Hepatopulmonary Syndrome chungchanga hriat tur awmte!

Nangmah emaw i hriat miin emaw liver natna i neih chuan, emaw, nangmah ngei pawhin he natna hi i neih chuan, he natna hi hriat a pawimawh a, a chang chuan thawk harsatna a thlen thei a ni. Hepatopulmonary Syndrome kan ti a. A hming hi a buaithlak deuhin a lang thei a, mahse a awlsam zawngin han sawi ila, kan ti ang em? A chhan chu liver atanga lung thlenga kal buaina a nih vang a ni.

Hepatopulmonary Syndrome hi eng nge ni tak tak?

A awlsam zawngin sawi ila, hepatopulmonary syndrome hi thin natna avanga harsatna awm lo mahse na tak a ni a, chu chuan lung a tichhe thei a ni. "Hepato" tih thumal hi "liver nena inzawm" tihna a ni. "pulmonary" tih awmzia chu "lungs nena inzawm" tihna a ni. Kan thin leh lung hi thisen kaltlangin a thlunzawm tih i hria em?

Tunah chuan han mitthla teh, mi pakhatin thin natna a neih a, a bik takin cirrhosis ang chi natna a neih chuan, a thin a lo khauh a, a lo hring chhuak a, chu chu lung nena inzawm thisen kalna kawng thenkhat chu a tul lovin a zau ta a ni. Balloon inflating ang maiin. Damdawi lamah chuan hei hi ``Vasodilation`` kan ti thin. Chutianga thisen kalna kawng a zau chuan lung chhunga thisen kal dan pangngai chu a danglam thin. A chang chuan thisen chu lung chhunga oxygen nen a inhmeh tawk lo va, chu ai chuan a kal tlang nghal zawk thin. Chutiang thisen kal dan mumal lo chu ``Shunts`` an ti a. Lung chhunga thisen kalna kawng zau zawng hi ``Vasodilation`` vang a ni a, chu ``Shunts`` avang chuan thisen a oxygen level a tlahniam bawk. Hei hi ``Hypoxemia`` kan ti a ni. I hrethiam em?

He dinhmun hian engtin nge a nghawng che? Thâwk harsa i ti em?

Tunah chuan, "Awle, hei hian engtin nge min nghawng?" Hei hi a nghawng ber chu thawk harsatna (Dyspnea) a ni. Hei hi a lo thleng nghal lo va, zawi zawiin a pung zel zawk a ni. Mi thenkhat chuan a tir lamah chuan an hre vak lo mai thei. Mahse hun kal zelah he natna hi a nasat em avangin ding reng chung pawhin thawk a harsa thei hle.

Mi thenkhat chuan an ṭhut lai emaw, an ding lai emaw chuan thawk harsa an ti a, mahse an mut lai chuan an rilru a hahdam zawk. Midang tan chuan a lehlam a ni; an mut laiin thawk harsatna an nei a, an ṭhut chuan an hahdam zawk. Mahse, he thawk hahna hi hun kal zelah a na zual zel avangin Chronic Respiratory Failure kan ti thin. Chumi awmzia chu engkim hi a tawp thut mai lo va, zawi zawiin i taksa peng leh tissue te hian oxygen an dawng tlem hle tihna a ni. Hei hi hypoxia kan ti a ni .

Hei hi dinhmun hlauhawm tak a ni. Eng nge i hria em? Oxygen hi kan taksa tan a pawimawh hle. A bo vek chuan thluak leh thinlung ang chi taksa peng pawimawh tak takte chu a tichhe vek thei a ni. Enkawl that loh chuan he natna hi nunna atana hlauhawm tak a ni thei.

Tute nge hepatopulmonary syndrome vei tam zawk?

Research atanga a lan dan chuan chronic liver disease vei zinga hmun li a\anga hmun khat vel, a nih loh leh 25% velin hepatopulmonary syndrome an vei tih hmuhchhuah a ni. Liver failure rang tak, na tak, acute liver failure an tih pawhin a awm thei a, mahse a tam lo hle.

A tam zawkah chuan hetiang hi a thleng thin: Thin natna (Cirrhosis of the liver) hian thin (liver) nena inzawm thisen kalna kawng hrang hrangah pressure a tisang a. Damdawi lamah chuan ``Portal Hypertension'' kan ti thin. Chu ``Portal Hypertension'' dinhmun chu mi thenkhatah chuan lung chhunga thisen kalna kawng a tizau a, he hepatopulmonary syndrome hi a thlen thin. Mahse, a tlem hle a, ``Portal Hypertension'' hi chhan dang, thisen zam ang chi avanga lo awm thei a ni a, chuta tang chuan he syndrome hi a lo awm thei bawk.

Hei hi a chhan dik tak chu eng nge ni?

Dik tak chuan scientist-te chuan he natna, portal hypertension an tih hian mi thenkhatah chuan lung chhunga thisen kalna kawng a tizau (vasodilation) chhan chiang takin an la hre lo. Hemi chungchangah hian theory leh ngaihdan tam tak a awm a. Tin, mi zawng zawng chungah a thlen loh chhan pawh a chiang kim lo a, mi thenkhatah chauh a thleng. Liver natna nasat dan nen hian direct-in a inzawm lo niin a lang.

Mahse thil pakhat chu a chiang. Lung chhunga vasodilation hian thisenah oxygen level a ti tlahniam a (Hypoxemia). A awlsam zawngin sawi ila, lung chhunga boruak lut zat leh lung chhunga thisen kal zat inkarah hian inthlauhna a awm a ni. Hei vang hian taksain oxygen a mamawh zat a hmu lo.

Eng nge a lan chhuah dan? Engtin nge hei hi kan hriat chian?

Hepatopulmonary Syndrome natna hi a na lutuk lo a nih chuan symptoms i hmu lo mai thei. Mi tam takin an hriat hmasak ber chu, a hmaa kan sawi tawh ang khan thawk harsa (Dyspnea) . Amaherawhchu, thawk a harsat theih chhan tam tak a awm. Thin natna vei chuan thaw hahdamna kawng hrang hrangin a tawk thei a. Chuvangin, a chang chuan damlo leh doctor-te chuan hei hi Hepatopulmonary Syndrome symptom a ni tih an hre nghal lo mai thei.

A natna a zual zel chuan symptom dang pawh i nei thei bawk a, chungte chu:

• Platypnoea: Hei hi ṭhut emaw, ding emawa thawk harsatna i neih laiin, i mut laiin hahdamna engemaw chen i neih lai a ni.
• Orthopnea: Hei hi a lehlamah a ni. Mut lai chuan thaw hahdam a har viau a, ṭhut lai erawh chuan a tha zawk.
• Cyanosis: Taksa tana oxygen tlakchham vangin hmui, kut zungtang leh a chang chuan vun rawng dum a inthlak thin. Hei hi hmuh theih symptom a ni.
• Kut zungtang club nei: 1.1.Kut zungtang emaw ke ruh emaw tip chu drumstick tip ang maiin a hring leh a bulh ang maiin a lang. Hei hi hypoxemia chhinchhiahna dang a ni.

Heng symptoms bakah hian liver disease leh/ emaw portal hypertension symptoms common tak tak i nei thei bawk. Entir nan:

• Spider angiomas: Thisen kalna kawng te tak te, sen, spider ang chi, vun hnuaia lo lang thin.
• Varicose veins: Thisen kalna kawng lian tak tak chu pum chhungah emaw chaw kawng chhungah emaw hmuh tur a awm.
• A hmaa gastrointestinal bleeding a awm tawhna history .
• Ascites (a pum chhunga natna) .

Engtin nge doctor-te hian hei hi an hriat chian?

Doctor-te chuan he hepatopulmonary syndrome hi a symptom lian pathum a awm dun hian an hre thei a ni:

1. Portal Hypertension: Hei hi thin natna nen a thleng fo thin.

2. Intrapulmonary vascular dilatations: Chumi awmzia chu lung chhunga thisen kalna kawngte chu a dilated tihna a ni.

3. Thisen a oxygen level tlahniam (Hypoxemia) .

A tam zawkah chuan he `(Hepatopulmonary Syndrome)` i neih hian i doctor ten thin natna `(Liver Disease)` emaw `(Portal Hypertension) emaw i nei tih an hmuchhuak tawh a ni. Tichuan i lung chhunga vein awmte chu an en ang a, i thisenah oxygen engzat nge awm tih an teh ang. Heng test te hian i lung chhunga thisen kalna kawngte chu a zau chho zel tih chiang takin a tarlang thei a, chu chuan i thisenah oxygen tlakchhamna `(Hypoxemia).` a tizau a ni

Hei atan hian eng test bik nge tih thin?

Doctor-te chuan he natna hi finfiah nan test eng emaw zat an nei ṭhin. Chung zinga ṭhenkhat chu:

• Pulse oximetry: Hetiang hi i lo ti tawh ngei ang. Test awlsam tak, hrehawm lo tak a ni. I kut zungtang tip-ah hian clip ang chi device te tak te a inbun a. I kut zungtang hmangin êng a ti eng a, a sir lehlamah êng chhuak zat a teh a, chu chu i thisena oxygen awm zat tehna atan hman a ni (Oxygen Saturation). Hei hi test bulpui a ni.
• Arterial Blood Gas (ABG): Pulse oximetry atanga i thisen oxygen a tlem tih a hriat chuan test i tih leh tur chu ABG a ni. Hei hi a chipchiar deuh deuh a ni. I kutphah a artery pakhat atang hian thisen sample tlemte lak a ni . Thisen sample chu i thisena oxygen dissolve zat (PaO2) hriat nan test a ni. Hei hi i lungin i thisenah oxygen a lakluh that dan tehna a ni.
• A rilru a hah lutuk chuan a rilru a buai em em a.Hei hi dilated pulmonary veins hmuhchhuahna atana radiological method tha ber a ni. Echocardiogram hi ultrasound hmanga tih a ni. High-frequency sound wave hmangin i thinlung leh i lung chhunga veins te thlalak a la thin. Contrast-enhanced ultrasound-ah chuan contrast agent, tui bik chu vein-ah an inject a, chu chuan vein te chu a langsar zawk a ni. Contrast echocardiogram i neih chuan technician chuan i vein-ah agitated saline solution a inject a. Hei hi tui chi (salt water)-ah boruak bubble te te dah a, solution siam a ni. Tichuan, heng bubble te te hi hun kal zelah i thinlung dinglam atanga veilam (right to left cardiac shunt) ah an kal em tih an en thin. Hei hian `(Hepatopulmonary Syndrome)` i neih leh neih loh a hriattir thei a ni.

Hei hi engtin nge enkawl a nih?

Tuna hepatopulmonary syndrome enkawlna awmchhun chu supplemental oxygen a ni . Oxygen therapy-ah hian i taksa tanpui nan 100% oxygen thawk chhuah a ngai a ni. Hospital-a pressurized chamber atanga oxygen i lak a ngai mai thei a, chu chu hyperbaric oxygen therapy an ti a ni. A nih loh leh, in lama i hruai theih tur hmanrua, oxygen mask ang chi pek i ni thei bawk. Oxygen hian symptoms, a bik takin thawk hah lutuk tihziaawmna kawngah a pui thei a, i taksa tissue te chu an mamawh oxygen pein a thawk tha thei bawk.

Hepatopulmonary syndrome hi a lo lang leh em? A dam kim thei ang em?

He hepatopulmonary syndrome tihdamna awmchhun chu liver transplant a ni . Ni e, min hre dik khawp mai. Liver transplant hlawhtling tak a nih hnuah chuan lung chhunga thisen kalna kawng zau zawng (vasodilation) leh thisena oxygen tlakchhamna (hypoxemia) te chu zawi zawiin a lo let leh thin. Chu chu a tha chho zel tihna a ni. I lung hnathawh dan pangngaia a lo awm leh theih nan thla ruk atanga thla sawm leh pahnih vel a ngai a ni.

Mahse, mi zawng zawng hi liver transplant atan an tling vek lo. Hei hi chhan hrang hrang a awm a. An tling a nih pawhin liver an dawn theih nan rei tak nghah a ngaih chang a awm. Chuvangin he dam lehna hi hun nena intlansiak ang a ni.

Hei hi thihna thlentu a ni em? Damchhuah hun chhung chu engtin nge ni ang?

Hepatopulmonary Syndrome i neih chuan Chronic Liver Disease i nei tawh ngei ang. End-stage liver disease hi liver transplant tel lo chuan thihna thlen thei a ni. Hepatopulmonary Syndrome hi a side effect leh complication awm zinga pakhat chauh a ni. Mi tam tak chu Hepatopulmonary Syndrome vangin an thi lo a, chu chu oxygen tlakchhamna (hypoxemia) a ni a, mahse an hriselna zawng zawngah a pui a, an dam chhung a ti tawi bawk.

Hepatopulmonary Syndrome vei hian eng chen nge i dam theih ang tih hi thil tam takah a innghat a ni. Hei hian i thin natna a nasat zia te, i hriselna zawng zawng te, leh damdawi lam harsatna dang i neih leh neih loh te a huam a ni. A vaiin liver cirrhosis nei mahse Hepatopulmonary Syndrome nei lo chu liver transplant tel lovin kum sarih vel a dam thei a ni. Mahse, cirrhosis leh Hepatopulmonary Syndrome vei tan chuan liver transplant tel lova dam rei zawng chu kum hnih velin a tlahniam thei a ni.

Mi thenkhat chuan mild hepatopulmonary syndrome an nei thei a, chu chu liver natna angin a na lo hle. Supportive therapy hmang hian an dam rei thei mai thei. Tin, mi thenkhat chu an natna a nasat chuan liver transplant atanga damchhuak lo pawh a ni thei bawk. Hepatopulmonary syndrome vei, liver transplant hlawhtling tak nei te kum nga chhunga dam rei zawng chu 70% vel a ni. Hei hi liver transplant hnua dam rei zawng zawng (75%) aiin a hniam deuh hlek a ni.

Liver natna hian mi tin a nghawng dan a inang lo. Hepatopulmonary Syndrome hi natna hlauhawm tak a ni a, thihna thlen thei a ni. Nangmah emaw, i hnaih ber emaw chunga a thlen hma loh chuan i hre lo mai thei.

Mi tam tak chuan symptoms an nei tlem emaw, an nei lo emaw. Mahse, mi ṭhenkhat tân, a bîk takin hrisêlna ṭha lo tawhte tân chuan hei hi “buh hnuhnung ber” angin a lang thei a ni. Liver natna ang bawkin hepatopulmonary syndrome (HPS) pawh hi hun kal zelah a zual zel a. Liver transplant waiting list-ah i awm tawh a nih chuan HPS i vei tih hriat a nih hunah list-ah hian i sang chho ang. Hei hi a chhan chu doctor-te chuan he natna hian i dam rei zawng a ti tawi thei a, i nunphung a tihhniam thei tih an hriat vang a ni – liver transplant hian a tidam thei tih an hriat vang a ni. Chutih lai chuan oxygen therapy chhunzawm zel chuan hahdamna engemaw chen i hmu thei a, dam rei zawkah a pui thei bawk.

A tawp berah chuan thil pawimawh thenkhat i hriat reng tur

Chuvangin, Hepatopulmonary Syndrome chungchanga kan sawiho atang hian chiang zawka in hriat ka beisei. Heng thute hi hre reng ang che:

• Hei hi liver natna avanga harsatna awm lo mahse na tak a ni thei .
• A lan chhuah dan ber chu thawk harsa (dyspnea) , a bik takin thin natna nei tan chuan a ni.
• Thin natna neiin thawk harsatna a neih chuan he natna (Hepatopulmonary Syndrome) pawh hi rinhlelh tur a ni a, doctor hnenah hrilh tur a ni.
• Tunah hian liver transplantation hi damdawi awmchhun a ni.
• Chu enkawlna chu a awm hma chuan oxygen therapy hian natna lan chhuah dan a thunun thei a, nunna a vawng reng thei bawk.
• Nangmah emaw, i hriat miin emaw heng symptoms te hi i neih chuan doctor pan vat a, thurawn lak a pawimawh hle. A chhan chu, hriat hmasak a nih chuan enkawl leh enkawl dan tur ruahmanna siam a awlsam zawk. Hlauthawng suh, mahse fimkhur a tha ber.

` Hepatopulmonary syndrome, thin natna, lung natna, thawk harsa, oxygen tlakchham, cirrhosis, thin transplant