I fa hian an taksaah lump danglam tak tak a nei em? Hei hi Complex Lymphatic Anomales (CLA) chhinchhiahna a ni thei!

A châng chuan kan fate taksaa inthlâk danglamna tenau te kan hmuh hian kan hlauthawng takzet a ni lawm ni? A bik takin chu thilte chu eng nge ni tih chiang taka kan hriat loh chuan. Vawiin hian kan sawi dawn a, thil awm lo tak, mahse hriat tur pawimawh tak kan sawi dawn a ni. Hei hi Complex Lymphatic Anomalies , a tawi zawngin (CLA) an ti a. Mi thenkhat chuan a hmain (Lymphangiomatosis) an ti bawk. Chuvangin heng hming pahnih hi i hre mai thei.

A hmasain, Complex Lymphatic Anomalies (CLA) hi eng nge ni?

A awlsam zawngin sawi ila, Complex Lymphatic Anomalies (CLA) hi a awm lo hle a, mahse pianpui atanga lo piang thei a ni a, naupangin naupang lymphatic system-ah lymphatic malformations emaw lymphangiomas emaw tih hming pu benign tumor a nei a ni. Heng tumor te hi naupang ruh, connective tissue leh taksa peng dang ah te a thang lian thei a, chhiatna a thlen thei a ni.

Ngaihtuah teh, kan fa hian a pian tirh atangin hetiang dinhmun hi nei mahse, a tam zawkah chuan a natna lan chhuah dan hi a lo upa deuh deuh a, kum engemaw zat hnuah pawh a lang tan thin. Chuvang chuan hei hi hriat chian a tlai fo thin.

Chuti a nih chuan, he Lymphatic System hi eng nge ni?

Okay, tunah chuan lymphatic system hi eng nge ni tih i ngaihtuah mai thei. A awlsam zawngin kan taksaah hian defense system mak tak a ni. Kan rama sipai te ang a ni. He lymphatic system hian kan taksa chu natna laka invenna atan a pui a, a lo awm chuan a do thei bawk. Kan immune system-a thil pawimawh tak a ni.

Lymphatic system hi tube te tak te network atanga siam a ni a, chu chu lymphatic vessels an tih te, lymph node ang chi gland te, leh spleen ang chi organ te a ni. Heng lymphatic vessels te hi tube te tak te ang mai an ni. Taksa tissue atanga lymph fluid an la khawm a, an filter a, an tifai a, thisenah an kir leh thin. Hei hi hna mak tak a ni lo maw?

CLA hi chi hnih a awm a, chungte chu Isolated leh Systemic te an ni.

Complex Lymphatic Anomalies hi chi hnih ah then theih a ni a:

1. Isolated CLAs: Hei hi naupang taksa hmun khata tumor te inkhung hran a nih chuan a ni. Entirnan, rilru chhungril chauh an nghawng thei. Hetiang a nih chuan lung leh rilru natna (mediastinum) te hi a nghawng nasa ber a ni.

2. Systemic CLAs: Hetiang a nih chuan heng tumor te hi naupang taksa hmun hrang hrangah a awm thei a, chu chu ruh, rilru leh pum chhungah te a awm thei a ni.

Chutiang chuan natna lan chhuah dan leh enkawl dan pawh a natna hmun azirin a inang lo thei.

Complex Lymphatic Anomalies (CLA) chi hrang hrangte chu engte nge ni?

CLA hi chi hrang hrang pali a awm a. Type tin hian symptoms inang thenkhat nei mahse, dinhmun hrang hrang an ni. Tin, anmahni thlentu gene mutations pawh a danglam bawk.

• A rilru a buai em em a, a rilru a hah em em bawk a. Generalized Lymphatic Anomaly (GLA):Hetiang dinhmun hian naupang taksa peng hrang hrang a nghawng tlangpui. Entirnan, heng tumor te hi ruh, spleen, liver, lung, leh rilru chhunga soft tissue (mediastinum) ah te a awm thei.
• Kaposiform Lymphangiomatosis (KLA): Hei hi CLA chi khat na ber leh darh chak ber a ni. KLA-ah chuan naupang taksa pum puia lymph fluid phurtu lymphatic vessels te chu a lian chho zel a. Hei hian an chhehvela taksa peng, ruh leh tissue te chu a rawn luhchilh a, a tichhia a ni.
• Central Conduction Lymphatic Anomaly (CCLA): Naupang CCLA vei te pawh hian lymph vessel lian tak tak an nei bawk. Mahse, CCLA-ah chuan heng vessel lian zawkte hi torso-ah an awm tam ber. Hei hian chaw ei kawng a nghawng thei a, naupang taksa atanga lymph fluid tha taka a chhuah theih loh nan a veng thei bawk.
• Gorham-Stout Disease (GSD): Gorham’s disease tia hriat bawk, ​​he natna hian ruh chhunga lymphatic vessels a siam avangin ruh tam tak a tithianghlim thin. "Vanishing bone disease" an ti bawk. Eng ruh pawh a nghawng thei. Mahse, GSD vei naupangte hian ruh hloh an nei tam ber a, chu chu ruh, luruh, kawr ruh leh serh ruh (cervical spine)-ah te ruh hloh a ni.

He CLA condition hi engtiang chiahin nge a awm?

Complex Lymphatic Anomalies hi a takah chuan a awm lo hle . An tam lutuk loh avângin, a châng chuan doctor-te tân dik taka hriat a harsa thei hle. Chuvangin symptoms i neih chuan a rang thei ang bera specialist pan a pawimawh hle.

Eng thilin nge he CLA hi a thlen?

Doctor leh zirchiangtute chuan CLA hi eng nge a thlen tih hriat tumin an la bei mek a ni. Mahse, tun hnaia zirchianna hrang hrangah chuan he natna hi nu leh pa atanga fate hnena pek chhuah hereditary gene mutations te, pian hnua somatic gene mutations te pawh a ni thei tih a tarlang. Chumi awmzia chu genetically linked a ni tihna a ni.

Tute nge CLA vei theihna hlauhawm?

Complex Lymphatic Anomalies hian tu pawh a nghawng thei. A bik takin, he natna lan chhuah dan hi naupan lai emaw, tleirawl lai emaw hian a lang tlangpui. Chuvangin, pian tirh lamah pawh he natna hi awm mahse, a natna lan chhuah nan hun engemaw chen a la ngai thei.

Chuti a nih chuan, CLA natna lanchhuahna chu engte nge ni?

He natna vei naupang hrang hrangah hian symptoms a inang lo thei. Tin, eng organ system nge a nghawng tih leh a nasat dan azirin symptoms a inang lo bawk. A tam zawkah chuan he natna hi a zual zel a. Chuvang chuan a lan chhuah dan thenkhat chu kan ngaihven vak lo mai thei a, a nih loh leh natna dang vang niin kan ngai mai thei bawk.

I fa thawkna kawng a nghawng a nih chuan:

Hetih lai hian Asthma ang chi symptoms a lang thei.

• Cough awm reng.
• Thâwk harsa (dyspnea).
• Thâwk chhuah laiin thawk hah ( a whistling sound ).

I fa ruhro (skeletal system) a nghawng a nih chuan:

• Ruh emaw ruh emaw a na.
• Tlu tlemte pawh hian ruh tliak a thlen thei .
• Ke ruh leh ke ruh (limbs) a natna (numbness) a awm.
• Nerve compression avanga natna emaw chak lohna emaw .

I fate chaw ei dan (digestive system) a nghawng a nih chuan:

• Abdominal distension leh pum na .
• Anemia leh hahna reng reng.
• Kawthalo.
• Chaw chu a thlum lo.
• Nausea leh luak chhuak.
• Chhan awm lovin taksa rihna tihtlem.

I fa zun kawng a nghawng a nih chuan:

• Zun chhunga thisen (hematuria) a awm.
• Flank natna a awm .
• Naupang thisen sang .

I fain heng symptoms pakhat emaw a aia tam emaw a neih chuan doctor rawn la. Hengte hi CLA-a symptoms bik a ni lo a, mahse test neih a pawimawh hle.

Engtin nge doctor-te hian he CLA natna hi an hriat chhuah?

CLA hi thil awm lo tak a nih avangin leh a natna lan chhuah dan pawh a inang lo hle a, a chang chuan doctor-te tan chuan a natna dik tak hriat a harsa thei hle. Naupangte lung leh ruh a nghawng fo avangin i fa doctor chuan hetiang test hi a ti thei ang:

• Bronchoscopy: Thlawhna kawngah natna hrik emaw thil dang dang emaw a awm leh awm loh enfiah nan.
• Pulmonary function testing: I lung hnathawh that dan teh rawh.
• Whole-body MRI: Thil chi hrang hrang, ruh natna, emaw, pum chhunga tui awm leh awm loh enfiah nan.
• X-ray: MRI-a ruh rinhlelh emaw hliam emaw anga langte enfiah lehzual nan. Chest X-ray hian lung chhunga thil dik lo awmte pawh a en thei bawk.

A châng chuan doctor-te chuan lymph node leh tissue sample te tak te (biopsy) an la a, microscope hmangin an enfiah ṭhin. He test hian CLA hi chiang takin a hriat theih laiin, a chang chuan harsatna a thlen thei a, chu chu lung chhehvela lymph fluid awmkhawm (chylothorax) te hi a ni. Chuvang chuan doctor-te chuan diagnosis siam nan less invasive test-ah an innghat fo thin.

CLA hi engtin nge enkawl a nih?

CLA hian naupang taksa hmun hrang hrang a nghawng theih avangin doctor-te chuan an thawk ho a, chu chu naupang tana remchang tur enkawlna ruahman nan multidisciplinary approach an hmang tihna a ni. CLA enkawl hian naupang natna lan chhuah dan control hi ngaih pawimawh ber a ni. Chutiang ti tur chuan hetiang hi i ti thei ang:

• Bone grafting: GSD ang chi condition-a ruh chhiatna atan.
• Protein tamna ei tur emaw, thisen chhunga ei tur (total parenteral nutrition emaw TPN) emaw.
• Sclerotherapy: Tumor emaw lymph vessel emaw tihtlem emaw tihchak emaw.
• Surgery: Tumor lakchhuah emaw, lymph fluid kal awlsam zawk nan tube te te (shunt) dah emaw.
• Radiation therapy emaw chemotherapy: Cancer ni lo tumor tihtlem nan (hengte hi natna khirh tak tak, nunna atana hlauhawm tak takah chauh hman a ni).

Tun hnaiah hian he natna thlentu genetic mutations targeted therapies targeted therapies te pawh hman a ni tawh bawk. Heng therapies te hi CLA enkawlna atana first-line treatment atan pawh a tangkai hle tih hmuhchhuah a ni bawk.

Complex Lymphatic Anomalies (CLA) hi ven theih a ni em?

Vanduaithlak takin, ni lo . CLA hi naupai laiin a awm a, a chhan dik tak erawh hriat a la ni lo. Chuvangin, i naute hian he natna hi a neih loh nan engmah tih theih i nei lo.

CLA avanga harsatna awm thei te chu engte nge ni?

CLA hian i fa chu hlauhawmah a dah thei a ni:

• Ascites: Pum chhunga tui awmkhawm.
• Ruh tliak a awm.
• Chylothorax leh Chylopericardium: Lung (pleura) emaw thinlung chhehvel bawm (pericardium) khuh tu membrane-a lymph fluid leh thau awmna milky fluid (chyle) awmkhawmna a ni.
• Lung / pneumothorax a tlakbuak.
• Liver a tha lo.
• Paralysis a awm.
• Pericardial atanga chhuak (Pericardial effusion) a awm.
• Pleural effusion leh cardiogenic pulmonary edema te a awm bawk.

Heng harsatna thenkhat hi a nasat em avangin a natna lan chhuah dan hriat chian a, doctor thupek zawm a pawimawh.

CLA nei mi pakhat hmalam hun chu eng nge ni?

Complex Lymphatic Anomalies (CLA) hi damdawi a awm lo . I fa hmalam hun chu eng taksa kalphung nge a nghawng tih leh a natna lan chhuah dan a nasat danah a innghat a ni.

CLA vei zingah hian Pleural effusions hi thihna thlentu ber a ni. Amaherawhchu, enkawl dan leh enkawl dan mumal tak a awm chuan naupang chu nun pangngaia a awm theih nan tanpui theih a ni.

Engtikah nge Doctor ka hmuh ang?

I fa hian heng symptoms te hi a neih chuan doctor pan nghal rawh:

• Pum emaw, intestine emaw a na.
• Zun ah thisen a awm chuan.
• Khuh, thawk hah, thawk harsat.
• Sawifiah loha rilru hahna, hahna, emaw, taksa rihna tlahniam emaw.

Chung zinga pakhat tal i neih chuan tihkhawtlai lova Doctor rawn pan mai tur a ni.

Doctor hnenah eng nge ka zawh ang?

I fa doctor hnenah hetiang zawhna hi i zawt mai thei:

• He natna hian ka fa taksa peng engte nge a nghawng?
• Ka fa tan hian eng enkawlna kawng nge awm?
• Ka fa hian operation a mamawh em?
• Complication symptoms te hi ka hriat chian tur em ni?

Heng zawhnate hi zawh a, thil awmdan hriatthiamna chiang tak neih a pawimawh hle.

A tawp berah chuan ka sawi tur chu...

I fain CLA (lymphangiomatosis) a vei tih i hriat chuan an hriselna leh hmalam hun a nghawng dan tur ngaihtuahin hlauhna leh lungkhamna i neih hi thil pangngai a ni. Mi tam takin he natna hi kan la hre ngai lo mai thei. Tin, chutiang tur venna tur engmah i tih theih tur a awm lo.

I fate ṭanpuina hmasa ber chu he natna, a lan chhuah dan leh a enkawl dante hriat chian a ngai a ni. Lymphatic system natna lama tui tak doctor hmu rawh. I zawhnate chu an chhang thei a, i fa mamawh damdawi lam enkawlna bik an pe thei bawk.

CLA damdawi awm lo mah se, enkawl dan dik leh enkawl dan dik chuan i fa chu nun hlim leh hrisel tak a neih theih nan a pui thei a ni. Chuvangin, chak takin awm la, i fa tan i theihtawp chhuah rawh.

` Complex Lymphatic Anomalies, Lymphangiomatosis, Lymphatic System Natna, Naupang Tumor, Osteomalacia, Pulmonary Symptoms, Naupan laia natna hmuh tur awm lo