkawl dan tur dik tak tan a ni. Lungngai suh, a chhan chu tunah hian he natna enkawlna tur a awm tawh a, dam rei zawng pawh a sei thei a ni. Chuvangin, i thinlungah thil danglam deuh i hriat chuan ngaihthah suh la, Doctor pan rawh. I thinlung kha enkawl rawh!
` Giant Cell Myocarditis, Giant Cell Myocarditis, Lung Natna, Lung Transplant, Giant Cells, Lung Rhythm Disorder, Immune System, Lung natna, Lung natna











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