Mi mal—a bîk takin naupang tê tê—an kâ atâna lei lian danglam tak anga langte chu i hmu ngai em, a nih loh leh i hre tawh mai thei em? A châng chuan lei chu ha emaw, hmui emaw kal tlangin a chhuak thei bawk. Damdawi lamah chuan he natna hi Macroglossia tia hriat a ni. A hming chu hlauhawm tak angin a lang thei a, mahse khawngaihin lungngai suh. Vawiin hian he thu hi a awmzia chiang taka i hriatthiam theih nan thu awlsam takin sawi ila.
Macroglossia hi eng nge ni tak tak a, engtin nge a hriat theih?
A awlsam zawngin sawi ila, macroglossia tih hian i lei chu i hmui nena inmil lo taka lian tihna a ni. Naupang tê têah hmuh tam ber a nih laiin, puitlingah pawh a nghawng thei bawk. Thil tam takah chuan pianpui natna a ni a, chu chu pian tirh atanga awm tihna a ni a, a tam zawkah chuan genetic disorders te nen a inzawm a, chu chuBeckwith-Wiedemann natna emaw Down syndrome emaw . Mahse, macroglossia hi a hnu lamah cancer chi hrang hrang, natna khirh tak tak, emaw, damdawi lam thil dang avanga lo awm thei a ni bawk.
I ngaihtuah mai thei, “Ka fa lei hi a lian deuh niin a lang, hei hi an nei thei ang em?” Chutiang a nih chuan heng chhinchhiahnate hi ngun takin ngaihven rawh:
- Lei chhuah chhunzawm zel: Hei hi chhinchhiahna langsar ber leh hmuh theih ber a ni. Lei chu nuam taka chawlh hahdam theihna tur ka chhungah hmun a awm lo mai mai ang maiin a lang fo thin.
- Thâwk lak harsatna: 1.1.
- Thâwk i tih laiin ri sang tak, whistling ri i hre mai thei a, chu chu damdawi lam chuan stridor tia hriat a ni.
- A dang pawhin, thawk laiin, a bîk takin mut laiin, bengchheng emaw, thawm ri emaw i hmu thei bawk. Hei hi stertor tia hriat a ni.
- Chaw ei harsa (dysphagia): Lei a lian lutuk avangin i fa chuan ei tur chu a hmuiah a dah a, a ei a, a ei tha thei lo thei bawk. Naute hian hnute pek emaw, bottle atanga in emaw atan latching on an nei harsa thei. A chang chuan chaw ei laiin choking sensation a awm thei bawk.
- Drooling: Lei hian hmui a khar tha thei lo a, chuvangin chronic drooling hi a awm fo a, chu chu pillow emaw thawmhnaw emaw hnim fo hian i hmu mai thei.
- Thusawi thiam lohna: Lei chu thusawi thiamna atân a pawimawh hle avângin, lei lian zâwk chuan thumal sawi thiam emaw, a inmil taka sawi emaw a ti harsa thei a, chu chuan thusawi thiam loh a thlen fo ṭhîn.
Takeaway pawimawh ber chu heng chhinchhiahnate hian macroglossia a lantir thei a, mahse hriselna dinhmun dang hnuaia awmte chhinchhiahna a ni thei bawk. Evaluation dik tak neih theih nan Nirogi Lanka -a professional te zawt fo thin ang che.
Hei hi a awm fo em tih i ngaihtuah mai thei. Dik tak chuan macroglossia hi thil awm lo tak a ni. A hluar dan dik tak hriat chian chu thil harsa tak a ni a, a chhan chu a mah chauhva primary diagnosis ang ni lovin, natna hnuaia awm chhinchhiahna angin a lang tlangpui zawk a ni.
Eng thilin nge macroglossia hi a thlen?
Macroglossia hian chhan hrang hrang a nei a. Thil thleng tlemteah chuan mimal chu hriselna lama harsatna dang nei lovin lei lian tak neia piang an ni. A tlangpuiin, damdawi lam dinhmun hnuaia awm chhinchhiahna a ni. Chungte chu pianpui (genetic) emaw, natna, hliam emaw, damdawi lam enkawlna avanga naupan laia neih emaw a ni thei.
Heng chhan hrang hrangte hi han chhui ila:
Pianpui (Genetic) Thil awm dan
Macroglossia hi genetic disorder engemaw zat nen a inzawm a, chung zingah chuan:
- Beckwith-Wiedemann syndrome: Hei hian taksa thanna a nghawng a. Hetiang natna nei naupangte hian taksa lian zawk leh taksa peng lian zawk an nei thei. Naupang cancer thenkhat vei pawh an hlauhawm zawk bawk. Thil pawimawh tak chu Beckwith-Wiedemann syndrome vei naupang 90% vel chuan macroglossia an nei a ni.
- Hurler/Hunter syndrome (Mucopolysaccharidosis): Hengte hi metabolic disorder a ni a, taksain sugar molecule a tihchhiat dan a nghawng a, chu chuan lei a ti lian thei a ni.
- Down syndrome: Down syndrome vei te hi pianpui chromosome extra nei an ni a, chu chuan thluak leh taksa hmasawnna a nghawng a ni. Macroglossia hi taksa mizia hriat lar tak a ni a, Down syndrome vei te zingah hmuh fo thin a ni.
Acquired Conditions te chu a awm
A châng chuan, macroglossia hi nakin lawkah metabolic, endocrine, emaw infectious diseases vangin a lo awm ṭhin.
- Amyloidosis natna: 1.1.Hei hi protein nena inzawm natna a ni a, protein pangngai lo chu tissue leh taksa peng hrang hrangah a awm a, an hnathawh a tichhe thin. Macroglossia hi amyloidosis chhinchhiahna langsar tak a ni a, oral region a inrawlh a ni.
- Hypothyroidism: I thyroid gland-in thyroid hormone a siam tlem a, i metabolism a ti hniam a, a awm fo thin. Hypothyroidism hi macroglossia thlentu a ni a, a bik takin naupangte zingah hian a awm fo thin.
- Acromegaly: Thil awm lo tak, growth hormone siam chhuah tam lutuk avanga lei, hmui, kut leh ke tihzauh dan pangngai lo.
- Diphtheria: Bacteria natna hrik kai thei a ni a, lei na tak a ti na thei.
Tumor leh Macroglossia te a awm
Benign emaw malignant emaw growth thenkhat chu macroglossia angin a lang thei a:
- Lymphangioma: Lymphatic system-a tumor tha lo tak a ni a, mucous membrane-ah fluid-filled cyst a awm thei a, chu chuan lei a ti lian thei a ni.
- Hemangioma: Thisen kalna kawng atanga siam benign growth.
- Lymphoma: Cancer chi khat, lymphatic system tichhe thei a ni.
Engtin nge macroglossia hi hmuhchhuah a nih?
Nangmah emaw, i fa emaw doctor i tlawh hunah, a hmasa ber chu taksa enfiahna a ni . Doctor chuan uluk takin lei, lu leh kawr a enfiah ang. Chumi hnuah chuan macroglossia leh a chhan awm thei hriselna dinhmun hnuaia awmte hriat theihna turin diagnostic test engemawzat neih theih a ni.
Heng diagnostic test thenkhat hi chu:
- Computed Tomography (CT scan): Hetiang tih dan hian X-ray leh computer processing hmangin i emaw i fa emaw hmui, lu leh kawr hmun 3D-a chipchiar taka thlalak siam a ni a, chu chuan a chhunga thil awmte chu chiang takin a hmu thei a ni.
- Magnetic Resonance Imaging (MRI): Hei hi hrehawm lo tak a ni a, magnet chak tak , radio wave , leh computer hmangin i taksa peng leh chhungril lam thil awmte thlalak chiang tak tak siam a ni.
Doctor-te chuan heng endikna result a\angin macroglossia awm chhan leh enkawlna ruahmanna \ha ber an ruat ang.
Macroglossia hi eng enkawlna nge awm?
Ngaihven awm tak chu, naupang thenkhat, macroglossia na lo nei te chuan an lo puitlin chuan hmasawnna an hmu thei a; an hmêl ruhte a lo ṭhan chhoh zêl chuan, taksa lian zâwk puan lian zâwka inhmeh ang maiin, lei atân hmun a tam zâwk fo ṭhîn.
Mahse, chutiang chu a ni reng reng lo. Macroglossia enkawl hian doctor-te chuan a hnuaia natna awm dan hriatchhuah leh enkawl hi an ngaih pawimawh hmasa ber a ni. Chumi hnuah chuan macroglossia ngei tan pawh symptomatic management a awm leh thin.
Macroglossia enkawlna kawng hrang hrangte chu:
- Damdawi: Lei hring tihziaawmna turin damdawi corticosteroid ang chi hi pek theih a ni.
- Orthodontic enkawlna: 1.1.Lei lian zawk hian ha alignment a nghawng a nih chuan orthodontic intervention hian heng thilte hi a siam tha thei a ni.
- Surgery: Thil engemaw takah chuan—a bîk takin thawk harsa emaw, ei harsa emaw ang chi harsatna nasa tak a awm hunah—lei lian zâwk tihtlem nân operation neih a ngai thei a ni. Mahse, macroglossia vei zinga 10% vel chauhvin surgical intervention an mamawh a ni.
Ka fain macroglossia a vei theihna tur chu ka tihtlem thei ang em?
Macroglossia hi pianpui emaw, thlahtute emaw nena inzawm a nih fo avangin, ven theih a ni lo fo. Mahse, a chang chuan natna hrik kai theih a nih avangin, chutiang dinhmun thlen thei natna laka inven nan vaccine (eg, diphtheria laka invenna) te chu a hun taka hriat reng a, a hlauhawmna chu i tihtlem thei a ni .
Ka fa hian macroglossia a vei a nih chuan eng nge ka beisei ang?
Kan sawi tawh ang khan macroglossia hi a tlangpuiin natna hnuaia awm, genetic emaw congenital disorder emaw chhinchhiahna a ni. Chuvangin, a pawimawh ber chu chu root cause chu hriatchhuah leh enkawl hi a ni.
I fa chuan an dinhmun bik (specific underlying condition) chu enkawlna a dawng tawh mai thei a; chu enkawlna ruahmanna chu zawm tlat chu i ngaih pawimawh ber a ni. An dinhmun kal dan tur leh follow-up appointment neih hun tur chungchangah i naupang enkawltu doctor nen inrawnkhawm rawh.
Doctor hnenah eng zawhna nge ka zawh ang?
I fain macroglossia a vei tih hmuhchhuah a nih hian zawhna tam tak neih hi thil awmdan pangngai a ni. I doctor zawh tur zawhna pawimawh thenkhat chu hetiang hi a ni:
- Macroglossia hi eng nge ni tak tak?
- Hei hian ka fate nitin nunah engtin nge nghawng a neih ang?
- Ka fate macroglossia natna chhan bulpui ber chu eng nge ni?
- Eng enkawlna nge i rawt a, a hlawhtlinna chu engzat nge ni?
- Enkawlna hian eng chen nge a daih ang a, eng side effects awm thei nge ka ngaihven tur?
- In lama ka fa enkawl dan tur chiang tak a awm em (eg, chaw pek dan emaw, mut dan tur emaw)?
Heng zawhnate hi zawh hreh ngai suh. I ngaihtuahnate tihfai chu enkawlna ṭha ber pêk nân a pawimawh hle. I doctor chuan heng thil chipchiar tak takte hi lawm takin a hrilhfiah ang che.
Takeaways pawimawh tak tak (Nirogi Lanka) .
Macroglossia diagnosis dawn hian lungngaihna a thlen thei a, mahse a chhan chu a hnuaia awm dinhmun chhinchhiahna pakhat chauh a ni fo thin. A pawimawh ber chu rilru hahdam taka awm a, professional medical guidance lak vat hi a ni.
- I fa lei chu a tlangpuiin a lian lo tih i hriat emaw, kan sawiho tawhte i hmuh chuan Pediatrician emaw, Ear, Nose, and Throat (ENT) surgeon emaw rawn la.
- A chhan bulpui hriatchhuah a, targeted treatment plan zawm a nih chuan Macroglossia hi a tha thei ang bera enkawl theih a ni.
- Naupang thenkhatah chuan he dinhmun hi an lo puitlin chuan a pianphungah a lo tha chho thei a ni.
- I fate hmangaihna leh puihna mumal tak pe chungin i doctor thurawn khauh taka zawm hi a pawimawh hle.
Nangmah chauh i ni lo tih hre reng ang che. Hetiang harsatna tawk nu leh pa dang tam tak an awm bawk. Damdawi lam kaihhruaina dik leh i inpekna nen chuan i fate tan a tha ber tur i hmu thei ang.
👩🏽 ⚕️ Zawhna tam tak (FAQs) .
💬 Macroglossia, a nih loh leh lei lian zawk chu eng nge ni?
Hetiang dinhmun hi hmui lian leh te nena khaikhin chuan lei a lian lo va, a chhuak emaw, ha a press emaw a nih chuan a thleng thin. Chuvang chuan lei chu a inzawm fo thei a, ha atanga pressure avanga lei sir lamah scalloped edges i hmu thei bawk.
💬 Hei hi pianpui (piang) natna a ni em?
Naupangah chuan pianpui natna a ni fo a, Down syndrome emaw Beckwith-Wiedemann syndrome emaw nei te zingah hmuh tur a awm fo. Mahse, puitling pakhatin a lei a lian nghal a nih chuan, a hnuaia thil awm, amyloidosis emaw hypothyroidism emaw nen a inzawm thei a ni.
💬 Lei a lian lutuk chuan eng nge thleng ang? Surgery hmanga tihtlem theih a ni em?
Lei lian lutuk chuan ei leh in, leh thusawi kawngah harsatna nasa tak a thlen thei a ni. Chubakah, thawk lama harsatna hlauhawm tak tak, Sleep Apnea, mut laiin lei hian thawkna kawng a tikhawlo thei a ni. Heng thilte hi a awm chuan doctor-te chuan lei lian tham tak chu functional level-a tihhniam nan glossectomy an tih procedure an ti thei a ni.
Thupui: Macroglossia, Lei lian, Naupang lei hriselna, Thâwk harsa, Chaw ei harsa, Beckwith-Wiedemann syndrome, Down syndrome, Nirogi Lanka, Lei lama harsatna
