Thisen thip tih i hre ngai em? Hei hi i tan chuan thil thar a ni mai thei. Kan taksaa thisen hi tui ang maia tui a ni lo va, a viscous deuh deuh a ni. Mahse, he viscosity hi a tul aia sang zawka lo awm ta se engtin nge ni ang? Chutah chuan kan sawi tur condition ``Hyperviscosity Syndrome'' tih chu kan hmu ta a ni. Hei hi i thisen chu a viscous hle a, i thisen kalna kawngah a kal tha thei lo a ni.
Hyperviscosity Syndrome hi eng nge ni? A awlsam zawngin i hrethiam ang u.
A awlsam zawngin, `(Hyperviscosity Syndrome)` tih awmzia chu i thisen a thim hle tihna a ni . Honey ang maiin ngaihtuah rawh. Tui aiin khawizu hi a thim zawk a, hetah pawh hian chutiang chu a thleng thin. Kan thisenah hian thisen zam (red blood cells), thisen var (white blood cells), thisen proteins te ang chi thil a awm a. Chung zinga pakhat emaw a aia tam emaw a tam chuan emaw, thisen sen (red blood cells) te chu a pianzia a danglam chuan thisen chu a thim hle thei a ni. Stew-ah flour tlem tal dah belh a, a thick ang mai a ni.
Chutianga thisen a thim chuan kan taksa pum puia thisen kalna kawng nalh tak tak kal tlangin awlsam takin a kal lo. Chutah chuan harsatna a lo chhuak tan ta a ni.
Hetiang dinhmun hi a hlauhawm thei ang em?
Ni e, Hyperviscosity Syndrome hi natna khirh tak a ni . Eng nge a nih i hria em? Thisen a kal tha lo a nih chuan kan taksa peng pawimawh tak tak (thluak, thinlung leh kal) te hian an mamawh oxygen leh nutrients an hmu lo. Hei hian thisen kalna kawng a tikhawlo thei a, organ dysfunction a thlen thei bawk.
Naupang têin he natna hi a neih chuan an ṭhanlenna leh an ṭhanlenna chu direct-in a nghawng thei a ni . A chhan chu an thluak leh taksa a lo thang chak lai hian thisen kal chak lohna hi harsatna lian tak a ni. Chuvang chuan hei hi kan hriat chian a pawimawh hle a ni.
Tute nge Hyperviscosity Syndrome vei tam zawk?
Hetiang dinhmun hi tu chungah pawh lo awm thei mahse, mi thenkhat chu an hlauhawm zawk. Waldenstrom macroglobulinemia tih natna hlauhawm tak nei te hi Hyperviscosity Syndrome vei an hlauhawm hle. Hei hi kan thisena protein chi khat bik macroglobulin an tih chu a tam lutuk hian a ni. Statistics atanga a lan dan chuan Waldenstrom macroglobulinemia vei zinga 30% aia tam chuan an dam chhungin engtik lai pawhin Hyperviscosity Syndrome an vei dawn a ni.
Hyperviscosity Syndrome natna lan chhuah dan chu engte nge ni? I fimkhur ang u!
He natna lan chhuah dan hi mi hrang hrangah a inang lo thei a, mahse common leh common lo zawkah kan then thei a ni.
A lan chhuah dan tlangpui:
- Lu na: Lu na fo, a chang chuan na tak tak.
- Seizures: Mi thenkhat chuan seizure ang chi an nei thei.
- Vun rawng sen (reddish skin tone): A chang chuan hmai leh kut ang chi hmunte chu a sen angin a lang thei.
A tam lo zawk, mahse a lan chhuah dan pawimawh tak tak:
- Chest pain: Chhung na a awm thei a, thinlung natna nen a inang.
- Kal harsa: Kal a harsa thei a, i balance hloh ang maiin.
- Hriatna lama harsatna: I hriatna hloh ang maiin i inhria thei a, i bengah thawm hrang hrang i hre thei bawk.
- Thisen chhuak mumal lo: Entirnan, hmui thisen chhuak leh hnar thisen chhuak fo.
- Thâwk harsa (Dyspnea): Stairs chhoh lai emaw, hna rit tak tak thawh lai pawhin thawk harsatna nei angin i inhria thei.
- Vertigo: I lu a buai thei a, i lu a inher ang maiin i ding thei a, i ding thei lo bawk.
- Mit a inthlak danglam: Mit hmuh fiah lo leh mit pahnih a awm thei.
Heng symptoms pakhat emaw a aia tam emaw i neih chhunzawm zel chuan doctor thurawn lak hi a tha ber ngei ang. Hlauthawng suh, mahse anmahni pawh ngaihthah suh.
Nausen naupangte zingah Hyperviscosity Syndrome hi eng thilin nge a thlen?
Nausen piang thara he natna hi a lo awm theih chhan bik engemaw zat a awm a:
- Genetic disorders: Entirnan, ``Down syndrome`` ang chi dinhmun.
- Gestational diabetes: Naupai laia nuin zunthlum a neih chuan naute a nghawng thei a ni.
- Hereditary disorders: Chhungkaw zinga mi tu emaw chuan heng natna hi a lo nei tawh a nih chuan.
- Late umbilical cord clamping: Hei hi a then phei chuan a thlen thei bawk.
- Twin-to-twin transfusion syndrome: Hei hi twins inang lo tak takte inkara placenta-a thisen kalna kawng inzawmna dik lo an neih chuan a thleng thei a ni.
Puitlingah hian he natna hi engte nge ni?
Puitlingah chuan a hmaa kan sawi tawh ang khan `(Waldenstrom macroglobulinemia)` hi a chhan ber a ni. Chumi piah lamah chuan a chhan dang engemaw zat a awm thei bawk:
- Thisen cancer chi hrang hrang: Entirnan, `(Acute myeloid leukemia - AML)` leh chi dang `(Leukemia)`.
- Chronic hypoxia: Hei hi thawkna lam natna thenkhat ang chi thil vang a ni thei.
- Connective tissue natna: Entirnan, `(Rheumatoid arthritis)` leh `(Lupus)` ang chi natna te.
- Cryoglobulinemia: Thisenah protein pangngai lo a lo awm thin.
- Essential thrombocythemia: Thisen platelet tamna nasa tak a ni.
- Multiple myeloma: Ruhro cancer a ni.
- (Paraneoplastic syndromes) te hi a awm a.Taksa hmun danga cancer vanga symptoms awmte khawlkhawm.
- (Polycythemia vera): Thisen sen (red blood cells) a pung lutuk.
- (Sjögren’s syndrome): Taksa chhunga tui siamtu glands te tichhe thei natna a ni.
- Myelodysplastic syndrome: Ruh chhunga cell siam chhuahna lama harsatna a awm.
Heng hmingte hi i tan chuan a buaithlak deuhin a lang mai thei. Hriat tur pawimawh tak chu heng natna zawng zawng hian Hyperviscosity Syndrome a thlen vek lo va, mahse hetiang dinhmun hnuaia awm hian thisen a ti thim thei tih hi a ni.
Hyperviscosity Syndrome hi engtin nge kan hriat theih ang? (Diagnosis) tih a ni.
Doctor-te chuan he natna hi thisen test eng emaw zat an tih hian an hmuchhuak tlangpui a , chung zinga ṭhenkhat chu:
- Arterial blood gas test: Thisen a oxygen leh carbon dioxide awm zat a enfiah thin.
- Bilirubin test: Thisen sen (red blood cells) a chhiat avanga thil sen (yellow substance) bilirubin awm zat a enfiah thin.
- Thisen thlum test: Thisen thlum (glucose) level enfiah thin ang che.
- Complete blood count (CBC): Thisen chhunga thil awm zawng zawng, thisen sen, thisen var, leh protein te level a teh thin.
- Creatinine test: Kal (kidney) hnathawh that leh that loh enfiah thin.
- Liver function test: Liver protein awm leh awm loh a enfiah thin.
- Serum viscosity emaw whole blood viscosity test: Thisen viscosity dik taka tehna test.
- Protein test: Thisen a protein chi hrang hrang awm zat tehna a ni.
Heng test result atang hian doctor chuan ``Hyperviscosity Syndrome'' i neih leh neih loh chiang takin a hre thei a ni.
Hei hi eng enkawlna nge ni? (Enkawl dan tur) .
``Hyperviscosity Syndrome'' enkawlna hi a chhan bulpui a zirin a danglam thei . Hetiang dinhmunah hian dehydration a na zual thei a, doctor chuan intravenous (IV) hydration .
Thil na tak tak thenkhatah chuan doctor-te chuan hetiang hi an hmang thei a:
- Partial exchange transfusions: Hei hian thisen tlemte lakchhuah a, saline solution hmanga thlak a ni. Hei hian thisen viscosity tihziaawmna kawngah a pui thei a ni.
- Plasmapheresis: Hei hian plasma tlemte, thisen tui lam chu lakchhuah a, plasma aiah dah a ni. Hei hian thisen atanga protein tha lo tak tak te chu a paih chhuak a, a viscosity a tihziaawm bawk.
Heng enkawlnate hi i doctor-in a ruat a, i dinhmun leh a chhan a zirin a ni.
Hyperviscosity Syndrome hi ven dan tur a awm em?
Dik tak chuan `(Hyperviscosity Syndrome)` hi a taka ven theih dan tur a awm lo. Mahse, naupai i nih chuan i naute hian he natna hi a vei theihna tur tihtlem nan thil engemaw zat i tih theih a awm :
- Genetic testing nei rawh: Hei hian genetic disease nei fa neih theihna chance a hriatthiam theih nan a pui ang che.
- Ei leh in tha tak ei la, exercise neih fo : Hei hian gestational diabetes vei theihna a ti tlem thei a ni.
- Medical clinic-ah kal la, a ruahman angin test la: I naupai chhung zawngin damdawi lam thurawn zawm a pawimawh hle.
Hyperviscosity Syndrome vei tan eng nge thleng? (Chhunzawmna)
Hyperviscosity Syndrome hi enkawl vat ngai a ni . Enkawl loh chuan nunna atana hlauhawm harsatna leh taksa peng hrang hrang a tichhe thei a ni.
Thu lawmawm tak chu naute leh puitling a hun taka enkawl te chu he natna atang hian an dam chhuak vek fo thin . Mahse, hyperviscosity syndrome hi underlying chronic condition avanga lo awm a nih chuan a lo awm leh loh nan enkawl chhunzawm zel a ngai mai thei.
Hyperviscosity Syndrome hi eng ang nge a nih?
Hei hi mi tin a inang lo thei. Thisen a thim chuan thluaka thisen kal a tlahniam a, chu chuan lu na, luak chhuak, a nih loh leh muhil pawh a thlen thei . Mi thenkhat chuan thawk harsatna emaw mitdelna emaw an nei thei bawk .
Eng thil dangin nge thisen zam tichhe thei?
I thisen a thim theih chhan hrang hrang a awm. I thisen sen (red blood cells) te chu a pianzia dik lo a nih chuan i thisen chu a thim thei a ni . I thisen chhunga thil awm zawng zawng, thisen zam, thisen var, emaw, i thisena protein awmte chu a pangngai lo taka a san chuan a thleng thei bawk.
A tawp berah chuan thil hriat reng tur (Take-Home Message) .
Okay, chuti a nih chuan tunah chuan kan sawi tawh, ``Hyperviscosity Syndrome.`` tih hi i hrethiam zawk tawh a ni.`` Hei hi thisen a thim a, taksa pum puiah a luang tha thei lo tih hre reng ang che.
Hei hi thisen lama harsatna nei thenkhatah a thleng thei a, chubakah nausen piang thar, genetic emaw hereditary disease thenkhat neiah pawh a thleng thei bawk.
Hei hi natna khirh tak ni mah se, a hmaa hriat chhuah leh enkawl a nih chuan mi tam zawk chu an dam vek a ni. Chuvangin, nangmah emaw, i fain emaw harsatna emaw, symptom emaw i neih chuan doctor pan vat la, thurawn la rawh. Hlauthawng suh, a pawimawh ber chu inhriattir hi a ni.
Zawhna dang i neih chuan i doctor hnenah zawh hreh suh:
- He `(Hyperviscosity Syndrome)` lo awm chhan ber chu eng nge ni?
- Hei hi hriat theih nan eng test nge tih thin?
- Engtin nge enkawl a nih?
- Enkawl ka chhunzawm a ngai dawn em ni?
- Fa dang ka neih chuan ani pawhin he natna hi a nei thei ang em?
Hetiang zawhna hi zawt la, i rilrua harsatna awm zawng zawng chu chinfel rawh.
` Hyperviscosity syndrome, thisen zam, thisen natna, symptom, enkawl dan, naupang hriselna, puitling hriselna











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